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Achalasia

Nānaina

ʻO ka achalasia he pilikia ia o ka ʻai ʻana e pili ana i ka paipu e hoʻohui ana i ka waha a me ka ʻōpū, i kapa ʻia ʻo ka esophagus. Ma muli o ka hōʻino ʻia ʻana o nā aʻalolo, ua paʻakikī i nā ʻiʻo o ka esophagus ke kāʻili i ka meaʻai a me ka wai i loko o ka ʻōpū. A laila, e hōʻiliʻili ka meaʻai i loko o ka esophagus, a i kekahi manawa e hoʻomaʻamaʻa a holo hou i luna i loko o ka waha. Hiki i kēia meaʻai i hoʻomaʻamaʻa ʻia ke ʻono ʻawaʻawa.

He kūlana maʻamau ʻole ka achalasia. Hoʻokāʻawale kekahi poʻe iā ia me ka maʻi reflux gastroesophageal (GERD). Eia naʻe, i ka achalasia, mai ka esophagus mai ka meaʻai. I ka GERD, mai ka ʻōpū mai ka mea.

ʻAʻohe lāʻau lapaʻau no ka achalasia. Ke hōʻino ʻia ka esophagus, ʻaʻole hiki i nā ʻiʻo ke hana pono hou. Akā hiki ke mālama pinepine ʻia nā hōʻailona me ka endoscopy, ka lāʻau lapaʻau liʻiliʻi a i ʻole ka ʻoki kino.

Nā hōʻailona

ʻO ka maʻi ʻAchalasia, ma ka laulā, e hōʻike mālie mai ana a e ʻoi aku ka ʻino i ka hala ʻana o ka manawa. ʻO nā hōʻailona e komo pū ai:

  • Paʻakikī ke ʻai, i kapa ʻia ʻo dysphagia, kahi e manaʻo ai paha ua paʻa ka meaʻai a i ʻole ka mea inu i loko o ka ʻāʻī.
  • Ke kahe hou mai o ka meaʻai a i ʻole ka wai ʻōpū i loko o ka ʻāʻī.
  • ʻAʻai puʻuwai.
  • Ke ʻōhū ʻana.
  • ʻEha umauma e hele mai ana a hele aku.
  • Ke kikī ʻana i ka pō.
  • Pneumonia mai ka komo ʻana o ka meaʻai i loko o nā māmā.
  • Ke emi ʻana o ke kaumaha.
  • Ka luaʻi ʻana.
Nā kumu

ʻAʻole maopopo pono ke kumu kūpono o ka achalasia. Manaʻo nā mea noiʻi he hiki ke hoʻokumu ʻia e ka nalowale ʻana o nā pūnaewele nerve i loko o ka esophagus. Aia nā manaʻo e pili ana i ka mea e hoʻokumu ai i kēia, akā ʻo ka maʻi viral a i ʻole nā pane autoimmune he mau mea hiki ke loaʻa. He mea maʻamau loa, hiki ke hoʻokumu ʻia ka achalasia e ka maʻi genetic i hoʻoilina ʻia a i ʻole ka maʻi.

Nā mea pilikia

Nā kumu pilikia no ka achalasia:

  • Makahiki. ʻOiai hiki i ka achalasia ke hoʻopili i nā kānaka o nā makahiki a pau, ʻoi aku ka nui ma waena o nā makahiki 25 a 60.
  • Nā kūlana olakino kūikawā. ʻOi aku ka nui o ka pilikia o ka achalasia i nā kānaka me nā maʻi ʻaliki, ka nele o ka adrenal a i ʻole ka Allgrove syndrome, kahi maʻi maʻi recessive autosomal koʻikoʻi.
ʻImi ʻike

Hiki ke nānā 'ole 'ia a i 'ole paha ke kuhi hewa 'ia ka achalasia no ka mea, ua like kona mau hō'ailona me nā hō'ailona o nā ma'i'ai'ai'ē a'e. No ka ho'ā'o 'ana i ka achalasia, he mea kūpono ka'ōlelo a kekahi limahana ola kino: Manometry esophageal. Ke ana nei kēia ho'ā'o i ka ho'onui 'ana o nā'i'o i loko o ka esophagus i ka wā e'ai ai. Ke ana nei ia i ka maika'i o ka wehe 'ana o ka sphincter esophageal ha'aha'a i ka wā e'ai ai. 'O kēia ho'ā'o ka mea kōkua loa i ka wā e ho'oholo ai i ke'ano o ka'ai'ai'ana āu paha. Nā ki'i X-ray o ka'ōnaehana'ai'ai luna. Lawe 'ia nā ki'i X-ray ma hope o ka inu 'ana i ka wai'ōpala i kapa 'ia'o barium. Ho'opili ka barium i ka papa o loko o ka'ōnaehana'ai'ai a ho'opiha i nā'ōnaehana'ai'ai. Ke'ae nei kēia ho'opili i kekahi limahana ola kino e'ike i kahi silhouette o ka esophagus, ka'ōpū a me ka'ōpū luna. Ma waho a'e o ka inu 'ana i ka wai, hiki i ka'ai'ana i ka pīlali barium ke kōkua i ka hō'ike 'ana i kahi pale i loko o ka esophagus. Endoscopy luna. Ho'ohana ka endoscopy luna i kahi kāmela li'ili'i ma ka hopena o kahi paipu'olu'olu e nānā pono ai i ka'ōnaehana'ai'ai luna. Hiki ke ho'ohana 'ia ka endoscopy e huli i kahi pale hapa o ka esophagus. Hiki nō ho'i ke ho'ohana 'ia ka endoscopy e hō'ili'ili i kahi la'ana o ka'i'o, i kapa 'ia'o biopsy, e ho'ā'o 'ia no nā pilikia o ka reflux e like me ka Barrett esophagus. Hana'ōnaehana ki'i'ike'ike luminal (FLIP) technology. He'enehana hou ka FLIP e hiki ke kōkua i ka hō'oia 'ana i kahi achalasia diagnosis inā'a'ole lawa nā ho'ā'o'ē a'e. Mālama ma ka Mayo Clinic Hiki i kā mākou hui mālama o nā'ike loea Mayo Clinic ke kōkua iā'oe me kāu mau pilikia olakino e pili ana i ka achalasia E ho'omaka ma'ane'i

