He aha ka maʻi Hirschsprung? Nā hōʻailona, nā kumu, a me ka mālama

ʻO ka maʻi Hirschsprung he kīnā hānau e pili ana i ka ʻōpū nui (colon) a hiki ke paʻakikī i nā pēpē ke komo i ka ʻōpū. Hana kēia kūlana ke nele nā ​​kiko nerve e kōkua ana i nā ʻōpū e kipaku i ka ʻōpala mai nā ʻāpana o ka colon.

Ma kahi o 1 i 5,000 mau pēpē i hānau ʻia me kēia kūlana, a ʻoi aku ka nui ma nā keikikāne ma mua o nā kaikamahine. ʻO ka mea maikaʻi, me ka mālama kūpono, hiki i nā keiki me ka maʻi Hirschsprung ke ola i ke ola olakino a maʻamau.

He aha ka maʻi Hirschsprung?

Hana ʻia ka maʻi Hirschsprung ke ulu ʻole nā ​​kiko nerve i kapa ʻia ʻo nā sela ganglion i ka paia o ka colon. Hōʻike kēia mau sela kūikawā i nā ʻiʻo ʻōpū i ka wā e hoʻomaha ai a hoʻoikaika ai e hoʻoneʻe i ka ʻōpala.

Me ka nele o kēia mau kiko nerve, ʻaʻole hiki i ka ʻāpana o ka colon i pilikia ke kipaku i ka ʻōpala maʻamau. E noʻonoʻo e like me ka hose māla me ka kink i loko - ua hoʻopaʻa ʻia nā mea a pau ma hope o ka wahi i ālai ʻia.

Hoʻomaka mau ka kūlana ma ka anus a hoʻolōʻihi i luna i ka colon. I ka hapanui o nā hihia, pili wale ka ʻāpana haʻahaʻa o ka colon, akā i kekahi manawa hiki ke komo i nā ʻāpana lōʻihi o ka ʻōpū.

He aha nā hōʻailona o ka maʻi Hirschsprung?

ʻIke pinepine ʻia nā hōʻailona o ka maʻi Hirschsprung i nā hebedoma mua o ke ola, ʻoiai i kekahi manawa ʻaʻole ʻike ʻia lākou a hiki i ka wā ma hope i ka wā kamaliʻi. ʻOkoʻa kēlā me kēia pēpē, akā aia kekahi mau hōʻailona maʻamau e nānā ai.

I nā pēpē hou, ʻo nā hōʻailona ʻōlelo nui loa:

• ʻAʻole hala ka ʻōpala mua (meconium) i loko o 48 mau hola ma hope o ka hānau ʻana
• ʻŌmaʻomaʻo a ʻeleʻele paha ka luaʻi
• ʻŌpū pehu e ʻike ʻia he paʻakikī
• Ke ea akā ʻaʻohe neʻe ʻana o ka ʻōpū
• Paʻakikī ka hānai ʻana a me ka emi ʻana o ke kaupaona
• Nā neʻe ʻana o ka ʻōpū ikaika ma hope o ke komo ʻana o ka manamana lima a i ʻole ka thermometer i loko o ka rectum

ʻO kēia mau hōʻailona mua e hiki mai ana ma muli o ka hiki ʻole ke neʻe aku o ka ʻōpala ma o ka ʻāpana o ka kolona i pilikia. ʻO ka hōʻiliʻili ʻana e hoʻoulu i ka kaomi ʻoluʻolu ʻole a pale i ka hānai maʻamau a me ka ulu ʻana.

I nā pēpē a me nā keiki kahiko, e ʻike paha ʻoe i:

• Ka constipation mau loa ʻaʻole e hoʻomaikaʻi me nā lāʻau lapaʻau maʻamau
• Ka nele o ka loaʻa kaumaha ma ka wikiwiki maʻamau
• Ka luhi a me ka nele o ka ikaika
• Ka ʻōpū pehu
• Nā neʻe ʻōpū nui, pinepine ʻole

ʻAʻole paha e hōʻike kekahi mau keiki me nā ʻano māmā o ke kūlana i nā hōʻailona a hiki i ko lākou lilo ʻana i nā kamaliʻi a i ʻole ʻoi aku ka lōʻihi. Hiki ke paʻakikī ke ʻike i kēia mau hihia no ka mea e like paha nā hōʻailona me ka constipation maʻamau i ka hoʻomaka.

