Created at:1/16/2025
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IPineoblastoma iwumdlavuza omningi, okhula ngokushesha we-brain oqala e-pineal gland, indawo encane ejulile e-brain yakho. Lo mdlavuza onamandla uqala kakhulu kubantwana nabantu abadala abasebancane, nakuba ungase uqale kunoma yimuphi ubudala.
I-pineal gland ikhiqiza i-melatonin, i-hormone esiza ukulawula isikhathi sakho sokulala nokuvuka. Uma i-pineoblastoma iqala lapha, ingaphazamisa umsebenzi ojwayelekile we-brain futhi idale izinselele ezinkulu zempilo ezidinga ukunakekelwa ngokushesha kwezokwelapha.
IPineoblastoma iyingxenye yama-brain tumors athiwa yi-pineal parenchymal tumors. Kubhekwa njenge-Grade IV tumor, okusho ukuthi ikhula ngokushesha kakhulu futhi isakazeka ngokushesha e-brain nase-spinal cord.
Lolu hlobo lomdlavuza luyingxenye engaphansi kuka-1% yazo zonke i-brain tumors, okwenza kube yinto engavamile kakhulu. Umdlavuza uqala ezicini ze-pineal gland kunokuba ezicini ezizungezile, okuyenza ihluke kwezinye izinhlobo ze-brain masses kule ndawo.
Ngenxa yendawo yayo ejulile e-brain, i-pineoblastoma ingavinjelwa ukusabela okujwayelekile kwe-cerebrospinal fluid. Lokhu kuvinjelwa kuvame ukubangela ukwanda kokucindezeleka ngaphakathi kwekhanda, okwenza izimpawu eziningi abantu abazibonayo.
Izimpawu ze-pineoblastoma zivela ngoba umdlavuza ukhulisa ukucindezeleka ngaphakathi kwekhanda lakho futhi uthinta izakhiwo ze-brain eziseduze. Abantu abaningi baphawula lezi zimpawu zikhula emavikini kuya ezinyangeni njengoba umdlavuza ukhula.
Nazi izimpawu ezivamile ongazihlangabezana nazo:
Abanye abantu baphawula iqoqo elithile lezinkinga zokunyakaza kwamehlo okuthiwa yi-Parinaud's syndrome. Lokhu kwenzeka lapho umdlavuza ucindezela ezindaweni ze-brain eziseduze eziqondisa ukunyakaza kwamehlo, okwenza kube nzima ukubuka phezulu noma kubangele abafundi bakho ukuthi basabela ngokuhlukile ekukhanyeni.
Ezimweni ezingavamile, ungase uqaphele ukushintsha kwe-hormone noma ukukhula kwasebusheni kubantwana, njengoba i-pineal gland iseduze kwezinye izakhiwo ze-brain ezikhiqiza i-hormone. Lezi zimpawu zingase zibe zingekho ngokucacile ekuqaleni kodwa zivame ukuba zimbi njengoba umdlavuza ukhula.
Imbangela eqondile ye-pineoblastoma ayaziwa, futhi lokhu kungabaza kungase kuzwakale kuyadumaza uma ufuna izimpendulo. Njengomdlavuza eminingi, cishe iqala ngokuhlanganiswa kwezinto zofuzo nezimo ezingaphandle esingaziqondi ngokugcwele.
Abacwaningi baye baqaphela ezinye izimo zofuzo ezikhulisa ingozi, nakuba lezi zingevamile kakhulu:
Izimo eziningi ze-pineoblastoma zivela ngokungahleliwe ngaphandle komlando womndeni noma ukunqanyulwa kwezinto zofuzo. Lokhu kusho ukuthi ezigamekweni eziningi, awekho wena noma umndeni wakho eningathanda ukwenza ukuvimbela ukukhula kwalo.
Izimo ezingaphandle njengokubekwa emikhakheni ye-radiation kuye kwaphakanyiswa njengabalingani abangaba khona, kodwa awekho ubufakazi obucacile obuhlanganisa izimbangela ezingaphandle ezithile ne-pineoblastoma. Ukungavamile kwalolu hlobo lomdlavuza kwenza kube nzima ukutadisha le miqondiso engaba khona ngokugcwele.
Kufanele ufuna ukunakekelwa kwezokwelapha ngokushesha uma uhlangabezana nobuhlungu obukhulu ekhanda obuqhubeka bukhula, ikakhulukazi uma buhlangene nokuphefumula, ukugabha, noma ukushintsha kobuso. Lezi zimpawu zingabonisa ukwanda kokucindezeleka e-brain yakho, okudinga ukuhlolwa okusheshayo.
