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October 10, 2025
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Ko te whakawhiti o ngā ngākau nui he mate ngākau nui tēnā e whakawhiti ai ngā oko toto nui e rua e puta ana i te ngākau. Ko te tikanga, kaore te toto e whai hau e tae tika ana ki te tinana, ā, kaore te toto kahore he hau e tae tika ana ki ngā pūkahukahu.
Ka puta tēnei āhuatanga i te wā hapu, i te wā e hanga ana te ngākau o te pēpi. E pā ana ki te 1 i roto i ngā pēpi 4,000 e whānau ana ia tau. Ahakoa he wehi te ahua, he rongoā pai kei a tātou nei e āwhina ana i ngā tamariki e pangia ana e tēnei āhuatanga kia ora ai i ngā oranga tino pai, hauora.
I roto i te ngākau noa, e rua ngā oko toto nui e kawe ana i te toto atu i te ngākau. Ko te aorta te kawe i te toto e whai hau ki te tinana, ā, ko te oko toto pūkahukahu te kawe i te toto kahore he hau ki ngā pūkahukahu. I te whakawhiti o ngā ngākau nui, ka whakawhitihia ēnei oko e rua, kāore rānei.
Whakaarohia he rite ki ngā huarahi e rua kua whakauruhia ō rātou huarahi putanga. Ka rere tonu te toto, engari ka haere ki ngā wāhi he. Ko te taha matau o te ngākau te pupuhi toto ki te tinana, kāore ki ngā pūkahukahu, ā, ko te taha maui te pupuhi toto ki ngā pūkahukahu, kāore ki te tinana.
Ka hanga tēnei i ngā porowhita rere toto e rua kaore e hono tika. Me kore te maimoatanga, kaore e taea e ngā pēpi te whiwhi hau nui ki ō rātou whekau me ngā kiko. Ko te rongo pai ko te taea e ngā tākuta te whakatika i tēnei āhuatanga mā te pokanga.
E rua ngā momo nui o tēnei āhuatanga, ā, ko te mārama ki te momo kei tō pēpi te āwhina i ngā tākuta ki te whakarite i te huarahi maimoatanga pai.
Whakawhiti Ngaro (D-TGA): Koinei te momo tino noa, kei reira anake ngā oko toto nui e whakawhitihia ana. Ko ngā ruma pupuhi o te ngākau me ngā pereti e mahi ana i te tikanga noa. E 70% o ngā take tēnei momo.
Whakawhiti Uaua (L-TGA): I roto i tēnei momo iti, ko ngā oko toto nui me ngā ruma raro o te ngākau e whakawhitihia ana. Ko tēnei momo te nuinga o te wā e haere tahi ana me ētahi atu hapa ngākau, ā, pea kaore e puta ngā tohu mo ngā tau.
Ka whakamahi tō tākuta i ngā whakamātautau motuhake hei whakatau i te momo kei tō tamaiti. Ka āwhina tēnei korero i a rātou ki te hanga i te mahere maimoatanga tino whai hua mō tō āhuatanga motuhake.
Ko te nuinga o ngā pēpi e pangia ana e tēnei āhuatanga e whakaatu ana i ngā tohu i roto i ngā rā tuatahi, kāore rānei wiki o te ora. Ka puta ngā tohu nā te mea kaore e whiwhi hau nui tō rātou tinana.
Ko ēnei ngā tohu ka kite koe i roto i tō pēpi iti:
Pea ka pai te ahua o ētahi pēpi i te wā whānau, engari ka puta ngā tohu i te wā e kati ana ngā hononga ngākau noa i roto i ngā rā tuatahi. Ki te kite koe i tētahi o ēnei tohu, whakapiri atu ki tō tākuta tamariki tonu.
I roto i ngā take onge me te whakawhiti uaua, pea kaore e puta ngā tohu tae noa ki muri i te tamarikitanga, kāore rānei ki te pakeketanga. Pea ka pāngia ēnei tamariki e te ngenge, te poto o te manawa i te wā e mahi ana, kāore rānei ngā raruraru o te tere o te ngākau.
