He aha te mate pukupuku pūtau kiri hiko taha? Tohutohu, Take, me te Maimoatanga

Ko te mate pukupuku pūtau kiri hiko taha (MPNST) tētahi momo mate pukupuku onge e tupu ana i te hipoki tiaki o ōu io. Ka tupu ēnei pukupuku i roto i ngā kiko e karapotia ana, e tautoko ana i ōu io taha, ara ngā io kei waho o tō roro me tō tuaiwi o te tuara.

Ahakoa ka raru pea tēnei whakamārama, ko te mārama ki te aha te MPNST me te pēhea te maimoatanga ka āhei te awhina i a koe kia rite ake. Ko ēnei pukupuku e 5-10% anake o ngā mate pukupuku kiko ngawari katoa, na reira kei te whakahaere koe i tētahi mea onge engari ka taea te whakahaere me te tiaki hauora tika.

He aha ngā tohu o te mate pukupuku pūtau kiri hiko taha?

Ko te tohu tuatahi tino noa ko te pupuku e tipu ana, te nui rānei i te taha o te ara io, ā, pea ka mate pē, kāore rānei. Ka kite pea koe i tēnei pupuku e nui haere ana i roto i ngā wiki, ngā marama rānei, he rerekē tēnei i ngā tipu pai e noho ana i te rahi kotahi.

Tā, tirohia ngā tohu ka pā pea ki a koe, kia mahara ko te kite wawe ka tino whakarereke i ngā hua o te maimoatanga.

• Te pupuku, te nui rānei e pakari ana, e tipu haere ana i raro i tō kiri
• Te mamae, te ngawari rānei i te wāhi o te pukupuku
• Te ngenge, te wiri rānei i te wāhi e whakaratohia ana e te io pānga
• Te ngoikore o ngā uaua e whakahaerea ana e te io pānga
• Te ngaro o te āhua, te mārama rānei i ngā wāhanga o tō tinana
• Ngā huringa i ngā mahi whakaata

I ētahi wā, ka kore pea koe e kite i tetahi tohu tae noa ki te nui haere o te pukupuku kia pēhi ki ngā kiko e karapotia ana. Koia te take he mea nui tetahi pupuku hou, e tipu haere ana ki tō tākuta, ahakoa kāore e mamae.

He aha ngā momo o te mate pukupuku pūtau kiri hiko taha?

Ko ngā pukupuku MPNST e whakarōpūtia ana i runga i te wāhi e tupu ana, me ō rātou take. Ko te mārama ki ēnei momo ka āhei te awhina i tō rōpū hauora ki te whiriwhiri i te huarahi maimoatanga pai mō tō āhuatanga motuhake.

Ko te nuinga o ngā tākuta e whakarōpū ana i ēnei pukupuku ki ngā rōpū e rua e hangai ana ki tō rātou takenga:

• MPNST koretake: Ka tupu enei kahore he take ira e mohiotia ana, ā, e 50% pea o ngā keehi
• MPNST e hono ana ki te NF1: Ka puta ēnei ki ngā tāngata e pangia ana e te neurofibromatosis momo 1, e 40-50% pea o ngā keehi
• MPNST i puta mai i te rongoā radiation: Ko ēnei pukupuku onge e tupu ana i muri i te maimoatanga rongoā radiation

Ka whakarōpūtia hoki e tō tākuta te pukupuku i runga i tona tohu, e whakaatu ana i te āhua o ngā pūtau mate pukupuku i raro i te microscope. Ko ngā pukupuku tohu teitei ka nui ake te tipu me te horapa atu i ngā pukupuku tohu iti.

He aha ngā take o te mate pukupuku pūtau kiri hiko taha?

Kāore i tino mārama te take tika o te MPNST, engari kua kitea e ngā kairangahau etahi take e whakapiki ana i te tūponotanga o te whanake i ēnei pukupuku. Ko te nuinga o ngā keehi ka puta kahore he whakaohooho mārama, ko ētahi atu ka hono atu ki ngā āhuatanga ira motuhake, ki ngā maimoatanga o mua rānei.

Ko ēnei ngā take matua ka taea te whakauru ki te whanaketanga MPNST:

• Neurofibromatosis momo 1 (NF1): Ka whakapiki nui tēnei āhuatanga ira i tō tūponotanga
• Te rongoā radiation o mua: Ka taea e ngā pukupuku te whanake i te 10-20 tau i muri i te maimoatanga radiation
• Ngā rerekētanga ira: Ngā huringa i ngā ira motuhake e whakahaere ana i te tipu pūtau
• Te hītori whānau: Ko ngā keehi onge e rere ana i roto i ngā whānau
• Ngā pukupuku io pai o mua: I ētahi wā ka taea e ngā pukupuku pai te huri hei pukupuku kino

Mēnā kei a koe te NF1, ko tō tūponotanga ora katoa ki te whanake i te MPNST ko te 8-13% pea, he nui atu i te taupori whānui. Heoi, ko te tikanga tenei ko te nuinga o ngā tāngata e pangia ana e te NF1 kāore e whanake i tēnei momo mate pukupuku.

