He aha te Hyperthermia Kino? Tohutohu, Take, me te Maimoatanga

Ko te hyperthermia kino he āhuatanga onge engari he kino te pānga ki ētahi rongoā whakamaori e whakamahia ana i te wā o te pokanga. Ka puta mai i te wā e pā ana ō uaua ki ēnei rongoā, ka piki tere ai te pāmahana o tō tinana, ā, ka pakari ō uaua.

Ko tēnei āhuatanga e pā ana ki te 1 i roto i te 5,000 ki te 1 i roto i te 50,000 o te hunga e whiwhi ana i te whakamaori whānui. Ahakoa he wehi te ahua, he tino whakaorahia ina kitea wawe, ā, he pai te taputapu o ngā ruma mahi i tēnei wā hei whakahaere i te āhuatanga.

He aha ngā tohu o te Hyperthermia Kino?

Ka tere te whanake o ngā tohu o te hyperthermia kino i te wā o te whakamaori, te whakamaori rānei i muri mai. Ka titiro atu tō rōpū hauora ki ēnei tohu i te wā katoa o te tukanga e whakamahi ana i ngā rongoā whakaohooho.

Ko ngā tohu whakatūpato tino noa ko:

• Te piki tere o te pāmahana o te tinana (ka tae pea ki te 106°F neke atu rānei)
• Te pakari o ngā uaua, ina koa ngā uaua kauae
• Te tere o te ngākau me te koretake o te ngākau
• Te teitei o te toto
• Te manawa tere, te ngenge
• Te wera nui
• Te tae kiri kākā, te whero rānei

I ngā take kino atu, ka pā pea koe ki te pakaru o ngā uaua, ngā raruraru whatukuhu, te rerekētanga kino rānei o te matū toto. Ko te rongo pai ko ngā rōpū ruma mahi kua whakangungua ki te kite i ēnei tohu i te wa poto, ā, ki te mahi tere.

He aha ngā take o te Hyperthermia Kino?

Ko te hyperthermia kino te take i te āhuatanga ira e pā ana ki te whakahaere a ō pūtau uaua i te kāratiuma. I te wā e whakamahia ana ētahi rongoā whakamaori, ka whakaohooho tēnei rerekētanga ira i te whakautu uaua.

Ko ngā mea whakaohooho matua ko ētahi rongoā whakamaori motuhake:

• Ngā hau whakamaori rere (penei i te sevoflurane, isoflurane, me te halothane)
• Succinylcholine (he whakahaere uaua)

Ka riro i a koe tēnei āhuatanga ira whakaohooho mai i ō mātua. Ka hono atu ki ngā rerekētanga i roto i ngā ira e whakahaere ana i te tuku kāratiuma ki roto i ngā pūtau uaua, ina koa ngā ira RYR1 me CACNA1S. Ki te kore ēnei ira e mahi tika ana, ka puta te kāratiuma ki roto i ō pūtau uaua kaore e taea te whakahaere.

Ko tēnei āhuatanga ira e rere ana i roto i ngā whānau, engari ko te mau i te ira kaore e tino tikanga ka pā atu koe. Ka mau etahi i te ira kaore e kitea ngā tohu, ka pā atu ētahi ki ngā tohu kino i te wā tuatahi e whakamahia ana ngā rongoā whakaohooho.

Nōhea te haere ki te taote mō te Hyperthermia Kino?

Mēnā kei te whakarite koe mō te pokanga, me kōrero koe ki tō anesthesiologist i mua ki te mea kei a koe tētahi hītori whānau o ngā raruraru ki te whakamaori. Ka āwhina tēnei kōrero i tō rōpū hauora ki te whakarite i te huarahi tino haumaru mō tō tukanga.

Me kōrero motuhake koe mēnā kei te whānau koe i tetahi o ēnei:

• Ngā pāmahana teitei kaore i te mārama i te wā o te pokanga
• Ngā whakaora uaua mai i te whakamaori
• Ngā raruraru uaua, te ngoikore rānei
• Te whakaohooho hyperthermia kino

I te wā o te pokanga, ka tirotiro tonu tō rōpū whakamaori i a koe, na reira kaore koe e manukanuka ki te mohio ki ngā tohu. Engari, ki te mea kua whakamātau koe i te ira e whakaatu ana i te whakaohooho, me whakamōhio tonu ki tetahi kaiwhakarato hauora i mua i te whiwhi whakamaori, ētahi rongoā rānei.

He aha ngā take morearea mō te Hyperthermia Kino?

Ko tō take morearea nui ko te whai hītori whānau o te hyperthermia kino, ngā raruraru kaore i te mārama i te wā o te whakamaori rānei. I te mea he āhuatanga ira tēnei, ka rere i roto i ngā whānau i ngā whakatupuranga.

