He aha te Mate Whatukuhu Polycystic? Tohutohu, Take, me te Maimoatanga

Ko te mate whatukuhu polycystic (PKD) tētahi āhuatanga ira tuku iho e tupu ai ngā putea kī wai e kiia nei ko ngā cysts i roto i ō whatukuhu i te roanga o te wā. Ka taea e ēnei cysts te whakawhānui ake i ō whatukuhu, ā, ka pā pea ki te pai o te mahi i te horoi i te paru i tō toto. Ahakoa ka rongo pea tenei he āwangawanga, he tokomaha ngā tāngata e ora ana i te ora tino whānuitia, mahi, me te tiaki tika me te arotake.

He aha te Mate Whatukuhu Polycystic?

Ka puta te PKD ina whānau mai ngā rōpū o ngā cysts i roto i ō whatukuhu e piki haere ana te rahi me te maha. Whakaarohia ēnei cysts hei pōro iti kī wai e hangaia ana i roto i te kiko o ō whatukuhu. Ko te nuinga o ngā tāngata ka whiwhi i tēnei āhuatanga i ō rātou mātua mā ō rātou ira.

E rua ngā momo matua o te PKD. Ko te momo tino noa, e kiia nei ko te autosomal dominant PKD, ka puta i te pakeketanga. Ko te momo onge, te autosomal recessive PKD, ka puta i ngā pepeha iti rānei, tamariki rānei. Ka taea e ngā momo e rua te pā ki te mahi o te whatukuhu, engari ka rerekē te whakawhānui me ngā tohu rerekē.

Ko ō whatukuhu te tikanga ka horoi i te paru me te wai nui atu i tō toto hei hanga i te mimi. Ina tangohia e ngā cysts te wāhi i roto i ō whatukuhu, ka taea e rātou te whakaroa i tēnei mahi nui. Heoi, he tokomaha ngā tāngata e pupuri ana i te mahi pai o te whatukuhu mo ngā tau maha, tekau tau rānei i muri i te whakatau.

He aha ngā Tohutohu o te Mate Whatukuhu Polycystic?

He tokomaha ngā tāngata e whai ana i te PKD kaore e kite i ngā tohu mo ngā tau maha, nā te mea ka whakawhānui haere te āhuatanga. Ina puta mai ngā tohu, ka tīmata pea rātou i te whakawhānui haere, ā, ka rite pea ki ētahi atu take hauora noa.

Ko ngā tohu tino noa ka pā atu ki a koe ko:

• Te mamae i tō tua, taha, kākahu rānei e haere mai ana, haere atu ana rānei
• Te toto i roto i tō mimi, ka taea te whakakī i te tae whero, whero, kōpara rānei
• Ngā mate mimi maha
• Ngā kōhatu whatukuhu e puta ai te mamae koi
• Te toto teitei, ahakoa i te tamarikitanga
• Ngā mamae o te upoko e tino noa ana, nui atu rānei i te noa
• Te ngenge, te ngoikore rānei

He tāngata anō e pā ana ki ngā tohu onge ake, pēnei i te ngākau nui i roto i ō rātou kopu, te makona wawe rānei i te kai. Ka puta ēnei nā te mea ka taea e ngā whatukuhu nui te pēhi ki ētahi atu okana i roto i tō puku.

He mea tika te mōhio ka rereke haere ngā tohu i waenga i ngā tāngata, ahakoa i roto i te whānau kotahi. He tāngata kei a rātou ngā tohu marama i ō rātou tekau tau rua tekau, engari kaore ētahi e pā ana ki ngā raruraru tae noa ki ō rātou tekau tau rima tekau atu rānei.

He aha ngā Momo o te Mate Whatukuhu Polycystic?

E rua ngā momo matua o te PKD, ā, ko te mārama ki te momo kei a koe ka āwhina i te aratohu i tō maimoatanga me ō tumanakohanga. Kei ia momo ngā tauira tuku ira me ngā raupapa wā rerekē.

Ko te autosomal dominant PKD (ADPKD) te momo tino noa, e pā ana ki te 90% o ngā tāngata e whai ana i te PKD. Me whiwhi noa koe i tetahi ira kino mai i tētahi mātua hei whānau i tēnei momo. Ka puta ngā tohu i waenga i ngā tau 30 me te 40, ahakoa ka kite ētahi i ngā tohu i mua atu, i muri atu rānei.

Ko te autosomal recessive PKD (ARPKD) he tino onge, he tino kino hoki. Me whiwhi koe i ngā ira kino mai i ngā mātua e rua hei whānau i tēnei momo. Ka puta pea i ngā pepeha i mua i te whānau, i te wā iti rānei, ā, ka taea te puta mai i ngā raruraru nui i te tīmatanga o te ora.

