Hemophilia

Ko te hemophilia he mate tino onge kaore te toto e totohu i te huarahi noa, na te mea kaore e ranea nga pūtau toto totohu (nga take totohu). Ki te mate koe i te hemophilia, ka taea e koe te toto mo te wa roa atu i muri i te whara atu i to toto totohu tika.

Kaore e tino raru nga wahi iti. Ki te he te āhua o te mate, ko te take nui ko te toto i roto i to tinana, ina koa i o turi, o ou turi, me ou rekereke. Ka taea e te toto o roto te whakangaro i o whatukuhu me o kiko, a ka mate pea.

Ko te hemophilia he mate ira tino. Ko te maimoatanga ko te whakakapi tonu i te take totohu motuhake kua iti. Kei te whakamahia ano nga rongoa hou kaore e whakauru i nga take totohu.

Ko ngā tohu me ngā pūāhua o te hemophilia e rerekē ana, kei te whakawhirinaki ki tō taumata o ngā take toto. Ki te iti rawa te taumata o ō take toto, ka toto pea koe i muri i te pokanga, i te whara rānei. Ki te kaha rawa tō ngoikore, ka taea e koe te ngāwari te toto kahore he take. Ko ngā tohu me ngā pūāhua o te toto whaiaro e whai ake nei: Te toto kahore he whakamaarama, me te nui atu i te tikanga mai i ngā kotinga, i ngā whara rānei, i muri rānei i te pokanga, i te mahi niho rānei He maha ngā pupuhi nui, ngā pupuhi hohonu rānei Te toto rerekē i muri i ngā inokara Te mamae, te pupuhi, te pīngao rānei o ō hononga Te toto i roto i tō mimi, i tō paru rānei Ngā toto ihu kahore he take e mohiotia ana Ki ngā pēpi, te riri kahore he whakamaarama He papa whakahi rarangi ngāwari ki te upoko ka taea te toto ki te roro mō ētahi tāngata he hemophilia kino. Kaore e tino puta, engari ko tētahi o ngā raruraru nui rawa ka puta. Ko ngā tohu me ngā pūāhua e whai ake nei: Te mamae, te upoko roa Te ruaki anō Te moe, te ngenge rānei Te tirohanga rua Te ngoikore, te kore-āhei rānei o te nekehanga Ngā wiri, ngā hopu rānei Rapua te tiaki ohorere ki te whai koe, ki te whai tō tamaiti rānei i: Ngā tohu, ngā pūāhua rānei o te toto ki te roro Te whara kaore e mutu te toto Ngā hononga pupuhi e wera ana ki te pa, me te mamae ki te piko

Rapua te tiaki mate tere mena kei a koe, kei a tō tamaiti rānei:

• Ngā tohu, ngā pūāhua rānei o te toto e rere ana ki te roro
• Te whara e kore ai e mutu te toto
• Ngā hononga pupū e wera ana ki te pa atu, ā, e mamae ana ki te piko

Ka taea e te tinana te whakakotahi i ngā pūtau toto kia hanga ai te toto toto hei whakamutu i te toto. Ko ngā take toto he pūmua kei roto i te toto e mahi tahi ana me ngā pūtau e kiia nei ko ngā pūtau toto hei hanga i ngā toto. Ka puta mai te Hemophilia ina ngaro te take toto, kāore rānei e nui te nui o te take toto.

He tikanga te Hemophilia, arā, ka whānau mai te tangata me te mate (congenital). Ka wehewehea te Hemophilia congenital i runga i te momo take toto e iti ana.

Ko te momo tino noa ko te Hemophilia A, e hono ana ki te iti o te take 8. Ko te momo tuarua tino noa ko te Hemophilia B, e hono ana ki te iti o te take 9.

Ka whanake etahi i te Hemophilia, ahakoa kāore he hītori whānau o te mate. Ka kiia tēnei ko te Hemophilia i whiwhi.

Ko te Hemophilia i whiwhi he momo o te āhuatanga e puta mai ana ina whakaeke te pūnaha ārai mate o te tangata i te take toto 8, 9 rānei kei roto i te toto. Ka taea te hono atu ki:

• Te hapu
• Ngā āhuatanga ārai mate
• Te mate pukupuku
• Te mate mariao maha
• Ngā āhuatanga rongoa

I ngā momo tino noa o te Hemophilia, kei runga i te karōme X te ira kino. E rua ngā karōme ira kei te katoa, tētahi mai i ia mātua. Ka whiwhi ngā wāhine i te karōme X mai i te whaea, me te karōme X mai i te papa. Ka whiwhi ngā tāne i te karōme X mai i te whaea, me te karōme Y mai i te papa.

