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Mals

Nānaina

Ho okumu ka ligament arcuate waena i kahi ala ma waena o ka umauma a me ka ʻōpū no ke kīʻaha koko nui o ke kino, i kapa ʻia ʻo ka aorta. Ma ke ʻano maʻamau, hele ka ligament ma luna o ka aorta. Aia ka artery celiac ma lalo pono o ke ʻāʻī.

Hiki i ka MALS ke loaʻa i kekahi, ʻoiai nā keiki. ʻO nā inoa ʻē aʻe no ka MALS:

  • Celiac axis syndrome.
  • Dunbar syndrome.
Nā hōʻailona

Nā hōʻailona o ka MALS e komo pū ana me:

  • ʻEha ʻōpū ma hope o ka ʻai ʻana a i ʻole ka hoʻoikaika kino.
  • Ke emi ke ʻeha ʻōpū ma ka kūlou i mua a i hope paha a i ʻole ke kū ʻana i ka wā e ʻai ana.
  • Makau i ka ʻai ʻana i ka meaʻai ma muli o ka ʻeha.
  • Pau ke kaumaha me ka manaʻo ʻole.
  • Pūpū.
  • Diarrhea.
  • Nā ʻōpū a me ka luaʻi.
ʻO ka manawa hea e ʻike ai i ke kauka

He nui nā kumu like ʻole o ka ʻeha ʻōpū. Inā mau ka ʻeha ʻōpū ʻoiai me ka mālama home, kāhea i kāu limahana mālama ola. Pono ʻoe i kahi hoʻokolokolo kino piha a me nā hoʻokolohua e hoʻoholo ai i ke kumu kūikawā.

Inā ʻino loa kou ʻeha ʻōpū a ʻoi aku ka ʻino ma muli o ka hana a i ʻole ka neʻe ʻana, e kāhea koke i kāu limahana mālama ola. E kiʻi koke i ke kōkua lapaʻau inā loaʻa kāu ʻeha ʻōpū me:

  • Ka wai koko mai ka ʻōpū.
  • Ke kuni.
  • Ka luhi a me ka luaʻi ʻaʻole e hala.
  • ʻEha nui ke pā i kou ʻōpū.
  • Pehu o ka ʻōpū.
  • Melemele o ka ʻili a i ʻole nā ​​keʻokeʻo o nā maka, i kapa ʻia hoʻi he jaundice.

I kekahi manawa, hiki ke huikau ʻia ka ʻeha ʻōpū luna me ka ʻeha umauma. I kekahi manawa, hiki i ka ʻeha umauma ke loaʻa mai kahi hoʻouka naʻau. E kāhea i ka 911 a i ʻole ke kōkua lapaʻau pilikia inā loaʻa iā ʻoe ka ʻeha umauma a i ʻole ka ʻeha ʻōpū luna me a i ʻole me kekahi o kēia mau hōʻailona:

  • Ka ʻeha haki a i ʻole ka ʻeha kuni e pālahalaha ana i kou ihu, ʻāʻī, poʻohiwi, a me hoʻokahi a ʻelua paha lima.
  • Ka ʻeha e mau ana ma mua o kekahi mau minuke a ʻoi aku ka ʻino me ka hana.
  • Ka hanu pōkole.
  • Ka hou ʻana o ke anu.
  • Ka luhi a i ʻole ka nāwaliwali.
  • Ka luhi a i ʻole ka luaʻi.
Nā kumu

ʻAʻole maopopo ka kumu kūpono o ka maʻi median arcuate ligament syndrome, i kapa ʻia hoʻi ʻo MALS.

Nā mea pilikia

ʻAʻole maopopo ka kumu o ka MALS, no laila ʻaʻole maopopo nā mea pilikia. ʻOi aku ka nui o ka maʻi Median arcuate ligament syndrome i nā mākua ma mua o nā keiki. ʻOi aku hoʻi ka nui i nā wāhine ma mua o nā kāne.

Ua ʻike ʻia hoʻi ka MALS i nā māhoe hoʻokahi, no laila hiki i ka genetics ke pāʻani i kahi kuleana.

Ua loaʻa i kekahi poʻe ka maʻi median arcuate ligament syndrome ma hope o ka ʻoki ʻana o ka pancreas a i ʻole ka hōʻeha ʻana i ka ʻōpū o luna.

ʻImi ʻike

No ka hōʻoiaʻana i ka maʻi median arcuate ligament syndrome, i kapa ʻia hoʻi ʻo MALS, e nānā kekahi limahana olakino iā ʻoe a e nīnau i nā nīnau e pili ana i kou mau hōʻailona. Hiki i ke limahana olakino ke lohe i kahi kani ʻūhā, i kapa ʻia ʻo bruit, i ka hoʻolohe ʻana i kou ʻōpū me kahi stethoscope. Hiki ke hana kēia kani i ka wā e liʻiliʻi ai ka moku koko.

