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Neuroma Acoustic

Tirohanga whānui

Ko te neuroma acoustic he mate pukupuku kaore e tupu ana i runga i te ihu nui e puta mai ana i te taringa o roto ki te roro. Ko te ingoa o tenei ihu ko te ihu vestibular. Ko nga manga o te ihu ka pa tika ki te taurite me te rongohongo. Ko te pehanga mai i te neuroma acoustic ka taea te tinihanga o te rongohongo, te ringi i te taringa me nga raruraru ki te taurite. Ko tetahi atu ingoa mo te neuroma acoustic ko te schwannoma vestibular. Ko te neuroma acoustic ka tupu mai i nga pūtau Schwann e hipoki ana i te ihu vestibular. Ko te neuroma acoustic te nuinga o te wa ka tupu haere. Ko te mea iti, ka taea te tere te tipu me te nui ki te pehi ki te roro me te pa ki nga mahi nui. Ko nga maimoatanga mo te neuroma acoustic ko te tirotiro, te radiation me te tango wawe.

Ngā tohu

I te tipu o te mate pukupuku, ka nui ake pea te tūponotanga o te whakaeke i ngā tohu ka kitea ake, kāore rānei i te kino ake. Ko ngā tohu noa o te acoustic neuroma ko:

  • Te ngaro o te rongohongo, te nuinga o te wā i te iti iho i ngā marama ki ngā tau. I etahi wā, ka taea te ngaro o te rongohongo. Ko te ngaro o te rongohongo te nuinga o te wā ka puta ki tetahi taha, kāore rānei i te kino ake ki tetahi taha.
  • Te ringa i te taringa e pā ana, e mohiotia ana ko te tinnitus.
  • Te ngaro o te taurite, kāore rānei e pai te tū.
  • Te mauiui.
  • Te mumura o te mata, ā, ko te tino iti rawa, te ngoikore, te ngaro rānei o te nekehanga o te uaua. Tirohia tetahi kaimahi hauora mena ka kite koe i te ngaro o te rongohongo i tetahi taringa, te ringa i tō taringa, te raruraru rānei o te taurite. Ka āhei pea te whakamōhio wawe o te acoustic neuroma ki te pupuri i te mate pukupuku kei te nui rawa te tipu kia puta ai ngā raruraru penei i te ngaro katoa o te rongohongo. Rehita atu mō te kore utu ka whiwhi i ngā korero hou mō te maimoatanga o te mate pukupuku o te roro, te whakamōhio me te pokanga.
Āhea te kite i te tākuta

Kaore he uara (NaN)

Ngā take

Ko te take o nga neuromas acoustic ka taea pea te hono atu ki te raru o te ira i te chromosome 22. I te nuinga o te waa, ka whakaputa tenei ira i te pūmua whakakore i te mate pukupuku e awhina ana i te whakahaere i te tipu o nga pūtau Schwann e hipoki ana i nga io. Kaore nga tohunga e mohio ki te take o tenei raru ki te ira. I te nuinga o te wa kaore he take e mohiotia ana mo te neuroma acoustic. Ka riro tenei huringa ira i roto i nga tangata he mate onge e kiia nei ko te neurofibromatosis momo 2. Ko nga tangata he neurofibromatosis momo 2 te nuinga ka tipu nga mate pukupuku i runga i nga io whakarongo me te toenga i nga taha e rua o te matenga. E mohiotia ana enei mate pukupuku ko nga schwannomas vestibular rua taha.

Ngā āhuatanga tūpono

I roto i te mate pūngao rangatira autosomal, ko te huringa o te ira he ira rangatira. Kei tetahi o ngā karōmētere kore-taane, e kiia nei ko ngā autosomes. Kotahi anake te huringa o te ira e hiahiatia ana kia pā tetahi ki tēnei momo āhuatanga. He 50% te tūponotanga o te tangata he mate pūngao rangatira autosomal – i roto i tēnei tauira, te matua – kia whānau he tamaiti e pā ana, he ira huringa kotahi, ā, he 50% te tūponotanga kia whānau he tamaiti kore pā.

Ko te take morearea anake kua whakau i te neuroma acoustic ko te whai matua he mate ira onge neurofibromatosis momo 2. Heoi, ko te neurofibromatosis momo 2 anake te take mo te 5% o ngā keehi neuroma acoustic.

He tohu tino nui o te neurofibromatosis momo 2 ngā pūngāwerewere kore-mate pūngāwerewere i runga i ngā uaua taurite i ngā taha e rua o te matenga. Ka taea hoki te whanake o ngā pūngāwerewere i runga i ētahi atu uaua.

