He aha te Sarcoma Pleomorphic Korekore? Tohutohu, Take, me te Maimoatanga

Ko te sarcoma pleomorphic korekore (UPS) tētahi momo mate pukupuku ngohengohe e taea te whanake i nga wahi katoa o to tinana, ahakoa ko te nuinga o te wā ka puta ki o ringa, waewae, rānei te pouaka. Ka whiwhi tēnei mate pukupuku i tōna ingoa nā te mea he rerekē rawa te ahua o ngā pūtau i raro i te microscope, ā, kāore e rite ki tetahi momo kiko noa.

E kiia ana ko te UPS he mate pukupuku onge, e pā ana ki te 1 i roto i te 100,000 o te iwi ia tau. Ahakoa te whakaaro nui o te whiwhi i tēnei whakatau, ko te mārama ki te mea kei te whakahaere koe ka taea te awhina i a koe kia rite ake, kia maia hoki ki tō haerenga maimoatanga e haere mai ana.

He aha te sarcoma pleomorphic korekore?

Ko te sarcoma pleomorphic korekore he mate pukupuku e whanake ana i roto i ō kiko ngohengohe penei i ngā uaua, ngā ngako, ngā oko toto, ngā kiko hono rānei. Ko te kupu "korekore" te tikanga kāore ngā pūtau mate pukupuku e rite ki tetahi momo pūtau noa, e uaua ai te whakatau.

Ko te "Pleomorphic" te whakaahuatanga o te ahua o ēnei pūtau mate pukupuku i roto i te maha o ngā āhua me ngā rāhi rerekē ina tirohia i raro i te microscope. Ko tēnei rerekētanga o te ahua tētahi o ngā āhuatanga matua e whakamahia ana e ngā tākuta hei tohu i tēnei momo sarcoma.

Ko te UPS te nuinga o te tipu hei kohinga pakari, kore mamae e taea te whānuitanga mai i te torutoru henimita ki te nui rawa. Ko te nuinga o te iwi ka kite tuatahi i te mea he kohinga e tipu haere ana i roto i ngā wiki, marama rānei.

Ko tēnei mate pukupuku te nuinga o te pā ki ngā pakeke i waenga i te 50 me te 70 tau te pakeke, ahakoa ka puta i tetahi tau.

He aha ngā tohu o te sarcoma pleomorphic korekore?

Ko te tohu tuatahi tino noa o te UPS he kohinga kore mamae, he kohinga rānei e taea te kite i raro i tō kiri. Ko tēnei kohinga te nuinga o te ahua pakari, pakeke rānei ki te pa atu, ā, ka tipu haere pea i te wā.

He tokomaha kaore e kite i te mamae i te tīmatanga, e arahi ana i etahi wā ki te whakaroa i te rapu awhina hauora. Ko ēnei ngā tohu ka kite koe:

• He kohinga pakari, e tipu haere ana, he kohinga rānei i tetahi wāhi o tō tinana
• Te pupuhi i te wāhi e pā ana
• Te mamae, te ngawari rānei, ina koa ka nui ake te tipu o te mate pukupuku
• Te iti o te nekehanga mena ka pā te mate pukupuku ki ngā uaua, ki ngā hononga rānei
• Te ngenge, te wiri rānei mena ka pēhi te mate pukupuku ki ngā io

Ka kite etahi i ētahi atu tohu motuhake kei te whakawhirinaki ki te wāhi e whanake ana te mate pukupuku. Mena ka tipu te UPS i tō waewae, i tō ringa rānei, ka kite pea koe i te ngoikore, te uaua rānei ki te neke i taua waewae, ringa rānei.

I roto i ngā take onge, ina whanake te UPS i roto i ngā kiko hohonu, i ngā kiko o roto rānei, ka kite pea koe i ētahi atu tohu whānui penei i te ngaro o te taumaha kaore i te whakamārama, te ngenge, te kirika rānei. Heoi, he iti rawa ēnei tohu, ā, ko te nuinga o te wā ka puta anake me te mate pukupuku tino whanake.

He aha ngā take o te sarcoma pleomorphic korekore?

Kāore i tino mārama te take tika o te sarcoma pleomorphic korekore, engari e whakapono ana ngā kairangahau ka whanake ina puta ngā huringa ira ki ngā pūtau noa i roto i ō kiko ngohengohe e arahi ana ki te tipu kore mana. Ko ēnei huringa te nuinga o te wā ka puta noa atu i te whakawhiwhia mai i ō mātua.

