Created at:1/16/2025
Question on this topic? Get an instant answer from August.
Ko te amyloidosis tetahi ahuatanga e hangaia ai nga pūtau pūmua koretake e kiia nei ko te amyloid ki roto i ōu whekau me ōu kiko. Ka pakaru ke enei pūmua, ka piri tahi, ka hanga he kohinga kaore e taea e tō tinana te wawahi, te tango rānei.
Whakaarohia he mea piripiri e hōki ana i ngā wāhanga rerekē o tō tinana. I te roanga o te wā, ka taea e enei kohinga pūmua te whakaroa i te mahi a ō whekau. Ka pā te ahuatanga ki ngā whekau maha, tae atu ki tō ngākau, tō whatukuhu, tō ate, me tō pūnaha io.
Ahakoa he wehi te amyloidosis, ko te matauranga ki te mea kei te puta i roto i tō tinana ko te tuatahi ki te whakahaere pai. He maha ngā momo o tenei ahuatanga, ā, he tokomaha ngā tāngata e ora pai ana me te maimoatanga tika me te tiaki.
He maha ngā momo matua o te amyloidosis, ia momo i puta mai i ngā pūmua rerekē. Ko te momo tino noa ko te AL amyloidosis, e puta ana ina hangaia e tō pūnaha mate pūkohu ngā pūtau pūmua antibodi koretake.
Ka puta te AA amyloidosis mai i te mumura roa i roto i tō tinana, e hono ana ki ngā ahuatanga mumura roa penei i te mate rewiti rheumatoid. Ko tenei momo te nuinga o te pā ki ō whatukuhu, ate, me te kōpū.
Ka rere te amyloidosis whakatūpato i roto i ngā whānau, ā, i puta mai i ngā rerekētanga ira e hanga ana i ngā pūtau pūmua he. Ko te amyloidosis momo-māori, e kiia ana hoki ko te amyloidosis koroheke, te nuinga o te pā ki te ngākau, ā, ka puta i ngā tāngata pakeke, ina koa ngā tāne neke atu i te 70.
Ka rereke te mahi o ia momo, ā, ka hiahia pea ki ngā huarahi maimoatanga motuhake. Ka whakatau tō tākuta ko wai te momo kei a koe mā te whakamātautau motuhake.
Ka taea e ngā tohutohu o te amyloidosis te ngawari i te tīmatanga, ā, ka rite ki ētahi atu ahuatanga, koia te take i karangatia ai ko te "kaiwhakaatu nui". Ko ngā tohutohu e pā ana ki a koe e whakawhirinaki ana ki tehea whekau e pā ana ki ngā kohinga pūmua.
Koinei ngā tohutohu tino noa ka kitea e koe:
Ka pāngia ano ētahi tāngata e ngā tohutohu kaore i te noa penei i te mārōngaro ngāwari, ina koa i te taha o ngā kanohi, te rerekētanga rānei o te kiko o te kiri. Ka taea e tō arero te nui ake, te kite rānei i ngā rerekētanga i tō reo.
Ka taea e enei tohutohu te whanake haere i roto i ngā marama, ngā tau rānei. He tokomaha ngā tāngata e whakakore ana i te tīmatanga hei tohu o te koroheketanga, te ahotea rānei, na kaua e whakaroa ki te kōrero ki ō tohunga hauora mō ngā tohutohu e mau tonu ana.
Ka puta te amyloidosis ina pakaru ke ngā pūmua i roto i tō tinana, ka hanga i ngā kohinga kino. Ka rerekē te take tika i runga i te momo amyloidosis kei a koe.
I roto i te AL amyloidosis, ka hangaia e tō wheua iwi ngā pūtau plasma koretake e hanga ana i ngā pūmua he. He rite enei pūtau ki te hunga e kitea ana i te myeloma maha, engari ehara i te mate pukupuku i te ara kotahi.