He aha ka mea e hoʻoulu ai i ka maʻi Hirschsprung?

Hana ʻia ka maʻi Hirschsprung i ka wā hāpai mua ke ulu nei ka pēpē i loko o ka ʻōpū. ʻAʻole maopopo loa ke kumu pololei, akā ʻike mākou e pili ana i nā pilikia me ke ʻano o ka ulu ʻana a me ka neʻe ʻana o kekahi mau pūnaewele nerve.

I nā mahina mua o ka hāpai ʻana, hoʻomaka nā pūnaewele nerve kūikawā i ka ʻōnaehana digestive e ulu ana o ka pēpē a neʻe mālie i lalo i ka anus. I nā pēpē me ka maʻi Hirschsprung, e kū koke kēia mau pūnaewele ma mua o ka hiki ʻana i ko lākou wahi hope.

Me he mea lā he ʻāpana genetic kēia kūlana, ʻo ia hoʻi hiki ke holo i nā ʻohana. Inā loaʻa i ke keiki hoʻokahi ka maʻi Hirschsprung, aia kahi manawa 3-12% o nā kaikuaʻana e loaʻa pū kekahi, ma muli o nā kumu like ʻole.

Ua pili kekahi mau gene i kēia kūlana, ʻo ka gene RET ka mea i pili pinepine ʻia. Eia naʻe, ʻaʻole hōʻoia ka loaʻa ʻana o kēia mau hoʻololi genetic e ulu ka maʻi i ke keiki - hoʻonui wale ia i ka hiki.

He aha nā ʻano o ka maʻi Hirschsprung?

Hoʻokaʻawale nā kauka i ka maʻi Hirschsprung ma muli o ka nui o ka kolona i pilikia e nā pūnaewele nerve nele. ʻO ka hoʻomaopopo ʻana i ke ʻano e kōkua i ka hoʻoholo ʻana i ke ala lapaʻau maikaʻi loa.

ʻO ka maʻi pōkole ka ʻano maʻamau loa, e pili ana i ka 80% o nā hihia. I kēia ʻano, ʻo ka hapa lalo wale nō o ka kolona (rectum a me ka sigmoid colon) ka mea nele i nā pūnaewele nerve. He mau hōʻailona māmā nā keiki me kēia ʻano a maikaʻi loa ma hope o ka mālama ʻana.

Hoʻopili ka maʻi lōʻihi i kahi ʻāpana nui o ka kolona a loaʻa i ka 20% o nā hihia. Hoʻokumu kēia ʻano i nā hōʻailona ʻoi aku ka nui a pono paha i ka mālama ʻoi aku ka paʻakikī. Pono paha kekahi mau keiki i nā ʻoki kino he nui a i ʻole nā ​​pilikia hoʻoheheʻe mau.

I nā hihia kakaikahi, hiki i ke kūlana ke hoʻopili i ka kolona holoʻokoʻa a hiki ke hoʻolōʻihi i loko o ka ʻōpū liʻiliʻi. Pono kēia mau hihia i ka mālama kūikawā a hoʻopili pinepine ʻia me ka hana pū ʻana me kahi hui o nā loea pediatric.

I ka wā e ʻike ai i ke kauka no ka maʻi Hirschsprung?

Pono ʻoe e hoʻokaʻaʻike koke i ke kauka o kāu keiki inā ʻaʻole hele mai kāu pēpē hou i kā lākou ʻōpala mua i loko o 48 mau hola ma hope o ka hānau ʻana. ʻO kēia kekahi o nā hōʻailona hoʻomaopopo mua nui loa.

