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Maʻi Eisenmenger

Nānaina

ʻO ka maʻi Eisenmenger (I-sun-meng-ur) kahi pilikia lōʻihi o kahi kūlana naʻau i hoʻoponopono ʻole ʻia i loaʻa mai ka wā hānau, i kapa ʻia ʻo ka hemahema naʻau i hānau ʻia. He mea weliweli i ke ola ka maʻi Eisenmenger. I ka maʻi Eisenmenger, aia kahe koko kūpono ʻole i loko o ka naʻau a me nā māmā. Ke kumu kēia i ka paʻakikī a me ka hoʻonui ʻia ʻana o nā kīʻaha koko i loko o nā māmā. Piʻi ke kaomi koko i loko o nā arteries o nā māmā. Hana ka maʻi Eisenmenger i ka pōʻino mau loa i nā kīʻaha koko i loko o nā māmā. ʻO ka ʻike mua ʻana a me ka hoʻoponopono ʻana i nā hemahema naʻau i hānau ʻia e pale pinepine i ka maʻi Eisenmenger. Inā ulu ia, ʻo ka mālama ʻana e komo pū me nā nānā olakino maʻamau a me nā lāʻau lapaʻau e hoʻomaikaʻi ai i nā hōʻailona.

Nā hōʻailona

ʻO nā hōʻailona o ka maʻi Eisenmenger syndrome: ʻIli uliuli a hina paha. Ma muli o ke kala o ka ʻili, hiki ke paʻakikī a maʻalahi paha ke ʻike i kēia mau loli. ʻEha umauma a i ʻole ka ʻāʻī. Ka haʻalulu koko. Ka luhi a i ʻole ka hiolo. Ka luhi maʻalahi a me ka hanu pōkole me ka hana. Nā poʻoʻeha. Nā kui lima a i ʻole nā ​​kui wāwae nui a puni, i kapa ʻia ʻo ka clubbing. Ka ʻeha a i ʻole ka wiliwili i nā manamana lima a i ʻole nā ​​manamana wāwae. Ka hanu pōkole i ka wā hoʻomaha. Ka pōloli a i ʻole ka holo wikiwiki ʻana o ka naʻau. Inā loaʻa iā ʻoe kekahi hōʻailona o ka maʻi Eisenmenger syndrome, e ʻike i kāu kauka lapaʻau. E hana i kahi kūkā ʻana ʻoiai inā ʻaʻohe ou maʻi naʻau i ʻike ʻia. E kiʻi i ka kōkua lapaʻau pilikia no nā hōʻailona e like me ka hanu pōkole a i ʻole ka ʻeha umauma.

ʻO ka manawa hea e ʻike ai i ke kauka

Inā loaʻa iā ʻoe kekahi mau hōʻailona o ka maʻi Eisenmenger, e ʻike i kāu kauka lapaʻau. E hana i kahi kūkā, ʻoiai inā ʻaʻohe ou maʻi naʻau i ʻike ʻia. E kiʻi i ka lāʻau lapaʻau pilikia no nā hōʻailona e like me ka hanu ʻole a i ʻole ka ʻeha umauma.

Nā kumu

ʻO ka maʻi Eisenmenger maʻamau ka mea i hoʻokumu ʻia e ka puka ʻole i hoʻoponopono ʻia ma waena o nā kīʻaha koko nui a i ʻole nā ​​keʻena o ka naʻau. ʻO ka puka ka mea i kapa ʻia he shunt. He pilikia naʻau ka shunt i loaʻa i ka wā hānau, ʻo ia hoʻi he hemahema naʻau congenital. ʻO nā hemahema naʻau congenital e hiki ke hoʻokumu i ka maʻi Eisenmenger: Ventricular septal defect. ʻO kēia ka kumu maʻamau loa o ka maʻi Eisenmenger. Aia kahi puka ma ka paia o ka ʻiʻo ma waena o nā keʻena naʻau lalo. Atrioventricular canal defect. He puka nui kēia ma waenakonu o ka naʻau. ʻO ka puka kahi e hui ai nā paia ma waena o nā keʻena luna a me nā keʻena lalo. ʻAʻole paha e hana pono kekahi o nā valve i loko o ka naʻau. Atrial septal defect. He puka kēia ma ka paia o ka ʻiʻo ma waena o nā keʻena naʻau luna ʻelua. Patent ductus arteriosus. He wehe kēia ma waena o ke kīʻaha e lawe i ke koko haʻahaʻa oxygen i nā māmā a me ke kīʻaha nui o ke kino. I kēlā me kēia o kēia mau kūlana naʻau, ke kahe nei ke koko ma ke ʻano maʻamau ʻole. Ma muli o kēia, piʻi ka kaomi i loko o ke kīʻaha pulmonary. Ma hope o kekahi manawa, hoʻopōʻino ka kaomi kiʻekiʻe i nā kīʻaha koko liʻiliʻi i loko o nā māmā. Hana paʻakikī nā paia kīʻaha koko i hōʻino ʻia i ka naʻau e hoʻopuka i ke koko i nā māmā. I ka maʻi Eisenmenger, piʻi ka kaomi koko ma ka ʻaoʻao o ka naʻau i loaʻa ke koko haʻahaʻa oxygen, i kapa ʻia hoʻi he koko uliuli. Ke hele nei ke koko uliuli ma o ka puka i loko o ka naʻau a i ʻole nā ​​kīʻaha koko. Ke hui pū nei ke koko momona oxygen a me ke koko haʻahaʻa oxygen. Hana kēia i nā pae oxygen haʻahaʻa.