Ka puta mai te AA amyloidosis mai i ngā ahuatanga mumura roa e tino hanga ana e tō ate te pūmua e kiia nei ko te serum amyloid A. Ka taea e ngā ahuatanga penei i te mate rewiti rheumatoid, te mate pūkohu o te kopu, te mate mumura roa rānei te whakaoho i tenei tukanga.
Ka puta mai ngā momo whakatūpato mai i ngā rerekētanga ira e tukuna ana i roto i ngā whānau. Ka hangaia e enei rerekētanga te hanga e tō tinana i ngā pūmua koretake e ngawari ana te pakaru ke, te kohikohi hoki i te roanga o te wā.
Ka puta te amyloidosis momo-māori ina pā te tukanga koroheketanga noa ki te pūmua e kiia nei ko te transthyretin, ka puta he koretake, ka hanga i ngā kohinga, ina koa i roto i te kiko ngākau.
Me whakapiri atu koe ki ō tohunga hauora mena ka pāngia koe e ngā tohutohu e mau tonu ana kaore he take mārama. Ka taea e te kitenga wawe te whakarereke nui i ō hua maimoatanga.
Rapua te awhina hauora wawe mena ka kite koe i te pupuhi kaore i te whakaarohia i ō waewae, kopu rānei, ina koa ki te hono atu ki te poto o te manawa. Ka taea e enei tohutohu te tohu kei te pā ngā kohinga amyloid ki tō ngākau, whatukuhu rānei.
Kaua e tatari mena kei te pāngia koe e te ngenge nui e whakaroa ana i ngā mahi o ia rā, te ngaro o te taumaha kaore i te whakaarohia, ngā raruraru puku e mau tonu ana rānei. Ko te ngenge me te wiri i ō pito e kino ake ana i te roanga o te wā e tika ana hoki te aromatawai.
Mena he hītori whānau kei a koe mō te amyloidosis, ngā ahuatanga mumura rānei e mohiotia ana, whakahuahia enei ki tō tākuta. Ka taea e rātou te awhina ki te whakatau mena ka hono atu ō tohutohu ki te amyloidosis, ka whakarite i ngā whakamātautau tika.
He maha ngā take ka taea te whakapiki ake i tō tūponotanga ki te whanake i te amyloidosis, ahakoa ko te whai i ngā take pāngarau kaore e tikanga ka whanake koe i te ahuatanga. Ka taea e te matauranga ki enei take te awhina i a koe me tō tākuta ki te tiaki mo ngā tohu wawe.
He mahi te tau i roto i te nuinga o ngā momo amyloidosis. Ko te AL amyloidosis te nuinga o te pā ki ngā tāngata neke atu i te 50, ko te amyloidosis momo-māori te nuinga o te puta i ngā tāne neke atu i te 70. Heoi, ka taea te puta mai ngā momo whakatūpato i tetahi tau.
Ko te whai i ngā ahuatanga hauora motuhake ka whakapiki ake i tō tūponotanga. Ko ngā mate mumura roa penei i te mate rewiti rheumatoid, te mate pūkohu o te kopu, te mate mumura roa rānei ka taea te arahi ki te AA amyloidosis. Ko ngā mate toto penei i te myeloma maha e hono ana ki te AL amyloidosis.
He mea nui te hītori whānau mō te amyloidosis whakatūpato. Mena kua whakatauhia ngā whānau tata ki a koe ki te amyloidosis, ngā raruraru ngākau, whatukuhu rānei kaore i te mārama, ka mau pea koe i ngā rerekētanga ira e whakapiki ake ana i tō tūponotanga.
Ka pā te ira tangata ki ētahi momo amyloidosis. Ko ngā tāne te nuinga o te whanake i te amyloidosis momo-māori, ko te AL amyloidosis te pā ki ngā tāne me ngā wāhine rite tonu. Ko ētahi papamuri iwi kei a rātou hoki ngā tūponotanga teitei mō ngā momo whakatūpato motuhake.
