He aha te Kānara Pūtake Koroidi? Tohutohu, Take, me te Maimoatanga

Ko te kānara pūtake koroidi he mate pukupuku roro onge e tupu ana i te pūtake koroidi, arā, te kiko e hanga ana i te wai roro i roto i tō roro. Ko tēnei wai te ārai i tō roro me tō tuaiwi o muri, e rere ana i ngā ruma motuhake e kiia nei ko ngā wēneti.

Ahakoa ka rongo te ingoa he wehi, ko te mārama ki tēnei āhuatanga ka āhei te awhina i a koe kia rite ake, kia mōhio ake. He tino onge enei mate pukupuku, e pā ana ki te iti iho i te 1 i roto i te miriona o te tangata, ā, ka puta ake te nuinga i ngā tamariki iti i raro i te 5 tau.

He aha te Kānara Pūtake Koroidi?

Ko te kānara pūtake koroidi he mate pukupuku kino e tupu ana i ngā pūtau o te pūtake koroidi. Whakaarohia te pūtake koroidi hei whare whakahaere iti, motuhake i roto i tō roro e hanga ana i te wai roro.

Ko tēnei mate pukupuku kei roto i te rōpū e kiia nei ko ngā mate pukupuku pūtake koroidi, ā, ka taea te pai (kāore i te mate pukupuku) te kino (mate pukupuku). Ko ngā kārānara ko te momo kino, arā, ka taea te tupu tere ake, ā, ka horapa pea ki ētahi atu wāhanga o te roro, o te tuaiwi o muri rānei.

Ka whakaroa te mate pukupuku i te hanga wai noa me te rere, ka āhei te arahi ki te kohikohi o te wai roro i roto i te roro. Ko tēnei āhuatanga, e kiia nei ko te haidrokepārū, ka hanga i te pehanga nui i roto i te anga o te anga, ā, ka puta mai ngā tohu maha e pā ana ki te tangata.

He aha ngā Tohutohu o te Kānara Pūtake Koroidi?

Ka puta mai ngā tohu o te kānara pūtake koroidi nā te mea ka aukati te mate pukupuku i te whakaheke wai noa i roto i te roro, e hanga ana i te pehanga. Nō te mea ko ēnei mate pukupuku te nuinga o te pānga ki ngā pēpi me ngā tamariki iti, ka taea te ngāwari o ngā tohu i te tīmatanga.

Ko ngā tohu tino noa ka kitea e koe ko:

• Te nui ake o te anga o te anga i ngā pēpi (makrokepārū)
• Te ruaki tonu, ina koa i te ata
• Ngā mamae o te upoko nui e kino ake ana i te wā
• Te riri koretake, te rerekētanga rānei o te whāinga
• Te uaua ki te taurite, ki te hikoi rānei
• Ngā raruraru tirohanga, te rerekētanga rānei o te nekehanga o te kanohi
• Ngā hopu e puta mai ana i te wā poto
• Te moe nui rawa atu, te ngenge rānei

I ngā pēpi, ka taea hoki e koe te kite i ngā wahi ngawari o to ratou anga (fontanelles) e pupū ana i waho, e pēnei ana rānei. Ka raru pea ētahi pēpi ki te kai, ki te ahua rānei he whakaarokore rawa atu, kāore he take mārama.

Ka taea e ngā tohu onge engari nui te āhuatanga te ngoikore i te taha kotahi o te tinana, ngā raruraru kōrero, te rerekētanga rānei o te mohio. Ka puta ake ngā tohu i te wā roa i roto i ngā wiki ki ngā marama i te wā e tupu ana te mate pukupuku, e piki ana te pehanga.

He aha ngā Take o te Kānara Pūtake Koroidi?

Ko te take tika o te kānara pūtake koroidi kāore i te tino mohiotia, ka taea te ahua whakahawea ina rapu koe i ngā whakautu. Pēnei i ngā mate pukupuku onge maha, ka puta mai te ahua e tupu ana i ngā rerekētanga ohorere i roto i te DNA o ngā pūtau pūtake koroidi.

