He aha ka Pulmonary Atresia me ka Intact Ventricular Septum? Nā Hōʻailona, Nā Kumu, a me ka Lapaʻau

ʻO ka pulmonary atresia me ka intact ventricular septum kahi ʻano naʻau maʻamau loa i hānau ʻia nā pēpē me ia, kahi i hana ʻole pono ʻia ai ka puka pulmonary a pale i ke kahe koko i nā māmā. E noʻonoʻo iā ia e like me ka puka i wehe ʻole ʻia ma waena o ka naʻau a me nā māmā, e paʻakikī ai i ke koko o kāu pēpē ke loaʻa i ka oxygen e pono ai.

Hoʻopili kēia kūlana i kahi 1 i 10,000 mau pēpē a pono i ka nānā ʻana o nā kauka koke ma hope o ka hānau ʻana. ʻOiai he mea weliweli ke kani, ua hoʻomohala nā poʻe loea naʻau keiki akamai i nā lapaʻau pono e hiki ke kōkua i kāu keiki e ola i kahi ola piha a hana nui.

He aha ka Pulmonary Atresia me ka Intact Ventricular Septum?

I loko o kēia kūlana, ua pani loa ʻia a i ʻole nalowale ka puka pulmonary, e pale ana i ke kahe koko mai ka ventricle ʻākau i nā māmā. Ke kūpaʻa nei ka paia ma waena o nā keʻena haʻahaʻa o ka naʻau (ka ventricular septum), ʻokoʻa ia mai nā kūlana naʻau ʻē aʻe.

Ke ho'āʻo nei ka naʻau o kāu pēpē e uku ma ka hoʻouna ʻana i ke koko ma nā ala ʻē aʻe, akā ʻaʻole lawa kēia e hoʻolako i ka oxygen lawa i ke kino. Hoʻemi pinepine ʻia a mānoanoa hoʻi ka ventricle ʻākau, kahi e hoʻopuka ai i ke koko i nā māmā, no ka mea ʻaʻole hiki ke hoʻopuka pono i ke koko.

Hoʻokumu kēia i kahi kūlana paʻakikī kahi e hilinaʻi ai ke kahe koko o kāu pēpē i nā pilina e pani maʻamau ma hope o ka hānau ʻana. Liuliu kēia mau ala manawa a hiki i ka hoʻoponopono ʻana o ka ʻokiʻoki.

He aha nā Hōʻailona o ka Pulmonary Atresia me ka Intact Ventricular Septum?

ʻO ka hapa nui o nā pēpē me kēia kūlana e hōʻike ana i nā hōʻailona i loko o nā hola mua a i ʻole nā lā o ke ola, ʻoiai ke hakakā nei ko lākou kino e loaʻa i ka lawa o ke koko momona oxygen. Malia paha e ʻike ʻoe ua ʻāʻā a hina hina paha kāu pēpē, ʻoi aku hoʻi a puni nā lehelehe, nā manamana lima, a me nā manamana wāwae.

Eia nā hōʻailona nui āu e ʻike ai:

• ʻĀʻā a hina hina paha ke kala o ka ʻili (cyanosis), ʻoi aku hoʻi a puni ka waha a me nā kui manamana lima
• ʻO ka hanu wikiwiki a paʻakikī paha, ʻoiai ke hoʻomaha nei kāu pēpē
• ʻAi ʻole maikaʻi a luhi koke paha i ka wā e hānai ana
• Hiamoe nui a ʻike ʻole ʻia ma mua o ka mea i manaʻo ʻia
• Anuanu nā lima a me nā wāwae, ʻoiai ke mahana ka lumi
• Nāwaliwali ka puʻuwai a i ʻole ka murmur naʻau i ʻike ʻia e kāu kauka

Malia paha e hōʻike pū kekahi mau pēpē i nā hōʻailona o ka hāʻule naʻau, me ka pehu ʻana i nā wāwae, ka ʻōpū, a i ʻole a puni nā maka. Ke hana nei kēia mau hōʻailona no ka mea ke hana nui nei ka naʻau e hoʻopuka i ke koko, akā ʻaʻole hiki ke hoʻolako i ka lawa o ka oxygen e hoʻokō i nā pono o ke kino.

