He aha ka Fuchs' Dystrophy? Nā Hōʻailona, Nā Kumu, a me ka Lapaʻau

ʻO ka Fuchs' dystrophy kahi maʻi maka e holomua ana e pili ana i ka cornea, ʻo ia ka papa mua maopopo o kou maka. Hana ia ke pau nā hana o nā pūnaewele kūikawā i kapa ʻia ʻo nā endothelial cells ma ka hope o kou cornea, e hoʻoulu ai i ka wai e hōʻiliʻili a hoʻolilo i kou ʻike maka i ʻālohilohi a palupalu paha.

Hoʻomaka maʻamau kēia maʻi i nā makahiki he nui, pinepine ma kou mau makahiki 40 a 50 paha. ʻOiai hiki ke hopohopo, nui nā kānaka me ka Fuchs' dystrophy e mālama i ka ʻike maka maikaʻi no nā makahiki me ka mālama pono a me nā koho lapaʻau i loaʻa ke pono.

He aha nā hōʻailona o ka Fuchs' dystrophy?

Hoʻomaka pinepine nā hōʻailona mua o ka Fuchs' dystrophy i kahi mālie loa ʻaʻole paha ʻoe e ʻike koke. Hiki i kou ʻike maka ke ʻālohilohi iki i ke kakahiaka, a laila maopopo i ka lā.

E hele kākou i nā hōʻailona āu e ʻike ai, e hoʻomaka ana me nā mea maʻamau loa:

• ʻIke maka palupalu a ʻālohilohi paha, ʻoi aku hoʻi i ke ala ʻana
• Mālamalama a me ka maʻalahi i nā kukui mālamalama
• ʻIke ʻana i nā halo a puni nā kukui, ʻoi aku hoʻi i ka pō
• ʻIke maka ʻeha a ʻoluʻolu ʻole paha
• ʻIke maka e loli ana i ka lā
• Paʻakikī ke ʻike maopopo i nā kūlana kukui haʻahaʻa

I ka holomua ʻana o ka maʻi, hiki iā ʻoe ke ʻike i kou ʻike maka e noho palupalu ana i ka lā. Loaʻa i kekahi poʻe nā ʻeha liʻiliʻi ma ka ʻili o ko lākou maka, ʻoiai ke hana nei kēia i nā pae holomua.

I nā hihia kakaʻikahi, hiki i ka Fuchs' dystrophy nui ke alakaʻi i ka nalowale nui o ka ʻike maka e pili ana i nā hana o kēlā me kēia lā e like me ka heluhelu a me ke kaʻa ʻana. ʻO ka ʻoiaʻiʻo maikaʻi, me nā nānā maka maʻamau, hiki i kāu kauka ke nānā i nā loli a paipai i ka lapaʻau ma mua o ka nui o nā hōʻailona.

He aha nā ʻano o ka Fuchs' dystrophy?

Hoʻokaʻawale ʻia ka Fuchs' dystrophy i ʻelua ʻano nui ma muli o ka hoʻomaka ʻana a me ke kumu. Ke hoʻomaopopo ʻoe i ke ʻano āu e loaʻa ai, e kōkua ia i kāu kauka e hoʻolālā i ke ala maikaʻi loa no kou mālama.

ʻO ke ʻano hoʻomaka mua, i kapa ʻia ʻo Fuchs' dystrophy 1, e ʻike pinepine ʻia ma mua o 40 mau makahiki. Hoʻoili pinepine ʻia kēia ʻano, ʻo ia hoʻi, e holo ana i nā ʻohana ma o nā loli genetic kikoʻī. Loaʻa pinepine i nā kānaka me kēia ʻano kahi moʻolelo ʻohana o ka maʻi.

ʻO ke ʻano hoʻomaka hope, i ʻike ʻia ʻo Fuchs' dystrophy 2, ʻoi aku ka maʻamau a hoʻomaka maʻamau ma hope o 40 mau makahiki. Hiki i kēia ʻano ke loaʻa kekahi ʻāpana genetic, akā he mau kumu kūlohelohe a me ka ʻelemakule kūlohelohe ke pāʻani i nā kuleana nui i kona hoʻomohala ʻana.

