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October 10, 2025
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Ko te mate whenua o Paget he āhuatanga roa e tupu tere ana ō wheua, ka nui haere, ka ngoikore, ka hē te āhua. Whakaarohia he tere rawa te mahi hanga wheua o tō tinana i etahi wāhi, ka hangaia he wheua nui atu, engari kāore i te kaha ake.
Ko te tikanga, ka pa tenei āhuatanga ki ngā tāngata neke atu i te 50 tau, ā, he maha ngā whānau e pā ana. Ahakoa e rangona ana he āwangawanga, he maha ngā tāngata e ora ana i te ora noa, i te ora mahi me te whakahaere tika me te tiaki.
Ka whakakore te mate o Paget i te tukanga whakahoki wheua noa o tō tinana. I te nuinga, ka pakaru te kōeke wheua tawhito ka whakakapihia e te kōeke wheua hou i roto i te huringa rite.
I te mate o Paget, ka tere haere tenei tukanga i roto i ētahi wheua. Ka tere rawa te pakaru o tō tinana i te wheua tawhito ka whakakapihia e te wheua hou e hanga tere ana. Ka hangaia e tēnei hanganga wheua tere he kōeke wheua nui atu, engari he ngoikore me te ngāwari ki te raruraru.
Ko te nuinga o te mate ka pa ki ngā wheua motuhake, kāore ki tō iwi katoa. Ko ō wheua upoko, tuara, anga, me ngā waewae ngā wāhi tino pāngia.
He maha ngā tāngata e pangia ana e te mate o Paget kāore e kite i tetahi tohu, ina koa i ngā wā tuatahi. Ki te puta mai ngā tohu, ka tupu haere pea, ka rerekē hoki i runga i ngā wheua e pā ana.
Ko ēnei ngā tohu tino noa ka kite koe:
Ko ngā tohu iti ake ka uru mai te pehi o te io, kei reira ngā wheua nui e pēhi ana ki ngā io e tata ana, ka puta he ngawari, he wiri rānei. Ka kite etahi i te ngenge, ahakoa he iti ake tenei, ka ngaro pea.
Ko te mamae mai i te mate o Paget he kino ake i te pō, ā, pea kāore e pai te whakautu ki ngā rongoā mamae noa. Ki te pāngia koe e te mamae wheua roa, he mea tika kia kōrero ki tō kaiwhakarato hauora.
Kāore i tino mōhiotia te take pono o te mate o Paget, engari e whakapono ana ngā kairangahau he hua mai i te whakakotahitanga o ngā take ira me ngā taiao e mahi tahi ana.
He tino mahi ngā ira i roto i tēnei āhuatanga. Ki te whai koe i ngā mema whānau e pangia ana e te mate o Paget, he nui ake te tūponotanga ka whāngaia koe. Kua kitea e ngā kārehu etahi ira e whakanui ana i tō tūponotanga, ko ngā rerekētanga i roto i te ira SQSTM1 tetahi o ngā tino noa.
Pea ka whakaoho hoki ngā take taiao i te mate i roto i ngā tāngata e whai take ira ana. E whakaaro ana etahi kairangahau ko ētahi mate huaketo i mua i te ora pea ka awhina ki te whāngaia te mate o Paget i muri mai, ahakoa kāore i tino whakamāramahia tēnei hononga.
Ko te tau tetahi atu take nui. Kāore te āhuatanga e pāngia ngā tāngata i raro i te 40 tau, ka nui haere te pānga i te pakeke. He iti te tūponotanga o ngā tāne ki te whāngaia te mate o Paget i te wāhine.
Me whakapiri atu koe ki tō kaiwhakarato hauora ki te pāngia koe e te mamae wheua roa kāore e pai ake me te okioki, ngā rongoā mamae noa rānei. He mea nui tēnei, ina koa ki te hohonu te mamae, te mamae, te kino ake rānei i te pō.
Ko ētahi atu tohu whakatūpato e hiahia ana ki te tiaki hauora ko ngā huringa e kitea ana i te āhua o tō wheua, pēnei i te kōwhiu o ō waewae, ngā huringa rānei i te āhua o tō anga. Ki te pāngia koe e ngā whati kāore i te mōhiotia, ngā wheua rānei e whati ana i te ngāwari atu i te tumanako, pea ka tohu tēnei i te mate o Paget.
