Created at:1/16/2025
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Ko ngā whakahekenga ihu o te pūnaha nerve pūmatua he hononga rerekē i waenga i ngā oko toto i roto i tō roro, i tō tūpuna rānei. Ka hangaia ēnei rōpū oko toto kōtiti i te wā o te whanaketanga o mua, ā, ka pā pea ki te āhua o te rere o te toto i roto i tō pūnaha nerve.
Whakaarohia ngā oko toto o tō roro he pūnaha arai waka i whakaritea pai. I roto i ngā whakahekenga ihu, kei ētahi o ēnei arai he huarahi rerekē, he hononga rānei kaore i roto i te mahere taketake. Ahakoa ka rangona pea tenei he wehi, he tokomaha ngā tāngata e ora ana i o rātou oranga katoa kaore e mōhio ana kei a rātou tētahi.
Ko ēnei whakahekenga he rōpū o ngā oko toto rerekē e whānau ana i mua i te whānautanga. Kāore ngā oko toto e hanga i ngā huarahi maeneene noa i waenga i ngā uaua me ngā uaua, engari he whatunga kōtiti.
Ko te nuinga o ngā whakahekenga ihu ka mau tonu i te ora katoa. Kāore etahi e arai ana i ngā raruraru, engari ko ētahi atu pea ka arai ki ngā tohumate pēnei i ngā mamae o te upoko, i ngā hopu rānei. Ko te mea nui kia mārama ko te whai i tētahi kāore e tikanga tonu ka pāngia koe e ngā raruraru hauora nui.
Ko tō pūnaha nerve kei roto tō roro me tō tūpuna, na reira ka puta pea ēnei whakahekenga i tetahi wāhi rānei. Ko ngā whakahekenga roro te nuinga atu i ngā whakahekenga tūpuna, ā, kua tino pūkenga ngā tākuta ki te whakahaere i ngā momo e rua.
He maha ngā momo rerekē, he āhuatanga motuhake, he āhua whāinga hoki ōna. Ko te mārama ki te momo kei a koe ka āwhina i tō rōpū hauora ki te hanga i te mahere tiaki pai mō tō āhuatanga motuhake.
Ko ngā whakahekenga arteriovenous (AVMs) te momo tino mohiotia. Ka hangaia ēnei he hononga tika i waenga i ngā uaua me ngā uaua, mā te ngaro i te whatunga noa o ngā oko toto iti e kiia nei ko ngā capillaries. Ka taea e tenei te arai i te rere o te toto kia tere rawa atu i te wāhi.
Ko ngā whakahekenga cavernous, e kiia ana hoki ko ngā cavernomas, he rite ki ngā rōpū o ngā wāhi iti kua kīia ki te toto. Ko ēnei te iti ake te rahi, ā, te iti ake te tohumate i ngā AVMs. Ka taea e rātou te ngaro i ngā rahinga iti o te toto, e ora ana i te nuinga o te wā.
Ko ngā whakahekenga uaua e pā ana ki te whanaketanga uaua rerekē. Ko ēnei te momo ngawari rawa, ā, te nuinga kaore e arai ana i tetahi tohumate. He tokomaha ngā tāngata e kite ana kei a rātou ēnei i te wā o ngā tirotiro roro i mahia mō ētahi take.
Ko ngā telangiectasias capillary he iti ngā oko toto whānui e tino iti te raruraru. Ka kitea pea ēnei i te wā, ā, te nuinga kaore e hiahiatia te maimoatanga.
He tokomaha ngā tāngata e whai ana i ngā whakahekenga ihu kaore e wheako ana i tetahi tohumate. Ina puta mai ngā tohumate, ka rereke pea te whānuitanga, kei runga i te wāhi me te rahi o te whakahekenga.
Ko ngā tohumate tino noa ka kitea e koe ko:
Ko ētahi tāngata e wheako ana i ngā huringa ngāwari ake pēnei i te uaua ki te aro, te ngenge rānei. Ka taea e ēnei tohumate te haere mai, te haere atu rānei, ka taea hoki te whānuitanga i te wā.
