He aha ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa? Nā Hōʻailona, Nā Kumu, a me ka Lapaʻau

ʻO ka hoʻi hou ʻana o nā vein pulmonary ʻaʻole loaʻa (PAPVR) kahi kūlana o ka naʻau kahi e pili ana kekahi o nā kīʻaha koko o kou māmā i kahi ʻāpana hewa o kou naʻau. Ma kahi o nā vein pulmonary ʻehā a pau e hoʻihoʻi mai ana i ke koko momona oxygen mai kou māmā i kou atrium hema, hoʻokahi a ʻoi aku paha nā vein e hoʻokahe hewa i kou atrium ʻākau a i ʻole nā ​​​​keʻena naʻau ʻē aʻe.

Hana ʻia kēia hemahema naʻau i hānau ʻia ma kahi o 0.4 a 0.7% o ka lehulehu, e hana ana i ka mea maʻamau ʻole akā ʻaʻole nui loa. Nui nā kānaka me PAPVR e ola ana i nā ola maʻamau me ka ʻike ʻole ʻana iā lākou, ʻoiai ke hoʻopili ʻia nei hoʻokahi vein wale nō.

He aha nā hōʻailona o ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa?

Nui nā kānaka me PAPVR ʻaʻole loaʻa nā hōʻailona, ​​​​ʻoiai ke māmā ka kūlana. Hoʻoholo ka nui o nā hōʻailona i ka nui o nā vein pulmonary i pili hewa ʻia a me ka nui o ke koko keu e kahe ana i ka ʻaoʻao ʻākau o kou naʻau.

Ke ʻike ʻia nā hōʻailona, ​​​​e ulu mālie lākou a hiki ke komo pū me:

• Pōkole o ka hanu i ka wā o ka hana kino a i ʻole ka hoʻoikaika kino
• Luhi maʻamau e like ʻole me kou pae hana
• Nā maʻi hanu pinepine a i ʻole ka hoʻōla lōʻihi mai nā anu
• Nā palpitations naʻau a i ʻole ka ʻike ʻana i kou puʻuwai
• Hoʻemi ʻia ka hoʻomanawanui hoʻoikaika kino i hoʻohālikelike ʻia me nā hoa
• ʻEha umauma a i ʻole ʻeha umauma māmā i ka wā o ka hoʻoikaika kino

I nā hihia nui aʻe, hiki iā ʻoe ke ʻike i ka pehu ʻana i kou mau wāwae a i ʻole nā ​​​​kuʻekuʻe wāwae, ʻoi aku hoʻi ma hope o ka lā. Loaʻa i kekahi poʻe kahi kahakaha mau ʻaʻole e like me ka maʻi.

Hiki i nā keiki me PAPVR ke hōʻike i nā ʻano ulu lohi a i ʻole e luhi maʻalahi i ka wā o ka pāʻani i hoʻohālikelike ʻia me nā keiki ʻē aʻe o ko lākou makahiki. Eia naʻe, hiki i kēia mau hōʻailona ke mālie loa a pinepine ʻia e ʻike ʻole ʻia no nā makahiki.

He aha nā ʻano o ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa?

Hoʻokaʻawale ʻia ʻo PAPVR ma muli o nā vein pulmonary i hoʻopili ʻia a me kahi e pili hewa ai lākou. ʻO ka ʻano maʻamau ka vein pulmonary ʻākau kiʻekiʻe, kahi e pili ana i kahi 90% o nā hihia PAPVR a pau.

