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October 10, 2025
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He kūlana o ka naʻau ka hemahema o ke ala ʻauwai atrioventricular i loaʻa mai ka hānau ʻana, kahi i hana pono ʻole ai nā paia e hoʻokaʻawale ana i nā keʻena o ka naʻau. Hana kēia i nā puka ma waena o nā keʻena luna a me lalo o ka naʻau, e ʻae ana i ke koko e hui pū i ka wā ʻaʻole pono.
Hoʻopili kēia kūlana i ke kahe maʻamau o ke koko ma o ka naʻau o kāu pēpē, kahi e hiki ai ke hana nui aku ka naʻau ma mua o ka maʻamau. ʻOiai he mea hopohopo loa ia, nui nā keiki me kēia kūlana e ola ana i nā ola piha a hana nui me ka mālama lapaʻau kūpono a me ka mālama.
Hana ʻia ka hemahema o ke ala ʻauwai atrioventricular i ka wā i ulu pono ʻole ai ka ʻiʻo e hoʻokaʻawale maʻamau i nā keʻena ʻehā o kou naʻau i ka wā hāpai. Ma kahi o ka loaʻa ʻana o nā paia paʻa ma waena o nā keʻena, aia nā hakahaka e ʻae ana i ke koko e kahe i kahi ʻaʻole pono.
ʻEhā keʻena kou naʻau - ʻelua keʻena luna i kapa ʻia ʻo atria a ʻelua keʻena lalo i kapa ʻia ʻo ventricles. Ma ke ʻano maʻamau, noho ke koko haʻahaʻa oxygen ma ka ʻaoʻao ʻākau ʻoiai ke koko kiʻekiʻe oxygen ma ka ʻaoʻao hema. Me kēia hemahema, hui pū ke koko ma waena o kēia mau ʻaoʻao, ʻo ia hoʻi ʻaʻole lawa paha ke koko kiʻekiʻe oxygen i kou kino.
Kapa ʻia kēia kūlana he hemahema atrioventricular septal a i ʻole hemahema endocardial cushion. ʻO ia kekahi o nā hemahema naʻau congenital paʻakikī loa, ʻo ia hoʻi, aia mai ka hānau ʻana a hoʻopili i nā ʻāpana he nui o ke ʻano o ka naʻau.
ʻElua ʻano nui o kēia hemahema naʻau, a ʻo ka hoʻomaopopo ʻana i ke ʻano e hoʻopilikia ana i kāu keiki e kōkua i nā kauka e hoʻolālā i ke ala mālama maikaʻi loa.
Ka hemahema o ke ala atrioventricular hapa e pili ana i kahi puka ma ka paia ma waena o nā keʻena ʻelua o luna o ka naʻau. Hiki nō hoʻi i nā valve naʻau e kaohi ana i ke kahe koko ke ʻano ʻole, akā ua hoʻokaʻawale ʻia nō lākou. ʻO kēia ʻano maʻamau e hoʻopuka ai i nā hōʻailona liʻiliʻi a ʻaʻole paha e ʻike ʻia a hiki i ka wā ma hope o ke kamaliʻi.
Ka hemahema o ke ala atrioventricular piha he mea paʻakikī loa ia, me nā puka ma nā paia o luna a me lalo. Hoʻohui ʻia nā valve naʻau, e hana ana i hoʻokahi valve nui ma mua o ʻelua mau mea kaʻawale. ʻO kēia ʻano maʻamau e hoʻopuka ai i nā hōʻailona ma mua i ka wā kamaliʻi no ka mea nui ka hui ʻana o ke koko.
Loaʻa i kekahi mau keiki ka mea a nā kauka i kapa ai he ʻano waena a i ʻole hoʻololi, kahi i waena o ka hapa a me ka piha. E hoʻoholo kāu kauka naʻau pediatric i ke ʻano āu keiki me ka hoʻohana ʻana i nā hoʻokolohua naʻau kūikawā a me nā kiʻi.
ʻO nā hōʻailona āu keiki e ʻike ai e hilinaʻi ana i ka nui o ka hemahema a me ka nui o ke koko e hui ana i loko o kā lākou naʻau. Hōʻike kekahi mau keiki i nā hōʻailona i ka wā mua, ʻoiai ʻaʻole paha e loaʻa i nā mea ʻē aʻe nā hōʻailona maopopo no nā mahina a i ʻole nā makahiki.
