He aha ka Truncus Arteriosus? Nā Hōʻailona, Nā Kumu, a me ka Lapaʻau

ʻO ka truncus arteriosus kahi hemahema naʻau maʻamau loa i loaʻa i ka wā hānau, kahi e lawe ai kahi moku koko nui hoʻokahi i ke koko mai ka naʻau ma kahi o nā moku ʻelua kaʻawale. Ma ke ʻano maʻamau, loaʻa i kou naʻau ʻelua mau arteries nui - ka aorta a me ka pulmonary artery - akā, hānau ʻia nā pēpē me kēia kūlana me hoʻokahi moku wale nō e hana ana i nā hana ʻelua.

Hoʻopili kēia kūlana i kahi 1 i 10,000 mau pēpē a pono i ka lapaʻau ʻoki kino i loko o ka makahiki mua o ke ola. ʻOiai ke kani nui nei, ua holomua nā holomua i ka ʻoki naʻau pediatric i hana i ka lapaʻau holomua loa i ka wā i ʻike koke ʻia.

He aha ka Truncus Arteriosus?

Hana ʻia ka truncus arteriosus i ka wā ʻaʻole i hoʻokaʻawale pono ʻia nā arteries nui o ka naʻau i ka wā hāpai mua. Ma kahi o ka hoʻomohala ʻana i ʻelua mau moku kaʻawale, noho lākou ma ke ʻano he kumu nui hoʻokahi e noho ana ma luna o nā ʻaoʻao ʻelua o ka naʻau.

Loaʻa i kēia moku hoʻokahi ke koko mai nā ventricles ʻākau a me ka hema ma o kahi puka i ka paia ma waena o lākou. A laila, holo ke koko i nā māmā, ke kino, a me nā arteries coronary a pau mai kēia kumu hoʻokahi.

E noʻonoʻo e like me ka loaʻa ʻana o hoʻokahi paipa wai nui ma kahi o ʻelua mau paipa kaʻawale no nā ʻāpana like ʻole o kou hale. ʻO ke koko hui ʻia ke ʻano he emi ka oxygen ma mua o ka maʻamau, ʻo ia ke kumu e ʻike koke ʻia ai nā hōʻailona i ke ola.

He aha nā Hōʻailona o ka Truncus Arteriosus?

Hōʻike pinepine nā pēpē me ka truncus arteriosus i nā hōʻailona i loko o nā hebedoma mua o ke ola. Hana ʻia nā hōʻailona no ka mea ʻaʻole lawa ka oxygen i kā lākou koko e hoʻokō i nā pono o ko lākou kino.

Eia nā hōʻailona maʻamau e ʻike paha ʻoe:

• ʻIli uliuli, lehelehe, a i ʻole nā ​​manikini (cyanosis), ʻoi aku hoʻi i ka wā e uē ai a i ʻai ai
• Paʻakikī ka hānai ʻana a i ʻole ka luhi koke i ka wā e hānai ai
• Hanu wikiwiki a paʻakikī paha
• Loaʻa ʻole ke kaupaona maikaʻi ʻoiai he makemake maʻamau
• Ke ʻeha nui, ʻoi aku hoʻi i ka wā e hānai ai
• Hoʻonāukiuki a huhū paha
• Nā maʻi hanu pinepine

Hiki i kekahi mau pēpē ke hoʻomohala i nā hōʻailona o ka hemahema naʻau i ka wā e hana nui ai ko lākou naʻau e hoʻopuka i ke koko. E ʻike nui ʻia kēia mau hōʻailona i ka wā e ulu ai kāu pēpē a hoʻonui ʻia kā lākou pono oxygen.

He aha nā ʻAno o ka Truncus Arteriosus?

Hoʻokaʻawale nā kauka i ka truncus arteriosus i nā ʻano like ʻole ma muli o ke ʻano o ka hoʻohui ʻana o nā arteries pulmonary i ke kumu nui. Ke kōkua ka hoʻomaopopo ʻana i ke ʻano i kāu hui lapaʻau e hoʻolālā i ke ala lapaʻau maikaʻi loa.

