Created at:1/16/2025
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He kūlana naʻau maʻamau loa ka apo vascular kahi e hoʻokumu ai nā kīʻaha koko i kahi pōʻai piha a puni kou puʻu hanu a me kou puʻu ʻai. Hana kēia ke ulu ʻole nā kīʻaha koko nui kokoke i kou naʻau i ko lākou ʻano maʻamau i ka wā hāpai.
E noʻonoʻo iā ia e like me ka lei mālie akā paʻa i kāʻei ʻia a puni ʻelua mau puʻu nui i loko o kou umauma. ʻOiai ke kani nei kēia he mea hopohopo, nui nā kānaka me nā apo vascular e ola ana i nā ola maʻamau, olakino maikaʻi me ka mālama kūpono a me ka lapaʻau ke pono.
Hana ʻia ka apo vascular i ka wā e hoʻokumu ai ka aorta a me kona mau lālā i kahi ʻano apo e kāʻei ana i kou trachea (puʻu hanu) a me kou esophagus (puʻu ʻai). ʻO ka aorta kou kīʻaha koko nui e lawe ana i ke koko momona oxygen mai kou naʻau a i ke koena o kou kino.
Hoʻomohala ʻia kēia kūlana i loko o nā hebedoma mua o ka hāpai ʻana i ka wā e hoʻokumu ai ka naʻau a me nā kīʻaha koko o kāu pēpē. Ma kahi o ka wili U-ʻano maʻamau, hana nā kīʻaha koko i kahi loop piha a puni kēia mau ʻano nui.
Hiki i ka apo ke lohi a ʻaʻohe pilikia, a i ʻole hiki iā ia ke pā i kou hanu a me kou ʻai ʻana. ʻO ke kiʻekiʻe o ke kaomi e hoʻoholo ai inā e ʻike ʻoe i nā hōʻailona a pehea ka nui o lākou.
Aia nā hōʻailona o ka apo vascular ma ka pehea o ke kaomi ʻana o nā kīʻaha koko i kou puʻu hanu a me kou puʻu ʻai. Nui nā kānaka me nā apo lohi ʻaʻohe hōʻailona.
ʻO nā hōʻailona maʻamau āu e ʻike ai:
I nā pēpē a me nā keiki ʻōpio, hiki iā ʻoe ke ʻike pū i nā pilikia hānai, ka hoʻemi ʻana o ke kaupaona, a i ʻole nā maʻi hanu hou. Hoʻomaka pinepine kēia mau hōʻailona i ka wā maʻi i ka wā e hoʻonāukiuki ʻia ai nā puʻu hanu.
ʻAʻohe hōʻailona o kekahi poʻe a hiki i ka wā ma hope o ke kamaliʻi a i ʻole ka wā makua, ʻoi aku ka nui inā he lohi ka apo. Hiki i nā hōʻailona ke hoʻonui mālie i ka manawa e hoʻololi ai ka ulu ʻana i ka pilina ma waena o nā kīʻaha a me nā ʻano a puni.
Nui nā ʻano o nā apo vascular, kēlā me kēia e pili ana i nā hoʻonohonoho kīʻaha koko like ʻole. ʻO ka ʻano maʻamau loa ka mea i kapa ʻia ʻo ka aortic arch pālua, kahi āu e loaʻa ai ʻelua mau aortic arches ma mua o hoʻokahi.
Hana ʻia ka aortic arch pālua i ka wā e mau ai nā aortic arches ʻākau a hema i ka wā ulu. Hoʻohui pū kēia mau arches ʻelua ma hope o kou esophagus, e hana ana i kahi apo piha a puni kou puʻu hanu a me kou puʻu ʻai.
ʻO kekahi ʻano ʻo ka aortic arch ʻākau me ka ligamentum arteriosum hema kahi e wili ai ka aorta nui i ka ʻaoʻao ʻākau ma mua o ka hema. Hoʻopau kahi kāʻei fibrous i kapa ʻia ʻo ka ligamentum arteriosum i ka apo ma ka ʻaoʻao hema.
ʻO nā ʻano liʻiliʻi loa e komo pū me ka pulmonary artery sling, kahi e puka mai ai ka pulmonary artery hema mai ka pulmonary artery ʻākau a e kāʻei ana a puni kou puʻu hanu. Hana kēia i kaomi mai kahi kihi ʻokoʻa iki.