Ka taea e te amyloidosis te arahi ki ngā raruraru kino ina whakaroa ngā kohinga pūmua i te mahi o te whekau. Ko ngā raruraru motuhake e whakawhirinaki ana ki tehea whekau e pā ana, te nui o te amyloid kua kohikohi.
Ko ngā raruraru ngākau kei roto i ngā mea tino kino, ā, ka uru atu ki:
Ka taea e ngā raruraru whatukuhu te haere ki te kore o te whatukuhu, ka hiahia ki te dialysis, te whakawhiti rānei.
Ka taea e te uru atu o te pūnaha io te whakaoho i te ngenge haere, te ngoikore, te mamae rānei i ō ringa me ō waewae. Ka whanake ētahi tāngata i ngā raruraru ki ngā mahi tinana aunoa penei i te whakahaere toto, te kai.
Ka uru atu ngā raruraru puku ki te kore o te kai nui, ka arahi ki ngā kore o te kai, te ngaro tonu o te taumaha.
Ahakoa he wehi enei raruraru, ka taea e te kitenga wawe me te maimoatanga te aukati, te whakaiti rānei i te haere tonu. He tokomaha ngā tāngata e whai amyloidosis ana e pupuri ana i te kounga ora pai me te tiaki tika.
Ko te whakatau i te amyloidosis e hiahia ana ki ngā kaupae maha, na te mea ka rite ngā tohutohu ki ētahi atu ahuatanga. Ka tīmata tō tākuta me te hītori hauora me te whakamātautau tinana, ka aro nui ki tō ngākau, whatukuhu, me te pūnaha io.
Ka awhina ngā whakamātautau toto me te mimi ki te kimi i ngā pūmua koretake, ki te aromatawai i te mahi o te whekau. Ka titiro tō tākuta ki ngā tohu motuhake penei i ngā mekameka mārama teitei i roto i te AL amyloidosis, ngā tohu mumura rānei i roto i te AA amyloidosis.
Ko te whakatau tika e hiahia ana ki te biopsy kiko, kei reira te tauira iti o te kiko e tirotirohia ana i raro i te microscope motuhake. Ko ngā wāhi biopsy noa ko te kiko ngako mai i tō kopu, te wheua iwi, ngā whekau pānga rānei penei i te ngākau, whatukuhu rānei.
Ka awhina ngā rangahau whakaahua penei i ngā echocardiograms, te MRI ngākau, ngā kara ngākau pūkaha rānei ki te aromatawai i te kino o te whekau, ki te arahi i ngā whakatau maimoatanga. Ka whakaatu enei whakamātautau i te pai o te mahi a ō whekau, te nui o te amyloid kua kohikohi.
Ka tūtohutia pea te whakamātautau ira mena ka whakaarohia te amyloidosis whakatūpato. Ka taea e tenei whakamātautau te kimi i ngā rerekētanga motuhake, te awhina i te whakatau i te huarahi maimoatanga pai mō tō momo motuhake.
Ko te maimoatanga mō te amyloidosis e aro ana ki te mutu i te hanga i ngā pūmua koretake, ki te whakahaere i ngā tohutohu hei tiaki i ō whekau. Ko te huarahi motuhake e whakawhirinaki ana ki te momo amyloidosis kei a koe, ngā whekau e pā ana rānei.
Mō te AL amyloidosis, ko te maimoatanga te nuinga o te whakauru i ngā rongoā chemotherapy rite ki te hunga e whakamahia ana mō te myeloma maha. Ka taea e enei rongoā te whakaeke i ngā pūtau plasma koretake e hanga ana i ngā pūmua kino. I ētahi wā, ka tūtohutia pea te whakawhiti pūtau pūtau.
Ko te maimoatanga AA amyloidosis e aro ana ki te whakahaere i te ahuatanga mumura kei raro. Ka uru pea tenei ki ngā rongoā hei whakaiti i te mumura, te whakaora i ngā mate, te whakahaere rānei i ngā ahuatanga mate pūkohu e whakaoho ana i te hanga pūmua.
