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He aha ka Pulmonary Atresia? Nā Hōʻailona, Nā Kumu, a me ka Lapaʻau
He aha ka Pulmonary Atresia? Nā Hōʻailona, Nā Kumu, a me ka Lapaʻau

Health Library

He aha ka Pulmonary Atresia? Nā Hōʻailona, Nā Kumu, a me ka Lapaʻau

October 10, 2025


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ʻO ka pulmonary atresia kahi hemahema nui o ka naʻau i loaʻa mai i ka wā hānau, kahi i hana ʻole ai ka puka pulmonary valve a i ʻole ua pani loa ia. ʻO ia hoʻi, ʻaʻole hiki i ke koko ke kahe maʻamau mai ka naʻau i nā māmā e kiʻi i ka oxygen.

Hoʻopili kēia kūlana i kahi 1 i kēlā me kēia 10,000 pēpē i hānau ʻia. ʻOiai ke kani nui nei, ua hiki i nā holomua lapaʻau ke ola piha a hana i nā keiki he nui me ka pulmonary atresia me ka lapaʻau kūpono a me ka mālama.

He aha ka Pulmonary Atresia?

Hana ʻia ka pulmonary atresia i ka wā i hana ʻole ai ka puka pulmonary valve, ka mea i noho ma waena o ka ventricle ʻākau o ka naʻau a me ka artery pulmonary, i kūpono. E noʻonoʻo iā ia e like me ka puka ʻaʻole e wehe ma waena o ʻelua lumi nui i loko o kou naʻau.

I loko o ka naʻau olakino, hoʻokuʻu ka ventricle ʻākau i ke koko ma o ka puka pulmonary valve i nā māmā. Ke loaʻa iā ʻoe ka pulmonary atresia, ua pani loa ʻia kēia ala a i ʻole ua nalowale loa. Loaʻa i ke kino o kāu pēpē nā ala hana noʻeau e lawe i ke koko i nā māmā ma o nā pilina ʻē aʻe, akā ʻaʻole ia mau mea e lilo i mau hoʻonā mau.

Aia ʻelua ʻano nui o kēia kūlana. Kaukaʻi ka ʻano inā ua ulu maʻamau ka ventricle ʻākau a i ʻole ua liʻiliʻi a hoʻomohala ʻole ʻia.

He aha nā ʻAno o ka Pulmonary Atresia?

ʻO ka pulmonary atresia me ka ventricular septum intact, ʻo ia hoʻi ua pau ka paia ma waena o nā keʻena haʻahaʻa o ka naʻau, akā maʻamau ka liʻiliʻi a hoʻomohala ʻole ʻia ka ventricle ʻākau. Pono pinepine kēia ʻano i ka lapaʻau paʻakikī loa no ka mea ʻaʻole paha i lawa ka ikaika o ka ventricle ʻākau e hoʻokuʻu pono i ke koko.

Hoʻopili ka pulmonary atresia me ka ventricular septal defect i kahi puka i loko o ka paia ma waena o nā keʻena haʻahaʻa o ka naʻau, a maʻamau ka nui o ka ventricle ʻākau. Loaʻa pinepine i kēia ʻano nā kīʻaha koko keu e kōkua i ka lawe ʻana i ke koko i nā māmā, hiki ke hoʻololi i ka hoʻolālā lapaʻau.

He aha nā Hōʻailona o ka Pulmonary Atresia?

Hōʻike ka hapa nui o nā pēpē me ka pulmonary atresia i nā hōʻailona i loko o nā lā mua a i ʻole nā pule o ke ola. ʻO ka hōʻailona i ʻike nui ʻia ʻo ia ka cyanosis, ʻo ia hoʻi, hiki i ka ʻili, nā lehelehe, a i ʻole nā kui o kāu pēpē ke nānā polū a hina paha no ka mea ʻaʻole lawa ka oxygen i lawe ʻia e ko lākou koko.