Heoi, kua kitea e ngā kairangahau ētahi take ira e piki ake ai te tūponotanga. Ko te hononga tino nui e pā ana ki te mate Li-Fraumeni, he āhuatanga tuku iho onge e puta mai ana i ngā rerekētanga i roto i te kiripuaki TP53. Ko ngā whānau e whai ana i tēnei mate he tūponotanga teitei ake ki te whanake i ngā mate pukupuku maha, tae atu ki ngā kārānara pūtake koroidi.

Ka whakaatu mai ētahi rangahau ko ētahi mate huaketo i te wā hapu pea he wāhi, engari kāore i te tino whakamāramahia tēnei hononga. Kāore i te hono mārama ngā take taiao ki ēnei mate pukupuku, ā, kāore te ahua e puta mai ana i tetahi mea i mahi, kāore rānei i mahi ngā mātua i te wā hapu.

Ko te mea nui kia mārama ko ēnei mate pukupuku e tupu ana i te wā poto i te nuinga o ngā take. Kāore i te puta mai i ngā whiringa oranga, kai, i ngā whakaaturanga taiao rānei i taea te aukati.

Nōhea te Tiro ki te Tākura mō te Kānara Pūtake Koroidi?

Me rapu wawe koe i te tiaki hauora mena ka kite koe i ngā tohu tonu e whakaatu ana i te piki o te pehanga o te roro, ina koa i ngā tamariki iti. Whakawhirinaki ki ō tūmanako hei mātua, hei kai tiaki rānei.

Whakapa atu ki tō tākura tonu mena ka kite koe i ngā mamae o te upoko nui, te ruaki anō, ngā rerekētanga o te tirohanga, ngā hopu hou rānei. I ngā pēpi, ko te tupu tere o te anga, ngā wahi ngawari e pupū ana, te rerekētanga nui rānei o te kai, o te whāinga rānei he mea nui kia tirotirohia tonu.

Kaua e tatari mena ka kitea e koe ngā tohu e kino ake ana i ngā rā, i ngā wiki rānei. Ahakoa he maha ngā tohu ka taea te whai take iti ake, ko ngā mate pukupuku roro he mea nui kia whakamāramahia, kia maimoatia tonu mō ngā hua pai.

Mena kua whakamāramatia tō tamaiti me te mate Li-Fraumeni, kei te whānau rānei tēnei āhuatanga, kōrerohia te tirotiro auau ki tō rōpū hauora. Ka taea e te kitenga wawe te whakakotahi i te angitu o te maimoatanga.

He aha ngā Take Tūponotanga mō te Kānara Pūtake Koroidi?

He tino iti ngā take tūponotanga mō te kānara pūtake koroidi, e whakaatu ana i te onge me te kore whakaaro o ēnei mate pukupuku. Ka taea e te mārama ki ēnei take te awhina i a koe ki te whakatakoto i tō āhuatanga.

Ko ngā take tūponotanga matua ko:

• Te pakeke iti, ina koa te iti iho i te 5 tau
• Te whai i te mate Li-Fraumeni, i ngā rerekētanga kiripuaki TP53 rānei
• Te hītori whānau o te mate Li-Fraumeni
• Te whakamahinga o te radiation ki te anga (he tino onge)

Ko te pakeke te take tino nui, me te 70% o ēnei mate pukupuku e puta ana i ngā tamariki i raro i te 2 tau. Ka heke te tūponotanga i muri i te 5 tau, ā, he tino onge ēnei mate pukupuku i ngā pakeke.

Ko ngā take ira, ahakoa he mea nui ina puta, e whakaatu ana i te iti o ngā take. Ko te nuinga o ngā tamariki e whanake ana i te kānara pūtake koroidi kāore he take tūponotanga e mohiotia ana, arā, ko ēnei mate pukupuku te nuinga o te tupu ohorere.

He aha ngā Hua Ka Taea o te Kānara Pūtake Koroidi?

Ko ngā hua mai i te kānara pūtake koroidi e puta mai ana i te piki o te pehanga i roto i te roro me te wāhi o te mate pukupuku e tata ana ki ngā hanganga nui. Ka taea e te mārama ki ēnei wāhi te awhina i a koe ki te whakarite mō te mea kei mua.

