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He aha ka Syndroma Eisenmenger? Nā Hōʻailona, Nā Kumu, a me ka Lapaʻau

Created at:1/16/2025

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ʻO ka syndroma Eisenmenger kahi kūlana pilikia o ka naʻau e ulu mai ana i ka wā e hoʻopuka ai kahi puka ma kou naʻau i ka holo ʻana o ke koko ma ke ʻano kūpono ʻole. ʻO kēia kahe hope e hōʻino ai i nā kīʻaha koko o kou māmā, e hoʻopilikia ai i ka hana ʻana o kou naʻau i ke koko.

ʻO ka mea e hoʻokaʻawale ai i kēia kūlana, ʻo ia ka hoʻomaka ʻana ma ke ʻano he pilikia hoʻokahi akā e loli ai i kekahi ma hope o kekahi manawa. Hānau ʻia ʻoe me kahi hemahema o ka naʻau e ʻae ai i ke koko momona a me ke koko ʻole i ka hui ʻana, akā e hoʻomanawanui kou mau māmā i ke kahe koko hou. Eia naʻe, ma hope o nā mahina a i ʻole nā ​​makahiki, e hoʻomaka ana nā kīʻaha koko o kou māmā e kūʻē i kēia kahe kūpono ʻole, e hana ana i kahi ʻano o nā pilikia e hoʻololi ai i ka hana ʻana o kou ʻōnaehana cardiovascular holoʻokoʻa.

He aha nā hōʻailona o ka syndroma Eisenmenger?

ʻO ka hōʻailona i ʻike nui ʻia, ʻo ia kahi kala uliuli i kou ʻili, nā lehelehe, a i ʻole nā ​​kui, i kapa ʻia ʻo cyanosis. Hana kēia no ka mea ʻo ke koko ʻole i ka oxygen e holo ana ma kou kino ma mua o ka hoʻomaʻemaʻe pono ʻia ma o kou mau māmā.

I ka wā e hana nui ai kou naʻau e uku, e ʻike paha ʻoe i nā hōʻailona ʻē aʻe e hiki ke hoʻopilikia i kou mau hana i kēlā me kēia lā:

  • Pōkole o ka hanu, ʻoi aku hoʻi i ka wā o ka hana kino a i ʻole ka hoʻoikaika kino
  • Luhi e like ʻole me kou pae hana
  • ʻEha umauma a i ʻole ka ʻoluʻolu ʻole i ka wā e hoʻoikaika ai
  • Nā ʻōlelo dizziness a i ʻole fainting, ʻoi aku hoʻi i ka wā e kū koke ai
  • Nā palpitations naʻau a i ʻole nā ​​hana naʻau kūpono ʻole
  • ʻEhu i kou mau wāwae, nā kuʻekuʻe wāwae, a i ʻole nā ​​wāwae
  • Clubbing o nā manamana lima a me nā manamana wāwae (e puni a hoʻonui ʻia nā ʻōlelo)

Hoʻomohala pinepine ʻia kēia mau hōʻailona, ​​ʻo ia hoʻi ʻaʻole paha ʻoe e ʻike koke iā lākou. Loaʻa i kou kino kahi mana kupaianaha e hoʻololi ai, akā ma hope o kekahi manawa, e nui loa ka pilikia e uku piha ai.

He aha nā kumu o ka syndroma Eisenmenger?

Hoʻomaka mau ka syndroma Eisenmenger me kahi hemahema naʻau congenital, ʻo ia hoʻi ua hānau ʻia ʻoe me kahi pilikia kūkulu i kou naʻau. ʻO nā hemahema maʻamau e hana ai i nā pilina kūpono ʻole ma waena o nā keʻena o kou naʻau a i ʻole nā ​​kīʻaha koko nui.

