He aha te Craniopharyngioma? Tohutohu, Take, me te Maimoatanga

Ko te craniopharyngioma he pūngāwerewere pūtau roro onge, ehara i te mate pukupuku, e tupu ana i te taha o tō kōpū pituitary, kei raro i tō roro. Ahakoa kaore ēnei pūngāwerewere e horapa ki ētahi atu wāhanga o tō tinana penei i te mate pukupuku, ka taea e rātou te whakaputa i ngā raruraru nui nā te wāhi e tupu ai rātou.

Whakaarohia tō kōpū pituitary hei 'pokapū mana nui' mō ngā homoni o tō tinana. Ka tupu te craniopharyngioma i te taha, ka taea e ia te pēhi ki tēnei kōpū me ngā hanganga roro e tata ana, ka whakaroa i ngā mahi nui penei i te tipu, te whakahaere i te kaha, me te tirohanga. Ko ēnei pūngāwerewere te nuinga o te pānga ki ngā tamariki i waenga i ngā tau 5-14 me ngā pakeke i waenga i ngā tau 50-74.

He aha ngā tohu o te craniopharyngioma?

Ka tupu haere ngā tohu o te craniopharyngioma i te tipu o te pūngāwerewere me te pēhi ki ngā hanganga roro e tata ana. Kaore pea koe e kite i tetahi mea i te tīmatanga, engari ka kitea ake ngā tohu i te wa roa.

Nō te mea ka pāngia e ēnei pūngāwerewere tō kōpū pituitary me ngā uaua optic, he maha ngā tohu e pā ana ki ngā koretake homoni me ngā huringa tirohanga. Ko ēnei ngā tohu tino noa hei titiro:

• Nga raruraru tirohanga: Tirohanga māreikura, ngaro o te tirohanga taha, te tirohanga rua rānei
• Ngā mamae o te upoko: Te nuinga o te wa e mau tonu ana, ā, ka kaha ake i te wa roa
• Nga raruraru tipu i ngā tamariki: Te tipu puhoi atu i te noa, te whakaroa rānei o te pakeketanga
• Te ngenge me te ngoikore: Te ngenge nui atu i te noa, te kore rānei o te kaha
• Ngā huringa taumaha: Te piki o te taumaha kaore i te whakamaarama, te uaua rānei ki te ngaro taumaha
• Te matewai nui me te mimi nui: Te hiahia ki te inu me te mimi nui atu i te noa
• Ngā huringa ngākau: Te pouri, te riri, te huringa o te ahua rānei
• Ngā raruraru mahara: Te uaua ki te aro atu, ki te mahara rānei ki ngā mea

I ētahi wā, ka pāngia koe e ngā tohu onge ake penei i te ruaki, te ruaki, te raruraru rānei o te taurite. Ka puta ēnei i te wa e tupu nui ana te pūngāwerewere kia piki ake te pehanga i roto i tō angaanga.

He aha ngā momo craniopharyngioma?

Ka wehewehea e ngā tākuta ngā craniopharyngioma ki ē rua ngā momo nui i runga i te āhua o rātou i raro i te microscope me te hunga e pāngia ana e rātou. Ko te mārama ki ēnei momo ka āwhina i tō rōpū hauora ki te whakarite i te huarahi maimoatanga pai.

Ko te momo adamantinomatous te nuinga o te pānga ki ngā tamariki me ngā tāne taitamariki. Ko ēnei pūngāwerewere te nuinga o te wā e wātea ana ngā kōeke kōhatu me ngā whekau kī. Ka piri atu rātou ki te kōpū roro e tata ana, ka taea te whakahirahira i te tango pokanga.

Ko te momo papillary te nuinga o te pānga ki ngā pakeke, ina koa ki te hunga neke atu i te 40. Ko ēnei pūngāwerewere te nuinga o te wa ka uaua ake, ā, ka iti ake te whekau kī. Ka ngāwari ake te wehe i te kōpū roro e tata ana i te wa o te pokanga, ka taea te arahi ki ngā hua pai ake.

Ko ngā momo e rua he kore-mate pukupuku, engari ko tō rātou wāhi me te tauira tipu te whakatau i te āhua o te pānga ki tō hauora me ngā whiringa maimoatanga e pai ana mō tō āhuatanga.

He aha te take o te craniopharyngioma?