No ka mea, nui nā kūlana e hiki ke hoʻoulu i ka ʻeha ʻōpū, maʻamau ʻoe e loaʻa i nā hoʻokolohua he nui e ʻimi i ke kumu a kāpae i nā kūlana ʻē aʻe i hiki ke loaʻa.

ʻO nā hoʻokolohua e hōʻoiaʻiʻo i ka maʻi median arcuate ligament syndrome e komo pū paha:

  • Nā hoʻokolohua koko. Hana ʻia kēia mau hoʻokolohua e nānā i nā kūlana olakino e pili ana i ke ate, pancreas, nā puʻupaʻa a me nā ʻāpana ʻē aʻe o ke kino. Hōʻike ka helu piha o nā sela koko i ka nui o nā sela koko keʻokeʻo a me nā sela koko ʻulaʻula. Hiki i ka nui o nā sela koko keʻokeʻo ke ʻōlelo aku aia kahi maʻi.
  • Upper endoscopy. Kīaʻia kēia kaʻina hana ʻo esophagogastroduodenoscopy, i ʻike ʻia ʻo EGD. Hana ʻia ia e ʻike i ka esophagus, ʻōpū a me ka ʻāpana luna o ka ʻōpū liʻiliʻi. I ka wā o kahi EGD, e alakaʻi ke kauka i kahi paipu lōʻihi, palupalu me kahi kāmela ma ka hopena i lalo i ka ʻāʻī ma hope o ka hoʻopili ʻana i ka lāʻau lapaʻau. Eia kekahi, hiki ke wehe ʻia nā ʻāpana o nā pūnaewele, i kapa ʻia ʻo biopsies, no nā hoʻokolohua labo.
  • Magnetic resonance imaging (MRI). Hoʻohana ka MRI i nā mea huki a me nā nalu lekiō e hana i nā kiʻi kikoʻī o ka wahi kino e aʻo ʻia ana. I kekahi manawa, hāʻawi ʻia ka waihoʻoluʻu, i kapa ʻia ʻo contrast, ma o ka IV. Hōʻike ka waihoʻoluʻu i ke ʻano o ke koko e hele ana ma nā arteries. Kīaʻia kēia ʻo ka magnetic resonance angiogram, i ʻike ʻia hoʻi ʻo MRA.
  • Abdominal computerized tomography (CT). Hoʻohana ka CT scan i nā X-rays e hana i nā kiʻi cross-sectional o nā ʻāpana o ke kino. Hiki i kēia hoʻokolohua ke hōʻike inā ua liʻiliʻi a pani paha ka celiac artery. Hiki ke hāʻawi ʻia ka waihoʻoluʻu, i kapa ʻia ʻo contrast, ma o ka IV. Kūleʻa ka waihoʻoluʻu i nā moku koko e ʻike ʻia maopopo aku ma nā kiʻi hoʻokolohua. I ka wā e hoʻohana ʻia ai ka waihoʻoluʻu, kīaʻia ka hoʻokolohua ʻo computerized tomography angiogram.
  • Celiac plexus block. Hoʻokomo ʻia ka lāʻau lapaʻau i nā aʻalolo e noho ana ma kēlā ʻaoʻao o ka celiac artery. Loaʻa ka lāʻau lapaʻau no kekahi mau hola. Hoʻohālikelike kēia lapaʻau i ka mea e hana ana i ka wā o ka ʻoki e mālama i ka MALS. Hoʻohana pinepine ʻia kēia hoʻokolohua e aʻo i ka mea e hana maikaʻi ai me ka ʻoki MALS.
Ka mālama ʻana

ʻO ka ʻoki kino wale nō ka lāʻau lapaʻau no ka median arcuate ligament syndrome, i kapa ʻia hoʻi ʻo MALS. Hiki i ka ʻoki kino no ka MALS ke hoʻomaikaʻi a hoʻemi paha i nā hōʻailona i ka hapa nui o nā kānaka.

Ka mālama ponoʻī

Hoʻopili pinepine ka ʻeha a me ke kaumaha i loko o kahi pōʻaiapuni. Hiki i ka ʻeha ke hoʻonāukiuki iā ʻoe. Hiki i ke kaumaha ke hoʻoʻino i ka ʻeha. Hiki i ka ʻeha MALS ke hoʻopilikia i ka ʻai, ka hoʻoikaika kino, ka hiamoe a me nā hana o kēlā me kēia lā.