Eia nā hemahema naʻau e alakaʻi pinepine ai i ka syndroma Eisenmenger:

  • Ventricular septal defect (VSD) - kahi puka ma waena o nā keʻena haʻahaʻa o ka naʻau
  • Atrial septal defect (ASD) - kahi puka ma waena o nā keʻena kiʻekiʻe o ka naʻau
  • Patent ductus arteriosus (PDA) - i ka wā e wehe ai kahi kīʻaha koko e pono e pani ma hope o ka hānau ʻana
  • Atrioventricular septal defect - nā puka e hoʻopilikia ana i nā keʻena kiʻekiʻe a me nā haʻahaʻa
  • Truncus arteriosus - i ka wā e puka mai ai hoʻokahi kīʻaha nui mai ka naʻau ma mua o ʻelua kīʻaha kaʻawale

ʻO ka mea e hoʻololi ai i kēia mau hemahema i ka syndroma Eisenmenger, ʻo ia ka manawa a me ke kaomi. I ka hoʻomaka, e kahe ke koko mai ka ʻaoʻao hema o kou naʻau (kaomi kiʻekiʻe) i ka ʻaoʻao ʻākau (kaomi haʻahaʻa) ma o kēia mau wehe kūpono ʻole. E hoʻoikaika kēia nui o ke koko i kou mau māmā e hana nui, a ma hope o nā mahina a i ʻole nā ​​makahiki, e mānoanoa a paʻakikī nā kīʻaha koko i kou mau māmā e pale aku iā lākou iho.

Ma hope iho, e kiʻekiʻe loa ke kaomi i kou mau māmā e ʻoi aku ka nui ma mua o ke kaomi ma ka ʻaoʻao hema o kou naʻau. I ka wā e hana ai kēia, e hoʻololi ke kahe koko i ke kuhikuhi, a e hoʻomaka ke koko ʻole i ka oxygen e hui pū me ke koko momona i ka oxygen ma kou kino.

I ka wā e ʻike ai i ke kauka no ka syndroma Eisenmenger?

Pono ʻoe e ʻimi i ka mālama ola kino koke inā ʻike ʻoe i ka pōkole o ka hanu, ʻeha umauma, a i ʻole nā ​​hanana fainting. Hiki i kēia mau hōʻailona ke hōʻike i ka hoʻopilikia ʻana o kou kūlana a i ʻole ke ulu ʻana o nā pilikia e pono ai ka mālama wikiwiki.

He mea nui nō hoʻi ke ʻike i kāu kauka maʻamau inā ʻike ʻoe i nā loli mālie i kou mau pae ikehu a i ʻole ka hoʻomanawanui hoʻoikaika kino. ʻO nā loli liʻiliʻi i ka ʻano o kou manaʻo i nā hana i kēlā me kēia lā e hāʻawi i ka ʻike waiwai e pili ana i ka hoʻokele ʻana o kou naʻau a me kou mau māmā.

Inā loaʻa iā ʻoe kahi hemahema naʻau i ʻike ʻia mai ka hānau ʻana mai, he mea nui ka mālama ʻana i nā hālāwai kūkākūkā maʻamau ʻoiai inā maikaʻi kou manaʻo. Hiki i ka ʻike mua ʻana i nā kaomi māmā e pale aku i ka hoʻomohala piha ʻana o ka syndroma Eisenmenger ma o ka hana ʻoki ʻana i ka manawa kūpono.

He aha nā pilikia o ka syndroma Eisenmenger?

ʻO ka mea nui loa ka hānau ʻia ʻana me kekahi mau ʻano o nā hemahema naʻau, ʻoi aku hoʻi nā mea e hana ai i nā pilina kūpono ʻole ma waena o nā ʻāpana like ʻole o kou ʻōnaehana cardiovascular. Eia naʻe, ʻaʻole nā ​​kānaka a pau me kēia mau hemahema e hoʻomohala i ka syndroma Eisenmenger.