Rapua te tiaki hauora ki te whāngaia koe e ngā raruraru rongohere, ngā mamae o te upoko roa, ngā tohu neurological rānei pēnei i te ngawari, te wiri rānei i ō ringa, waewae rānei. Pea ka tohu ēnei tohu kei te pā ngā wheua nui ki ngā io e tata ana, ngā hanganga rānei.
Ki te whai koe i te hītori whānau o te mate o Paget, he mea tika kia kōrero ki tō taakuta mō te whakamātautau, ahakoa kāore koe e whai tohu. Ka taea e te kite wawe te āwhina i te aukati i ngā raruraru me te whakapai ake i ō hua roa.
He maha ngā take ka whakanui i tō tūponotanga ki te whāngaia te mate o Paget, ko ētahi kei roto i tō mana whakahaere, ko ētahi kāore he wāhanga e taea te whakarereke o wai koe.
Ko ēnei ngā take tūponotanga tino nui:
Ko te whai i ēnei take tūponotanga kāore e tikanga ka whāngaia koe e te mate o Paget. He maha ngā tāngata e whai take tūponotanga maha ana kāore e whāngaia te āhuatanga, ko ētahi atu e whai take tūponotanga iti ana ka whāngaia.
E whakaatu ana te wāhi whenua he mahi, me ngā reiti teitei e kitea ana i Ingarangi, Kōtirana, Ahitereiria, me Aotearoa. He mea whakamīharo, he tino onge te mate i Āhia me Āwherika, e whakaatu ana i ngā awe ira me ngā taiao.
Ahakoa he maha ngā tāngata e pangia ana e te mate o Paget e ora ana kaore he raruraru nui, ka taea e te āhuatanga te arahi ki ngā raruraru e pā ana ki tō kounga ora me tō hauora katoa.
Ko ēnei ngā raruraru tino noa ka tūtaki koe:
Ko ngā raruraru onge engari he kino ka uru mai te mate pūngāwerewere wheua, ahakoa ka puta tenei i raro i te 1% o ngā tāngata e pangia ana e te mate o Paget. Pea ka whāngaia hoki ngā kohatu whatukuhu na te nui haere o te kōhatu i roto i tō toto mai i te pakaru tere o te wheua.
Ko te rongo pai ko te maimoatanga tika ka taea te whakaiti nui i tō tūponotanga ki te whāngaia ēnei raruraru. Ka taea e te tirotiro auau me te rongoā tika te āwhina i te pupuri i ō wheua hauora me te aukati i te tupu o ēnei raruraru.
Ko te whakamātautau i te mate o Paget ka tīmata ki tō taakuta e arotake ana i ō tohu me tō hītori hauora, ka whai ake he whakamātautau tinana hei tirotiro i te ngawari o te wheua, ngā hē rānei.
Ko ngā whakamātautau toto te mahi whakamātautau tuatahi. Ka tirotirohia e tō taakuta ō taumata alkaline phosphatase, e whakanuia ana i te mate o Paget. Ka piki ake tēnei enzyme ina pakaru ana ō wheua ka hangaia ano.
Ka homai e ngā X-rays ngā korero nui mō te hanganga o tō wheua, ka taea te whakaatu i ngā huringa tohu o te mate o Paget. Ka whakaatu ēnei whakaahua i ngā wheua nui, ngā wāhi o te nui o te kōeke wheua, me te ahua "purapura koroka" motuhake e rapu ana ngā taakuta.
Pea ka tūtohutia he karapa wheua hei kimi i ngā wāhi katoa e pā ana puta noa i tō iwi. Ko tēnei whakamātautau e uru ana ki te whakauru i te iti o te rauemi pāmahana e kohikohi ana i ngā wāhi o te hanganga wheua mahi, ka āwhina i tō taakuta ki te kite i te whānui o te mate.
I ētahi wā, pea ka tono tō taakuta i te CT scan, MRI rānei mō ngā whakaahua taipitopito ake, ina koa ki te whakapaehia ngā raruraru. Ka taea e ēnei whakamātautau te whakaatu me pēhea te pā o te mate ki ngā hononga e tata ana, ngā io, ngā hanganga rānei.