He maha ngā take e āhei ana ki te whanaketanga o te UPS, ahakoa te whai i ēnei take morearea kāore e tikanga ka whanake koe i te mate pukupuku:

• Te maimoatanga radiation o mua mō tētahi atu mate pukupuku
• Te whakaū ki ētahi kemika, poizon rānei
• Te mumura roa, te whara rānei ki ngā kiko ngohengohe
• Ētahi āhuatanga ira tūturu (onge rawa)
• Ngā huringa pūtau e pā ana ki te pakeke i te wā

Ko te maimoatanga radiation o mua tētahi o ngā take morearea tino whakapumautia. Mena i whiwhi koe i te maimoatanga radiation mō tētahi atu mate pukupuku i ngā tau kua pahure, he iti te pikinga o te morearea o te whanaketanga o te UPS i te wāhi i maimoatia i mua.

Heoi, he mea nui kia mōhio ko te nuinga o te iwi me te UPS kāore he take morearea mārama. Ka puta te mate pukupuku ki te koretake i roto i te iwi hauora, e āhei ana te whakaaro pouri ina ngana koe ki te mārama he aha i puta ai tēnei ki a koe.

Nōhea te kite i te tākuta mō te sarcoma pleomorphic korekore?

Me kite koe i tō tākuta mena ka kite koe i tetahi kohinga hou, he kohinga rānei e mau tonu ana mo te neke atu i ngā wiki torutoru, ina koa mena kei te tipu, kei te huri rānei. Ahakoa ko te nuinga o ngā kohinga he pai, he pai tonu te arotake i a rātou i te tīmatanga.

Whakahaere he whakatau tere mena ka kite koe i ēnei tohu whakatūpato:

• He kohinga nui atu i te 2 inihi (5 henimita) te whānuitanga
• Tetahi kohinga e tipu haere ana, kei te huri rānei te āhua
• He kohinga e ahua pakari ana, e mau ana rānei
• Te mamae, te ngenge, te ngoikore rānei i te wāhi e pā ana
• Tetahi kohinga e whakaroa ana i te nekehanga noa

Kaua e tatari mena kei te whakararu te kohinga i a koe, kei te pā rānei ki ō mahi o ia rā. Ko te kite wawe me te maimoatanga te nuinga o te arahi ki ngā hua pai ake me ngā sarcomas.

Mena he hītori o te maimoatanga radiation koe, kia tupato rawa ki ngā kohinga hou i ngā wāhi i maimoatia i mua. Ahakoa he iti tonu te morearea, ka hiahia tō tākuta ki te arotake i ngā kohinga hou katoa kia tino.

He aha ngā take morearea mō te sarcoma pleomorphic korekore?

Ko te mārama ki ngā take morearea ka taea te awhina i a koe kia mōhio ki ngā tohu whakatūpato, ahakoa te whai i ngā take morearea kāore e tikanga ka whanake koe i te UPS. Ko te nuinga o te iwi me tēnei mate pukupuku kāore he take morearea e taea te tohu.

Ko ngā take morearea matua kua tohua e ngā tākuta ko ēnei:

• Te pakeke i waenga i te 50-70 tau (ahakoa ka puta i tetahi tau)
• Te maimoatanga radiation o mua, te nuinga o te 10-20 tau i mua
• Ētahi āhuatanga ira tūturu penei i te mate Li-Fraumeni
• Te whakaū ki ētahi kemika i roto i ngā āhuatanga mahi
• Te lymphedema roa (te pupuhi roa)

Ko te maimoatanga radiation o mua te take morearea tino whakapumautia. Mena i whiwhi koe i te radiation mō te mate pukupuku u, te lymphoma, tētahi atu mate pukupuku rānei, he iti te pikinga o te morearea o te whanaketanga o te UPS i te wāhi i maimoatia i ngā tau maha i muri mai.

Ka taea hoki e ētahi āhuatanga ira tūturu te whakanui ake i te morearea, engari ko ēnei e iti iho i te 5% o ngā take UPS katoa. Ko te nuinga o te iwi me te UPS kāore he hītori whānau o te mate pukupuku, kāore hoki he whakapae ira e mohiotia ana.

He mea tika te kōrero ko ngā take oranga penei i te kai, te whakakori tinana, te whakakā rānei kāore e āhei te pānga nui ki te morearea UPS. Ka puta te mate pukupuku ma te koretake atu i te mea he take ka taea te karo.

He aha ngā raruraru pea o te sarcoma pleomorphic korekore?