Ka whanake tēnei āhuatanga i roto i ngā wiki 8 tuatahi o te hapu, i te wā e hanga ana te ngākau o tō pēpi. Kaore i tino mōhiotia te take tika, engari ka puta ina kaore e whanake tika ngā oko toto nui ki ō rātou wāhi noa.
I te wā o te whanaketanga ngākau noa, ka tīmata te ngākau hei pūtau ngākau ngāwari e huri ana, e wehewehe ana ki ngā ruma. I etahi wā kaore tēnei mahi uaua e puta tika, ka ārai i ngā oko toto ki te hono ki ngā ruma he.
Ko te nuinga o ngā take ka puta noa atu kahore he take motuhake. Kaore tēnei i te mea i mahi koe, kāore rānei i mahi i te wā hapu. Kaore tēnei āhuatanga e tuku iho, ahakoa he iti te piki o te tupono mō ngā haputanga kei mua ki te whānau kotahi te tamaiti e pangia ana e te hapa ngākau.
Ko ētahi take pea ka piki haere te tūpono, tae atu ki te mate huka o te whaea, ētahi rongoā i te wā hapu, kāore rānei te pakeke o te whaea. Heoi, ko te nuinga o ngā pēpi e pangia ana e tēnei āhuatanga e whānau ana ki ngā whaea kahore he take tūpono.
Karanga atu ki tō tākuta tamariki tonu ki te kite koe i te tae kikorangi i te kiri, ngutu, kāore rānei ngā makawe o tō pēpi iti. Ko tēnei tae kikorangi, e kiia nei ko te cyanosis, te tikanga kaore e whiwhi hau nui tō pēpi, ā, me āwhina tonu.
Me whakapiri atu hoki koe ki tō tākuta tonu ki te uaua tō pēpi ki te manawa, te kai kino, kāore rānei te ngenge, kāore rānei te ngangau. Ka taea e ēnei tohu te whanake tere i roto i ngā pēpi iti e pangia ana e ngā āhuatanga ngākau.
Ki te whakatauhia tō pēpi e tēnei āhuatanga i mua i te whānau, kia tino whānau koe i te whare hauora e whai pokapū ngākau tamariki ana. Ko te whai i ngā tohunga e rite ana mai i te wā whānau ka taea te whakarerekē nui i te tiaki o tō pēpi.
Mō ngā tamariki pakeke ake e pangia ana e te whakawhiti uaua, kia titiro ki ngā tohu penei i te ngenge kore noa i te wā e takaro ana, te poto o te manawa, kāore rānei ngā amuamu o te mamae uma. Pea ka whanake haere ēnei tohu, ā, me whakamātautau hauora.
Ko te nuinga o ngā pēpi e pangia ana e tēnei āhuatanga kahore he take tūpono motuhake, engari pea ka piki haere ētahi āhuatanga i te tupono. Ko te mārama ki ēnei take ka āwhina ki te kite wawe me te whakarite mahere tiaki.
Ko ēnei ngā take pea ka piki ake te tūpono:
Kia mahara ko te whai i ngā take tūpono kaore e tikanga ka pangia tō pēpi e tēnei āhuatanga. Ko te nuinga o ngā pēpi e whai ana i ēnei take tūpono e whānau ana me ngā ngākau tino hauora. I tetahi atu taha, ko te nuinga o ngā pēpi e pangia ana e te whakawhiti kahore he take tūpono e taea te tautuhi.
Me kore te maimoatanga, ka taea e tēnei āhuatanga te ārai i ngā raruraru nui nā te mea kaore e whiwhi hau nui te tinana. Ko te mārama ki ēnei raruraru te āwhina i te whakamārama he aha te nui o te maimoatanga tere.