I nā hihia maʻamau, ʻike ʻia kekahi mau pēpē i kūpaʻa mua akā a laila e hoʻomohala i nā hōʻailona i ka wā e hoʻomaka ai nā pilina kūlohelohe e kōkua i ke kahe koko i nā māmā e pani. ʻO ia ke kumu o ka nānā mau ʻana i ka haukapila he mea nui loa ia i loko o kēlā mau lā koʻikoʻi mua.

He aha nā Kumu o ka Pulmonary Atresia me ka Intact Ventricular Septum?

Ke hoʻomohala nei kēia kūlana i loko o nā wiki mua o ka hāpai ʻana i ka wā e hoʻokumu ai ka naʻau o kāu pēpē. ʻAʻole maopopo loa ke kumu pololei, akā ʻike ʻia he hanana kūpono ʻole ia e hana ʻia i ka wā e hoʻomohala ai ka naʻau maʻamau.

ʻO ka hapa nui o nā hihia e hana me ka ʻole o kekahi kumu maopopo a i ʻole kumu kumu. ʻAʻole ia he mea āu i hana ai a i ʻole i hana ʻole ai i ka wā hāpai, a ʻaʻole ia i hana ʻia e kekahi mea āu i ʻai ai, inu ai, a i ʻike ʻia paha.

ʻAʻole like me kekahi mau kūlana naʻau ʻē aʻe, ʻaʻole pinepine ka pulmonary atresia me ka intact ventricular septum i nā ʻohana. ʻO ka hapa nui o nā hihia e hana ana i nā ʻohana me ka ʻole o ka mōʻaukala o nā pilikia naʻau.

Manaʻo nā mea noiʻi ua hopena ia mai kahi hoʻopilikia ʻana i ke kaʻina hana maʻamau o ka hoʻokumu ʻana o ka puka naʻau. I ka wā hāpai mua, ʻaʻole hoʻomohala pono nā ʻano naʻau e lilo i ka puka pulmonary, e alakaʻi ana i ka pale.

I ka wā e ʻike ai i ke Kauka no ka Pulmonary Atresia me ka Intact Ventricular Septum?

Hoʻomaopopo pinepine ʻia kēia kūlana i ka haukapila koke ma hope o ka hānau ʻana, pinepine i loko o nā hola 24 mua. Inā hōʻike kāu pēpē i kekahi hōʻailona o ke kala ʻāʻā, nā pilikia hanu, a i ʻole nā pilikia hānai, pono koke ka nānā ʻana o nā kauka.

Pono ka mālama pilikia inā ʻike ʻoe e lilo ana kāu pēpē i ʻāʻā nui, pilikia i ka hanu, a i ʻole hiamoe a pane ʻole paha. Ke hōʻike nei kēia mau hōʻailona ʻaʻole lawa ka oxygen o kāu pēpē a pono i ka hoʻoponopono ʻana o nā kauka koke.

Inā ua ʻike ʻia kāu pēpē me kēia kūlana, he mea nui nā hālāwai nānā maʻamau me kahi cardiologist keiki. E nānā kēia mau loea i ka hana naʻau o kāu keiki a hoʻoholo i ka manawa kūpono no nā kaʻina hana e pono ai.

ʻOiai ma hope o ka lapaʻau holomua, he mea nui ka mālama mau ʻana i loko o ke ola o kāu keiki. E hoʻonohonoho ka cardiologist i nā nānā maʻamau e hōʻoia i ka hana maikaʻi ʻana o ka naʻau a e hoʻoponopono i nā hopohopo hou e hiki mai ana.

He aha nā mea pilikia no ka Pulmonary Atresia me ka Intact Ventricular Septum?

Me ka ʻole o ka lapaʻau, hiki i kēia kūlana ke alakaʻi i nā pilikia koʻikoʻi i ka wā e hakakā ai ke kino o kāu pēpē e loaʻa i ka lawa o ka oxygen. ʻO ka hopohopo koke loa, ʻaʻole loaʻa i nā ʻōnaehana koʻikoʻi, me ka lolo a me nā puʻupaʻa, ka lawa o ke koko momona oxygen.