Hiki i kāu kauka maka ke hoʻoholo i ke ʻano āu e loaʻa ai ma o ka nānā pono a ma ka nīnau ʻana e pili ana i kou moʻolelo ʻohana. E kōkua kēia ʻike i ka wānana ʻana i ka holomua o ka maʻi a e alakaʻi i nā hoʻoholo lapaʻau.

He aha ke kumu o ka Fuchs' dystrophy?

Hana ʻia ka Fuchs' dystrophy ke nalowale nā ​​endothelial cells i kou cornea i ko lākou hiki ke hoʻopuka i ka wai nui mai ka cornea. E noʻonoʻo i kēia mau pūnaewele e like me nā pump liʻiliʻi e mālama i kou cornea i ka maopopo a me ka wai pono.

Nui nā kumu e hiki ke hoʻopili i kēia hōʻino pūnaewele i ka manawa:

• Nā mutations genetic i hoʻoili ʻia ma o nā ʻohana
• Ke kaʻina hana ʻelemakule kūlohelohe e hoʻopilikia i ka hana pūnaewele
• Nā hōʻeha maka a i ʻole nā ​​​​kaʻina hana ma mua
• Kekahi mau maʻi maka inflammatory
• Ka lōʻihi o ka hoʻolaha ʻana i ka ultraviolet light

I nā hihia he nui, ʻaʻole maopopo ke kumu pololei, a he hui pū ʻana paha o ka predisposition genetic a me nā kumu kūlohelohe e hana pū ana. ʻO ka mea a mākou e ʻike ai, ke hōʻino ʻia kēia mau pūnaewele, ʻaʻole hiki iā lākou ke hoʻoponopono hou a hoʻoponopono iā lākou iho.

Ua ʻike nā mea noiʻi i nā gene he nui e pili ana i ka Fuchs' dystrophy, ʻoi aku hoʻi i nā ʻohana kahi i pilikia ai nā lālā he nui. Eia naʻe, ʻaʻole hōʻoia ka loaʻa ʻana o kēia mau loli genetic e hoʻomohala ʻoe i ka maʻi.

I ka wā e ʻike ai i ke kauka no ka Fuchs' dystrophy?

Pono ʻoe e hoʻonohonoho i kahi nānā maka inā ʻike ʻoe i nā loli ʻike maka mau, ʻoi aku hoʻi inā ʻike ʻoe i kou ʻike maka e ʻālohilohi mau ana i ke kakahiaka a i ʻole ʻoe e ʻike i ka nui o ka maʻalahi i ka mālamalama. ʻAe ka ʻike mua i ka nānā ʻana a me ka hoʻolālā lapaʻau maikaʻi.

E hoʻokaʻaʻike koke i kāu kauka maka inā ʻike ʻoe i nā loli ʻike maka koke, ʻeha nui o ka maka, a i ʻole inā hoʻomohala nā blisters ma ka ʻili o kou maka. Hiki i kēia mau hōʻailona ke hōʻike i ka holomua o ka maʻi a i ʻole nā ​​​​pilikia e hoʻomohala ana.

ʻOiai inā ʻike ʻia kou mau hōʻailona he māmā, e lilo nā nānā maka maʻamau i mea nui loa ke loaʻa iā ʻoe ka Fuchs' dystrophy. Hiki i kāu kauka ke hahai i nā loli i kou cornea a paipai i ka lapaʻau ma mua o ka pilikia nui o nā hōʻailona i kou ola o kēlā me kēia lā.

Inā loaʻa iā ʻoe kahi moʻolelo ʻohana o ka Fuchs' dystrophy, e noʻonoʻo e kūkākūkā me kāu kauka maka i nā nānā maʻamau. Hiki iā lākou ke paipai i ka nānā pinepine a i ʻole ka ʻōlelo aʻo genetic e kōkua iā ʻoe e hoʻomaopopo i kou pilikia.