Ka tupu ngā craniopharyngioma mai i ngā pūtau toenga i whakaarohia kia ngaro i te wa e whānau ana koe i roto i te kopu. Ko ēnei pūtau te nuinga o te wā e āwhina ana ki te hangai i tetahi wāhanga o tō kōpū pituitary i te tīmatanga o te haputanga, engari i ētahi wā kaore rātou e ngaro penei i te mea e tika ana.

I muri i ngā tau maha, i ngā tekau tau rānei, ka tīmata ēnei pūtau toenga ki te tipu me te hangai i te pūngāwerewere. Kāore tēnei tukanga i puta mai i tetahi mea i mahi koe, i kore rānei koe i mahi. Kāore i te hono atu ki tō oranga, kai, ki ngā āhuatanga taiao rānei.

Kua kitea e ngā rangahau hou kei te nuinga o ngā craniopharyngioma ngā huringa ira motuhake i roto i ngā pūtau pūngāwerewere. Heoi, ka puta enei huringa i te tino koretake, kāore hoki i te whakawhiwhia mai i ō mātua. Ko te tikanga kaore ngā craniopharyngioma e rere i roto i ngā whānau, kāore hoki koe e taea te tuku atu ki ō tamariki.

Ko te whakaohooho tika e whakaohooho ana i ēnei pūtau moe ki te tīmata ki te tipu tonu te koretake. Kei te haere tonu ngā kairangahau ki te ako i tēnei āhuatanga onge kia pai ake te mārama ki te take he aha ētahi tangata ka whānau mai ēnei pūngāwerewere, ētahi atu kāore.

Nōhea te haere ki te tākuta mō te craniopharyngioma?

Me whakapiri atu koe ki tō tākuta ki te pāngia koe e ngā tohu mau tonu kaore e pai ake i te wa roa, ina koa ngā huringa tirohanga, ngā mamae upoko rānei e mau tonu ana. Nō te mea ka tupu haere ngā tohu craniopharyngioma, he ngāwari ki te whakakore i te ahotea, te pakeketanga noa rānei.

Whakaritea he whakatau i te wa poto ki te kite koe i ngā raruraru tirohanga penei i te ngaro o tō tirohanga taha, te kite rua rānei. Ka taea e ēnei tohu te pānga nui ki ō mahi o ia rā me tō ora, ina koa i te wā e taraiwa ana, e haere ana rānei i ngā kaupae.

Mō ngā mātua, titiro ki ngā tohu kaore tō tamaiti e tipu penei i te mea e tika ana, te ahua rānei e puhoi ake ana te whanaketanga i ō rātou hoa. Ki te amuamu tō tamaiti mō ngā mamae upoko maha, te uaua rānei ki te kite i te papa i te kura, ka tika ēnei ki te tiaki hauora.

Rapua te tiaki hauora i te wa poto ki te pāngia koe e ngā mamae upoko nui me te ruaki, te ngaro o te tirohanga ohorere, te huringa nui rānei o te mohio. Ahakoa he onge, ka taea e ēnei tohu te tohu i te piki o te pehanga i roto i tō roro e hiahia ana ki te maimoatanga i te wa poto.

He aha ngā take morearea mō te craniopharyngioma?

Kāore i rite ki ētahi atu āhuatanga hauora, kāore te craniopharyngioma e whai take morearea noa e taea ai te whakahaere, te whakarereke rānei. Ko te take morearea nui ko te tau noa, me ngā wā tiketike e rua ka tino tupu ai ēnei pūngāwerewere.

Ko ngā tamariki i waenga i ngā tau 5-14 te nui o te morearea, ina koa mō te momo adamantinomatous. Ko te tuarua o te tiketike ka puta i ngā pakeke i waenga i ngā tau 50-74, e tino whānau ana i te momo papillary.

Kāore he mōhiohio e whakaatu ana ko te hītori whānau, ngā whiringa oranga, ngā whakaū taiao, ngā maimoatanga hauora o mua rānei e piki ake ai tō morearea ki te whānau mai i te craniopharyngioma. Ka taea tēnei te whakamarie, engari ko te tikanga kaore he huarahi ki te kīhai, ki te aukati rānei i ēnei pūngāwerewere mai i te hangai.

I kōrerotia, ka pāngia ngā tane me ngā wāhine, ā, ka puta tēnei āhuatanga puta noa i ngā rōpū iwi me ngā rohe whenua. Ko te onge o ēnei pūngāwerewere te tikanga he iti rawa tō morearea takitahi ahakoa tō rōpū tau.

He aha ngā raruraru pea o te craniopharyngioma?

