He aha ka Cardiomyopathy Hypertrophic? Nā Hōʻailona, Nā Kumu, a me ka Lapaʻau

ʻO ka cardiomyopathy hypertrophic kahi kūlana kahi e lilo ai kou ʻiʻo naʻau i mānoanoa loa, e paʻakikī ai i kou naʻau ke pūʻiwa i ke koko. E noʻonoʻo iā ia e like me ke kanaka hoʻoikaika kino nona nā ʻiʻo i ulu nui loa a hoʻopilikia maoli i ka neʻe ʻana - ke mānoanoa kou ʻiʻo naʻau a hiki i kahi e hiki ai ke pale i ke kahe koko maʻamau.

Hoʻopili kēia kūlana genetic ma kahi o 1 i 500 mau kānaka ma ka honua holoʻokoʻa, ʻoiai ʻaʻole ʻike ka nui o nā kānaka a lākou i loaʻa ai. ʻO ka mānoanoa pinepine ma ka paia e hoʻokaʻawale ai i nā keʻena lalo ʻelua o kou naʻau, akā hiki ke loaʻa ma nā wahi a pau o ka ʻiʻo naʻau.

He aha nā hōʻailona o ka cardiomyopathy hypertrophic?

ʻAʻole ʻike ka nui o nā kānaka me ka cardiomyopathy hypertrophic i nā hōʻailona, ​​​​ʻoi aku hoʻi i nā wā mua. I ka wā e ʻike ʻia ai nā hōʻailona, ​​​​pinepine lākou e ulu mālie i ka wā e hoʻomau ai ka mānoanoa o ka ʻiʻo naʻau.

ʻO nā hōʻailona maʻamau āu e ʻike ai:

• Pōkole o ka hanu, ʻoi aku hoʻi i ka wā e hana kino ai a i ʻole ke moe pālahalaha
• ʻEha umauma a i ʻole ka ʻāʻī, ʻoi aku hoʻi i ka wā e hoʻoikaika kino ai
• Nā palpitations naʻau a i ʻole ka manaʻo e like me kou naʻau e holo wikiwiki ana a i ʻole e lele ana nā hahau
• Nā dizziness a i ʻole nā ​​​​lightheadedness, ʻoi aku hoʻi i ka wā e kū koke ai
• Ka luhi e like ʻole me kou pae hana
• Nā fainting spells, ʻoi aku hoʻi i ka wā a i ʻole ma hope koke o ka hoʻoikaika kino

Hiki i nā hōʻailona ʻaʻole maʻamau akā ʻoi aku ka koʻikoʻi ke komo pū me ka pehu ʻana i kou mau wāwae, nā kuʻekuʻe wāwae, a i ʻole nā ​​​​wāwae, a me ka pilikia o ka hanu e ʻoi aku ka maikaʻi i ka wā e moe ai. Hōʻike kēia mau hōʻailona e hoʻoikaika nui ana kou naʻau e pūʻiwa i ke koko.

I nā hihia kakaikahi, ʻo ka hōʻailona mua o ka cardiomyopathy hypertrophic hiki ke hoʻomaka koke ʻana o ka naʻau, ʻoi aku hoʻi i nā ʻōpio. ʻO ia ke kumu i loaʻa ai ka nānā nui o ke kūlana i ka lāʻau lapaʻau haʻuki, ʻoiai he mea maʻamau ʻole ia.

He aha nā ʻano o ka cardiomyopathy hypertrophic?

Loaʻa ka cardiomyopathy hypertrophic i ʻelua mau ʻano nui, ʻo kēlā me kēia e hoʻopilikia ana i kou naʻau. ʻO ke ʻano āu e loaʻa ai e hoʻoholo i kāu mau hōʻailona a me ke ala lapaʻau.

Hana ʻia ka cardiomyopathy hypertrophic obstructive i ka wā e pale ai ka ʻiʻo naʻau mānoanoa i ke kahe koko mai kou naʻau. Hana ʻia kēia ma kahi o 70% o nā hihia a maʻamau e hoʻokumu ai i nā hōʻailona ʻike ʻia e like me ka ʻeha umauma a me ka pōkole o ka hanu i ka wā e hana ai.