ʻO ke ʻano I ka ʻano maʻamau loa, kahi e puka mai ai nā arteries pulmonary mai ke kua o ka truncus. Hana ʻia ke ʻano II i ka wā e puka mai ai nā arteries pulmonary kaʻawale akā kokoke mai ke kua o ke kumu.

Hana ʻia ke ʻano III i ka wā e puka mai ai hoʻokahi a ʻelua paha mau arteries pulmonary mai ka ʻaoʻao o ka truncus. Loaʻa nō hoʻi ke ʻano IV, ʻoiai ke manaʻo nei nā loea he nui i kēia he kūlana ʻokoʻa i kapa ʻia ʻo pulmonary atresia me nā arteries aortopulmonary collateral nui.

ʻAʻole hoʻololi nui ke ʻano kikoʻī i ka hoʻolālā lapaʻau, akā kōkua ia i nā kauka ʻoki e hoʻomākaukau no ka ʻenehana hoʻoponopono maikaʻi loa no kāu keiki.

He aha ka mea e hoʻokumu ai i ka Truncus Arteriosus?

Hoʻomohala ʻia ka truncus arteriosus i loko o nā hebedoma 8 mua o ka hāpai ʻana i ka wā e hoʻomohala ana ka naʻau o kāu pēpē. ʻAʻole maopopo loa ke kumu pololei, akā hana ia i ka wā ʻaʻole i hoʻokaʻawale ʻia nā ʻano hana i loko o ka naʻau e ulu ana e like me kā lākou pono.

Hiki i kekahi mau mea ke hoʻonui i ka pilikia, ʻoiai ʻaʻohe mea hōʻailona pilikia i ʻike ʻia i ka hapa nui o nā pēpē me kēia kūlana:

• Nā kūlana genetic e like me ka DiGeorge syndrome a i ʻole 22q11.2 deletion syndrome
• Ka maʻi diabetes makuahine i ka wā hāpai
• Nā lāʻau lapaʻau i lawe ʻia i ka wā hāpai mua
• Nā maʻi viral i ka wā hāpai, e like me ka rubella
• Mōʻaukala ʻohana o nā hemahema naʻau congenital
• Ka makahiki makuahine holomua

He mea nui e hoʻomanaʻo ʻaʻohe mea āu i hana ai a i ʻole i hana ʻole ai i ka wā hāpai i hoʻokumu ai i kēia kūlana. Hana ʻia nā hemahema naʻau e like me ka truncus arteriosus i ka wā hoʻomohala mua, pinepine ma mua o kou ʻike ʻana ua hāpai ʻoe.

I ka wā e ʻike ai i ke Kauka no ka Truncus Arteriosus?

Pono ʻoe e hoʻokaʻaʻike koke i kāu pediatrician inā ʻike ʻoe i kekahi hōʻailona o ka emi ʻana o ka oxygen i loko o kāu pēpē. ʻO ka ʻili uliuli, ʻoi aku hoʻi a puni nā lehelehe a i ʻole nā ​​manikini, e koi mau ana i ka nānā ʻana i ka lāʻau lapaʻau.

ʻO nā hōʻailona pilikia ʻē aʻe e pono ai ka loiloi koke, ʻo ia ka paʻakikī o ka hānai ʻana, ka hanu wikiwiki, a i ʻole ka huhū maʻamau ʻole. Hiki paha i kāu pēpē ke ʻike ʻia he luhi nui ma mua o ka maʻamau a i ʻole ka pilikia i ka loaʻa ʻana o ke kaupaona ʻoiai e ʻai maʻamau ana.

Inā hoʻomohala kāu pēpē i nā hōʻailona o ka pilikia hanu e like me ka grunting, flaring nostrils, a i ʻole ka huki ʻana o nā ʻiʻo umauma, e ʻimi i ka mālama pilikia koke. Hōʻike kēia mau hōʻailona e hana nui ana kāu pēpē e hanu a pono i ka kōkua koke.

E hilinaʻi i kou manaʻo ma ke ʻano he mākua. Inā ʻaʻole kūpono kekahi mea me ka hanu, ka hānai ʻana, a i ʻole ke ʻano holoʻokoʻa o kāu pēpē, mai kānalua e kāhea i kāu mea mālama ola.