Eia nā hōʻailona maʻamau i ʻike ʻia e nā mākua i nā pēpē a me nā keiki ʻōpio:
I ka ulu ʻana o nā keiki, e ʻike paha ʻoe ʻaʻole hiki iā lākou ke hoʻomau me nā hoa pāʻani i nā hana kino. Pono paha lākou e hoʻomaha pinepine aʻe a pale aku paha i nā hana e hana ai iā lākou i ka hanu pōkole.
ʻAʻole paha e hōʻike kekahi mau keiki me nā ʻano palupalu o kēia kūlana i nā hōʻailona maopopo a hiki i ko lākou wā kamaliʻi a i ʻole ke kula paha. ʻO ia ke kumu o ka nui o nā nānā maʻamau o nā keiki - hiki i kāu kauka ke ʻike i nā murmurs o ka naʻau a i ʻole nā hōʻailona ʻē aʻe i nā nānā maʻamau.
Hoʻomohala ʻia kēia hemahema naʻau i loko o nā hebedoma ʻewalu mua o ka hāpai ʻana i ka wā e hoʻokumu ai i ka naʻau o kāu pēpē. ʻAʻole maopopo mau ke kumu pololei, akā hana ia i ka wā e ulu pono ʻole ai ka pūnaewele e hoʻokaʻawale i nā keʻena naʻau i kēia manawa koʻikoʻi.
ʻO ka hapa nui o nā hihia e hana kūʻokoʻa me ka ʻole o kekahi mea hoʻonāukiuki kikoʻī a i ʻole ka hana o nā mākua e hoʻokumu ai iā lākou. He mea nui ia e hoʻomaopopo ʻaʻole ʻoe i hana a ʻaʻole i hana i ka wā hāpai i kēia kūlana - ʻo ia wale nō ke ʻano o ka hoʻomohala ʻana o ka naʻau o kāu pēpē.
Eia naʻe, aia kekahi mau mea e hiki ke hoʻonui i ka hiki ke hana ʻia o kēia hemahema:
ʻOiai me kēia mau pilikia, ʻo ka hapa nui o nā pēpē i hānau ʻia me nā naʻau maʻamau. ʻO ka hapa nui o nā hemahema atrioventricular canal e hana i nā ʻohana me ka ʻole o ka mōʻaukala o nā pilikia naʻau.
Inā ʻike ʻoe i kekahi mau hōʻailona e hopohopo ai ʻoe no ka hanu, ka hānai, a i ʻole ka nui o ka ikaika o kāu keiki, ʻoi aku ka maikaʻi o ka nānā ʻana iā lākou ma mua o ka kali ʻana. E hilinaʻi i kou manaʻo ma ke ʻano he mākua - ʻo ʻoe ka mea ʻike nui loa i kāu keiki.
E kelepona koke i kāu kauka keiki inā hōʻike kāu keiki i kekahi o kēia mau hōʻailona:
E kāhea koke i nā lawelawe pilikia inā pilikia nui kāu keiki i ka hanu, lilo i keʻokeʻo a uliuli paha, a i ʻole ke nānā aku nei he luhi loa a pane ʻole. Hiki i kēia ke lilo i mau hōʻailona ʻaʻole i hoʻopuka pono ʻia ko lākou naʻau e hoʻokō i nā pono o ko lākou kino.
E hoʻomanaʻo ʻo ka ʻike mua ʻana a me ka mālama ʻana e alakaʻi i nā hopena maikaʻi loa. He nui nā keiki me kēia kūlana e hana maikaʻi loa inā mālama ʻia ko lākou mālama ʻana e nā poʻe loea o ka naʻau o nā keiki.
ʻOiai ka nui o nā hihia e hana kūlohelohe, hiki i kekahi mau mea ke hoʻonui i ka manawa e hānau ʻia ai ka pēpē me kēia hemahema naʻau. Hiki i ka hoʻomaopopo ʻana i kēia mau kumu pilikia ke kōkua iā ʻoe e ʻike i ka mea e manaʻo ai a i ka wā e pono ai ka nānā pono.
ʻO ka mea pilikia ikaika loa ʻo ia ka Down syndrome, ʻoiai kokoke i ka hapalua o nā keiki me kēia kūlana genetic he atrioventricular canal defects. Inā loaʻa i kāu keiki ka Down syndrome, e nānā pono paha kāu hui lapaʻau i ko lākou naʻau mai ka hānau ʻana.