Nui nā mea e hoʻopilikia ai i ka hoʻomohala ʻana o kahi hemahema naʻau i ka syndroma Eisenmenger:

  • Ka nui a me ka wahi o ka hemahema naʻau - ʻae nā hemahema nui i ka nui o ke kahe koko kūpono ʻole
  • Ka makahiki i ʻike ʻia a mālama ʻia ai ka hemahema - pale pinepine ka hoʻoponopono mua i ka holomua
  • Ke olakino holoʻokoʻa i ka wā kamaliʻi a me ka wā ʻōpio
  • Ke loaʻa ʻana o nā hemahema naʻau ʻē aʻe e hoʻonui i ka paʻakikī
  • Ke noho ʻana ma kahi kiʻekiʻe, kahi e hoʻonui ai nā pae oxygen haʻahaʻa i ke kaomi ma ka naʻau a me nā māmā

Hiki i ka Genetics ke pāʻani i kahi kuleana, ʻoiai kekahi mau ʻohana he nui nā hemahema naʻau congenital. Eia kekahi, hiki i kekahi mau kūlana i ka wā hāpai, e like me ka maʻi diabetes makuahine a i ʻole ka hōʻike ʻana i nā lāʻau lapaʻau kikoʻī, ke hoʻonui i ka hiki ke loaʻa nā hemahema naʻau i nā pēpē.

He aha nā pilikia hiki ke loaʻa i ka syndroma Eisenmenger?

Hiki i ka syndroma Eisenmenger ke hoʻopilikia i nā ʻōnaehana kino he nui no ka mea ʻaʻole lawa ke koko momona i ka oxygen e loaʻa ana i kou kino holoʻokoʻa. Ke hoʻomaopopo ʻana i kēia mau pilikia hiki ke kōkua iā ʻoe e ʻike i nā hōʻailona hoʻomaopopo a hana pū me kāu hui mālama ola e pale a mālama paha iā lākou me ka maikaʻi.

ʻO nā pilikia maʻamau loa:

  • Nā abnormalities o ka naʻau (arrhythmias) e hiki ke hoʻokumu i nā palpitations a i ʻole nā ​​hanana naʻau koke
  • Heart failure i ka wā e nāwaliwali ai kou ʻiʻo naʻau mai nā makahiki o ka hana hou
  • Nā clots koko e hiki ke hele i kou mau māmā, lolo, a i ʻole nā ​​mea kino ʻē aʻe
  • Stroke, ʻoi aku hoʻi i nā ʻōpio me kēia kūlana
  • Nā pilikia o ka puʻupaʻa ma muli o ka emi ʻana o ke kahe koko a me ka lawe ʻana i ka oxygen
  • Gout mai nā pae uric acid kiʻekiʻe
  • Gallstones, ka mea e hana pinepine ai i nā poʻe me nā kūlana naʻau lōʻihi

ʻO kekahi mau pilikia liʻiliʻi akā koʻikoʻi, ʻo ia nā pilikia koko ma muli o nā mea hoʻohui koko kūpono ʻole, a me nā maʻi o nā valves naʻau (endocarditis). Hāʻawi ka hāpai keiki i nā pilikia nui no nā wahine me ka syndroma Eisenmenger a pono i ka mālama kūikawā mai kahi hui o nā loea.

ʻOiai paha e manaʻo ʻia kēia papa inoa he nui loa, nui nā kānaka me ka syndroma Eisenmenger e ola ana i nā ola piha ma ka hana pū ʻana me kā lākou hui lapaʻau a me ka hana ʻana i nā hoʻololi nohona kūpono.

Pehea ka hōʻoia ʻana o ka syndroma Eisenmenger?

Hoʻomaka pinepine ka hōʻoia ʻana me kāu kauka e hoʻolohe i kou naʻau a me kou mau māmā, e ʻimi ana i nā leo kikoʻī a me ka nānā ʻana i kou kala ʻili a me kou mau kui. E nīnau nō hoʻi lākou i nā nīnau kikoʻī e pili ana i kou mau hōʻailona a me kekahi moʻolelo o nā pilikia naʻau mai ka hānau ʻana mai.

Nui nā hoʻokolohua e kōkua i ka hōʻoia ʻana i ka hōʻoia a loiloi i ka nui o kou kūlana. Hoʻohana ka echocardiogram i nā nalu kani e hana i nā kiʻi neʻe o kou naʻau, e hōʻike ana i ke kūkulu a me ka hana o nā keʻena a me nā valves o kou naʻau. Hiki i kēia hoʻokolohua ke hōʻike i ka hemahema naʻau mua a ana i nā kaomi i loko o kou naʻau.

