Hana ʻia kahi apo koko ke hana kekahi ʻāpana o ke kumu nui o ke koko o ke kino, i kapa ʻia ʻo ka aortic arch, a i ʻole kona mau lālā i kahi apo a puni ka trachea a i ʻole ka esophagus a i ʻole nā ʻelua. Hōʻike ʻia kahi naʻau maʻamau ma ka hema. Hōʻike ʻia kahi laʻana o kahi apo koko - kahi aortic arch pālua - ma ka ʻākau.
He pilikia naʻau kahi apo koko i loaʻa i ka wā hānau. ʻO ia hoʻi, he hemahema naʻau congenital ia. I kēia kūlana, hana kekahi ʻāpana o ke kumu nui o ke koko o ke kino a i ʻole kona mau lālā i kahi apo a puni ka puka ea, ka paipu ʻai a i ʻole nā ʻelua.
Hiki i kahi apo koko ke piha a i ʻole hapa.
Pono pinepine ka ʻoki kino e mālama i kahi apo koko.
Hōʻailona o kahi apo kīʻaha koko paha:
Loaʻa paha i kekahi poʻe i hānau ʻia me kahi apo kīʻaha koko nā pilikia naʻau ʻē aʻe i ka hānau ʻana. Kaukaʻi nā hōʻailona kikoʻī ma ke ʻano o nā pilikia naʻau i loaʻa.
Hana ka mea lawelawe ola kino i kahi hoʻokolohua kino a nīnau i nā nīnau e pili ana i nā hōʻailona. Loaʻa paha nā hoʻokolohua i hana ʻia e ʻike i kahi apo kīʻaha koko:
Hiki i nā hoʻokolohua kiʻi ʻē aʻe ke komo pū me ka echocardiogram, kahi CT angiogram a i ʻole kahi MRI scan. Hiki i nā mea lawelawe ola kino ke hoʻohana i kēia mau hoʻokolohua e hoʻolālā i ka mālama.
Nā hoʻokolohua kiʻi. Hiki i kahi X-ray umauma ke hōʻike i nā loli i ka puka ea e hōʻike paha i kahi apo kīʻaha koko. Hiki i ka hoʻokolohua ke hōʻike pū i ka ʻaoʻao o ke kino o ka ʻāʻī aortic.
Hiki i nā hoʻokolohua kiʻi ʻē aʻe ke komo pū me ka echocardiogram, kahi CT angiogram a i ʻole kahi MRI scan. Hiki i nā mea lawelawe ola kino ke hoʻohana i kēia mau hoʻokolohua e hoʻolālā i ka mālama.
Kaukaʻi ke ʻano kikoʻī o ka ʻoki kino ma ke ʻano o nā pilikia naʻau i loaʻa.
Pono nā kānaka i hānau ʻia me kahi apo kīʻaha koko i nā nānā ola kino maʻamau no ke ola e pale aku i nā pilikia.
Ua pane ke kauka naʻau pediatric ʻo Jonathan Johnson, M.D., i nā nīnau i nīnau pinepine ʻia e pili ana i nā hemahema naʻau i hānau ʻia i nā keiki.
Hiki i kekahi mau ʻano liʻiliʻi loa o ka maʻi naʻau i hānau ʻia, e like me nā puka liʻiliʻi loa i loko o ka naʻau a i ʻole ka stenosis palupalu loa o nā valve naʻau like ʻole, ke pono wale nō e hahai ʻia i kēlā me kēia mau makahiki me kekahi ʻano o ka noiʻi kiʻi e like me ka echocardiogram. Hiki i nā ʻano nui aʻe o ka maʻi naʻau i hānau ʻia ke koi i ka ʻoki kino e hiki ke hana ʻia ma o ka ʻoki naʻau ākea, a i ʻole hiki ke hana ʻia i loko o ka lumi catheterization naʻau me nā hāmeʻa like ʻole a i ʻole nā ʻano like ʻole. I loko o kekahi mau kūlana koʻikoʻi loa, inā ʻaʻole hiki ke hana ʻia ka ʻoki kino, hiki ke kuhikuhi ʻia ka transplant.