Ko ngā raruraru tino tere:
Me te maimoatanga pokanga hou, ko te nuinga o ngā tamariki ka karo i ēnei raruraru nui. Heoi, ahakoa muri i te pokanga angitu, kei reira ētahi whakaaro roa. Pea ka uru atu ki ēnei te hiahia mō ētahi atu mahi, te tirotiro i te tere o te ngākau, kāore rānei ngā ārai mahi.
Ko te rongo pai ko te nuinga o ngā tamariki e whiwhi ana i te maimoatanga tika e tupu ana kia ora ai i ngā oranga noa, mahi. Ko te whai i te whai wāhi tonu ki te kaitohutohu ngākau tamariki te āwhina ki te hopu me te whakatika i ngā take wawe.
Ka taea e ngā tākuta te whakatau i tēnei āhuatanga i mua i te whānau, tika i muri i te whānau, kāore rānei i muri mai ki te whanake haere ngā tohu. Ko te tukanga whakatau te nuinga o te wā e tīmata ana ina kite tetahi i ngā tohu āwangawanga, kāore rānei i te tirotiro hapu noa.
I mua i te whānau, ka taea e te ultrasound e kiia nei ko te echocardiogram fetal te whakaatu i te hanganga o te ngākau. Ka hoatu e tēnei ultrasound motuhake ki ngā tākuta ngā whakaahua taipitopito o te rere o te toto i roto i te ngākau o tō pēpi. Ki te whakatauhia i mua i te whānau, ka taea e ngā tākuta te whakarite mō te tiaki tonu i muri i te whānau.
I muri i te whānau, ko te whakatau te nuinga o te wā e tīmata ana me te whakamātautau tinana kei reira te tākuta e whakarongo ana ki te ngākau me te tirotiro mō te tae kikorangi. Pea ka tono rātou i ngā whakamātautau maha tae atu ki te X-ray uma, te electrocardiogram (EKG), me te echocardiogram hei kite i te hanganga me te mahi o te ngākau.
I etahi wā ka hiahia ngā tākuta ki ētahi atu whakamātautau penei i te catheterization ngākau, kei reira rātou e whakauru ana i te pūtau angiangi ki ngā oko toto hei whiwhi i ngā whakaahua taipitopito ake. Ka āwhina ēnei whakamātautau i ngā tākuta ki te mārama ki te hanganga o te ngākau o tō tamaiti me te whakarite i te huarahi maimoatanga pai.
Ko te maimoatanga mō tēnei āhuatanga te nuinga o te wā e whai ana i te pokanga hei hono anō i ngā oko toto ki ngā ruma tika. Ko te rongo pai ko ngā tikanga pokanga kua pai ake te whakapai, ā, ko te nuinga o ngā tamariki e tino pai ana i muri i te maimoatanga.
I roto i ngā rā tuatahi o te ora, pea ka hiahia ngā tākuta ki te mahi i te mahi e kiia nei ko te balloon atrial septostomy. Ka hanga tēnei i te whakatuwhera wā poto i waenga i ngā ruma o runga o te ngākau, e tuku ana i te toto e whai hau me te toto kahore he hau ki te whakaranu pai ake tae noa ki te taea te mahi pokanga.
Ko te maimoatanga pokanga matua e kiia nei ko te mahi whakawhiti oko toto. Ka wehewehe ngā tākuta pokanga i ngā oko toto nui, ā, ka whakauru anō ki ngā ruma tika. Ka nekehia hoki e rātou ngā oko toto koroni, e whakarato ana i te toto ki te uaua ngākau anō. Ko tēnei pokanga te nuinga o te wā e mahia ana i roto i ngā wiki tuatahi o te ora.
Mō ngā take uaua, pea ka tūtohu ngā tākuta i tetahi huarahi rerekē e kiia nei ko te mahi Mustard, kāore rānei Senning, kei reira rātou e arahi anō ana i te rere o te toto mā ngā papatahi, kāore rānei te kiko o te ngākau anō. Ko te whiriwhiri e whakawhirinaki ana ki te hanganga motuhake o tō tamaiti me ētahi atu take.