Ka taea e ngā craniopharyngioma te whakaputa i ngā raruraru maha i runga i tō rātou rāhi, wāhi, me te āhua o te pānga ki ngā hanganga roro e tata ana. Ko te nuinga o ēnei raruraru e pā ana ki te pānga o te pūngāwerewere ki tō kōpū pituitary me ngā wāhi e tata ana.

Ko te mārama ki ēnei raruraru pea ka taea te āwhina i a koe ki te mohio ki te wa hei rapu i te tiaki hauora me te aha e tatari ana koe i te wa o te maimoatanga:

• Ngā koretake homoni: Kaore pea tō kōpū pituitary e whakaputa i te homoni tipu, homoni tairoirora, ētahi atu homoni nui rānei
• Te mate huka insipidus: Te kore e taea te whakauru pai i te mimi, ka arahi ki te matewai nui me te mimi nui
• Te ngaro o te tirohanga: Te ngaro o te tirohanga, te tirohanga taha rānei
• Ngā huringa hinengaro: Ngā raruraru mahara, te uaua ki te aro, te huringa o te ahua rānei
• Te momona: Te piki nui o te taumaha nā te kino o ngā pokapū whakahaere kai i roto i tō roro
• Ngā raruraru moe: Ngā tauira moe whakaroa, te moe nui rānei i te awatea
• Hydrocephalus: Te hanga o te wai i roto i te roro ki te aukati te pūngāwerewere i te waipuke wai noa

Ka taea hoki e ētahi raruraru te puta mai i te maimoatanga anō. Ko te pokanga i te taha o te kōpū pituitary me te roro he morearea, ā, ka taea e te rongoā radiation te whakaputa i ngā pānga roa ki te whakaputa homoni. Ka kōrero tō rōpū hauora mō ēnei morearea, ā, ka mahi ki te whakaiti i ngā raruraru i te wa e maimoatia ana tō pūngāwerewere.

Me pēhea te whakatau i te craniopharyngioma?

Ko te whakatau i te craniopharyngioma te nuinga o te wā e tīmata ana mā tō tākuta e ui ki ō tohu me te mahi i te whakamātautau tinana. Ka aro nui rātou ki tō tirohanga, ngā whakautu, me ngā tohu o ngā raruraru homoni.

Ko te taputapu whakatau tino nui ko te whakaahua pūtau maikuku (MRI) o tō roro. Ka taea e tēnei tirohanga taipitopito te whakaatu mārama i te rāhi o te pūngāwerewere, te wāhi, me te hononga ki ngā hanganga e tata ana. Ka taea e tō tākuta te tono i te CT scan kia kite pai ake i ngā kōeke kōhatu i roto i te pūngāwerewere.

Ka āwhina ngā whakamātautau toto ki te kite i ngā koretake homoni e tohu ana i ngā raruraru kōpū pituitary. Ka tirotirohia e tō tākuta ngā taumata o ngā homoni maha tae atu ki te homoni tipu, ngā homoni tairoirora, me te cortisol. Ka āwhina ēnei whakamātautau ki te whakatau i te nui o te pānga o te pūngāwerewere ki tō mahi pituitary.

He mea nui te whakamātautau kanohi whānui nā te mea he maha ngā tangata e whai craniopharyngioma ana e whai raruraru tirohanga ana. Ka whakamātautau tō ophthalmologist i ō mara tirohanga kia whakaatu tika i ngā wāhi o te tirohanga e pāngia ana. Ka āwhina tēnei mōhiohio ki te arahi i ngā whakatau maimoatanga me te aroturuki i tō ahunga whakamua.

He aha te maimoatanga mō te craniopharyngioma?

Ko te maimoatanga mō te craniopharyngioma te nuinga o te wā e whakauru ana i te pokanga hei huarahi matua, te nuinga o te wā ka whakakotahitia ki ētahi atu maimoatanga. Ko te whāinga ko te tango i te nuinga o te pūngāwerewere i te wa e tiaki ana i ngā mahi roro nui.

Ka tīpako tō neurosurgeon i te huarahi pokanga pai rawa atu i runga i te rāhi me te wāhi o tō pūngāwerewere. Ka taea e rātou te mahi mā tō ihu (huarahi transsphenoidal) mō ngā pūngāwerewere iti ake, mā te tuwhera iti rānei i tō angaanga (craniotomy) mō ngā pūngāwerewere nui ake. Kāore te tango katoa i te wa katoa e taea ana me te kore e raru te kino ki ngā wāhi roro nui.

