

Health Library
October 10, 2025
Question on this topic? Get an instant answer from August.
He mate toto onge te mate Moyamoya e pā ana ki ngā oko toto i tō roro. Ka puta mai i te whakaiti haere o ngā oko toto nui e whakarato ana i te toto ki tō roro, ā, ka mutu ka aukati i te wa roa.
Ina puta mai tēnei whakaiti, ka ngana tō tinana ki te whakakapi mā te hanga i ngā oko toto iti hou e rite ana ki te paowa i runga i ngā tirohanga hauora. Ko te tikanga o te kupu "moyamoya" ko te "paowa" i te reo Hapani, te wāhi i akohia whānuitia ai tēnei mate. Ka āwhina ēnei oko hou ki te pupuri i te rere o te toto ki tō roro, engari he ngoikore rātou, ā, ka taea te whakaeke i ngā raruraru.
Ka rerekē ngā tohu o te mate Moyamoya, kei runga i tō tau me te āhua o te pānga o te mate ki te rere o te toto o tō roro. He tokomaha ngā tāngata e whiwhi ana i ō rātou tohu tuatahi i te tamarikitanga, i te taitamarikitanga rānei, ahakoa ka puta te mate i tetahi tau.
Ko te mārama ki te mea hei titiro atu ka āwhina i a koe ki te rapu i te tiaki hauora tika. Ko ēnei ngā tohu nui ka kite koe:
Ki ngā tamariki, ka kite pea koe i ngā whakaroa whanaketanga, i ngā raruraru ako rānei e puta mai ana ohorere. Ka whiwhi etahi tamariki i ngā tohu e whakaohotia ana e ngā mahi penei i te tangi, te kōhū, te kaha tinana rānei, no te mea ka taea e ēnei mahi te whakaiti i te rere o te toto ki te roro kua ngoikore.
He mea nui kia mōhio kei taea e ngā tohu te haere mai, te haere atu rānei, ā, ka taea e ētahi tāngata te whai i ngā wā e tino pai ana i waenga i ngā wāhanga. Kāore tēnei e tikanga kua ora ake te mate.
Kāore i tino mōhiotia te take pono o te mate Moyamoya, engari kua kitea e ngā kairangahau etahi take whakauru. Ka puta mai pea i te whakakotahitanga o te tūāhua ira me ngā āhuatanga taiao.
He tino nui te wāhi o te ira tangata ki tēnei mate. E 10-15% pea o ngā keehi e rere ana i roto i ngā whānau, ā, kua kitea e ngā kāre e ngā rerekētanga ira motuhake e whakapiki ana i tō tūponotanga. Ko te rerekētanga ira RNF213 te take ira tino noa, ina koa ki ngā tāngata o te iwi Āhia ki te Raki.
Heoi, ko te whai i ēnei huringa ira tangata kāore e whakamana ka whanake koe i te mate. Ka taea hoki e ngā āhuatanga taiao me ētahi atu āhuatanga hauora te whakauru:
He maha atu te mate ki ngā tāngata o te iwi Āhia ki te Raki, ina koa ki ngā tāngata o Hapani, Kōrea, me Haina. He nui ake te tūponotanga o ngā wāhine ki te pāngia i ngā tāne.
Me rapu wawe koe i te tiaki hauora mena ka whiwhi koe i ētahi tohu e taea ai te tohu i te pōkainga roro, i te raruraru nui rānei o te roro. Kaua e tatari kia pai ake ngā tohu.
Waea atu ki ngā ratonga āwhina ohorere inaianei ka kite koe i te ngoikore ohorere i tetahi taha o tō tinana, te raruraru ki te kōrero, te mamae nui o te upoko e rerekē ana i te mea i whiwhi koe i mua, te huringa tirohanga ohorere rānei. Ka taea e ēnei te tohu i te pōkainga, e hiahia ana ki te maimoatanga wawe.
Whakaritea he whakatau me tō taote ina tata nei ka whiwhi koe i ngā mamae o te upoko e puta ana, ngā wāhanga ngoikore, ngenge rānei, ngā hopu kaore i whakamāramahia, ngā huringa haere mā te whakaaro rānei. Ahakoa he ngawari ēnei tohu, e tika ana kia arotakehia e te hauora.
