Livmarli
Hoʻohana ʻia ka Maralixibat no ka mālama ʻana i ka pruritus cholestatic (ka ʻili ʻili) i nā mea maʻi me ka Alagille syndrome (ALGS) a me ka progressive familial intrahepatic cholestasis (PFIC). Loaʻa wale kēia lāʻau lapaʻau me ke kauoha a kāu kauka. Loaʻa kēia huahana ma nā ʻano helu helu ma lalo nei:
I ka hoʻoholo ʻana e hoʻohana i kahi lāʻau lapaʻau, pono e kaulike i nā pilikia o ka lawe ʻana i ka lāʻau lapaʻau me ka pono e hana ai. He hoʻoholo kēia āu a me kāu kauka e hana ai. No kēia lāʻau lapaʻau, pono e noʻonoʻo i kēia mau mea: E haʻi aku i kāu kauka inā ua loaʻa iā ʻoe kekahi hopena maʻamau ʻole a i ʻole nā hopena ʻē aʻe i kēia lāʻau lapaʻau a i ʻole nā lāʻau lapaʻau ʻē aʻe. E haʻi aku pū i kāu limahana mālama ola inā loaʻa iā ʻoe nā ʻano ʻē aʻe o nā maʻi ʻiliʻili, e like me nā meaʻai, nā mea kala, nā mea mālama, a i ʻole nā holoholona. No nā huahana kūʻai ʻole ʻia, e heluhelu pono i ka lepili a i ʻole nā mea hoʻohui pūʻolo. ʻAʻohe mau haʻawina kūpono i hana ʻia ma ka pilina o ka makahiki i nā hopena o ka maralixibatto e mālama i ka ʻili me ka Alagille syndrome (ALGS) i nā keiki ma lalo o 3 mau mahina o ka makahiki a me ka mālama ʻana i ka ʻili me ka progressive familial intrahepatic cholestasis (PFIC) i nā keiki ma lalo o 12 mau mahina o ka makahiki. ʻAʻole i hoʻokumu ʻia ka palekana a me ka pono. ʻAʻohe mau haʻawina kūpono i hana ʻia ma ka pilina o ka makahiki i nā hopena o ka maralixibat i nā poʻe ʻelemakule. ʻAʻole i hoʻokumu ʻia ka palekana a me ka pono. ʻAʻohe mau haʻawina lawa i nā wāhine no ka hoʻoholo ʻana i ka pilikia o ka pēpē i ka hoʻohana ʻana i kēia lāʻau lapaʻau i ka wā hānai. E kaulike i nā pono hiki ke loaʻa me nā pilikia hiki ke loaʻa ma mua o ka lawe ʻana i kēia lāʻau lapaʻau i ka wā hānai. ʻOiai ʻaʻole pono e hoʻohana pū ʻia kekahi mau lāʻau lapaʻau, i nā hihia ʻē aʻe, hiki ke hoʻohana pū ʻia ʻelua mau lāʻau lapaʻau ʻokoʻa ʻoiai inā hiki ke loaʻa kahi pilina. I kēia mau hihia, makemake paha kāu kauka e hoʻololi i ka nui, a i ʻole pono paha nā palekana ʻē aʻe. E haʻi aku i kāu limahana mālama ola inā ke lawe nei ʻoe i kekahi lāʻau lapaʻau ʻē aʻe a i ʻole lāʻau lapaʻau kūʻai ʻole ʻia (over-the-counter [OTC]). ʻAʻole pono e hoʻohana ʻia kekahi mau lāʻau lapaʻau i ka wā a i ʻole kokoke i ka wā e ʻai ai i ka meaʻai a i ʻole ka ʻai ʻana i kekahi mau ʻano meaʻai ʻoiai hiki ke loaʻa nā pilina. ʻO ka hoʻohana ʻana i ka waiʻona a i ʻole ka paka me kekahi mau lāʻau lapaʻau hiki ke hana i nā pilina. E kūkākūkā me kāu limahana mālama ola i ka hoʻohana ʻana i kāu lāʻau lapaʻau me ka meaʻai, ka waiʻona, a i ʻole ka paka. Hiki i ka loaʻa ʻana o nā pilikia olakino ʻē aʻe ke hoʻopilikia i ka hoʻohana ʻana i kēia lāʻau lapaʻau. E hōʻoia e haʻi aku i kāu kauka inā loaʻa iā ʻoe nā pilikia olakino ʻē aʻe, ʻoiai:
Lawe pono i kēia lāʻau e like me ke kauoha a kāu kauka. Mai lawe hou aku, mai lawe pinepine aku, a mai lawe lōʻihi aku ma mua o ka kauoha a kāu kauka. Hiki mai kēia lāʻau me kahi Alakaʻi Lāʻau a me nā ʻōlelo aʻo no nā mea maʻi. E heluhelu a hahai pono i kēia mau ʻōlelo aʻo. E nīnau i kāu kauka inā he nīnau kāu. E lawe i kēia lāʻau ma kahi o 30 mau minuke ma mua o ka ʻaina mua o ka lā. E nānā i ka wai i loko o ka hue. Pono ia e maopopo a kokoke i ka maopopo a me ke kala ʻole a i ʻole melemele māmā. Mai hoʻohana i ka lāʻau inā he kala ʻē aʻe ka wai, a i ʻole he mau ʻāpana i loko. No ka hoʻohana ʻana: E lawe i kēia lāʻau ma kahi o 4 mau hola ma mua a i ʻole 4 mau hola ma hope o ka hoʻohana ʻana i nā mea hoʻopaʻa wai bile (e laʻa, cholestyramine, colesevelam, colestipol). E ʻokoʻa ka nui o kēia lāʻau no nā mea maʻi like ʻole. E hahai i nā kauoha a kāu kauka a i ʻole nā kuhikuhi ma ka lepili. Hoʻokomo wale nā ʻike ma lalo i nā nui awelika o kēia lāʻau. Inā ʻokoʻa kāu nui, mai hoʻololi inā ʻaʻole i kauoha mai kāu kauka iā ʻoe e hana pēlā. ʻO ka nui o ka lāʻau āu e lawe ai e hilinaʻi ana i ka ikaika o ka lāʻau. Eia kekahi, ʻo ka nui o nā nui āu e lawe ai i kēlā me kēia lā, ka manawa i ʻae ʻia ma waena o nā nui, a me ka lōʻihi o ka manawa āu e lawe ai i ka lāʻau e hilinaʻi ana i ka pilikia olakino āu e hoʻohana nei i ka lāʻau. Inā nalowale ʻoe i kahi nui o kēia lāʻau, e lawe koke iā ia. Eia naʻe, inā kokoke ka manawa no kāu nui aʻe, e haʻalele i ka nui i nalowale a hoʻi i kāu papa hana maʻamau. Mai pāpālua i nā nui. Hoʻokahi manawa i ka lā: Inā nalowale kahi nui ma mua o 12 mau hola a emi iho paha, e lawe koke iā ia, a laila e hoʻi i kāu papa hana maʻamau. Inā nalowale kahi nui ma mua o 12 mau hola, mai lawe i kahi nui hou. E lawe i ka nui aʻe i ka manawa i hoʻonohonoho ʻia. ʻElua manawa i ka lā: Inā nalowale kahi nui ma mua o 6 mau hola a emi iho paha, e lawe koke iā ia, a laila e hoʻi i kāu papa hana maʻamau. Inā nalowale kahi nui ma mua o 6 mau hola, mai lawe i kahi nui hou. E lawe i ka nui aʻe i ka manawa i hoʻonohonoho ʻia. E mālama ma kahi i hiki ʻole ai i nā keiki ke kiʻi. Mai mālama i ka lāʻau kahiko a i ʻole ka lāʻau ʻaʻole pono hou. E nīnau i kāu limahana mālama ola pehea ʻoe e hoʻolei ai i kekahi lāʻau āu ʻaʻole e hoʻohana. E mālama i ka lāʻau i loko o kahi pahu pani ʻia ma ka mahana o ka lumi, mamao aku i ka wela, ka makū, a me ka mālamalama pololei. E mālama mai ka hau. E mālama i kēia lāʻau me ka pāpale ma luna o ka hue. E hoʻolei i kekahi lāʻau i hoʻohana ʻole ʻia ma hope o 100 mau lā ma hope o ka wehe ʻana i ka hue.
Hōʻole: He kahua ʻike olakino ʻo ʻAukake a ʻaʻole hōʻike kāna mau pane i ka ʻōlelo aʻoaʻo lapaʻau. E kūkākūkā mau me kahi ʻoihana lapaʻau laikini kokoke iā ʻoe ma mua o ka hana ʻana i nā hoʻololi.
Hana ʻia i India, no ka honua