Hiki iā ʻoe ke ʻike i kekahi mau hōʻailona pilikia ʻē aʻe e hōʻike ana ʻaʻole lawa ka oxygen o kāu pēpē:

  • Paʻakikī ka hanu a i ʻole ka wikiwiki o ka hanu
  • ʻAʻole maikaʻi ka hānai a i ʻole ka luhi koke i ka wā hānai
  • Hiamoe nui a i ʻole ka nele o ka ikehu
  • Lohi ka hoʻonui ʻana o ke kaumaha ʻoiai he maikaʻi ka makemake
  • Hoʻonāukiuki a i ʻole ka hoʻonāukiuki maʻamau ʻole
  • Ke hoʻoheheʻe ʻana i ka wā hānai a i ʻole ka hana māmā

Hiki i kekahi mau pēpē ke loaʻa nā hōʻailona mālie, ʻoiai inā loaʻa iā lākou kahi kahe koko maikaʻi i ko lākou mau māmā. Eia naʻe, ʻaʻole pono e nānā ʻole ʻia nā hōʻailona māmā no ka mea hiki i ke kūlana ke ʻoi aku ka ʻino i ka pani ʻana o nā ala kākoʻo kūlohelohe ma hope o ka hānau ʻana.

He aha nā Kumu o ka Pulmonary Atresia?

Hoʻomohala ʻia ka pulmonary atresia i loko o nā hebedoma ʻewalu mua o ka hāpai ʻana i ka wā e hoʻokumu ai i ka naʻau o kāu pēpē. ʻAʻole maopopo loa ke kumu pololei, akā me he mea lā he hui pū ʻana o nā kumu genetic a me nā kumu kūlohelohe e hana pū ana.

Hana ʻia ka hapa nui o nā hihia me ka ʻole o ka mōʻaukala ʻohana o nā hemahema naʻau. Hoʻokumu ʻia nā ʻano naʻau o kāu pēpē ma o kahi kaʻina hana paʻakikī, a i kekahi manawa ʻaʻole ulu ka puka pulmonary valve e like me ia.

Hiki i kekahi mau mea ke hoʻonui iki i ka pilikia, ʻoiai ʻaʻole lākou e hoʻokumu pololei i ke kūlana. ʻO kēia mau mea e komo pū ana me ka maʻi diabetes i ka wā hāpai, ka lawe ʻana i kekahi mau lāʻau lapaʻau, a i ʻole ka loaʻa ʻana o ka mōʻaukala ʻohana o nā hemahema naʻau i hānau ʻia. Eia naʻe, hānau ʻia nā pēpē he nui me ka pulmonary atresia i nā mākua ʻaʻohe o kēia mau mea pilikia.

I ka wā e ʻike ai i ke Kauka no ka Pulmonary Atresia?

Inā hōʻike kāu pēpē i kekahi kala polū a puni ko lākou mau lehelehe, nā kui, a i ʻole ka ʻili, pono ʻoe e ʻimi koke i ka mālama lapaʻau. ʻO kēia kala polū ʻo ia hoʻi ʻaʻole lawa ka oxygen o kāu pēpē a pono i ka mālama pilikia koke.

Pono nō hoʻi ʻoe e hoʻokaʻaʻike koke i kāu pediatrician inā pilikia kāu pēpē i ka hānai ʻana, me he mea lā ua luhi loa, hanu wikiwiki, a i ʻole ʻaʻole e hoʻonui maʻamau ke kaumaha. Hiki i kēia mau hōʻailona ke hoʻomohala mālie, akā hōʻike lākou e hana nui ana ka naʻau o kāu pēpē ma mua o ia.

I nā nānā maʻamau, e hoʻolohe kāu kauka i ka naʻau o kāu pēpē a hiki ke lohe i kahi murmur naʻau. ʻOiai he nui nā murmur naʻau ʻaʻole pilikia, hiki i kekahi ke hōʻike i nā kūlana koʻikoʻi e like me ka pulmonary atresia e pono ai ka loiloi koke e kahi cardiologist pediatric.