Ungalindi uma uqaphela ukushintsha ngokuzumayo kokulinganisela, ukulinganisela, noma ukunyakaza kwamehlo. Nakuba lezi zimpawu zingaba nezimbangela eziningi, zidinga ukuhlolwa kwezokwelapha okusheshayo ukuze kuvinjwe izimo ezinkulu njenge-brain tumors.
Xhumana nodokotela wakho phakathi nezinsuku ezimbalwa uma uhlangabezana nezinkinga zokulala eziqhubekayo, izinkinga zokukhumbula, noma ukukhathala okungavamile okungaphuli ngokuphumula. Lezi zimpawu zingase zikhule kancane kancane kodwa zisadinga ukuhlolwa kwezokwelapha.
Kubantwana, qaphela ngokukhethekile ukushintsha kwesimo sengqondo, ukusebenza esikoleni, noma izigaba zokukhula. Ukukhula kwasebusheni noma ukushintsha okukhulu ngokuzumayo kufanele futhi kukhuthaze ukubonisana kwezokwelapha, njengoba lokhu kungase kube uphawu lwemiphumela ehlobene ne-hormone evela kuma-brain tumors.
Ukuqonda izinto ezikhulisa ingozi kungakusiza ukuthi uqonde ukuthi kungani lo mdlavuza ongajwayelekile ukhula, nakuba kubalulekile ukukhumbula ukuthi ukuba nezinto ezikhulisa ingozi akusho ukuthi uzokuthola i-pineoblastoma.
Izinto ezikhulisa ingozi eziyinhloko zifaka:
Lokhu kushiwo, iningi labantu abane-pineoblastoma abanawo ama-risk factors aqondakalayo. Lo mdlavuza ubonakala ukhula ngokungahleliwe ezimweni eziningi, okungase kuzwakale kuyadumaza kodwa futhi kusho ukuthi cishe awukwazanga ukuvimbela.
Ubulili abubonakali buthinta kakhulu ingozi, futhi awekho ubufakazi obucacile bokuthi izinto zokuphila ezifana nokudla noma ukuzivocavoca zithinta ukukhula kwe-pineoblastoma. Ukungavamile kwalolu hlobo lomdlavuza kwenza kube nzima ukuqonda ama-risk factors amancane angase abe khona.
IPineoblastoma ingabangela izingozi ezinkulu ngenxa yendlela yayo enamandla nendawo yayo endaweni ebalulekile ye-brain. Ukuqonda lezi zingozi ezingaba khona kungakusiza ukuba ulungiselele uhambo oluzayo futhi wazi izimpawu okumele uzilandele.
Izingozi eziqondile zivame ukuphathelene nokucindezeleka okukhulu kwe-brain:
Ngenxa yokuthi i-pineoblastoma isakazeka kalula nge-cerebrospinal fluid, ingase ihlwanyele ezinye izingxenye ze-brain ne-spinal cord. Lokhu kusakazeka, okuthiwa yi-leptomeningeal dissemination, kungabangela izimpawu ezintsha ezindaweni ezahlukene zesimiso sakho sezinzwa.
Izingozi ezihlobene nokuphathwa zingase zenzeke, kufaka phakathi imiphumela evela ekusebenzeni, ukwelashwa kwe-radiation, noma i-chemotherapy. Lezi zingase zibe izinkinga zokukhumbula, ubunzima bokufunda, noma ukungalingani kwe-hormone, ikakhulukazi kubantwana abanawo ama-brain asekhulayo.
Abaphila isikhathi eside bangase bahlangabezane nezinselele eziqhubekayo ngokulinganisela, ukubona, noma umsebenzi wokwazi. Noma kunjalo, abantu abaningi bazivumelanisa kahle nalezi zinguquko ngokusekelwa okufanele nezinsizakalo zokuvuselela.
Ukuhlonishwa kwe-pineoblastoma kudinga ukuhlolwa okukhethekile ngenxa yendawo yomdlavuza ejulile e-brain. Iqembu lakho lezokwelapha lizosebenzisa izithombe eziphambili nezinye izindlela ukuze lithole isithombe esicacile sokuthi kwenzekani.
Inqubo yokuhlola ivame ukuqala nge-MRI scans ye-brain yakho ne-spine. Lezi zithombe eziningiliziwe zisiza odokotela ukuba babone usayizi womdlavuza, indawo, nokuthi usakazeke yini kwezinye izingxenye zesimiso sakho sezinzwa.
Nanku okumelwe ukulindele ngesikhathi somsebenzi wokuhlola:
Ukuthola isampula yesicubu se-biopsy kungase kube nzima ngenxa yendawo ye-pineal gland. Ezimweni ezithile, odokotela bangase baqale ukwelashwa ngokusekelwe ezithombeni nezinye izivivinyo uma i-biopsy ingaba yingozi kakhulu.