Hoʻomohala ʻia nā apo vascular i nā kahua mua loa o ka hāpai ʻana i ka wā e hoʻokumu ai ka naʻau a me nā kīʻaha koko o kāu pēpē. Hana kēia ma waena o ka hebedoma ʻekolu a me ka ʻewalu o ka hāpai ʻana, ma mua o kou ʻike ʻana ua hāpai ʻoe.
I ka wā ulu maʻamau, nui nā ʻano kīʻaha koko i kapa ʻia ʻo nā aortic arches e hoʻokumu ʻia a laila e hoʻololi iā lākou iho. Nui o kēia mau arches e nalowale i ka wā e ulu ai, e waiho ana i ka ʻano aortic arch maʻamau.
I nā apo vascular, ʻaʻole hana kēia kaʻina hana maʻamau e like me ka manaʻo. Ma kahi o ka nalowale a me ka hoʻololi maʻamau, mau kekahi o kēia mau ʻano kīʻaha koko mua a hana i ka hoʻokumu ʻana o ka apo.
ʻAʻole maopopo loa ke kumu o kēia. ʻAʻole ia i hana ʻia e kekahi mea āu i hana ai a i ʻole ʻaʻole i hana i ka wā hāpai. ʻAʻole ia i hoʻoilina pinepine ʻia, ʻoiai he mea maʻamau loa ia i loko o nā ʻohana.
ʻIke ʻia ka hapa nui o nā hihia he mau hoʻololi ulu maʻamau e hana ʻia i ka wā o ke kaʻina hana paʻakikī o ka hoʻokumu ʻana o ka naʻau a me nā kīʻaha koko. ʻAʻole i pili pono nā kumu kūlohelohe i ka hoʻomohala ʻana o ka apo vascular.
Pono ʻoe e hoʻokaʻaʻike i kāu kauka inā ʻoe a i ʻole kāu keiki e ʻike i nā pilikia hanu mau a i ʻole nā pilikia ʻai. ʻOiai hiki i kēia mau hōʻailona ke loaʻa i nā kumu he nui, he mea nui ia e loiloi pono ʻia.
E ʻimi i ka mālama lapaʻau koke inā ʻike ʻoe i ka hanu walaʻau ʻaʻole e hoʻomaikaʻi, ʻoi aku ka nui inā pili pū me ka ʻūhā lōʻihi a i ʻole nā pilikia hānai i nā pēpē. Pono kēia mau hōʻailona e noiʻi ʻia ʻoiai inā he mālie lākou.
E kāhea koke i kāu kauka inā ʻike ʻoe i nā pilikia hanu nui, ka waihoʻoluʻu uliuli a puni nā lehelehe a i ʻole nā kui, a i ʻole inā kū koke ka hanu o ke keiki. Hiki i kēia ke hōʻike i kaomi nui o nā puʻu hanu.
No nā pēpē, e hoʻokaʻaʻike i kāu pediatrician inā lilo ka hānai i mea paʻakikī, inā paʻakikī kou pēpē i ka hanu i ka wā a ma hope paha o ka hānai ʻana, a i ʻole inā he emi ke kaupaona. Hiki i ka loiloi mua ke kōkua i ka pale ʻana i nā pilikia.
Hana ʻia ka hapa nui o nā apo vascular me ka ʻole o nā kumu pōpilikia maopopo. Eia naʻe, aia kekahi mau kūlana kahi e kiʻekiʻe iki ai ka hiki ke loaʻa.
ʻO ka loaʻa ʻana o nā hemahema naʻau i hānau ʻia hiki ke hoʻonui i ka manawa o ka loaʻa ʻana o kahi apo vascular. Ma kahi o 5-10% o nā kānaka me nā apo vascular he mau ʻano naʻau ʻē aʻe.
He mea maʻamau loa, hiki i nā apo vascular ke holo i loko o nā ʻohana, e hōʻike ana i kahi ʻāpana genetic i kekahi mau hihia. Eia naʻe, he mea maʻamau loa kēia, a hana ka hapa nui o nā hihia i nā ʻohana ʻaʻohe mōʻaukala ma mua.
Hiki i kekahi mau syndromes genetic, e like me ka DiGeorge syndrome, ke pili i kahi pilikia kiʻekiʻe o nā apo vascular. Hoʻopili kēia mau syndromes i nā ʻōnaehana kino he nui a hoʻokomo pinepine i nā hemahema naʻau.