Ahakoa ko te nuinga o te iwi me te UPS ka taea te maimoatanga pai, ko te mārama ki ngā raruraru pea ka awhina i a koe kia mōhio ki te mea hei titiro atu me te wā hei whakapiri atu ki tō rōpū hauora. Ko te take nui rawa atu me te UPS ko tōna kaha ki te horapa ki ētahi atu wāhi o tō tinana mena kaore i te maimoatia wawe.

Ko ngā raruraru tino nui ko ēnei:

• Te horapa (horapa) ki ngā pūkahukahu, ate, ētahi atu kiko rānei
• Te hokinga mai o te rohe i muri i te maimoatanga
• Te kino o ngā io mena ka pēhi te mate pukupuku ki ngā io nui
• Te ngaro o te mahi i roto i ngā uaua, i ngā hononga rānei e pā ana
• Ngā raruraru mai i te pokanga, ētahi atu maimoatanga rānei

He āhei te UPS ki te horapa i roto i te toto, ko ngā pūkahukahu te wāhi tino noa o te horapa. Koia te take ka tono pea tō tākuta i te whakaahua uma hei wāhanga o tō arotake tīmatanga me tō tiaki whai muri.

Ka taea te hokinga mai o te rohe, kei hea te mate pukupuku e hoki mai ana i te wāhi ano i muri i te maimoatanga, mena kei te toe ngā pūtau mate pukupuku iti i muri i te pokanga. Koia te take he mea nui te tango pokanga katoa me ngā taha mārama.

I roto i ngā take onge, ka taea e ngā mate pukupuku nui te whakaputa i ngā raruraru nui i mua i te maimoatanga. Ka āhei ēnei ki te pēhinga o ngā oko toto nui, ngā io, ngā kiko rānei, kei te whakawhirinaki ki te wāhi o te mate pukupuku.

Me pēhea te whakatau o te sarcoma pleomorphic korekore?

Ko te whakatau i te UPS e hiahia ana ki ētahi kaupae hei whakau i te momo mate pukupuku me te whakatau i te tawhiti o tōna horapa. Ka tīmata tō tākuta me te whakamātau tinana, ka tono i ngā whakamātau motuhake hei whiwhi i te pikitia katoa.

Ko te tukanga whakatau te nuinga o te wā e whai ake nei:

1. Te whakamātau tinana me te hītori hauora
2. Ngā rangahau whakaahua (MRI, CT scan, ultrasound rānei)
3. Te biopsy hei tirotiro i te kiko i raro i te microscope
4. Ngā whakamātau atu hei tirotiro i te horapa (te whakatūnga)
5. Te whakamātau ira o te mate pukupuku (i ētahi wā)

Ko te biopsy te kaupae tino nui nā te mea koia anake te huarahi hei whakatau tika i te UPS. Ka tangohia e tō tākuta he wahi iti o te mate pukupuku mā te ngira, mā te tapahi pokanga iti rānei.

Ka awhina ngā rangahau whakaahua ki te whakatau i te rahi me te wāhi tika o te mate pukupuku, me tōna hononga ki ngā hanganga tata penei i ngā oko toto, ngā io, ngā wheua rānei. He mea nui tēnei mōhiohio mō te whakarite i tō maimoatanga.

Ka awhina ngā whakamātau whakatūnga, ka āhei pea te X-ray uma, ngā CT scan rānei, ki te whakatau mena kua horapa te mate pukupuku ki ētahi atu wāhi o tō tinana. He nui te pānga o tēnei mōhiohio ki ō kōwhiringa maimoatanga me te whakatau.

He aha te maimoatanga mō te sarcoma pleomorphic korekore?

Ko te maimoatanga mō te UPS te nuinga o te wā e whai ake nei i te huinga o ngā huarahi e rite ana ki tō āhuatanga motuhake. Ko te pokanga te maimoatanga matua, te nuinga o te wā ka whakakotahitia ki te maimoatanga radiation, te chemotherapy rānei hei hoatu i a koe i te tupono pai rawa atu o te rongoā.

Ka āhei tō mahere maimoatanga ki te whai ake nei:

• Te pokanga hei tango i te mate pukupuku me ngā taha mārama
• Te maimoatanga radiation i mua, i muri rānei i te pokanga
• Te chemotherapy, ina koa mō ngā mate pukupuku nui ake, teitei ake rānei
• Te maimoatanga e whai ana, te immunotherapy rānei (i ētahi wā)
• Te whakaora me te tiaki tautoko

Ko te whāinga o te pokanga ko te tango i te mate pukupuku katoa me te taha o te kiko hauora i te taha. I etahi wa ka hiahia tenei ki te tango i ngā uaua e pā ana, ā, i roto i ngā take onge, ka hiahiatia pea te tapahi, ahakoa he taea te pokanga whakaora waewae i roto i te nuinga o ngā take.