Nā mea pilikia

Ke hoʻonui nei ka mōʻaukala ʻohana o nā hemahema naʻau i hānau ʻia i ka pilikia o nā pilikia naʻau like i loko o ka pēpē. Inā ua ʻike ʻia ʻoe me ka maʻi Eisenmenger, e kamaʻilio me kāu limahana mālama ola e pili ana i ka nānā ʻana i nā lālā ʻohana ʻē aʻe no nā hemahema naʻau i hānau ʻia.

Nā pilikia

ʻO ka maʻi Eisenmenger he kūlana weliweli i ke ola. Aia ke kūlana o ka mea maʻi Eisenmenger ma ke kumu kūikawā a inā he mau kūlana olakino ʻē aʻe.

Hiki i nā pilikia o ka maʻi Eisenmenger ke komo pū me:

  • Haʻahaʻa ka oxygen i loko o ke koko. Hoʻouna ka loli o ke kahe koko ma o ka naʻau i ka oxygen emi i nā pūnaewele a me nā ʻōnaehana o ke kino. Me ka ʻole o ka mālama koke ʻana, e emi hou aku ka oxygen.
  • ʻO nā hahau naʻau kūpono ʻole, i kapa ʻia hoʻi he arrhythmias. Hoʻokumu ka maʻi Eisenmenger i ka nui a me ka mānoanoa o nā paia o ka naʻau. Hoʻokumu pū ia i ka emi ʻana o ka oxygen. Hiki i kēia mau loli ke alakaʻi i nā hahau naʻau kūpono ʻole. Hoʻonui kekahi mau hahau naʻau kūpono ʻole i ka pilikia o nā ʻāpana koko e hiki ke hoʻokumu i nā maʻi naʻau a i ʻole nā ​​stroke.
  • Ka hopu naʻau koke. ʻO kēia ka nalowale koke ʻana o ka hana naʻau ma muli o ka hahau naʻau kūpono ʻole. Inā ʻaʻohe mālama koke ʻana, hiki i ka hopu naʻau koke ke alakaʻi koke i ka make. Hiki ke ola me ka mālama olakino wikiwiki a kūpono.
  • Ke kahe koko i loko o nā māmā. Hiki i ka maʻi Eisenmenger ke hoʻokumu i ke kahe koko weliweli i loko o nā māmā a me nā ala hanu. Hiki ke kahe koko i nā ʻāpana ʻē aʻe o ke kino.
  • Stroke. Inā hele kahi ʻāpana koko mai ka ʻaoʻao ʻākau a i ka ʻaoʻao hema o ka naʻau, hiki i ka ʻāpana ke pani i ka ipu koko i loko o ka lolo. Hiki i kahi ʻāpana koko i loko o ka lolo ke alakaʻi i kahi stroke.
  • Ka maʻi puʻupaʻa. Hiki i ka haʻahaʻa o ka oxygen i loko o ke koko ke alakaʻi i ka pilikia me nā puʻupaʻa.
  • Gout. Hiki i ka maʻi Eisenmenger ke hoʻonui i ka pilikia o kahi ʻano o ka maʻi ʻiliʻili i kapa ʻia ʻo gout. Hoʻokumu ka Gout i nā hoʻouka koke, ʻeha nui a me ka pehu i hoʻokahi a ʻoi aku paha nā hui, maʻamau ka manamana nui.
  • Ka maʻi naʻau. Loaʻa i nā kānaka me ka maʻi Eisenmenger kahi pilikia kiʻekiʻe o ka maʻi naʻau i kapa ʻia ʻo endocarditis.
  • Nā pilikia hāpai keiki. I ka wā hāpai, pono ka naʻau a me nā māmā e hana ikaika e kākoʻo i ke keiki e ulu ana. Ma muli o kēia, ʻo ka hāpai keiki me ka maʻi Eisenmenger he pilikia nui o ka make no ka mea hāpai a me ke keiki. Inā loaʻa iā ʻoe ka maʻi Eisenmenger, e kamaʻilio me kāu kauka e pili ana i kāu mau pilikia hāpai keiki kūikawā.
ʻImi ʻike