ʻO nā ʻano nui e komo pū me:

• PAPVR vein pulmonary ʻākau kiʻekiʻe: ʻO ka ʻano pinepine loa, pinepine e kahe ana i ka vena cava kiʻekiʻe
• PAPVR vein pulmonary ʻākau haʻahaʻa: ʻAʻole pinepine, hiki ke kahe i ka vena cava haʻahaʻa a i ʻole atrium ʻākau
• PAPVR ʻaoʻao hema: ʻAʻole pinepine, e pili ana i nā vein pulmonary hema e kahe hewa ana
• Scimitar syndrome: ʻO kahi ʻano kūikawā kahi e hana ai nā vein pulmonary ʻākau i kahi ʻano wili e like me ka pahi kaua scimitar ma nā X-ray umauma

Hōʻike kēlā me kēia ʻano i nā pilikia like ʻole a hiki ke koi i nā ala lapaʻau like ʻole. E hoʻoholo kāu cardiologist i ke ʻano pololei āu e loaʻa ai ma o nā hoʻokolohua kiʻi kūikawā.

He aha ka mea e hoʻokumu ai i ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa?

E ulu ana ʻo PAPVR i ka wā hāpai mua ke hana nei kou naʻau a me nā kīʻaha koko. Hana ʻia kēia ma waena o ka ʻehā a me ka walu o nā hebedoma o ka hāpai ʻana, lōʻihi ma mua o ka ʻike ʻana o ka hapanui o nā wahine i ka manaʻo.

Hana ʻia ke kūlana ke hele iki ke kaʻina hana hoʻomohala maʻamau o ka hana ʻana o ka vein pulmonary. I ka wā o ka ulu ʻana o ka pēpē, pono e neʻe a hoʻopili nā vein pulmonary i ka atrium hema, akā i kekahi manawa ʻaʻole hoʻopau pono kēia kaʻina hana.

ʻAʻole like me kekahi mau kūlana naʻau, ʻaʻole maʻamau ka PAPVR e hoʻokumu ʻia e kekahi mea i hana a i ʻole i hana ʻole ʻia e nā mākua i ka wā hāpai. He hoʻololi wale ia i ke ʻano o ka ulu ʻana o ka naʻau, e like me ke ʻano o kekahi poʻe i hānau ʻia me nā kala maka like ʻole.

Hana ʻia ka hapa nui o nā hihia me ka ʻole o ka mōʻaukala ʻohana o nā pilikia naʻau. Eia naʻe, ma kahi liʻiliʻi, hiki i ka PAPVR ke lilo i ʻāpana o nā syndrome genetic a i ʻole e holo i nā ʻohana, ʻoiai ke hōʻike nei kēia i kahi hapa liʻiliʻi loa o nā hihia.

I ka wā e ʻike ai i ke kauka no ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa?

Pono ʻoe e kelepona i kāu kauka inā ʻike ʻoe i ka pōkole o ka hanu i wehewehe ʻole ʻia, ʻoi aku hoʻi i ka wā o nā hana i hana ʻole mua i nā pilikia hanu. He mea nui loa kēia inā e ʻike ʻia ka hanu ʻole e ʻoi aku ka nui ma mua o ka manawa.

ʻO nā hōʻailona ʻē aʻe e hopohopo nei e pono ai ka nānā ʻana o ke kauka e komo pū me ka luhi mau e hoʻopilikia ana i kāu mau hana i kēlā me kēia lā, nā maʻi hanu pinepine, a i ʻole nā ​​​​palpitations naʻau e manaʻo ʻia he ʻoluʻolu ʻole a hopohopo paha.

Inā he mākua ʻoe, e nānā i nā hōʻailona i kāu keiki e like me ka paʻakikī e mālama i nā hoa i ka wā o ka pāʻani, ka luhi maʻamau ma hope o ka hana liʻiliʻi, a i ʻole nā ​​​​anu pinepine e like me ka lōʻihi ma mua o ka manaʻo.

Mai kānalua e ʻimi i ka mālama ola kino koke inā ʻike ʻoe i ka ʻeha umauma, ka pōkole o ka hanu nui i ka hoʻomaha, a i ʻole ka hoʻopilikia koke ʻana o kekahi mau hōʻailona. ʻOiai ʻaʻole pinepine ka PAPVR e hoʻokumu i nā pilikia pōpilikia, hiki i kēia mau hōʻailona ke hōʻike i nā pilikia e pono ai ka nānā koke.