ʻO nā hōʻailona kūikawā e loaʻa paha i kahi keiki inā loaʻa iā lākou ka maʻi naʻau i hānau ʻia, hilinaʻi maoli ia i ka makahiki o ke keiki. No nā pēpē, ʻo kā lākou kumu nui loa o ka hoʻolilo caloric ʻo ia maoli nō ia i ka wā e ʻai ai. A no laila, ʻo ka hapa nui o nā hōʻailona o ka maʻi naʻau i hānau ʻia a i ʻole ka hāʻule naʻau e hele mai maoli nō ia i ka wā e ʻai ai lākou. Hiki i kēia ke komo pū me ka pōkole o ka hanu, ka paʻakikī o ka hanu, a i ʻole ka hou ʻana i ka wā e hānai ai lākou. E hōʻike pinepine nā keiki ʻōpio i nā hōʻailona e pili ana i kā lākou ʻōnaehana ʻōpū. Loaʻa paha iā lākou ka nausea, ka luaʻi ʻana me ka ʻai ʻana, a loaʻa paha iā lākou kēlā mau hōʻailona me ka hana pū kekahi. ʻO nā ʻōpio ʻōpio, ma kekahi ʻaoʻao, e hōʻike pinepine i nā hōʻailona e like me ka ʻeha umauma, ka hiolo ʻana a i ʻole nā palpitations. Loaʻa paha iā lākou nā hōʻailona i ka wā o ka hoʻoikaika kino a i ʻole ka hana. A ʻo ia maoli nō ka hōʻailona ʻulaʻula nui loa iaʻu ma ke ʻano he kauka naʻau. Inā lohe au e pili ana i kahi keiki, ʻoi aku hoʻi kahi ʻōpio i loaʻa i ka ʻeha umauma, a i ʻole i hiolo me ka hana a i ʻole me ka hoʻoikaika kino, pono maoli wau e ʻike i kēlā keiki a pono wau e hōʻoia e loaʻa iā lākou kahi hana kūpono.
I ka manawa pinepine i wā i ʻike hou ʻia ai kāu keiki me ka maʻi naʻau i hānau ʻia, he mea paʻakikī ke hoʻomanaʻo i nā mea a pau i ʻōlelo ʻia iā ʻoe i kēlā kipa mua. Hiki iā ʻoe ke pīhoihoi i ka lohe ʻana i kēia lono. A i ka manawa pinepine ʻaʻole paha ʻoe e hoʻomanaʻo i nā mea a pau. No laila, he mea nui ia i nā kipa hahai e nīnau i kēia mau ʻano nīnau. Pehea ka ʻano o kaʻu mau makahiki ʻelima e hiki mai ana? Aia kekahi mau kaʻina hana e pono ai i loko o kēlā mau makahiki ʻelima? Kekahi mau ʻoki kino? He aha ke ʻano o ka hoʻokolohua, he aha ke ʻano o ka hahai, he aha ke ʻano o nā kipa halemai e pono ai? He aha ka manaʻo o kēia no nā hana a kāu keiki, nā haʻuki, a me nā mea like ʻole āna e makemake ai e hana i kēlā me kēia lā. A ʻo ka mea nui loa, pehea kākou e hana pū ai e hiki ai i kēia keiki ke ola maʻamau e like me ka hiki ke ʻole me kēlā ʻike o ka maʻi naʻau i hānau ʻia.