Inqubo yonke yokuhlola ivame ukuthatha izinsuku ezimbalwa kuya kwesonto, kuye ngokuhlelwa nokuthi imiphumela iyatholakala kanjani ngokushesha. Iqembu lakho lezokwelapha lizosebenza ukuze lithole izimpendulo ngokushesha ngangokunokwenzeka ngenkathi liqinisekisa ukunemba.
Ukuphathwa kwe-pineoblastoma kuvame ukufaka ukusebenza, ukwelashwa kwe-radiation, ne-chemotherapy ngenxa yendlela yomdlavuza onamandla. Uhlelo lwakho lokwelashwa luzolungiswa ngesimo sakho esithile, kufaka phakathi usayizi womdlavuza, ukusakazeka, nempilo yakho yonke.
Ukusebenza kuvame ukuba yisinyathelo sokuqala uma kungenzeka. Izinjongo zukuhlanza umdlavuza ngokuphephile ngangokunokwenzeka futhi unciphise ukucindezeleka e-brain. Ukususa okuphelele kungase kube nzima ngenxa yendawo ejulile ye-pineal gland eduze kwezakhiwo ze-brain ezibalulekile.
Uhlelo lwakho lokwelashwa lungase lufake lezi zindlela:
Ukuphathwa kwe-radiation kubaluleke kakhulu ngoba i-pineoblastoma ivame ukusakazeka nge-cerebrospinal fluid. Lokhu kusho ukwelapha hhayi nje indawo yomdlavuza wokuqala kodwa futhi lonke i-brain ne-spine ukuvimbela ukubuyela.
Ukuphathwa kunzima futhi kuvame ukuthatha izinyanga eziningi. Iqembu lakho lezokwelapha lizokuqapha eduze kulo lonke le nqubo futhi lilungise uhlelo njengoba kudingeka ngokusekelwe endleleni oqaphela ngayo.
Ukuphathwa kokunakekelwa ekhaya ngesikhathi sokwelashwa kwe-pineoblastoma kudinga ukunakekelwa kokubili izimpawu zomzimba nokuphila kwengqondo. Iqembu lakho lezokunakekelwa kwezempilo lizokuhlinzeka ngemiyalo eminingiliziwe, kodwa nazi ezinye izindlela ezijwayelekile ezingasiza.
Gxila ekutholeni ukudla okuhle nokugcina umzimba uqinisile, ngisho noma imiphumela yokwelashwa yenza ukudla kube nzima. Ukudla okuncane, okuvamile kuvame ukusebenza kangcono kunokudla okukhulu, futhi ukudla okungenamnandi kungase kube lula ukubekezelela ngesikhathi se-chemotherapy.
Nazi izindawo ezibalulekile zokuqapha nokulawula:
Ukuphumula kubalulekile ngesikhathi sokwelashwa, kodwa umsebenzi olula ungasiza ekuqinisweni kwamandla nasesimweni sengqondo uma uzizwa ukhululekile. Lalela umzimba wakho futhi ungaphuli kakhulu ezinsukwini ezinzima.
Ukusekelwa kwengqondo kubaluleke kakhulu njengokunakekelwa komzimba. Cabanga ngokuxhumana namaqembu okusekela, izinsizakalo zokwelapha, noma eminye imindeni ehlangabezane nezinselele ezifanayo. Abaningi bathola induduzo ekuhlanganyeleni amava nabanye abaqonda ngempela.
Ukulungiselela imihlangano ehlobene ne-pineoblastoma kungakusiza ukuba wenze kakhulu isikhathi sakho neqembu lezokwelapha futhi uqinisekise ukuthi imibuzo ebalulekile iphendulwa. Ukufika uqondisile kunganciphisa ukucindezeleka futhi kukusize uzizwe ulawula kakhulu.
Ngaphambi komhlangano wakho, bhala zonke izimpawu ozibonile, kufaka phakathi ukuthi zaqala nini nokuthi zishintshe kanjani ngokuhamba kwesikhathi. Faka imininingwane mayelana nemithetho yekhanda, ukushintsha kokulala, izinkinga zobuso, noma noma yikuphi ukukhathazeka okunye.
Letha lezi zinto ezibalulekile kuyo yonke imihlangano:
Lungisa imibuzo ethile mayelana nokuhlolwa kwakho, izinketho zokwelapha, nokuthi yini okufanele uyilindele. Buza ngemiphumela, isikhathi, nokuthi ukwelashwa kungase kuthinte kanjani imisebenzi yansuku zonke noma umsebenzi. Unganqikazi ukucela incazelo uma amagama ezempilo ebonakala ephazamisa.