Ko te rongoā radiation te nuinga o te wā e whai ake ana i te pokanga, ina koa ki te toe mai tetahi pūngāwerewere. Ko ngā hangarau hou penei i te radiosurgery stereotactic ka taea te taumata tika i ngā pūtau pūngāwerewere toenga i te wa e whakaiti ana i te kino ki ngā kōpū hauora. Ka taea te hoatu tēnei maimoatanga i muri tonu i te pokanga, te tiaki rānei mō muri mai ki te tipu anō te pūngāwerewere.

Ko te maimoatanga whakakapi homoni te nuinga o te wā e hiahiatia ana i mua, i muri rānei i te maimoatanga. Ka hiahia pea koe ki ngā rongoā hei whakakapi i te homoni tairoirora, homoni tipu, cortisol, ētahi atu homoni rānei kaore tō kōpū pituitary e taea te whakaputa tika. Ka āwhina ēnei rongoā ki te whakahoki i ngā mahi tinana noa me te whakapai ake i tō kounga ora.

Me pēhea te whakahaere i ngā tohu i te kāinga i te wa o te maimoatanga craniopharyngioma?

Ko te whakahaere i ngā tohu craniopharyngioma i te kāinga e whakauru ana i te mahi tata ki tō rōpū hauora i te wa e whakarite ana i ngā whakaritenga mahi ki tō mahi o ia rā. Ko te tango i ō rongoā i tohua i ia rā te mahi nui rawa atu e taea e koe te mahi.

Ki te whakahaere koe i ngā huringa tirohanga, kia haumaru ake tō taiao kāinga mā te whakapai ake i te mārama, te tango i ngā morearea tū, me te whakamahi i ngā tae rerekē hei āwhina i te wehewehe i ngā mea. Whakaarohia te whakamahi i ngā karāhe nui mō te pānui me te tono ki ngā mema whānau kia whakamōhio i a rātou i te wā e tomo ana ki ngā ruma.

Mō ngā tohu e pā ana ki te homoni penei i te ngenge, whakaritea ngā kaupapa moe noa me te tere o ō mahi i te rā. Ki te pāngia koe e ngā huringa taumaha, mahi tahi me te kai tohunga kai hei whakawhanake i te mahere kai e tautoko ana i ō whāinga hauora i te wa e whakaae ana ki ngā huringa hiahia kai.

Tūhonohia he pukapuka tohu hei aroturuki i ngā huringa i ō mamae upoko, tirohanga, taumata kaha, me te ngākau. Ka āwhina tēnei mōhiohio i tō rōpū hauora ki te whakarite i ngā maimoatanga me te hopu i ngā huringa awangawanga i te tīmatanga. Kaua e whakaroa ki te whakapiri atu ki tō kaiwhakarato hauora ki te kino ake ngā tohu, ki te whānau mai rānei ngā tohu hou.

Me pēhea te whakarite mō tō whakatau tākuta?

I mua i tō whakatau, tuhia katoa ō tohu, tae atu ki te wā i tīmata ai rātou me te āhua o te huringa i te wa roa. Kia tino mārama mō ngā raruraru tirohanga, ngā tauira mamae upoko, me ngā huringa i tō kaha, ngākau, taumaha rānei.

Kawe mai he rārangi katoa o ō rongoā o nāianei, tae atu ki ngā horopeta me te auau o te tango. Kohikohia hoki ngā rekoata hauora o mua, ngā hua whakamātautau, ngā rangahau whakaahua rānei e pā ana ki tō āhuatanga. Ki te kite koe i ētahi atu tākuta mō ēnei tohu, kawe mai hoki aua rekoata.

Whakaritea he rārangi o ngā pūrongo e hiahia ana koe ki te ui ki tō tākuta. Whakaarohia te ui mō ngā whiringa maimoatanga, ngā pānga pea, te tirohanga roa, me te āhua o te pānga o te āhuatanga ki ō mahi o ia rā. Kaua e manukanuka ki te ui i ngā pūrongo maha - e hiahia ana tō rōpū hauora kia mārama koe ki tō āhuatanga.

Whakaarohia te kawe mai i te mema whānau, te hoa rānei ki tō whakatau. Ka taea e rātou te āwhina i a koe ki te mahara ki ngā mōhiohio nui me te whakarato i te tautoko ngākau. Ka taea hoki te āwhina o tetahi atu kei reira i te wā e kōrero ana mō ngā whakatau maimoatanga uaua, te mahara rānei ki ngā tohutohu muri i te whakatau.