Ko ngā hua tere tonu ko:

• Te haidrokepārū e hiahia ana ki te whakaheke rongoā
• Ngā raruraru tirohanga, te matapo rānei mai i te pehanga ki ngā uaua tirohanga
• Ngā whakaroa whanaketanga i ngā tamariki iti
• Ngā mate hopu ka mau tonu i muri i te maimoatanga
• Te ngoikore, te pararutiki rānei mai i te pehanga ki ngā wāhi motuka
• Te ngaro o te rongohanga mai i te pehanga ki ngā ara rongohanga

Ka taea e ngā hua roa te whai pānga ki te hinengaro, ina koa i ngā tamariki iti kei te whanake tonu o rātou roro. Ka raru pea ētahi tamariki ki te ako, ki ngā raruraru mahara, ki ngā whakaroa rānei ki te tae ki ngā tohu tohu whanaketanga.

He mea tika hoki ngā hua e pā ana ki te maimoatanga, tae atu ki ngā pānga mai i te rongoā, te chemotherapy, te rongoā radiation rānei. Heoi, ka mahi tahi tō rōpū hauora kia iti rawa ēnei tūponotanga i te wā e maimoatia ana te mate pukupuku.

Me pēhea te Whakamārama i te Kānara Pūtake Koroidi?

Ko te whakamārama i te kānara pūtake koroidi e whai ana i ngā kaupae maha, e tīmata ana i te hītori hauora me te tirotiro tinana. Ka ui tō tākura ki ngā tohu, ka mahi pea i ngā whakamātautau neurological ki te tirotiro i ngā reflexes, te whakahaere, te mahi roro rānei.

Ko te taputapu whakamārama tino nui ko te whakaahua pūtau maikuku (MRI) o te roro. Ka taea e tēnei whakaahua taipitopito te whakaatu i te rahi o te mate pukupuku, te wāhi, te hononga rānei ki ngā hanganga roro e tata ana. Ka āhei te MRI ki te whakamārama i te haidrokepārū me te whakarite i ngā huarahi maimoatanga.

Ka taea te whakamahi i te tātaritanga rorohiko (CT) i te tīmatanga, ina koa i ngā āhuatanga ohorere, engari ka homai e te MRI ngā korero taipitopito ake. Ka tono pea tō tākura i te MRI o te tuaiwi o muri ki te tirotiro mena kua horapa te mate pukupuku.

Ko te whakamārama tino tika e hiahia ana ki te tauira kiko, e whiwhitia ana i te wā rongoā ki te tango i te mate pukupuku. Ka tirotirohia e te pathologist tēnei kiko i raro i te microscope kia whakamāramahia ai te whakamārama me te whakatau i ngā āhuatanga motuhake o te mate pukupuku.

Ka taea e ngā whakamātautau atu te whakamātautau ira ki te rapu i te mate Li-Fraumeni, ina koa mena he hītori whānau o te mate pukupuku. Ka taea hoki te mahi i te tātaritanga wai roro ki te tirotiro i ngā pūtau mate pukupuku.

He aha te Maimoatanga mō te Kānara Pūtake Koroidi?

Ko te maimoatanga mō te kānara pūtake koroidi e whai ana i te huarahi rōpū, e whakakotahi ana i te rongoā, te chemotherapy, me te rongoā radiation i ētahi wā. Ko te mahere motuhake e whakawhirinaki ana ki te pakeke o tō tamaiti, te rahi me te wāhi o te mate pukupuku, me te mea kua horapa.

Ko te rongoā te tikanga tuatahi, e whai ana ki te tango i te nui o te mate pukupuku. Ko te tango katoa te tino wāhi mō te whakaora, ahakoa kāore i te taea tonu tēnei nā te wāhi o te mate pukupuku e tata ana ki ngā hanganga roro nui.

Ka whai te chemotherapy i te rongoā i te nuinga o ngā take, e whakamahi ana i ngā rongoā e whai ana i ngā pūtau mate pukupuku puta noa i te tinana. Ko ngā rongoā motuhake me te roa e whakawhirinaki ana ki ngā take pēnei i te pakeke o tō tamaiti me te nui o te mate pukupuku i tangohia i te wā rongoā.