He aha nā Mea Pilikia no ka Truncus Arteriosus?

ʻOiai hiki ke loaʻa ka truncus arteriosus i kekahi hāpai ʻana, hiki i kekahi mau mea ke hoʻonui iki i ka hiki. Hiki i ka hoʻomaopopo ʻana i kēia mau mea pilikia ke kōkua i ka ʻike mua a me ka nānā ʻana.

Pāʻani nā mea genetic i kahi kuleana i kekahi mau hihia:

• Mōʻaukala ʻohana o nā hemahema naʻau congenital
• Nā hemahema chromosomal, ʻoi aku hoʻi ka 22q11.2 deletion syndrome
• DiGeorge syndrome
• Ka pilina makua (nā mākua pili)

Hiki i nā mea makuahine i ka wā hāpai ke komo pū:

• Ka maʻi diabetes maikaʻi ʻole ma mua a i ʻole i ka wā hāpai
• Nā lāʻau lapaʻau, ʻoi aku hoʻi kekahi mau lāʻau lapaʻau hoʻopaʻa
• Nā maʻi e like me ka rubella i ka wā hāpai mua
• Ka makahiki makuahine holomua (ma mua o 35)
• Ka puhipaka a i ʻole ka inu waiʻona i ka wā hāpai

E hoʻomanaʻo ʻaʻole ʻo ka loaʻa ʻana o nā mea pilikia ke ʻano e loaʻa ana i kāu pēpē kēia kūlana. ʻAʻohe mea hōʻailona pilikia i ʻike ʻia i ka nui o nā pēpē me ka truncus arteriosus.

He aha nā Pilikia Hiki o ka Truncus Arteriosus?

Me ka ʻole o ka lapaʻau, hiki i ka truncus arteriosus ke alakaʻi i nā pilikia koʻikoʻi i ka wā e ulu ai kāu pēpē. ʻO ka lono maikaʻi, ʻo ka hoʻoponopono ʻoki kino mua ke pale aku i ka hapa nui o kēia mau pilikia mai ka hoʻomohala ʻana.

ʻO nā mea hopohopo koke loa:

• Ka hemahema naʻau congestive i ka wā e hana nui ai ka naʻau e hoʻopuka i ke koko hui
• Ka ulu a me ka hoʻomohala maikaʻi ʻole ma muli o ka lawe ʻole ʻana o ka oxygen
• Nā maʻi hanu pinepine
• Nā manawa cyanotic kahi e hāʻule koke ai nā pae oxygen

Nā pilikia lōʻihi e hiki ke hoʻomohala me ka ʻole o ka ʻoki kino:

• Eisenmenger syndrome, kahi e hōʻino mau ʻia ai nā moku koko māmā
• Nā rhythm naʻau maʻamau ʻole (arrhythmias)
• Pilikia stroke ma muli o nā clots koko
• Make naʻau koke i nā hihia koʻikoʻi

Hōʻike kēia mau pilikia i ke kumu nui o ka hoʻoponopono ʻoki kino mua. Me ka lapaʻau kūpono, hiki i ka hapa nui o nā keiki me ka truncus arteriosus ke pale aku i kēia mau pilikia koʻikoʻi a ola i ke ola olakino.

Pehea ka Diagnosis ʻana o ka Truncus Arteriosus?

Hiki i nā kauka ke hōʻoia i ka truncus arteriosus ma o kekahi mau ala, hoʻomaka pinepine me nā ʻike hoʻokolohua kino. Hiki paha i kāu pediatrician ke lohe i kahi murmur naʻau a i ʻole e ʻike i nā hōʻailona o ka emi ʻana o ka oxygen i ka wā o nā nānā maʻamau.

ʻO ka ho'āʻo hōʻoia nui loa ka echocardiogram, kahi e hoʻohana ai i nā nalu kani e hana i nā kiʻi o ka naʻau o kāu pēpē. Hiki i kēia ho'āʻo ke hōʻike maopopo i ke ʻano o ka naʻau a me nā moku koko me ka ʻole o ka ʻoluʻolu ʻole i kāu pēpē.