No ka hōʻoiaʻana i ka maʻi Eisenmenger, e nānā ana kāu limahana mālama ola iā ʻoe a e nīnau i nā nīnau e pili ana i kou mau hōʻailona a me ka mōʻaukala lapaʻau.

Hiki i nā ho'okolohua e hōʻoia i ka maʻi Eisenmenger ke komo pū me:

  • Nā ho'okolohua koko. Hoʻokō pinepine ʻia ka helu piha o nā keʻena koko. Hiki ke kiʻekiʻe ka nui o nā keʻena koko ʻulaʻula i ka maʻi Eisenmenger. Hana ʻia nō hoʻi nā ho'okolohua koko e ʻike ai i ka hana maikaʻi ʻana o nā puʻupaʻa a me ke ake. ʻO kekahi ho'okolohua koko e nānā ana i ka pae hao.
  • Electrocardiogram (ECG a EKG). ʻO kēia ho'okolohua wikiwiki a ʻoluʻolu ʻole e ana i ka hana uila o ka naʻau. I ka wā o ka ECG, hoʻopili ʻia nā ʻāpana pipili me nā mea ʻike ma luna o lākou i ka umauma a i kekahi manawa i nā lima a i nā wāwae. Hoʻohui nā kaula i nā mea ʻike i ka mīkini, kahi e hōʻike a i ʻole paʻi i nā hopena. Hiki i ka ECG ke hōʻike i ka wikiwiki a i ʻole ka lohi o ka hahau ʻana o ka naʻau.
  • X-ray umauma. Hōʻike ka X-ray umauma i ke kūlana o ka naʻau a me nā māmā.
  • Echocardiogram. Hoʻokumu nā hawewe leo i nā kiʻi kikoʻī o ka naʻau e neʻe ana. Hōʻike ka echocardiogram i ke kahe koko ma o ka naʻau a me nā valve naʻau.
  • Computerized tomography (CT) scan o nā māmā. Hoʻohana kēia ʻano CT scan i nā X-rays e hana i nā kiʻi kikoʻī o nā māmā a me nā arteries māmā. Hāʻawi nā kiʻi CT scan i ka ʻike kikoʻī hou aku ma mua o nā X-rays maʻamau.
  • Magnetic resonance imaging (MRI) scan o nā māmā. Hoʻohana kēia ho'okolohua i nā kahua magnetic a me nā hawewe radio e hana i nā kiʻi kikoʻī o nā kīʻaha koko i loko o nā māmā.
  • Ho'okolohua hele wāwae. Hiki ke noi ʻia ʻoe e hele no kekahi mau minuke e ʻike ai i ka pane ʻana o kou kino i ka hoʻoikaika māmā.
Ka mālama ʻana

ʻO nā pahuhopu o ka mālama ʻana i ka maʻi Eisenmenger:

  • Ke hoʻokele nei i nā hōʻailona.
  • Ke hoʻomaikaʻi nei i ka maikaʻi o ke ola.
  • Ke pale aku nei i nā pilikia.

Inā loaʻa iā ʻoe ka maʻi Eisenmenger, hoʻouna pinepine ʻia ʻoe i ke kauka i aʻo ʻia i nā maʻi naʻau, i kapa ʻia he cardiologist. He mea kōkua ke loaʻa iā ʻoe kahi cardiologist nona ka ʻike i ka mālama ʻana i nā poʻe i loaʻa nā hemahema naʻau i hānau ʻia. ʻO nā nānā olakino maʻamau - ma ka liʻiliʻi hoʻokahi manawa i ka makahiki - he ʻāpana nui ia o ka mālama ʻana i ka maʻi Eisenmenger.

ʻO nā lāʻau lapaʻau ka mālama nui no ka maʻi Eisenmenger. ʻAʻole hiki i nā lāʻau lapaʻau ke ho'ōla i ka maʻi Eisenmenger, akā hiki iā lākou ke kōkua i ka hoʻomaikaʻi ʻana i ka maikaʻi o ke ola.