Ko ētahi atu mea ka piki ai tō morearea ko:

• Ko te tane (he iti te tūponotanga o ngā tāne ki te pānga)
• Ko te taitamariki (he nui ake te rerenga o ngā tamariki me ngā tāne taitamariki)
• Te whai i ētahi āhuatanga uaua penei i te mate ngākau matua
• Ngā pānga kaore i te mārama ki te whakamaori i mua

Ka hono atu ētahi āhuatanga uaua onge ki te morearea teitei. Kei roto i ēnei ngā myopathies whānau, ngā dystrophies uaua, me ngā mate pāwera waatea. Ki te mea kei a koe tētahi mate uaua kua kitea, ka nui ake te tupato o tō rōpū whakamaori.

He mea tika te kōrero ko te ahotea, te wera, te whakakori rānei kaore e whakaohooho i te hyperthermia kino. Ko te pānga ka hiahia tonu ki te whakamahi i ngā rongoā whakamaori motuhake i roto i te hunga e whai ira whakaohooho ana.

He aha ngā raruraru pea o te Hyperthermia Kino?

Ina whakaorahia wawe, ka ora tonu te nuinga o te iwi mai i te hyperthermia kino kaore he pānga roa. Engari, ki te kore e kitea te pānga, te whakaora wawe rānei, ka arahi pea ki ngā raruraru kino.

Ko ngā raruraru tino awangawanga ko:

• Te pakaru o ngā uaua (rhabdomyolysis) e taea ai te kino o ō whatukuhu
• Ngā raruraru o te ngākau e taea ai te mate
• Te kino o te roro mai i ngā pāmahana tinana teitei rawa
• Ngā mate toto
• Te maroke nui me te koretake o te waikawa
• Te kore mahi o ngā pūnaha maha

Ko te ki hei aukati i ēnei raruraru ko te kite wawe me te whakaora tonu. Kei ngā ruma mahi i tēnei wā ngā taputapu tirotiro pāmahana me ngā rongoā āwhina, ka iti ake te noa o ngā raruraru kino i te wā o mua.

Me te whakaora tika, ko te reiti ora neke atu i te 95%. Ko te nuinga o te hunga e pā ana ki te hyperthermia kino ka ora tonu, ahakoa me karo i ngā rongoā whakaohooho i ngā pokanga a muri ake nei.

Me pēhea te whakatau o te Hyperthermia Kino?

Ko te whakatau o te hyperthermia kino e whakamahia ana i runga i ō tohu me tō whakautu ki te whakaora i te wā o te whakamaori. Ka whakatau tēnei tohu e tō rōpū whakamaori mā te tirotiro i ngā tohu tino kitea me te kite i tō whakautu ki ngā rongoā āwhina.

I te wā o te mate, ka titiro ngā taote ki te whakakotahitanga o te pāmahana teitei, te pakari o ngā uaua, me ngā rerekētanga matū toto motuhake. Ka tirotirohia hoki te whakautu ki te dantrolene, te rongoā whakaora motuhake.

I muri i tō ora, ka āwhina te whakamātautau ira ki te whakau i tō whakaohooho me te aratohu i te tiaki hauora a muri ake nei. Ka titiro tēnei whakamātautau ki ngā rerekētanga i roto i ngā ira e hono ana ki te hyperthermia kino. Engari, kaore ngā whakamātautau ira e hopu i ngā take katoa, na reira kaore te hua noa e tino tikanga kaore koe e whakaohooho.

Mō ngā mema whānau, ko te whakamātautau biopsy uaua i whakamahia hei paerewa koura mō te whakatau. Kei roto i tēnei te tango i tetahi wahi iti o te kiko uaua me te whakaatu ki ngā mea whakaohooho i roto i te taiwhanga. Engari, ko tēnei whakamātautau kaore i te waatea i ngā pokapū motuhake, kaore hoki e whakamahia i te nuinga o te wā mai i te wā i waatea ai te whakamātautau ira.

He aha te maimoatanga mō te Hyperthermia Kino?

Ko te maimoatanga mō te hyperthermia kino e aro ana ki te mutu tonu o te rongoā whakaohooho me te hoatu i tetahi rongoā whakaora e kiia nei ko te dantrolene. Ka mahi tēnei rongoā mā te aukati i te tuku kāratiuma ki roto i ō pūtau uaua, ka mutu te pānga kino.