ʻO ka cardiomyopathy hypertrophic non-obstructive ʻo ia hoʻi he mānoanoa ka ʻiʻo akā ʻaʻole ia e pale nui i ke kahe koko. Pinepine nā kānaka me kēia ʻano i nā hōʻailona liʻiliʻi, ʻoiai ʻaʻole hoʻomaha pono ka naʻau ma waena o nā hahau, kahi e hiki ai ke hoʻokumu i nā pilikia ma hope.

Aia kekahi ʻano kakaikahi i kapa ʻia ʻo apical hypertrophic cardiomyopathy, kahi e mānoanoa ai ma ka piko o ka naʻau. ʻOi aku ka maʻamau o kēia ʻano i nā kānaka o ka lāhui Kepani a pinepine e hoʻokumu ai i nā hōʻailona liʻiliʻi ma mua o nā ʻano ʻē aʻe.

He aha nā kumu o ka cardiomyopathy hypertrophic?

ʻO ka cardiomyopathy hypertrophic kahi kūlana genetic nui i hoʻoili ʻia ma o nā ʻohana. Ma kahi o 60% o nā hihia i hoʻokumu ʻia e nā mutations i nā genes e kaohi ana i ka hana ʻana o nā protein o kou ʻiʻo naʻau.

ʻO nā genes i hoʻopilikia pinepine ʻia:

• MYH7 a me MYBPC3, ka mea e hana ai i nā protein pono no ka hoʻoikaika ʻana o ka ʻiʻo naʻau
• TNNT2 a me TNNI3, ka mea e kōkua ai i ka hoʻoponopono ʻana i ka wā e hoʻoikaika a hoʻomaha ai kou ʻiʻo naʻau
• TPM1 a me ACTC1, ka mea e kākoʻo ai i ka ʻōnaehana hoʻolālā o nā sela ʻiʻo naʻau

Inā loaʻa i kekahi o kou mau mākua ka cardiomyopathy hypertrophic, loaʻa iā ʻoe ka 50% manawa e hoʻoili ai i ka mutation genetic. Eia naʻe, ʻaʻole hōʻoia ka loaʻa ʻana o ka gene e ulu ʻoe i nā hōʻailona - lawe kekahi poʻe i ka mutation akā ʻaʻole hōʻike i nā hōʻailona o ke kūlana.

I nā hihia kakaikahi, hiki ke ulu ka cardiomyopathy hypertrophic me ka ʻole o ka mōʻaukala ʻohana. Hiki paha kēia ma muli o nā mutations genetic hou a i ʻole, he mea maʻamau ʻole, ma muli o nā kūlana ʻē aʻe e like me kekahi mau maʻi metabolic a i ʻole ke koko kiʻekiʻe lōʻihi.

I ka wā e ʻike ai i ke kauka no ka cardiomyopathy hypertrophic?

Pono ʻoe e ʻike koke i ke kauka inā ʻike ʻoe i ka ʻeha umauma, ka pōkole o ka hanu i nā hana maʻamau, a i ʻole nā ​​​​fainting spells. Pono kēia mau hōʻailona i ka loiloi lapaʻau ʻoiai inā he māmā a hele mai a hele paha.

E ʻimi i ka mālama lapaʻau koke inā loaʻa iā ʻoe ka ʻeha umauma nui, ka pilikia o ka hanu i ka wā e hoʻomaha ai, a i ʻole inā ʻoe e fainting i ka wā a i ʻole ma hope o ka hoʻoikaika kino. Hiki i kēia ke hōʻike i ka hoʻopilikia ʻana o kou kūlana i ka hiki o kou naʻau ke pūʻiwa i ke koko.

Inā loaʻa iā ʻoe ka mōʻaukala ʻohana o ka cardiomyopathy hypertrophic, ka make koke ʻana o ka naʻau, a i ʻole ka hāʻule naʻau i wehe ʻole ʻia, e noʻonoʻo i ka ʻōlelo aʻo genetic a me ka nānā ʻana ʻoiai me ka ʻole o nā hōʻailona. Hiki i ka ʻike mua ke kōkua i ka pale ʻana i nā pilikia a me ka alakaʻi ʻana i nā hoʻoholo nohona.