He aha nā kumu pilikia no ka Fuchs' dystrophy?

Nui nā kumu e hiki ke hoʻonui i kou hiki ke hoʻomohala i ka Fuchs' dystrophy, ʻoiai ʻaʻole ʻo ka loaʻa ʻana o kēia mau kumu pilikia e ʻōlelo ai e loaʻa maoli iā ʻoe ka maʻi. Ke hoʻomaopopo ʻoe i kou pilikia, e kōkua ia iā ʻoe e noho i mua e pili ana i ke olakino maka.

Eia nā kumu pilikia nui e makaʻala ai:

• Moʻolelo ʻohana o ka Fuchs' dystrophy
• Ke ʻoi aku ma mua o 50 mau makahiki, ʻoi aku hoʻi no nā wāhine
• Wahine wahine (ʻoi aku ka nui o nā wāhine ma mua o nā kāne)
• Hōʻeha maka a i ʻole kaʻina hana ma mua
• Kekahi mau kūlana autoimmune
• Ka hoʻohana lōʻihi o kekahi mau lāʻau lapaʻau

ʻO ka makahiki kekahi o nā kumu pilikia ikaika loa, me ka nui o nā hihia e hoʻomohala ana ma hope o 50 mau makahiki. ʻOi aku ka nui o nā wāhine ma mua o nā kāne e hoʻomohala i kēia maʻi, ʻoiai ʻaʻole maopopo loa i nā mea noiʻi ke kumu o kēia ʻokoʻa.

I nā hihia kakaʻikahi, hiki i kekahi mau lāʻau lapaʻau a i ʻole nā ​​​​kūlana lapaʻau e hoʻopilikia i ka ʻōnaehana pale kino ke hoʻopili i ka hōʻino ʻana i nā pūnaewele cornea. Hiki i kāu kauka ke kōkua iā ʻoe e hoʻomaopopo i ke ʻano o kāu mau kumu pilikia pilikino e hiki ke hoʻopilikia i kou olakino maka.

He aha nā pilikia hiki ke loaʻa o ka Fuchs' dystrophy?

ʻIke ka hapa nui o nā kānaka me ka Fuchs' dystrophy i ka holomua mālie me nā hōʻailona hiki ke mālama ʻia no nā makahiki he nui. Eia naʻe, ke hoʻomaopopo ʻoe i nā pilikia hiki ke loaʻa, e kōkua ia iā ʻoe e ʻike i ka wā e ʻimi ai i ka mālama hou aku.

ʻO nā pilikia maʻamau loa e komo pū ana:

• Ka pupu ʻana o ka cornea e hoʻoulu ai i nā pilikia ʻike maka mau
• Nā blisters cornea ʻeha e hiki ke haki
• Hoʻonui ʻia ka pilikia o ka maʻi inā haki nā blisters
• Paʻakikī me ke kaʻa ʻana i ka pō ma muli o ka mālamalama
• Nā pilikia me nā hana o kēlā me kēia lā e like me ka heluhelu

I nā hihia holomua, hiki i ka pupu nui o ka cornea ke alakaʻi i ka nalowale nui o ka ʻike maka e hoʻopilikia i kou maikaʻi o ke ola. Loaʻa i kekahi poʻe nā erosions cornea hou, kahi e haki ai ka papa ʻili o ka cornea i nā manawa he nui.

Kakaʻikahi, hiki i ka Fuchs' dystrophy holomua i mālama ʻole ʻia ke hopena i ka scarring cornea a i ʻole ka nalowale mau o ka ʻike maka. Eia naʻe, hiki ke pale ʻia kēia mau pilikia nui me ka nānā pono a me ka lapaʻau kūpono.

ʻO ka nūhou hoʻoikaika, hiki ke mālama maikaʻi ʻia ka hapa nui o nā pilikia me ka lapaʻau kūpono, a mālama ka nui o nā kānaka i ka ʻike maka hana maikaʻi i ko lākou ola.

Pehea e ʻike ʻia ai ka Fuchs' dystrophy?