Ko te maimoatanga mō te mate o Paget e whai ana ki te whakahaere i ō tohu, te aukati i ngā raruraru, me te whakaiti i te tukanga whakahoki wheua hē. Ko te rongo pai ko ngā maimoatanga whai hua kei te wātea.
Ko ngā rongoā e kiia nei ko ngā bisphosphonates te maimoatanga matua mō te mate o Paget. Ka mahi ēnei rongoā ma te whakaiti i te tukanga pakaru wheua, ka taea te hanganga wheua noa ake. Ko ngā bisphosphonates noa ko te alendronate, risedronate, me te zoledronic acid.
Ka tīpako tō taakuta i te rongoā pai rawa atu i runga i tō āhuatanga motuhake. Ko ētahi bisphosphonates ka tangohia hei rongoā, ko ētahi atu ka hoatu hei whakaurunga. Ko ngā momo whakaurunga te nuinga o te manakohia na te mea he ngāwari ake, pea ka whai hua ake.
Ko te whakahaere mamae tetahi atu āhuatanga nui o te maimoatanga. Pea ka tūtohu tō taakuta i ngā rongoā mamae motuhake, ngā rongoā anti-inflammatory rānei hei āwhina i te whakahaere i tō ngoikoretanga. Ka taea hoki e te whakaora tinana te āwhina i te pupuri i tō kaha neke me tō kaha.
I ētahi wā onge kei reira ngā raruraru e whāngaia ana, pea ka hiahiatia te pokanga. Pea ka uru mai tēnei ki te whakakapi hononga mō te mate hononga kino, ngā mahi rānei hei whakatika i ngā hē o te wheua e pā ana ki tō mahi.
Ko te whakahaere i te mate o Paget i te kāinga e uru ana ki te mahi i ngā whiringa ora e tautoko ana i tō hauora wheua me tō oranga pai katoa. Ka taea e ngā huringa iti i tō mahi o ia rā te whakarereke i te āhua o tō āhua.
He mea nui te noho mahi hei pupuri i tō kaha wheua me tō kaha neke. Ka taea e ngā whakakorikori iti-pānga pēnei i te hikoi, te kauhoe, te hikoi paihikara rānei te āwhina i te pupuri i ō wheua me ō hononga hauora kaore e tino pēhi i ngā wāhi e pā ana.
He mahi nui te kai i te hauora wheua. Kia tino whiwhi koe i te nui o te kōhatu me te hua D mā tō kai, ngā taapiri rānei. Ko ngā kai e whai kōhatu ana ko ngā hua waiū, ngā rau kakariki, me ngā kai kua whakakikitia.
Ka taea e te whakaora wera te āwhina i te whakahaere i te mamae me te ngoikore. Whakamātauhia ngā kaukau mahana, ngā papa whakamahana, ngā kākahu wera rānei i runga i ngā wāhi mamae. Ka kite etahi ko te whakakapi i te wera me te makariri te tino whakaora.
Hangaia he taiao haumaru i te kāinga hei aukati i ngā hinga me ngā whati. Tangohia ngā mohiti ngawari, kia pai te mārama, kia tāutahia ngā pou hopu i roto i ngā ruma kaukau ki te hiahiatia. Na te mea he ngāwari ake te whati o ngā wheua e pā ana ki te mate o Paget, ka nui ake te hiranga o te aukati i ngā hinga.
Ko te whakamahere mō tō hui ka taea te āwhina i te whakarite ka whiwhi koe i te nuinga o tō wā me tō kaiwhakarato hauora, ka whiwhi i te tiaki pai rawa atu mō tō āhuatanga.
Tuhia katoa ō tohu, tae atu ki te wā i tīmata ai, he aha te mea e pai ake ai, te kino ake rānei, me pehea te pā ki ō mahi o ia rā. Kia tino mōhiotia ō taumata mamae me ngā huringa kua kitea e koe i ō wheua, kaha neke rānei.