He aha nā kumu pilikia no ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa?

ʻOiai he kūlana hānau ʻia ʻo PAPVR e ulu ana ma mua o ka hānau ʻana, ʻaʻole pili nā kumu pilikia maʻamau e like me nā koho nohona. Eia naʻe, hiki i kekahi mau kūlana ke hoʻonui iki i ka hiki ke loaʻa kēia kūlana.

ʻO nā kumu pilikia nui e komo pū me:

• Mōʻaukala ʻohana o nā hemahema naʻau i hānau ʻia, ʻoiai he mea maʻamau ʻole kēia
• Ke loaʻa o nā kūlana naʻau ʻē aʻe i hānau ʻia
• Ke hānau ʻia me kekahi mau syndrome genetic
• Ka maʻi maʻi makuahine i ka wā hāpai, ʻoiai he nāwaliwali ka pilina

He mea nui e hoʻomaopopo ʻaʻole ʻo ka loaʻa ʻana o kēia mau kumu pilikia ʻaʻole ia e manaʻo e loaʻa iā ʻoe a i kāu keiki paha ʻo PAPVR. ʻAʻohe kumu pilikia i ʻike ʻia i ka hapa nui o nā kānaka me kēia kūlana.

Hoʻopili like ke kūlana i nā kāne a me nā wahine a hana ʻia ma nā hui lāhui āpau. ʻAʻole he kumu pilikia ka makahiki ʻoiai ua hānau ʻia ʻoe me ke kūlana, ʻoiai hiki ke ʻike ʻia nā hōʻailona ke ʻoi aku ka nui o kou mau makahiki.

He aha nā pilikia hiki ke loaʻa o ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa?

Nui nā kānaka me PAPVR ʻaʻole loaʻa nā pilikia, ʻoiai ke komo wale nei hoʻokahi vein pulmonary. Eia naʻe, ke kōkua ka hoʻomaopopo ʻana i nā pilikia hiki ke kōkua iā ʻoe e makaʻala i nā loli i kou olakino.

ʻO nā pilikia maʻamau e ulu mālie ana i nā makahiki a komo pū me:

• Hoʻonui ʻia ka naʻau ʻākau ma muli o ka mālama ʻana i ka nui o ke koko keu
• Hypertension pulmonary (ke koko kiʻekiʻe i nā arteries māmā)
• Hoʻonui ʻia ka pilikia o nā pilikia rhythm naʻau
• Hoʻomanawanui hoʻoikaika kino e ʻoi aku ka nui ma mua o ka manawa
• ʻOi aku ka nui o ka maʻi hanu

I nā hihia liʻiliʻi, hiki ke ulu nā pilikia koʻikoʻi, ʻoi aku hoʻi ke hoʻopili ʻia nā vein pulmonary he nui. Hiki i kēia ke komo pū me ka hāʻule naʻau, ka hypertension pulmonary nui, a i ʻole nā ​​​​hoʻololi rhythm naʻau nui.

ʻO ka ʻoiaʻiʻo maikaʻi, me ka nānā pono a me ka lapaʻau ke pono, hiki ke pale ʻia a mālama pono ʻia ka hapa nui o nā pilikia. Kūkulu nā nānā maʻamau me kāu cardiologist e hopu i nā loli mua.

Pehea e ʻike ʻia ai ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa?

ʻIke pinepine ʻia ʻo PAPVR ma ka manawa like i ka wā o nā hoʻokolohua no nā kumu ʻē aʻe, ʻoiai ʻaʻole loaʻa i ka nui o nā kānaka nā hōʻailona maopopo. Hiki i kāu kauka ke kānalua mua i ke kūlana inā lohe lākou i kahi murmur naʻau maʻamau i ka wā o ka nānā maʻamau.