Ko ngā tohumate kino, engari he iti te maha, ka uru atu ngā mamae o te upoko nui, te ngaro o te mohio, te huringa neurological ohorere rānei. Ka taea e ēnei te tohu i te toto mai i te whakahekenga, e hiahia ana ki te tiaki hauora ohorere.
He mea tika te kōrero ko ngā tohumate e hono ana ki te wāhi o te whakahekenga i roto i tō roro, i tō tūpuna rānei. Ko te whakahekenga i te wāhi e whakahaere ana i te nekehanga ka arai pea ki te ngoikore, i te wāhi tata ki ngā pokapū reo ka pā pea ki te kōrero.
Ka whānau ēnei whakahekenga i ngā wā tīmata o te hapu ina tīmata ana te hanga o ō oko toto. Kāore i tino mārama te take tino o te putanga o tenei, engari kāore i puta mai i tetahi mea i mahi koe, i ō mātua rānei.
Ko te nuinga o ngā whakahekenga ihu ka puta ohorere i te wā o te whanaketanga. Ko ō ira e homai ana ngā tohutohu mō te hanganga o te oko toto, ā, i ētahi wā ka hurihia ēnei tohutohu i te wā o te mahi uaua o te hanga i tō pūnaha nerve.
I te kōrero atu, ko ētahi āhuatanga ira tino iti te maha ka taea te whakapiki i te tūponotanga o te whanaketanga o ētahi momo whakahekenga. Ko te hereditary hemorrhagic telangiectasia tētahi tauira, ahakoa koinei anake te pānga ki te iti o ngā tāngata e whai ana i ngā whakahekenga ihu.
Ko ngā take taiao i te wā hapu kāore te nuinga e arai ana i ēnei whakahekenga. Ko te nuinga ka whakaarohia he rerekētanga whanaketanga e puta ana i te mahi uaua o te hanga i tō pūnaha nerve.
Mai i te nuinga o ngā whakahekenga e hanga ana i mua i te whānautanga, kāore ngā take tūponotanga noa e whai hua rite ki ētahi atu āhuatanga hauora. Heoi, ko ētahi take ka pā pea ki te tūponotanga o te whai i tētahi.
Ko te tau e tākaro ana i te wā ka puta mai pea ngā tohumate. He tokomaha ngā tāngata e kite ana i ō rātou whakahekenga i te wā o ō rātou tau tekau, rua tekau, toru tekau rānei ina tīmata ana ngā tohumate. Kāore tēnei e tikanga i hangaia te whakahekenga i taua wā – i noho pea mai i te whānautanga.
Ko te hītori whānau e pā ana ki ētahi āhuatanga ira tino iti te maha e whakapiki ana i te tūponotanga o te whakahekenga. Heoi, ko te nuinga o ngā tāngata e whai ana i ngā whakahekenga ihu kāore he mema whānau e pāngia ana.
Ko te ira tangata e whakaatu ana i ētahi āhua, me ētahi momo e tino noa atu ana i ngā tāne, i ngā wāhine rānei. Heoi, he iti rawa ēnei rerekētanga, kāore hoki e pā nui ki tō tūponotanga motuhake.
Ka taea e te hapu te whakaoho i ngā tohumate i ngā wāhine e whai ana i ngā whakahekenga, na te huringa o te nui o te toto me te rere. Kāore tēnei e hanga i ngā whakahekenga hou, engari ka whakakite pea i ngā mea kei reira.
Me rapu koe i te tiaki hauora mena ka wheako koe i ngā tohumate neurological hou, rerekē rānei. Ahakoa he maha ngā tohumate he whakamārama ngāwari, he mea whakaaro tonu te arotake tika.
Whakapa atu ki tō tākuta wawe mena ka whānau koe i ngā mamae o te upoko e mau tonu ana, e rerekē ana i ētahi atu i wheakohia e koe i mua. Ko ngā hopu hou, ina koa i ngā pakeke, e hiahia ana hoki ki te arotake hauora, na te mea ka taea e rātou te tohu tuatahi o ngā āhuatanga maha tae atu ki ngā whakahekenga ihu.