Nōhea te haere ki te tākuta mō te mate pukupuku pūtau kiri hiko taha?

Me whakapiri atu koe ki tō tākuta mēnā ka kite koe i tetahi pupuku hou e tipu haere ana, e huri haere ana rānei, ina koa mēnā kei te ara o te io. Ko te aromatawai wawe ka hoatu ki a koe te tūponotanga pai mō te maimoatanga angitu.

Kaua e tatari mēnā ka pā ki a koe ēnei tohu whakatūpato:

• Te pupuku e nui haere ana i te wā
• Te ngenge hou, te ngoikore rānei o ō ringa, o ō waewae rānei
• Te mamae e kino haere ana, kāore rānei e whakautu ki ngā maimoatanga noa
• Ngā huringa i te āhua, te wiri rānei e mau tonu ana
• Tetahi huringa awangawanga mēnā kei a koe te NF1

Mēnā kei a koe te neurofibromatosis momo 1, he mea nui rawa te whai i ngā tirotiro auau me te ripoata i ngā huringa i ngā pupuku o mua, i ngā tohu hou rānei. Ka taea e tō rōpū hauora te awhina i te wehewehe i waenga i ngā huringa pai me ngā tohu e hiahia ana ki te aro nui.

He aha ngā take tūponotanga mō te mate pukupuku pūtau kiri hiko taha?

Ka taea e ngā take maha te whakapiki i ō tūponotanga ki te whanake i te MPNST, ahakoa ko te whai i ngā take tūponotanga kāore e tikanga ka whiwhi koe i tēnei mate pukupuku. Ko te mārama ki ēnei take ka āhei te awhina i a koe me tō tākuta ki te mataara mō ngā tohu wawe.

Ko ngā take tūponotanga tino nui ko:

• Neurofibromatosis momo 1: Ko te take tūponotanga tino kaha e mohiotia ana
• Te whakamahinga radiation o mua: Ina koa te radiation whakaora
• Te tau: Ka tino puta i ngā pakeke, me te nui o te mate i ngā tau 20-50
• Te ira tangata: Ka tino puta i ngā tāne atu i ngā wāhine
• Ngā neurofibromas o mua: Ngā pukupuku io pai e taea pea te huri i ētahi wā
• Ngā āhuatanga ira: Ngā āhuatanga onge e pā ana ki te whanaketanga io

Ko ētahi take tūponotanga onge rawa ko te whakamahinga i ētahi matū, te whai rānei i ētahi atu āhuatanga ira e pā ana ki te kiko io. Ka taea e tō tākuta te awhina i te aromatawai i tō tūponotanga motuhake i runga i tō hītori hauora me tō papamuri whānau.

He aha ngā raruraru pea o te mate pukupuku pūtau kiri hiko taha?

Ka taea e te MPNST te arahi ki ngā raruraru maha, mai i te pukupuku anō, mai i te maimoatanga rānei. Ko te mārama ki ēnei wāhi pea ka āhei te awhina i a koe ki te whakarite me te mahi tahi me tō rōpū hauora ki te whakaiti i ngā tūponotanga.

Ko ngā raruraru mai i te pukupuku pea ko:

• Te kino o te io: Te ngaro tonu o te mahi i ngā io pānga
• Te horapa: Te horapa o te mate pukupuku ki ngā pūkahukahu, ngā wheua, ki ētahi atu kiko rānei
• Te hokinga mai o te rohe: Te tipu anō o te pukupuku i te wāhi kotahi
• Te haepapa: Te ngaro o te nekehanga, te mārama rānei i ngā wāhi pānga
• Te mamae roa: Te pouri tonu mai i te pānga io

Ko ngā raruraru e pā ana ki te maimoatanga pea ko ngā tūponotanga pokanga, ngā pānga o te chemotherapy, ngā pānga rongoā radiation rānei. Ka kōrero tō rōpū hauora i ēnei wāhi pea, ka mahi ki te whakaiti i a rātou i te wā e whakapiki ana i ngā painga o tō maimoatanga.

Me pēhea te whakamārama o te mate pukupuku pūtau kiri hiko taha?

Ko te whakamārama i te MPNST e hiahia ana ki ngā mahi maha hei whakau i te whakamārama me te whakatūpato i te nui o te pukupuku. Ka tīmata tō tākuta me te tirotiro tinana, ka tono i ngā whakamātautau motuhake hei whiwhi i te whakaahua katoa.