Ka whakamahi te maimoatanga radiation i ngā hiwi kaha ki te whakamate i ngā pūtau mate pukupuku, ā, ko te nuinga o te wā ka hoatu i mua i te pokanga hei whakaiti i te mate pukupuku, i muri rānei i te pokanga hei whakangaro i ngā pūtau mate pukupuku e toe ana. Ko te wā e whakawhirinaki ana ki tō āhuatanga motuhake.

Ka tūtohutia pea te chemotherapy mena he nui tō mate pukupuku, heitei teitei rānei, mena he awangawanga mō te horapa iti. Ahakoa kāore te UPS e whakautu nui ki te chemotherapy, ka taea te awhina i roto i ētahi āhuatanga.

Ka mahi tahi tō rōpū maimoatanga hei hanga i te mahere e hoatu ana i a koe i te tupono pai rawa atu o te rongoā me te tiaki i te nui o te mahi i te wāhi e pā ana.

Me pēhea te whakahaere i te sarcoma pleomorphic korekore i te kāinga?

Ko te whakahaere i te UPS i te kāinga e whai ake nei i te tiaki i a koe i te wā o te maimoatanga me te whakaora me te pupuri i te mataara mō ētahi huringa e hiahia ana ki te tiaki hauora. He wāhanga nui ō kōwhiringa me tō oranga pai ki tō mahere maimoatanga katoa.

Ko ēnei ngā huarahi hei tautoko i tō hauora i te wā o te maimoatanga:

• Whai i tō kaupapa rongoā tika pera i te tohu
• Pupuri i ngā wāhi pokanga kia ma, kia maroke hoki pera i te tohu
• Pupuri i te kai pai hei tautoko i te whakaora
• Noho mahi pera i te tūtohu a tō tākuta
• Aroturuki mō ngā tohu o te mate, ngā raruraru rānei

Tātai ki ētahi huringa i tō wāhi pokanga, penei i te whero nui ake, te pupuhi, te mahana, te rere rānei. Ka taea ēnei hei tohu o te mate e hiahia ana ki te tiaki hauora wawe.

Ko te whakakori ngawari me te rongoā tinana, pera i te tūtohu a tō rōpū hauora, ka taea te awhina i te pupuri i te kaha me te ngawari i te wā o te whakaora. Kaua e pēhi i a koe, engari ko te noho mahi noa te nuinga o te awhina i te whakaora.

Ko te whakahaere i ngā pānga o te chemotherapy, radiation rānei ka āhei pea te kai i ngā kai iti, te noho makuku, te moe nui hoki ina ngenge koe.

Me pēhea te whakarite mō tō whakatau tākuta?

Ko te whakarite mō tō whakatau ka awhina i te whakarite kia whiwhi koe i te nuinga o tō wā me tō rōpū hauora. Ko te whai i ō patai me ō awangawanga kua whakaritea ka taea te awhina i te whakaiti i te manukanuka me te whakarite kia kaua e warewaretia tetahi mea nui.

I mua i tō whakatau, kohia tēnei mōhiohio:

• He rārangi o ō rongoā me ō taapiri katoa
• Tō hītori hauora katoa, tae atu ki ngā mate pukupuku o mua
• Te hītori whānau o te mate pukupuku, ngā āhuatanga ira rānei
• Ngā rangahau whakaahua, ngā hua whakamātau rānei mai i ētahi atu tākuta
• Ngā mōhiohio inihua me ngā puka tohutoro mena e hiahiatia ana

Tuhia ō patai i mua i te wā kia kaua e wareware i a rātou i te whakatau. Ko ngā patai noa pea ka whai ake nei i te uiui mō ngā kōwhiringa maimoatanga, ngā pānga pea, te whakatau, me te āhua o te maimoatanga ki tō oranga o ia rā.

Whakaarohia te kawe mai i tētahi hoa whakawhirinaki, mema whānau rānei hei awhina i a koe ki te mahara ki ngā mōhiohio i kōrerotia i te whakatau. Ka taea hoki te awhina o te tautoko ngākau ina whakahaerehia ana tētahi whakatau mate pukupuku.

Kaua e whakaroa ki te tono ki tō tākuta kia whakamārama i tetahi mea kaore koe e mārama. He mea nui kia pai koe ki tō mahere maimoatanga me te mōhio ki te mea e tatari ana koe.

He aha te mea nui mō te sarcoma pleomorphic korekore?

