ʻO ka coarctation o ka aorta kahi ho'onui iki ʻana ma kahi hapa o ke kīʻaha nui o ke kino, i kapa ʻia ʻo ka aorta. Pono ka naʻau e pūʻiwa nui aku e hoʻouna i ke koko ma o ka aorta a i nā ʻāpana ʻē aʻe o ke kino.
ʻO ka coarctation o ka aorta (ko-ahrk-TAY-shun) kahi ho'onui iki ʻana o kahi hapa o ke kīʻaha nui o ke kino, i kapa ʻia ʻo ka aorta. Ke koi nei ke kūlana i ka naʻau e hana ikaika e pūʻiwa i ke koko.
Loaʻa pinepine ka coarctation o ka aorta i ka wā hānau. ʻO ia hoʻi, he kīnā hānau ia o ka naʻau. Akā, i kekahi manawa, hiki ke loaʻa ke kūlana ma hope i ke ola.
Loaʻa pinepine ka coarctation o ka aorta me nā kīnā hānau ʻē aʻe o ka naʻau. Hoʻokō pinepine ʻia ka mālama ʻana e hoʻoponopono i ke kūlana. Akā, pono nā nānā olakino maʻamau no ke ola e nānā i nā loli i ke olakino o ka naʻau.
Hōʻailona o ka coarctation o ka aorta e hilinaʻi ana i ka nui o ka aorta i hoʻoemi ʻia. ʻAʻohe hōʻailona o ka hapanui o nā kānaka. ʻAʻole paha he hōʻailona nā mākua a me nā keiki kahiko me ka coarctation iki o ka aorta a ua like paha ko lākou naʻau me ke olakino. Inā hānau ʻia ke pēpē me ka hoʻoemi nui ʻana o ka aorta, hiki ke ʻike ʻia nā hōʻailona ma hope koke o ka hānau ʻana. ʻO nā hōʻailona o ka coarctation o ka aorta i nā pēpē e komo pū ana: Paʻakikī ke hanu. Paʻakikī ke hānai. Ke kaumaha nui nei. Hoʻonāukiuki. Hoʻololi i ke kala o ka ʻili. ʻO nā hōʻailona o ka coarctation o ka aorta ma hope i ke ola e komo pū ana: ʻEha umauma. Ke kiʻekiʻe o ke koko. ʻO ka poʻo ʻeha. Nāwaliwali o nā ʻiʻo. ʻO ka ʻeha o nā wāwae. Nā wāwae anu. Kahe koko i ka ihu. Hoʻomaka pinepine ka coarctation o ka aorta me nā kūlana naʻau ʻē aʻe i loaʻa i ka hānau ʻana. ʻO nā hōʻailona ʻē aʻe e hilinaʻi ana i nā ʻano kikoʻī o nā hemahema naʻau i hānau ʻia. E kiʻi koke i ke kōkua lapaʻau no kekahi ʻeha umauma i koʻikoʻi a ʻaʻole hiki ke wehewehe ʻia. E kiʻi pū i ke kōkua lapaʻau no kēia mau hōʻailona: Ke hiolo ʻana. Ke pokopoko koke ʻana o ka hanu. Ke kiʻekiʻe o ke koko i hiki ʻole ke wehewehe ʻia. Hiki i kēia mau hōʻailona ke hoʻokumu ʻia e nā kūlana olakino like ʻole. Pono ka nānā olakino piha e ʻike i ke kumu.
E hele koke i ke kōkua lapaʻau no kekahi ʻeha umauma ikaika loa a i ʻole hiki ʻole ke wehewehe. E hele pū kekahi i ke kōkua lapaʻau no kēia mau hōʻailona: Hina ʻana. Pōkole koke o ka hanu. Ke koko kiʻekiʻe i hiki ʻole ke wehewehe. Hiki i kēia mau hōʻailona ke hoʻokumu ʻia e nā kūlana olakino like ʻole. Pono ka nānā olakino piha e ʻike i ke kumu.
ʻAʻole maopopo ke kumu o ka coarctation o ka aorta. ʻO ka mea maʻamau, he pilikia naʻau ia i loaʻa i ka wā hānau, i kapa ʻia ʻo ka hemahema naʻau congenital. Hana ʻia ka hemahema naʻau congenital i ka wā e ulu ana ke pēpē i loko o ka ʻōpū i ka wā hāpai. ʻO ka mea pinepine, ʻaʻole ʻike ʻia ke kumu.
