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Paralysisis Supranuclearis E Ahu Whakamua Ana

Tirohanga whānui

Ko te ngoikore o ngā pūtau i roto i te pūtake o te roro, te kiri o te roro, te cerebellum me ngā ganglia whanau – he rōpū pūtau hohonu kei roto i tō roro – koia te take o ngā raruraru whakahaere me te nekehanga o te palsy supranuclear arā.

He mate roro onge te palsy supranuclear arā e pā ana ki te hikoi, te tū, ngā nekehanga kanohi me te horomi. Ko te mate te hua o te pakaru o ngā pūtau i ngā wāhi o te roro e whakahaere ana i te nekehanga o te tinana, te whakahaere, te whakaaro me ētahi atu mahi nui. Ka kiia hoki te palsy supranuclear arā ko te mate a Steele-Richardson-Olszewski.

Ka kino haere te palsy supranuclear arā i te wā, ā, ka āhei te arahi ki ngā raruraru kino, pēnei i te mate huhu me te raruraru ki te horomi. Kāore he rongoā mō te palsy supranuclear arā, no reira ka āta whakahaere i ngā tohu.

Ngā tohu

Ko ngā tohu o te mate pāngarau supranuclear e whai ake nei: Te ngaro o te tūpato i te wā e hikoi ana. Ka taea te hinga whakamuri i te timatanga o te mate. Te kore e taea te whakatū tika i ō koutou kanohi. Ka kore pea e taea e te hunga e pangia ana e te mate pāngarau supranuclear te titiro ki raro. Ka raru pea rātou ki te mōrearea me te tiro rua. Ko te kore e taea te aro atu ki ngā kanohi ka taea ai te ringihia te kai e ētahi. Ka kitea hoki pea he kore whakaaro ki te kōrero nā te kore o te hononga kanohi. Ko ētahi atu tohu o te mate pāngarau supranuclear ka rerekē, ā, ka rite pea ki ngā tohu o te mate Parkinson me te mate wareware. Ka kaha ake ngā tohu i te wā, ā, ka uru pea ki: Te pakari, inā te kaki, me ngā nekehanga whakakake. Te hinga, inā te hinga whakamuri. Te kōrero puhoi, te kōrero whakapohehe rānei. Te raru ki te horomia, ka taea te whakaohooho, te whakakī rānei. Te mārō ki te mārama kanapa. Te raru ki te moe. Te ngaro o te hiahia ki ngā mahi whakangahau. Te whāinga ngāwari, te kata, te tangi rānei, he kore take. Te raru ki te whakaaro, te whakatau rapanga, me te whakatau. Te pouri me te manukanuka. Te ahua miharo, te wehi rānei o te mata, nō te ngohe o ngā uaua o te mata. Te māuiui. Me whakarite he whakatau ki tō kaimahi hauora mena ka pā atu ki a koe tetahi o ngā tohu i whakarārangihia i runga nei.

Āhea te kite i te tākuta

Whakapaa atu ki tō kaimahi hauora mena ka pāngia koe e tetahi o ngā tohu kua whakarārangihia i runga nei.

Ngā take

E kore e mohiotia te take o te mate pāwera o te supranuclear. Ko ona tohu e puta mai ana i te pakaru o ngā pūtau i ngā wāhi o te roro,inā, ko ngā wāhi hei āwhina i a koe ki te whakahaere i ngā nekehanga o te tinana me te whakaaro.

Kua kitea e ngā kairangahau he nui rawa te nui o te pūmua e kiia nei ko te tau i roto i ngā pūtau roro kua pakaru o te hunga e pangia ana e te mate pāwera o te supranuclear. Ka kitea hoki ngā kohinga o te tau i roto i ētahi atu mate o te roro, pēnei i te mate Alzheimer.

Ko te tino onge, ka puta te mate pāwera o te supranuclear i roto i tētahi whānau. Engari ehara i te mea mārama te hononga ira. Ko te nuinga o te hunga e pangia ana e te mate pāwera o te supranuclear kāhore i whiwhi i te mate.

Ngā āhuatanga tūpono

Ko te mea whakamārama anake mō te mate pāngarau supranuclear e whakaheke ana ko te pakeke. Ko te tikanga ka pā te āhuatanga ki te hunga kei ngā tekau tau e ono tekau mā waru, me ngā tekau tau e whitu tekau. Kaore i te mohiotia i roto i te hunga kei raro iho i te tekau tau e wha tekau.