Liʻiliʻi nā nānā maʻamau inā ua ʻike ʻia ʻoe, ʻoiai hiki ke loli kou kūlana i ka manawa. Makemake kāu kauka e nānā i ka hana ʻana o kou naʻau a hoʻoponopono i ka lapaʻau e like me ka pono.

He aha nā pilikia no ka cardiomyopathy hypertrophic?

ʻOiai ke ola nei ka nui o nā kānaka me ka cardiomyopathy hypertrophic i nā ola maʻamau, hiki i ke kūlana ke alakaʻi i nā pilikia koʻikoʻi. Ke hoʻomaopopo nei i kēia mau mea hiki ke kōkua iā ʻoe e hana pū me kāu kauka e pale a hoʻokele paha iā lākou.

ʻO nā pilikia maʻamau:

• Atrial fibrillation - kahi rhythm naʻau kūpono ʻole e hoʻonui ai i ka pilikia o ka hahau
• Heart failure - i ka wā ʻaʻole hiki i kou naʻau ke pūʻiwa i ke koko me ka maikaʻi e hoʻokō i nā pono o kou kino
• Sudden cardiac arrest - ʻoiai he mea kakaikahi, ʻo kēia ka pilikia koʻikoʻi loa
• Nā clots koko - ʻoi aku hoʻi inā loaʻa iā ʻoe ka atrial fibrillation
• Nā pilikia o ka mitral valve - hiki i ka ʻiʻo mānoanoa ke hoʻopilikia i ka hana ʻana o nā valves o kou naʻau

Hiki i nā pilikia ʻaʻole maʻamau akā koʻikoʻi ke komo pū me ka infective endocarditis, kahi e hoʻopilikia ai nā bacteria i nā valves o kou naʻau, a me ka pale ʻana o ka outflow koʻikoʻi e pono ai ka hana ʻoki.

ʻO ka pilikia o ka hoʻomaka koke ʻana o ka naʻau, ʻoiai he mea weliweli e noʻonoʻo ai, e hoʻopilikia ana i ka liʻiliʻi ma mua o 1% o nā kānaka me ka cardiomyopathy hypertrophic i kēlā me kēia makahiki. Hiki i kāu kauka ke loiloi i kāu pilikia pilikino a hāʻawi i nā hana pale inā pono, e like me ka pale ʻana i kekahi mau lāʻau a i ʻole ke noʻonoʻo ʻana i kahi defibrillator implantable.

Pehea e ʻike ʻia ai ka cardiomyopathy hypertrophic?

Hoʻomaka ka ʻike ʻana i ka cardiomyopathy hypertrophic me kāu kauka e hoʻolohe ana i kou naʻau a nīnau ana e pili ana i kāu mau hōʻailona a me ka mōʻaukala ʻohana. Ke ʻimi nei lākou i nā leo naʻau a me nā murmurs kikoʻī e hōʻike ana i ke kahe koko kūpono ʻole.

ʻO ka hoʻokolohua ʻike nui ka echocardiogram, kahi e hoʻohana ai i nā nalu kani e hana i nā kiʻi kikoʻī o kou naʻau. Hōʻike kēia hoʻokolohua ʻeha ʻole i ka mānoanoa o kou ʻiʻo naʻau, pehea ka maikaʻi o ka pūʻiwa ʻana o kou naʻau, a inā ua pale ʻia ke kahe koko.

Hiki i kāu kauka ke hāʻawi aku:

• Electrocardiogram (ECG) e nānā i ka hana uila o kou naʻau
• Hoʻokolohua kaumaha hoʻoikaika kino e ʻike i ka pane ʻana o kou naʻau i ka hana kino
• Cardiac MRI no nā kiʻi kikoʻī o kou ʻano naʻau
• Holter monitor e hoʻopaʻa i ka rhythm o kou naʻau ma luna o 24-48 mau hola
• Genetic testing e ʻike i nā mutations kikoʻī a nānā i nā lālā ʻohana

I kekahi mau hihia, hiki i kāu kauka ke hana i ka catheterization naʻau, kahi e hoʻokomo ʻia ai kahi tube lahilahi i kou naʻau e ana i nā kaomi a nānā pono i ke kahe koko. Hoʻopaʻa ʻia kēia no nā hihia paʻakikī a i ʻole ke noʻonoʻo ʻia nei ka hana ʻoki.