ʻO nā mea ʻē aʻe e hoʻonui paha i ka pilikia, ʻo ia:
He mea nui e hoʻomanaʻo ʻaʻole ʻo ka loaʻa ʻana o nā mea pilikia e hōʻoiaʻiʻo ana e loaʻa i kāu keiki kēia kūlana. He nui nā pēpē i hānau ʻia i nā makuahine me nā mea pilikia he nui loa i loaʻa nā naʻau maʻamau loa, ʻoiai ʻo nā mea ʻē aʻe me nā mea pilikia ʻole e hiki ke hoʻomohala i nā hemahema puʻuwai.
Me ka ʻole o ka mālama kūpono, hiki i kēia hemahema puʻuwai ke alakaʻi i nā pilikia koʻikoʻi i ka manawa. Eia naʻe, me ka mālama lapaʻau kūpono a me ka ʻoki kino ke pono, hiki ke pale ʻia a mālama ʻia paha ka hapa nui o kēia mau pilikia.
ʻO nā pilikia maʻamau loa e hiki ke hoʻomohala pū me:
Hiki i nā pilikia koʻikoʻi akā ʻoi aku ka liʻiliʻi ke komo pū me ka stroke, ʻoi aku hoʻi i nā keiki me ke ʻano piha o ka hemahema. Hiki i kekahi mau keiki ke hoʻomohala i kahi kūlana i kapa ʻia ʻo Eisenmenger syndrome, kahi e hōʻino mau ʻia ai nā kīʻaha koko i nā māmā mai ke kaomi kiʻekiʻe.
ʻO ka mea maikaʻi, ʻo ka hoʻoponopono ʻana i ka ʻoki kino i ka wā mua e hōʻemi nui ai i ka pilikia o kēia mau pilikia. ʻO ka hapa nui o nā keiki i hana ʻia ka ʻoki kino i ka manawa kūpono e ola mau ai me ke ola maʻamau, olakino maikaʻi me ka pilikia haʻahaʻa loa o nā pilikia o ka naʻau nui.
Hoʻomaka pinepine ka ʻike ʻana i ka manawa e lohe ai kāu kauka keiki i ka leo ʻano ʻē o ka naʻau i kapa ʻia ʻo ka murmur i ka wā o ka nānā maʻamau. ʻAʻole nā murmur naʻau a pau e hōʻike ana i nā pilikia, akā makemake kāu kauka e noiʻi hou aku e hōʻoia i ka hana pono ʻana o ka naʻau o kāu keiki.
ʻO ka hana mua pinepine ka echocardiogram, ʻo ia hoʻi ka ultrasound o ka naʻau. Hoʻohana kēia hoʻokolohua i nā nalu kani e hana i nā kiʻi kikoʻī o ke ʻano o ka naʻau o kāu keiki a hōʻike i ke ʻano o ke kahe koko ma o nā keʻena. He ʻoluʻolu loa ia a ʻaʻohe pono o nā nila a i ʻole nā lāʻau lapaʻau.
Hiki i kāu kauka ke kauoha aku i kēia mau hoʻokolohua hou aku:
I kekahi manawa, ʻike ʻia kēia kūlana ma mua o ka hānau ʻana i ka wā o nā ultrasound hāpai maʻamau. Inā manaʻo nā kauka i ka hemahema o ka naʻau i ka wā hāpai, hiki iā ʻoe ke loaʻa kahi fetal echocardiogram kūikawā e kiʻi i kahi kiʻi maopopo o ka ulu ʻana o ka naʻau o kāu pēpē.
ʻO ka loaʻa ʻana o kahi ʻike pololei e kōkua i kāu hui lapaʻau e hoʻolālā i ke ala lapaʻau maikaʻi loa a me ka manawa no ke kūlana kikoʻī o kāu keiki.
Aia ke lapaʻau ma ke ʻano a me ka nui o ka hemahema kikoʻī o kāu keiki. ʻO ka pahuhopu nui ka hoʻihoʻi ʻana i ke kahe koko maʻamau ma o ka naʻau a pale i ka ulu ʻana o nā pilikia ma hope.
No nā hemahema hapa me nā hōʻailona māmā, hiki i nā kauka ke nānā pono i kāu keiki ma mua, ʻoiai e hoʻokele ana i nā hōʻailona me nā lāʻau lapaʻau. Hiki i kēia mau lāʻau lapaʻau ke kōkua i ka puʻuwai e pūʻiwa maikaʻi a hoʻemi i ka wai i loko o nā māmā.
