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October 10, 2025
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ʻO ka maʻi ʻoihana paʻa o ka iwi he kūlana maʻi mau loa ia kahi e ulu wikiwiki ai kou mau iwi a lilo i nui, nāwaliwali, a me ka ʻano ʻole. E noʻonoʻo iā ia e like me ke kaʻina hana kūkulu iwi o kou kino e hele ana i ka overdrive ma kekahi mau wahi, e hana ana i nā iwi nui akā ʻaʻole ikaika.
ʻO ka maʻi maʻamau kēia i nā kānaka ma luna o 50 a holo pinepine i nā ʻohana. ʻOiai ke kani nei ia he mea hopohopo, nui nā kānaka me ka maʻi ʻoihana paʻa e ola ana i nā ola maʻamau, hana me ka hoʻokele kūpono a me ka mālama.
Hoʻopilikia ka maʻi ʻoihana paʻa i ke kaʻina hana hou o ka iwi maʻamau o kou kino. Ma ke ʻano maʻamau, e haki ka ʻiʻo iwi kahiko a hoʻololi ʻia e ka ʻiʻo iwi hou i kahi kaʻina kaulike.
I ka maʻi ʻoihana paʻa, e wikiwiki loa kēia kaʻina hana i kekahi mau iwi. E haki koke kou kino i ka iwi kahiko a hoʻololi iā ia me ka iwi hou e hana wikiwiki loa. Hoʻokumu kēia hana iwi wikiwiki i ka ʻiʻo iwi nui akā nāwaliwali a maʻalahi i nā pilikia.
Hoʻopili pinepine ka maʻi i nā iwi kūikawā ma mua o kou iwi āpau. ʻO kou pelvis, spine, skull, a me nā iwi wāwae nā wahi i hoʻopilikia pinepine ʻia.
Nui nā kānaka me ka maʻi ʻoihana paʻa ʻaʻohe hōʻailona, ʻoi aku hoʻi i nā wā mua. Ke ʻike ʻia nā hōʻailona, hoʻomohala pinepine lākou i ke ʻano mālie a hiki ke loli ma muli o nā iwi i hoʻopilikia ʻia.
Eia nā hōʻailona maʻamau āu e ʻike ai:
ʻO nā hōʻailona maʻamau ʻole e komo pū ai ka hoʻokaumaha ʻana o nā aʻalolo, kahi e pā ai nā iwi nui i nā aʻalolo kokoke, e hoʻoulu ai i ka ʻōʻiliʻili a i ʻole ka tingling. Loaʻa nō hoʻi i kekahi poʻe ka luhi, ʻoiai he mea ʻoi aku ka mālie a pinepine ʻia e nānā ʻole ʻia.
ʻO ka ʻeha mai ka maʻi Paget e ʻoi aku ka ʻino i ka pō a ʻaʻole paha e pane maikaʻi i nā lāʻau ʻeha maʻamau ma luna o ka papa kūʻai. Inā ʻike ʻoe i ka ʻeha iwi mau, he mea kūpono ke kūkākūkā me kāu mea lawelawe ola.
ʻAʻole maopopo loa ke kumu o ka maʻi Paget, akā manaʻo nā mea noiʻi ua loaʻa ia mai ka hui ʻana o nā kumu genetic a me nā kumu kūlohelohe e hana pū ana.
He kuleana nui kāu mau gene i kēia kūlana. Inā loaʻa iā ʻoe nā ʻohana me ka maʻi Paget, ʻoi aku ka nui o kou loaʻa ʻana iā ia iā ʻoe iho. Ua ʻike nā kānaka ʻepekema i kekahi mau gene e hoʻonui i kou pilikia, me nā mutations i ka gene SQSTM1 kekahi o nā mea maʻamau loa.
Hiki i nā kumu kūlohelohe ke hoʻoulu i ka maʻi i nā poʻe i hoʻonohonoho ʻia ma ke ʻano genetic. Manaʻo kekahi mau mea noiʻi e hiki i kekahi mau maʻi viral i ka wā mua o ke ola ke kōkua i ka hoʻomohala ʻana i ka maʻi Paget ma hope, ʻoiai ʻaʻole i hōʻoia ʻia kēia pilina.