He momo tino onge anō e kiia nei ko te mate whatukuhu cystic whiwhi. Ka whānau mai tēnei ki ngā tāngata e whai ana i ngā raruraru whatukuhu mai i ētahi atu take, pēnei i te dialysis roa. Kāore i rite ki ngā momo tuku ira, kāore i tukuna atu tēnei momo mā ngā whānau.

He aha ngā Take o te Mate Whatukuhu Polycystic?

Ka puta te PKD nā ngā huringa i roto i ngā ira motuhake e whakahaere ana i te tipu me te mahi o ngā pūtau whatukuhu. Ko ēnei huringa ira te tikanga ka whiwhihia mai i ō mātua, ko te tikanga ka rere i roto i ngā whānau.

Mō te autosomal dominant PKD, ko ngā ira kino e kiia nei ko PKD1 me PKD2. Ko te ira PKD1 te take mo te 85% o ngā take, ā, ka nui ake te pānga ki ngā tohu nui ake. Ko te ira PKD2 te take mō ngā take toenga, ā, ka whakawhānui haere pea.

I roto i te autosomal recessive PKD, ko te ira e kiia nei ko PKHD1 te take. Me mau e ngā mātua e rua tēnei huringa ira hei whānau i te āhuatanga. Ki te mau e ngā mātua e rua te kawe, ka 25% te tūponotanga o ia haputanga hei whānau i te tamaiti e whai ana i te ARPKD.

He tino onge, ka taea e te PKD te whānau mai i ngā huringa ira hou kāore i whiwhihia mai i ngā mātua. Ka puta mai tēnei i raro iho i te 10% o ngā take, ko te tikanga ko te tangata te tuatahi i roto i tōna whānau e whai ana i te āhuatanga.

Nōhea te Tiro ki te Tākura mō te Mate Whatukuhu Polycystic?

Me whakapiri atu koe ki tō tākura ki te kite koe i te toto i roto i tō mimi, ahakoa kotahi noa te wā. Ahakoa he maha ngā take, he mea tika tonu te tirotiro, ina koa ki te whai koe i te hītori whānau o ngā raruraru whatukuhu.

Ko te mamae o te tua, taha rānei e kore e pai ake me te okioki tētahi atu take hei rapu i te tiaki hauora. He mea nui tēnei, ina koa ki te rereke te mamae i ngā mamae uaua noa, i te puta mai rānei me ētahi atu tohu pēnei i te kirika, i ngā huringa mimi rānei.

Ki te whai koe i te hītori whānau o te PKD, whakaarohia te kōrero ki tō tākura mō te tohutohu ira, ahakoa kei te pai koe. Ka taea e te kite wawe te āwhina i a koe me tō rōpū hauora ki te whakarite mō te heke mai me te hopu i ngā rarurangi i mua i te nui o te kino.

Ko te toto teitei i te tamarikitanga, ngā mate mimi maha, kōhatu whatukuhu rānei me whakaoho i te haerenga ki tō kaiwhakarato hauora. Ka taea e ēnei tohu te puta mai me te PKD, engari he take anō kei a rātou e hiahia ana ki te aromatawai tika.

He aha ngā Take Tūpono mō te Mate Whatukuhu Polycystic?

Ko te take tūpono nui rawa atu mō te PKD ko te whai i te mātua e whai ana i te āhuatanga. Nā te nuinga o ngā momo PKD ka tuku ira, ko tō hītori whānau te mea nui rawa atu e whakatau ana i tō tūponotanga.

Ki te whai tētahi o ō mātua i te autosomal dominant PKD, he 50% te tūponotanga o te whiwhi i te āhuatanga. Ko te tikanga mō ia tamaiti, he tūponotanga rite te whiwhi i te ira kino, i te ira noa rānei.

Mō te autosomal recessive PKD, me mau e ngā mātua e rua te kawe i te huringa ira. He tokomaha ngā kawe kaore e mōhio kei a rātou te kawe i te ira nā te mea kaore rātou e whai tohu.

Ka taea hoki e tō iwi te pā ki tō tūponotanga. Ka pā te PKD ki ngā iwi katoa, engari he maha ake ngā rerekētanga ira i roto i ētahi taupori. Heoi, ko te hītori whānau tonu te kairāhui kaha ahakoa te iwi.

He aha ngā Raruraru Ka Taea o te Mate Whatukuhu Polycystic?

