

Health Library
October 10, 2025
Question on this topic? Get an instant answer from August.
ʻO ka antiphospholipid syndrome (APS) kahi kūlana autoimmune kahi e hoʻouka ai kou ʻōnaehana pale kino i nā protein i loko o kou koko, e hoʻolilo ana iā ia i mea maʻalahi ke hana i nā clots pōʻino. E noʻonoʻo iā ia e like me ke ʻano clotting kūlohelohe o kou kino e hele ana i ka overdrive i ka wā ʻaʻole pono. Hoʻopili kēia kūlana i nā kāne a me nā wahine, ʻoiai ʻoi aku ka nui o nā wahine i ka makahiki hānau keiki, a ʻoiai ke kani nui nei, he mea maʻalahi loa ia me ka mālama kūpono olakino.
Hana ʻia ka antiphospholipid syndrome i ka wā e hana ai kou ʻōnaehana pale kino i nā antibodies e hoʻopili i nā phospholipids a me nā protein e hoʻopili i nā phospholipids i loko o kou koko. ʻO nā Phospholipids nā momona nui e kōkua i ka mālama ʻana i nā membrane cell a pāʻani i kahi kuleana nui i ka clotting koko.
Ke hoʻouka nei kēia mau antibodies, hoʻopilikia lākou i ke kaʻina clotting maʻamau o kou koko. Ma mua o ka clotting wale nō i ka wā e hōʻeha ai ʻoe, lilo kou koko i mea maʻalahi ke hana i nā clots i loko o kou mau kīʻaha koko i ka wā ʻaʻole pono ʻoe iā lākou. Hiki i kēia ke alakaʻi i nā pilikia nui e like me nā hahau, nā hoʻouka naʻau, a i ʻole nā pilikia hāpai.
Hiki i ka APS ke hana ma kona iho, i kapa ʻia ʻo ka antiphospholipid syndrome mua, a i ʻole ma ka ʻaoʻao o nā kūlana autoimmune ʻē aʻe e like me ka lupus, kahi i kapa ʻia ʻo ka antiphospholipid syndrome lua. ʻO ka ʻoiaʻiʻo maikaʻi, me ka mālama kūpono, hiki i ka hapa nui o nā kānaka me ka APS ke ola i nā ola maʻamau a olakino.
Hiki i nā hōʻailona o ka APS ke ʻokoʻa nui no ka mea hilinaʻi lākou i kahi e hana ai nā clots koko i loko o kou kino. ʻAʻohe hōʻailona o kekahi poʻe a hiki i ka hoʻomohala ʻana o kahi clot, ʻoiai ke ʻike paha kekahi i nā hōʻailona mālie e hoʻopōʻino mālie.
Eia nā hōʻailona maʻamau āu e ʻike ai:
No nā wāhine, hiki i nā hōʻailona pili i ka hapai ke komo pū me nā miscarriage hou, ʻoi aku hoʻi i ka lua a i ʻole ke kolu o ka trimester, a i ʻole nā pilikia e like me ka preeclampsia. Loaʻa kēia mau hōʻailona no ka mea hiki i nā clots koko ke hoʻopilikia i ke kahe koko i ka placenta.
Hiki i kekahi poʻe me ka APS ke ʻike pū i nā hōʻailona maʻamau ʻole e like me ka loli koke o ka ʻike, ka ʻōlelo ʻōlelo, a i ʻole ka nāwaliwali ma kekahi ʻaoʻao o ke kino. ʻOiai hiki i kēia mau mea ke hopohopo, e hoʻomanaʻo ʻaʻole e ʻike nā kānaka a pau me ka APS i kēia mau hōʻailona a pau, a hiki ke hoʻokele maikaʻi ʻia ka nui me ka mālama.
Hoʻokaʻawale ʻia ka APS i ʻelua ʻano nui ma muli o ka loaʻa ʻana a i ʻole ʻole me nā kūlana ʻē aʻe. Ke hoʻomaopopo ʻoe i ke ʻano āu e loaʻa ai, e kōkua i kāu kauka e hana i ka papahana mālama maikaʻi loa no ʻoe.