Hoʻomaka pinepine ka kaʻina hana diagnostic me ka echocardiogram, kahi e hoʻohana ai i nā nalu kani e hana i nā kiʻi o kou naʻau. Hiki i kēia hoʻokolohua ke hōʻike i nā ʻano kahe koko maʻamau ʻole a kōkua i ka ʻike ʻana i kahi e hoʻopili ai kāu mau vein pulmonary.

Hiki ke komo pū nā hoʻokolohua hou aku:

• X-ray umauma e nānā i ka hoʻonui ʻana o ka naʻau a i ʻole nā ​​​​ʻano kīʻaha koko maʻamau ʻole
• MRI naʻau no nā kiʻi kikoʻī o kou ʻano naʻau a me ke kahe koko
• CT scan me ka contrast e ʻike maopopo i nā vein pulmonary
• Cardiac catheterization i kekahi mau hihia e ana i nā kaomi a hōʻoia i ka ʻike

Kōkua kēia mau hoʻokolohua i kāu cardiologist e hoʻomaopopo i nā vein i hoʻopili ʻia a me ka nui o ke koko keu e kahe ana i ka ʻāpana hewa o kou naʻau. He mea nui kēia ʻike no ka hoʻoholo ʻana inā pono ka lapaʻau.

He aha ka lapaʻau no ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa?

Hoʻoholo ka lapaʻau no PAPVR i ka nui o ke koko keu e kahe ana i ka ʻaoʻao ʻākau o kou naʻau a inā ʻoe e ʻike ana i nā hōʻailona. Nui nā kānaka me ka PAPVR māmā e pono wale nō ka nānā maʻamau me ka ʻole o kekahi ʻoki.

Ke pono ka lapaʻau, ʻo ka hoʻoponopono ʻoki ka koho nui. Hoʻopili ka ʻoki i ka hoʻohuli ʻana i nā vein pulmonary maʻamau ʻole e kahe i ka atrium hema kahi e noho ai lākou, e hoʻihoʻi ana i nā ʻano kahe koko maʻamau.

E paipai kāu cardiologist i ka ʻoki inā:

• Loaʻa iā ʻoe nā hōʻailona nui e hoʻopilikia ana i kou ola
• Ke hoʻonui nei kou naʻau ʻākau mai ka mālama ʻana i ke koko keu
• Hōʻike nā hoʻokolohua i ka nui o ke kahe koko maʻamau ʻole
• Ke hoʻomohala nei ʻoe i nā pilikia e like me ka hypertension pulmonary

Hana pinepine ʻia ka hana ʻoki ma o ka ʻoki naʻau ākea, ʻoiai ke ʻimi nei kekahi mau kikowaena i nā ala liʻiliʻi invasive. Hoʻōla maikaʻi ka hapa nui o nā mea maʻi a ʻike i ka hoʻomaikaʻi nui ʻana i kā lākou mau hōʻailona ma hope o ka ʻoki.

Inā ʻaʻole pono koke ka ʻoki, e hoʻonohonoho kāu kauka i nā hālāwai kūkākūkā ma hope e nānā i kou kūlana a e nānā i nā loli e pono ai ka hoʻoponopono ma hope.

Pehea e mālama ai i nā hōʻailona ma ka home i ka wā o ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa?

ʻOiai ʻo ka lapaʻau lapaʻau ka ala nui no PAPVR, aia kekahi mau mea hiki iā ʻoe ke hana ma ka home e kōkua i ka mālama ʻana i nā hōʻailona a kākoʻo i kou olakino naʻau holoʻokoʻa.

E nānā i ka mālama ʻana i ka olakino cardiovascular maikaʻi i loko o kou mau palena. Hiki i ka hoʻoikaika kino maʻamau, like me ka hele wāwae a i ʻole ka ʻauʻau, ke kōkua i ka hoʻoikaika ʻana i kou naʻau, akā e hoʻolohe i kou kino a mai hoʻoikaika i ka pōkole o ka hanu nui a i ʻole ka ʻeha umauma.