Ua ʻōlelo ʻia, hana ka hapa nui o nā apo vascular i nā kānaka ʻaʻohe kumu pōpilikia i ʻike ʻia. ʻIke ʻia lākou he mau hoʻololi ulu maʻamau e hana ʻia i ka wā hāpai mua.
Nui nā kānaka me nā apo vascular e ola ana i nā ola maʻamau me ka ʻole o nā pilikia nui, ʻoi aku ka nui inā he lohi ka apo a ʻaʻohe kaomi nui. Eia naʻe, hiki i kekahi mau pilikia ke hoʻomohala inā e kaomi ikaika ka apo i kou hanu a i ʻole kou ʻai ʻana.
Hiki i nā pilikia hanu ke komo pū me nā maʻi hanu hou no ka mea ʻaʻole e hoʻomaʻemaʻe pono nā airways i kaomi ʻia i nā secretions. Hiki iā ʻoe ke ʻike pū i ka intolerance hoʻomaʻamaʻa a i ʻole ka pilikia hanu i ka wā hana kino.
Hiki i nā pilikia ʻai ke alakaʻi i nā pilikia meaʻai, ʻoi aku ka nui i nā keiki e hiki ke pale aku i kekahi mau meaʻai a i ʻole ka ʻai ʻana i ka liʻiliʻi. Hiki i kēia ke hopena i ka ulu ʻana a i ʻole ke kaupaona ʻana.
I nā hihia maʻamau, hiki i ke kaomi nui ke hana i nā pilikia hanu nui a i ʻole ka aspiration pneumonia, kahi e komo ai ka meaʻai a i ʻole ka wai i loko o nā māmā. He mea maʻamau ʻole kēia mau pilikia akā pono e loaʻa ka mālama lapaʻau koke.
Hiki i ke kaomi lōʻihi ke alakaʻi i nā loli i ke ʻano o kou puʻu hanu, kahi kūlana i kapa ʻia ʻo tracheomalacia. Hana kēia i nā paia puʻu hanu i palupalu a maʻalahi i ka hiolo i ka wā hanu.
Hoʻomaka pinepine ka diagnosis ʻana o kahi apo vascular me kāu kauka e hoʻolohe ana i kou mau hōʻailona a e nānā ana iā ʻoe a i kāu keiki paha. E makaʻala lākou i nā kani hanu a me nā pilikia ʻai.
ʻO ka hoʻokolohua kiʻi mua pinepine kahi X-ray umauma, kahi e hōʻike ai i ke kūlana maʻamau ʻole o nā kīʻaha koko a i ʻole nā hōʻailona o ke kaomi airway. Eia naʻe, ʻaʻole mau e hōʻike maopopo nā X-rays i nā apo vascular.
Hāʻawi kahi CT scan a i ʻole MRI i nā kiʻi ʻoi aku ka maopopo o kou mau kīʻaha koko a me ko lākou pilina i kou puʻu hanu a me kou esophagus. Hiki i kēia mau hoʻokolohua ke hōʻike maopopo inā aia kahi apo vascular a pehea ka nui o ke kaomi.
Hiki i kāu kauka ke ʻōlelo aku i kahi barium swallow study, kahi āu e inu ai i ka wai hoʻohālikelike e hōʻike ʻia ma nā X-rays. Hiki i kēia hoʻokolohua ke hōʻike i ke kaomi ʻana o kou esophagus a kōkua i ka loiloi ʻana i ka hana ʻai ʻana.
Hoʻokō pinepine ʻia kahi echocardiogram (ultrasound naʻau) e nānā i nā hemahema naʻau ʻē aʻe e hana pū pinepine me nā apo vascular. Hoʻohana kēia hoʻokolohua i nā nalu kani e hana i nā kiʻi o kou ʻano naʻau a me ka hana.
Aia ka lapaʻau no ka apo vascular ma ka loaʻa ʻana o nā hōʻailona a pehea ka nui o lākou. Nui nā kānaka me nā apo lohi ʻaʻohe pilikia pono wale nō ka nānā mau me ka ʻole o kahi lapaʻau kūikawā.
Inā loaʻa iā ʻoe nā hōʻailona nui, ʻo ka ʻoki pinepine ka lapaʻau i ʻōlelo ʻia. Hoʻokomo ka ʻano ʻoki ʻana i ka hoʻokaʻawale ʻana i kahi ʻāpana o ka apo vascular e hoʻomaha i ke kaomi ʻana ʻoiai e mālama ana i ke kahe koko maʻamau.