Mō ngā mātua, titiro ki ngā tohu i ō tamariki penei i te whakahekenga whanaketanga ohorere, ngā raruraru ako hou, ngā wāhanga ngoikore e whakaohotia ana e te tangi, te kaha rānei, ngā huringa whānau rānei. Kāore pea ngā tamariki e taea te whakaatu mārama i ō rātou tohu, no reira ko ētahi atu huringa e manukanuka ana e tika ana kia uiuihia e te hauora.
Ka taea e ētahi take te whakapiki i tō tūponotanga ki te whanaketanga o te mate Moyamoya, ahakoa ko te whai i ēnei take tūponotanga kāore e tikanga ka whiwhi koe i te mate. Ko te mārama ki a rātou ka āwhina i a koe me tō kaiwhakarato hauora ki te titiro atu mō ngā tohu wawe.
Ko ēnei ngā take tūponotanga tino nui:
Ko ētahi take tūponotanga onge kei roto i ētahi āhuatanga ā-whakatipuranga, ngā whara o te ārō i mua, me ngā mate ira motuhake. Heoi, he tokomaha ngā tāngata e whai ana i ēnei take tūponotanga kāore e whanake i te mate Moyamoya, ā, ka whanake etahi tāngata kaore he take tūponotanga e mohiotia ana.
Mena he maha ngā take tūponotanga, kōrerohia ngā kōwhiringa whakamātautau me tō kaiwhakarato hauora. Ka taea e rātou te āwhina ki te whakatau mena he pai ake te aroturuki atu, te whakamātautau rānei mō tō āhuatanga.
Ka taea e te mate Moyamoya te arahi ki ētahi atu raruraru nui mena kāore i maimoatia, engari ko te mārama ki ēnei wāhi pea ka āwhina i a koe ki te mahi tahi me tō rōpū hauora ki te aukati i a rātou. Ko te āwangawanga nui ko te whakaiti i te rere o te toto ki tō roro ka taea te whakaeke i te kino pumau i te wa roa.
Ko ēnei ngā raruraru tino noa:
Ki ngā tamariki, ka taea e ngā raruraru atu te whakauru i ngā whakaroa whanaketanga, ngā raruraru ako, me ngā huringa whānau. Ka taea e ēnei te pānga nui ki te mātauranga me te whanaketanga pāpori o te tamaiti mena kāore i whakahaeretia tika.
Ko ngā raruraru onge engari nui ka taea te whakauru i ngā toto nui o te roro, te coma, te pōkainga mate rānei. Heoi, me te tiaki hauora me te maimoatanga tika, ka taea te aukati i te maha o ēnei raruraru, te whakaiti rānei i tō rātou pānga.
Ko te rongo pai ko te tautuhi wawe me te maimoatanga tika ka taea te whakaiti nui i tō tūponotanga ki te whiwhi i ēnei raruraru. He tokomaha ngā tāngata e whai ana i te mate Moyamoya e ora ana i ngā oranga tino pai, mahi nui me te whakahaere hauora tika.
Aroha mai, kāore he huarahi e mohiotia ana ki te aukati katoa i te mate Moyamoya, no te mea he maha ngā take ira tangata kaore e taea e koe te whakahaere. Heoi, ka taea e koe te tango i ngā kaupae ki te whakaiti i tō tūponotanga ki ngā raruraru, ā, ka taea pea te whakaheke i te whanaketanga o te mate.
Mena he hītori whānau o te mate Moyamoya, ka taea e te tohutohu ira tangata te āwhina i a koe ki te mārama ki tō tūponotanga, ki te mahi rānei i ngā whakatau whakamārama mō te whakamātautau me te aroturuki. He mea nui tēnei ina koa mena kei te whakaaro koe ki te whānau tamariki.
Ko te whakahaere i ētahi atu āhuatanga hauora e whakapiki ana i tō tūponotanga ka taea te āwhina. Mahi tahi me tō kaiwhakarato hauora ki te whakahaere tika i ngā āhuatanga penei i te toto teitei, te mate huka, me ngā mate ā-whakatipuranga. Ka taea e ēnei āhuatanga te whakaiti i ngā raruraru oko toto, te whakapiki rānei i tō tūponotanga ki te pōkainga.