Ka taea te tūtohutia te rongoā radiation mō ngā tamariki pakeke ake, te nuinga o ngā tamariki neke atu i te 3 tau, ina koa ki te kore e taea te tango katoa i te mate pukupuku. Heoi, ko te radiation te nuinga o te karohia i ngā tamariki iti rawa nā te pānga pea ki te roro e whanake ana.

Mena kei te puta te haidrokepārū, pea ka hiahia tō tamaiti ki tetahi shunt, he taputapu iti e whakaheke ana i te nui o te wai roro mai i te roro ki tētahi atu wāhanga o te tinana. Ka taea e tēnei mahi te homai i te whakaora tere mai i ngā tohu e puta mai ana i te piki o te pehanga o te roro.

Me pēhea te Whakahaere i te Tiaki Kāinga i te Wā Maimoatanga?

Ko te whakahaere i te tiaki i te kāinga i te wā maimoatanga e hiahia ana ki te manawanui, ki te whakarite, ki te hononga tata rānei ki tō rōpū hauora. Ka taea e te hanga i te taiao tautoko te awhina i tō tamaiti ki te whakatau i ngā wero o te maimoatanga.

Aro atu ki te pupuri i ngā mahi noa i te wā e ngāwari ana i te wā e āhua ana ngā pānga o te maimoatanga. Pupuri i ngā tohu, ngā rongoā, me ngā rerekētanga katoa ka kitea e koe, nā te mea ka āhei tēnei korero ki tō rōpū hauora te whakarite i te maimoatanga kia rite ki te hiahia.

Ka tino nui te kai i te wā maimoatanga. Mahi tahi me te kai kai ki te whakarite kei te whiwhi tō tamaiti i ngā kalori me ngā matū, ahakoa he iti te hiahia. Ko ngā kai iti, auau te mahi pai ake i ngā kai nui.

Tirohia ngā tohu o te mate, pēnei i te kirika, te ngenge koretake, te rerekētanga rānei o te whāinga, nā te mea ka ngoikore te pūnaha ārai mate i te chemotherapy. Whakapa atu ki tō rōpū hauora tonu mena ka kite koe i ngā tohu e awangawanga ana.

Kaua e wareware ki te tiaki i a koe me ētahi atu mema whānau i tēnei wā wero. Tangohia te awhina mai i ngā hoa me ngā whānau, ā, whakaarohia te hono atu ki ngā rōpū tautoko, ki ngā ratonga tohutohu rānei.

Me pēhea te Whakarite mō tō Hui Tākura?

Ko te whakarite mō ngā hui hauora ka taea te awhina i a koe ki te whakamahi pai i tō wā me te rōpū hauora, kia whakaritea ai ngā pātai nui e whakautua ana. Tīmata ma te tuhi i ngā tohu katoa kua kitea e koe, tae atu ki te wā i tīmata ai rātou me te āhua o te rerekētanga.

Mau mai he rārangi o ngā rongoā, ngā tāpiri, me ngā maimoatanga katoa kei te whiwhi tō tamaiti. Tāpirihia ngā rāpoi me te wā, nā te mea ka āhei tēnei korero ki ngā tākuta te karo i ngā mahi kino pea.

Whakaritea ō pātai i mua, aro atu ki ngā awangawanga tino nui tuatahi. Whakaarohia te ui mō ngā whiringa maimoatanga, ngā hua e tumanakohia ana, ngā pānga pea, me te whakahaere i ngā tohu i te kāinga.

Mau mai he mema whānau, he hoa whakawhirinaki rānei ki ngā hui mena ka taea. Ka taea e rātou te awhina i te mahara ki ngā korero i kōrerotia, te whakarato rānei i te tautoko ngākau i ngā kōrero uaua.

Kaua e whakaroa ki te tono i ngā korero tuhituhi, i ngā rauemi rānei mō te āhuatanga o tō tamaiti. He maha ngā whānau e kite ana he mea whai hua te tuhi i ngā wāhanga nui o te kōrero (me te whakaaetanga) ki te arotake i muri mai.

He aha te Tākutake Matua mō te Kānara Pūtake Koroidi?

Ko te kānara pūtake koroidi he mate pukupuku roro onge engari nui e pā ana ki ngā tamariki iti. Ahakoa ka taea te ahua o te whakahawea o te whakamārama, kua pai ake ngā hua o te maimoatanga i te wā nei mō te maha o ngā tamariki e whai ana i tēnei āhuatanga.