ʻO nā pilikia nui a nā kauka e nānā ai, me:

• Ka hāʻule naʻau, kahi i hiki ʻole ai i ka naʻau ke hoʻopuka pono e hoʻokō i nā pono o ke kino
• Nā rhythm naʻau kūpono ʻole (arrhythmias) ma muli o ka naʻau e hana ana ma lalo o ke kaumaha
• Ke hoʻokumu ʻana o nā clots koko i loko o ka naʻau, hiki ke hele i nā ʻōnaehana ʻē aʻe
• Hoʻopaneʻe ʻia ka ulu a me ka hoʻomohala ʻana ma muli o ka hoʻemi ʻia o ka hoʻolako ʻana o ka oxygen
• Nā pilikia puʻupaʻa a i ʻole ate mai ke kahe koko lawa ʻole
• Stroke a i ʻole ka pōʻino lolo i nā hihia koʻikoʻi

ʻOiai me ka lapaʻau, hiki i kekahi mau keiki ke kū i nā pilikia lōʻihi. Hiki i kēia ke komo pū me ka hoʻemi ʻia o ka hoʻomanawanui hoʻoikaika kino, ka pono no nā lāʻau mau, a i ʻole nā ​​​​kaʻina hana hou i ko lākou ulu ʻana.

Eia naʻe, me ka mālama kūpono o nā kauka a me ka hoʻoponopono koke, hiki ke pale ʻia a mālama ʻia paha ka nui o kēia mau pilikia. ʻO ke kī ka hana pili me kāu hui cardiology keiki e nānā i ke kūlana o kāu keiki a hoʻoponopono i nā pilikia i ka wā mua.

Pehea ka ʻike ʻia o ka Pulmonary Atresia me ka Intact Ventricular Septum?

Hoʻomaka pinepine ka ʻike ʻana i ka wā e ʻike ai nā kauka i nā hōʻailona o nā pilikia naʻau i ka wā o nā nānā pēpē maʻamau a i ʻike paha nā mākua i nā hōʻailona hopohopo. E hoʻolohe ke kauka o kāu pēpē i ka naʻau a lohe paha i nā leo maʻamau ʻole a i ʻike paha i ke kala ʻāʻā o ka ʻili.

ʻO ka ho'āʻo nui i hoʻohana ʻia e hōʻoia i ka ʻike ʻana he echocardiogram, kahi e hoʻohana ai i nā nalu kani e hana i nā kiʻi kikoʻī o ka naʻau o kāu pēpē. Ke hōʻike nei kēia ho'āʻo ʻeha ʻole i ke ʻano o ka naʻau a pehea ke kahe koko ma o ia.

Nā ho'āʻo hou aku e hiki ke hana ʻia:

• X-ray umauma e ʻike i ka nui a me ke ʻano o ka naʻau
• Electrocardiogram (ECG) e nānā i ka hana uila o ka naʻau
• Pulse oximetry e ana i nā pae oxygen i loko o ke koko
• Cardiac catheterization no ka ʻike kikoʻī hou aku e pili ana i nā kaomi naʻau a me ke kahe koko

I kekahi manawa, ʻike ʻia kēia kūlana ma mua o ka hānau ʻana i ka wā o nā ultrasound prenatal maʻamau. Inā ʻike ʻia ma mua o ka hānau ʻana, e hoʻonohonoho kāu kauka i ka mālama kūikawā e loaʻa koke ma hope o ka hānau ʻana.

Ke kōkua nei ke kaʻina hana ʻike i nā kauka e hoʻomaopopo i nā hiʻohiʻona kikoʻī o ke kūlana o kāu pēpē, me ka nui a me ka hana o ka ventricle ʻākau, he mea nui ia no ka hoʻolālā ʻana i ka lapaʻau.

He aha ka Lapaʻau no ka Pulmonary Atresia me ka Intact Ventricular Septum?