Ko te tikanga tenei ka puta tonu te Hemophilia ki ngā tama, ā, ka tukuna atu e te whaea ki tana tama, mā tētahi o ngā ira a te whaea. Ko te nuinga o ngā wāhine he ira kino kei a rātou he kaimau kāore he tohu, kāore rānei he tohu o te Hemophilia. Engari ka taea e ētahi kaimau te whai tohu toto, ki te iti haere te nui o ō rātou take toto.

Ko te mea nui rawa e arai ana ki te hemophilia ko te whai whānau e pangia ana e te mate. He nui atu te tūponotanga o ngā tane ki te whiwhi hemophilia i ngā wāhine.

Ko ngā raruraru o te hemophilia e āhei ana:

• Te toto i roto i te korokoro, i te kaki rānei. Ka pā tēnei ki te kaha o te tangata ki te manawa.
• Te mate huaketo. Ki te whakamahia ngā take toto e whakaora ai i te hemophilia mai i te toto tangata, ka nui ake te tūpono o ngā mate huaketo penei i te hepatitis C. Nō te tikanga tirotiro i ngā kai hoatu, he iti te tūpono.
• Te pānga kino ki te rongoā take toto. I ētahi o ngā tāngata he hemophilia kino, ka pā kino te pūnaha ārai mate ki ngā take toto e whakamahia ana hei whakaora i te toto. Ka puta tēnei, ka whakawhanake te pūnaha ārai mate i ngā pūmua e ārai ana i te mahi a ngā take toto, ka iti ake te whai hua o te rongoā.

Kaore he uauatanga

Ko ngā keehi kino o te hemophilia te nuinga o te wā ka tautuhia i roto i te tau tuatahi o te oranga. Ka kore pea e kitea ngā āhua ngawari tae noa ki te pakeketanga. Ka kite etahi i te mate hemophilia i muri i te nui o te toto i te wa o te mahi pokanga.

Ka taea e ngā whakamātautau whakauru toto te whakakite i te kore o te whakauru toto me te whakatau i te kaha o te hemophilia.

Mō te hunga he hītori whānau o te hemophilia, ka taea te whakamahi i te whakamātautau ira ki te kimi i ngā kaimau hei whakarite i ngā whakatau whakamārama mō te hapu.

He mea whai hua ano te whakatau i te wa o te haputanga mena kua pā te hemophilia ki te peepi. Heoi, he raruraru ētahi whakamātautau mō te peepi. Taria te hunga tohunga hauora mō ngā painga me ngā raruraru o te whakamātautau.

Ko te rongoā matua mō te hemophilia kino ko te whakakapi i te take toto e hiahiatia ana e koe mā te tūpē i roto i te uaua.

Ka taea te hoatu tenei rongoā whakakapi hei whakaora i te toto e puta mai ana. Ka taea hoki te hoatu i runga i te kaupapa noa ki te kāinga hei āwhina i te aukatinga i ngā mate toto. Ko ētahi tāngata e whiwhi ana i te rongoā whakakapi tonu.

Ka taea te hanga i te take toto whakakapi mai i te toto i hoatu. Ko ngā hua rite, e kiia ana ko ngā take toto whakakapi, ka hangaia i roto i te taiwhanga, ehara i te toto tangata.

Ko ētahi atu rongoā ko:

• Emicizumab (Hemlibra). Koinei te rongoā hou kaore i roto i ngā take toto. Ka taea e tēnei rongoā te āwhina i te aukatinga i ngā mate toto i ngā tāngata e pangia ana e te hemophilia A.
• Ngā rongoā whakaora toto. E mohiotia ana hoki ko ngā anti-fibrinolytics, ka āwhina ēnei rongoā i te aukatinga i te pakaru o ngā toto.
• Ngā whakapiri muka. Ka taea te whakamahi tika ki ngā wāhi whara hei whakapiki i te toto me te whakaora. He tino whai hua ngā whakapiri muka mō te mahi niho.
• Rongoā tinana. Ka taea te whakaora i ngā tohu me ngā āhuatanga mena kua pakaru ōu hononga i te toto o roto. Ko te kino nui pea ka hiahia ki te pokanga.

Kaore he uauatanga