ʻO ka makahiki kekahi kumu nui. ʻAʻole pinepine ka hopena o ke kūlana i nā poʻe ma lalo o 40 a lilo i mea maʻamau ke ʻelemakule ʻoe. ʻOi aku ka nui o nā kāne e loaʻa i ka maʻi Paget ma mua o nā wāhine.
Pono ʻoe e hoʻokaʻaʻike i kāu mea lawelawe ola inā ʻike ʻoe i ka ʻeha iwi mau ʻaʻole e hoʻomaikaʻi me ka hoʻomaha a i ʻole nā lāʻau ʻeha ma luna o ka papa kūʻai. He mea nui loa kēia inā hohonu ka ʻeha, ʻeha, a ʻoi aku ka ʻino i ka pō.
ʻO nā hōʻailona ʻē aʻe e pono ai ke nānā ʻana o ke kauka, ʻo ia nā loli i ʻike ʻia i ke ʻano o kou iwi, e like me ka kūlou ʻana o kou mau wāwae a i ʻole nā loli i ke ʻano o kou poʻo. Inā loaʻa iā ʻoe nā ʻeha iwi i wehe ʻole ʻia a i ʻole nā iwi e haki maʻalahi ma mua o ka mea i manaʻo ʻia, hiki nō hoʻi kēia ke hōʻike i ka maʻi Paget.
E ʻimi i ka mālama olakino inā loaʻa iā ʻoe nā pilikia lohe, nā ʻeha poʻo mau loa, a i ʻole nā hōʻailona neurological e like me ka ʻōʻili a i ʻole ka ʻūhā i kou mau lima a i kou mau wāwae. Hiki i kēia mau hōʻailona ke hōʻike i ka hoʻopilikia ʻana o nā iwi nui i nā aʻalolo kokoke a i ʻole nā mea ʻē aʻe.
Inā loaʻa iā ʻoe ka mōʻaukala ʻohana o ka maʻi Paget, pono ke kūkākūkā me kāu kauka e pili ana i ka nānā ʻana, ʻoiai inā ʻaʻohe ou hōʻailona. Hiki i ka ʻike mua ke kōkua i ka pale ʻana i nā pilikia a me ka hoʻomaikaʻi ʻana i kāu mau hopena lōʻihi.
Hiki i kekahi mau mea ke hoʻonui i kou manawa e loaʻa ai ka maʻi Paget, ʻo kekahi o ia mau mea i loko o kou mana a ʻo kekahi he mau ʻāpana ʻaʻole hiki ke hoʻololi ʻia o ʻoe.
ʻO nā kumu pilikia nui loa:
ʻAʻole ʻo ia hoʻi ke loaʻa iā ʻoe kēia mau kumu pilikia e loaʻa nō ʻoe i ka maʻi Paget. He nui nā kānaka me nā kumu pilikia he nui ʻaʻole loaʻa i ke kūlana, ʻoiai kekahi me nā kumu pilikia liʻiliʻi.
Me he mea lā he kuleana ko ka wahi honua, me nā helu kiʻekiʻe i loaʻa ma ʻEnelani, Scotland, ʻAusetalia, a me Niu Zilani. He mea hoihoi, he mea maʻamau loa ka maʻi ma ʻAsia a me ʻApelika, e hōʻike ana i nā hopena genetic a me ka ʻāina.
ʻOiai he nui ka poʻe me ka maʻi Paget e ola ana me ka ʻole o nā pilikia nui, hiki i ke kūlana ke alakaʻi i nā pilikia e hoʻopilikia i kou ola maikaʻi a me kou olakino holoʻokoʻa.
ʻO nā pilikia maʻamau loa āu e hālāwai ai penei:
ʻO nā pilikia koʻikoʻi akā kakaikahi hiki ke komo pū me ka maʻi kanesa o ka iwi, ʻoiai ke hana nei kēia ma lalo o 1% o nā kānaka me ka maʻi Paget. Hiki nō hoʻi ke ulu nā pōhaku kidney ma muli o ka hoʻonui ʻana o ka calcium i loko o kou koko mai ka haki wikiwiki ʻana o ka iwi.