Ko te karo i te whakaū rā kaore e hiahiatia, ina koa ki te ārō me te kaki, ka taea te āwhina ki te whakaiti i te tūponotanga i ētahi wāhi. Mena e hiahia ana koe ki ngā tikanga hauora e whakauru ana i te whakaū rā, kōrerohia ngā tūponotanga me ngā painga me tō kaiwhakarato hauora.
Ko te ora i te oranga hauora roro ka tautoko i tō hauora oko toto katoa. Kei roto i ēnei te whakakori tinana noa e tika ana mō tō āhuatanga, te kai tōtika e whai hua ana i ngā hua me ngā huawhenua, te kore e pāpaho, me te whakahaere pai i te ahotea.
Ko te tautuhi i te mate Moyamoya e hiahia ana ki te whakaahua roro motuhake e taea ai te whakaatu i te whakaiti o ngā oko toto me te hanganga o ngā oko toto iti hou. Ka tīmata tō taote me te hītori hauora me te whakamātautau tinana.
Ko ēnei ngā whakamātautau tautuhi matua:
Ka taea hoki e tō taote te tono i ngā whakamātautau toto ki te whakakore i ētahi atu āhuatanga e taea ai te whakaeke i ngā tohu rite, penei i ngā mate ā-whakatipuranga, i ngā raruraru toto toto rānei. Ka āwhina ēnei whakamātautau ki te whakarite ka whiwhi koe i te tautuhi tino tika.
Ka roa pea te tukanga tautuhi, no te mea ka taea e te mate Moyamoya te whakaatu i ētahi atu āhuatanga. E hiahia ana tō rōpū hauora ki te tino tika kia whakarite ai ka whiwhi koe i te maimoatanga tino tika mō tō āhuatanga motuhake.
I ētahi wāhi, ka taea e tō taote te tūtohutia te whakamātautau ira tangata, ina koa mena he whānau kei a koe e whai ana i te mate. Ka taea te āwhina i tēnei mōhiohio mō te whakarite maimoatanga me te tohutohu whānau.
Ko te maimoatanga mō te mate Moyamoya e aro ana ki te whakapai ake i te rere o te toto ki tō roro me te aukati i ngā raruraru penei i ngā pōkainga. Ko te whakawhitinga kei runga i ō tohu, i tō tau, me te āhua o te mate ina tautuhia.
Ko te maimoatanga pokanga te kōwhiringa tino pai mō te mate Moyamoya. Ko ēnei ngā huarahi pokanga matua:
Ko te whakahaere hauora he tino āwhina ki tō mahere maimoatanga. Ka taea e tō taote te tuhi i ngā rongoā ki te aukati i ngā toto toto, ki te whakahaere i ngā hopu mena ka puta, ki te whakahaere rānei i ētahi atu tohu. Ka taea e te rongoā mamae te āwhina ki ngā mamae o te upoko, ā, ka taea e ngā rongoā antiplatelet penei i te aspirin te whakaiti i te tūponotanga o te pōkainga.
Ko te kōwhiringa i waenga i te maimoatanga pokanga me te hauora kei runga i ngā take maha, tae atu ki tō tau, hauora katoa, te kaha o ngā tohu, me ngā manakohanga whaiaro. Ka mahi tahi tō rōpū hauora me koe ki te whakawhanake i te mahere maimoatanga e tika ana mō ō hiahia me ō āhuatanga motuhake.
He mea nui te tiaki aroturuki noa ahakoa ko tehea whakawhitinga maimoatanga e whiriwhiri ana koe. Ka āwhina tēnei ki te aroturuki i tō āhuatanga me te whakarite maimoatanga i te wa roa.
Ko te whakahaere i te mate Moyamoya i te kāinga e whakauru ana i te hanganga tautoko e whakapiki ana i te hauora roro me te whakaiti i tō tūponotanga ki ngā raruraru. Ka taea e ō tikanga o ia rā me ō kōwhiringa oranga te pānga nui ki te pai o tō whakahaere i tēnei mate.