I muri i te pokanga, ko te nuinga o ngā tamariki e hiahia ana ki te tiaki whai wāhi tonu me te kaitohutohu ngākau tamariki. Ka āwhina tēnei ki te whakarite ka mau tonu te mahi pai o te ngākau i te wā e tupu ana, e whanake ana tō tamaiti.
Ko te tiaki i tō tamaiti i te kāinga i muri i te pokanga ngākau e hiahia ana ki te aro ki ētahi wāhi nui. Ka hoatu e tō rōpū hauora ngā tohutohu motuhake, engari ko ēnei ngā aratohu whānui e āwhina ana ki te whakapakari i te ora.
Tuatahi, aro ki te kai me te whāngai. Pea ka ngenge tō pēpi i te wā e whāngai ana, na, tukua ngā kai iti ake, maha atu. Ki te uaua te whāngai u, kaua e whakaroa ki te tono āwhina mai i te kaitohutohu whāngai u e mārama ana ki ngā āhuatanga ngākau.
Kia titiro ki ngā tohu o te mate i te taha o te pokanga, tae atu ki te whero nui ake, te pupuhi, kāore rānei te rere. Kia ma, kia maroke te wahi tapahi penei i te tohutohu a tō rōpū pokanga. Ko te nuinga o ngā pēpi iti ka taea te kaukau ngāwari ina whakaae te tākuta.
Kia tirotirohia tō tamaiti mō ētahi tohu āwangawanga penei i te tae kikorangi nui ake, te uaua ki te manawa, te kai kino, kāore rānei te ngangau kore noa. Ko te whai i te rārangi tuhituhi o te wā ki te karanga atu ki te tākuta te āwhina i a koe ki te whakapono ki te tiaki o tō tamaiti.
I te wā e tupu ana tō tamaiti, pea ka hiahia rātou ki ētahi ārai mahi i te tīmatanga, engari ko te nuinga o ngā tamariki ka taea te whai wāhi i ngā mahi tamarikitanga noa. Ka ārahi tō kaitohutohu ngākau i a koe ki te mea e tika ana i ia wahanga o te whakaora.
Ko te whakarite mō ngā hui me te rōpū ngākau o tō tamaiti te āwhina i a koe ki te whakamahi pai i tō wā tahi, ā, kia whakarite ai koe ka whiwhi i ngā whakautu ki ō patai tino nui.
I mua i ia haerenga, tuhituhia ētahi tohu kua kite koe, ngā patai mō te tiaki o tō tamaiti, me ngā āwangawanga mō te whanaketanga, kāore rānei ngā mahi. Kawe mai he rārangi o ngā rongoā katoa e tangohia ana e tō tamaiti, tae atu ki ngā horopeta me te wā.
Kia pupuri i te rekoata o te tupu o tō tamaiti, ngā tauira whāngai, me ngā taumata mahi i waenga i ngā haerenga. Ka āwhina tēnei korero i ngā tākuta ki te mārama ki te pai o te mahi a tō tamaiti. Ka taea hoki te whai hua ngā whakaahua, kāore rānei ngā ataata o ngā tohu āwangawanga.
Kawe mai he mema whānau, kāore rānei he hoa whakawhirinaki ki ngā hui nui. Ko te whai i te tautoko te āwhina i a koe ki te tukatuka i ngā korero me te mahara ki ngā kōrero nui. Kaua e whakaroa ki te tono ki ngā tākuta kia whakamārama i ngā mea i ngā huarahi rerekē ki te kore tetahi mea e mārama ana.
Whakaritea tō tamaiti pakeke ake mō ngā hui mā te whakamārama i te mea ka puta i ngā kupu e tika ana mō te tau. Ko te kawe mai i ngā taonga whakamārama penei i te taonga tino pai te āwhina ki te whakaiti i te manukanuka mō kōrua.
Ko te mea tino nui hei mahara ko te whakawhiti o ngā ngākau nui he āhuatanga nui e hiahia ana ki te tiaki hauora tere, engari he tino taea te rongoā me ngā hua roa pai.