Pono ʻoe e nīnau i kāu kauka i ke ʻano o nā kaʻina hana e pono ai no kēia ʻano o ka maʻi naʻau i hānau ʻia i ka wā e hiki mai ana. Hiki ke hana ʻia lākou me ka ʻoki naʻau ākea, a i ʻole hiki ke hana ʻia me ka catheterization naʻau. No ka ʻoki naʻau ākea, he mea nui ke nīnau i kāu kauka e pili ana i ka manawa o kēlā ʻoki kino. No nā ʻano like ʻole, kūikawā o ka maʻi naʻau i hānau ʻia, aia maoli nā manawa i ʻoi aku ka maikaʻi o ka hana ʻana i ka ʻoki kino ma mua o nā mea ʻē aʻe e loaʻa ai ka hopena maikaʻi loa, pōkole a lōʻihi hoʻi no kēlā keiki. No laila, e nīnau i kāu kauka inā aia kahi manawa kūikawā e hana maikaʻi ai no kēlā maʻi kūikawā a no kāu keiki.
ʻO kēia maoli nō ka nīnau pinepine loa aʻu e loaʻa mai nā mākua a me nā keiki ma hope o kā mākou ʻike ʻana i ka maʻi naʻau i hānau ʻia. He mea nui loa nā haʻuki i ka nui o ke ola o kēia mau keiki, i kā lākou mau hui hoaaloha a me ke ʻano o kā lākou launa pū ʻana me kā lākou mau kaiāulu. I ka hapa nui o nā ʻano o ka maʻi naʻau i hānau ʻia, hana mākou i kā mākou mea maikaʻi loa e hoʻāʻo e ʻike i kahi ala e hiki ai iā lākou ke komo mau. Aia kekahi mau ʻano o ka maʻi naʻau i hānau ʻia, akā naʻe, kahi ʻaʻole ʻōlelo ʻia kekahi mau haʻuki. No ka laʻana, no kekahi o kā mākou poʻe maʻi, loaʻa paha iā lākou kekahi ʻano o kahi syndrome genetic e hoʻoliʻiliʻi i nā paia o kā lākou mau arteries. A ʻo kēlā mau mea maʻi, ʻaʻole mākou makemake iā lākou e hāpai kaumaha a i ʻole e hana i kekahi ʻano o kaomi kaumaha e hiki ke hoʻonui i kēlā mau arteries a hiki ke haki. I ka hapa nui o nā hihia, hiki iā mākou ke ʻike i kahi ala e hiki ai i nā keiki ke pāʻani i nā haʻuki ā lākou e aloha ai i kēlā me kēia lā.
No kā mākou poʻe maʻi i loaʻa ka maʻi naʻau i hānau ʻia, i ka wā e ulu ai lākou, pinepine mākou e aʻo aku iā lākou e hoʻoilina ʻia kekahi mau ʻano o ka maʻi naʻau i hānau ʻia. ʻO ia hoʻi, inā loaʻa i kahi mākua ka maʻi naʻau i hānau ʻia, aia kekahi pilikia liʻiliʻi e loaʻa paha i kā lākou keiki ka maʻi naʻau i hānau ʻia. Hiki paha kēia ke ʻano like o ka maʻi naʻau i hānau ʻia i loaʻa i kā lākou mākua, a i ʻole hiki ke ʻokoʻa. No laila, inā hāpai kēlā mau mea maʻi, pono mākou e nānā pono iā lākou i ka wā hāpai, me ka hana ʻana i nā scan hou aku o ka fetus me ka echocardiography i ka wā hāpai. Maikaʻi, ʻo ka hapa nui o kā mākou poʻe maʻi maʻi naʻau i hānau ʻia e hiki ke loaʻa nā keiki ponoʻī i kēia wā.
He mea nui loa ka pilina ma waena o ka mea maʻi, ko lākou ʻohana a me ke kauka naʻau. Pinepine mākou e hahai i kēia mau mea maʻi no nā makahiki he nui i ka wā e ulu ai lākou. Nānā mākou iā lākou e hele mai nā pēpē a hiki i nā mākua. Inā hele mai kekahi mea ʻaʻole maopopo iā ʻoe, akā ʻaʻole maopopo iā ʻoe, e nīnau i nā nīnau. Mai makaʻu e hōʻea aku. Pono ʻoe e manaʻo mau e hiki ke hoʻokaʻaʻike i kāu hui cardiology a e nīnau iā lākou i nā nīnau āpau e kū mai.