ʻO ka ʻike ʻana i ka Fuchs' dystrophy e komo pū ana i kahi nānā maka piha kahi e nānā ai kāu kauka i ke olakino a me ka hana o nā pūnaewele cornea. He pololei a ʻoluʻolu ka hana.

E hoʻomaka kāu kauka maka ma ka nīnau ʻana e pili ana i kou mau hōʻailona a me kou moʻolelo ʻohana, a laila e hana i kekahi mau hoʻokolohua kūikawā. E nānā lākou i kou cornea ma lalo o ka hoʻonui kiʻekiʻe e ʻimi i nā loli hiʻohiʻona i nā endothelial cells.

ʻO nā hoʻokolohua diagnostic nui e komo pū ana i ke ana ʻana i ka mānoanoa o ka cornea, ka helu ʻana i nā endothelial cells, a me ka nānā ʻana i ka hana maikaʻi o kēia mau pūnaewele. Hiki i kāu kauka ke hoʻokolohua i kou ʻike maka i nā manawa like ʻole o ka lā ʻoiai e loli pinepine nā hōʻailona.

I kekahi mau hihia, kōkua nā hoʻokolohua kiʻi hou aku e loiloi i ka nui a me ka hoʻolālā lapaʻau. Hana ʻia kēia mau hoʻokolohua a pau ma ke keʻena a hāʻawi i nā hopena koke e alakaʻi i kāu hoʻolālā mālama.

He aha ka lapaʻau no ka Fuchs' dystrophy?

ʻO ka lapaʻau no ka Fuchs' dystrophy e kau nui ana i ka mālama ʻana i nā hōʻailona a me ka mālama ʻana i kou ʻike maka, me nā koho mai nā kulu maka maʻalahi a i nā kaʻina hana ʻokiʻoki ma muli o ka nui o kou maʻi.

No nā hōʻailona māmā a waena paha, hiki i kāu kauka ke paipai i:

• Nā kulu saline hypertonic a i ʻole nā ​​​​ointments e hoʻemi i ka pupu ʻana o ka cornea
• Ke hoʻomaloʻo ʻana i kou maka i kēlā me kēia kakahiaka e kōkua i ka maopopo ʻana o ka ʻike maka
• Ke komo ʻana i nā aniani lā e hoʻemi i ka maʻalahi o ka mālamalama
• Ke hoʻohana ʻana i nā waimaka artificial no ka ʻoluʻolu
• Ke pale ʻana i ka hamo ʻana i kou mau maka e pale aku i ka hōʻino hou aku

Ke lawa ʻole nā ​​​​lapaʻau mālama, e loaʻa nā koho ʻokiʻoki. ʻO ka hana maʻamau loa ka corneal transplantation, kahi e pani ʻia ai ka ʻiʻo i hōʻino ʻia me ka ʻiʻo mea hāʻawi olakino.

Hoʻomaikaʻi nā ʻenehana hou e like me DSEK a i ʻole DMEK i ka papa pūnaewele i hōʻino ʻia ma mua o ka cornea holoʻokoʻa, e alakaʻi ana i ka hoʻōla wikiwiki a me nā hopena maikaʻi. Loaʻa i kēia mau kaʻina hana nā helu holomua kiʻekiʻe a hiki ke hoʻomaikaʻi nui i ka ʻike maka.

E hana pū kāu kauka me ʻoe e hoʻoholo i ka manawa maikaʻi loa no kekahi hana ʻokiʻoki, e kaulike ana i nā pono me kou maikaʻi o ke ola i kēia manawa a me nā pono ʻike maka.

Pehea e mālama ai i ka Fuchs' dystrophy ma ka home?

Nui nā hana maʻalahi e hiki ke kōkua iā ʻoe e mālama i nā hōʻailona a pale i kou olakino maka ma waena o nā kipa kauka. Hana maikaʻi kēia mau ala ke hui pū ʻia me kāu mau lapaʻau i kuhikuhi ʻia.