ʻO ka ʻoiaʻiʻo maikaʻi, ʻo ka mālama kūpono ke hōʻemi nui i kou pilikia o ka loaʻa ʻana o kēia mau pilikia. Hiki i ka nānā mau a me ka lāʻau kūpono ke kōkua i ka mālama ʻana i kou mau iwi olakino a pale aku i ka nui o kēia mau pilikia mai ka hana ʻana.
Hoʻomaka pinepine ka hōʻoia ʻana o ka maʻi Paget me kāu kauka e nānā ana i kou mau hōʻailona a me ka mōʻaukala lapaʻau, a laila he nānā kino e nānā i ka palupalu o ka iwi a i ʻole nā deformities.
ʻO nā ho'okolohua koko ka hana hōʻoia mua. E nānā kāu kauka i kāu mau pae alkaline phosphatase, ka mea pinepine i hoʻokiʻekiʻe ʻia i ka maʻi Paget. Hoʻonui kēia enzyme i ka wā e haki ai a kūkulu hou ai kāu mau iwi me ka wikiwiki.
Hāʻawi nā X-rays i ka ʻike koʻikoʻi e pili ana i kou ʻano iwi a hiki ke hōʻike i nā loli hiʻohiʻona o ka maʻi Paget. Hōʻike kēia mau kiʻi i nā iwi nui, nā wahi o ka hoʻonui ʻana o ka mānoanoa o ka iwi, a me ke ʻano
Hiki ke ʻōlelo ʻia kahi scan iwi e ʻike i nā wahi āpau i pilikia ma kou iwi āpau. Hoʻopili kēia hoʻokolohua i ka hoʻopili ʻana i kahi liʻiliʻi o ka mea radioactive e hōʻiliʻili i nā wahi o ka hana ʻana o ka iwi, e kōkua ana i kāu kauka e ʻike i ka nui o ka maʻi.
I kekahi mau hihia, hiki i kāu kauka ke kauoha i kahi scan CT a i ʻole MRI no nā kiʻi kikoʻī hou aku, ʻoiai inā manaʻo ʻia nā pilikia. Hiki i kēia mau hoʻokolohua ke hōʻike i ke ʻano o ka maʻi e pili ana i nā hono kokoke, nā aʻalolo, a i ʻole nā mea ʻē aʻe.
ʻO ka pahuhopu o ka mālama ʻana i ka maʻi Paget, ʻo ia ke kaohi i kou mau hōʻailona, pale i nā pilikia, a hoʻomāmā i ke kaʻina hana iwi iwi maʻamau ʻole. ʻO ka ʻoiaʻiʻo maikaʻi, aia nā lāʻau lapaʻau maikaʻi.
ʻO nā lāʻau i kapa ʻia ʻo bisphosphonates ka lāʻau lapaʻau nui no ka maʻi Paget. Hana kēia mau lāʻau ma ka hoʻomāmā ʻana i ke kaʻina hana o ka iwi, e ʻae ana i kou mau iwi e hana maʻamau hou aku. ʻO nā bisphosphonates maʻamau e komo pū ana ʻo alendronate, risedronate, a me zoledronic acid.
E koho kāu kauka i ka lāʻau lapaʻau maikaʻi loa ma muli o kou kūlana kikoʻī. Lawe ʻia kekahi mau bisphosphonates ma ke ʻano he papa, ʻoiai ʻē aʻe ke hāʻawi ʻia ma ke ʻano he inikini. Hoʻomaopopo pinepine ʻia nā ʻano inikini no ka mea ʻoi aku ka maʻalahi a ʻoi aku ka maikaʻi.
ʻO ka mālama ʻana i ka ʻeha kekahi ʻaoʻao nui o ka mālama ʻana. Hiki i kāu kauka ke ʻōlelo aku i nā lāʻau lapaʻau ʻeha kikoʻī a i ʻole nā lāʻau anti-inflammatory e kōkua i ke kaohi ʻana i kou ʻeha. Hiki i ka physiotherapy ke kōkua i ka mālama ʻana i kou neʻe a me kou ikaika.