He mea nui rawa te noho makuku, no te mea ka taea e te ngenge te whakaiti i ngā raruraru rere toto. Whakaarohia te inu wai maha i te rā, ina koa i te wā wera, i te wā ka mahi tinana rānei koe.
Aro atu ki ngā mahi ka taea te whakaoho i ngā tohu. Ka kite etahi tāngata ko te tangi, te kōhū, te kaha tinana nui rānei ka taea te whakaoho i ngā wāhanga. Ahakoa kaua e karo i ngā mahi tinana katoa, mahi tahi me tō kaiwhakarato hauora ki te rapu i ngā kōwhiringa whakakori e tika ana mōu.
Ko te whakahaere pai i te ahotea ka taea te āwhina ki te whakaiti i te auau me te kaha o ngā tohu. Whakaarohia ngā tikanga whakahaerenga penei i te manawa hohonu, te yoga ngawari, te whakaaroaro rānei. He mea nui hoki te moe pai mō te hauora roro me te ora.
Hangaia he pūnaha aroturuki tohu hei āwhina i a koe me tō kaiwhakarato hauora ki te mārama ki ngā tauira i tō āhuatanga. Tuhia te wā e puta mai ana ngā tohu, te mea i mahi koe, me te kaha o rātou. Ka taea te whai hua i tēnei mōhiohio mō te whakarite i tō mahere maimoatanga.
Pupurihia ngā korero whakapā āwhina ohorere, kia mōhio hoki ngā mema whānau ki ngā tohu o te pōkainga e hiahia ana ki te tiaki hauora wawe.
Ko te whakarite mō tō whakatau me te taote ka taea te āwhina ki te whakarite ka whiwhi koe i te hua pai o tō haerenga, ka whakarato hoki i tō kaiwhakarato hauora ki te mōhiohio e hiahia ana rātou ki te āwhina i a koe. Ko te whakarite pai ka arahi ki te whakawhitiwhiti korero pai ake me te tiaki.
I mua i tō whakatau, tuhia ō tohu katoa, tae atu ki te wā i tīmata ai rātou, te auau o te putanga, me te mea e whakaoho ana i a rātou. Kia tino mōhio ki te wā me te roa o ngā wāhanga, no te mea ka āwhina tēnei mōhiohio i tō taote ki te mārama pai ake ki tō āhuatanga.
Kohikohia tō hītori hauora, tae atu ki ētahi atu pōkainga, whara o te ārō, i te hītori whānau rānei o te mate Moyamoya, i ētahi atu āhuatanga oko toto rānei. Kawe mai he rārangi katoa o ngā rongoā katoa e inu ana koe, tae atu ki ngā rongoā-ā-te-kāinga me ngā taapiri.
Whakaritea he rārangi o ngā pātai e hiahia ana koe ki te ui. Whakaarohia te uiui mō ngā kōwhiringa maimoatanga, ngā whakarerekētanga oranga, ngā tohu whakatūpato hei titiro atu, me te wā hei rapu i te tiaki āwhina ohorere. Kaua e whakaroa ki te ui mō te whakamārama mena kāore koe e mārama ki tetahi mea.
Mena ka taea, kawe mai he mema whānau whakawhirinaki, he hoa rānei e taea te āwhina i a koe ki te mahara ki ngā mōhiohio nui me te whakarato tautoko i te whakatau. Ka taea hoki e rātou te kite i ngā tohu, i ngā huringa rānei kaore koe i kite.
Kawe mai ētahi atu rēkōta hauora, hua whakamātautau, i ngā tirohanga roro rānei kei a koe. Ka āwhina tēnei mōhiohio i tō taote ki te karo i te whakahoki i ngā whakamātautau kaore e hiahiatia, ka whakarato hoki i ngā mōhiohio turanga nui mō te whakataurite.
He mate nui engari ka taea te whakahaere te mate Moyamoya e pā ana ki te rere o te toto ki tō roro. Ahakoa ka ātaahua pea i te tīmatanga, ko te mārama kei reira ngā maimoatanga whai hua ka taea te whakarato i te tumanako me te aronga mō te haere tonu.
Ko te mea nui hei mahara ko te tautuhi wawe me te maimoatanga tika ka taea te whakapai ake i tō tirohanga me te kounga o te ora. He tokomaha ngā tāngata e whai ana i te mate Moyamoya e ora ana i ngā oranga tino pai, mahi nui me te whakahaere oranga tika.