Loaʻa ka antiphospholipid syndrome mua ke loaʻa iā ʻoe ka APS me ka ʻole o kekahi maʻi autoimmune ʻē aʻe. ʻO kēia ka ʻano pololei loa, kahi ʻo nā pilikia clotting koko ka mea nui e hopohopo ai. ʻOi aku ka pane maikaʻi o ka hapa nui o nā kānaka me ka APS mua i nā lāʻau lapaʻau e hoʻonāwaliwali i ke koko.
Hoʻomohala ʻia ka antiphospholipid syndrome lua ma ka ʻaoʻao o nā kūlana autoimmune ʻē aʻe, ʻoi aku ka maʻamau o ka systemic lupus erythematosus (SLE a i ʻole lupus). Ma kahi o 30-40% o nā kānaka me ka lupus loaʻa pū nā antiphospholipid antibodies. ʻO nā kūlana ʻē aʻe e hiki ke loaʻa me ka APS, ʻo ia ka rheumatoid arthritis, scleroderma, a me ka Sjögren's syndrome.
Aia nō hoʻi kahi ʻano maʻamau ʻole akā koʻikoʻi i kapa ʻia ʻo ka catastrophic antiphospholipid syndrome (CAPS), kahi e pilikia ai ma lalo o ka 1% o nā kānaka me ka APS. Ma CAPS, hana koke nā ʻōpala koko he nui ma ke kino holoʻokoʻa, e pono ai ka mālama pilikia koke. ʻOiai ke kani nui nei kēia, he mea maʻamau ʻole loa ia a maʻamau hoʻi ke mālama ʻia inā loaʻa koke.
ʻAʻole maopopo loa ke kumu o ka APS, akā manaʻo nā mea noiʻi ua ulu mai ia mai ka hui pū ʻana o ka predisposition genetic a me nā mea hoʻonāukiuki o ke kaiapuni. Hoʻopilikia ʻia kāu ʻōnaehana pale kino a hoʻomaka e hoʻouka i nā protein o kou kino ponoʻī.
Hiki i kekahi mau mea ke kōkua i ka hoʻomohala ʻana i ka APS:
He mea nui e hoʻomaopopo ʻaʻole ʻo ka loaʻa ʻana o nā mea pilikia ʻaʻole ia e manaʻo e hoʻomohala ʻoe i ka APS. ʻAʻole hoʻomohala nā kānaka he nui me kēia mau mea pilikia i ke kūlana, ʻoiai kekahi poʻe ʻē aʻe me nā mea hoʻonāukiuki ʻike ʻole ʻia e hana pēlā. ʻO ka hoʻomohala ʻana o ka APS e pono ai ka makani kūpono o ka susceptibility genetic a me nā kumu kaiapuni.
I kekahi manawa, hiki i nā kānaka ke loaʻa nā antiphospholipid antibodies i loko o ko lākou koko me ka ʻole o ka hoʻomohala ʻana i nā hōʻailona a i ʻole nā ʻōpala koko. He ʻokoʻa kēia mai ka loaʻa ʻana o ka APS ponoʻī, a ʻaʻole pono ka nui o kēia poʻe i ka mālama.
Pono ʻoe e ʻike koke i ke kauka inā loaʻa iā ʻoe nā hōʻailona e hōʻike ana i kahi ʻōpala koko, ʻoiai hiki i ka mālama koke ke pale aku i nā pilikia koʻikoʻi. Mai kali e ʻike inā hoʻomaikaʻi nā hōʻailona ma o lākou iho.
E ʻimi i ka mālama lapaʻau koke inā loaʻa iā ʻoe:
Pono nō hoʻi ʻoe e hoʻonohonoho i kahi kūkā me kāu kauka inā loaʻa iā ʻoe nā pohō hāpai keiki hou, ʻoi aku inā ua loaʻa iā ʻoe ʻelua a ʻoi aku paha nā miscarriage. ʻOiai he nui nā kumu o ka pohō hāpai keiki, hiki i nā miscarriage hou ke hōʻike i ka APS a i ʻole kekahi kūlana hiki ke mālama ʻia.