I nā manawa kakaikahi, hiki i ka coarctation o ka aorta ke hana ma hope i ke ola. ʻO nā kūlana a i ʻole nā hanana e hiki ke hoʻonui i ka aorta a hoʻokumu i kēia kūlana, ʻo ia hoʻi:
Nā kumu pilikia no ka coarctation o ka aorta:
Nā hemahema naʻau congenital e pili ana i ka coarctation o ka aorta:
Hōʻino o ka coarctation o ka aorta e kū mai ana no ka mea, pono ka keʻena naʻau hema haʻahaʻa e hana ikaika e pūpū i ke koko ma o ke kīʻaha koko haiki. ʻO kēia ka mea e piʻi ai ke kaomi koko i loko o ke keʻena naʻau hema haʻahaʻa. Eia kekahi, hiki i ka paia o ke keʻena ke mānoanoa. Ua kapa ʻia kēia kūlana he ventricular hypertrophy. ʻO nā hōʻino o ka coarctation o ka aorta e komo pū ana: Ke kaomi koko kiʻekiʻe lōʻihi. Maʻamau ka emi ʻana o ke kaomi koko ma hope o ka ʻoki kino e hoʻoponopono i ka aorta. Akā, hiki ke kiʻekiʻe ma mua o ka maʻamau. ʻO ka kīʻaha koko nāwaliwali a i ʻole puʻupuʻu i loko o ka lolo, i ʻike ʻia hoʻi he aneurysm lolo. Ke koko koko i loko o ka lolo. ʻO ka haki a i ʻole ka haehae i loko o ke kīʻaha nui o ke kino, i kapa ʻia ʻo ka aortic dissection. ʻO ka puʻupuʻu i loko o ka paia o ke kīʻaha nui o ke kino, i kapa ʻia ʻo ka aortic aneurysm. ʻO ka maʻi kīʻaha coronary. Stroke. Pono ka mālama koke e kōkua i ka pale ʻana i nā hōʻino. Me ka ʻole o ka mālama ʻana, hiki i ka coarctation o ka aorta ke alakaʻi i: ka hōʻino ʻana o ka puʻupaʻa. Ka hōʻino ʻana o ka naʻau. Make. Loaʻa i kekahi poʻe nā hōʻino ma hope o ka mālama ʻana no ka coarctation o ka aorta. ʻO kēia mau hōʻino e komo pū ana: Ke hoʻohaiki hou ʻana o ka aorta, i kapa ʻia ʻo re-coarctation. Aortic aneurysm a i ʻole rupture. No ka pale ʻana i nā hōʻino, pono nā poʻe me ka coarctation o ka aorta i nā nānā olakino maʻamau no ke ola.
ʻAʻohe ala i ʻike ʻia e pale aku ai i ka coarctation o ka aorta. E haʻi aku i kāu kime mālama ola inā he mōʻaukala ʻohana kāu o nā kūlana naʻau i loaʻa i ka wā hānau.
Hiki ke hilinaʻi ka ʻike ʻana o ka coarctation aortic i ka nui o ka pilikia o ka naʻau. Hoʻomaopopo pinepine ʻia ka coarctation aortic koʻikoʻi ma hope koke o ka hānau ʻana. Hiki ke ʻike ʻia ke kūlana ma nā kiʻi ultrasound i lawe ʻia i ka wā hāpai.
Inā māmā ke kūlana, ʻaʻole paha e ʻike ʻia a hiki i ka wā ma hope.
Hiki ke lohe ʻia kahi kani ʻūlū i kapa ʻia he murmur naʻau i ka hoʻolohe ʻana i ka naʻau.
Hana ʻia nā hoʻokolohua e ʻike i ka coarctation o ka aorta.
I ka wā o ka cardiac catheterization, waiho ʻia kahi tube māmā a palupalu i kapa ʻia he catheter i loko o kahi kīʻaha koko, maʻamau ma ka ʻūhā a i ʻole ka lima, a alakaʻi ʻia i ka naʻau. Kahe ke kala ma o ka catheter i nā arteries i loko o ka naʻau. Hana maʻalahi ka kala i nā arteries i ka ʻike ʻana ma nā kiʻi X-ray a me nā wikiō. Hiki i ka cardiac catheterization ke kōkua i ka hoʻoholo ʻana i ka nui o ka aorta i hoʻonui ʻia.
Coronary angiogram me ka cardiac catheterization. Hoʻohana ka coronary angiogram i nā X-rays e nānā i nā kīʻaha koko o ka naʻau, i kapa ʻia he coronary arteries. Hana pinepine ʻia ia e ʻike inā hoʻonui ʻia a i ʻole paha i pani ʻia kahi kīʻaha koko. ʻO ka coronary angiogram kahi ʻāpana o kahi hui nui o nā hoʻokolohua naʻau a me nā mālama i kapa ʻia ʻo cardiac catheterization.