Ko te tukanga whakamārama e ngā mea nei:

1. Te tirotiro tinana: Ka tirotirohia e tō tākuta te pupuku, ka whakamātautau i te mahi io
2. Te whakamātautau MRI: Ko ngā whakaahua taipitopito e whakaatu ana i te rahi o te pukupuku me te hononga ki ngā io
3. Te whakamātautau CT: Pea ka whakamahia hei tirotiro mēnā kua horapa ki ētahi atu wāhi
4. Te biopsy: Ko te tauira kiko iti e whakau ana i te whakamārama
5. Te whakamātautau PET: I ētahi wā ka whakamahia hei titiro mēnā kua horapa te mate pukupuku
6. Te whakamātautau ira: Pea ka tūtohutia mēnā kei te whakapaehia te NF1

Ko te biopsy te whakamātautau tino nui, no te mea koia anake te huarahi ki te whakamārama tino i te MPNST. Ka whakarite tika tō tākuta i tēnei tukanga hei whiwhi i ngā hua tika i te wā e whakaiti ana i te tūponotanga o te horapa i ngā pūtau mate pukupuku.

He aha te maimoatanga mō te mate pukupuku pūtau kiri hiko taha?

Ko te maimoatanga mō te MPNST e whakauru ana i te pokanga hei huarahi matua, e hono atu ana ki ētahi atu rongoā. Ka whakaritea tō mahere maimoatanga ki tō āhuatanga motuhake, tae atu ki te wāhi o te pukupuku, te rahi, me te horapa atu rānei.

Ko ngā whiringa maimoatanga matua ko:

• Te pokanga: Te tango katoa i te pukupuku me ngā taha whānui ina taea
• Te rongoā radiation: Ngā hihi kaha ki te whakamate i ngā pūtau mate pukupuku e toe ana
• Te chemotherapy: Ngā rongoā hei whai i ngā pūtau mate pukupuku puta noa i tō tinana
• Ngā whakamātautau hauora: Te uru atu ki ngā maimoatanga hou, ngā whakamātautau rānei
• Te rongoā e whai ana i te taumata: Ngā rongoā e whakaeke ana i ngā āhuatanga motuhake o te pūtau mate pukupuku

Ko te pokanga te maimoatanga tuatahi, te tino nui hoki. Ka ngana tō kaitātari ki te tango i te pukupuku katoa me ētahi kiko hauora e karapotia ana hei whakau i te ngaro o ngā pūtau mate pukupuku katoa. I ētahi wā, ko te tikanga tenei ka ngaro te mahi io, engari ka kōrero tō rōpū ki a koe i ēnei whakawhitinga.

Mō ngā pukupuku kaore e taea te tango katoa, kua horapa atu rānei, pea ka tūtohu tō tākuta i te chemotherapy, i te rongoā radiation rānei. Ka taea e ēnei maimoatanga te awhina i te whakaiti i ngā pukupuku, te whakaheke i tō rātou tipu, te whakaiti rānei i ngā tohu.

Me pēhea te whakahaere i ngā tohu i te kāinga i te wā e maimoatia ana te mate pukupuku pūtau kiri hiko taha?

Ko te whakahaere i ngā tohu i te kāinga he wāhanga nui o tō mahere tiaki whānui. Ka taea e ngā rautaki ngāwari te awhina i a koe kia pai ake te noho, kia mau tonu ai tō kounga ora i te wā e maimoatia ana.

Ko ēnei ngā huarahi ki te whakahaere i ngā tohu noa:

• Te whakahaere mamae: Whakamahia ngā rongoā kua tohua penei i te aratohu, ka whakamātautau i te whakamahana ngawari, te whakamakuku rānei
• Te ngenge: Whakatūpatohia te mahi me te okioki, kia mau tonu ai te wā moe
• Te kai: Kai i ngā kai iti, auau, kia mau tonu ai te inu wai
• Te whakakori ngawari: Te hikoi mārama, te whakatete rānei penei i te whakaae a tō tākuta
• Te whakahaere ahotea: Whakamātautau i ngā tikanga whakamahinga, te whakaaroaro rānei
• Te tiaki kiri: Kia ma, kia maroke te wāhi pokanga

Tirohia tonu ki tō rōpū hauora i mua i te whakamātautau i ngā huarahi hou ki te whakahaere i ngā tohu. Ka taea e rātou te aratohu i a koe ki te mea e haumaru ana, e whai hua ana mō tō āhuatanga motuhake.

Me pēhea te whakarite mō tō hui tākuta?

Ko te whakarite mō tō hui ka āhei te whakau i te whiwhi i te nuinga o tō wā me tō tākuta. Ko te haere mai i te whakahaere me ngā pūrongo me ngā korero ka whakaputa i te haerenga kia hua ake mō te katoa.