Ahakoa he tokomaha ngā tāngata e whai ana i te PKD e pupuri ana i te hauora pai mo ngā tau maha, he mea whai hua te mōhio ki ngā raruraru ka taea kia taea ai e koe te mahi tahi me tō rōpū hauora hei aukati, hei whakahaere rānei i a rātou.

Ko ngā raruraru tino noa ko:

• Te toto teitei, e pā ana ki te 75% o ngā tāngata e whai ana i te PKD
• Te mate whatukuhu roa e taea te whakawhānui haere i ngā tekau tau
• Ngā mate whatukuhu e taea te nui ake te kino i ngā UTIs noa
• Ngā kōhatu whatukuhu e tino noa ake ana i ngā tāngata kāore e whai PKD
• Ngā raruraru cyst pēnei i te toto, te pakaru rānei, e puta ai te mamae nui
• Ngā cysts ate e kore e pā ki te mahi ate

Ko ngā raruraru onge ake, nui ake te kino, ka taea te whakauru i ngā raruraru o te taumanu o te ngakau, ngā aneurysms o te roro (ngā wahi ngoikore i roto i ngā oko toto), me te diverticulosis (ngā putea iti i te pakitara o te kōroa). Ahakoa ka rongo pea ēnei he wehi, ka pā noa ki te iti o ngā tāngata e whai ana i te PKD.

Ko te rongo pai ko te arotake noa e āwhina ana ki te hopu i ngā raruraru i te tīmatanga ina tino taea te whakaora. Ka tiaki tō rōpū hauora mō ēnei take, ā, ka taea pea te aukati i a rātou kei te riro hei raruraru nui.

Me pēhea te Whakatau i te Mate Whatukuhu Polycystic?

Ko te whakatau i te PKD te tikanga ka tīmata me ngā whakamātautau whakaahua e taea ai te whakaatu i ngā cysts āhuatanga i roto i ō whatukuhu. Ko te ultrasound te whakamātautau tuatahi, nā te mea he haumaru, he mamae kore, he pai ki te kite i ngā cysts whatukuhu.

Ki te whai koe i te hītori whānau o te PKD, ka taea e tō tākura te tūtohutia te whakamātautau ahakoa kaore koe e whai tohu. Ko te wā o te whakamātautau ka whakawhirinaki ki tō tau me tō hītori whānau, engari ka tīmata pea i ō tekau tau rua tekau, toru tekau rānei.

I etahi wā ka whakamahi ngā tākuta i ngā CT scans, MRI scans rānei hei tiki i ngā whakaahua taipitopito ake o ō whatukuhu. Ka taea e ēnei whakamātautau te whakaatu i ngā cysts iti ake, ā, ka hoatu he whakaaro pai ake ki te nui o te pānga o tō mahi whatukuhu.

He whakamātautau ira kei te wātea, ā, ka taea te whakau i te whakatau, ina koa i ngā take mārama kore, i ngā take whakarite whānau rānei. Heoi, ko ngā whakamātautau whakaahua te tikanga he nui mō te whakatau ina whakakotahitia ki te hītori whānau me ngā tohu.

He aha te Maimoatanga mō te Mate Whatukuhu Polycystic?

Ahakoa kāore he rongoā mō te PKD, ka taea e ngā maimoatanga whai hua te whakawhānui haere, te āwhina rānei i a koe ki te whakahaere i ngā tohu. Ko te whāinga ko te pupuri i a koe i te pai o te hauora me te tiaki i tō mahi whatukuhu mo te roa o te wā.

Ko te whakahaere i te toto teitei te wahi tino nui o te maimoatanga. Ko te pupuri i tō toto teitei i roto i te tawhiti hauora ka taea te whakawhānui haere i te kino o te whatukuhu. Ka taea e tō tākura te tuhi i ngā rongoā e kiia nei ko ngā ACE inhibitors, ARBs rānei, e tino tiaki ana mō ngā whatukuhu.

Mō te autosomal dominant PKD, ka taea e te rongoā e kiia nei ko te tolvaptan te āwhina i te whakawhānui haere o te tipu cyst me te tiaki i te mahi whatukuhu. Ka pai ake te mahi o tēnei maimoatanga ina tīmata i mua i te nui o te kino o te whatukuhu, ahakoa e hiahia ana ki te arotake noa.

Ko te whakahaere i ngā raruraru he mea nui hoki. Ka taea tenei te whakauru i ngā rongoā mō ngā mate whatukuhu, ngā rongoā mō ngā kōhatu whatukuhu, i ngā maimoatanga rānei mō ētahi atu take hauora e pā ana. Ka hanga e tō rōpū hauora he mahere whaiaro e whakawhirinaki ana ki ō hiahia motuhake.