E hoʻomaka i kou lā ma ka hoʻomaloʻo mālie i kou maka me ka ea anuanu no kekahi mau minuke. E kōkua kēia i ka hoʻoheheʻe ʻana i ka wai nui mai kou cornea a hiki ke hoʻomaikaʻi i ka maopopo o ka ʻike maka kakahiaka.

E pale i kou mau maka mai nā kukui mālamalama a me ka mālamalama ma ka komo ʻana i nā aniani lā maikaʻi ma waho a me ka hoʻohana ʻana i nā kukui palupalu i loko ke hiki. E hoʻemi kēia i ka ʻoluʻolu ʻole a e kōkua iā ʻoe e ʻike maopopo aku.

E hoʻohana i kāu mau kulu maka i kuhikuhi ʻia e like me ke kuhikuhi ʻia, a mālama i nā waimaka artificial no ka ʻoluʻolu hou aku i ka lā. ʻO ka kūpaʻa me nā lāʻau lapaʻau e kōkua i ka mālama ʻana i ka ʻike maka paʻa.

E pale i ka hamo ʻana i kou mau maka, ʻoiai inā ʻike ʻia lākou he huhū, ʻoiai hiki i kēia ke hoʻopilikia i ka hōʻino ʻana o ka cornea. Ma kahi o kēia, e hoʻohana i nā compresses anuanu a i ʻole nā ​​​​waimaka artificial preservative-free no ka hoʻomaha.

Pehea ʻoe e hoʻomākaukau ai no kāu ʻaha kūkā kauka?

Ke hoʻomākaukau nei no kāu nānā maka e kōkua i ka hōʻoia ʻana e loaʻa iā ʻoe ka mālama piha loa a loaʻa nā pane i kāu mau nīnau a pau. He lōʻihi ka hoʻomākaukau iki.

E kākau i kou mau hōʻailona, ​​e komo pū ana i ka wā e hana ai, pehea ka lōʻihi o ko lākou mau, a he aha ka mea e hoʻomaikaʻi ai a i ʻole e ʻino ai. E hoʻomaopopo inā loli kou ʻike maka i ka lā a i ʻole i nā kūlana kukui like ʻole.

E lawe mai i kahi papa inoa piha o nā lāʻau lapaʻau, nā mea hoʻohui, a me nā kulu maka āu e hoʻohana nei. E komo pū me nā huahana kuhikuhi a me nā mea kūʻai aku, ʻoiai hiki i kekahi ke hoʻopilikia i kou olakino maka.

E hōʻiliʻili i ka ʻike e pili ana i ka moʻolelo olakino maka o kou ʻohana, ʻoi aku hoʻi inā loaʻa i nā hoahānau nā pilikia cornea a i ʻole nā ​​​​pilikia ʻike maka. E kōkua kēia ʻike i kāu kauka e loiloi i kou mau kumu pilikia.

E hoʻomākaukau i kahi papa inoa o nā nīnau e pili ana i kou maʻi, nā koho lapaʻau, a me ka mea e manaʻo ai e hele mai. Mai kānalua e nīnau e pili ana i kekahi mea e hopohopo ai ʻoe.

He aha ka lawe ʻana i ka Fuchs' dystrophy?

ʻO ka Fuchs' dystrophy kahi maʻi hiki ke mālama ʻia e holomua mālie ana i ka hapa nui o nā kānaka, e hāʻawi ana iā ʻoe a me kāu kauka i ka manawa e hoʻolālā ai i nā hoʻolālā lapaʻau maikaʻi. ʻOiai e pono ai ka nānā mau, mālama ka nui o nā kānaka i ka ʻike maka maikaʻi a me ke ola maikaʻi no nā makahiki.

ʻO ka mea nui loa āu e hiki ke hana ai, ʻo ia ke noho pili me kāu hui mālama maka a hahai i kā lākou mau manaʻo no ka nānā ʻana a me ka lapaʻau. Hoʻopau pinepine ka hoʻoponopono mua i nā pilikia koʻikoʻi a mālama i kou ʻike maka lōʻihi.