Ka mālama ʻana

ʻO ka mālama ʻana i ka achalasia ke kau nui ma ka hoʻomaha a i ʻole ka hoʻolōʻihi ʻana i ka sphincter esophageal haʻahaʻa, i hiki ai i ka meaʻai a me ka wai ke neʻe maʻalahi ma o ka ʻōnaehana digestive.

Kaukaʻi ka mālama kūikawā ma kāu mau makahiki, kūlana olakino a me ka nui o ka achalasia.

ʻO nā koho ʻaʻole ʻoki kino e komo pū me:

  • Pneumatic dilation. I loko o kēia kaʻina hana ma waho, hoʻokomo ʻia kahi pulupulu i loko o ka waenakonu o ka sphincter esophageal a hoʻonui ʻia e hoʻonui i ka puka. Pono paha e hana hou i ka pneumatic dilation inā ʻaʻole e noho wehe ka sphincter esophageal. Aneane hoʻokahi hapakolu o nā kānaka i mālama ʻia me ka dilation pulupulu e pono ai ka mālama hou i loko o ʻelima mau makahiki. Pono kēia kaʻina hana i ka sedation.
  • OnabotulinumtoxinA (Botox). Hiki ke hoʻokomo pololei ʻia kēia mea hoʻomaha iʻiʻo i loko o ka sphincter esophageal me kahi nila i ka wā o ka endoscopy. Pono paha e hana hou i nā inikini, a hiki i nā inikini hou ke hana i ka paʻakikī o ka hana ʻoki kino ma hope inā pono.

Hoʻomaopopo ʻia ka Botox ma ke ʻano maʻamau wale nō no nā kānaka ʻaʻole hiki ke loaʻa i ka pneumatic dilation a i ʻole ka ʻoki kino ma muli o ka makahiki a i ʻole ke olakino holoʻokoʻa. ʻAʻole mau ka lōʻihi o nā inikini Botox ma mua o ʻeono mau mahina. Hiki i ka hoʻomaikaʻi ikaika mai ka inikini o Botox ke kōkua i ka hōʻoia ʻana i ka hōʻailona o ka achalasia.

  • Lāʻau lapaʻau. Hiki i kāu kauka ke manaʻo i nā mea hoʻomaha iʻiʻo e like me ka nitroglycerin (Nitrostat) a i ʻole ka nifedipine (Procardia) ma mua o ka ʻai ʻana. Loaʻa i kēia mau lāʻau lapaʻau ka hopena mālama palena a me nā hopena ʻaoʻao koʻikoʻi. Manaʻo ʻia nā lāʻau lapaʻau ma ke ʻano maʻamau wale nō inā ʻaʻole ʻoe he moho no ka pneumatic dilation a i ʻole ka ʻoki kino a ʻaʻole i kōkua ka Botox. Loaʻa ʻole kēia ʻano o ka mālama ʻana.

OnabotulinumtoxinA (Botox). Hiki ke hoʻokomo pololei ʻia kēia mea hoʻomaha iʻiʻo i loko o ka sphincter esophageal me kahi nila i ka wā o ka endoscopy. Pono paha e hana hou i nā inikini, a hiki i nā inikini hou ke hana i ka paʻakikī o ka hana ʻoki kino ma hope inā pono.

Hoʻomaopopo ʻia ka Botox ma ke ʻano maʻamau wale nō no nā kānaka ʻaʻole hiki ke loaʻa i ka pneumatic dilation a i ʻole ka ʻoki kino ma muli o ka makahiki a i ʻole ke olakino holoʻokoʻa. ʻAʻole mau ka lōʻihi o nā inikini Botox ma mua o ʻeono mau mahina. Hiki i ka hoʻomaikaʻi ikaika mai ka inikini o Botox ke kōkua i ka hōʻoia ʻana i ka hōʻailona o ka achalasia.