Inā loaʻa iā ʻoe ka mōʻaukala ʻohana o nā clots koko a i ʻole nā maʻi autoimmune, e haʻi aku i kāu mea lawelawe olakino. Hiki iā lākou ke ʻōlelo aku i ka hoʻokolohua no ka APS, ʻoi aku inā ʻoe e hoʻolālā ana i ka hāpai keiki a i ʻole e hoʻomaka ana i ka birth control hormonal, ʻelua o lākou e hiki ke hoʻonui i ka pilikia clotting.
Hiki i kekahi mau mea ke hoʻonui i kou hiki ke loaʻa i ka APS, ʻoiai ʻaʻole hōʻoia ka loaʻa ʻana o kēia mau kumu pilikia e loaʻa iā ʻoe ke kūlana. Ke hoʻomaopopo ʻoe i kou pilikia, e kōkua iā ʻoe a me kāu kauka e makaʻala no nā hōʻailona mua.
ʻO nā kumu pilikia nui loa e komo pū ana:
Hiki i kekahi mau kūlana manawa pōkole ke hoʻonui i kou pilikia o ka loaʻa ʻana o nā clots koko inā loaʻa iā ʻoe ka APS. ʻO kēia mau mea e komo pū ana ka hāpai keiki, ka ʻoki kino, ka moe lōʻihi, a i ʻole ka lawe ʻana i ka birth control a i ʻole ka hormone replacement therapy e komo pū ana i ka estrogen.
He kuleana ke makahiki, ʻoiai e hoʻonui ana ka pilikia o ka loaʻa ʻana o ka APS me ka makahiki, ʻoiai hiki ke loaʻa i kēlā me kēia makahiki. Hiki i nā keiki ke loaʻa i ka APS, akā ʻoi aku ka liʻiliʻi ma mua o nā mākua.
ʻOiai he pilikia nui paha nā pilikia o ka APS, hiki i ka hapa nui o nā kānaka me ka mālama kūpono a me ka nānā ʻana ke pale aku iā lākou āpau. ʻO ka mea nui, ʻo ia ka hoʻomaopopo ʻana i nā mea e nānā ai a hana pono pū me kāu hui olakino.
ʻO nā pilikia maʻamau loa e komo pū ana:
Hiki i kekahi poʻe me ka APS ke loaʻa nā pilikia ʻaʻole nui akā ʻoi aku ka nui. Hiki i kēia ke komo pū me nā ʻāpana koko i nā wahi maʻamau ʻole e like me ke ake, nā maka, a i ʻole ka lolo, kahi e hiki ai ke loaʻa nā hōʻailona e like me nā pilikia ʻike, ka huikau, a i ʻole nā seizures.
ʻO ke ʻano catastrophic maʻamau ʻole o ka APS hiki ke hoʻopilikia i ka hana ʻole o nā ʻōnaehana he nui, akā ʻo kēia ka mea e loaʻa ai ma lalo o 1% o nā kānaka me ka APS. Me nā ʻano mālama hou, hiki ke pale ʻia a i ʻole ke mālama ʻia nā pilikia nui ke hopu ʻia i ka wā mua.
ʻO ka hōʻoia ʻana i ka APS e pono ai nā hōʻike maʻi (e like me nā ʻāpana koko a i ʻole nā pilikia hāpai) a me ka hōʻoia ʻana o ka hale hana o nā antiphospholipid antibodies. E pono pinepine kāu kauka e hōʻoia i ka hōʻoia me ʻelua mau hōʻike koko maikaʻi i lawe ʻia ma kahi o 12 mau wiki ma waena.
ʻO ke kaʻina hana hōʻoia e komo pinepine ana i kekahi mau ʻanuʻu. ʻO ka mea mua, e lawe kāu kauka i ka moʻolelo olakino kikoʻī, e nīnau ana e pili ana i nā ʻāpana koko, nā pilikia hāpai, a i ʻole nā hōʻailona āu i ʻike ai. E hana pū lākou i kahi nānā kino e ʻimi ana i nā hōʻailona o nā pilikia clotting.