He aha nā Mea Pilikia no ka Pulmonary Atresia?

Hiki i kekahi mau mea ke hoʻonui i ka hiki ke loaʻa i kahi pēpē me ka pulmonary atresia, ʻoiai ʻo ka loaʻa ʻana o kēia mau mea pilikia ʻaʻole ia he manaʻo e loaʻa maoli i kāu pēpē kēia kūlana. Hānau ʻia ka hapa nui o nā pēpē me ka pulmonary atresia i nā mākua ʻaʻohe o kēia mau mea.

Hoʻokani nā kumu genetic i kahi kuleana i kekahi mau hihia. Inā loaʻa iā ʻoe ka mōʻaukala ʻohana o nā hemahema naʻau i hānau ʻia, hiki ke kiʻekiʻe iki kāu pilikia. Hoʻopili pū ʻia kekahi mau syndrome genetic, e like me ka DiGeorge syndrome a i ʻole ka Noonan syndrome, me ka hoʻonui ʻana o ka pilikia o nā hemahema naʻau.

Hiki i nā kūlana olakino makuahine i ka wā hāpai ke hoʻopilikia i ka pilikia. ʻO ka loaʻa ʻana o ka maʻi diabetes, ʻoiai inā ʻaʻole i kaohi maikaʻi ʻia, hiki ke hoʻonui i ka manawa o nā hemahema naʻau. Hiki i ka lawe ʻana i kekahi mau lāʻau lapaʻau i ka wā hāpai mua, ʻoiai kekahi mau lāʻau lapaʻau no ka hoʻopaʻa ʻana a i ʻole nā ​​​​lāʻau lapaʻau acne, ke hoʻopilikia i ka hoʻomohala ʻana o ka naʻau.

Hiki i nā kumu kūlohelohe e like me ka puhipaka, ka inu ʻawaʻawa, a i ʻole ka hōʻike ʻia i kekahi mau kemika i ka wā hāpai ke hoʻopili i ka pilikia. Eia naʻe, he nui nā mākuahine e ʻike i kēia mau hōʻike i nā pēpē me nā naʻau olakino loa.

He aha nā Pilikia Hiki o ka Pulmonary Atresia?

Me ka ʻole o ka lapaʻau, hiki i ka pulmonary atresia ke alakaʻi i nā pilikia koʻikoʻi no ka mea ʻaʻole lawa ka oxygen o ke kino o kāu pēpē. ʻO ka hopohopo koke loa ʻo ia ka hiki i ka pae oxygen o kāu pēpē ke hāʻule i lalo loa, ʻoiai ke pani ʻia nā pilina kākoʻo kūlohelohe i nā lā mua ma hope o ka hānau ʻana.

I ka manawa lōʻihi, hiki i ka pulmonary atresia i mālama ʻole ʻia ke hoʻokumu i kekahi mau pilikia ma ke kino holoʻokoʻa o kāu keiki:

  • Hāʻule naʻau mai ka naʻau e hana nui ana e hoʻokuʻu i ke koko
  • Hoʻopaneʻe ʻia ka ulu a me ka hoʻomohala ʻana ma muli o ka lawa ʻole o ka oxygen
  • Hoʻonui ʻia ka pilikia o nā clots koko a me ka hahau
  • Nā pilikia o ka puʻupaʻa mai ka emi ʻana o ke kahe koko
  • Poino lolo mai ka nele o ka oxygen
  • Nā maʻi hanu pinepine

ʻOiai me ka lapaʻau, hiki i kekahi mau keiki ke kū i nā pilikia lōʻihi. Hiki i kēia ke komo pū me ka pono ʻana i nā ʻoki kino he nui i loko o ka wā kamaliʻi, ka lawe ʻana i nā lāʻau lapaʻau no ke ola, a i ʻole ka loaʻa ʻana o nā palena hana. Eia naʻe, me ka mālama lapaʻau kūpono, hiki i ka hapa nui o nā keiki ke ola i nā ola maʻamau, hana.