Ka tango tō rōpū hauora i ētahi mahi tere:

1. Mutu tonu i ngā rongoā whakamaori whakaohooho katoa
2. Hoatu dantrolene mā tō IV (he 2.5 mg ia kg o te taumaha tinana)
3. Whakamatao i tō tinana mā ngā peke huka, ngā wai IV makariri, me ngā tauera whakamatao
4. Hoatu hauora me te tautoko i tō manawa
5. Tirotiro me te whakatika i ngā raruraru o te ngākau
6. Tirotiro me te whakataurite i tō matū toto

Ko te maimoatanga dantrolene e hiahia ana ki te whakahoki i ngā haora torutoru tae noa ki te mutu katoa o ō tohu. Ko te nuinga o te iwi e hiahia ana ki ngā rongoā maha i roto i te 24 ki te 48 haora hei aukati i te hokinga mai o te pānga.

Ka tirotirohia hoki e tō rōpū hauora tō mahi whatukuhu me te hoatu i ngā wai maha hei āwhina i te horoi i ngā hua pakaru uaua. I ngā take kino, ka hiahia pea koe ki te dialysis hei tautoko i ō whatukuhu i te wā e ora ana.

Me pēhea te whakahaere i te ora mai i te Hyperthermia Kino?

Ko te ora mai i te hyperthermia kino e puta ana i te waahanga tiaki nui i te wā e taea ai e tō rōpū hauora te tirotiro i a koe. Ko te nuinga o te iwi ka tīmata te pai ake i roto i ngā haora i muri i te whiwhi dantrolene, ahakoa ka roa pea ngā rā hei ora katoa.

I te wā o tō ora, ka hoatu tonu e tō rōpū hauora te dantrolene me te tirotiro i ō tohu ora, mahi whatukuhu, me ngā uaua. Ka noho pea koe ki te hohipera mo te 24 ki te 48 haora hei whakarite kaore e hoki mai te pānga.

Ina tae koe ki te kāinga, me okioki koe me te tuku i tō tinana ki te ora katoa. Ka pā pea etahi ki te mamae o ngā uaua, te ngoikore rānei mō etahi rā, he mea noa tēnei. Ko te inu i ngā wai maha ka āwhina i ō whatukuhu ki te tukatuka i ngā hua pakaru uaua e toe ana.

Ko te wāhanga tino nui o tō ora ko te whiwhi i te tuhinga tika o tō pānga me te tohutohu ira mēnā e taunakitia ana. He mea nui tēnei mōhiohio mō ngā tukanga hauora a muri ake nei me te whakamōhio i ngā mema whānau e pā ana pea.

Me pēhea te aukati i te Hyperthermia Kino?

Ko te aukati pai mō te hyperthermia kino ko te karo i ngā rongoā e whakaohooho ana. Ki te mea e mohiotia ana koe he whakaohooho, he hītori whānau kaha rānei, ka whakamahi tō rōpū whakamaori i ētahi atu rongoā e tino haumaru ana mōu.

Ko ngā kōwhiringa whakamaori haumaru ko:

• Propofol me ētahi atu whakamaori IV kaore e whakaohooho
• Ngā whakamaori rohe penei i te lidocaine
• Te whakamaori rohe (ngā poraka tuaiwi, epidural rānei)
• Ngā whakahaere uaua kaore e whakaohooho
• Nitrous oxide (hau kata)

Ki te mea kei a koe te hītori whānau o te hyperthermia kino, whakaarohia te whakamātautau ira i mua i tetahi pokanga e whakaritea ana. Ka āwhina tēnei i tō rōpū hauora ki te whakatau i ngā whakatau tino haumaru mō tō tiaki whakamaori.

Me kakahu tonu i te peke whakamōhio hauora, te kawe rānei i te kāri e whakamōhio ana i tō whakaohooho hyperthermia kino. I ngā āhuatanga āwhina, ka ora tēnei mōhiohio me te āwhina i ngā rōpū hauora ki te whiriwhiri i ngā rongoā tika i te wa poto.

Mō te whakarite whānau, ka āwhina te tohutohu ira ki te mārama koe ki ngā morearea o te tuku i tēnei āhuatanga ki ō tamariki me te kōrero i ngā kōwhiringa whakamātautau mō ngā mema whānau.

Me pēhea te whakarite mō tō hui taote?

Ki te mea kei te manukanuka koe ki te morearea hyperthermia kino, tīmata mā te kohikohi i ngā mōhiohio taipitopito mō te hītori hauora o tō whānau. Aro atu ki ngā raruraru i pā ki ngā mema whānau ki te whakamaori, ngā raruraru kaore i te mārama i te wā o te pokanga rānei.