ʻO nā hoʻokolohua koko ke kumu o ka ʻike ʻana i ka APS. ʻO nā hoʻokolohua nui e ʻimi ana i ʻekolu ʻano o nā antibody antiphospholipid: nā antibody anticardiolipin, nā antibody anti-beta-2 glycoprotein I, a me ka lupus anticoagulant. ʻOiai kona inoa, hoʻonui maoli ka lupus anticoagulant i ka pilikia o ka hoʻopaʻa ʻana ma mua o ka pale ʻana.
Hiki i kāu kauka ke kauoha aku i nā hoʻokolohua hou aʻe e kāpae i nā kūlana ʻē aʻe a i ʻole e ʻimi i nā pilikia. Hiki i kēia ke komo pū me nā haʻawina kiʻi e like me nā ultrasounds e nānā i nā clots koko, a i ʻole nā hoʻokolohua e loiloi i kāu hana o ka puʻupaʻa, naʻau, a i ʻole ka lolo inā loaʻa iā ʻoe nā hōʻailona e pili ana i kēia mau kino.
ʻO ka lapaʻau no ka APS e kau i ka pale ʻana i nā clots koko a me ka mālama ʻana i nā pilikia i hana mua ʻia. ʻO ka ʻoiaʻiʻo maikaʻi, me ka mālama kūpono, hiki i ka hapa nui o nā kānaka me ka APS ke ola i nā ola maʻamau, hana ʻole me nā palena nui.
ʻO nā ala lapaʻau nui e komo pū ana:
E hilinaʻi kāu papahana lapaʻau kūikawā i kāu kūlana pilikino. Inā loaʻa iā ʻoe nā clots koko ma mua, pono paha ʻoe i ka anticoagulation lōʻihi. Inā loaʻa iā ʻoe ka APS akā ʻaʻohe clots i loaʻa iā ʻoe, hiki i kāu kauka ke ʻōlelo aku i ka aspirin haʻahaʻa ma ke ʻano he ana pale.
No nā wāhine e hoʻolālā ana i ka hāpai ʻana, hoʻopili pinepine ka lapaʻau i ka hui pū ʻana o ka aspirin haʻahaʻa a me nā inikini heparin. He palekana kēia mau lāʻau i ka wā hāpai a hoʻemi nui i ka pilikia o nā pilikia hāpai. E nānā pono kāu kauka iā ʻoe i ka wā hāpai a hiki ke hoʻoponopono i kāu lapaʻau e like me ka pono.
He mea nui ka nānā mau ʻana no kēlā me kēia kanaka me ka APS. Pono ʻoe i nā hoʻokolohua koko manawa e nānā ai i kāu hana hoʻopili koko a e hōʻoia i ka hana pono ʻana o kāu mau lāʻau lapaʻau. E nānā pū kāu kauka i nā hōʻailona o nā pilikia a i ʻole nā hopena ʻaoʻao mai ka mālama ʻana.
ʻO ka mālama ʻana i ka APS ma ka home, ʻo ia ka lawe mau ʻana i kāu mau lāʻau lapaʻau a me ka hana ʻana i nā koho no ke ola e kākoʻo i kou olakino holoʻokoʻa. ʻOiai he mea nui ka mālama lapaʻau, nui nā mea hiki iā ʻoe ke hana ma ka home e kōkua i ka mālama pono ʻana i kou kūlana.
ʻO ka hoʻokō ʻana i ka lāʻau lapaʻau ʻo ia kāu hana mālama home nui loa. E lawe i kāu mau mea hoʻohilahila koko e like me ka mea i kuhikuhi ʻia, i ka manawa hoʻokahi i kēlā me kēia lā. Inā ʻoe ma ka warfarin, pono ʻoe i nā hoʻokolohua koko mau e nānā i kāu mau pae, no laila e mālama i kāu mau hālāwai a pau a hahai i nā palena ʻai āu kauka e kuhikuhi mai.