E mohiotia ana te neurofibromatosis momo 2 he mate pūngao rangatira autosomal. Ko te tikanga ka taea te tuku i te ira e pā ana ki te mate ki te tamaiti e tetahi matua anake. He 50-50 te tūponotanga o ia tamaiti o te matua e pā ana ki te whiwhi.

Ngā raruraru

He raru pea te neuroma acoustic, tae atu ki:

  • Ngaro o te rongohongo.
  • Korenga o te mata me te ngoikore.
  • Raru o te taurite.
  • Ringihanga i te taringa.
Te ārai

Kaore he uauatanga

Te tātaritanga

Ko te whakamātautau tinana tino tika, tae atu ki te whakamātautau taringa, te mahi tuatahi i te nuinga o te wā i te tautuhi me te whakaora i te neuroma acoustic.

He uaua te tautuhi i te neuroma acoustic i nga wa o mua, na te mea ka ngawari te wareware ki nga tohu, ka puea haere hoki i te wa roa. Ko nga tohu noa penei i te ngaro o te rongohere e hono ana ki etahi atu raruraru o te taringa waenganui me te taringa o roto.

I muri i te uiui mo o tohu, ka whakahaere te mema o to rōpū hauora i te whakamātautau taringa. Ka hiahia pea koe ki enei whakamātautau e whai ake nei:

  • Whakamātautau rongohere, e kiia ana ko te audiometry. Ka whakahaerehia tenei whakamātautau e te tohunga rongohere e kiia nei ko te audiologist. I te wa o te whakamātautau, ka arahina nga oro ki tetahi taringa i te wa kotahi. Ka whakaputa te audiologist i te whānuitanga o ngā oro o ngā āhuatanga rerekē. Ka tohu koe i ia wa e rongo ai koe i te oro. Ka whakahokia ano ia āhuatanga i ngā taumata ngoikore kia kitea ai te wā ka tata kore koe e rongo.

    Ka taea hoki e te audiologist te whakaputa i ngā kupu rerekē hei whakamātautau i tō rongohere.

  • Whakaahua. Ko te whakaahua pūmanawa maikuku (MRI) me te tae whakawhāiti te tikanga e whakamahia ana hei tautuhi i te neuroma acoustic. Ka taea e tenei whakamātautau whakaahua te kite i ngā pūngāwerewere iti rawa atu i te 1 ki te 2 millimeters te whānuitanga. Ki te kore e wātea te MRI, ki te kore rānei e taea e koe te whakamātautau MRI, ka taea te whakamahi i te tomography rorohiko (CT). Heoi, ka ngaro pea ngā pūngāwerewere iti i ngā tirotiro CT.

Whakamātautau rongohere, e kiia ana ko te audiometry. Ka whakahaerehia tenei whakamātautau e te tohunga rongohere e kiia nei ko te audiologist. I te wa o te whakamātautau, ka arahina nga oro ki tetahi taringa i te wa kotahi. Ka whakaputa te audiologist i te whānuitanga o ngā oro o ngā āhuatanga rerekē. Ka tohu koe i ia wa e rongo ai koe i te oro. Ka whakahokia ano ia āhuatanga i ngā taumata ngoikore kia kitea ai te wā ka tata kore koe e rongo.

Ka taea hoki e te audiologist te whakaputa i ngā kupu rerekē hei whakamātautau i tō rongohere.

Te rongoā

Ka rereke pea te maimoatanga o tō neuroma acoustic, kei te whakawhirinaki ki:

  • Te rahi me te tere tipu o te neuroma acoustic.
  • Tō hauora whānui.
  • ō tohu. E toru ngā huarahi maimoatanga mō te neuroma acoustic: te tirotiro, te pokanga, te rongoā radiation rānei. Ka whakatau pea koe me tō rōpū hauora ki te tirotiro i tētahi neuroma acoustic, ki te iti rawa, kāore rānei e tipu ana, ki te puāwai haere rānei. He whiringa pea tēnei mena he torutoru noa ngā tohu o te neuroma acoustic, kāore rānei he tohu. Ka tūtohu pea te tirotiro mena he kaumātua koe, kāore rānei koe e pai ki te maimoatanga kaha ake. I te wā e tirotirohia ana, ka hiahia koe ki ngā whakamātautau whakaahua me ngā whakamātautau whakarongo, i ia 6 ki te 12 marama. Ka taea e ēnei whakamātautau te whakatau mena kei te tipu te mate pukupuku me te tere o te tipu. Mena ka whakaatu ngā karapa kei te tipu te mate pukupuku, kei te pāngia rānei e te mate pukupuku ngā tohu kino atu, ngā raruraru rānei, ka hiahia pea koe ki te pokanga, ki te radiation rānei. Ka hiahia pea koe ki te pokanga hei tango i tētahi neuroma acoustic, ina koa ki te:
  • Kei te tipu tonu.
  • Nui rawa.
  • Kei te pā te tohu. Ka whakamahi pea tō taote i tētahi o ngā tikanga maha mō te tango i tētahi neuroma acoustic. Kei te whakawhirinaki te tikanga pokanga ki te rahi o te mate pukupuku, ki tō mana whakarongo, ki ētahi atu mea. Ko te whāinga o te pokanga ko te tango i te mate pukupuku me te tiaki i te uaua kanohi kia kaua e pararutiki ngā uaua i tō mata. Kāore pea e taea te tango i te mate pukupuku katoa. Hei tauira, ki te tata rawa te mate pukupuku ki ngā wāhanga nui o te roro, ki te uaua kanohi rānei, ka tangohia pea tētahi wāhanga noa o te mate pukupuku. Ka mahia te pokanga mō te neuroma acoustic i raro i te mate moe whānui. Kei roto i te pokanga te tango i te mate pukupuku mā te taringa o roto, mā te matapihi rānei i tō anga. I etahi wā, ka kaha ake pea ngā tohu mena ka whakapouritia, ka pakaru rānei ngā taringa, te toenga, ngā uaua kanohi rānei i te wā o te mahi. Ka ngaro pea te whakarongo i te taha i mahia ai te pokanga. Kei te pāngia te toenga mo te wā poto. Ka uru pea ngā raruraru ki:
  • Te rerenga o te wai e karapotia ana tō roro me tō tuaiwi, e mohiotia ana ko te wai cerebrospinal. Ka puta pea te rerenga mā te whara.
  • Te ngaro o te whakarongo.
  • Te ngoikore o te kanohi, te mumura rānei.
  • Te ngāringari i te taringa.
  • Ngā raruraru toenga.
  • Te mamae o te upoko tonu.
  • Ko te mate o te wai cerebrospinal, e mohiotia ana ko te meningitis.
  • Ko te mate o te roro, te toto roro rānei. Ka whakamahi te hangarau radiosurgery stereotactic i ngā hihi gamma iti maha hei tuku i te horopeta radiation tika ki te whāinga. E maha ngā momo rongoā radiation e whakamahia ana hei whakaora i tētahi neuroma acoustic:
  • Radiosurgery stereotactic. He momo rongoā radiation e mohiotia ana ko te radiosurgery stereotactic ka taea te whakaora i tētahi neuroma acoustic. Ka whakamahia pea mena he iti te mate pukupuku—iti iho i te 2.5 henimita te whānuitanga. Ka whakamahia pea te rongoā radiation mena he kaumātua koe, kāore rānei koe e manawanui ki te pokanga mō ngā take hauora. Ka whakamahi te radiosurgery stereotactic, penei i te Gamma Knife me te CyberKnife, i ngā hihi gamma iti maha hei tuku i te horopeta radiation tika ki te mate pukupuku. Ka tukuna e tēnei tikanga te maimoatanga kaore e pakaru te kiko e karapotia ana, kāore rānei e hanga he tapahi. Ko te whāinga o te radiosurgery stereotactic ko te mutu i te tipu o te mate pukupuku, ko te tiaki i te mahi o te uaua kanohi, me te tiaki pea i te whakarongo. Ka roa pea ngā wiki, ngā marama, ngā tau rānei i mua i tō kite i ngā pānga o te radiosurgery. Ka tirotirohia e tō rōpū hauora tō ahunga whakamua mā ngā rangahau whakaahua me ngā whakamātautau whakarongo. Ko ngā tūponotanga o te radiosurgery e whai ake nei:
    • Te ngaro o te whakarongo.
    • Te ngāringari i te taringa.
    • Te ngoikore o te kanohi, te mumura rānei.
    • Ngā raruraru toenga.
    • Te tipu tonu o te mate pukupuku.
  • Te ngaro o te whakarongo.
  • Te ngāringari i te taringa.
  • Te ngoikore o te kanohi, te mumura rānei.
  • Ngā raruraru toenga.
  • Te tipu tonu o te mate pukupuku.