He mea nui te mahi tata me te rōpū hauora e whai wheako ana ki te maimoatanga i te mate Moyamoya. Ko te tikanga kei roto i ēnei ngā neurologists, ngā neurosurgeons, me ētahi atu tohunga e taea ai te whakahaere i tō tiaki me te āwhina i a koe ki te whakarite i ngā whakatau maimoatanga.
Kaua e whakaroa ki te rapu tautoko mai i ngā whakahaere manawanui, ngā rōpū tautoko, i ngā ratonga tohutohu rānei. Ko te ora me te mate roa kāore e pā ana ki tō hauora tinana anake, engari ki tō oranga hinengaro me ō hononga.
Kia mahara he rerekē te wheako o ia tangata me te mate Moyamoya. Ko te mea e mahi ana mō tetahi tangata kāore pea te whakawhitinga pai mō tētahi atu, no reira he mea nui te mahi tahi me tō kaiwhakarato hauora ki te whakawhanake i te mahere maimoatanga whaiaro e whakautu ana ki ō hiahia me ō āhuatanga motuhake.
He wāhanga ira tangata te mate Moyamoya, engari kāore i tino whakatūturu i te tikanga noa. E 10-15% pea o ngā keehi e rere ana i roto i ngā whānau, ā, ko ngā rerekētanga ira motuhake penei i te RNF213 e whakapiki ana i te tūponotanga. Heoi, ko te whai i te rerekētanga ira tangata kāore e whakamana ka whanake koe i te mate. Mena he hītori whānau kei a koe, ka taea e te tohutohu ira tangata te āwhina i a koe ki te mārama ki tō tūponotanga me te mahi i ngā whakatau whakamārama mō te whakamātautau.
Kāore e taea e ngā tamariki te ora ake i te mate Moyamoya, no te mea he mate e haere tonu ana e tino kino haere ana i te wa roa kaore he maimoatanga. Heoi, me te tiaki hauora tika me te pokanga mena e hiahiatia ana, ka taea e ngā tamariki te whai i ngā hua pai me te ora noa. He mea nui rawa te maimoatanga wawe ki ngā tamariki ki te aukati i ngā whakaroa whanaketanga me ngā raruraru ako e taea ai te puta mai i ngā pōkainga iti e puta ana.
Me te maimoatanga tika, he tokomaha ngā tāngata e whai ana i te mate Moyamoya e whai ana i te roa o te ora noa, tata noa rānei. Ko te mea nui ko te tautuhi wawe me te whakawhitinga tika, ka taea te aukati i ngā raruraru nui penei i ngā pōkainga ka taea te whakapoto i te ora. He mea nui te tiaki aroturuki noa me te pupuri ki ngā tūtohu maimoatanga mō te pupuri i ngā hua pai mo te wa roa.
Ka taea e te hapu te whakaiti i te mate Moyamoya na te nui o te toto me te ahotea o te ngakau. Me mahi ngā wāhine e whai ana i te mate Moyamoya me tō rātou neurologist me tō rātou obstetrician i te wa e whakaaro ana ki te hapu me te hapu katoa. Me te aroturuki ata me ngā whakaritenga tika, ka taea e te maha o ngā wāhine e whai ana i te mate Moyamoya te whai i ngā hapu angitu, ahakoa te tūponotanga o ngā raruraru he nui ake i ngā wāhine kaore i te mate.
Aro atu ki te pupuri i te hauora pai katoa mā te whakakori tinana e tika ana mō tō āhuatanga, te noho makuku, te whakahaere pai i te ahotea, me te whiwhi moe pai. Karohia ngā mahi ka taea te whakaoho i ngā tohu, penei i te kaha tinana nui, te manawa nui rānei. Kaua e pāpaho, no te mea ka taea te whakaiti i ngā raruraru oko toto. Mahi tahi me tō kaiwhakarato hauora ki te whakawhanake i te mahere whaiaro e whakaaro ana ki ō tohu me ō hiahia maimoatanga motuhake.
6Mpeople
Get clear medical guidance
on symptoms, medications, and lab reports.