Ko te sarcoma pleomorphic korekore he mate pukupuku onge engari ka taea te maimoatanga e hiahia ana ki te tiaki hauora wawe me te maimoatanga whānui. Ahakoa te whakaaro nui o te whiwhi i tēnei whakatau, ko te nuinga o te iwi me te UPS ka taea te maimoatanga pai, ina koa ka kite wawetia te mate pukupuku, kāore hoki i te horapa ki ētahi atu wāhi o te tinana.

Ko te mea nui rawa atu hei mahara ko te kite wawe me te maimoatanga e te rōpū sarcoma wheako e whakanui ake ana i ngā hua. Mena ka kite koe i tetahi kohinga e mau tonu ana, e tipu haere ana rānei, kaua e tatari kia arotakehia.

He motuhake te āhuatanga o ia tangata, ā, ka whakaritea tō mahere maimoatanga motuhake ki ō hiahia. Ko te mahi tata atu ki tō rōpū hauora, te uiui i ngā patai, te noho mōhio hoki mō tō āhuatanga ka awhina i a koe kia nui ake te mana o tō haerenga.

Ahakoa ka āhei te ara i mua, kia mahara ko ngā whakapainga i roto i te maimoatanga sarcoma e haere tonu ana te whakapai ake i ngā hua mō te iwi me te UPS. Kei reira tō rōpū hauora hei tautoko i a koe i ia kaupae o te ara.

Ngā patai e ui ana te iwi mō te sarcoma pleomorphic korekore

P.1 He mate mate tonu te sarcoma pleomorphic korekore?

Kāore, kāore te UPS i te mate mate tonu. Ka taea te rongoā i te nuinga o te iwi me te UPS, ina koa ka kite wawetia te mate pukupuku, kāore hoki i te horapa ki ētahi atu wāhi o te tinana. Ko te whakatau e whakawhirinaki ana ki ngā take penei i te rahi me te wāhi o te mate pukupuku, mena kua horapa, me te āhua o tōna whakautu ki te maimoatanga. Me te maimoatanga tika mai i te rōpū sarcoma wheako, ka haere tonu te nuinga o ngā turoro ki te noho oranga noa, hauora.

P.2 Ka taea te hoki mai o te sarcoma pleomorphic korekore i muri i te maimoatanga?

Ae, ka taea te hokinga mai o te UPS i muri i te maimoatanga, ahakoa kāore tēnei e puta ki te katoa. Ko te hokinga mai o te rohe i te wāhi ano e puta ana i te 10-20% o ngā take, ahakoa he iti te hokinga mai o te tawhiti (horapa). Koia te take he mea nui ngā whakatau whai muri me ngā rangahau whakaahua. Ko te kite wawe i tetahi hokinga mai ka taea te maimoatanga wawe, ka taea tonu te tino whai hua.

P.3 Kia tere te tipu o te sarcoma pleomorphic korekore?

Ko te UPS te nuinga o te wā e tipu ana i te wā roa i roto i ngā wiki ki ngā marama, ahakoa ka rerekē te tere o te tipu mai i te tangata ki te tangata. Ka taea e ētahi mate pukupuku te tipu tere ake, ka whanake atu ētahi i te wā roa ake. Ko te āhua o te mate pukupuku, e whakaatu ana i te āhua o te mate pukupuku i raro i te microscope, ka taea te hoatu ki ngā tākuta he whakaaro o te tere o tōna tipu me te horapa.

P.4 Me hiahia ahau ki te tapahi mena he sarcoma pleomorphic korekore ahau?

He onge te hiahia ki te tapahi mō te UPS. I roto i te nuinga o ngā take, ka taea e te pokanga whakaora waewae te tango i te mate pukupuku me te tiaki i te ringa, te waewae rānei e pā ana. Ko ngā hangarau pokanga hou, ka whakakotahitia ki te maimoatanga radiation, ka taea e ngā tākuta te whakatutuki i te mana mate pukupuku pai me te pupuri i te mahi. Ko te tapahi ka whakaarohia anake i roto i ngā take onge e tino hiahiatia ana te tango katoa i te mate pukupuku.

P.5 He whakawhiwhia mai te sarcoma pleomorphic korekore?

He onge te whakawhiwhia mai o te UPS. He iti iho i te 5% o ngā take e hono ana ki ngā āhuatanga ira tūturu penei i te mate Li-Fraumeni. Ko te nuinga o te iwi me te UPS kāore he hītori whānau o te mate, kāore hoki he whakapae ira. Ko te mate pukupuku te nuinga o te wā e whanake ana na ngā huringa ira koretake e puta ana i te wā o te oranga o te tangata i te mea kāore i te whakawhiwhia mai i ngā mātua.