  • Te radiotherapy stereotactic wāhanga. Ka tuku te radiotherapy stereotactic wāhanga (SRT) i te horopeta iti o te radiation ki te mate pukupuku i roto i ngā hui maha. Ka mahia te SRT hei whakaheke i te tipu o te mate pukupuku kaore e pakaru te kiko roro e karapotia ana.
  • Te rongoā pūtake proton. Ka whakamahi tēnei momo rongoā radiation i ngā hihi kaha o ngā pūtau utu pai e kiia nei ko ngā proton. Ka tukuna ngā hihi proton ki te wāhi e pāngia ana i roto i ngā horopeta e whai take ana hei whakaora i ngā mate pukupuku. Ka whakaiti tēnei momo maimoatanga i te whakamahinga radiation ki te wāhi e karapotia ana. Radiosurgery stereotactic. He momo rongoā radiation e mohiotia ana ko te radiosurgery stereotactic ka taea te whakaora i tētahi neuroma acoustic. Ka whakamahia pea mena he iti te mate pukupuku—iti iho i te 2.5 henimita te whānuitanga. Ka whakamahia pea te rongoā radiation mena he kaumātua koe, kāore rānei koe e manawanui ki te pokanga mō ngā take hauora. Ka whakamahi te radiosurgery stereotactic, penei i te Gamma Knife me te CyberKnife, i ngā hihi gamma iti maha hei tuku i te horopeta radiation tika ki te mate pukupuku. Ka tukuna e tēnei tikanga te maimoatanga kaore e pakaru te kiko e karapotia ana, kāore rānei e hanga he tapahi. Ko te whāinga o te radiosurgery stereotactic ko te mutu i te tipu o te mate pukupuku, ko te tiaki i te mahi o te uaua kanohi, me te tiaki pea i te whakarongo. Ka roa pea ngā wiki, ngā marama, ngā tau rānei i mua i tō kite i ngā pānga o te radiosurgery. Ka tirotirohia e tō rōpū hauora tō ahunga whakamua mā ngā rangahau whakaahua me ngā whakamātautau whakarongo. Ko ngā tūponotanga o te radiosurgery e whai ake nei:
  • Te ngaro o te whakarongo.
  • Te ngāringari i te taringa.
  • Te ngoikore o te kanohi, te mumura rānei.
  • Ngā raruraru toenga.
  • Te tipu tonu o te mate pukupuku. I tua atu i te maimoatanga hei tango, hei mutu rānei i te tipu o te mate pukupuku, ka taea te awhina i ngā maimoatanga tautoko. Ka whakautu ngā maimoatanga tautoko ki ngā tohu, ki ngā raruraru rānei o te neuroma acoustic me tōna maimoatanga, penei i te māuiui, i ngā raruraru toenga rānei. Ka taea te whakamahi i ngā whakatoto cochlear, i ētahi atu maimoatanga rānei mō te ngaro o te whakarongo. Rēhita atu mō te kore utu, ka whiwhi i ngā mea hou mo te maimoatanga o te mate pukupuku roro, te whakatau, me te pokanga. Te hononga wetewete i te īmēra. He tino awangawanga te whakahaere i te tūponotanga o te ngaro o te whakarongo me te pararutiki kanohi. Ka uaua pea te whakatau i tehea maimoatanga te pai mōu. Ka taea e ēnei whakaaro te awhina:
  • Whakaako koe mo ngā neuromas acoustic. Ko te nui o tō mōhiotanga, ko te pai ake o tō whakarite ki te mahi i ngā whiringa pai mo te maimoatanga. I tua atu i te kōrero ki tō rōpū hauora me tō kaiwhakarongo, ka hiahia pea koe ki te kōrero ki tētahi kaiāwhina, ki tētahi kaimahi whānau rānei. Rānei, ka kite pea koe he whai hua te kōrero ki ētahi atu tangata kua pāngia e te neuroma acoustic. Ka awhina pea te ako atu mo ō rātou wheako i te wā o te maimoatanga me muri iho.
  • Whakarite i tētahi pūnaha tautoko kaha. Ka taea e te whānau me ngā hoa te awhina i a koe i te wā e tūtaki ana koe ki tēnei wā uaua. Engari, i etahi wā, ka kite pea koe he whakamārama, he mārama hoki ngā whakaaro o ētahi atu tangata kua pāngia e te neuroma acoustic. Ka taea pea e tō rōpū hauora, e tētahi kaimahi whānau rānei te whakapiri atu ki tētahi rōpū tautoko. Rānei, ka kite pea koe i tētahi rōpū tautoko kanohi, i tētahi rōpū tautoko ipurangi rānei mā te Acoustic Neuroma Association. Whakarite i tētahi pūnaha tautoko kaha. Ka taea e te whānau me ngā hoa te awhina i a koe i te wā e tūtaki ana koe ki tēnei wā uaua. Engari, i etahi wā, ka kite pea koe he whakamārama, he mārama hoki ngā whakaaro o ētahi atu tangata kua pāngia e te neuroma acoustic. Ka taea pea e tō rōpū hauora, e tētahi kaimahi whānau rānei te whakapiri atu ki tētahi rōpū tautoko. Rānei, ka kite pea koe i tētahi rōpū tautoko kanohi, i tētahi rōpū tautoko ipurangi rānei mā te Acoustic Neuroma Association.
Te tiaki whaiaro

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