Ngā raruraru

Ko ngā raruraru o te mate pāwera supranuclear ka puta mai ma te neke haere o ngā uaua, he puhoi, he uaua hoki. Ā, ētahi o ēnei raruraru:

  • Te hinga, ka taea te whara i te matenga, te whati i ngā wheua, me ētahi atu whara.
  • Te raruraru ki te aro atu ki ō koutou kanohi, ka taea hoki te whara.
  • Te raruraru ki te moe, ka taea te ngenge me te moe nui i te awatea.
  • Te kore e taea te titiro ki ngā mārama kanapa.
  • Te raruraru ki te horomi, ka taea te ngākau kino, te whakauru rānei i te kai, te wai rānei ki roto i te ara hau, e kiia nei ko te horomia.
  • Te mate huango, ka taea te puta mai i te horomia. Ko te mate huango te take mate tino noa i roto i te hunga e pangia ana e te mate pāwera supranuclear.
  • Ngā whāinga whakahihi. Hei tauira, te tū ake kahore he tatūnga, ka taea te hinga.

Hei karo i ngā tūponotanga o te ngākau kino, ka taea e tō kaiwhakaora hauora te tūtohutia he pūnaha whāngai. Hei karo i ngā whara nō te hinga, ka taea te whakamahi i te kaihaere, i te wīra rānei.

Te ārai

Kaore he uauatanga

Te tātaritanga

Ka uaua pea te whakatau i te mate pāngarau supranuclear na te mea he rite ngā tohu ki ngā tohu o te mate Parkinson. Ka whakaaro pea tō kaiāwhina hauora kei a koe te mate pāngarau supranuclear, ehara i te mate Parkinson, ki te:

  • Kāore ō wiri.
  • Kei te maha ngā hinga kaore i te marama te take.
  • He iti, he wā poto, kāore rānei te whakautu ki ngā rongoā Parkinson.
  • Kei te uaua te nekehanga o ō kanohi, inā te titiro ki raro.

Ka hiahia pea koe ki te MRI hei ako mena kei a koe te whakaiti i ngā wāhanga motuhake o te roro e hono ana ki te mate pāngarau supranuclear. Ka taea hoki e te MRI te awhina i te whakakore i ngā mate ka rite ki te mate pāngarau supranuclear, pēnei i te pēhanga toto.

Ka tūtohu pea hoki te whakamahi i te tātaritanga positron emission tomography (PET) hei tirotiro i ngā tohu o mua o ngā huringa i roto i te roro kaore pea e puta i runga i te MRI.

Te rongoā

Ahakoa kaore he rongoā mō te mate pāngarau supranuclear e piki haere ana, he rongoā kei te wātea hei awhina i te whakaheke i ngā tohu o te mate. Ko ngā kōwhiringa e wātea ana ko:

  • Ngā rongoā mate Parkinson, e whakapiki ana i ngā taumata o te matū roro e uru ana ki ngā nekehanga uaua ngawari, mana. Ko te whai hua o ēnei rongoā he iti, ā, he wā poto noa iho, e 2 ki te 3 tau te roa mō te nuinga o ngā turoro.
  • OnabotulinumtoxinA (Botox), ā, ka taea te whakauru i roto i ngā rāpoi iti ki ngā uaua o tō kanohi. Ka aukati a Botox i ngā tohu matū e pā ana ki te whakawhāiti i ngā uaua, ā, ka taea te whakapai ake i ngā koropupū o te kamo.
  • Ngā karāhe kanohi me ngā karāhe bifocal, rānei prism, ā, ka taea te awhina i ngā raruraru ki te titiro ki raro. Ka taea e ngā karāhe prism te kite i raro mō te hunga e pangia ana e te mate pāngarau supranuclear e piki haere ana, me te kore e nekehia o rātou kanohi ki raro.
  • Ngā aromatawai kōrero me te horomi, hei awhina i a koe ki te ako i ētahi atu huarahi hei whakawhitiwhiti kōrero me ngā tikanga horomi haumaru.
  • Ngā rongoā tinana me ngā rongoā mahi, hei whakapai ake i te toenga. Ko ngā whakakori kanohi, ngā papapātuhi kōrero me te whakangungu i te hikoi me te toenga ka taea hoki te awhina i te maha o ngā tohu o te mate pāngarau supranuclear e piki haere ana.

Kei te mahi ngā kairangahau ki te whakawhanake i ngā rongoā mō te mate pāngarau supranuclear e piki haere ana, tae atu ki ngā rongoā ka taea te aukati i te hanganga o te tau, te awhina rānei ki te whakangaro i te tau.

Te tiaki whaiaro

Kaore he uauatanga

Te whakarite mō tō whakaritenga

Kaore he uauatanga

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