ʻO ka ʻoiaʻiʻo maikaʻi, ʻo ka ʻike mua ʻana a me ka lapaʻau hiki ke pale aku i ka hapa nui o kēia mau pilikia. Ua hoʻomaikaʻi nui nā ʻenehana ʻoki hou i nā hopena no nā keiki me ka pulmonary atresia.

Pehea ka Diagnosis ʻana o ka Pulmonary Atresia?

Hoʻomaopopo pinepine ʻia ka pulmonary atresia i loko o nā lā mua o ke ola i ka wā e hōʻike ai nā pēpē i nā hōʻailona o nā pae oxygen haʻahaʻa. E hoʻolohe mua kāu pediatrician i ka naʻau o kāu pēpē a hiki ke lohe i nā leo kūpono ʻole e hōʻike ana i kahi pilikia naʻau.

ʻO ka hoʻokolohua nui i hoʻohana ʻia e hoʻomaopopo i ka pulmonary atresia he echocardiogram, kahi e hoʻohana ai i nā nalu kani e hana i nā kiʻi neʻe o ka naʻau o kāu pēpē. ʻAʻole ʻeha kēia hoʻokolohua a hōʻike i nā kauka i ke ʻano o ka naʻau a pehea ke kahe koko ma o ia.

Hiki i kāu kauka ke kauoha i nā hoʻokolohua hou aku e kiʻi i kahi kiʻi piha o ka naʻau o kāu pēpē. Hiki i kahi X-ray umauma ke hōʻike i ka nui a me ke ʻano o ka naʻau a me nā māmā. Ana ka electrocardiogram (EKG) i ka hana uila o ka naʻau a hiki ke hōʻike inā hana nui ana ka naʻau ma mua o ka maʻamau.

I kekahi mau hihia, hiki i nā kauka ke hoʻohana i ka catheterization naʻau, kahi i hoʻokomo ʻia ai kahi tube lahilahi i loko o kahi kīʻaha koko a alakaʻi ʻia i ka naʻau. Hāʻawi kēia hoʻokolohua i ka ʻike kikoʻī e pili ana i ke kahe koko a me ke kaomi i loko o ka naʻau a hiki ke hoʻohana ʻia no ka lapaʻau i ka manawa like.

He aha ka Lapaʻau no ka Pulmonary Atresia?

Pono pinepine ka lapaʻau no ka pulmonary atresia i ka ʻoki kino, akā kaukaʻi ka manawa a me ke ʻano i ke kūlana kikoʻī o kāu pēpē a me ka nui o ko lākou mau hōʻailona. ʻO ka pahuhopu ke hana i kahi ala no ke koko e hiki ai i nā māmā a e hōʻoia i ka loaʻa ʻana o kāu keiki i ka oxygen lawa.

Pono nā pēpē he nui i ka mālama koke e mālama iā lākou i ka pae kūpaʻa. Hiki i kāu kauka ke hāʻawi i kahi lāʻau lapaʻau i kapa ʻia ʻo prostaglandin E1 e mālama i kekahi mau kīʻaha koko i wehe ʻia no ka manawa pōkole. Kōkua kēia lāʻau lapaʻau e mālama i ke kahe koko i nā māmā a hiki ke hana ʻia ka ʻoki kino.

Kaukaʻi ka ʻano ʻoki kino i ke ʻano o ka pulmonary atresia o kāu pēpē. No nā pēpē me ka ventricle ʻākau nui, hoʻolālā pinepine nā kauka e hana i kahi hoʻoponopono piha e ʻae ai i ka ventricle ʻākau e hoʻokuʻu i ke koko i nā māmā maʻamau. Hiki paha kēia ke komo pū me ka wehe ʻana i ka puka i pani ʻia a me ka pani ʻana i nā puka ma waena o nā keʻena naʻau.