ʻO ka ʻoki ʻana maʻamau loa e komo pū ana i ka hoʻokaʻawale ʻana i ka ʻāpana liʻiliʻi a i ʻole ka mea nui ʻole o ka apo. No ka aortic arch pālua, hoʻokaʻawale pinepine nā kauka i ka arch liʻiliʻi, ma ka ʻaoʻao hema.
He mea holomua loa nā ʻano ʻoki hou, me ka nui o nā kānaka e ʻike ana i ka hoʻomaikaʻi nui ʻana i ko lākou mau hōʻailona. Hoʻokō pinepine ʻia ka ʻoki ma o kahi ʻoki liʻiliʻi ma ka ʻaoʻao o kou umauma.
Hoʻomaʻamaʻa pinepine ka hoʻōla ʻana mai ka ʻoki ʻana i nā hebedoma he nui, a hiki i ka hapa nui o nā kānaka ke hoʻi i nā hana maʻamau i loko o kekahi mau mahina. He mea maikaʻi loa nā hopena lōʻihi, me ka nui o nā kānaka e ola ana i nā ola maʻamau loa ma hope o ka lapaʻau.
ʻOiai ke kali nei no ka lapaʻau a i ʻole inā loaʻa iā ʻoe nā hōʻailona mālie, aia kekahi mau mea āu e hiki ai ke hana ma ka home e kōkua i ka hoʻokele ʻana i kou kūlana. Hiki i kēia mau ana ke hāʻawi i ka hōʻoluʻolu a pale aku i nā pilikia.
No nā pilikia hanu, e ho'āʻo e pale aku i nā mea hoʻonāukiuki hanu e like me ka uahi, nā mea ʻala ikaika, a i ʻole ka lepo. Hiki i ka mālama ʻana i kou home maʻemaʻe a me ka hoʻohana ʻana i nā mea hoʻomaʻemaʻe ea ke kōkua i ka hoʻemi ʻana i ka hoʻonāukiuki airway.
Inā paʻakikī ka ʻai ʻana, e ʻai i nā meaʻai liʻiliʻi, pinepine a ʻai pono i ka meaʻai. He mea maʻalahi pinepine nā meaʻai palupalu a me nā wai ma mua o nā meaʻai paʻa a i ʻole nā meaʻai nui.
E noho pololei no ka liʻiliʻi o 30 mau minuke ma hope o ka ʻai ʻana e kōkua i ka neʻe ʻana o ka meaʻai ma o kou esophagus. Hoʻohana kēia kūlana i ka gravity e kōkua i ka ʻai ʻana a hoʻemi i ka pilikia o ka pili ʻana o ka meaʻai.
E mālama pono iā ʻoe iho i ka wai, ʻoiai ke kōkua nei ka inu wai lawa e hoʻonui i nā secretions a hana iā lākou i mea maʻalahi ke hoʻomaʻemaʻe mai kou airways. Eia naʻe, e pale aku i ka inu ʻana i ka nui o ka wai i ka wā e ʻai ana inā paʻakikī ka ʻai ʻana.
Ma mua o kāu hālāwai, e kākau i kāu mau hōʻailona a pau, me ka wā i hoʻomaka ai lākou a me ka mea e hoʻomaikaʻi ai a i ʻole ka hoʻopilikia ʻana iā lākou. Kōkua kēia ʻike i kāu kauka e hoʻomaopopo maikaʻi i kou kūlana.
E hana i kahi papa inoa o nā lāʻau lapaʻau, nā mea hoʻohui, a me nā wikamina āu e lawe nei. E hoʻomākaukau pū i kahi mōʻaukala lapaʻau ʻohana, ʻoi aku ka nui o ka hoʻomaopopo ʻana i nā kūlana naʻau a i ʻole nā hemahema hānau i nā hoahānau.
E kākau i nā nīnau āu e makemake ai e nīnau i kāu kauka. Hiki i nā nīnau nui ke komo pū me ke koʻikoʻi o kou kūlana, nā koho lapaʻau, a me ka mea e manaʻo ai i ka wā e hiki mai ana.
Inā no kāu keiki kēia, e lawe mai i kā lākou mau papa kuhikuhi ulu a me nā moʻolelo hānai inā loaʻa. E noʻonoʻo pū e lawe mai i kahi hoa a i ʻole kahi ʻohana no ke kākoʻo a e kōkua i ka hoʻomanaʻo ʻana i ka ʻike.