Hiki i nā ho'āʻo hou ke komo pū:

• X-ray umauma e nānā i ka nui o ka naʻau a me ke ʻano o ka māmā
• Electrocardiogram (ECG) e loiloi i ka rhythm naʻau
• Pulse oximetry e ana i nā pae oxygen i ke koko
• Cardiac catheterization no nā ana kikoʻī ma mua o ka ʻoki kino
• Ho'āʻo genetic e nānā no nā syndromes pili

I kekahi manawa, ʻike ʻia ka truncus arteriosus i ka wā hāpai ma o ka fetal echocardiography. Hāʻawi kēia i kāu hui lapaʻau e hoʻolālā no ka hānau ʻana a me ka mālama koke ma hope o ka hānau ʻana.

He aha ka Lapaʻau no ka Truncus Arteriosus?

Hoʻopili mau ka lapaʻau no ka truncus arteriosus i ka ʻoki kino, maʻamau i hana ʻia i loko o ka makahiki mua o ke ola. ʻO ka pahuhopu ke hoʻokaʻawale i ke kahe koko i nā māmā a me ke kino, e hana ana i ʻelua mau ala like ʻole e like me ka naʻau maʻamau.

Ma mua o ka ʻoki kino, pono paha kāu pēpē i nā lāʻau lapaʻau e kōkua i kā lākou naʻau e hana maikaʻi aʻe. Hiki i kēia ke komo pū me nā diuretics e wehe i ka wai nui a me nā lāʻau lapaʻau e kōkua i ka naʻau e hoʻopuka ikaika aʻe.

Hoʻopili ka hoʻoponopono ʻoki kino nui i kekahi mau ʻanuʻu:

1. Ke pani ʻana i ka puka ma waena o nā keʻena haʻahaʻa o ka naʻau (VSD closure)
2. Ke hoʻohui ʻana i ka ventricle hema i ka aorta
3. Ke hana ʻana i kahi ala hou mai ka ventricle ʻākau i nā māmā me ka hoʻohana ʻana i kahi conduit
4. Ke hoʻoponopono ʻana i ka valve truncal inā pono

Pono ka hapa nui o nā keiki i nā ʻoki kino hou aʻe i ko lākou ulu ʻana no ka mea ʻaʻole ulu ka conduit me lākou. Hoʻolālā ʻia kēia mau kaʻina hana hoʻomau a emi iki ka paʻakikī ma mua o ka hoʻoponopono mua.

ʻO ka manawa o ka ʻoki kino e hilinaʻi ana i nā hōʻailona o kāu pēpē a me ka maikaʻi o ko lākou ulu ʻana. E hana pū kāu hui ʻoki naʻau me ʻoe e hoʻoholo i ka manawa kūpono loa no kāu keiki.

Pehea e Hāʻawi ai i ka Mālama Home i ka wā o ka Lapaʻau Truncus Arteriosus?

ʻO ka mālama ʻana i kahi pēpē me ka truncus arteriosus ma ka home e koi ana i ka nānā ʻana i kā lākou pono kūikawā ʻoiai e mālama ana i kahi papa hana maʻamau e like me ka hiki. E hāʻawi kāu hui mālama ola i nā kuhikuhi kikoʻī no ka mālama ʻana i kāu keiki.

Koi pinepine ka hānai ʻana i ka hoʻomanawanui hou aʻe a me ka hoʻolālā. Hiki i kāu pēpē ke luhi koke i ka wā e hānai ai, no laila, ʻoi aku ka maikaʻi o nā ʻai liʻiliʻi, pinepine ma mua o nā mea nui. Pono kekahi mau pēpē i nā pūhui kiʻekiʻe-calorie e kākoʻo i ka ulu kūpono.

E nānā no nā hōʻailona ʻaʻole lawa ka oxygen i kāu pēpē:

• Hoʻonui ʻia ka kala uliuli a puni nā lehelehe a i ʻole nā ​​manikini
• ʻOi aku ka paʻakikī o ka hānai ʻana ma mua o ka maʻamau
• Ka huhū maʻamau ʻole a i ʻole ka hoʻonāukiuki
• Nā loli i nā ʻano hanu
• Ka emi ʻana o ka pae hana

E mālama i kahi maʻemaʻe o kāu pēpē e hoʻemi i ka pilikia o ka maʻi, akā mai hoʻokaʻawale nui ʻia. ʻO ka holoi lima maʻamau a me ka pale ʻana i nā kānaka maʻi maopopo ka palekana lawa.

