Olipudase alfa-rpcp (ala intravena)

Xenpozyme

Hoʻohana ʻia ka inikini ʻolipudase alfa-rpcp e mālama i nā hōʻailona o ka ʻōnaehana hoʻomaha waena ʻole o ka hemahema acid sphingomyelinase (ASMD). He maʻi kuʻuna ka ASMD e hoʻopilikia ana i nā ʻōnaehana he nui (e laʻa, ate, māmā, ʻōpū, koko, ʻōpū) a hiki ke ʻino aku i ka hala ʻana o ka manawa. Pono e hāʻawi ʻia kēia lāʻau lapaʻau e ke kauka a ma lalo paha o ka nānā pololei a kāu kauka. Loaʻa kēia huahana ma nā ʻano helu helu e like me kēia:

I ka hoʻoholo ʻana e hoʻohana i kahi lāʻau lapaʻau, pono e kaulike i nā pilikia o ka lawe ʻana i ka lāʻau lapaʻau me ka pono e hana ai. He hoʻoholo kēia āu a me kāu kauka e hana ai. No kēia lāʻau lapaʻau, pono e noʻonoʻo i kēia mau mea: E haʻi aku i kāu kauka inā ua loaʻa iā ʻoe kekahi hopena maʻamau ʻole a i ʻole nā ​​hopena ʻē aʻe i kēia lāʻau lapaʻau a i ʻole nā ​​lāʻau lapaʻau ʻē aʻe. E haʻi pū aku i kāu limahana mālama ola inā loaʻa iā ʻoe nā ʻano ʻē aʻe o nā mea ʻē aʻe, e like me nā meaʻai, nā mea kala, nā mea mālama, a i ʻole nā ​​holoholona. No nā huahana ʻole-prescription, e heluhelu pono i ka lepili a i ʻole nā ​​mea hoʻohui pūʻolo. ʻAʻole i hōʻike nā haʻawina kūpono i hana ʻia a hiki i kēia lā i nā pilikia kūikawā pediatric e kaupalena ai i ka pono o ka olipudase alfa-rpcp injection i nā keiki. Ua hoʻokumu ʻia ka palekana a me ka pono. ʻAʻole i hana ʻia nā haʻawina kūpono ma ka pilina o ka makahiki i nā hopena o ka olipudase alfa-rpcp injection i ka heluna geriatric. ʻAʻohe mau haʻawina lawa i nā wāhine no ka hoʻoholo ʻana i ka pilikia o ka pēpē ke hoʻohana ʻia kēia lāʻau lapaʻau i ka wā hānai waiū. E kaulike i nā pono hiki ke loaʻa me nā pilikia hiki ke loaʻa ma mua o ka lawe ʻana i kēia lāʻau lapaʻau i ka wā hānai waiū. ʻOiai ʻaʻole pono e hoʻohana pū ʻia kekahi mau lāʻau lapaʻau, i nā hihia ʻē aʻe, hiki ke hoʻohana pū ʻia ʻelua mau lāʻau lapaʻau ʻokoʻa ʻoiai inā hiki ke loaʻa kahi pilina. I kēia mau hihia, makemake paha kāu kauka e hoʻololi i ka nui, a i ʻole pono paha nā palekana ʻē aʻe. E haʻi aku i kāu limahana mālama ola inā ke lawe nei ʻoe i kekahi lāʻau lapaʻau ʻē aʻe a i ʻole lāʻau lapaʻau ʻole (over-the-counter [OTC]). ʻAʻole pono e hoʻohana ʻia kekahi mau lāʻau lapaʻau i ka wā a i ʻole kokoke i ka wā e ʻai ai i ka meaʻai a i ʻole ka ʻai ʻana i kekahi mau ʻano meaʻai ʻoiai hiki ke loaʻa nā pilina. ʻO ka hoʻohana ʻana i ka waiʻona a i ʻole ka paka me kekahi mau lāʻau lapaʻau hiki ke hana i nā pilina. E kūkākūkā me kāu limahana mālama ola i ka hoʻohana ʻana i kāu lāʻau lapaʻau me ka meaʻai, ka waiʻona, a i ʻole ka paka.