Ka taea e te amyloidosis whakatūpato te whai hua mai i ngā rongoā e whakau ana i te pūmua koretake, te whakaiti rānei i te hanga. Ka whakaarohia pea te whakawhiti ate, na te mea ko te ate te hanga i te nuinga o ngā pūmua raruraru.
Ka awhina ngā maimoatanga tautoko ki te whakahaere i ngā tohutohu, ki te tiaki i te mahi o te whekau. Ka uru pea enei ki ngā rongoā mō te kore o te ngākau, te whakahaere toto, te whakahaere mamae mō ngā tohu io, te tautoko kai.
Ko tō rōpū maimoatanga pea ka uru atu ngā tohunga mai i ngā mara rerekē e mahi tahi ana hei whakarato i te tiaki whānui. Ka awhina te arotake auau ki te aroturuki i tō whakautu ki te maimoatanga, ki te whakarite i ngā rongoā i runga i te hiahia.
Ko te whakahaere i te amyloidosis i te kāinga e whakauru ana ki te tango i ō rongoā i runga i te tohutohu, ki te aroturuki i ō tohutohu. Pupurihia he rārangi o tō taumaha, na te mea ka taea e te piki ohorere o te taumaha te tohu i te pupuhi wai.
Whai i te kai hauora ngākau, te iti o te tote hei whakaiti i te ahotea ki tō pūnaha toto ngākau. Whakamāramahia tō inu wai mena ka tūtohu tō tākuta, ina koa ki te pāngia koe e te pupuhi, ngā tohutohu kore o te ngākau rānei.
Noho mahi i runga i ō whakawhitinga. Ka taea e te whakakori ngawari penei i te hikoi te awhina i te pupuri i tō kaha, te whakapai ake i te rere toto. Heoi, karohia ngā mahi kaha mena he pānga ngākau kei a koe.
Titiro ki ō waewae me ō ringa mena he pānga io kei a koe. Tirohia ia rā mō ngā whara, kakahu i ngā kākahu tika, tiaki i a rātou i ngā pāmahana nui, na te mea pea kaore koe e rongo i te mamae noa.
Pupurihia te hononga auau ki tō rōpū hauora, kaua e whakaroa ki te karanga mena ka kite koe i ngā tohutohu hou, te kino ake rānei o ngā mea kei reira.
Ko te whakarite mō tō hui e awhina ana ki te whakarite ka whiwhi koe i te mea nui mai i tō wā me ō tohunga hauora. Tuhia katoa ō tohutohu, tae atu ki te wā i tīmata ai rātou, me te āhua o te rerekētanga i te roanga o te wā.
Kawe mai i te rārangi katoa o ō rongoā, tae atu ki ngā rongoā ka hokona i te toa rānei ngā taapiri. Huihuia hoki ō rēkōti hauora, ina koa ngā hua whakamātautau hou, ngā ripoata rānei mai i ētahi atu tākuta.
Whakaritea he rārangi o ngā pātai mō tō ahuatanga, ngā whiringa maimoatanga, me te mea e tatari ana. Kaua e manukanuka ki te maha o ngā pātai – e hiahia ana tō rōpū hauora ki te awhina i a koe ki te mārama ki tō ahuatanga.
Whakaarohia te kawe mai i te mema whānau, te hoa rānei hei awhina i a koe ki te mahara ki ngā korero nui i kōrerotia i te wā o te hui. Ka taea hoki e rātou te whakarato i te tautoko ngākau, te awhina i te tautoko i ō hiahia.
Tuhia tō hītori hauora whānau, ina koa ngā whānau tata e whai raruraru ngākau, mate whatukuhu, ngā ahuatanga io rānei. Ka taea e tēnei korero te mea nui mō te whakatau i tō momo amyloidosis.