Rapua te tiaki ohorere wawe mena ka wheako koe i te mamae o te upoko nui, te ngaro o te mohio, te ngoikore ohorere, te ngenge rānei, te huringa tirohanga ohorere rānei. Ka taea e ēnei te tohu i te toto mai i te whakahekenga, e hiahia ana ki te maimoatanga ohorere.
Ahakoa ngā huringa ngāwari ake pēnei i te uaua ki te mahara, ki te whakarite, ki ngā mahi o ia rā rānei e hiahia ana ki te tiaki hauora. Ka taea e tō tākuta te āwhina ki te whakatau mena e hiahia ana ēnei tohumate ki te whakamātautau atu.
Mena he hītori whānau kei a koe mō ngā whakahekenga ihu, ngā āhuatanga ira e hono ana rānei, kōrerohia tēnei ki tō kaiwhakarato hauora. Ka taea e rātou te āwhina i a koe ki te mārama ki tō tūponotanga me te whai hua pea tetahi whakamātautau.
Ko te nuinga o ngā tāngata e whai ana i ngā whakahekenga ihu e ora ana i ngā oranga noa, hauora, kaore he raruraru nui. Heoi, ko te mārama ki ngā raruraru pea ka āwhina i a koe ki te whakatau whakamārama mō te aroturuki me te maimoatanga.
Ko te raruraru nui ko te toto (hemorrhage) mai i te whakahekenga. Koinei te mea pea ki ētahi momo pēnei i ngā AVMs, ahakoa i taua wā, ko te tūponotanga o ia tau te iti rawa. Ina puta mai te toto, ka taea e te arai ki ngā tohumate rite ki te pōka.
Ka taea te whānau hopu ina pā ana ngā whakahekenga ki te whatu roro i ngā huarahi e whakararu ana i te mahi hiko noa. He tokomaha ngā tāngata e whai ana i ngā hopu e hono ana ki te whakahekenga e whakautu pai ana ki ngā rongoā anti-seizure.
Ka taea te whānau ngoikore neurological mena ka pā ana te whakahekenga ki te mahi roro mā te pehanga, te rere toto rerekē rānei, ngā toto iti i te wā. Ka uru atu ēnei ki te ngoikore, ngā raruraru kōrero, ngā huringa mohio rānei.
Ka taea te puta mai ngā tohumate e haere tonu ana i ētahi tāngata, ahakoa kaore he toto mārama. Ka taea pea tenei na te huringa ngāwari i te rere toto, ngā toto iti, kaore i kitea e hanga ana i te whatu.
Ko ngā raruraru iti te maha ko te hydrocephalus (te kohikohi wai i roto i te roro) te whakapiki rānei i te pehanga i roto i te anga. Ko ēnei te nuinga ka puta anake ki ngā whakahekenga nui ake, i muri rānei i ngā wāhanga toto.
Ko te rongo pai ko te tiaki hauora hou kua tino whai hua ki te aukati me te whakahaere i ēnei raruraru ina puta mai.
Ko te tikanga whakatau e whakawhirinaki ana ki ngā take maha tae atu ki te momo, te rahi, me te wāhi o tō whakahekenga, me te wheako rānei i ngā tohumate. Kāore te katoa e whai ana i te whakahekenga ihu e hiahia ana ki te maimoatanga mahi.
Ko te tirotiro me te aroturuki noa te tikanga pai, ina koa mō ngā whakahekenga iti kāore e arai ana i ngā tohumate. Ka aroturuki tō rōpū hauora i ngā huringa i te wā mā ngā tirotiro waatea.
Ka taea e ngā rongoā te whakahaere pai i ngā tohumate pēnei i ngā hopu, i ngā mamae o te upoko rānei. Ko ngā rongoā anti-seizure e mahi pai ana mō te nuinga o ngā tāngata e whai ana i ngā hopu e hono ana ki te whakahekenga, i te wā ka taea e ngā rongoā maha te āwhina ki te whakahaere i te mamae o te upoko.
Ka taea te tūtohutia te tango wawe mō ētahi whakahekenga, ina koa ētahi kua toto, he tūponotanga rānei ki te arai i ngā raruraru. Ko ngā tikanga neurosurgical hou kua tino haumaru ake ēnei mahi i te wā o mua.