Hiki i nā hoʻokolohua koko ke kōkua i ka hoʻopau ʻana i nā kūlana ʻē aʻe e hiki ke hoʻokumu i nā hōʻailona like, e like me nā pilikia thyroid a i ʻole nā ​​​​maʻi naʻau ʻē aʻe.

He aha ka lapaʻau no ka cardiomyopathy hypertrophic?

Ke nānā nei ka lapaʻau no ka cardiomyopathy hypertrophic i ka hoʻokele ʻana i nā hōʻailona, ​​​​ka pale ʻana i nā pilikia, a me ke kōkua ʻana iā ʻoe e mālama i kahi ola hana, piha.

ʻO nā lāʻau lapaʻau pinepine ka laina mua o ka lapaʻau a hiki ke komo pū me:

• Beta-blockers e like me metoprolol e hoʻomāmā i kou naʻau a hoʻemi i nā hōʻailona
• Calcium channel blockers e like me verapamil e kōkua i kou naʻau e hoʻomaha ma waena o nā hahau
• Nā lāʻau anti-arrhythmic inā loaʻa iā ʻoe nā rhythms naʻau kūpono ʻole
• Nā mea hoʻoheheʻe koko inā pilikia ʻoe i nā clots koko
• Diuretics e hoʻemi i ka waihona wai inā loaʻa iā ʻoe nā hōʻailona o ka naʻau

No nā hihia obstructive koʻikoʻi ʻaʻole pane i ka lāʻau lapaʻau, pono paha nā koho hana ʻoki. Hoʻokomo ʻia ka Septal myectomy i ka wehe ʻana i kahi ʻāpana o ka ʻiʻo mānoanoa e hoʻomaikaʻi i ke kahe koko, ʻoiai ke hoʻohana nei ka alcohol septal ablation i ka waiʻona e hoʻemi i ka ʻiʻo pilikia.

I nā hihia kakaikahi kahi e pilikia nui ai ʻoe i ka hoʻomaka koke ʻana o ka naʻau, hiki i kāu kauka ke hāʻawi i kahi implantable cardioverter defibrillator (ICD). Ke nānā nei kēia hāmeʻa i ka rhythm o kou naʻau a hiki ke hāʻawi i kahi shock ola inā loaʻa nā rhythms weliweli.

ʻO ka koho lapaʻau hou loa ʻo mavacamten, kahi lāʻau i hoʻolālā ʻia no ka cardiomyopathy hypertrophic e hiki ke hoʻemi i ka mānoanoa o ka ʻiʻo naʻau a hoʻomaikaʻi i nā hōʻailona i kekahi poʻe.

Pehea e hoʻokele ai i ka cardiomyopathy hypertrophic ma ka home?

ʻO ke ola maikaʻi me ka cardiomyopathy hypertrophic ke komo pū me ka hana ʻana i nā koho nohona noʻonoʻo e kākoʻo i kou olakino naʻau. Hiki i nā hoʻoholo liʻiliʻi i kēlā me kēia lā ke hoʻopilikia nui i kou manaʻo a me ka hana.

He mea nui loa ka noho hydrated no ka mea hiki i ka dehydration ke hoʻopilikia i nā hōʻailona. E inu i ka wai nui i ka lā holoʻokoʻa, ʻoi aku hoʻi ma mua a ma hope paha o ka hana kino a i ʻole i ka wā mahana.

He mea nui nā kuhikuhi hoʻoikaika kino akā pilikino. ʻOiai pono ʻoe e noho hana, e pale i nā haʻuki hoʻokūkū ikaika a me nā hana e hoʻokumu ai i ka pōkole o ka hanu a i ʻole ka ʻeha umauma. ʻO ka hele wāwae, ka ʻauʻau, a me ka hoʻomaʻamaʻa kū'ē māmā he mau koho palekana maʻamau.

