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Mastocytosis Pūnaha

Tirohanga whānui

Systemic mastocytosis is a rare condition where your body has too many mast cells. Mast cells are a type of white blood cell, a part of your immune system, that are normally found in tissues throughout your body. Their job is to help protect you from infections.

In systemic mastocytosis, these extra mast cells gather in places like your skin, bone marrow, digestive system, or other organs. When something triggers these extra mast cells, they release chemicals. These chemicals can cause symptoms like those of an allergic reaction, ranging from mild discomfort to more serious inflammation that can damage organs. Things that can trigger these mast cell reactions include alcohol, spicy foods, insect bites, and some medicines.

Ngā tohu

Ko nga tohu me nga tohu o te mastocytosis pūnaha e whakawhirinaki ana ki te wāhanga o te tinana e pā ana ki te nui o ngā pūtau mast. Ka taea te whakaputu i te nui o ngā pūtau mast ki te kiri, ate, kōpiro, iho o te kōiwi, o te kōpiro rānei. He iti ake te nuinga, ka taea hoki te pā ki ētahi atu whēkau pērā i te roro, te manawa, te pūkahukahu rānei. Ko nga tohu me nga tohu o te mastocytosis pūnaha ka taea te whakauru: Te kōwhā, te mākūkū, te hīwera rānei. Te mamae o te puku, te mate hūware, te whakapairua, te ruaki rānei. Te mate hukihuki, te mate toto rānei. Te mamae o te kōiwi me te uaua. Te whakanui ake o te ate, te kōpiro, ngā pūtau waitara rānei. Te pōuri, te huri o te ngākau, te raruraru ki te aro atu. Ka whakahohea ngā pūtau mast ki te whakaputa i ngā mea e whakapā mai ai te kōhukihuki me nga tohu. He rerekē ngā mea whakahohe a te tangata, engari ko ngā mea noa ko: Te waipiro. Te whakakino o te kiri. Ngā kai kaha. Te korikori tinana. Ngā wero o te ngārara. Ētahi rongoā Āhea koe kite tākuta Kōrero ki tō tākuta mēnā he raruraru ki te kōwhā, te hīwera rānei, mēnā rānei he āwangawanga ki ngā tohu, ngā tohu rānei kua rārangi ake nei.

Āhea te kite i te tākuta

Kaore he uauatanga

Ngā take

Ko te nuinga o ngā keehi o te mastocytosis pūnaha e puta mai ana i te huringa ohorere (whakakē) i roto i te kiripuaki KIT. Ko te tikanga, ehara tenei hapa i roto i te kiripuaki KIT i te mea kua oti te whakawhiwhi. He maha rawa ngā pūtau mast e whakaputaina ana, ā, ka horapa ki ngā kiko me ngā tūpuna o te tinana, ka tukuna ngā mea penei i te histamine, leukotrienes me ngā cytokines e pā ana ki te mumura me ngā tohu.

Ngā āhuatanga tūpono

Kaore he uauatanga

Ngā raruraru

Ko ngā raruraru o te mastocytosis pūnaha e āhei ana te whakauru i:

  • Te tauhohenga anaphylactic. Ko tēnei tauhohenga mate pāwera nui e whakauru ana i ngā tohu me ngā tohu pēnei i te tere o te ngākau, te ngaro o te ngākau, te ngaro o te wairua me te pakaru. Ki te pāngia koe e te tauhohenga mate pāwera nui, pea e hiahia ana koe ki te whakauru i te epinephrine.
  • Ngā mate toto. Ka taea e ēnei te whakauru i te mate toto me te kore pai o te toto.
  • Te mate peptic ulcer. Ka taea e te mamae o te kopu roa te arahi ki ngā mate pūngio me te toto i roto i tōu pūnaha kai.
  • Te iti o te mātotoru o te wheua. Nō te mea ka taea e te mastocytosis pūnaha te pā ki ō wheua me te wheua wheua, pea ka raru koe ki ngā raruraru wheua, pēnei i te osteoporosis.
  • Te korenga o ngā kōeke. Ka taea e te hanga o ngā pūtau mast i roto i ngā kōeke o te tinana te whakaoho i te mumura me te kino ki te kōeke.
Te ārai