E hoʻomanaʻo e hoʻomaikaʻi mau nā koho lapaʻau, a ua lilo nā ʻenehana ʻokiʻoki i mea ʻoi aku ka maikaʻi a me ka holomua. Me ka mālama pono, hiki i ka hapa nui o nā kānaka me ka Fuchs' dystrophy ke hoʻomau i ka hana ʻana i nā hana ā lākou e hauʻoli ai.

E noho manaʻolana a i mua e pili ana i kou olakino maka. Hoʻomaopopo maikaʻi ʻia kēia maʻi e nā poʻe loea mālama maka, a loaʻa nā lapaʻau maikaʻi ke pono ʻoe iā lākou.

Nā nīnau i nīnau pinepine ʻia e pili ana i ka Fuchs' dystrophy

He hereditary anei ka Fuchs' dystrophy?

ʻAe, hiki i ka Fuchs' dystrophy ke holo i nā ʻohana, ʻoi aku hoʻi ke ʻano hoʻomaka mua e ʻike ʻia ma mua o 40 mau makahiki. Eia naʻe, ʻaʻole hōʻoia ka loaʻa ʻana o kahi moʻolelo ʻohana e hoʻomohala ʻoe i ka maʻi. Hana pū kekahi mau hihia me ka ʻole o kahi moʻolelo ʻohana, ʻoi aku hoʻi ke ʻano hoʻomaka hope ʻoi aku ka maʻamau.

E makaʻu anei wau mai ka Fuchs' dystrophy?

He kakaʻikahi loa ka makapō piha mai ka Fuchs' dystrophy. ʻOiai hiki i ka maʻi ke hoʻoulu i nā pilikia ʻike maka nui inā waiho ʻia me ka mālama ʻole, hiki i nā lapaʻau hou e like me ka corneal transplantation ke hoʻihoʻi i ka ʻike maka maikaʻi i ka hapa nui o nā hihia. Me ka nānā pono a me ka mālama, mālama ka hapa nui o nā kānaka i ka ʻike maka hana i ko lākou ola.

Pehea ka wikiwiki o ka holomua o ka Fuchs' dystrophy?

Hoʻomaka maʻamau ka Fuchs' dystrophy i nā makahiki he nui a i ʻole nā ​​​​decades. Loaʻa i kekahi poʻe nā hōʻailona māmā e noho paʻa no nā makahiki, ʻoiai hiki i kekahi ke ʻike i nā loli ʻike ʻia. He nui ka ʻokoʻa o ka holomua ma waena o nā kānaka, ʻo ia ke kumu e nui ai ka nānā mau.

Hiki i nā loli ʻano ola ke hoʻolohi i ka Fuchs' dystrophy?

ʻOiai ʻaʻole hiki iā ʻoe ke hoʻopau i ka holomua o ka Fuchs' dystrophy, hiki i kekahi mau ʻano ke kōkua i ka pale ʻana i kou olakino maka. E komo pū kēia me ke komo ʻana i ka pale UV, ke pale ʻana i ka hōʻeha maka, ke mālama ʻana i nā kūlana olakino ʻē aʻe, a me ka hahai ʻana i kāu hoʻolālā lapaʻau mau. Eia naʻe, hoʻoholo nui ʻia ka holomua o ka maʻi e nā kumu genetic a me nā mea ola.

He aha ka helu holomua o ka corneal transplant no ka Fuchs' dystrophy?

Loaʻa i ka corneal transplantation no ka Fuchs' dystrophy nā helu holomua maikaʻi loa, me ka ʻoi aku ma mua o 90% o nā kānaka e loaʻa ana ka hoʻomaikaʻi nui ʻana o ka ʻike maka. Loaʻa i nā ʻenehana hou e like me DSEK a me DMEK nā helu holomua ʻoi aku ka kiʻekiʻe a me nā manawa hoʻōla wikiwiki ma mua o nā transplants holoʻokoʻa maʻamau. Hoʻi ka hapa nui o nā kānaka i ko lākou mau hana maʻamau i loko o kekahi mau mahina.