Hiki i ka hoʻokele ʻana i ke kaumaha ma o nā ʻenehana hoʻomaha, ka hiamoe lawa, a me nā hana leʻaleʻa ke kōkua i ka hoʻemi ʻana i nā hōʻailona. Hiki i ke kaumaha lōʻihi ke hoʻopilikia i nā palpitations naʻau a me nā hōʻailona ʻē aʻe āu e ʻike ai.

E makaʻala i nā hōʻailona o kou kino a hoʻomaha i ka wā e pono ai. ʻAʻole kōkua ka hoʻoikaika ʻana i ka luhi nui a i ʻole ka pōkole o ka hanu a hiki ke hōʻike i kou pono i ka mālama lapaʻau.

E pale i kekahi mau mea e hiki ke hoʻopilikia i kou kūlana, me ka waiʻona nui, nā stimulants, a me nā lāʻau decongestant e hiki ke hoʻonui i kou naʻau a i ʻole ke koko.

Pehea ʻoe e hoʻomākaukau ai no kāu manawa kauka?

Ke hoʻomākaukau nei no kāu manawa e kōkua ai e hōʻoia e loaʻa iā ʻoe ka mea nui mai kāu manawa me kāu mea lawelawe olakino. E hoʻomaka ma ka kākau ʻana i kāu mau hōʻailona a pau, me ka wā e loaʻa ai a me nā mea e hoʻonāukiuki ai.

E lawe mai i ka papa inoa piha o kāu mau lāʻau lapaʻau, me nā lāʻau lapaʻau ma luna o ka counter a me nā mea hoʻohui. Hiki i kekahi mau lāʻau ke launa pū me nā kūlana naʻau a i ʻole nā ​​​​lapaʻau, no laila pono kāu kauka i kēia ʻike.

E hōʻiliʻili i kāu mōʻaukala lapaʻau ʻohana, ʻoi aku hoʻi i nā hoahānau me nā pilikia naʻau, ka make koke ʻana o ka naʻau, a i ʻole ka fainting i wehe ʻole ʻia. He mea nui kēia ʻike genetic no ka hoʻomaopopo ʻana i kou kūlana a me nā pilikia.

E hoʻomākaukau i nā nīnau e pili ana i kou kūlana kikoʻī, e like me nā pae hoʻoikaika kino palekana, nā hōʻailona hoʻomaopopo e nānā ai, a me ka pinepine āu e pono ai ka mālama hahai. E kākau i kēia mau mea i ʻole ʻoe e poina i ka wā o ka manawa.

Inā he kipa hahai kēia, e hoʻomaopopo i nā loli i kāu mau hōʻailona a i ʻole pehea ʻoe e pane ai i ka lapaʻau. E kūpaʻa e pili ana i ka hoʻohana ʻana i ka lāʻau lapaʻau a me nā hopena ʻaoʻao āu e ʻike ai.

He aha ka mea nui e pili ana i ka cardiomyopathy hypertrophic?

ʻO ka cardiomyopathy hypertrophic kahi kūlana naʻau genetic hiki ke hoʻokele ʻia e hoʻopilikia ana i kēlā me kēia kanaka i nā ʻano like ʻole. ʻOiai paha ke manaʻo nui ʻia ka ʻike mua, ola ka nui o nā kānaka me kēia kūlana i nā ola piha, hana me ka mālama lapaʻau kūpono a me nā hoʻoponopono nohona.

ʻO ke kī i ke ola maikaʻi me ka cardiomyopathy hypertrophic ka hoʻomohala ʻana i kahi pilina ikaika me kāu hui olakino. ʻAe ka nānā maʻamau i ka ʻike mua ʻana i nā loli a me ka hoʻoponopono ʻana i nā lapaʻau e like me ka pono.

E hoʻomanaʻo ʻaʻole e hoʻoholo kēia kūlana i kāu mau palena - ʻo ia wale nō ke pono ʻoe e noʻonoʻo i kou olakino naʻau. Hoʻokele ka nui o nā kānaka i nā hana, nā pilina, a me nā hana kino ʻoiai ke ola nei me ka cardiomyopathy hypertrophic.