Kaore he uauatanga

Te tātaritanga

Hei whakatau i te mastocytosis pūnaha, ka tīmata pea tō tākuta mā te arotake i ō tohu me te kōrero mō tō hītori hauora, tae atu ki ngā rongoā kua inu koe. Ka taea e ia te tono whakamātautau ka rapu i ngā taumata teitei o ngā pūtau mast, te whakamahinga rānei e tukuna ana e rātou. Ka taea hoki te aromatawai i ngā kōpū e pā ana ki te āhuatanga. Ko ētahi whakamātautau pea: Ngā whakamātautau toto, mimi Te tātaritanga o te wheua wheua Te tātaritanga o te kiri Ngā whakamātautau whakaahua penei i te X-ray, te ultrasound, te karapa wheua me te CT scan Te tātaritanga o ngā kōpū e pā ana ki te mate, penei i te ate Te whakamātautau ira Ngā momo mastocytosis pūnaha Ko ngā momo matua e rima o te mastocytosis pūnaha: Te mastocytosis pūnaha ngāwari. Koinei te momo tino noa, ā, kaore e whakauruhia te mahi kore o ngā kōpū. He noa ngā tohu kiri, engari ka pā pea ki ētahi atu kōpū, ā, ka kaha ake pea te mate i te wā. Te mastocytosis pūnaha werawera. Ka hono tenei momo ki ngā tohu nui ake, ā, ka whakauru pea te mahi kore o ngā kōpū me te kino o te mate i te wā. Te mastocytosis pūnaha me tetahi atu mate toto, wheua wheua rānei. Ka tere te whanake o tēnei momo kino, ā, ka hono pinepine ki te mahi kore o ngā kōpū me te kino. Te mastocytosis pūnaha kaha. He kino ake tēnei momo onge, he nui ngā tohu, ā, ka hono pinepine ki te mahi kore o ngā kōpū me te kino. Te leukemia pūtau mast. Koinei te ahua tino onge, kaha o te mastocytosis pūnaha. Ko te mastocytosis pūnaha te nuinga o te wā ka puta ki ngā pakeke. Ko tētahi atu momo mastocytosis, te mastocytosis kiri, ka puta te nuinga o te wā ki ngā tamariki, ā, ka pā noa ki te kiri. Kāore e ahu whakamua ki te mastocytosis pūnaha. Te tiaki i te Kaupapa Hauora o Mayo Ka taea e tā mātou rōpū manaaki o ngā tohunga o te Kaupapa Hauora o Mayo te āwhina i a koe ki ō kaupapa hauora e pā ana ki te mastocytosis pūnaha Tīmata konei

Te rongoā

Ka rereke pea te maimoatanga, kei te whakawhirinaki ki te momo mastocytosis pūnaha me ngā kōpū o te tinana e pā ana. Ko te nuinga o te maimoatanga ko te whakahaere i ngā tohu, te whakaora i te mate, me te arotautanga tonu. Whakahaere i ngā mea whakaoho Mā te kimi me te karo i ngā take ka taea te whakaoho i ō pūtau mast, penei i ētahi kai, rongoā, rānei ngā kīwaha pepeke, ka āwhina i te pupuri i ō tohu mastocytosis pūnaha i raro i te mana. Rongoā Ka taea e tō tākuta te tūtohutia ngā rongoā hei: Whakaora i ngā tohu, hei tauira, mā ngā antihistamines Whakaiti i te waikawa puku me te ngoikoretanga i roto i tō pūnaha nakunaku Whakakore i ngā pānga o ngā mea e tukuna ana e ō pūtau mast, hei tauira mā ngā corticosteroids Tāpiri i te kiripuaki KIT hei whakaiti i te whakaputa o ngā pūtau mast Ka taea e te tohunga hauora te whakaako ki a koe me pēhea te hoatu i tētahi werohinga epinephrine ki a koe ano i te mea kei a koe tētahi whakautu mate pāwera nui ina whakaohohia ō pūtau mast. Kemoterapi Mēnā he mastocytosis pūnaha kaha tō, he mastocytosis pūnaha e hono ana ki tētahi atu mate toto, rānei he mate toto mast cell, ka taea pea te whakamaimoa koe mā ngā rongoā kemoterapi hei whakaiti i te maha o ngā pūtau mast. Nekehanga pūtau pūtau Mō te hunga he momo mastocytosis pūnaha whanui e kiia nei ko te mate toto mast cell, ka taea pea te whiriwhiri i tētahi nekehanga pūtau pūtau. Arotautanga tonu Ka arotaui tonu tō tākuta ki te tūāhua o tō āhuatanga mā te whakamahi i ngā tauira toto me te mimi. Ka taea pea e koe te whakamahi i tētahi kete kāinga motuhake hei kohikohi i ngā tauira toto me te mimi i te wā e pā ana koe ki ngā tohu, ā, ka hoatu tēnei ki tō tākuta tētahi whakaahua pai ake o te āhua o te mastocytosis pūnaha ki tō tinana. Ka taea te arotaui tonu i ngā ine matotoru wheua hei tirotiro i a koe mō ngā raruraru penei i te osteoporosis.

