I-acoustic neuroma yi-tumor engathuthuki elikhula esimithweni esikhulu esivela endlebeni yangaphakathi siye ebuchosheni. Lo mthwemi ubizwa ngokuthi yi-vestibular nerve. Amasebe omthwemi athinta ngokuqondile ukulinganisela nokuzwa. Ukuqina okuvela kwi-acoustic neuroma kungabangela ukulahleka kokuzwa, ukukhala ezindlebeni nezingqinamba zokulinganisela. Elinye igama le-acoustic neuroma yi-vestibular schwannoma. I-acoustic neuroma ikhula emachibini e-Schwann ahlanganisa i-vestibular nerve. I-acoustic neuroma ivame ukukhula kancane. Ngokungavamile, ingakhula ngokushesha futhi ibe khulu ngokwanele ukucindezela ubuchopho futhi ithonye imisebenzi ebalulekile. Ukwelashwa kwe-acoustic neuroma kuhlanganisa ukuqapha, ukukhishwa kweradieysheni nokususwa ngokusebenza.
Njengoba isibopho sikhulayo, kungenzeka kakhulu ukuba sibangele izimpawu ezibonakalayo noma ezimbi kakhulu. Izimpawu ezivamile ze-acoustic neuroma zihlanganisa:
Imbangela ye-acoustic neuromas ngezinye izikhathi ingahlotshaniswa nenkinga ene-gene ekhromosome 22. Ngokuvamile, le gene ikhiqiza i-protein ecindezela i-tumor esiza ukulawula ukukhula kwama-Schwann cells ahlanganisa izicubu. Ochwepheshe abazi ukuthi yini ebangela le nkinga ene-gene. Ngokuvamile ayikho imbangela eaziwayo ye-acoustic neuroma. Lushintsho lwe-gene luzuzwe kubantu abane-disorder engaqondakali okuthiwa yi-neurofibromatosis uhlobo 2. Abantu abane-neurofibromatosis uhlobo 2 ngokuvamile baba nokwanda kwe-tumors ezicubwini zokuzwa nokuqondisa ekhanda ngezinhlangothi zombili. Lezi tumors ziyaziwa ngokuthi yi-bilateral vestibular schwannomas.
Ekuguleni okubangelwa yi-autosomal dominant, i-gene eshintshile iyi-gene ebusayo. Itholakala kwenye ye-chromosomes ezingelona ubulili, ebizwa ngokuthi yi-autosomes. I-gene eyodwa eshintshile kuphela edingekayo ukuze umuntu athinteke yilolu hlobo lwesimo. Umuntu onesimo se-autosomal dominant—kulesi sibonelo, ubaba—unesilinganiso sama-50% sokuthola ingane ethintekile ene-gene eyodwa eshintshile kanye nesilinganiso sama-50% sokuthola ingane engathintekile.
Isici esiyedwa esiqinisekisiwe sokungena engozini kwe-acoustic neuromas ukuba nomzali onalesi sifo esingavamile se-genetic esibizwa nge-neurofibromatosis type 2. Noma kunjalo, i-neurofibromatosis type 2 ibalelwa kuphela cishe ku-5% yezimo ze-acoustic neuroma.
Fani ephawulekayo ye-neurofibromatosis type 2 yi-tumors ezingahlukumezi ezinamathambo okuqondisa ekhanda kokubili. I-tumors nayo ingase ithuthukiswe kwamanye amathambo.
I-Neurofibromatosis type 2 iyaziwa njengokugula kwe-autosomal dominant. Lokhu kusho ukuthi i-gene ehlobene nesifo ingadluliselwa engwaneni ngomzali oyedwa kuphela. Ingane ngayinye yomzali othintekile inesilinganiso sama-50-50 sokuyizuza.
I-acoustic neuroma lingabangela ukukhubazeka okungapheli, okuhlanganisa:
Ukuhlolwa okuhlelekile komzimba, okuhlanganisa nokukheka kwezindlebe, kuvame ukuba yisinyathelo sokuqala ekuxilongeni nasekwelapheni i-acoustic neuroma.
I-acoustic neuroma ivame ukuba nzima ukuyixilonga emazingeni okuqala ngoba izimpawu zingase zibe lula ukungazinaki futhi zithuthuke kancane kancane ngokuhamba kwesikhathi. Izimpawu ezivamile ezinjengokuphulukela kokuzwa zibuye zihambisane nezinye izinkinga eziningi zezindlebe eziphakathi nezingaphakathi.
Ngemva kokubuza imibuzo mayelana nezimpawu zakho, ilungu leqembu lakho lokunakekelwa kwezempilo liyakwenza ukuhlolwa kwezindlebe. Ungase udinga lezi zilingo ezilandelayo:
Ukuhlolwa kokuzwa, okuyaziwa ngokuthi yi-audiometry. Lolu viwo luqhutshwa yisazi sokuzwa esibizwa ngokuthi yi-audiologist. Phakathi nokuhlolwa, imisindo iqondiswa endlebeni eyodwa ngesikhathi. I-audiologist iveza uchungechunge lwemisindo yemithamo ehlukahlukene. Ubonisa njalo lapho uzwa umsindo. Umgomo ngamunye ubuyiselwa emazingeni aphansi ukuthola ukuthi nini ungasazwa kahle.
I-audiologist ingase futhi iveze amazwi ahlukahlukene ukuhlola ukuzwa kwakho.
Izithombe. Ukucubungula komfanekiso olukhulu lwe-magnetic resonance (MRI) olunezidakamizwa ezibonakalayo kuvame ukusetshenziswa ekuxilongeni i-acoustic neuroma. Lolu viwo lokucubungula izithombe lungathola iziphumu ezincane njenge-1 kuya ku-2 millimeters ububanzi. Uma i-MRI ingatholakali noma awukwazi ukwenza isikhombiso se-MRI, i-computerized tomography (CT) ingase isetshenziswe. Noma kunjalo, ukuhlola kwe-CT kungase kudlulisele iziphumu ezincane.
Ukuhlolwa kokuzwa, okuyaziwa ngokuthi yi-audiometry. Lolu viwo luqhutshwa yisazi sokuzwa esibizwa ngokuthi yi-audiologist. Phakathi nokuhlolwa, imisindo iqondiswa endlebeni eyodwa ngesikhathi. I-audiologist iveza uchungechunge lwemisindo yemithamo ehlukahlukene. Ubonisa njalo lapho uzwa umsindo. Umgomo ngamunye ubuyiselwa emazingeni aphansi ukuthola ukuthi nini ungasazwa kahle.
I-audiologist ingase futhi iveze amazwi ahlukahlukene ukuhlola ukuzwa kwakho.
Ukwelashwa kwenu kwe-acoustic neuroma kungase kuhluke, kuye ngokuthi:
Umshwana wokuzihlangula: I-August iyinkundla yolwazi lwezempilo futhi izimpendulo zayo azihlanganisi iseluleko sezokwelapha. Njalo thintana nochwepheshe bezokwelapha onelayisensi eduze nawe ngaphambi kokwenza noma yiluphi ushintsho.