He aha te mea nui mō te craniopharyngioma?

Ko te craniopharyngioma he pūngāwerewere roro onge engari ka taea te maimoatanga e hiahia ana ki te tiaki hauora motuhake me te whakahaere roa. Ahakoa ka raru te whakatau, he maha ngā tangata e whai tēnei āhuatanga ana e ora tonu ana i ngā oranga whai hua me te maimoatanga me te tautoko tika.

Ko te mea nui rawa atu hei mahara ko te whakatau me te maimoatanga i te tīmatanga te nuinga o te wā e arahi ana ki ngā hua pai ake. Ki te pāngia koe e ngā tohu mau tonu penei i ngā huringa tirohanga, ngā mamae upoko, ngā raruraru homoni rānei, kaua e whakaroa ki te rapu i te tiaki hauora.

Ko te maimoatanga te nuinga o te wā e whakauru ana i te huarahi mahi tahi me ngā neurosurgeons, endocrinologists, ophthalmologists, me ētahi atu tohunga e mahi tahi ana. Ahakoa ka hiahia pea koe ki te maimoatanga whakakapi homoni e haere tonu ana me te aroturuki noa, ka taea e ēnei maimoatanga te whakahaere tika i te nuinga o ngā tohu me ngā raruraru.

Noho hono atu ki tō rōpū hauora, whai i tō mahere maimoatanga i ia rā, kaua hoki e whakaroa ki te ui i ngā pūrongo, ki te whakaputa rānei i ngā awangawanga. Me te tiaki hauora me te tautoko tika, ka taea e koe te whakahaere pai i tēnei āhuatanga me te pupuri i te kounga ora pai.

Ngā pūrongo e ui pinepinetia ana mō te craniopharyngioma

P1: He mate pukupuku te craniopharyngioma?

Kāore, ehara te craniopharyngioma i te mate pukupuku. Ko ēnei he pūngāwerewere ngāwari (kore-mate pukupuku) kāore e horapa ki ētahi atu wāhanga o tō tinana. Heoi, ka taea tonu e rātou te whakaputa i ngā raruraru nui nā tō rātou wāhi e tata ana ki ngā hanganga roro nui penei i te kōpū pituitary me ngā uaua optic.

P2: Ka taea te whakaora katoa te craniopharyngioma?

He maha ngā tangata e whiwhi ana i te mana roa pai o tō rātou craniopharyngioma me te maimoatanga, ahakoa ko te whakaora katoa e whakawhirinaki ana ki ngā take maha. Ki te taea te tango katoa o te pūngāwerewere mā te pokanga, ka nui ake te tupono o te whakaora. Heoi, ka hiahia pea ētahi tangata ki te maimoatanga me te aroturuki e haere tonu ana ahakoa te maimoatanga angitu i te tīmatanga.

P3: Ka hiahia au ki te maimoatanga whakakapi homoni mō te ora?

He maha ngā tangata e whai craniopharyngioma ana e hiahia ana ki te maimoatanga whakakapi homoni ora, ina koa ki te pāngia nui tō rātou kōpū pituitary. Ko ngā homoni motuhake e hiahia ana koe e whakawhirinaki ana ki ngā mahi pituitary e ngoikore ana. Ka aroturuki tonu tō endocrinologist i ō taumata homoni me te whakarite i ngā rongoā i runga i te hiahia.

P4: Me pehea te auau o ngā whakatau aroturuki me ngā tirohanga?

Ka rerekē ngā kaupapa aroturuki i runga i tō maimoatanga me tō āhuatanga takitahi. I te tīmatanga, ka hiahia pea koe ki ngā tirohanga MRI i ia 3-6 marama, me te iti haere o te auau i te wa roa ki te mau tonu tō āhuatanga.

P5: Ka taea e te craniopharyngioma te pānga ki tō kaha ki te mahi, ki te taraiwa rānei?

Ka taea e ngā huringa tirohanga mai i te craniopharyngioma te pānga ki tō kaha ki te taraiwa haumaru, ina koa ki te ngaro o tō tirohanga taha. Ka aromatawai tō tohunga kanohi mena e tutuki ana tō tirohanga ki ngā whakaritenga taraiwa. He maha ngā tangata e taea te haere tonu ki te mahi me te maimoatanga tika me ngā whakaritenga wāhi mahi mena e hiahiatia ana.