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Tezacaftor/ivacaftor ne ivacaftor (inowanikwa semvura inonwiwa)

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Mhando dzinowanikwa
Nezve mushonga uyu

Tezacaftor/ivacaftor neivacaftor inoshandiswa kurapa cystic fibrosis (CF) muvarwere vane makore matanhatu ekuberekwa nekupfuura. Inoshandiswa chete kune varwere vane makopi maviri eF508delmutation, kana vane mutation imwe chete muCF transmembrane conductance regulator (CFTR) gene yavo. Chiremba wenyu achashandisa bvunzo yekutarisa mutation usati watanga kurapwa nechinodawa ichi. Chinodawa ichi chinowanikwa chete kana uine chinyorwa chechiremba. Chigadzirwa ichi chinowanikwa mumaumbirwo anotevera edoserage:

Usati washandisa mushonga uyu

Pakusarudza kushandisa mushonga, ngozi dzokutora mushonga iyeye dzinofanira kuyeranidzwa nezvakanaka zvichaita. Iyi sarudzo iwe nesachiremba wenyu muchaita. Kune mushonga uyu, zvinotevera zvinofanira kufungwa: Udza chiremba wako kana wakambonzwa chero chirwere chisina kujairika kana allergic reaction kumushonga uyu kana mimwe mishonga. Uyewo udza nyanzvi yako yehutano kana uine mamwe marudzi eallergies, akadai sekudya, dyes, preservatives, kana mhuka. Kune zvigadzirwa zvisingadi kuraira, verenga zvinyorwa zvepachena kana zvinosanganiswa zvakanaka. Ongororo dzakakodzera hadzina kuitwa pane hukama hwezera kune migumisiro ye tezacaftor / ivacaftor ne ivacaftor musanganiswa muvana vane makore asingasviki 6. Kwakachengeteka uye kushanda hazvina kusimbiswa. Ongororo dzakakodzera pane hukama hwezera kune migumisiro ye tezacaftor / ivacaftor ne ivacaftor musanganiswa hazvina kuitwa muvanhu vakwegura. Zvisinei, hapana matambudziko chaiwo evagere vakanyorwa kusvika pari zvino. Hapana ongororo dzakakwana muvakadzi dzekuona ngozi yemwana pakushandisa mushonga uyu panguva yekuyamwisa. Yera mabhenefiti anogona kuitika pamwe nengozi dzinogona kuitika usati watora mushonga uyu panguva yekuyamwisa. Kunyangwe mimwe mishonga isingafaniri kushandiswa pamwe chete, mune mamwe mamiriro mishonga miviri yakasiyana inogona kushandiswa pamwe chete kunyangwe kuwirirana kungangoitika. Mumamiriro ezvinhu aya, chiremba wako angada kuchinja chiyero, kana mamwe matanho angave achidiwa. Paunenge uchitora mushonga uyu, zvakakosha kuti nyanzvi yako yehutano izive kana uri kutora chero mishonga iri pazasi. Kuwirirana kunotevera kwakasarudzwa zvichienderana nechinangwa chavo uye hazvisi zvese zvinosanganisirwa. Kushandisa mushonga uyu nechero mishonga inotevera hakusi kukurudzirwa. Chiremba wako angasarudza kusakubata nemushonga uyu kana kuchinja mimwe mishonga yaunotora. Kushandisa mushonga uyu nechero mishonga inotevera kazhinji hakusi kukurudzirwa, asi kunogona kudiwa mune zvimwe zviitiko. Kana mishonga yose ikanyorwa pamwe chete, chiremba wako angachinja chiyero kana kuti ungashandisa imwe kana ese mishonga. Mimwe mishonga haifaniri kushandiswa panguva yekudya kana pedyo nenguva yekudya kana kudya marudzi akati wandei ezvokudya sezvo kuwirirana kungangoitika. Kushandisa doro kana fodya nemimwe mishonga kunogona zvakare kukonzera kuwirirana kuitika. Kuwirirana kunotevera kwakasarudzwa zvichienderana nechinangwa chavo uye hazvisi zvese zvinosanganisirwa. Kushandisa mushonga uyu nechero chinotevera kazhinji hakusi kukurudzirwa, asi kungasava nyore kudzivisa mune zvimwe zviitiko. Kana zvakashandiswa pamwe chete, chiremba wako angachinja chiyero kana kuti ungashandisa mushonga uyu, kana kukupa mirairo yakakosha pamusoro pekushandisa zvokudya, doro, kana fodya. Kuvapo kwemamwe matambudziko ehutano kunogona kukanganisa kushandiswa kwemushonga uyu. Ita shuwa kuti unoudza chiremba wako kana uine mamwe matambudziko ehutano, kunyanya:

Mashandisirwo aungaita mushonga uyu

Tora mushonga uyu chaizvoizvo sezvakarayirwa nachiremba wako. Usatore zvakawanda, usatore kazhinji, uye usatore kwenguva yakareba kupfuura yakarayirwa nachiremba wako. Kuita izvozvo kunogona kuwedzera mukana wezvinhu zvinokanganisa. Mushonga uyu unouya nechiratidzo chemashoko emurwere. Verenga utevedzere mirairo nekufunga. Bvunza chiremba wako kana uine mibvunzo ipi neipi. Mimedze mapiritsi ese. Usapwanyisa, kuputsa, kana kucheka. Tora mushonga uyu nezvokudya zvine mafuta, kusanganisira zvokudya zvakagadzirwa nemafuta kana mafuta, chizi, mazai, nyama, nati, kana mukaka wose. Usadya grapefruit kana kunwa muto we grapefruit paunenge uchishandisa mushonga uyu. Doses yemushonga uyu ichave yakasiyana kune varwere vakasiyana. Tevedzera mirairo yechiremba wako kana mirairo iri parinenge. Ruzivo runotevera rinosanganisira chete avhareji doses yemushonga uyu. Kana dose yako yakasiyana, usachinje kunze kwekunge chiremba wako akakuudza kuti uite izvozvo. Huwandu hwemushonga waunotora hunotsamira pakusimba kwemushonga. Uyewo, nhamba ye doses yaunotora zuva rega rega, nguva inobvumirwa pakati pe doses, uye nguva yaunotora mushonga inotsamira pane dambudziko remuviri rauri kushandisa mushonga. Kana wakanganwa dose yemushonga uyu, tora nekukurumidza sezvinobvira. Zvisinei, kana iri nguva yeku dose yako inotevera, siya dose yakarasika udzokere kune yako dosing schedule. Usatore doses kaviri. Kana wakanganwa dose uye iri maawa 6 kana mashoma kubva panguva yaunotora mushonga wako, tora dose nekukurumidza sezvinobvira. Kana iri kupfuura maawa 6, mirira kusvika ipapo kushandisa mushonga uye siya dose yakarasika. Usatore mushonga wakawedzerwa kuti uwedzere dose yakarasika. Chengetedza mushonga mubhodhoro rakavharwa pane tembiricha yekamuri, kure nekupisa, hunyoro, uye chiedza chakananga. Chengetedza kuti urege kuvhunduka. Chengetedza kure nevana. Usachengetse mushonga wakapfuura zuva kana mushonga usingachadiwi. Bvunza nyanzvi yehutano maitiro aunofanira kubvisa chero mushonga usingashandisi.

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