ʻO nā kumu wikiwiki ʻē aʻe e ʻimi ai i ka mālama lapaʻau e komo pū ana me ka luaʻi ʻōmaʻomaʻo a ʻeleʻele paha, ka ʻōpū pehu a paʻakikī paha, a i ʻole nā ​​hōʻailona ʻaʻole e hānai maikaʻi kāu pēpē a me he mea lā ʻoluʻolu ʻole. Hiki i kēia mau hōʻailona ke hōʻike i ka pani koʻikoʻi e pono ai ka mālama koke.

No nā pēpē a me nā keiki kahiko, ʻo ka constipation mau ʻaʻole e pane i nā loli meaʻai a i ʻole nā ​​mālama mālie e pono ai ka hele ʻana i ke kauka. Inā emi iho ka nui o ka hele ʻana o kāu keiki i ka ʻōpala ma mua o ʻekolu mau manawa i ka hebedoma a i ʻole me he mea lā ke hoʻoikaika nui nei, pono ke kūkākūkā me kāu pediatrician.

Mai kali inā ʻike ʻoe ʻaʻole ulu a loaʻa paha ke kaumaha o kāu keiki e like me ka manaʻo, ʻoi aku hoʻi inā hana pū kēia me nā hōʻailona hoʻoheheʻe. Hiki i ka ʻike mua a me ka mālama ʻana ke pale aku i nā pilikia a kōkua i kāu keiki e ulu.

He aha nā kumu pilikia no ka maʻi Hirschsprung?

He mau kumu e hiki ai ke hoʻonui i ka nui o ka hānau ʻana o kahi pēpē me ka maʻi Hirschsprung. ʻO ka hoʻomaopopo ʻana i kēia mau kumu pilikia e kōkua i nā ʻohana a me nā kauka e makaʻala no nā hōʻailona mua.

ʻO ka lilo ʻana i kāne ka mea pilikia nui loa - ʻoi aku ka nui o nā keikikāne e loaʻa i kēia kūlana ma mua o nā kaikamahine. ʻAʻole maopopo loa ke kumu o kēia ʻokoʻa kāne, akā ua ʻike mau ʻia ma waena o nā heluna like ʻole.

He kuleana nui ka mōʻaukala ʻohana. ʻO ka loaʻa ʻana o ka makua a i ʻole ke kaikuaʻana me ka maʻi Hirschsprung e hoʻonui nui i ka pilikia. ʻOi aku ka nui o ka pilikia inā he wahine ka lālā ʻohana i pilikia a i ʻole he ʻano lōʻihi o ka maʻi.

Hoʻopili ʻia kekahi mau kūlana genetic me ka maʻi Hirschsprung, me ka maʻi Down, kahi i loaʻa ma kahi o 2-10% o nā keiki me kēia kūlana ʻōpū. Loaʻa nō hoʻi i nā maʻi genetic ʻē aʻe e like me ka maʻi Waardenburg a me ka maʻi congenital central hypoventilation syndrome ka pilikia nui.

Hiki i kekahi mau mutation genetic kānalua ke hoʻolilo i nā ʻohana i ʻoi aku ka maʻalahi, ʻoiai ʻo kēia mau mea wale nō kahi hapa liʻiliʻi o nā hihia. ʻAʻohe o ka hapa nui o nā keiki me ka maʻi Hirschsprung i kēia mau loli genetic kūikawā.

He aha nā pilikia hiki ke loaʻa i ka maʻi Hirschsprung?

ʻOiai hiki ke mālama maikaʻi ʻia ka maʻi Hirschsprung, hiki iā ia ke alakaʻi i nā pilikia nui inā ʻaʻole i ʻike ʻia a mālama pono ʻia. ʻO ka ʻike ʻana i kēia mau pilikia hiki ke kōkua i ka hōʻoia ʻana i ka mālama koke.