Hiki i kahi ultrasound fetal 2D ke kōkua i kāu mea mālama ola e loiloi i ka ulu a me ka hoʻomohala ʻana o kāu pēpē.
Hiki ke ʻike ʻia kahi hemahema naʻau i hānau ʻia i ka wā hāpai a ma hope o ka hānau ʻana. Hiki ke ʻike ʻia nā hōʻailona o kekahi mau hemahema naʻau ma kahi hoʻokolohua ultrasound hāpai maʻamau (fetal ultrasound).
Ma hope o ka hānau ʻana o kahi pēpē, manaʻo paha kekahi mea mālama ola aia kahi hemahema naʻau i hānau ʻia inā loaʻa i ka pēpē:
Lohe paha ke kauka mālama ola i kahi kani, i kapa ʻia ʻo ka murmur, i ka wā e hoʻolohe ai i ka naʻau o ke keiki me ka stethoscope. ʻO ka hapa nui o nā murmurs he mea hemolele, ʻo ia hoʻi ʻaʻohe hemahema naʻau a ʻaʻole weliweli ka murmur i ke olakino o kāu keiki. Eia naʻe, hiki i kekahi mau murmurs ke hana ʻia e nā loli kahe koko i a mai ka naʻau.
ʻO nā hoʻokolohua e ʻike i kahi hemahema naʻau i hānau ʻia e komo pū me:
ʻO ka mālama ʻana i nā hemahema o ka naʻau i hānau ʻia i nā keiki e hilinaʻi ana i ka pilikia o ka naʻau kikoʻī a me kona nui.
ʻAʻohe hopena lōʻihi o kekahi mau hemahema o ka naʻau i hānau ʻia i ke olakino o ke keiki. Hiki paha ke hele mālie ʻole ʻia.
Hiki ke pani ʻia kekahi mau hemahema o ka naʻau i hānau ʻia, e like me ka puka liʻiliʻi ma ka naʻau, i ka wā e ulu ai ke keiki.
Pono ka mālama koke ʻana i nā hemahema o ka naʻau i hānau ʻia. Hiki i ka mālama ke komo pū me:
Hiki ke hoʻohana ʻia nā lāʻau lapaʻau e mālama i nā hōʻailona a i ʻole nā pilikia o ka hemahema o ka naʻau i hānau ʻia. Hiki ke hoʻohana ʻia wale nō a i ʻole me nā mālama ʻē aʻe. ʻO nā lāʻau lapaʻau no nā hemahema o ka naʻau i hānau ʻia:
Inā loaʻa i kāu keiki kahi hemahema nui o ka naʻau i hānau ʻia, hiki ke ʻōlelo ʻia kahi kaʻina hana naʻau a i ʻole ka ʻoki.
ʻO nā kaʻina hana naʻau a me nā ʻoki ʻoki e hana ʻia e mālama i nā hemahema o ka naʻau i hānau ʻia:
Pono kekahi mau keiki i hānau ʻia me kahi hemahema o ka naʻau i hānau ʻia i nā kaʻina hana a me nā ʻoki ʻoki i loko o ko lākou ola. He mea nui ka mālama hoʻomau ola. Pono ke keiki i nā nānā olakino maʻamau e kahi kauka i aʻo ʻia i nā maʻi naʻau, i kapa ʻia he cardiologist. Hiki i ka mālama hoʻomau ke komo pū me nā hoʻokolohua koko a me nā kiʻi e nānā i nā pilikia.
[Hīmeni e kani ana]
Manaʻolana a me ka hoʻōla no nā naʻau liʻiliʻi.