I ka wā o ka cardiac catheterization, waiho ʻia kahi tube māmā a palupalu i kapa ʻia he catheter i loko o kahi kīʻaha koko, maʻamau ma ka ʻūhā a i ʻole ka lima, a alakaʻi ʻia i ka naʻau. Kahe ke kala ma o ka catheter i nā arteries i loko o ka naʻau. Hana maʻalahi ka kala i nā arteries i ka ʻike ʻana ma nā kiʻi X-ray a me nā wikiō. Hiki i ka cardiac catheterization ke kōkua i ka hoʻoholo ʻana i ka nui o ka aorta i hoʻonui ʻia.
ʻO ke ʻano o ka mālama ʻana i ka coarctation o ka aorta e hilinaʻi ana i ka makahiki o ke kanaka i ka wā i ʻike ʻia ai ke kūlana o ka naʻau. E hilinaʻi pū ana ke ʻano o ka mālama ʻana i ka nui o ka aorta i hoʻonui ʻia.
Hiki i ka mālama ʻana i ka coarctation o ka aorta ke komo pū me:
Inā aia nā hemahema naʻau i hānau ʻia, hiki ke hoʻoponopono ʻia i ka manawa like.
Hiki i nā lāʻau lapaʻau no ka coarctation o ka aorta ke komo pū me:
Hiki ke hana ʻia ka ʻoki ʻana a i ʻole kahi kaʻina hana naʻau e hoʻoponopono ai i ka coarctation o ka aorta. ʻO nā koho e komo pū me:
Balloon angioplasty a me ka stenting. Hiki paha kēia ke mālama mua ʻia no ka coarctation o ka aorta. I kekahi manawa, hana ʻia inā hoʻonui hou ʻia ka aorta ma hope o ka ʻoki ʻana o ka coarctation. Kūleʻa ke ʻano o ka mālama ʻana i ka hoʻonui ʻana i ka artery i hoʻonui ʻia a hoʻomaikaʻi i ke kahe koko.
I ka wā o ka angioplasty, hoʻohana ka kauka i kahi tube lahilahi i kapa ʻia ʻo ka catheter a me kahi balloon liʻiliʻi e wehe i ka artery i hoʻonui ʻia. Maʻamau, waiho ʻia kahi coil metala liʻiliʻi i kapa ʻia ʻo ka stent i loko o ka artery. Mālama ka stent i ka artery e wehe ana. Hoʻemi pū ia i ka pilikia o ka hoʻonui hou ʻana.
Resection me ka end-to-end anastomosis. Wehe ka mea ʻoki i ka wahi i hoʻonui ʻia o ka aorta. Kēia ka mea i kapa ʻia ʻo ka resection. A laila hoʻohui ka mea ʻoki i nā ʻāpana olakino ʻelua o ka aorta. Kēia ka mea i kapa ʻia ʻo anastomosis.
Subclavian flap aortoplasty. Lawe ka mea ʻoki i kahi ʻāpana o ka moku koko e hāʻawi ana i ke koko i ka lima hema, i kapa ʻia ʻo ka subclavian artery hema, a hoʻohana ia e hoʻonui i ka wahi i hoʻonui ʻia o ka aorta.
Bypass graft repair. Hoʻohana kēia ʻoki ʻana i kahi tube i kapa ʻia ʻo ka graft e hana i kahi ala hou no ke koko e kahe ai a puni ka wahi i hoʻonui ʻia o ka aorta.
Patch aortoplasty. ʻoki ka mea ʻoki i ka wahi i hoʻonui ʻia o ka aorta a hoʻopili i kahi ʻāpana o ka mea e hoʻonui ai i ka moku koko. He mea pono kēia ʻano o ka mālama ʻana inā komo ka coarctation i kahi ʻāpana lōʻihi o ka aorta.
Balloon angioplasty a me ka stenting. Hiki paha kēia ke mālama mua ʻia no ka coarctation o ka aorta. I kekahi manawa, hana ʻia inā hoʻonui hou ʻia ka aorta ma hope o ka ʻoki ʻana o ka coarctation. Kūleʻa ke ʻano o ka mālama ʻana i ka hoʻonui ʻana i ka artery i hoʻonui ʻia a hoʻomaikaʻi i ke kahe koko.
I ka wā o ka angioplasty, hoʻohana ka kauka i kahi tube lahilahi i kapa ʻia ʻo ka catheter a me kahi balloon liʻiliʻi e wehe i ka artery i hoʻonui ʻia. Maʻamau, waiho ʻia kahi coil metala liʻiliʻi i kapa ʻia ʻo ka stent i loko o ka artery. Mālama ka stent i ka artery e wehe ana. Hoʻemi pū ia i ka pilikia o ka hoʻonui hou ʻana.
Hōʻole: He kahua ʻike olakino ʻo ʻAukake a ʻaʻole hōʻike kāna mau pane i ka ʻōlelo aʻoaʻo lapaʻau. E kūkākūkā mau me kahi ʻoihana lapaʻau laikini kokoke iā ʻoe ma mua o ka hana ʻana i nā hoʻololi.
Hana ʻia i India, no ka honua