ʻO ka ʻoki kino ka lāʻau lapaʻau kūpono no ka hapa nui o nā keiki me kēia kūlana. Aia ka manawa i nā hōʻailona o kāu keiki a me ka maikaʻi o ka hana ʻana o ko lākou puʻuwai:
I ka wā o ka ʻoki kino, pani ka kauka puʻuwai i nā puka ʻole me nā ʻāpana a hoʻoponopono a hoʻololi paha i nā valve puʻuwai ʻole. ʻO ka hapa nui o nā keiki pono wale nō hoʻokahi ʻoki kino, ʻoiai kekahi e pono ai nā kaʻina hana hou aʻe i ko lākou ulu ʻana.
He kiʻekiʻe loa ka holomua o ka ʻoki kino, ʻoi aku ka nui inā hana ʻia ma nā kikowaena puʻuwai pediatric kūikawā. Hoʻōla maikaʻi ka hapa nui o nā keiki a hiki ke komo i nā hana kamaliʻi maʻamau i loko o kekahi mau mahina ma hope o ka ʻoki kino.
ʻO ka mālama ʻana i kahi keiki me kēia kūlana puʻuwai ma ka home e pili ana i ka nānā ʻana i kā lākou hōʻailona, e hahai ana i nā papa lāʻau lapaʻau, a me ka hana ʻana i kahi ʻano e kākoʻo ai i ko lākou olakino a me ka ulu ʻana.
Ma mua o ka ʻoki kino, e nānā i ke kōkua ʻana i kāu keiki e mālama i ka ikehu a ulu maikaʻi. Hiki paha kēia ke ʻano o ka hāʻawi ʻana i nā ʻaina liʻiliʻi, pinepine inā paʻakikī ka hānai ʻana, a i ʻole e ʻae i ka manawa hoʻomaha hou i ka lā.
Eia nā ʻāpana nui o ka mālama home:
Ma hope o ke ʻoki kino, pono i kāu keiki ka manawa e hoʻōla ai, akā nui nā keiki e hoʻi koke mai. E hahai i nā ʻōlelo a kāu kauka e pili ana i nā palena o ka hana, ka mālama ʻana i ka ʻeha, a me ka wā e hoʻomaka hou ai i nā hana maʻamau.
E hoʻomanaʻo e hoʻōla kēlā me kēia keiki ma ko lākou wikiwiki ponoʻī. Ua ʻoi aku ka maikaʻi o kekahi mau keiki i loko o nā hebedoma, ʻoiai he mau mahina paha kekahi e hoʻihoʻi i ko lākou ikaika a me ko lākou ikaika piha.
ʻO ka hoʻomākaukau maikaʻi ʻana no nā hālāwai lapaʻau e kōkua iā ʻoe e loaʻa nā ʻike kōkua loa a me ka hilinaʻi i ka hoʻolālā mālama o kāu keiki. E kākau i kāu mau nīnau ma mua i ʻole ʻoe e poina i nā manaʻo nui i ka wā o ka kipa.
E lawe mai i ka papa inoa piha o nā lāʻau lapaʻau a i ʻole nā mea hoʻohui a kāu keiki e lawe ai, me nā nui a me ka manawa. E ʻohi pū i nā hopena hoʻokolohua ma mua, nā moʻolelo lapaʻau, a i ʻole nā ʻike hoʻouna mai nā kauka ʻē aʻe.
E noʻonoʻo e hoʻomākaukau i kēia mau nīnau no kāu hui lapaʻau:
Mai kānalua e noi i ka ho'ākāka hou ʻana inā paʻakikī nā huaʻōlelo lapaʻau a i ʻole nā hoʻolālā mālama. Makemake kāu hui olakino e hōʻoia i kou hoʻomaopopo piha ʻana i ke kūlana o kāu keiki a me ka ʻoluʻolu me ka hoʻolālā mālama.
E lawe mai i kahi puke memo a i ʻole e noi inā hiki iā ʻoe ke hoʻopaʻa leo i nā ʻāpana koʻikoʻi o ke kamaʻilio ʻana. Hiki ke nui loa ka ʻike lapaʻau, a he kōkua nui ka loaʻa ʻana o nā memo e kuhikuhi ai ma hope.
ʻOiai ke aʻo ʻana ua loaʻa i kāu keiki kahi hemahema o ka naʻau, he mea nui ia e ʻike he mau kūlana maopopo maikaʻi nā hemahema o ke ala atrioventricular me nā hopena mālama maikaʻi loa. ʻO ka hapa nui o nā keiki e loaʻa ana i ka mālama kūpono e ola i nā ola maʻamau loa.