Ko te amyloidosis he ahuatanga nui engari ka taea te whakahaere, kei reira ngā pūmua koretake e kohikohi ana i ō whekau. Ahakoa ka taea te pā ki ngā pūnaha tinana maha, ka taea e te kitenga wawe me te maimoatanga tika te whakapai ake i tō kounga ora, te whakaiti i te haere tonu o te mate.
Ko te mea nui rawa atu hei mahara ko te amyloidosis ehara i te mate mate. He tokomaha ngā tāngata e ora ana i ngā oranga tino whānui, mahi me tenei ahuatanga ina whiwhi rātou i te tiaki hauora tika, ka whai i ō rātou mahere maimoatanga.
Ko te mahi tata atu ki tō rōpū hauora, te noho whakamārama mō tō ahuatanga, te pupuri i te kōrero whakatuwhera mō ō tohutohu me ō awangawanga he mea nui ki te whakahaere angitu. Ko te tautoko mai i te whānau me ngā hoa he mea nui hoki ki tō oranga whānui.
Kia mahara kei te haere tonu te rangahau ki ngā maimoatanga amyloidosis, me ngā rongoā hou e whanakehia ana. Kia tumanako, kia aro ki te mea ka taea e koe te whakahaere – te tango i ō rongoā, te whai i tō mahere maimoatanga, te ora hauora.
Ko ētahi momo amyloidosis he whakatūpato, ka rere i roto i ngā whānau, ko ētahi kaore. Ko te amyloidosis whakatūpato i puta mai i ngā rerekētanga ira e tukuna ana mai i ngā mātua ki ngā tamariki. Heoi, ko te momo tino noa, ko te AL amyloidosis, kaore i te whakatūpato. Mena he hītori whānau kei a koe mō ngā raruraru ngākau, whatukuhu, io rānei kaore i te mārama, ka tūtohutia pea te tohutohu ira, te whakamātautau.
I tēnei wā, kaore he rongoā mō te amyloidosis, engari ka taea te whakahaere me te maimoatanga pai. Ko te maimoatanga e aro ana ki te mutu i te hanga i ngā pūmua koretake, ki te whakahaere i ngā tohutohu hei aukati i te kino o te whekau. He tokomaha ngā tāngata e whai amyloidosis ana e ora ana i ngā oranga roa me te maimoatanga tika. Kei te haere tonu te rangahau, ā, kei te whanakehia tonu ngā maimoatanga hou.
Ko te roa o te ora me te amyloidosis e rerekē ana rawa i runga i te momo, ngā whekau e pā ana, me te wā e tīmata ai te maimoatanga. He tokomaha ngā tāngata e ora ana mō ngā tekau tau me te ahuatanga, ko ētahi pea he haere tonu. Ko te kitenga wawe me te maimoatanga e whakapai ake ana i ngā hua. Ka taea e tō tākuta te whakarato i ngā korero motuhake atu i runga i tō āhuatanga motuhake.
I te nuinga, me whai koe i te kai iti o te tote hei whakaiti i te ahotea ki tō ngākau me ō whatukuhu. Whakamāramahia ngā kai kua tukatuka, ngā taonga kua oti te whakakī, ngā kai hōtēra rānei e teitei ana te tote. Mena he pānga whatukuhu kei a koe, pea ka hiahia koe ki te whakamārama i te pūmua me te phosphorus. Ka taea e tō rōpū hauora, te kai tohunga rānei te whakarato i ngā aratohu kai motuhake i runga i tō uru atu o te whekau me tō hauora whānui.
Ahakoa kaore te ahotea e tino whaka kino i te amyloidosis, ka taea te pā ki tō hauora whānui, te pānga pea ki tō pūnaha mate pūkohu. Ko te whakahaere i te ahotea mā ngā tikanga whakahaerenga, te whakakori ngawari, te tohutohu, ngā rōpū tautoko rānei ka taea te whakapai ake i tō kounga ora, te awhina i a koe ki te whakahaere pai i tō ahuatanga. Ka taea hoki e te ahotea roa te whaka kino i ngā tohutohu penei i te ngenge me ngā raruraru moe.