ʻO ka pilikia nui loa kahi kūlana i kapa ʻia ʻo enterocolitis, ʻo ia ka mumū o nā ʻōpū. Hiki i kēia ke hana ma mua a ma hope paha o ke ʻoki ʻana a pono i ka nānā ʻana o nā kauka koke. ʻO nā hōʻailona e komo pū ana ka mahana, ka luaʻi ʻana o ka ʻōpū, ka luaʻi ʻana, a me ka ʻōpū pehu.

ʻO ka toxic megacolon kekahi pilikia koʻikoʻi kahi e lilo ai ka colon i nui a mumū loa. Hiki i kēia kūlana weliweli ke hoʻopōʻino i ka paia o ka ʻōpū inā ʻaʻole i mālama koke ʻia me nā lāʻau ʻalopona a i kekahi manawa i ka ʻoki ʻana pilikia.

Hiki ke ulu nā pilikia ulu a me ka hānai ʻana i ka wā hiki ʻole i nā keiki ke komo pono i nā mea hānai ma muli o nā pilikia hoʻohaʻahaʻa mau. Pono paha kekahi mau keiki i ke kākoʻo hānai kūikawā a i ʻole nā mea hoʻohui e kōkua iā lākou e ulu maʻamau.

Ma hope o ka ʻoki kino, hiki i kekahi mau keiki ke ʻike i nā pilikia mau e like me ka constipation mau, nā ulia lepo, a i ʻole ka pilikia me ke aʻo ʻana i ka halepaku. Eia naʻe, me ke ahonui a me ka mālama hoʻomau kūpono, ʻoi aku ka maikaʻi o ka nui o kēia mau pilikia ma mua o ka manawa.

ʻO ke kī i ka pale ʻana i nā pilikia, ʻo ia ka ʻike mua ʻana, ka mālama ʻoki kino kūpono, a me ka hahai mau ʻana me ka hui mālama ola o kāu keiki. ʻO ka hapa nui o nā keiki e loaʻa ana i ka mālama kūpono e hele aku i ka nohona maʻamau a olakino.

Pehea ka ʻIke ʻia ʻana o ka Maʻi Hirschsprung?

ʻO ka ʻike ʻana i ka maʻi Hirschsprung e komo pū ana i kekahi mau hoʻokolohua e kōkua i nā kauka e ʻike i ka hana maikaʻi ʻana o ka colon a inā aia nā pūnaewele nerve. He pololei maʻamau ke kaʻina hana, ʻoiai paha he mau hoʻokolohua like ʻole e loaʻa ai kahi kiʻi piha.

E hoʻomaka kāu kauka me kahi hōʻoia kino a me ka moʻolelo lapaʻau kikoʻī. E nīnau lākou e pili ana i nā neʻe ʻana o ka ʻōpū, nā ʻano hānai, a me nā hōʻailona āu i ʻike ai. E ʻike pū lākou i ka ʻōpū o kāu keiki e nānā i ka pehu a i ʻole nā wahi ʻeha.

ʻO ka barium enema pinepine ka hoʻokolohua kiʻi mua loa i hana ʻia. E inu a loaʻa paha i kāu keiki kahi wai kūikawā e hōʻike ʻia ma nā X-ray, e ʻae ana i nā kauka e ʻike i ke ʻano a me ka hana o ka colon. I ka maʻi Hirschsprung, hōʻike maʻamau kēia hoʻokolohua i kahi wahi ʻāpana i hahai ʻia e kahi ʻāpana hoʻonui ma luna.

ʻO ka ʻike maopopo e hele mai ana mai kahi rectal biopsy, kahi e wehe ai nā kauka i kahi ʻāpana liʻiliʻi o ka ʻiʻo mai ka paia rectal e nānā ma lalo o ka microscope. Hiki i kēia hoʻokolohua ke hōʻike maopopo inā aia nā pūnaewele nerve a i ʻole ʻaʻohe.