No nā pēpē me kahi ventricle ʻākau liʻiliʻi, maʻamau ka lapaʻau i kahi papa o nā ʻoki kino i kapa ʻia ʻo single ventricle palliation. Hoʻokuʻu hou kēia mau kaʻina hana i ke kahe koko i hiki ai i hoʻokahi ventricle ke hana i ka hana o nā mea ʻelua, me ka hoʻohana ʻole ʻana i ka ventricle ʻākau hoʻomohala ʻole ʻia.

Pono kekahi mau keiki i nā kaʻina hana hou aku i ko lākou ulu ʻana. Pono paha e hoʻololi i nā valves naʻau, a pono paha e hoʻoponopono a hoʻonui i nā kīʻaha koko. E nānā pono kāu hui cardiology iā lākou a e ʻōlelo i nā lapaʻau e like me ka pono.

Pehea e Hāʻawi ai i ka Mālama Home i ka wā Lapaʻau?

ʻO ka mālama ʻana i kahi pēpē me ka pulmonary atresia ma ka home e pono ai ka nānā ʻana i ko lākou mau pono kūikawā, akā like nā ʻano o ka mālama ʻana me nā pēpē ʻē aʻe. Pono ʻoe e nānā i nā hōʻailona ʻaʻole lawa ka oxygen o kāu pēpē, e like me ka hoʻonui ʻia o ka kala polū, ka pilikia i ka hānai ʻana, a i ʻole ka luhi maʻamau ʻole.

Hiki ke lōʻihi ka hānai ʻana a pono i ka hoʻomanawanui hou aku. Hiki ke luhi koke kāu pēpē i ka wā hānai, no laila pono paha ʻoe e hāʻawi i nā ʻai liʻiliʻi a pinepine aku. Inā paʻakikī ka hānai ʻana i ka waiū umauma, hiki i kāu hui mālama ola ke kōkua iā ʻoe e ʻimi i ke ala hānai maikaʻi loa no nā pono o kāu pēpē.

E mālama i kahi kūlana mālie a me ka hopohopo ʻole o kāu pēpē. Hiki i ka uē nui a i ʻole ka hoʻonāukiuki ke hana i ka paʻakikī no lākou e loaʻa i ka oxygen lawa. Hiki i nā ʻano hoʻoluʻolu mālie a me ka mālama ʻana i kahi mahana ʻoluʻolu ke kōkua i ka mālama ʻana i kāu pēpē.

E hahai pono i kāu papa lāʻau lapaʻau e like me ka mea i kuhikuhi ʻia. Pono nā pēpē he nui me ka pulmonary atresia i nā lāʻau lapaʻau e kōkua i ka hana ʻana o ko lākou naʻau a i ʻole e pale aku i nā clots koko. Mai haʻalele i nā doses a i ʻole e hoʻōki i nā lāʻau lapaʻau me ka ʻole o ka kamaʻilio ʻana me kāu kauka mua.

He mea nui nā nānā ma hope. Pono kāu pēpē i nā nānā pinepine me ko lākou cardiologist e nānā i ko lākou kūlana a e hoʻolālā i nā lapaʻau e hiki mai ana. Kōkua kēia mau kipa e hopu koke i nā loli a e hōʻoia i ka ulu a me ka hoʻomohala ʻana o kāu pēpē e like me ka hiki.

Pehea ʻoe e Hoʻomākaukau ai no kāu Appoint Kauka?

Ma mua o kāu appointment, e kākau i nā nīnau a i ʻole nā ​​hopohopo āu e loaʻa nei. He mea maʻalahi ke poina i nā nīnau nui i ka wā e hopohopo ai ʻoe no kāu pēpē, no laila ke kōkua nei ka loaʻa ʻana o kahi papa inoa e hōʻoia iā ʻoe e loaʻa i ka ʻike āu e pono ai.