E kauoha paha kāu kauka i nā hoʻokolohua hou aku e kiʻi i kahi kiʻi piha o kou olakino cardiovascular. Hoʻopaʻa ka electrocardiogram (ECG) i ka hana uila o kou naʻau a hiki ke ʻike i nā pilikia rhythm a i ʻole nā ​​hōʻailona o ka pilikia. Hōʻike nā X-rays umauma i ka nui a me ke ʻano o kou naʻau a me kou mau māmā, ʻoiai e ana nā hoʻokolohua koko i nā pae oxygen a nānā i nā pilikia ʻē aʻe.

I kekahi mau hihia, pono paha nā hoʻokolohua kūikawā e like me ka catheterization naʻau. Hoʻopili kēia kaʻina hana i ka hoʻopili ʻana i kahi tube lahilahi ma o kou mau kīʻaha koko e ana pololei i nā kaomi i kou naʻau a me kou mau māmā, e hāʻawi ana i ka loiloi pololei loa o ka nui o kou kūlana.

He aha ka lapaʻau no ka syndroma Eisenmenger?

ʻO ka lapaʻau e kaulele ana i ka mālama ʻana i nā hōʻailona a me ka pale ʻana i nā pilikia ma mua o ka hoʻōla ʻana i ke kūlana kumu. Ke hoʻomohala piha ʻia ka syndroma Eisenmenger, ʻo nā loli i nā kīʻaha koko o kou māmā he mau, e hoʻolilo ana i ka hoʻoponopono ʻoki ʻana o ka hemahema naʻau mua i ka pilikia nui.

E kuhikuhi paha kāu hui lapaʻau i nā lāʻau lapaʻau e kōkua i kou naʻau e hana me ka maikaʻi a hoʻemi i nā hōʻailona. Hiki i kēia ke komo i nā lāʻau lapaʻau e hoʻomaha i nā kīʻaha koko i kou mau māmā, kōkua i kou naʻau e pā mai me ka maikaʻi, a pale i nā clots koko mai ka hana ʻana.

No nā kānaka me nā hōʻailona koʻikoʻi, hiki ke noʻonoʻo ʻia nā lapaʻau holomua:

  • Oxygen therapy e hoʻonui i ka nui o ka oxygen i kou koko
  • Nā lāʻau lapaʻau i hoʻolālā ʻia e mālama i ka hypertension pulmonary
  • Nā kaʻina hana e wehe i nā sela koko ʻulaʻula keu inā hana nui kou kino
  • Heart-lung transplantation i nā hihia i koho pono ʻia

He mea nui ka nānā maʻamau no ka mea hiki ke loli kou kūlana i ka manawa. E hoʻoponopono kāu hui mālama ola i nā lapaʻau ma muli o kou manaʻo a me ka mea e hōʻike ai kāu mau hoʻokolohua, e pahuhopu mau ana e kōkua iā ʻoe e mālama i ka maikaʻi o ke ola.

Pehea e mālama ai i ka syndroma Eisenmenger ma ka home?

ʻO ke ola maikaʻi me ka syndroma Eisenmenger e komo pū ana i ka hana ʻana i nā koho noʻonoʻo e pili ana i kou mau hana i kēlā me kēia lā ʻoiai e noho ana i ka hana e like me ka palekana. ʻO ke kī, ʻo ia ka loaʻa ʻana o ke kaulike kūpono ma waena o ka mālama ʻana i kou kūlana a me ka pale ʻana i ka hoʻoikaika nui e hiki ke hoʻopilikia i kou mau hōʻailona.

Pono e mālie ka hana kino a ma muli o kou manaʻo i kēlā me kēia lā. Hiki i ka hele wāwae, ka ʻauʻau māmā, a i ʻole ka hoʻolōʻihi māmā ke kōkua i ka mālama ʻana i kou ikaika me ka ʻole o ka hoʻoikaika nui i kou naʻau a me kou mau māmā. E makaʻala i nā hōʻailona o kou kino a hoʻomaha i ka wā e pōkole ai kou hanu a luhi.