I kekahi manawa, hoʻohana nā kauka i ka anorectal manometry, kahi hoʻokolohua e ana i ka mana a me ka hana o nā ʻiʻo ma ka rectum a me ka anus. Hiki i kēia ke kōkua i ka ʻike ʻana i nā reflexes ʻiʻo kūpono ʻole i ʻike ʻia i ka maʻi Hirschsprung.

He aha ka lāʻau lapaʻau no ka maʻi Hirschsprung?

ʻO ka lāʻau lapaʻau nui no ka maʻi Hirschsprung ʻo ia ka ʻokiʻoki e wehe i ka ʻāpana o ka colon i nele i nā pūnaewele nerve a hoʻohui hou i nā ʻāpana olakino. ʻOiai paha kēia e lohe ai he kaumaha, he holomua loa kēia mau hana a kōkua i nā keiki e hoʻi i ka hana maʻamau o ka ʻōpū.

Loaʻa i ka hapanui o nā keiki ka mea i kapa ʻia ʻo ka hana

E mālama i ka wahi ʻoki ʻia e maʻemaʻe a maloʻo e like me nā ʻōlelo a kāu kauka ʻoki. He nui paha ʻoe e pono ai e hoʻololi pinepine i nā kāwele a nānā i nā hōʻailona o ka maʻi e like me ka ʻulaʻula nui ʻana, ka pehu, a i ʻole ka wai. Mai kānalua e kāhea aku i kāu kauka inā loaʻa iā ʻoe kekahi mau manaʻo hopohopo.

Pono paha e hoʻoponopono ʻia ka hānai ʻana i ka hoʻomaka mua, ʻoiai inā loaʻa i kāu keiki kahi colostomy. E hāʻawi kāu hui olakino i nā kuhikuhi kikoʻī e pili ana i nā meaʻai e hāʻawi ai a i ka wā e hoʻomaka ai i ka ʻai. E hoʻomaka mālie a nānā i ke ʻano o ka hoʻomanawanui ʻana o kāu keiki i nā meaʻai like ʻole.

He mea nui ka mālama ʻeha no ka hōʻoluʻolu a me ka ho'ōla. E hāʻawi i nā lāʻau lapaʻau e like me ka mea i kuhikuhi ʻia a mai haʻalele i nā mahele inā paha e ʻoluʻolu ana kāu keiki. ʻO ka loaʻa ʻana o ka papa hana hoʻomalu ʻeha mau e kōkua i nā keiki e ola koke.

E nānā i nā hōʻailona o nā pilikia e like me ka mahana kiʻekiʻe, ka luaʻi mau, a i ʻole nā ​​hoʻololi i nā neʻe ʻana o ka ʻōpū e hopohopo iā ʻoe. E hāʻawi kāu hui ʻoki iā ʻoe i kahi papa inoa o nā hōʻailona hoʻomaopopo a me ka ʻike pilikia.

E hoʻomanaʻo e ola kēlā me kēia keiki ma ko lākou wikiwiki ponoʻī. Hiki i kekahi ke hoʻi i nā hana maʻamau i loko o kekahi mau pule, ʻoiai ʻo nā mea ʻē aʻe e pono ai ka manawa hou aku. E hahai i ke alakaʻi a kāu keiki a mai wikiwiki i ke kaʻina hoʻōla.

Pehea ʻoe e hoʻomākaukau ai no kāu kūkā lāʻau lapaʻau?

ʻO ka hoʻomākaukau ʻana no kāu kūkā e kōkua i ka hōʻoia ʻana e loaʻa iā ʻoe ka ʻike kōkua loa a hana i nā hoʻoholo maikaʻi loa no ka mālama ʻana i kāu keiki. Hiki i ka hoʻonohonoho iki ma mua ke hoʻolilo i kahi ʻokoʻa nui i ka huahana o kāu kipa.

E mālama i kahi moʻolelo kikoʻī o nā neʻe ʻana o ka ʻōpū o kāu keiki, me ka pinepine, ka kūpaʻa, a me nā ʻano āu e ʻike ai. E hahai pū i nā ʻano hānai, nā hoʻololi kaumaha, a me nā hōʻailona e like me ka luaʻi a i ʻole ka ʻeha ʻōpū. E kōkua kēia ʻike i nā kauka e hoʻomaopopo pono i ka mea e hana nei.