Te tiaki whaiaro

Ko te tiaki i te mate roa penei i te mastocytosis pūnaha ka taea te awangawanga me te whakamauiui. Whakaarohia enei rautaki: Akohia te mate. Akohia te nui o te mea e taea ana e koe mo te mastocytosis pūnaha. Katahi ka taea e koe te mahi i nga whiringa pai me te whakahaere mo koe ano. Āwhina i ō whānau me ō hoa ki te mārama ki te āhuatanga, ki te tiaki e hiahiatia ana, me nga whakatūpato haumaru e hiahia ana koe ki te tango. Rapua he rōpū o ngā tohunga whakawhirinaki. Me whakatau koe i ngā whakatau nui mō te tiaki. Ka taea e ngā pokapū hauora me ngā rōpū motuhake te tuku i ngā mōhiohio ki a koe mō te mastocytosis pūnaha, me te tohutohu me te tautoko, ā, ka taea te āwhina i a koe ki te whakahaere i te tiaki. Rapua ētahi atu tautoko. Ko te kōrero ki ngā tāngata e mahi ana i ngā wero rite tonu ka taea te tuku i ngā mōhiohio me te tautoko hinengaro ki a koe. Pātai atu ki tō tākuta mō ngā rauemi me ngā rōpū tautoko kei tō hapori. Ki te kore koe e pai ki te rōpū tautoko, ka taea pea e tō tākuta te whakapiri atu ki tetahi kua mahi i te mastocytosis pūnaha. Ka taea rānei e koe te kimi i tētahi rōpū tautoko, tētahi rānei i runga i te ipurangi. Pātai atu mō te āwhina mai i ngā whānau me ngā hoa. Pātai atu, tēnā rānei te whakaae ki te āwhina mai i ngā whānau me ngā hoa ina hiahiatia. Tangohia te wā mō ō hiahia me ō mahi. Ka taea e te tohutohu me tetahi tohunga hauora hinengaro te āwhina ki te whakarite me te whakahaere.

Te whakarite mō tō whakaritenga

Ahakoa ka whai whakaaro pea koe ki te toro atu ki tō tākuta whānau i te tīmatanga, ka tino tono pea ia koe ki tetahi tākuta e mōhio ana ki ngā mate pāwera me ngā mate ārai (tākuta pāwera) tetahi rānei e mōhio ana ki ngā mate toto (hematologist). Ko te whakarite me te whakaaro ki ngā pūrongo ka āwhina i a koe ki te whakamahi pai i tō wā ki te tākuta. Koinei etahi kōrero hei āwhina i a koe ki te whakarite mō tō whakaritenga tuatahi. Ngā mea ka taea e koe I mua i tō whakaritenga, hanga he rārangi e whai ana i: ō tohu, tae atu ki te wā i tīmata ai rātou, me te mea kei te whai take tetahi mea ki te whakaiti i a rātou, ki te whakapai ake rānei Ngā raruraru hauora kua pā ki a koe me ō rātou maimoatanga Ngā rongoā katoa, ngā huaora, ngā taonga whakaora tipu me ngā taonga tāpiri kai e inu ana koe Ngā pūrongo e hiahia ana koe ki te ui ki te tākuta Ui atu ki tētahi mema whakawhirinaki o te whānau, ki tētahi hoa rānei kia haere tahi mai ki a koe ki te whakaritenga. Tangohia tetahi hei tautoko wairua me te āwhina i a koe ki te maumahara ki ngā kōrero katoa. Ngā pūrongo hei ui ki tō tākuta pea: He aha te take pea o ō tohu? He take ke atu pea mō ēnei tohu? Ngā momo whakamātautau e hiahiatia ana e au? Me haere ahau ki tētahi tohunga? Ngā mea e tatari ana mai i tō tākuta Ka ui pea tō tākuta i ngā pūrongo penei i: Ngā tohu kei te pā atu ki a koe? Nō hea i tīmata ai ō tohu? Kei a koe ngā mate pāwera, kua pā atu rānei ki a koe etahi āhuatanga pāwera? He aha te mea e whakaohooho ana i tō mate pāwera? He aha te mea e whai take ana ki te whakaiti i ō tohu, ki te whakapai ake rānei? Kua whakatauhia, kua maimoatia rānei koe mō ētahi atu āhuatanga hauora? Ka ui atu tō tākuta ki ētahi atu pūrongo e hāngai ana ki ō whakautu, ō tohu me ō hiahia. I muri i te whiwhi i ngā kōrero taipitopito e pā ana ki ngā tohu me te hītori hauora o tō whānau, ka tono pea tō tākuta i ngā whakamātautau hei āwhina i te whakatau me te whakarite maimoatanga. Na te kaimahi o te Kura Hauora o Mayo

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