E makaʻala i ka pale ʻana i nā maʻi hanu, hiki ke paʻakikī loa no nā kānaka me PAPVR:

• E kiʻi i nā lāʻau ʻoki maʻi influenza makahiki a e mālama i ka lā me nā immunizations i paipai ʻia
• E holoi pinepine i kou mau lima, ʻoi aku hoʻi i ka wā anu a me ka wā maʻi
• E pale i ka pilina pili kokoke me nā kānaka maʻi ke hiki
• E noʻonoʻo e hoʻohana i ka humidifier e mālama i kou mau ala hanu i ka pulu

E mālama i kahi nohona olakino naʻau me ka ʻai kaulike, ka hiamoe lawa, a me ka hoʻokele kaumaha. ʻOiai ʻaʻole kēia e hoʻōla iā PAPVR, e kākoʻo lākou i kou olakino cardiovascular holoʻokoʻa a hiki ke kōkua iā ʻoe e ʻoluʻolu i kēlā me kēia lā.

Pehea ʻoe e hoʻomākaukau ai no kāu hālāwai kauka?

Ke hoʻomākaukau nei no kāu hālāwai cardiology e kōkua i ka hōʻoia ʻana e loaʻa iā ʻoe ka mea nui loa mai kāu kipa a ʻaʻole poina i nā nīnau koʻikoʻi a i ʻole ka ʻike.

Ma mua o kāu hālāwai, e kākau i kāu mau hōʻailona a pau, me ka wā e hana ai lākou a me ka mea e hoʻonāukiuki ai iā lākou. E hoʻomaopopo i nā loli i kou hoʻomanawanui hoʻoikaika kino a i ʻole nā ​​​​pae ikehu, ʻoiai ke ʻano liʻiliʻi lākou.

E lawe mai i kahi papa inoa piha o kāu mau lāʻau lapaʻau, me nā mea hoʻohui over-the-counter a me nā huaora. E hōʻiliʻili pū i nā hopena hoʻokolohua ma mua, ʻoi aku hoʻi nā hoʻokolohua pili naʻau e like me nā echocardiograms a i ʻole nā ​​​​X-ray umauma.

E hoʻomākaukau i kāu mau nīnau ma mua. E noʻonoʻo e nīnau e pili ana i:

• Pehea ka nui o kāu hihia PAPVR kūikawā?
• He aha nā hōʻailona e pono ai e kāhea koke?
• Aia kekahi mau palena hana e pono ai ʻoe e hahai?
• Pehea ka pinepine e pono ai nā hālāwai kūkākūkā ma hope?
• He aha nā hōʻailona e hōʻike paha e pono ai ka ʻoki ma ka wā e hiki mai ana?

E noʻonoʻo e lawe mai i kahi lālā ʻohana a i ʻole hoaaloha e kōkua iā ʻoe e hoʻomanaʻo i ka ʻike i kūkākūkā ʻia i ka wā o kāu hālāwai, ʻoi aku hoʻi inā ʻoe e manaʻo hopohopo e pili ana i ka ʻike.

He aha ka lawe ʻana i ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa?

ʻO PAPVR kahi kūlana naʻau hiki ke mālama ʻia i ola nui nā kānaka me ka holomua i ko lākou ola. ʻOiai ke kani nei ia he mea hopohopo, ʻo ka ʻoiaʻiʻo, ʻo ka hapa nui o nā hihia he māmā a ʻaʻole hoʻopilikia nui i ke ola i kēlā me kēia lā.

ʻO ka mea nui loa e hoʻomanaʻo ai ʻaʻole ʻo ka loaʻa ʻana o PAPVR ʻaʻole ia e manaʻo ʻaʻole hiki iā ʻoe ke ola i kahi ola ikaika a piha hoʻi. Me ka nānā pono o ke kauka a me ka lapaʻau ke pono, hana maikaʻi ka hapa nui o nā kānaka me kēia kūlana.