Hoʻomaka koke ka lapaʻau ma hope o ka ʻike ʻana me nā lāʻau lapaʻau e mālama i nā kīʻaha koko nui e wehe a hiki i ka hoʻoponopono ʻana o ka ʻokiʻoki. Ke kōkua nei ka lāʻau lapaʻau i kapa ʻia ʻo prostaglandin E1 e mālama i ke kahe koko i nā māmā ma o nā pilina kūlohelohe e pani maʻamau ma hope o ka hānau ʻana.

ʻO ke ala lapaʻau nui e komo pū ana i hoʻokahi a ʻoi aku paha nā kaʻina hana ʻokiʻoki, ma muli o ke ʻano kikoʻī o ka naʻau o kāu pēpē. ʻO ka pahuhopu ke hana i kahi ala no ke koko e hiki ai i nā māmā a hoʻomaikaʻi i ka hoʻolako ʻana o ka oxygen i ke kino.

Nā koho ʻokiʻoki maʻamau:

• Balloon valvuloplasty, kahi e wehe ai kahi pā popo liʻiliʻi i ka puka pulmonary i pale ʻia
• Blalock-Taussig shunt, kahi e hana ai i kahi pilina ma waena o nā arteries e hoʻomaikaʻi i ke kahe koko māmā
• Hoʻololi ʻia ka puka pulmonary i ka wā hiki ʻole ke hoʻoponopono ʻia ka puka kūlohelohe
• Kaʻina hana Fontan no nā hihia kahi i hiki ʻole ai ke hoʻoponopono ʻia ʻelua ventricle

Malia paha e pono kāu keiki i nā kaʻina hana he nui ma nā makahiki he nui i ko lākou ulu ʻana. Hoʻolālā pono ʻia ka hoʻolālā ʻokiʻoki i ke ʻano kikoʻī o ka naʻau o kāu pēpē a pehea ka hana maikaʻi ʻana o ka ventricle ʻākau.

Ma waena o nā kaʻina hana, pono kāu keiki i ka nānā mau ʻana a pono paha i nā lāʻau lapaʻau e kōkua i ka naʻau e hana me ka maikaʻi. Hiki i ka nui o nā keiki ke komo i nā hana maʻamau, ʻoiai kekahi poʻe e loaʻa paha nā palena hoʻoikaika kino.

Pehea e Hāʻawi ai i ka Mālama Home i ka wā Lapaʻau?

Ke koi nei ka mālama ʻana i kahi pēpē me kēia kūlana i ka nānā ʻana i ko lākou mau pono kūikawā, akā nui nā ʻaoʻao o ka mālama i kēlā me kēia lā e like me ka pēpē. E hāʻawi kāu hui lapaʻau i nā kuhikuhi kikoʻī no ka hānai ʻana, ka hana, a me ka wā e ʻimi ai i ke kōkua.

Nā ʻaoʻao nui o ka mālama home:

• Ke hāʻawi nei i nā lāʻau lapaʻau e like me ka mea i kuhikuhi ʻia, ʻoiai inā ʻike ʻia kāu pēpē e hana maikaʻi ana
• Ke nānā nei i nā loli i ke kala ʻili, ka hanu, a i ʻole nā ​​​​ʻano hānai
• Ke hōʻoia nei i ka loaʻa ʻana o ka lawa o ka meaʻai i kāu pēpē, e pono paha i nā hānai liʻiliʻi pinepine
• Ke pale aku nei i nā maʻi ma o ka hoʻomaʻemaʻe maikaʻi a me ka pale ʻana i nā pilina maʻi
• Ke mālama nei i nā hālāwai nānā maʻamau me kāu hui cardiology

Ua ʻike ka nui o nā mākua he mea kōkua ke aʻo i ka CPR pēpē a me ke kōkua mua maʻamau. Hiki i kāu haukapila ke hāʻawi i nā papa kūikawā no nā mākua o nā keiki me nā kūlana naʻau.

Mai kānalua e hoʻokaʻaʻike i kāu hui lapaʻau inā ʻike ʻoe i kekahi loli i ke kūlana o kāu pēpē a i loaʻa paha iā ʻoe nā hopohopo. Makemake lākou e lohe mai iā ʻoe e pili ana i kahi mea liʻiliʻi ma mua o ka nalo ʻana i kahi loli nui.