Cabanga ngokuletha incwadi noma ucele imvume yokurekhoda izingxenye ezibalulekile yengxoxo. Uzothola ulwazi oluningi, futhi kuyinto evamile ukukhohlwa imininingwane kamuva, ikakhulukazi uma uzizwa ucindezelekile.
IPineoblastoma iwumdlavuza we-brain ongajwayelekile kodwa onzima odinga ukwelashwa okusheshayo, okunamandla. Nakuba ukuhlolwa kungase kuzwakale kuyadumaza, ukuthuthuka ekwelapheni kuye kwathuthukisa imiphumela eminingi yabantu abahlangabezana nale nsimo enzima.
Into ebaluleke kakhulu okumele uyikhumbule ukuthi awuwedwa kule nkambo. Amaqembu ezokwelapha akhethekile anamava ekwelapheni i-pineoblastoma, futhi azokusebenza eduze nawe ukuze akhe uhlelo lokwelapha oluhle kakhulu lesimo sakho.
Ukuqaphela izimpawu ngokushesha nokwelashwa okusheshayo kubalulekile ukuze uthole imiphumela emihle kakhulu. Uma uhlangabezana nezimpawu ze-neurological ezikukhathazayo, ungalihli ukufuna ukunakekelwa kwezokwelapha. Isinyathelo esisheshayo singenza umehluko omkhulu ekusebenzeni kokwelashwa.
Ukuphulukisa nokuphathwa isikhathi eside kuvame ukufaka ukusekelwa okuqhubekayo ochwepheshe bezempilo abahlukahlukene. Ukwelashwa komzimba, ukwelashwa komsebenzi, nokusekelwa kwengqondo konke kungase kudlale indima ebalulekile ekusikweni ukuba uvumelane futhi ugcine ikhwalithi yempilo enhle kakhulu.
IPineoblastoma iyisimo esinzima, kodwa ayihlali ibulawa. Amanani okusinda athuthukile ngokuthuthuka ekwelapheni, ikakhulukazi uma umdlavuza utholakala ngokushesha futhi uthola ukwelashwa okunamandla. Izinto eziningi zithinta i-prognosis, kufaka phakathi ubudala besikhathi sokuhlolwa, usayizi womdlavuza, nokuthi uyaphendula kanjani ekwelapheni. Iqembu lakho lezokwelapha lingakunikeza ulwazi oluqondile ngokusekelwe esimweni sakho.
Okwamanje, awekho indlela eyaziwayo yokuvimbela i-pineoblastoma njengoba singaqondi ngokugcwele ukuthi yini eyibangela. Ngokungafani nezinye izinhlobo zomdlavuza ezihlobene nezinto zokuphila, i-pineoblastoma ibonakala ikhula ngokungahleliwe ezimweni eziningi. Kubantu abanawo ama-genetic risk factors aziwayo, ukuqapha okuvamile kungasiza ekutholeni ama-tumors ngokushesha, kodwa ukuvimbela akunakwenzeka ngolwazi olukhona.
Ukuphathwa kuvame ukuthatha izinyanga eziningi futhi kufaka izigaba eziningi. Ukusebenza kwenzeka kuqala uma kungenzeka, kulandele ukwelashwa kwe-radiation okuvame ukuthatha amasonto angu-6-8. I-Chemotherapy ingaqhubeka izinyanga eziningi ngemva kwalokho. Isikhathi esiqondile siyehluka kuye ngohlelo lwakho lokwelapha, indlela oqaphela ngayo ekwelapheni, nokuthi yiziphi izingozi ezivela ngesikhathi sokwelashwa.
Abantu abaningi bangabuyela emisebenzini yabo eminingi evamile ngemva kokwelashwa, nakuba lokhu kuhluka kakhulu kumuntu nomuntu. Abanye bangase bahlangabezane nemiphumela eqhubekayo njengokukhathala, izinkinga zokulinganisela, noma ukushintsha kokwazi okudinga ukulungiswa kwemisebenzi yansuku zonke. Izinsizakalo zokuvuselela zingakusiza ukuba uvumelane futhi uthole umsebenzi omningi ngangokunokwenzeka. Iqembu lakho lezokwelapha lizosebenza nawe ukuba ubeke ithemba nemigomo eqondile.
Ezimweni eziningi, amalungu omndeni awadingi ukuhlolwa okukhethekile njengoba i-pineoblastoma ivame ukwenzeka ngokungahleliwe. Noma kunjalo, uma unayo i-genetic syndrome eyaziwayo njenge-Li-Fraumeni syndrome noma i-bilateral retinoblastoma, umndeni wakho ungase uzuze ekuqondiseni kwezinto zofuzo. Umqondisi wezinto zofuzo angahlola umlando womndeni wakho futhi ancome ukuhlolwa okufanele uma kudingeka.