Me pēhea te Tiaki i a koe i te Kāinga me te Mate Whatukuhu Polycystic?

Ko te tiaki i a koe i te kāinga he tino nui ki te whakahaere i te PKD. Ka taea e ngā huringa noho ora ngāwari te whakarereke i te āhua o tō rongo me te whakawhānui haere o tō āhuatanga.

Ko te pupuri i te wai pai e āwhina ana i ō whatukuhu ki te mahi pai ake, ā, ka whakaiti pea i te tūponotanga o ngā kōhatu whatukuhu. Whakamātauria te inu i te wai nui kia kowhai mā te mimi i te rā katoa.

Ko te whai i te kai pai mō te whatukuhu ka tautoko i tō hauora whānui. Ko te tikanga tenei ko te kai iti o te tote, te whakaiti i ngā kai tukatuka, me te whakauru i ngā hua me ngā huawhenua maha. Ka taea e tō tākura, i te kaiwhakaora kai rānei te hoatu i ngā aratohu motuhake e whakawhirinaki ana ki tō mahi whatukuhu.

Ko te whakakori tinana noa e pai ana mō tō ngakau, tō toto teitei, me tō hauora whānui. Ko te nuinga o ngā tāngata e whai ana i te PKD ka taea te whakakori tinana noa, ahakoa ka hiahia pea koe ki te karo i ngā hākinakina hononga e taea ai te whara i ngā whatukuhu nui.

Ko te whakahaere i te ahotea mā ngā tikanga whakamahinga, te moe pai, me ngā mahi whakangahau e tautoko ana i tō pūnaha mate, me tō hauora whānui. Kaua e whakaiti i te kaha o te tiaki pai i a koe i te whakahaere i tetahi āhuatanga roa.

Me pēhea te Aukati i te Mate Whatukuhu Polycystic?

Nā te mea ka tuku ira te PKD, kāore e taea e koe te aukati i te momo ira o te āhuatanga. Heoi, ka taea e koe te mahi hei whakawhānui haere, hei aukati rānei i ngā raruraru ina mōhio koe kei a koe.

Ki te rere te PKD i roto i tō whānau, ka taea e te tohutohu ira te āwhina i a koe ki te mōhio ki ō tūponotanga me te mahi i ngā whakatau whai whakaaro mō te whakarite whānau. Kāore tenei e whakarereke i te mea kei a koe te āhuatanga, engari ka āwhina i a koe ki te whakarite me te whakarite.

Ko te kite wawe mā te whakamātautau e tuku ana i te maimoatanga wawe, ka taea te whakarereke i te hua roa. Ki te whai koe i te hītori whānau o te PKD, korero ki tō tākura mō te wā e tika ana te whakamātautau.

Ko te noho i te noho ora hauora whatukuhu mai i te wā iti e pai ana mō te katoa, ahakoa kei a rātou te PKD, kāore rānei. Ka whakauruhia tenei te pupuri i te taumaha hauora, te kore whakakī, te whakaiti i te waipiro, me te whakahaere i ētahi atu āhuatanga hauora pēnei i te mate huka.

Me pēhea te Whakarite mō tō Hui Tākura?

Ko te whakarite mō tō hui e āwhina ana i a koe ki te whakamahi pai i tō wā me tō kaiwhakarato hauora. Kawe mai he rārangi o ō tohu katoa, tae atu ki te wā i tīmata ai rātou me te aha e pai ake ai, e kino ake ai rānei.

Kohikohia tō hītori hauora whānau, ina koa ngā whānau e whai ana i te mate whatukuhu, te toto teitei, te PKD rānei. He mea nui tēnei mō te aromatawai me te mahere maimoatanga a tō tākura.

Hangaia he rārangi o ngā rongoā, ngā taapiri, me ngā huaora katoa e inu ana koe. Whakauruhia ngā rāpoi me te auau o te inu. Ka taea e ētahi rongoā te pā ki te mahi whatukuhu, no reira he mea nui tēnei mōhiohio.

Tuhia ngā pātai e hiahia ana koe ki te ui. Kaua e manukanuka ki te ui i ngā pātai maha – e hiahia ana tō rōpū hauora ki te āwhina i a koe ki te mōhio ki tō āhuatanga me te maia ki tō mahere tiaki.

He aha te Tākutake Matua mō te Mate Whatukuhu Polycystic?

Ko te PKD tētahi āhuatanga e taea te whakahaere e pā ana ki te katoa. Ahakoa he āhuatanga ora tonu, he tokomaha ngā tāngata e whai ana i te PKD e ora ana i te ora tino whānuitia, mahi me te tiaki hauora tika me te whakahaere noho ora.