I mua i tō hui, tuhia:

• Tetahi hītori whānau o ngā raruraru whakamaori, hyperthermia kino rānei
• Ngā pokanga i mua i a koe me te āhua o tō ora
• Ngā mate uaua, te ngoikore rānei i roto i tō whānau
• Ngā pūrongo mō te whakamātautau ira, te haumaru whakamaori rānei
• Ngā rongoā o nāianei me ngā mate pāwera

Ki te mea kei te whakarite koe mō te pokanga, whakaritea he kōrero i mua i te pokanga me tō anesthesiologist. Ka hoatu tēnei ki a koe te wā ki te kōrero i ō awangawanga me te tuku i a rātou ki te whakarite i te huarahi whakamaori tino haumaru mō tō tukanga.

Kawe mai i ngā rēkōta hauora o mua e pā ana ki ngā pānga whakamaori, ngā hua whakamātautau ira, ngā pūrongo biopsy uaua rānei ki te mea kei a koe. Ka āwhina tēnei mōhiohio i tō rōpū hauora ki te whakatau i ngā whakatau tino mārama mō tō tiaki.

He aha te mea nui mō te Hyperthermia Kino?

Ko te hyperthermia kino he āhuatanga kino engari he tino whakaorahia e puta ana i te hunga e whai ira whakaohooho ana ki ētahi rongoā whakamaori. Ahakoa ka mate pea ki te kore e kitea tere, kua tino ora te tiaki hauora o nāianei me te whakaora tika.

Ko te mea tino nui hei mahara ko te mātauranga ko tō tiaki pai. Ki te mea kei a koe tetahi hītori whānau o ngā raruraru whakamaori, kōrero ki ō kaiwhakarato hauora i mua i tetahi pokanga. Ka taea e rātou te whakamahi i ētahi atu rongoā tino haumaru me te whakarite ki ngā maimoatanga āwhina mēnā e hiahiatia ana.

Me ngā tupato tika me te matauranga hauora, ka taea e te hunga e whai ira whakaohooho ana te hyperthermia kino te pokanga haumaru me te ora noa. Ko te ki ko te whakarite kei te mohio tō rōpū hauora ki tō morearea kia taea ai e rātou te tango i ngā tupato tika.

Ngā pūrongo e ui ana mō te Hyperthermia Kino

Q1: Ka puta mai rānei te hyperthermia kino kaore he whakamaori?

Ko te hyperthermia kino ka hiahia tonu ki te whakamahi i ngā rongoā whakaohooho motuhake e whakamahia ana i te whakamaori. Ahakoa he onge rawa ngā take kua pūrongohia me te wera nui, ētahi atu rongoā rānei, ko te nuinga o ngā pānga ka puta anake i te wā o te pokanga me ngā anesthetics rere, succinylcholine rānei.

Q2: Ki te mea i pā atu tō mātua ki te hyperthermia kino, ka pā atu rānei ahau?

Kāo. Ko te whakaohooho hyperthermia kino e riro ana, engari kaore e whai tauira ngāwari. Kei a koe te 50% o te tūponotanga o te riro i te whakaohooho ira mēnā kei tetahi mātua tēnei, engari ko te mau i te ira kaore e tino tikanga ka pā atu koe. Ka mau etahi i te ira kaore e kitea ngā tohu.

Q3: Kia tere te whanake o te hyperthermia kino i te wā o te pokanga?

Ka taea te whanake o te hyperthermia kino i roto i ngā meneti i muri i te whakamahi i ngā rongoā whakaohooho, ahakoa ka roa pea te kite. Ko te pānga e kitea ana i roto i te haora tuatahi o te whakamaori, koia te take e tirotiro ana tō rōpū hauora i a koe i tenei wā.

Q4: Ka taea e au te mahi niho mēnā kei te whakaohooho ahau ki te hyperthermia kino?

Ae, ka taea e koe te mahi niho haumaru. Ko ngā whakamaori rohe penei i te lidocaine me te novocaine he tino haumaru mō te hunga e whai whakaohooho ana ki te hyperthermia kino. Me whakamōhio noa atu ki tō kaitoi niho mō tō āhuatanga kia taea ai e rātou te karo i ngā rongoā whakaohooho mēnā e hiahiatia ana te whakamaori hohonu.

Q5: Me karo ahau i ngā pokanga a muri ake nei mēnā kua pā atu ahau ki te hyperthermia kino?

Kāo. Ka taea e koe te pokanga haumaru i ngā pokanga a muri ake nei mā te whakamahi i ngā rongoā whakamaori kaore e whakaohooho. Ka whakamahi tō rōpū whakamaori i ētahi atu rongoā e tino haumaru ana mōu. He tokomaha ngā tangata e whai whakaohooho ana ki te hyperthermia kino e whai pokanga angitu maha ana i o rātou oranga me ngā tupato tika.