Hiki i nā hoʻololi ʻana i ke ola ke kōkua nui i ka mālama ʻana i kāu APS:
E makaʻala i kou kino a e nānā i nā hōʻailona hōʻailona o nā pili koko. E mālama i ka papa inoa o nā hōʻailona e nānā ai, a mai kānalua e hoʻokaʻaʻike i kāu kauka inā ʻike ʻoe i kekahi mea e hopohopo ai. ʻOi aku ka maikaʻi o ka nānā ʻana me kāu hui olakino ma mua o ka nānā ʻole ʻana i nā hōʻailona koʻikoʻi.
Inā ʻoe e hoʻolālā ana i kekahi hana ʻoki a i ʻole nā hana niho, e hōʻoia e haʻi aku i kāu poʻe lawelawe olakino e pili ana i kāu APS a me nā lāʻau lapaʻau āu e lawe nei. Pono paha lākou e hoʻoponopono i kāu mālama ʻana i ka manawa pōkole e hoʻemi ai i ka pilikia o ke kahe koko i ka wā o nā hana.
ʻO ka hoʻomākaukau ʻana no kāu kūkā ʻana e kōkua i ka hōʻoia ʻana e loaʻa iā ʻoe ka pono loa mai kāu manawa me kāu kauka a e kōkua iā lākou e hāʻawi i ka mālama maikaʻi loa. Hiki i ka hoʻomākaukau iki ke hoʻolilo i kahi ʻokoʻa nui i kāu mālama.
Ma mua o kāu kūkā ʻana, e hōʻiliʻili i ka ʻike e pili ana i kāu mau hōʻailona a me ka mōʻaukala lapaʻau. E kākau i ka manawa i hoʻomaka ai nā hōʻailona, he aha ka mea e hoʻomaikaʻi ai a ʻoi aku ka maikaʻi, a pehea lākou e hoʻopilikia ai i kou ola i kēlā me kēia lā. Inā loaʻa iā ʻoe nā clots koko a i ʻole nā pilikia hāpai ʻana, e hoʻomaopopo i nā lā a me nā kikoʻī.
E lawe mai i ka papa inoa piha o nā lāʻau āpau āu e lawe nei, me nā lāʻau lapaʻau ma luna o ka pākaukau, nā mea hoʻohui, a me nā lāʻau lapaʻau. Hiki i kekahi o kēia mau mea ke launa pū me nā mea hoʻohaʻahaʻa koko a i ʻole e hoʻopilikia i kāu mau hualoaʻa hoʻokolohua, no laila he mea nui ia no kāu kauka e ʻike i nā mea āpau āu e lawe nei.
E hoʻomākaukau i kahi papa inoa o nā nīnau e nīnau aku i kāu kauka. Makemake paha ʻoe e ʻike e pili ana i:
Inā ʻoe e ʻike ana i kahi loea no ka manawa mua, e noi i kāu kauka mālama mua e hoʻouna i kāu mau moʻolelo lapaʻau ma mua o ka manawa. ʻO kēia ka mea e komo pū ana i nā hualoaʻa hoʻokolohua koko ma mua, nā haʻawina kiʻi, a i ʻole nā moʻolelo lapaʻau e pili ana i kou kūlana.
ʻO ka mea nui loa e hoʻomaopopo e pili ana i ka APS ʻo ia ʻoiai he kūlana koʻikoʻi ia, hiki ke mālama ʻia loa ke hoʻokele pono ʻia. Hiki i ka hapa nui o nā kānaka me ka APS e loaʻa ana ka mālama kūpono ke manaʻo e ola i nā ola maʻamau, olakino me nā palena iki.
He mea nui ka ʻike koke ʻana a me ka mālama ʻana no ka pale ʻana i nā pilikia. Inā loaʻa iā ʻoe nā hōʻailona e hiki ke hōʻike i nā ʻāpana koko a i ʻole inā loaʻa iā ʻoe nā kumu pilikia no ka APS, mai kānalua e kūkākūkā me kāu kauka. Hiki i nā hoʻokolohua koko ke ʻike maʻalahi i nā antibodies e hoʻokumu ai i ka APS, a hiki ke hoʻomaka koke ka mālama ʻana inā pono.