ʻO ke kī i ka holomua ʻo ka hana pū ʻana me nā poʻe loea naʻau pediatric akamai e hiki ke alakaʻi iā ʻoe ma ke kaʻina hana mālama. Ua hana nā ʻenehana ʻoki hou i ka hoʻoponopono ʻana i kēia mau hemahema i mea palekana a maikaʻi loa, me nā helu holomua i ʻoi aku ma mua o 95% ma nā kikowaena naʻau pediatric nui.
E hana kāu hui lapaʻau o kāu keiki i kahi hoʻolālā mālama pilikino e pili ana i kā lākou ʻano hemahema a me ke olakino holoʻokoʻa. Me ka mālama kūpono, hiki i ka hapa nui o nā keiki me kēia kūlana ke komo i nā hana maʻamau o ke kamaliʻi, me nā haʻuki a me nā hana kino ʻē aʻe.
E hoʻomanaʻo ʻaʻole ʻoe wale nō i kēia huakaʻi. He nui nā ʻohana i hele ma kēia ala ma mua ou, a he mau kumuwai kākoʻo maikaʻi loa e kōkua iā ʻoe e hoʻokele i nā ʻaoʻao lapaʻau a me ka manaʻo o ka mālama ʻana i kāu keiki.
Hiki i ka hapanui o nā keiki ke komo i nā hana kino maʻamau a me nā haʻuki ma hope o ka hana ʻoki kūleʻa. E loiloi kāu kauka naʻau pediatrik i ka hana o ka naʻau o kāu keiki a hāʻawi i nā kuhikuhi kikoʻī e pili ana i nā pae hana. He nui nā keiki me nā hemahema canal atrioventricular i hoʻoponopono ʻia e komo i nā haʻuki hoʻokūkū me ka ʻole o nā palena, ʻoiai ke loaʻa paha i kekahi poʻe nā palena iki ma nā hana ikaika loa.
Hoʻololi nā pono lāʻau ma muli o ke kūlana kikoʻī o kāu keiki a me ka maikaʻi o ka hana ʻana o ko lākou naʻau ma hope o ka hana ʻoki. Pono kekahi mau keiki i nā lāʻau lapaʻau wale nō ma mua a ma hope o ka hana ʻoki, ʻoiai ke pono paha i kekahi poʻe no ka lōʻihi e kōkua i ka hana maikaʻi ʻana o ko lākou naʻau. E loiloi mau kāu kauka naʻau inā pono nā lāʻau lapaʻau a hoʻoponopono i ka papa hana mālama e like me ka ulu ʻana o kāu keiki.
ʻOi aku ka nui o ka pilikia o ka loaʻa ʻana o kekahi keiki me ka hemahema naʻau i hānau ʻia, akā emi iki. ʻAʻole loaʻa i ka hapanui o nā ʻohana kekahi keiki me ka mea like. Hiki i kāu kauka ke ʻōlelo aku i ka ʻōlelo aʻo genetic e kūkākūkā i nā kumu pilikia kikoʻī o kou ʻohana a me nā koho hoʻokolohua i loaʻa i nā hāpai ʻana i ka wā e hiki mai ana.
ʻO ka hapanui o nā keiki e pono wale nō i hoʻokahi hana ʻoki e hoʻoponopono i kā lākou hemahema canal atrioventricular. Eia naʻe, pono paha i kekahi mau keiki nā kaʻina hana hou aʻe i ko lākou ulu ʻana, ʻoiai inā ʻaʻole hana maikaʻi nā valve naʻau ma hope o ka hoʻoponopono mua. E nānā kāu kauka naʻau i ka hana o ko lākou naʻau i ka manawa a e ʻōlelo aku i nā mālama hou aʻe inā pono wale nō.
ʻO ka manawa hoʻōla e ʻokoʻa ana, akā hiki i ka hapa nui o nā keiki ke hoʻi mālie i nā hana maʻamau i loko o 6-8 mau pule ma hope o ke ʻoki kino. E hāʻawi mai kāu kauka ʻoki kino i nā kuhikuhi kikoʻī e pili ana i nā palena kaumaha, i ka wā e hiki ai i kāu keiki ke hoʻi i ke kula, a i ka wā e hiki ai iā lākou ke hoʻomaka hou i nā hana kino. ʻOi aku ka maikaʻi o ka hapa nui o nā keiki i loko o nā pule mua a hoʻomau i ka holomua i nā mahina e hiki mai ana.
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