I nā hihia kakaikahi kahi e ulu ai nā pilikia, hiki ke pono ka ʻoki kino. Hiki ke komo pū kēia i ka hoʻololi ʻana i ka hono no ka maʻi ʻeha nui a i ʻole nā kaʻina hana e hoʻoponopono i nā deformities iwi e hoʻopilikia i kāu hana.
ʻO ka mālama ʻana i ka maʻi Paget ma ka home, ʻo ia ka hana ʻana i nā koho no ke ola e kākoʻo i kou olakino iwi a me kou olakino maikaʻi holoʻokoʻa. Hiki i nā loli liʻiliʻi i kāu hana i kēlā me kēia lā ke hoʻolilo i kahi ʻokoʻa nui i kāu manaʻo.
He mea nui ka noho ʻana i ka hana no ka mālama ʻana i kou ikaika iwi a me ka neʻe ʻana. Hiki i nā hana hoʻomaʻamaʻa haʻahaʻa e like me ka hele wāwae, ka ʻauʻau, a i ʻole ka holo paikikala ke kōkua i ka mālama ʻana i kou mau iwi a me nā hono me ka ʻole o ka hoʻoikaika nui ʻana i nā wahi i pilikia.
He kuleana nui ka meaʻai i ke olakino o nā iwi. E hōʻoia i kou loaʻa ʻana i ka calcium a me ka huaora D ma o kāu meaʻai a i ʻole nā mea hoʻohui. ʻO nā meaʻai momona i ka calcium, ʻo ia nā huahana waiū, nā lau ʻōmaʻomaʻo, a me nā meaʻai i hoʻoikaika ʻia.
Hiki i ka hoʻomehana ke kōkua i ka mālama ʻana i ka ʻeha a me ka paʻakikī. E ho'āʻo i nā ʻauʻau mahana, nā pāhana hoʻomehana, a i ʻole nā mea hoʻomehana ma nā wahi ʻeha. Loaʻa i kekahi poʻe ka hoʻololi ʻana i ka wela a me ke anu e hāʻawi i ka mea maikaʻi loa.
E hana i kahi wahi palekana ma ka home e pale aku ai i nā hāʻule a me nā haki. E wehe i nā moena palahalaha, e hōʻoia i ka mālamalama maikaʻi, a e kau i nā pā hao ma nā lumi ʻauʻau inā pono. ʻOiai ʻoi aku ka maʻalahi o nā iwi i hoʻopilikia ʻia e ka maʻi Paget i nā haki, lilo ka pale ʻana i nā hāʻule i mea nui loa.
Hiki i ka hoʻomākaukau ʻana no kāu hālāwai ke kōkua i ka hōʻoia ʻana e loaʻa iā ʻoe ka mea maikaʻi loa mai kāu manawa me kāu mea lawelawe olakino a loaʻa iā ʻoe ka mālama maikaʻi loa no kou kūlana.
E kākau i kāu mau hōʻailona a pau, me ka manawa i hoʻomaka ai lākou, ka mea e hoʻomaikaʻi ai a ʻoi aku ka maikaʻi, a pehea lākou e hoʻopilikia ai i kāu mau hana i kēlā me kēia lā. E kūikawā e pili ana i kāu mau pae ʻeha a me nā loli āu i ʻike ai i kāu mau iwi a i ʻole ka neʻe ʻana.
E lawe mai i ka papa inoa piha o nā lāʻau āpau āu e lawe nei, me nā lāʻau lapaʻau ma luna o ka pākaukau, nā mea hoʻohui, a me nā huaora. Kōkua kēia ʻike i kāu kauka e pale aku i nā pilina hiki ke loaʻa a e hoʻomaopopo i nā mālama āu i ho'āʻo mua ai.
E hōʻiliʻili i ka mōʻaukala lapaʻau o kou ʻohana, ʻoiai kekahi mau hoahānau i loaʻa iā lākou ka maʻi Paget a i ʻole nā kūlana iwi ʻē aʻe. Hiki i kēia ʻike ke koʻikoʻi no kāu ʻike maʻi a me ka hoʻolālā mālama.
E hoʻomākaukau i kahi papa inoa o nā nīnau āu e makemake ai e nīnau. E noʻonoʻo e nīnau e pili ana i nā koho mālama, nā hopena ʻaoʻao, nā hoʻololi ʻano ola, a me ka mea e manaʻo ai i ka wā e hiki mai ana. Mai kānalua e noi i ka wehewehe inā ʻaʻole maopopo kekahi mea.