Hiki i kou papa hana i kēlā me kēia lā ke hoʻolilo i kahi ʻokoʻa nui i kou manaʻo. E noho wai maikaʻi akā e pale i ka nui o ka wai inā ua kuhikuhi kāu kauka i nā palena. E ʻai i ka meaʻai kaulike momona i ka hao, ʻoiai pono paha kou kino i ke kākoʻo hou aku e hana i nā sela koko ʻulaʻula olakino. E loaʻa i ka nui o ka hoʻomaha, ʻoiai he mea maʻamau ka luhi me kēia kūlana.

He mea nui ke pale aku iā ʻoe iho mai nā maʻi, ʻoi aku hoʻi nā maʻi hanu e hiki ke hoʻonui i ke kaomi ma kou naʻau a me kou mau māmā. E holoi pinepine i kou mau lima, e noho hou i nā lāʻau lapaʻau, a e pale i nā wahi piha i ka wā o ka wā maʻi maʻi.

Pehea ʻoe e hoʻomākaukau ai no kāu hālāwai kauka?

Ma mua o kāu hālāwai, e lawe i ka manawa e hahai ai i kou mau hōʻailona a me nā pae ikehu no kekahi mau lā a i ʻole nā ​​hebedoma. E hoʻomaopopo i nā hana e hoʻolilo iā ʻoe i ka pōkole o ka hanu, i ka wā e ʻike ai ʻoe i ka ʻeha umauma, a pehea kou maikaʻi o ka hiamoe. E kōkua kēia ʻike i kāu kauka e hoʻomaopopo i ke ʻano o kou kūlana i ka hoʻopilikia ʻana i kou ola i kēlā me kēia lā.

E lawe mai i kahi papa inoa piha o nā lāʻau lapaʻau āpau āu e lawe nei, me nā lāʻau lapaʻau ma luna o ka counter a me nā mea hoʻohui. Hiki i kekahi mau lāʻau lapaʻau ke launa pū me nā kūlana naʻau a i ʻole ke komo pū me nā lapaʻau, no laila pono i kāu kauka ke ʻike i nā mea āpau āu e hoʻohana nei.

E kākau i nā nīnau āu e makemake ai e nīnau ma mua o kou poina ʻana iā lākou i kēia manawa. E noʻonoʻo e nīnau e pili ana i nā hōʻailona hou āu i ʻike ai, inā kūpono kou pae hana, a he aha nā hōʻailona hoʻomaopopo e pono ai ke kāhea koke aku. Mai kānalua e noi i ka wehewehe inā nā huaʻōlelo lapaʻau a i ʻole nā ​​koho lapaʻau e like me ka huikau.

Inā hiki, e lawe mai i kahi lālā ʻohana a i ʻole hoaaloha i kāu hālāwai. Hiki iā lākou ke kōkua iā ʻoe e hoʻomanaʻo i ka ʻike nui a hāʻawi i ke kākoʻo manaʻo i ka wā o nā kūkākūkā e pili ana i kāu hoʻolālā mālama.

He aha ka mea nui e pili ana i ka syndroma Eisenmenger?

ʻO ka syndroma Eisenmenger kahi kūlana paʻakikī e ulu ana i ka manawa mai kahi hemahema naʻau kumu, akā me ka mālama lapaʻau kūpono a me nā hoʻololi nohona, nui nā kānaka e ola ana i nā ola ʻano a me ka hana. ʻO ka mea nui loa e hoʻomanaʻo ai, ʻaʻole ʻoe wale nō i ka mālama ʻana i kēia kūlana.

Hana ka ʻike mua ʻana a me ka mālama lapaʻau mau i kahi ʻokoʻa nui i nā hopena. Inā loaʻa iā ʻoe kahi hemahema naʻau i ʻike ʻia a i ʻike paha ʻoe i nā hōʻailona e like me ka pōkole o ka hanu a i ʻole nā ​​loli kala ʻili, mai hoʻokaʻulua i ka ʻimi ʻana i ka loiloi lapaʻau. Hiki i nā lapaʻau hou ke hoʻomaikaʻi nui i ka maikaʻi o ke ola a kōkua i ka pale ʻana i nā pilikia.