Ma hope o ka ʻoki kino, e hahai i nā kuhikuhi kikoʻī o kāu kauka ʻoki e pili ana i nā pae hana, ka mālama ʻana i ka ʻeha, a me nā papa manawa lāʻau lapaʻau. Hoʻōla maikaʻi ka hapa nui o nā pēpē me ka mālama a me ka nānā pono.

Pehea ʻoe e Hoʻomākaukau ai no kāu Hālāwai Kauka?

ʻO ka hoʻomākaukau ʻana no nā hālāwai me ka cardiologist a i ʻole ka kauka ʻoki o kāu pēpē e kōkua i ka hōʻoia ʻana e loaʻa iā ʻoe ka mea nui loa mai kāu kipa. E kākau i kāu mau nīnau ma mua e ʻaʻole ʻoe e poina i kekahi mea nui i ka wā o ka hālāwai.

E mālama i ka moʻolelo o nā hōʻailona o kāu pēpē, me ka wā e hana ai lākou a me ka nui o ko lākou ʻano. E hoʻomaopopo i nā loli i nā ʻano hānai, hanu, a i ʻole nā ​​pae hana mai kāu kipa hope loa.

E lawe mai i nā ʻike koʻikoʻi me ʻoe:

• Papa inoa o nā lāʻau lapaʻau a pau a me nā dosages
• Nā hopena ho'āʻo hou a i ʻole nā ​​haʻawina imaging
• Nā kāleka ʻinikua a me ka ʻike
• Nā ʻike pili no nā mea mālama ola ʻē aʻe
• Kekahi mau nīnau e pili ana i ka mālama a i ʻole ka hoʻomohala ʻana o kāu pēpē

Mai kānalua e noi i kāu hui mālama ola e wehewehe i kekahi mea āu i ʻike ʻole ai. Makemake lākou e manaʻo ʻoe i ka hilinaʻi a me ka ʻike e pili ana i ka mālama ʻana i kāu pēpē.

E noʻonoʻo e lawe mai i kahi lālā ʻohana a i ʻole hoaaloha no ke kākoʻo, ʻoi aku hoʻi i ka wā o nā kūkākūkā koʻikoʻi e pili ana i nā hoʻolālā ʻoki kino a i ʻole lapaʻau. Hiki i ka loaʻa ʻana o kekahi kanaka ʻē aʻe ke kōkua iā ʻoe e hoʻomanaʻo i nā ʻike koʻikoʻi.

He aha ka mea nui e pili ana i ka Truncus Arteriosus?

ʻO ka truncus arteriosus kahi kūlana naʻau koʻikoʻi akā hiki ke mālama ʻia e pono ai ka hoʻoponopono ʻoki kino i loko o ka makahiki mua o ke ola. Me ka ʻike mua a me ka lapaʻau kūpono, hiki i ka hapa nui o nā keiki ke manaʻo e ola i ke ola piha, hana.

Ua holomua nui nā kūleʻa no ka hoʻoponopono truncus arteriosus i nā makahiki i hala iho nei. ʻO ka hapa nui o nā keiki i loaʻa kēia ʻoki kino e hele i ka komo ʻana i nā hana kino kūpono i ko lākou makahiki, hele i ke kula maʻamau, a ulu i nā mākua olakino.

ʻOiai hiki ke manaʻo nui ka hōʻoia, e hoʻomanaʻo ʻaʻole ʻoe wale nō i kēia huakaʻi. Loaʻa i kāu hui mālama ola nā loea i loaʻa ka ʻike nui i ka mālama ʻana i kēia kūlana a me ke kākoʻo ʻana i nā ʻohana ma o ke kaʻina hana.