E mālama i ka moʻolelo o nā hōʻailona o kāu pēpē, me ka wā e loaʻa ai a me ka nui o ko lākou ʻano. E hoʻomaopopo i nā loli i nā ʻano hānai, nā pae hana, a i ʻole nā ​​kala. Kōkua kēia ʻike i kāu kauka e hoʻomaopopo i ke ʻano o kāu pēpē ma waena o nā kipa.

E lawe mai i kahi papa inoa o nā lāʻau lapaʻau a pau a kāu pēpē e lawe nei, me nā dosages a me ka manawa. E lawe mai pū i nā hopena hoʻokolohua mua a i ʻole nā ​​​​moʻolelo mai nā kauka ʻē aʻe. Inā he kipa mua kēia me kahi loea hou, he mea nui loa ka loaʻa ʻana o ka mōʻaukala lapaʻau piha o kāu pēpē.

E noʻonoʻo e lawe mai i kahi mea kōkua iā ʻoe i ka appointment. Hiki i ka loaʻa ʻana o kahi pākeke ʻē aʻe ke kōkua iā ʻoe e hoʻomanaʻo i nā ʻike nui a hāʻawi i ke kākoʻo manaʻo i ka wā hiki ke lilo i manawa kaumaha.

E hoʻomākaukau i nā nīnau hana e pili ana i ka mālama o kēlā me kēia lā o kāu pēpē, e like me nā kuhikuhi hānai, nā palena hana, a me nā hōʻailona hoʻomaopopo e nānā ai. Ke kōkua nei ka hoʻomaopopo ʻana i kēia mau kikoʻī iā ʻoe e ʻike hou aku i ka mālama ʻana i kāu pēpē ma ka home.

He aha ka Key Takeaway e pili ana i ka Pulmonary Atresia?

ʻO ka pulmonary atresia kahi kūlana naʻau koʻikoʻi e pono ai ka mālama lapaʻau koke a me ka lapaʻau, akā me ka mālama naʻau hou, hiki i ka hapa nui o nā keiki ke ola i nā ola piha a hana.

ʻOiai ʻo ka huakaʻi hiki ke komo pū me nā ʻoki kino he nui a me ka mālama lapaʻau mau, ulu ka nui o nā keiki me ka pulmonary atresia e komo i nā hana kamaliʻi maʻamau, hele i ke kula, a hahai i ko lākou mau moeʻuhane. E hana pū kāu hui mālama ola me ʻoe e hana i ka wā e hiki mai ana maikaʻi loa no kāu keiki.

E hoʻomanaʻo ʻaʻole ʻoe wale nō i kēia huakaʻi. Hoʻokomo nā hui naʻau pediatric i nā loea e hoʻomaopopo i nā ʻaoʻao lapaʻau a me ka manaʻo o ka mālama ʻana i nā keiki me nā kūlana naʻau. Hiki i nā hui kākoʻo a me nā ʻohana ʻē aʻe i hele i kēia ala ke hāʻawi i nā alakaʻi a me ka hoʻoikaika waiwai.

Nā Nīnau Pinepine e pili ana i ka Pulmonary Atresia

Hiki ke ʻike ʻia ka pulmonary atresia ma mua o ka hānau ʻana?

ʻAe, hiki ke ʻike ʻia ka pulmonary atresia i kekahi manawa i nā ultrasounds prenatal maʻamau, maʻamau i ka trimester ʻelua ma kahi o 18-22 mau wiki o ka hāpai ʻana. Eia naʻe, ʻaʻole ʻike ʻia nā hihia a pau ma mua o ka hānau ʻana, a ʻike ʻia kekahi mau pēpē wale nō ma hope o ka hōʻike ʻana i nā hōʻailona ma hope o ka hānau ʻana. Inā ʻike ʻia ma mua o ka hānau ʻana, e kuhikuhi kāu kauka iā ʻoe i kahi cardiologist pediatric a e kōkua iā ʻoe e hoʻolālā no ka hānau ʻana ma kahi haukapila i hoʻolako ʻia e mālama i nā pono koke o kāu pēpē.