Pehea ʻoe e hoʻomākaukau ai no kāu hālāwai kauka?

Ke hoʻomākaukau nei no nā hālāwai cardiology hiki ke kōkua iā ʻoe e hana i ka nui o kāu manawa me ka hui lapaʻau a hōʻoia i ka pane ʻia o kāu mau hopohopo a pau. E kākau i kāu mau nīnau ma mua, ʻoiai he mea maʻalahi ke poina i nā kumuhana nui i ka wā o ka hālāwai.

Ma mua o kāu kipa, e ʻohi i ka ʻike e pili ana i:

• Kekahi mau loli i nā hōʻailona o kāu keiki, ka ʻai ʻana, a i ʻole ka pae hana
• Nā lāʻau lapaʻau i kēia manawa a pehea ka hoʻomanawanui o kāu keiki iā lākou
• Nā nīnau e pili ana i ka hoʻomohala ʻana o kāu keiki a me nā hana e hiki mai ana
• Nā hopohopo e pili ana i nā kaʻina hana a i ʻole nā ​​​​lapaʻau e hiki mai ana

E lawe mai i kahi papa inoa o nā lāʻau lapaʻau a pau, me nā doses a me ka manawa. Inā lawe kāu keiki i nā lāʻau lapaʻau he nui, e noʻonoʻo e lawe mai i nā hue maoli e pale aku i ka huikau.

Mai hopohopo e nīnau i nā nīnau he nui. Ke manaʻo nei a ke hoʻokipa nei kāu hui cardiology i nā nīnau mai nā mākua, a ke kōkua nei ka hoʻomaopopo ʻana i ke kūlana o kāu keiki iā ʻoe e hāʻawi i ka mālama maikaʻi ma ka home.

He aha ka lawe nui e pili ana i ka Pulmonary Atresia me ka Intact Ventricular Septum?

ʻOiai ke loaʻa ʻana o ka ʻike ʻana o ka pulmonary atresia me ka intact ventricular septum hiki ke manaʻo ʻia he mea kaumaha, he mea nui ke ʻike ʻia he kūlana hiki ke mālama ʻia kēia me ka mālama naʻau hou. Nui nā keiki me kēia kūlana e hele ana e ola i nā ola hana a hoʻokō.

ʻO ke kī i nā hopena maikaʻi loa ka ʻike mua ʻana a me ka lapaʻau ʻana e nā poʻe loea naʻau keiki akamai. E hana pū kāu hui lapaʻau me ʻoe e hoʻomohala i kahi hoʻolālā lapaʻau kūpono no nā pono kikoʻī o kāu keiki.

E hoʻomanaʻo ʻaʻole ʻoe wale nō i kēia huakaʻi. Aia kāu hui cardiology, nā nēnē, a me nā limahana kākoʻo ʻē aʻe e alakaʻi iā ʻoe ma kēlā me kēia ʻanuʻu o ka mālama ʻana o kāu keiki a pane i nā nīnau āu e loaʻa ai.

Me ka mālama kūpono o nā kauka, ka nānā mau ʻana, a me kāu kākoʻo aloha, hiki i nā keiki me kēia kūlana ke ulu a komo i ka nui o nā hana maʻamau o ka wā kamaliʻi. ʻOkoʻa ke huakaʻi o kēlā me kēia keiki, akā ke hoʻomaikaʻi mau nei ka manaʻo me ka holomua i ka mālama naʻau keiki.

Nā Nīnau Pinepine e pili ana i ka Pulmonary Atresia me ka Intact Ventricular Septum

Q1: Hiki i kaʻu keiki ke komo i nā haʻuki a me nā hana kino?

Hiki i nā keiki he nui me ka pulmonary atresia i mālama ʻia me ka holomua ke komo i nā hana kino, ʻoiai kekahi poʻe e loaʻa paha nā palena. E loiloi kāu cardiologist i ka hana naʻau o kāu keiki a e hāʻawi i nā kuhikuhi kikoʻī e pili ana i nā pae hana palekana. Hiki i kekahi mau keiki ke komo i nā haʻuki hoʻokūkū, ʻoiai kekahi poʻe e ʻōlelo ʻia e pale aku i nā hana kiʻekiʻe. ʻO ke kī ka nānā mau ʻana a me ke kamaʻilio ākea me kāu hui lapaʻau e pili ana i nā makemake a me nā hiki o kāu keiki.