Ko ngā mahi endovascular e whakamahi ana i ngā pūpoi iti e whakauruhia ana mā ngā oko toto ki te whakahaere i ngā whakahekenga mai i roto. Ka taea e ēnei huarahi iti te aukati i ngā oko toto rerekē, te whakakaha rānei i ngā wāhi ngoikore.
Ko te radiosurgery stereotactic e whakamahi ana i ngā hihi radiation aro ki te kati i ngā oko toto rerekē. Ko tēnei maimoatanga kore-whakauru e toru marama ki ngā tau ki te whakaatu i ngā hua katoa, engari ka taea te tino whai hua mō ētahi whakahekenga.
Ka mahi tahi tō rōpū maimoatanga ki a koe ki te whiriwhiri i te huarahi e tuku ana i te pai o ngā painga me ngā tūponotanga mō tō āhuatanga motuhake.
Ko te noho me te whakahekenga ihu e hiahia ana ki te mahi i ngā whiringa oranga whakaaro e tautoko ana i tō hauora whānui, e whakaiti ana i ngā tūponotanga pea. Ko te nuinga o ngā tāngata ka taea te pupuri i ngā oranga noa, mahi.
Whai i tō mahere rongoā mā te atawhai mena kei te tango koe i ngā rongoā anti-seizure, i ētahi atu rongoā rānei. Ko te mau tonu e āwhina ana ki te pupuri i ngā taumata pumau i roto i tō pūnaha mō te whai hua pai.
Kia mōhio ki ō tohumate me ngā huringa. Pupuri i te rārangi ngāwari o ngā mamae o te upoko, ngā hopu, i ētahi atu tohumate rānei ki te whakawhiti ki tō rōpū hauora i ngā haerenga whai muri.
Pupuri i te hauora whānui pai mā te whakakori noa, te moe tika, me te whakahaere i te ahotea. Ko ēnei e tautoko ana i te mahi whānui o tō pūnaha nerve, ā, ka taea te āwhina ki te aukati i ngā tohumate.
Kōrerohia ngā ārai mahi ki tō tākuta. He tokomaha ngā tāngata ka taea te whai wāhi ki ngā mahi noa, ahakoa ko ētahi pea e hiahia ana ki te karo i ētahi hākinakina, mahi rānei e taea te whakapiki i te tūponotanga toto.
Akohia mō tō momo whakahekenga motuhake kia taea ai e koe te whakatau whakamārama mō tō tiaki. Ko te mārama ki tō āhuatanga e āwhina ana i a koe ki te whakawhitiwhiti tika me ngā kaiwhakarato hauora, ki te mohio hoki ki ngā huringa nui.
Hononga atu ki ngā rōpū tautoko, ki ngā hapori ipurangi rānei mena ka kite koe he whai hua. He tokomaha ngā tāngata e whai hua ana i te kōrero ki ētahi atu e whai ana i ngā wheako rite.
Ko te whakarite mō tō hui e āwhina ana ki te whakarite ka whiwhi koe i ngā korero me ngā aratohu tino nui mai i tō rōpū hauora. Ko te iti o te whakahaere i mua ka taea te whakarereke nui.
Tuhia ō tohumate katoa, tae atu ki te wā i tīmata ai, te maha o te putanga, me te mea e pai ake ai, e kino ake rānei. Tāpirihia ngā tohumate e kore pea e hono – i ētahi wā ka homai e rātou ngā tohu nui.
Mau mai he rārangi katoa o ngā rongoā, tae atu ki ngā rongoā-ā-tauhokohoko me ngā taapiri. Ko ētahi rongoā ka taea te pānga ki ngā maimoatanga mō ngā whakahekenga ihu, na reira e hiahia ana tō tākuta ki te pikitia katoa.
Kohikohia ngā hua whakamātautau o mua, ngā tirotiro, ngā rēkōta hauora rānei e pā ana ki tō āhuatanga. Mena kua kite koe i ētahi atu tohunga, mau mai ō rātou ripoata me ngā tūtohu.
Whakaritea ngā pātai i mua. Whakaarohia te uiui mō tō momo whakahekenga motuhake, ngā whiringa maimoatanga, ngā ārai mahi, me ngā tohumate e hiahia ana ki te tiaki hauora ohorere.