Hiki i kaʻu keiki ke pāʻani i nā haʻuki a me ka hoʻoikaika maʻamau?

Hiki i nā keiki he nui me ka pulmonary atresia ke komo i nā hana kino, akā kaukaʻi ka pae o ka hana i ko lākou hana naʻau kikoʻī a me nā hopena ʻoki kino. E loiloi kāu cardiologist keiki i ko lākou hana naʻau maʻamau a e hāʻawi i nā kuhikuhi kikoʻī e pili ana i ka hoʻoikaika kino a me ka komo ʻana i nā haʻuki. Hiki i kekahi mau keiki ke loaʻa nā palena ʻole, ʻoiai pono paha kekahi e pale aku i nā hana ikaika loa. ʻO ke kī ke hana pū me kāu hui lapaʻau e ʻimi i ke kaulike kūpono o ka hana no ke kūlana kikoʻī o kāu keiki.

Ehia mau ʻoki kino e pono ai kaʻu keiki?

Hoʻololi nui ka nui o nā ʻoki kino ma muli o ke ʻano o ka pulmonary atresia a me ka maikaʻi o ka pane ʻana o kāu keiki i ka lapaʻau. Pono paha kekahi mau keiki me ka anatomy maikaʻi i hoʻokahi a ʻelua paha mau kaʻina hana, ʻoiai pono paha kekahi i nā ʻoki kino he nui i loko o ka wā kamaliʻi a i ka wā makua. E kūkākūkā kāu hui ʻoki kino i ka hoʻolālā lapaʻau kūpono no ke kūlana kikoʻī o kāu keiki, ʻoiai hiki ke loli nā hoʻolālā i ka ulu ʻana o kāu keiki a me ka hoʻololi ʻana o ko lākou mau pono.

He aha ka nānā lōʻihi no nā keiki me ka pulmonary atresia?

Ua hoʻomaikaʻi nui ka nānā lōʻihi i nā makahiki he nui i hala iho nei ma muli o nā holomua i nā ʻenehana ʻoki kino a me ka mālama lapaʻau. Ua ulu ka nui o nā keiki me ka pulmonary atresia e ola i nā ola maʻamau, hele i ke kula, hana, a loaʻa pū kekahi i nā ʻohana ponoʻī. Eia naʻe, pono ka hapa nui i ka nānā naʻau ola lōʻihi a pono paha i nā kaʻina hana hou aku ma ke ʻano he poʻe makua. Kaukaʻi kāu prognosis kikoʻī o kāu keiki i nā mea he nui, me ke ʻano o ka pulmonary atresia, ka holomua o kā lākou mau ʻoki kino, a me ko lākou olakino holoʻokoʻa.

Hiki i kēia kūlana ke hoʻopilikia i nā hāpai ʻana i ka wā e hiki mai ana?

Inā loaʻa iā ʻoe hoʻokahi keiki me ka pulmonary atresia, ʻoi aku ka kiʻekiʻe o kāu pilikia o ka loaʻa ʻana o kekahi keiki me kahi hemahema naʻau i hānau ʻia ma mua o ka awelika, akā emi iki. Ua hele ka hapa nui o nā ʻohana i loaʻa i hoʻokahi keiki me ka pulmonary atresia e loaʻa i nā keiki ʻē aʻe me nā naʻau olakino. Hiki i kāu kauka ke ʻōlelo i ka ʻōlelo aʻo genetic e kōkua iā ʻoe e hoʻomaopopo i kāu mau mea pilikia kikoʻī a e kūkākūkā i nā koho e like me ka nānā prenatal i hoʻonui ʻia i nā hāpai ʻana i ka wā e hiki mai ana.

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