Ko te kitenga wawe o ngā tohu me te tiaki hauora tere he mea nui mō te hua pai rawa atu. Ko te whakakotahitanga o te rongoā, te chemotherapy, me te tiaki tautoko e whakarato ana i te tumanako mō te maha o ngā whānau e tūturu ana ki tēnei whakamārama.

Mahara ko ia āhuatanga o te tamaiti he motuhake, ā, ka mahi tahi tō rōpū hauora ki a koe ki te whakawhanake i te mahere maimoatanga tino tika. Kaua e whakaroa ki te ui i ngā pātai, ki te rapu i ngā whakaaro tuarua, ki te tono rānei i te tautoko atu ina hiahia koe.

Ahakoa ka uaua pea te haerenga kei mua, kāore koe e tūturu ana. Ko ngā pokapū mate pukupuku tamariki whānui he rōpū tohunga e whai wheako ana ki te maimoatanga i ēnei mate pukupuku onge me te tautoko i ngā whānau puta noa i te tukanga katoa.

Ngā Pātai Auau e Uihia ana mō te Kānara Pūtake Koroidi

Q.1 He aha te onge o te kānara pūtake koroidi?

He tino onge te kānara pūtake koroidi, e pā ana ki te iti iho i te 1 i roto i te miriona o te tangata. E whakaatu ana i te iti iho i te 1% o ngā mate pukupuku roro katoa me te 2-5% o ngā mate pukupuku roro tamariki. Ko te nuinga o ngā take e puta ana i ngā tamariki i raro i te 5 tau, me te tino nui o te mate i ngā pēpi i raro i te 2 tau.

Q.2 He aha te reiti ora mō te kānara pūtake koroidi?

Ka rerekē ngā reiti ora nui e whakawhirinaki ana ki ngā take pēnei i te pakeke o te tamaiti, te whānui o te tango rongoā, me te whakautu ki te maimoatanga. I te katoa, ko ngā reiti ora 5-tau e tae ana ki te 40-70%, me ngā hua pai ake ina taea te tango katoa i te mate pukupuku ma te rongoā. Ko ngā tamariki i whakamāramatia i ngā tau iti ake me ētahi e whai ana i ngā mate pukupuku kua tangohia katoa he hua pai ake.

Q.3 Ka taea e te kānara pūtake koroidi te horapa ki ētahi atu wāhanga o te tinana?

Ka taea e te kānara pūtake koroidi te horapa i roto i te pūnaha io mā ngā ara wai roro, ka pā pea ki ētahi atu wāhanga o te roro, o te tuaiwi o muri rānei. Heoi, he tino onge te horapa ki waho o te pūnaha io ki ētahi atu okana. Koia te take e tirotiro ana ngā tākuta i te tuaiwi o muri me te MRI, ka āhei te tātaritanga wai roro i te wā whakamārama.

Q.4 Ka whai pānga roa tō tamaiti i muri i te maimoatanga?

Ko ngā pānga roa e whakawhirinaki ana ki ngā take maha tae atu ki te wāhi o te mate pukupuku, te kaha o te maimoatanga, me te pakeke o tō tamaiti i te wā whakamārama. Ka raru pea ētahi tamariki ki ngā rerekētanga hinengaro, ngā raruraru ako, ngā whakaroa whanaketanga rānei, ā, ka ora katoa ētahi atu. Ko te whai tonu i ngā tohunga e āhei ana te tirotiro i te whanaketanga me te whakarato i te whakauru wawe ina hiahiatia.

Q.5 He tuku iho te kānara pūtake koroidi?

Ko te nuinga o ngā take o te kānara pūtake koroidi e puta ana ohorere, kāore hoki e tuku iho. Heoi, ko te 10-15% o ngā take e hono ana ki te mate Li-Fraumeni, he mate tuku iho mate pukupuku e puta mai ana i ngā rerekētanga kiripuaki TP53. Mena kua whakamāramatia tō tamaiti me tēnei mate pukupuku, pea ka tūtohutia te tohutohu ira ki te aromatawai i te tūponotanga whānau.