Q2: Pehea ka pinepine e pono ai i kaʻu keiki nā hālāwai nānā?

ʻOkoʻa nā papa hana nānā ma muli o ke kūlana kikoʻī o kāu keiki a me ke kahua lapaʻau. I ka hoʻomaka, hiki ke pinepine nā hālāwai (kēlā me kēia mau wiki a i ʻole mau mahina), akā i ka wā e kūpaʻa ai kāu keiki, lilo pinepine nā kipa i liʻiliʻi. Pono ka nui o nā keiki i ka nānā cardiology mau loa, ʻoiai hiki ke hoʻonohonoho ʻia nā hālāwai i kēlā me kēia makahiki a i ʻole kēlā me kēia mau makahiki. E hoʻoholo kāu cardiologist i ka papa hana kūpono ma muli o nā pono o kāu keiki a pehea ka maikaʻi o kā lākou hana.

Q3: Hiki i kaʻu mau keiki e hiki mai ana ke loaʻa i ka kūlana like?

ʻO ka pilikia o ka loaʻa ʻana o kekahi keiki ʻē aʻe me ka pulmonary atresia me ka intact ventricular septum he haʻahaʻa loa ia, ʻoiai ka hapa nui o nā hihia e hana kūpono me ka ʻole o ke kumu genetic. Eia naʻe, loaʻa i nā ʻohana me hoʻokahi keiki me ka hemahema naʻau congenital kahi pilikia kiʻekiʻe iki o ka loaʻa ʻana o kekahi keiki ʻē aʻe me kekahi ʻano o ka kūlana naʻau. Hiki i kāu kauka ke kūkākūkā i kāu kūlana kikoʻī a hāʻawi paha i ka ʻōlelo aʻo genetic inā loaʻa nā hopohopo e pili ana i nā kumu hoʻoilina.

Q4: He aha kaʻu e nānā ai e hōʻike ana i kahi pilikia?

ʻO nā hōʻailona hoʻomaopopo nui, me ka hoʻonui ʻia o ke kala ʻāʻā o ka ʻili, nā lehelehe, a i ʻole nā ​​​​kui manamana lima, ka pilikia hanu a i ʻole ka hanu wikiwiki ma mua o ka maʻamau, ka hānai maikaʻi ʻole a i ʻole ka emi ʻana o ka makemake, ka hoʻonāukiuki maʻamau ʻole a i ʻole ka hiamoe, a me ka pehu ʻana o ka maka, nā lima, a i ʻole nā ​​​​wāwae. Ke koi nei kekahi loli nui i nā ʻano maʻamau o kāu keiki i kahi kelepona i kāu hui cardiology. E hilinaʻi i kāu mau manaʻo ma ke ʻano he mākua - inā ʻokoʻa a hopohopo paha kekahi mea, ʻoi aku ka maikaʻi o ka nānā ʻana me kāu hui lapaʻau.

Q5: Pono anei kaʻu keiki e lawe i nā lāʻau lapaʻau lōʻihi?

ʻOkoʻa nā pono lāʻau lapaʻau ma muli o ke kūlana kikoʻī o kāu keiki a pehea ka maikaʻi o ka hana ʻana o ko lākou naʻau ma hope o ka lapaʻau. Pono kekahi mau keiki i nā lāʻau lapaʻau no nā makahiki he nui, ʻoiai kekahi poʻe e pono wale nō iā lākou i ka manawa pōkole. Hiki i nā lāʻau lapaʻau maʻamau ke komo pū me nā mea e kōkua ai i ka naʻau e hoʻopuka me ka maikaʻi, pale i nā clots koko, a i ʻole ke kaohi i ka rhythm naʻau. E loiloi mau kāu cardiologist i nā lāʻau lapaʻau o kāu keiki a hoʻoponopono iā lākou e like me ka pono ma muli o ko lākou ulu ʻana a me ka hana naʻau.