Kawe mai he rārangi katoa o ngā rongoā katoa e tangohia ana e koe, tae atu ki ngā rongoā noa, ngā taapiri, me ngā huaora. Ka āwhina tēnei korero i tō taakuta ki te karo i ngā mahi pea, ki te mōhio ki ngā maimoatanga kua whakamātautauhia e koe.
Kohikohia tō hītori hauora whānau, ina koa ngā whānau tata kua whai mate o Paget, ngā āhuatanga wheua rānei. Ka taea e tēnei korero te tino nui mō tō whakamātautau me te mahere maimoatanga.
Whakamahia he rārangi o ngā pātai e hiahia ana koe ki te ui. Whakaarohia te ui mō ngā whiringa maimoatanga, ngā pānga pea, ngā whakarereketanga ora, me te aha e tatari ana i te heke mai. Kaua e whakaroa ki te ui mō te whakamārama ki te kore tetahi mea e mārama ana.
Kawe mai he hoa whakawhirinaki, mema whānau rānei ki te taea. Ka taea e rātou te āwhina i a koe ki te mahara ki ngā korero nui me te whakarato tautoko ngākau i tō hui.
Ko te mate whenua o Paget he āhuatanga e taea te whakahaere e pā ana ki te tupu o ō wheua, te hanga hou rānei. Ahakoa ka taea te puta mai te mamae me ngā raruraru, kei te wātea ngā maimoatanga whai hua hei āwhina i a koe ki te pupuri i te kounga ora pai.
Ko te mea tino nui hei mahara ko te whakamātautau wawe me te maimoatanga ka taea te aukati i te maha o ngā raruraru kino e hono ana ki tēnei āhuatanga. Ki te pāngia koe e te mamae wheua roa, he hītori whānau rānei o te mate o Paget, kaua e whakaroa ki te kōrero ki tō kaiwhakarato hauora.
Me te tiaki hauora tika, ngā whakarereketanga ora, me te tirotiro auau, ka taea e te nuinga o ngā tāngata e pangia ana e te mate o Paget te haere tonu ki te ora mahi, ora whai hua. Ko te matua ko te mahi tata atu ki tō rōpū hauora ki te kimi i te huarahi maimoatanga e pai ana mōu.
Ae, he tino mahi ngā ira i roto i te mate o Paget. Ki te whai koe i te whānau tata tuatahi e pangia ana e te āhuatanga, e whitu teitei ake tō tūponotanga i te taupori whānui. Heoi, ko te whai i te take ira kāore e whakamana ka whāngaia koe e te mate.
Ahakoa kāore he rongoā mō te mate o Paget, ka taea te whakahaere pai me te maimoatanga. Ka taea e ngā rongoā bisphosphonate te whakaiti nui i te whāngainga o te mate, ka maha ngā wā e whakarato ana i te whakaora roa mai i ngā tohu. He maha ngā tāngata e whiwhi ana i te whakahaere pai o tō rātou āhuatanga me te maimoatanga tika.
Mō te nuinga o ngā tāngata, kāore te mate o Paget e pā nui ki te roa o te ora. Ko te āhuatanga te nuinga e taea te whakahaere me te maimoatanga, ka taea te aukati i te nuinga o ngā raruraru me te tiaki tika. Ko ngā take onge anake kei reira ngā raruraru kino e whāngaia ana pea ka pā te mate ki te roa o te ora.
Ahakoa kāore te kai anake e taea te maimoatanga i te mate o Paget, ko te pupuri i te kai pai e tautoko ana i te hauora wheua katoa. Kia tino whiwhi koe i te nui o te kōhatu me te hua D, kia pupuri hoki i te kai rite e whai hua, huawhenua, me ngā hua katoa. Ka kite etahi ko te whakaiti i ngā kai whakaoho e āwhina ana ki te whakahaere mamae.
Ko te auau o ngā hui whai muri e whakawhirinaki ana ki tō āhuatanga motuhake me te whakautu maimoatanga. I te tīmatanga, pea ka kite koe i tō taakuta i ia toru marama hei tirotiro i te whai hua o te maimoatanga. Kia pumau tō āhuatanga, ko ngā tirotiro tau kotahi te nuinga o te nui, me ngā whakamātautau toto auau hei tirotiro i ō taumata alkaline phosphatase.
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