E kākau i kāu mau nīnau a pau ma mua o ka hālāwai, i ʻole e poina ʻoe i kekahi mea nui. E hoʻokomo i nā nīnau e pili ana i ka hōʻailona, nā koho lapaʻau, ka mea e manaʻo ai i ka wā hoʻōla, a me nā hopohopo e pili ana i nā hopena lōʻihi.

E lawe mai i ka papa inoa piha o nā lāʻau lapaʻau a i ʻole nā mea hoʻohui a kāu keiki e lawe ai, me nā nui a me ka pinepine o ka hāʻawi ʻana. E haʻi pū i nā maʻi ʻili a i ʻole nā ​​​​mea pane ma mua i nā lāʻau lapaʻau.

Inā hiki, e lawe mai i kekahi lālā ʻohana a hoaaloha paha no ke kākoʻo, ʻoiai inā ke kūkākūkā nei ʻoe i ka ʻoki kino a i ʻole nā ​​​​hoʻolālā lapaʻau paʻakikī. Hiki i ka loaʻa ʻana o kekahi e hoʻolohe iā ʻoe ke kōkua iā ʻoe e hoʻomanaʻo i ka ʻike a hāʻawi i ke kākoʻo manaʻo.

Mai makaʻu e noi i ka ʻike palapala a i ʻole nā ​​​​kumu waiwai e pili ana i ke kūlana o kāu keiki. He nui nā ʻohana i ʻike he kōkua ka loaʻa ʻana o nā mea i hiki iā lākou ke nānā hou ma ka home i ka wā ʻaʻole lākou e manaʻo nui.

He aha ka lawe nui e pili ana i ka maʻi Hirschsprung?

ʻO ka maʻi Hirschsprung kahi hemahema hānau hiki ke mālama ʻia e hoʻopilikia i ka hiki o ka colon ke hoʻoneʻe i ka ʻōpala maʻamau. ʻOiai hiki i ka hōʻailona ke manaʻo nui i ka wā mua, ʻo ka hapa nui o nā keiki e loaʻa ana i ka mālama kūpono e ola i nā ola maʻamau a olakino piha.

He mea nui ka ʻike mua a me ka mālama ʻana no nā hopena maikaʻi loa. Inā ʻike ʻoe i nā hōʻailona e like me ka hoʻopanee ʻia ʻana o nā neʻe ʻana o ka ʻōpū mua i nā pēpē hou a i ʻole ka constipation mau i nā keiki kahiko, mai kānalua e kūkākūkā i kēia mau hopohopo me kāu kauka keiki.

He holomua loa ka ʻoki kino i ka mālama ʻana i kēia kūlana, a ʻike ka hapa nui o nā keiki i ka hoʻomaikaʻi nui ʻana i kā lākou mau hōʻailona ma hope. ʻOiai e lawe ana ka hoʻōla i ka manawa a me ke ahonui, ʻike maʻamau nā ʻohana e hoʻi ka ola i ka maʻamau i loko o kekahi mau mahina o ka mālama ʻana.

E hoʻomanaʻo ʻaʻole e kaupalena ka loaʻa ʻana o ka maʻi Hirschsprung i ka mea hiki i kāu keiki ke hoʻokō i ke ola. Me ka mālama lapaʻau kūpono a me kāu kākoʻo aloha, komo piha nā keiki me kēia kūlana i ke kula, nā haʻuki, a me nā hana a pau e hana ai i ka wā kamaliʻi he mea kūikawā.

Nīnau Pinepine e pili ana i ka Maʻi Hirschsprung

E hiki anei i kaʻu keiki ke kaohi i kona mau neʻe ʻana o ka ʻōpū ma hope o ke ʻoki kino?