Mau mai tētahi hoa whakawhirinaki, mema whānau rānei mena ka taea. Ka taea e rātou te āwhina i a koe ki te mahara ki ngā korero i kōrerotia i te wā o te hui, ki te tuku tautoko ngākau hoki.
Tuhia ō māharahara matua, ngā whāinga rānei mō te haerenga. E āwhina ana tenei ki te whakarite ka whakautuhia ngā kaupapa nui ahakoa ka rangona pea te tere o te hui.
Ko ngā whakahekenga ihu o te pūnaha nerve pūmatua he āhuatanga e taea te whakahaere e ora ana te nuinga o ngā tāngata me te angitu. Ahakoa ka rangona pea te whakawehi i te tīmatanga, ko te rongoā hou e tuku ana i ngā taputapu pai mō te aroturuki me te maimoatanga ina hiahiatia.
Ko te mea nui kia mahara ko te whai i te whakahekenga ihu kāore e whakatau i tō hauora, kāore hoki e whakawhitia tō kaha mō te ora katoa, mahi.
Ko te mahi tata atu ki tō rōpū hauora, te noho mārama hoki ki tō āhuatanga ko ō rautaki pai mō te angitu roa. Ko te tiaki whai muri noa e āwhina ana ki te whakarite ka mau wawe ngā huringa, ka whakahaeretia tika.
Aro atu ki te mea ka taea e koe te whakahaere – te tango i ngā rongoā penei i te whakahaua, te pupuri i te hauora whānui pai, te noho mōhio hoki ki ō tohumate. Ko tēnei huarahi whakahaere e homai ana i a koe te turanga pai mō te whakahaere tika i tō āhuatanga.
Ko te nuinga o ngā whakahekenga ihu he hanganga pumau kāore e ngaro kaore he maimoatanga. Heoi, ko ētahi iti pea ka iti ake te mahi i te wā, ā, ko ētahi momo ka taea te whakahaere angitu ki te whakakore i ngā oko toto rerekē. Ka taea e tō tākuta te whakamārama i te mea e tumanakohia ana i runga i tō momo me tō āhuatanga motuhake.
Ko te nuinga o ngā whakahekenga ihu ka puta ohorere, kāore hoki e tukuna i roto i ngā whānau. Heoi, ko ngā āhuatanga ira tino iti te maha pēnei i te hereditary hemorrhagic telangiectasia ka taea te whakapiki i te tūponotanga. Mena he hītori whānau kei a koe mō ngā whakahekenga ihu, kōrerohia tēnei ki tō tākuta kia mārama ai koe ki ō tūponotanga motuhake.
He tokomaha ngā tāngata e whai ana i ngā whakahekenga ihu e whai ana i ngā haputanga angitu. Heoi, ka taea e te hapu te pā ki te rere toto, te pānga rānei ki ngā tohumate. Ka taea e tō rōpū hauora te āwhina i a koe ki te whakarite mō te hapu mā te whakarite i ngā rongoā mena e hiahiatia ana, te aroturuki hoki i a koe i te wā.
Ko te nuinga o ngā whakahekenga ihu e mau tonu ana i te ora katoa. Ko ētahi pea ka arai ki ngā tohumate e haere tonu ana, i te wā kaore ētahi e arai ana i ngā raruraru. Ko te aroturuki noa me tō rōpū hauora e āwhina ana ki te aroturuki i ngā huringa, te whakarite hoki i tō mahere tiaki. Ko te mea nui ko te hono atu ki te tiaki hauora i te manukanuka ki te mea pea ka puta.
Ko ngā ārai mahi e whakawhirinaki ana ki tō momo whakahekenga motuhake, tō wāhi, me te wheako rānei i ngā tohumate pēnei i te toto. He tokomaha ngā tāngata ka taea te whai wāhi ki ngā mahi noa tae atu ki te whakakori me ngā hākinakina. Ka taea e tō tākuta te tuku aratohu motuhake i runga i tō āhuatanga motuhake, te āwhina hoki i a koe ki te whakatau whakamārama mō ngā mahi.