ʻO nā koho ʻoki kino no ka mālama ʻana i ka achalasia e komo pū me:

  • Heller myotomy. Hoʻopili ka Heller myotomy i ka ʻoki ʻana i ka iʻiʻo ma ka hopena haʻahaʻa o ka sphincter esophageal. Hāʻawi kēia i ka meaʻai e hele maʻalahi i loko o ka ʻōpū. Hiki ke hana ʻia ke kaʻina hana me kahi ʻenehana liʻiliʻi i kapa ʻia ʻo ka laparoscopic Heller myotomy. Hiki i kekahi poʻe i loaʻa ka Heller myotomy ke loaʻa ma hope aku i ka maʻi gastroesophageal reflux (GERD).

No ka pale ʻana i nā pilikia ma hope me ka GERD, hiki i ke kauka ʻoki ke hana i kahi kaʻina hana i ʻike ʻia ʻo fundoplication i ka manawa like me ka Heller myotomy. I loko o ka fundoplication, e kāʻei ka kauka ʻoki i ka piko o ka ʻōpū a puni ka esophagus haʻahaʻa e hana i kahi valve anti-reflux, e pale ana i ka waikawa mai ka hoʻi ʻana i loko o ka esophagus. Hana ʻia ka fundoplication ma ke ʻano maʻamau me kahi kaʻina hana liʻiliʻi, i kapa ʻia hoʻi he kaʻina hana laparoscopic.

  • Peroral endoscopic myotomy (POEM). I loko o ke kaʻina hana POEM, hoʻohana ka kauka ʻoki i kahi endoscope i hoʻokomo ʻia ma o ka waha a i lalo i ka ʻāʻī e hana i kahi ʻoki i loko o ka papa o loko o ka esophagus. A laila, e like me ka Heller myotomy, e ʻoki ka kauka ʻoki i ka iʻiʻo ma ka hopena haʻahaʻa o ka sphincter esophageal.

Hiki ke hui pū ʻia ka POEM a i ʻole ma hope o ka fundoplication e kōkua i ka pale ʻana i ka GERD. Mālama ʻia kekahi mau mea maʻi i loaʻa ka POEM a loaʻa ka GERD ma hope o ke kaʻina hana me ka lāʻau lapaʻau i lawe ʻia i kēlā me kēia lā ma ka waha.

Heller myotomy. Hoʻopili ka Heller myotomy i ka ʻoki ʻana i ka iʻiʻo ma ka hopena haʻahaʻa o ka sphincter esophageal. Hāʻawi kēia i ka meaʻai e hele maʻalahi i loko o ka ʻōpū. Hiki ke hana ʻia ke kaʻina hana me kahi ʻenehana liʻiliʻi i kapa ʻia ʻo ka laparoscopic Heller myotomy. Hiki i kekahi poʻe i loaʻa ka Heller myotomy ke loaʻa ma hope aku i ka maʻi gastroesophageal reflux (GERD).

No ka pale ʻana i nā pilikia ma hope me ka GERD, hiki i ke kauka ʻoki ke hana i kahi kaʻina hana i ʻike ʻia ʻo fundoplication i ka manawa like me ka Heller myotomy. I loko o ka fundoplication, e kāʻei ka kauka ʻoki i ka piko o ka ʻōpū a puni ka esophagus haʻahaʻa e hana i kahi valve anti-reflux, e pale ana i ka waikawa mai ka hoʻi ʻana i loko o ka esophagus. Hana ʻia ka fundoplication ma ke ʻano maʻamau me kahi kaʻina hana liʻiliʻi, i kapa ʻia hoʻi he kaʻina hana laparoscopic.

Peroral endoscopic myotomy (POEM). I loko o ke kaʻina hana POEM, hoʻohana ka kauka ʻoki i kahi endoscope i hoʻokomo ʻia ma o ka waha a i lalo i ka ʻāʻī e hana i kahi ʻoki i loko o ka papa o loko o ka esophagus. A laila, e like me ka Heller myotomy, e ʻoki ka kauka ʻoki i ka iʻiʻo ma ka hopena haʻahaʻa o ka sphincter esophageal.

Hiki ke hui pū ʻia ka POEM a i ʻole ma hope o ka fundoplication e kōkua i ka pale ʻana i ka GERD. Mālama ʻia kekahi mau mea maʻi i loaʻa ka POEM a loaʻa ka GERD ma hope o ke kaʻina hana me ka lāʻau lapaʻau i lawe ʻia i kēlā me kēia lā ma ka waha.

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Hōʻole: He kahua ʻike olakino ʻo ʻAukake a ʻaʻole hōʻike kāna mau pane i ka ʻōlelo aʻoaʻo lapaʻau. E kūkākūkā mau me kahi ʻoihana lapaʻau laikini kokoke iā ʻoe ma mua o ka hana ʻana i nā hoʻololi.

Hana ʻia i India, no ka honua