Kauka Dearani: Inā nānā wau i kaʻu hana ponoʻī, hana nui wau i ka ʻoki naʻau liʻiliʻi. A ua hiki iaʻu ke hana pēlā no ka mea ua aʻo wau iā ia ma ka lehulehu o nā mākua, kahi i hoʻomaka ai. No laila, ʻo ka hana ʻana i ka ʻoki naʻau robotic i nā ʻōpio he mea ia ʻaʻole hiki ke loaʻa i kahi haukapila keiki no ka mea ʻaʻohe o lākou ʻenehana i loaʻa iā lākou kahi e hiki ai iā mākou ke hana pēlā ma aneʻi.
[Hīmeni e kani ana]
Inā loaʻa i kāu keiki kahi hemahema o ka naʻau i hānau ʻia mai, hiki ke ʻōlelo ʻia nā hoʻololi o ke ola e mālama ai i ke olakino o ka naʻau a pale aku i nā pilikia.
Hiki iā ʻoe ke ʻike e hāʻawi ana ka kamaʻilio ʻana me nā poʻe ʻē aʻe i hele ma kahi kūlana like iā ʻoe i ka hōʻoluʻolu a me ka hoʻoikaika. E nīnau i kāu hui olakino inā aia kekahi mau hui kākoʻo ma kou wahi.
ʻO ke ola ʻana me kahi hemahema o ka naʻau i hānau ʻia mai hiki ke hana i kekahi mau keiki i ka manaʻo kaumaha a i ʻole hopohopo. Hiki i ka kamaʻilio ʻana me kahi kākāʻōlelo ke kōkua iā ʻoe a me kāu keiki e aʻo i nā ala hou e hoʻokele ai i ke kaumaha a me ka hopohopo. E nīnau i kahi limahana olakino no ka ʻike e pili ana i nā kākāʻōlelo ma kou wahi.
He mea maʻi puʻuwai i hānau ʻia me ka pilikia nui e maʻi ai, a maʻamau ka ʻike ʻia koke ma hope o ka hānau ʻana. Hiki ke ʻike ʻia kekahi ma mua o ka hānau ʻana i ka wā o ka ultrasound hāpai.
Inā manaʻo ʻoe ua loaʻa i kāu keiki nā hōʻailona o ka maʻi puʻuwai, e kamaʻilio me ke kauka o kāu keiki. E mākaukau e wehewehe i nā hōʻailona o kāu keiki a hāʻawi i ka mōʻaukala lapaʻau ʻohana. Loaʻa i kekahi mau hemahema puʻuwai i hānau ʻia ka hele ʻana i nā ʻohana. ʻO ia hoʻi, ua hoʻoilina ʻia lākou.
I ka wā e hana ai ʻoe i ka ʻaha kūkā, e nīnau inā aia kekahi mea e pono ai kāu keiki e hana ma mua, e like me ka pale ʻana i ka ʻai a i ʻole nā mea inu no ka manawa pōkole.
E hana i ka papa inoa o:
Hiki i ka hoʻomākaukau ʻana i ka papa inoa o nā nīnau ke kōkua iā ʻoe a me kāu hui olakino e hoʻohana pono i kou manawa pū. Inā ʻike ʻia kāu keiki me ka hemahema puʻuwai i hānau ʻia, e nīnau i ka inoa kikoʻī o ke kūlana.
Nā nīnau e nīnau aku i ke kauka lapaʻau paha:
Hiki i ka hui olakino o kāu keiki ke nīnau iā ʻoe i nā nīnau he nui. ʻO ka mākaukau e pane iā lākou e hiki ke mālama i ka manawa e hele ai i nā kikoʻī āu e makemake ai e hoʻolilo i ka manawa hou aku. Hiki i ka hui olakino ke nīnau:
Hōʻole: He kahua ʻike olakino ʻo ʻAukake a ʻaʻole hōʻike kāna mau pane i ka ʻōlelo aʻoaʻo lapaʻau. E kūkākūkā mau me kahi ʻoihana lapaʻau laikini kokoke iā ʻoe ma mua o ka hana ʻana i nā hoʻololi.
Hana ʻia i India, no ka honua