E hoʻomanaʻo ʻaʻole ʻo ka loaʻa ʻana o ka APS he manaʻo ia e loaʻa iā ʻoe nā ʻāpana koko a i ʻole nā pilikia ʻē aʻe. Me ka mālama lapaʻau kūpono, ka hoʻokō ʻana i ka lāʻau lapaʻau, a me nā koho ola maikaʻi, hiki iā ʻoe ke hoʻokele pono i kēia kūlana. He nui nā kānaka me ka APS e hele i ka loaʻa ʻana o nā hāpai keiki holomua, nā ʻoihana hana, a me nā ola piha.
E noho pili me kāu hui mālama ola a mai makaʻu e nīnau i nā nīnau a i ʻole e ʻōlelo i nā hopohopo. ʻO kāu komo ʻana i kāu mālama ʻana kekahi o nā mea nui loa i ka hoʻokele pono ʻana i ka APS.
I kēia manawa, ʻaʻohe lāʻau lapaʻau no ka APS, akā hiki ke hoʻokele maikaʻi loa me nā lāʻau lapaʻau a me nā hoʻololi ʻana i ke ʻano o ke ola. ʻO ka hapa nui o nā kānaka me ka APS e loaʻa ana ka mālama kūpono hiki ke pale aku i nā ʻāpana koko a ola i nā ola maʻamau. Ke hoʻomau nei nā mea noiʻi e aʻo i nā lāʻau lapaʻau hou e hiki ke hāʻawi i nā hopena ʻoi aku ka maikaʻi i ka wā e hiki mai ana.
Ke hilinaʻi nei kēia i kou kūlana pilikino. Inā loaʻa iā ʻoe nā ʻāpana koko, e pono paha iā ʻoe ka anticoagulation lōʻihi e pale aku i nā ʻāpana koko i ka wā e hiki mai ana. Inā loaʻa iā ʻoe ka APS akā ʻaʻohe ou mau ʻāpana koko, hiki i kāu kauka ke ʻōlelo aku i ka aspirin haʻahaʻa a i ʻole ka nānā ʻana me ka ʻole o nā mea hoʻonāwaliwali koko. Hiki ke loli kāu papahana mālama ma muli o kāu mau kumu pilikia a me ka pane i ka mālama ʻana.
ʻAe, nui nā wāhine me ka APS i loaʻa nā hāpai keiki holomua me ka mālama lapaʻau kūpono. ʻO ka mālama ʻana i ka wā hāpai e pili pinepine ana i ka aspirin haʻahaʻa a me nā inikini heparin, he palekana no ka makuahine a me ke pēpē. Pono ʻoe i ka nānā pono i ka wā hāpai, akā hiki i ka hapa nui o nā wāhine me ka APS ke hāpai i kā lākou mau pēpē a hiki i ka manawa hānau.
Hiki i ka APS ke holo i loko o nā ʻohana, akā ʻaʻole ia i hoʻoilina pololei e like me kekahi mau kūlana genetic. Hiki iā ʻoe ke hoʻoilina i nā gene e hoʻonui i kou pilikia o ka loaʻa ʻana o ka APS, akā ʻo ka loaʻa ʻana o kahi lālā ʻohana me ka APS ʻaʻole ia e hōʻoiaʻiʻo e loaʻa iā ʻoe. Inā loaʻa iā ʻoe ka mōʻaukala ʻohana o ka APS a i ʻole nā kūmole koko, e kūkākūkā me kāu kauka no ka nānā kūpono.
ʻOiai ʻaʻole i hana pololei ke kaumaha i ka APS, hiki iā ia ke hoʻonui i kou pilikia o nā kūmole koko ma o ka hoʻopili ʻana i kou ʻōnaehana pale a me ka hoʻonui ʻana i ka mumū. ʻO ka hoʻokele ʻana i ke kaumaha ma o nā ʻano hoʻomaha, ka hoʻoikaika kino maʻamau, a me ka hiamoe lawa hiki ke pōmaikaʻi no kou olakino holoʻokoʻa a hiki ke kōkua i ka hoʻemi ʻana i kou pilikia clotting.
6Mpeople
Get clear medical guidance
on symptoms, medications, and lab reports.