Ko te kite wawe me te maimoatanga e whakarereke ana i ngā hua. Ki te whai koe i te hītori whānau o te PKD, whakaarohia te kōrero ki tō kaiwhakarato hauora mō te whakamātautau, ahakoa kei te tino hauora koe.

Kia mahara kei te whakatau koe, kāore rānei e whakaiti i te mea ka taea e koe te whakatutuki. Me ngā maimoatanga me ngā rautaki whakahaere o nāianei, ka taea e koe te whakahaere i tō hauora me te haere tonu ki te whai i ō whāinga me ō moemoea.

Noho hono atu ki tō rōpū hauora, tiaki i a koe, ā, kaua e whakaroa ki te ui i ngā pātai, ki te rapu rānei i te tautoko ina hiahia koe. Kāore koe i te kotahi i roto i tēnei haerenga.

Ngā Pātai Tino Uihia mō te Mate Whatukuhu Polycystic

Ka taea te ora i te ora noa me te mate whatukuhu polycystic?

Ae, he tokomaha ngā tāngata e whai ana i te PKD e ora ana i te ora tino whānuitia, noa. Ahakoa e hiahia ana te āhuatanga ki te tiaki hauora haere tonu me ngā whakarereketanga noho ora, kāore e hiahia kia whakaiti i tō mahi, whanaungatanga, mahi rānei. Ko te matua ko te mahi tata atu ki tō rōpū hauora, te whai i ngā tūtohu maimoatanga, me te pupuri i te noho ora hauora. He tokomaha ngā tāngata e whai ana i te PKD e mahi ana, haereere ana, whakakori tinana ana, e pai ana ki ngā mea katoa e tino nui ana ki a rātou.

Ka tuku ira tonu aku tamariki i te PKD ki te whai ahau?

Ki te whai koe i te autosomal dominant PKD, he 50% te tūponotanga o ia tamaiti ki te whiwhi i te āhuatanga. Ko te tikanga he rite te tūponotanga ka whiwhi rātou, kāore rānei. Mō te autosomal recessive PKD, me whiwhi ngā tamariki i ngā ira kino mai i ngā mātua e rua hei whānau i te āhuatanga. Ka taea e te tohutohu ira te āwhina i a koe ki te mōhio ki tō āhuatanga motuhake me ō kōwhiringa whakarite whānau.

Me pēhea te tere o te whakawhānui haere o te mate whatukuhu polycystic?

Ko te whakawhānui haere o te PKD he tino rerekē i waenga i ngā tāngata. He tāngata e pupuri ana i te mahi pai o te whatukuhu mo ngā tekau tau, engari ka taea e ētahi te whakawhānui haere tere ake. Ko te tikanga, ka whakawhānui haere te autosomal dominant PKD i ngā tau maha. Ko ngā take pēnei i te whakahaere toto teitei, te hauora whānui, me te ira motuhake e pā ana ka taea te pā ki te tere o te whakawhānui haere o te āhuatanga. Ko te arotake noa e āwhina ana ki te aroturuki i ngā huringa i te roanga o te wā.

Ka taea e ngā huringa kai te āwhina i te whakawhānui haere o te PKD?

Ahakoa kāore te kai anake e taea te mutu i te PKD, ko te kai i ngā kai pai mō te whatukuhu ka āwhina pea ki te whakawhānui haere me te whakaiti i ngā raruraru. Ko te tikanga tenei ko te whakaiti i te tote, te pupuri i te wai pai, te kai i ngā hua me ngā huawhenua maha, me te pupuri i te taumaha hauora. He rangahau e whakaatu ana ko te whakaiti i te kai pūmua ka whai hua pea, engari me mahi tahi koe me tō rōpū hauora, i te kaiwhakaora kai rānei hei hanga i te mahere e whakatutuki ana ki ō hiahia motuhake.

He haumaru te whakakori tinana me ngā whatukuhu nui mai i te PKD?

Ko te nuinga o ngā tāngata e whai ana i te PKD ka taea te whakakori tinana haumaru, me noho mahi tonu mō tō hauora whānui. Heoi, ka hiahia pea koe ki te karo i ngā hākinakina hononga, i ngā mahi rānei e nui ana te tūponotanga o te whara o te kopu e taea ai te whara i ngā whatukuhu nui. Ko ngā mahi pēnei i te hikoi, te kauhoe, te hikareti, me te yoga te tikanga he haumaru, he whai hua hoki. Kōrero tonu ki tō kaiwhakarato hauora mō ō mahere whakakori tinana hei tiki i ngā tūtohu whaiaro e whakawhirinaki ana ki te rahi o ō whatukuhu me tō hauora whānui.