I mua i tō hui:

1. Tuhia ō tohu: Tāpirihia te wā i tīmata ai rātou me te pēhea te huringa
2. Rārangihia ō rongoā: Tāpirihia ngā taapiri me ngā rongoā ka hokona
3. Kohikohia ngā rēkōta hauora: Mau mai ngā hua whakamātautau o mua me ngā rangahau whakaahua
4. Whakaritea ngā pūrongo: Tuhia te mea e hiahia ana koe ki te mohio mō tō āhuatanga
5. Mau mai te tautoko: Whakaarohia te haere mai o tētahi mema whānau, tētahi hoa rānei
6. Tāpirihia te hītori whānau: Tāpirihia tetahi whānau e pangia ana e te mate pukupuku, i ngā āhuatanga ira rānei

Kaua e whakaroa ki te ui atu ki tetahi mea kaore koe e mārama. E hiahia ana tō rōpū hauora ki te awhina i a koe kia whai mōhio me te noho marie ki tō mahere tiaki.

He aha te mea nui mō te mate pukupuku pūtau kiri hiko taha?

Ko te MPNST he momo mate pukupuku onge engari he kino e hiahia ana ki te aro nui o te hauora me te tiaki motuhake. Ahakoa ka raru pea te whakamārama, he maha ngā tāngata e whakahaere angitu ana i tēnei āhuatanga me te maimoatanga tika.

Ko ngā mea tino nui hei mahara ko te kite wawe ka pai ake ngā hua, ko ngā whiringa maimoatanga e mau tonu ana te pai ake, kāore hoki koe e tūtaki ana i tēnei anake. Kei a tō rōpū hauora te wheako ki te MPNST, ka taea te aratohu i a koe i ia kaupae o tō tiaki.

Noho hono atu ki ō kaiwhakarato hauora, kaua e whakaroa ki te ui atu i ngā pūrongo, kia aro nui ki te tango i ngā mea kotahi i te wā. Me te tiaki hauora tika me te tautoko, ka taea e koe te mahi ki te whiwhi i te hua pai rawa mō tō āhuatanga.

Ngā pūrongo e ui pinepinetia ana mō te mate pukupuku pūtau kiri hiko taha

U1: He onge rawa te mate pukupuku pūtau kiri hiko taha?

He tino onge te MPNST, e 5-10% anake o ngā mate pukupuku kiko ngawari katoa. Ka puta i te 1 i te 100,000 tāngata ia tau i roto i te taupori whānui. Heoi, mēnā kei a koe te neurofibromatosis momo 1, ka nui ake tō tūponotanga ki te 8-13% i roto i tō oranga.

U2: Ka taea te whakaora i te MPNST?

Ko te tirohanga e whakawhirinaki ana ki ngā take maha, tae atu ki te rahi o te pukupuku, te wāhi, me te horapa atu rānei. Ina kite wawetia, tangohia katoatia me te pokanga, he maha ngā tāngata e pai ana. Heoi, ka taea e te MPNST te kaha, na reira he mea nui te tirotiro tonu me ētahi atu maimoatanga i ētahi wā mō te angitu roa.

U3: Ko te whai i te neurofibromatosis te tikanga ka whiwhi ahau i te MPNST?

Kāo, ko te whai i te NF1 kāore e tikanga ka whanake koe i te MPNST. Ahakoa ka whakapiki nui te NF1 i tō tūponotanga ki te taupori whānui, ko te nuinga o ngā tāngata e pangia ana e te NF1 kāore e whanake i tēnei momo mate pukupuku. Ko te tirotiro auau ka āhei te awhina i te kite i ngā huringa wawe mēnā ka puta.

U4: He tere te tipu o ēnei pukupuku?

Ko ngā tere tipu MPNST he rerekē rawa. Ko ētahi e tipu haere ana i roto i ngā marama, ngā tau rānei, ko ētahi atu ka taea te tipu tere ake i roto i ngā wiki. Me aromatawai e te tākuta tetahi pupuku e tipu haere ana, e huri haere ana rānei, ahakoa te tere o te huringa.

U5: He aha te rerekētanga i waenga i te MPNST me te pukupuku io pai?

Ko ngā pukupuku io pai e tipu ana i te wā roa, noho tonu i te rahi kotahi mō ngā wā roa, kāore hoki e tino pānga ki ngā tohu. Ko te MPNST e tipu ana i te tere ake, pea ka pā te mamae, ngā tohu io rānei, ā, he tūponotanga ki te horapa ki ētahi atu wāhanga o te tinana. Ko te biopsy anake ka taea te kī tino i te rerekētanga i waenga i ngā rua.