ʻO ka hapa nui o nā keiki e hoʻomohala i ka kaohi maʻamau o ka ʻōpū ma hope o ke ʻoki kino, ʻoiai paha e pono ai kekahi mau mahina a i hoʻokahi makahiki paha no ka hoʻonohonoho piha ʻana o nā mea a pau. Pono paha kekahi mau keiki i ke kōkua hou aku me ke aʻo ʻana i ka halepaku a i ʻole ka mālama ʻana i nā ulia kūpono ʻole, akā ʻo ka hapa nui loa e loaʻa iā lākou ka kaohi maikaʻi ma hope o kekahi manawa. E hana pū kāu hui ʻoki kino me ʻoe e hoʻoponopono i nā pilikia e hoʻomau nei a hāʻawi i nā hoʻolālā e kōkua i kāu keiki e holomua.

Hiki anei ke pale aku i ka maʻi Hirschsprung?

ʻAʻohe ala i kēia manawa e pale aku ai i ka maʻi Hirschsprung, ʻoiai he kūlana hoʻomohala ia e hana ʻia i ka wā hāpai. Eia naʻe, inā loaʻa iā ʻoe ka mōʻaukala ʻohana o ke kūlana, hiki i ka ʻōlelo aʻo genetics ma mua o ka hāpai ke kōkua iā ʻoe e hoʻomaopopo i nā pilikia o kou ʻohana. ʻO ka mea nui loa ka ʻike mua ʻana a me ka mālama ʻana i ka wā hānau ʻia ke keiki.

Pehea ka lōʻihi o ke ʻoki kino a pehea hoʻi ka hoʻōla ʻana?

ʻO ka ʻoki kino pull-through maʻamau e lawe i 2-4 mau hola, ma muli o ka nui o ka colon i pilikia. ʻO ka hapa nui o nā keiki e noho i ka haukapila no 3-7 mau lā ma hope o ke ʻoki kino. ʻO ka hoʻōla piha maʻamau e lawe i kekahi mau pule a i kekahi mau mahina paha, i ka wā e hoʻi hou ai kāu keiki i nā hana maʻamau a me ka ʻai. E hāʻawi kāu hui ʻoki kino i kahi papa manawa kikoʻī a me ka hoʻolālā hoʻōla.

Pono anei kāu keiki i nā palena ʻai kūikawā ma hope o ka mālama ʻana?

Hiki i ka hapa nui o nā keiki ke hoʻi i ka ʻai maʻamau loa ma hope o ke ʻoki kino a me ka hoʻōla ʻana. I ka hoʻomaka, hiki i kāu kauka ke ʻōlelo e hoʻomaka me nā meaʻai maʻalahi e ʻeli ʻia a hoʻohui mālie i nā ʻano like ʻole. Loaʻa i kekahi mau keiki ka pōmaikaʻi mai ka ʻai ʻana i nā meaʻai liʻiliʻi, pinepine a i ʻole ka hoʻohui ʻana i ka fiber hou aku i kā lākou ʻai e kākoʻo i nā neʻe ʻana o ka ʻōpū olakino, akā ʻaʻole kēia mau mea he mau palena koʻikoʻi.

He aha nā manawa e loaʻa ai i nā keiki e hiki mai ana ka maʻi Hirschsprung?

Inā loaʻa iā ʻoe ke keiki hoʻokahi me ka maʻi Hirschsprung, ʻoi aku ka nui o ka pilikia no nā keiki e hiki mai ana ma mua o ka lehulehu akā emi iki nō hoʻi. Ke hilinaʻi nei ka pilikia pololei ma nā mea e like me ka wahine a kāne paha o ke keiki i loaʻa ka maʻi a me ka nui o ko lākou maʻi, akā ma waena o 3-12% ia. Hiki i kāu kauka ke hāʻawi i ka ʻike pilikia kikoʻī e pili ana i ke kūlana o kou ʻohana a hiki paha ke ʻōlelo aku i ka ʻōlelo aʻo genetics.