ʻOiai pono ka syndroma Eisenmenger i ka mālama ola lōʻihi, ke hoʻomau nei nā holomua i ka hoʻomaopopo a me ka lapaʻau e hāʻawi i ka manaʻolana. E hana pū me kāu hui mālama ola, e noho ʻike e pili ana i kou kūlana, a mai kānalua e kākoʻo iā ʻoe iho i ka wā e loaʻa ai iā ʻoe nā hopohopo a i ʻole nā ​​nīnau.

Nā nīnau i nīnau pinepine ʻia e pili ana i ka syndroma Eisenmenger

Hiki ke pale ʻia ka syndroma Eisenmenger?

Hiki ke pale ʻia ka syndroma Eisenmenger ma ka hoʻoponopono ʻana i ka hemahema naʻau kumu i ka wā kamaliʻi, maʻamau i ka wā pēpē a i ʻole ka wā kamaliʻi mua. Inā loaʻa iā ʻoe kahi keiki me kahi hemahema naʻau, he mea nui ka hahai ʻana i nā ʻōlelo a kāu kauka naʻau pediatric no ka manawa o ka hoʻoponopono ʻoki ʻana. Ke hoʻomohala piha ʻia ka syndroma, eia naʻe, ʻo nā loli i nā kīʻaha koko māmā he mau.

He mea hoʻoilina anei ka syndroma Eisenmenger?

Hiki i nā hemahema naʻau kumu e alakaʻi ai i ka syndroma Eisenmenger ke holo i nā ʻohana, akā ʻo ka hapa nui o nā hihia e hana kūpono ʻole me ka ʻole o kahi ʻano genetic maopopo. Inā loaʻa iā ʻoe ka syndroma Eisenmenger a i ʻole kahi hemahema naʻau congenital, hiki i ka ʻōlelo aʻo genetic ke kōkua iā ʻoe e hoʻomaopopo i nā pilikia no nā keiki e hiki mai ana a kūkākūkā i nā koho no ka hoʻolālā ʻohana.

Hiki i nā kānaka me ka syndroma Eisenmenger ke loaʻa nā keiki?

Hāʻawi ka hāpai keiki i nā pilikia nui no nā wahine me ka syndroma Eisenmenger a ʻaʻole ia i manaʻo ʻia ma muli o nā nui o nā pilikia no ka makuahine a me ke pēpē. Eia naʻe, ʻokoʻa kēlā me kēia kūlana, a inā ke noʻonoʻo nei ʻoe i ka hāpai keiki, he mea nui ke kūkākūkā pono ʻana me kahi hui o nā loea me kahi kauka naʻau a me kahi loea lapaʻau makuahine-pēpē.

Pehea ka lōʻihi o ka ola ʻana o nā kānaka me ka syndroma Eisenmenger?

Hoʻololi nui ka lōʻihi o ke ola ma muli o ka nui o ke kūlana, ke olakino holoʻokoʻa, a me ke komo ʻana i ka mālama lapaʻau kūpono. Nui nā kānaka me ka syndroma Eisenmenger e ola ana i ko lākou mau makahiki 30, 40, a ma mua, ʻoi aku hoʻi me nā lapaʻau hou. Hiki i ka mālama lapaʻau maʻamau a me nā hoʻololi nohona ke hoʻomaikaʻi nui i ka maikaʻi o ke ola a me ka lōʻihi.

Aia kekahi mau hana e pono ke pale loa ʻia?

Pono e pale ʻia nā hana kiʻekiʻe, nā hana hoʻoikaika kino nui loa, a me nā hana me ka pilikia o ka dehydration. ʻO ka huakaʻi lewa he mea hiki pinepine akā pono paha nā palekana kūikawā e like me ka oxygen hou. Hiki i kāu kauka ke hāʻawi i nā kuhikuhi kikoʻī ma muli o kou kūlana pilikino a kōkua iā ʻoe e hoʻoholo i nā pae hana palekana e mālama i kou olakino ʻoiai e ʻae iā ʻoe e hauʻoli i ke ola.

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