E lawe mai i kahi hoaaloha a hoa ʻohana paha i hilinaʻi ʻia inā hiki. Hiki iā lākou ke kōkua iā ʻoe e hoʻomanaʻo i ka ʻike koʻikoʻi a hāʻawi i ke kākoʻo manaʻo i ka wā o kāu ʻaha kūkā.
ʻO ka maʻi Paget o ka iwi he kūlana hiki ke hoʻokele ʻia e hoʻopilikia i ke ulu ʻana a me ka hana hou ʻana o kou mau iwi. ʻOiai hiki iā ia ke hoʻokau i ka ʻeha a me nā pilikia, loaʻa nā mālama maikaʻi e kōkua iā ʻoe e mālama i kahi ola maikaʻi.
ʻO ka mea nui loa e hoʻomanaʻo ai, ʻo ka ʻike mua ʻana a me ka mālama ʻana e hiki ke pale aku i nā pilikia nui e pili ana i kēia kūlana. Inā ʻeha mau kou iwi a i ʻole he mōʻaukala ʻohana o ka maʻi Paget, mai kānalua e kūkākūkā me kāu mea mālama ola.
Me ka mālama lapaʻau kūpono, nā hoʻololi ʻano ola, a me ka nānā mau ʻana, hiki i ka hapa nui o nā kānaka me ka maʻi Paget ke ola mau i nā ola ikaika a piha. ʻO ke kī, ʻo ia ka hana pili loa me kāu hui mālama ola e ʻimi i ke ʻano mālama e kūpono loa iā ʻoe.
ʻAe, he ʻāpana genetic ikaika ka maʻi Paget. Inā loaʻa iā ʻoe kahi hoahānau mua me ke kūlana, ʻehiku mau manawa ka nui o kou pilikia ma mua o ka lehulehu. Eia naʻe, ʻaʻole hōʻoia ka loaʻa ʻana o ka predisposition genetic e loaʻa iā ʻoe ka maʻi.
ʻAʻole lāʻau lapaʻau no ka maʻi Paget, akā hiki ke hoʻokele pono ʻia me ka mālama. Hiki i nā lāʻau bisphosphonate ke hoʻolohi nui i ka holomua o ka maʻi a hāʻawi pinepine i ka hōʻoluʻolu lōʻihi mai nā hōʻailona. Loaʻa i ka poʻe he nui ka mana maikaʻi o ko lākou kūlana me ka mālama kūpono.
No ka hapa nui o nā kānaka, ʻaʻole hoʻopilikia nui ka maʻi Paget i ka lōʻihi o ke ola. Hiki ke hoʻokele ʻia ka kūlana me ka mālama, a hiki ke pale ʻia ka hapa nui o nā pilikia me ka mālama pono. I nā hihia kakaikahi wale nō kahi e ulu ai nā pilikia koʻikoʻi, e hoʻopilikia paha ka maʻi i ka lōʻihi o ke ola.
ʻOiai ʻaʻole hiki i ka ʻai wale nō ke mālama i ka maʻi Paget, ke kākoʻo nei ka mālama ʻana i ka meaʻai maikaʻi i ke olakino o nā iwi holoʻokoʻa. E hōʻoia i ka lawa o ka calcium a me ka huaora D, a mālama i ka ʻai kaulike piha i nā hua, nā huaʻai, a me nā huaola holoʻokoʻa. Loaʻa i kekahi poʻe ka emi ʻana o nā meaʻai inflammatory e kōkua ana i ka hoʻokele ʻana i ka ʻeha.
Ke hilinaʻi nei ka pinepine o nā hālāwai hahai i kou kūlana pilikino a me ka pane mālama. I ka hoʻomaka, hiki iā ʻoe ke ʻike i kāu kauka i kēlā me kēia mau mahina e nānā i ka pono o ka mālama. I ka manawa e kūpaʻa ai kou kūlana, ua lawa pinepine nā nānā makahiki, me nā hoʻokolohua koko manawa e nānā ai i kāu mau pae alkaline phosphatase.
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