Hiki i nā ʻano hoʻomaha, e like me ka hanu hohonu a me ka noʻonoʻo, ke hoʻemi i ka ʻeha a me ka hoʻomaikaʻi ʻana i ke olakino noʻonoʻo.

Hāʻawi ka National MALS Foundation i ka ʻike a me nā pilina no nā kānaka me ka median arcuate ligament syndrome. Eia kekahi, e noi i kahi lālā o kāu hui mālama ola e hāʻawi i kahi hui kākoʻo ma kou wahi.

Ka hoʻomākaukau ʻana no kāu koho

E hoʻomaka i kahi kūkā me kāu kauka lapaʻau inā loaʻa iā ʻoe ka ʻeha ʻōpū ʻaʻole e hala a i ʻole nā ​​hōʻailona ʻē aʻe o ka median arcuate ligament syndrome.

Hiki ke pōkole kahi kūkā lāʻau lapaʻau, a nui pinepine nā mea e kūkākūkā ai. No laila, he manaʻo maikaʻi ke hoʻomākaukau pono no kāu kūkā. ʻO ka kākau ʻana i kāu papa inoa o nā nīnau a i ʻole nā ​​hopohopo kekahi o nā hana he nui āu e hiki ai ke hana e hoʻomākaukau ai no kāu kūkā.

  • E makaʻala i nā mea āpau āu e pono ai e hana ma mua o kāu kūkā. Hiki paha ke haʻi ʻia ʻaʻole ʻoe e ʻai a inu paha no kekahi mau hola ma mua o kekahi mau hoʻokolohua koko a i ʻole kiʻi.
  • E kākau i kāu mau hōʻailona a pau, me nā mea ʻaʻole paha e pili ana i ka median arcuate ligament syndrome.
  • E hana i kahi papa inoa o nā lāʻau lapaʻau a pau, nā wikamina a i ʻole nā ​​mea hoʻohui āu e lawe nei. E hoʻokomo i nā dosages a me nā kumu no ka lawe ʻana i kēlā me kēia.
  • E lawe mai i kahi lālā ʻohana a i ʻole hoaaloha pū me ʻoe, inā hiki. I kekahi manawa hiki ke paʻakikī ke hoʻomaopopo a hoʻomanaʻo i ka ʻike āpau āu e loaʻa ai i ka wā o kahi kūkā. Hiki i ka mea hele pū me ʻoe ke hoʻomanaʻo i kahi mea āu i nalo ai a poina paha.
  • E kākau i nā nīnau e nīnau i kāu kauka lapaʻau.

E papa inoa i kāu mau nīnau mai ka mea nui loa a hiki i ka mea liʻiliʻi loa inā pau ka manawa. No ka median arcuate ligament syndrome, ʻo kekahi mau nīnau kumu e nīnau ai i kāu kauka lapaʻau:

  • He aha ka mea e hiki ai ke kumu o kaʻu mau hōʻailona a i ʻole kūlana?
  • He aha nā kumu ʻē aʻe no kaʻu mau hōʻailona a i ʻole kūlana?
  • He aha nā ʻano hoʻokolohua e pono ai iaʻu?
  • He aha ka lāʻau lapaʻau maikaʻi loa?
  • He aha ka pae hana kino kūpono?
  • He aha nā mea ʻē aʻe i ka hana mua āu e manaʻo nei?
  • Loaʻa iaʻu nā kūlana olakino ʻē aʻe. Pehea ka maikaʻi o ka mālama ʻana iā lākou i ka hui?
  • Aia kekahi mau palena e pono ai iaʻu e hahai?
  • Aia kekahi ʻike e hiki iaʻu ke lawe i ka home me aʻu? He aha nā pūnaewele āu e manaʻo ai e kipa aku?

Mai kānalua e nīnau i nā nīnau ʻē aʻe.

Hiki i kāu kauka lapaʻau ke nīnau iā ʻoe i nā nīnau he nui. ʻO ka mākaukau e pane iā lākou hiki ke mālama i ka manawa e hele ai i nā hopohopo āu e makemake ai e hoʻolilo i ka manawa hou aku. Hiki i kāu hui olakino ke nīnau:

  • I ka wā hea i hoʻomaka ai nā hōʻailona?
  • Loaʻa mau iā ʻoe nā hōʻailona a i ʻole e hele mai a hele paha lākou?
  • Pehea ka nui o kou ʻeha?
  • He aha, inā he mea, e like me ka hoʻomaikaʻi ʻana i kāu mau hōʻailona?
  • He aha, inā he mea, e hoʻopilikia ai i kāu mau hōʻailona?
  • Ke pale nei ʻoe i ka ʻai ʻana a i ʻole ka hoʻoikaika kino ma muli o ka ʻeha ʻōpū?
  • Ua nalowale ʻoe i ke kaumaha?

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