E noho pili me kāu hui mālama ola kino a mai kānalua e nīnau i nā nīnau a i ʻole e hōʻike i nā hōʻailona hou. ʻAe ka ʻike mua ʻana i nā loli i ka hoʻoponopono manawa, kahi e alakaʻi pinepine ai i nā hopena maikaʻi.

E hoʻomanaʻo e hoʻomau ka hoʻomaopopo ʻana o ke kauka a me ka lapaʻau ʻana o PAPVR e hoʻomaikaʻi. ʻO ka mea nui loa ka hana pū ʻana me kāu cardiologist e hoʻomohala i kahi hoʻolālā nānā a me ka lapaʻau kūpono no kāu kūlana kūikawā.

Nā nīnau i nīnau pinepine ʻia e pili ana i ka Hoʻi Hou ʻAna o nā Vein Pulmonary ʻAʻole Loaʻa

Hiki iā ʻoe ke hoʻoikaika kino maʻamau me PAPVR?

Hiki i ka hapa nui o nā kānaka me ka PAPVR māmā ke hoʻoikaika kino maʻamau, ʻoiai pono ʻoe e kūkākūkā i nā kuhikuhi hana me kāu cardiologist. Hiki iā lākou ke paipai i ka pale ʻana i nā hana ikaika loa a i ʻole nā ​​​​haʻuki hoʻokūkū, ma muli o kāu hihia kūikawā. E hoʻolohe i kou kino a e kū inā ʻike ʻoe i ka pōkole o ka hanu maʻamau ʻole, ʻeha umauma, a i ʻole dizziness i ka wā o ka hoʻoikaika kino.

E ʻoi aku ka maikaʻi o PAPVR ma mua o ka manawa?

ʻAʻole ʻoi aku ka maikaʻi o PAPVR iho ʻoiai he hemahema kūkulu ʻoe i hānau ʻia me ia. Eia naʻe, hiki i nā hopena ma kou naʻau ke holomua ma mua o ka manawa inā he nui ke kahe koko maʻamau ʻole. ʻO ia ke kumu e pono ai nā nānā maʻamau o ka cardiology e nānā i nā loli e pono ai ka lapaʻau.

Hiki i nā wahine me PAPVR ke loaʻa nā hāpai maʻamau?

Hiki i nā wahine he nui me PAPVR ke loaʻa nā hāpai holomua, akā pono kēia i ka nānā pono ʻana e kāu cardiologist a me ka obstetrician. Hoʻokomo ka hāpai ʻana i nā koi hou aku i kou naʻau, no laila e makemake kāu mau kauka e loiloi i kāu kūlana kūikawā a hiki ke paipai i nā nānā pinepine i ka wā hāpai.

He mea hoʻoilina anei ʻo PAPVR?

Hana ʻia ka hapa nui o nā hihia o PAPVR me ka manawa kūpono ʻole a ʻaʻole hoʻoilina ʻia mai nā mākua. Eia naʻe, aia kahi manawa liʻiliʻi e hiki ai ke holo i nā ʻohana a i ʻole e pili ana i nā kūlana genetic. Inā loaʻa iā ʻoe ka PAPVR a ke hoʻolālā nei ʻoe e loaʻa nā keiki, e kūkākūkā me kāu cardiologist a e noʻonoʻo i ka ʻōlelo aʻo genetic inā paipai ʻia.

He aha ka mea e hana ai inā waiho ʻole ʻia ʻo PAPVR me ka lapaʻau ʻole?

Nui nā kānaka me ka PAPVR māmā ʻaʻole pono ka lapaʻau a ola i nā ola maʻamau. Eia naʻe, inā waiho ʻia ke kahe koko nui maʻamau ʻole me ka lapaʻau ʻole, hiki iā ia ke alakaʻi i ka hoʻonui ʻana o ka naʻau ʻākau, ka hypertension pulmonary, a i ʻole nā ​​​​pilikia rhythm naʻau. ʻO ia ke kumu e pono ai ka nānā maʻamau, ʻoiai inā ʻaʻole ʻoe e pono i ka ʻoki i kēia manawa.