ʻO nā lāʻau lapaʻau i hoʻohana ʻia e mālama i ka maʻi Eisenmenger:

  • Nā lāʻau lapaʻau e kaohi ai i ka hahau ʻana o ka naʻau. Kīaʻia kēia mau lāʻau lapaʻau he anti-arrhythmics. Kūkulu lākou i ka hoʻokele ʻana i ka leo o ka naʻau a pale aku i nā hahau naʻau kūpono ʻole.
  • Nā mea hoʻohui hao. Hiki i kāu limahana mālama ola ke manaʻo aku i kēia mau mea inā he haʻahaʻa loa kāu pae hao. Mai hoʻomaka e lawe i nā mea hoʻohui hao me ka ʻole o ke kamaʻilio ʻana me kāu hui mālama ola.
  • Aspirin a i ʻole nā lāʻau lapaʻau hoʻonui koko. Inā loaʻa iā ʻoe kahi hahau, kahi ʻāpana koko a i ʻole kekahi ʻano o nā hahau naʻau kūpono ʻole, pono paha ʻoe e lawe i ka aspirin a i ʻole kahi mea hoʻonui koko e like me ka warfarin (Jantoven). Hiki i kēia mau lāʻau lapaʻau ke hoʻonui i ka pilikia o ke kahe koko. Mai lawe iā lākou ke ʻole kāu hui mālama ola i haʻi aku iā ʻoe e hana pēlā.
  • Bosentan (Tracleer). Hoʻohana ʻia kēia lāʻau lapaʻau inā loaʻa iā ʻoe ka hypertension arterial pulmonary. Kūkulu ia i ka hoʻouna ʻana i ka nui o ke koko i nā māmā. Inā lawe ʻoe i kēia lāʻau lapaʻau, pono ʻoe i nā hoʻokolohua koko maʻamau no ka mea hiki i ka lāʻau ke hōʻino i ke akepaʻa.
  • Antibiotics. Hiki i kekahi mau hana niho a me nā hana lapaʻau ke hoʻokuʻu i nā germs i loko o ke koko. Pono kekahi poʻe e lawe i nā antibiotics ma mua o ka ʻoki a i ʻole nā hana niho e pale aku i ka maʻi naʻau i kapa ʻia ʻo endocarditis. Hoʻomaopopo wale ʻia nā antibiotics pale i nā kūlana kūikawā. E kamaʻilio me kāu limahana mālama ola e ʻike inā kūpono lākou no ʻoe.

ʻAʻole manaʻo nā limahana mālama ola i ka ʻoki e hoʻoponopono i ka puka ma ka naʻau ke hoʻomohala ʻia ka maʻi Eisenmenger.

ʻO nā ʻoki a i ʻole nā hana i hiki ke hana ʻia e mālama i nā hōʻailona a i ʻole nā pilikia o Eisenmenger:

  • Ka lawe ʻana i ke koko, i kapa ʻia hoʻi he phlebotomy. Inā nui loa kāu helu ʻāpana koko ʻulaʻula a ke hana nei i nā hōʻailona e like me nā poʻo ʻeha a i ʻole ka pilikia i ka ʻike ʻana a i ʻole ke kūkākūkā ʻana, pono paha ʻoe i kēia mālama. ʻAʻole pono e hana maʻamau ʻia ka phlebotomy a pono wale nō e hana ma hope o ke kamaʻilio ʻana me kahi loea maʻi naʻau i hānau ʻia. Pono e hāʻawi ʻia nā wai ma o kahi vein (IV) i loko o kēia mālama e kōkua i ka hoʻololi ʻana i nā wai i nalowale.
  • Ka hoʻololi naʻau a i ʻole māmā. Inā ʻaʻole hana nā mālama ʻē aʻe no ka maʻi Eisenmenger, pono paha kekahi poʻe i ka ʻoki e hoʻololi i ka naʻau a i ʻole nā māmā.

Inā pono ʻoe i ka mālama no ka maʻi Eisenmenger, e kiʻi i ka mālama ma kahi kikowaena lapaʻau me nā limahana mālama ola nona ka ʻike i nā maʻi naʻau i hānau ʻia.

Address: 506/507, 1st Main Rd, Murugeshpalya, K R Garden, Bengaluru, Karnataka 560075

Hōʻole: He kahua ʻike olakino ʻo ʻAukake a ʻaʻole hōʻike kāna mau pane i ka ʻōlelo aʻoaʻo lapaʻau. E kūkākūkā mau me kahi ʻoihana lapaʻau laikini kokoke iā ʻoe ma mua o ka hana ʻana i nā hoʻololi.

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