E noʻonoʻo e pili ana i kou kūlana, e hahai i kāu papa lapaʻau, a mai kānalua e hoʻopili aku i kāu kauka me nā nīnau a i ʻole nā ​​​​hopohopo. Hana nui kāu hana proactive i ka hoʻokele ʻana i kou olakino i kāu mau hopena lōʻihi.

Nā nīnau i nīnau pinepine ʻia e pili ana i ka cardiomyopathy hypertrophic

Hiki iā ʻoe ke ola i kahi ola maʻamau me ka cardiomyopathy hypertrophic?

ʻAe, ola ka nui o nā kānaka me ka cardiomyopathy hypertrophic i nā ola piha, piha me ka hoʻokele lapaʻau kūpono. ʻOiai pono paha ʻoe e hana i kekahi mau hoʻoponopono nohona a lawe i nā lāʻau lapaʻau, ʻaʻole pale ke kūlana iā ʻoe mai ka hana ʻana, ka huakaʻi ʻana, a i ʻole ka leʻaleʻa ʻana i nā pilina. Ke kōkua nei ka mālama hahai maʻamau e hōʻoia i kou olakino a me ka hana.

He hereditary anei ka cardiomyopathy hypertrophic?

He genetic ka cardiomyopathy hypertrophic ma kahi o 60% o nā hihia, ʻo ia hoʻi hiki ke hoʻoili ʻia mai nā mākua i nā keiki. Inā loaʻa iā ʻoe ke kūlana, loaʻa i kēlā me kēia o kāu mau keiki ka 50% manawa e hoʻoili ai i ka mutation genetic. Eia naʻe, hiki i ka hoʻokolohua genetic a me ka nānā ʻohana ke kōkua i ka ʻike mua ʻana i nā hoahānau pilikia, e ʻae ana i ka nānā ʻana a me ka lapaʻau maikaʻi.

He aha nā hana āu e pale ai me ka cardiomyopathy hypertrophic?

Pono ʻoe e pale i nā haʻuki hoʻokūkū ikaika, ʻoi aku hoʻi nā mea e pono ai nā bursts o ka ikehu e like me ka holo wikiwiki a i ʻole ka hāpai kaumaha. Pono nō hoʻi e kaupalena ʻia nā hana e hoʻokumu ai i ka pōkole o ka hanu, ka ʻeha umauma, a i ʻole ka dizziness. Eia naʻe, he mea maikaʻi a paipai ʻia nā hoʻoikaika kino māmā e like me ka hele wāwae, ka ʻauʻau, a me ka hoʻomaʻamaʻa kū'ē māmā ma lalo o ke alakaʻi lapaʻau.

Hiki i ka cardiomyopathy hypertrophic ke ʻoi aku ka maikaʻi i ka manawa?

Hiki i ka cardiomyopathy hypertrophic ke holomua, akā ʻokoʻa loa kēia ma waena o nā kānaka. Noho paʻa kekahi poʻe no nā makahiki, ʻoiai kekahi e ulu paha i nā hōʻailona a i ʻole nā ​​​​pilikia. Ke kōkua nei ka nānā maʻamau me kāu cardiologist i ka hahai ʻana i nā loli a me ka hoʻoponopono ʻana i ka lapaʻau e like me ke kūpono. Hoʻomaʻamaʻa pinepine ka hoʻoponopono mua i ka pale ʻana a i ʻole ka hoʻomāmā ʻana i ka holomua.

He aha ka manaʻolana ola me ka cardiomyopathy hypertrophic?

Loaʻa i ka nui o nā kānaka me ka cardiomyopathy hypertrophic kahi manaʻolana ola maʻamau a kokoke paha i ka maʻamau, ʻoi aku hoʻi me nā lapaʻau hou a me ka nānā ʻana. ʻOiai ke lawe nei ke kūlana i kekahi mau pilikia, ʻo ka nui o ka make makahiki he liʻiliʻi ma mua o 1% i ka nui o nā mea maʻi. Ke hilinaʻi nei kāu prognosis pilikino i nā mea e like me ka nui o nā hōʻailona, ​​​​ka mōʻaukala ʻohana, a me ka pane i ka lapaʻau.