E hoʻomākaukau e kūkākūkā pehea e hoʻopilikia ai nā hōʻailona i kou ola i kēlā me kēia lā a i ʻole nā hana o kāu keiki. Kōkua kēia i kāu kauka e hoʻomaopopo i ka hopena o ke kūlana a alakaʻi i nā hoʻoholo lapaʻau.
He kūlana naʻau maʻamau akā hiki ke hoʻokele ʻia ka apo vascular kahi e hoʻokumu ai nā kīʻaha koko i kahi apo a puni kou puʻu hanu a me kou puʻu ʻai. ʻOiai ke kani nei ia he mea hopohopo, nui nā kānaka e ola ana i nā ola maʻamau me kēia kūlana.
ʻO ka mea nui loa e hoʻomanaʻo ai, he mea maikaʻi loa ka lapaʻau ke loaʻa nā hōʻailona. Hāʻawi nā ʻano ʻoki hou i nā hopena maikaʻi loa me nā pilikia haʻahaʻa a me nā hopena lōʻihi maikaʻi.
Inā loaʻa iā ʻoe nā hōʻailona mālie a i ʻole ʻaʻohe hōʻailona, ʻo ka nānā mau me kāu kauka pinepine ka mea āpau e pono ai. E kōkua kāu hui lapaʻau iā ʻoe e hoʻoholo i ke ala kūpono no kāu kūlana kūikawā.
Me ka mālama lapaʻau kūpono, hiki i nā kānaka me nā apo vascular ke manaʻo e ola i nā ola piha, hana. Mai kānalua e kūkākūkā i nā hopohopo me kāu mea hoʻolako mālama ola, ka mea hiki ke hāʻawi i nā kuhikuhi pilikino ma muli o kāu mau kūlana pilikino.
ʻAʻole hiki ke pale ʻia ka apo vascular no ka mea e hoʻomohala ʻia ana i ka wā hāpai mua ma ke ʻano he ʻāpana o ka hoʻokumu ʻana o ka naʻau a me nā kīʻaha koko. ʻAʻole ia i hana ʻia e kekahi mea a nā mākua e hana ai a i ʻole ʻaʻole e hana i ka wā hāpai. ʻIke ʻia ke kūlana he hoʻololi ulu maʻamau e hana ʻia i ka wā o ke kaʻina hana paʻakikī o ka hoʻomohala ʻana o ka cardiovascular.
ʻAʻole ulu nā keiki i nā apo vascular no ka mea ʻaʻole e loli ka hoʻonohonoho ʻana o nā kīʻaha koko i ka manawa. Eia naʻe, hiki i nā hōʻailona ke hoʻomaikaʻi i ka wā e ulu ai kāu keiki a lilo i nui aʻe kā lākou airways. Hiki i kekahi mau keiki me kaomi mālie ke loaʻa nā hōʻailona emi i ka wā e ulu ai lākou, ʻoiai kekahi mau mea e pono ai ka lapaʻau me ka nānā ʻole i ka makahiki.
He mea maʻamau loa nā apo vascular, e hana ana i ka emi ma mua o 1% o nā hemahema naʻau i hānau ʻia. Hoʻopili lākou i kahi 1 i 10,000 a 20,000 mau hānau. ʻOiai he mea maʻamau ʻole, he mau kūlana maopopo lākou me nā ala lapaʻau i hoʻokumu ʻia ke pono.
ʻAe, hiki i kekahi mau mākua ke hoʻomohala i nā hōʻailona no ka manawa mua, ʻoi aku ka nui inā loaʻa iā lākou kahi apo lohi e lilo i mea nui aʻe i ka manawa. Hiki i nā loli i ke ʻano kino, ke kaupaona ʻana, a i ʻole nā kumu ʻē aʻe ke hana i kahi apo vascular asymptomatic i hoʻomaka e hana i nā pilikia i ka wā makua.
ʻAʻole pono mau ka ʻoki ʻana no nā apo vascular. Nui nā kānaka me nā apo lohi ʻaʻohe hōʻailona pono wale nō ka nānā mau. Hoʻokomo pinepine ʻia ka ʻoki ʻana wale nō ke hoʻopilikia nui nā hōʻailona i ka hanu, ka ʻai ʻana, a i ʻole ke ʻano o ke ola. E kōkua kāu kauka e hoʻoholo i ke ala kūpono ma muli o kāu kūlana kūikawā.