E kālele i ka lawe ʻana i nā mea hoʻokahi i ka manawa. Me ka mālama lapaʻau kūpono, ke kākoʻo ʻohana, a me ka hoʻomanawanui, hiki i kāu keiki ke lanakila i kēia hoʻomaka paʻakikī a ulu i nā makahiki e hiki mai ana.

Nā Nīnau Pinepine e pili ana i ka Truncus Arteriosus

Hiki i kaʻu keiki ke pāʻani haʻuki ma hope o ka ʻoki kino truncus arteriosus?

Hiki i ka hapa nui o nā keiki ke komo i nā hana kino kūpono i ko lākou makahiki ma hope o ka ʻoki kino holomua, ʻoiai pono paha lākou e pale aku i nā haʻuki hoʻokūkū nui a i ʻole nā ​​haʻuki pili. E hāʻawi kāu cardiologist i nā kuhikuhi hana kikoʻī ma muli o ka hana naʻau o kāu keiki a me ka hoʻōla ʻana. Loaʻa i nā keiki he nui ka leʻaleʻa i ka ʻauʻau, ka holo paikikala, a me nā hana leʻaleʻa ʻē aʻe me ka ʻole o nā palena.

Pehea pinepine e pono ai i kaʻu keiki nā hālāwai hoʻomau ma hope o ka ʻoki kino?

Pono pinepine nā keiki me ka truncus arteriosus i hoʻoponopono ʻia i nā hālāwai hoʻomau cardiology i ko lākou ola. I ka hoʻomaka, hiki paha i nā hālāwai ke lilo i mau mahina, a laila i kēlā me kēia makahiki a i ʻole i kēlā me kēia mau makahiki i ka wā e ulu ai kāu keiki. Kōkua kēia mau kipa e nānā i ka hana naʻau a me ka hoʻolālā no nā kaʻina hana hou e pono paha i ka wā e ulu ai kāu keiki.

Hiki i nā wāhine me ka truncus arteriosus i hoʻoponopono ʻia ke loaʻa nā keiki me ka palekana?

Hiki i nā wāhine he nui me ka truncus arteriosus i hoʻoponopono ʻia me ka holomua ke loaʻa nā hāpai olakino, ʻoiai pono lākou i ka mālama kūikawā mai kahi hui hāpai kiʻekiʻe. ʻO ka palekana e hilinaʻi ana i ka maikaʻi o ka hana ʻana o ko lākou naʻau i nā makahiki ma hope o ka hoʻoponopono ʻana. He mea nui ka ʻōlelo aʻo ma mua o ka hāpai ʻana me ka cardiologist e loiloi i nā pilikia a me nā pono pilikino.

He aha ka lōʻihi o ke ola no nā keiki me ka truncus arteriosus?

Me ka hoʻoponopono ʻoki kino holomua, hiki i ka hapa nui o nā keiki me ka truncus arteriosus ke manaʻo i ka lōʻihi o ke ola maʻamau a kokoke paha i ka maʻamau. ʻO nā hopena lōʻihi e hilinaʻi ana i nā mea e like me ka manawa o ka ʻoki kino, pehea ka maikaʻi o ka hoʻoponopono ʻana i ka manawa, a inā hoʻomohala ʻia nā pilikia naʻau hou aʻe. Loaʻa i nā mākua he nui me ka truncus arteriosus i hoʻoponopono ʻia ke ola kūʻokoʻa a loaʻa nā ʻohana ponoʻī.

Pono anei kaʻu keiki i nā lāʻau lapaʻau naʻau no ke ola?

ʻAʻole pono nā keiki a pau i nā lāʻau lapaʻau no ke ola ma hope o ka hoʻoponopono ʻana o ka truncus arteriosus, akā pono paha kekahi iā lākou e kōkua i kā lākou naʻau e hana maikaʻi. Hiki i nā lāʻau lapaʻau maʻamau ke komo pū me nā mea e pale aku ai i nā clots koko, e kaohi i ka rhythm naʻau, a i ʻole ke kākoʻo i ka hana naʻau. E loiloi mau kāu cardiologist inā pono nā lāʻau lapaʻau i ka wā e ulu ai kāu keiki a me ka hoʻopaʻa ʻana o kā lākou hana naʻau.