Me ngā tikanga pokanga hou, ko te nuinga o ngā tamariki e whiwhi ana i te maimoatanga tika e haere tonu ana kia ora ai i ngā oranga tino pai, mahi. Ka taea e rātou te whai wāhi ki ngā hākinakina, te haere ki te kura noa, me te whai i ō rātou moemoea penei i ētahi atu tamariki.
Ko te ki mō te angitu ko te whakatau me te maimoatanga wawe e ngā tohunga ngākau tamariki whai wheako. Ki te āwangawanga koe mō ngā tohu o tō tamaiti, whakawhirinaki ki ō tūmanako, ā, rapu āwhina hauora tonu.
Kia mahara kaore koe i te kotahi i roto i tēnei haerenga. Ko ngā rōpū ngākau tamariki e whai ana i ngā tākuta, ngā nēhi, ngā kaimahi pāpori, me ētahi atu tohunga e mārama ana ki ngā āhuatanga hauora me ngā āhuatanga ngakau o te tiaki i ngā tamariki e pangia ana e ngā āhuatanga ngākau.
Ae, ko te nuinga o ngā tamariki e whai ana i te pokanga angitu mō te whakawhiti e ora ana i ngā oranga tino noa. Ka taea e rātou te haere ki te kura, te takaro hākinakina, me te whai wāhi ki ngā mahi tamarikitanga noa. Pea ka hiahia ētahi ki te tirotiro tonu e te kaitohutohu ngākau, engari kaore tēnei e ārai i ō rātou mahi o ia rā. Ko te nuinga o ngā pakeke i whai i tēnei pokanga i te wā pēpi e haere tonu ana ki te whai i ō rātou whānau anō me te whai i te mahi e whiriwhiri ana rātou.
Ko te nuinga o ngā tamariki e whai ana i te mahi whakawhiti oko toto kaore e hiahia ki ētahi atu pokanga ngākau. Heoi, pea ka hiahia ētahi ki ngā mahi iti ki te whanake ngā take me ngā oko toto koroni, kāore rānei ngā pereti ngākau i te wā. Ka tirotiro tonu tō kaitohutohu ngākau o tō tamaiti i tō rātou ngākau, ā, ka whakamōhio atu ki a koe ki te hiahia ētahi atu maimoatanga.
Kāo, kahore he mea ka taea e koe te mahi rerekē hei ārai i tēnei āhuatanga. Ka puta te whakawhiti o ngā ngākau nui i te wā o te whanaketanga ngākau wawe, ā, kaore i te puta mai i tetahi mea e mahi ana ngā mātua, kāore rānei e mahi. Āe rawa ngā whaea e whai ana i ngā aratohu hapu katoa ka taea te whānau i ngā pēpi e pangia ana e tēnei āhuatanga. He rerekētanga whanaketanga noa tēnei e puta ana i te 1 i roto i ngā whānau 4,000.
Ko te wā e whakawhirinaki ana ki te āhuatanga motuhake o tō pēpi me ngā tohu. Ko ētahi pēpi e hiahia ana ki te pokanga i roto i ngā rā tuatahi, kāore rānei wiki o te ora, ā, ko ētahi atu pea ka tino pumau kia tatari poto ake. Ka tirotiro tika tō rōpū ngākau tamariki i tō pēpi, ā, ka tūtohu i te wā pai mō te pokanga e whakawhirinaki ana ki ō rātou hiahia motuhake me te hauora whānui.
Ki te whai koe i te tamaiti kotahi e pangia ana e te whakawhiti o ngā ngākau nui, ko te tupono o te whānau i tetahi atu tamaiti e pangia ana e tetahi momo hapa ngākau he nui ake i te noa, engari he iti tonu i te 2-3%. Ko te nuinga o ngā whānau e haere tonu ana ki te whānau i ngā tamariki atu me ngā ngākau tino noa. Ka taea e tō tākuta te kōrero i te tohutohu ira ki te hiahia koe ki ngā korero taipitopito ake mō ngā tūpono mō ngā haputanga kei mua.
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