Created at:1/16/2025
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Ko te vasculitis te mumura o ō ngā oko toto e pā ana ki ngā ātiretī, ngā uen, me ngā kapirī i roto i tō tinana. Ka mumura ēnei ara nui, ka whakaiti, ka ngoikore rānei, ā, ka mutu rawa te kati, ka whakaroa te rere o te toto ki ō whatunga me ō kiko.
Kāore tēnei mate i te kotahi noa te mate, engari he rōpū o ngā mate e hono ana e taea te rere mai i ngā pupuhi kiri ngawari ki ngā raruraru nui o ngā whatunga. Ahakoa ka rongo te kupu "vasculitis" he wehi, ko te mārama ki te aha te mea kei roto i tō tinana ka āwhina i a koe ki te mahi tahi pai me tō rōpū hauora ki te whakahaere i ngā tohu me te tiaki i tō hauora roa.
He rereke ngā tohu o te vasculitis, kei te whakawhirinaki ki tehea ngā oko toto e pā ana, me te kaha o te mumura. He maha ngā tāngata e kite tuatahi ana i ngā tohu whānui penei i te ngenge, te kirika, te ngaro o te taumaha kaore he take e rite ana ki te mate huka.
Na te mea ka taea e te vasculitis te pā ki ngā oko toto i nga wahi katoa o tō tinana, ka rongo pea koe i ngā whakakotahitanga rerekē o ngā tohu. Ko ēnei ngā tohu tino noa ka whakaatu pea tō tinana:
Ko ngā tohu motuhake ake kei te whakawhirinaki ki tehea ngā whatunga e pā ana. Ki te whakauru te vasculitis ki ō whatukuhu, ka kite pea koe i ngā huringa i te mimi, te pupuhi rānei o ō waewae. Ka pā ki ō ngā manawa, ka puta pea ngā raruraru o te manawa, te mare rānei e kore e mutu.
Ko ētahi tāngata e rongo ana i ngā tohu onge engari nui e hiahia ana ki te tiaki wawe. Ko ēnei ngā huringa o te tirohanga ohorere, te mamae o te kopu nui, te mamae o te uma, te tohu rānei o te pēhanga penei i te heke o te mata, te uaua rānei ki te kōrero. Ahakoa he onge ēnei raruraru, ka whakakitea te take he mea nui te mahi tata me tō tākuta.
He maha ngā momo vasculitis, ia momo e pā ana ki ngā rahi motuhake o ngā oko toto i ngā huarahi ā-āhua. Ka whakarōpū ngā tākuta i ēnei momo i runga i te mea kei roto i ngā oko toto nui, waenga, iti rānei.
Ko te vasculitis oko toto nui e pā ana ki ngā ātiretī nui o tō tinana. Ko te arteritis pūtau nui e whakauru ana ki ngā ātiretī i roto i tō mahunga me tō kaki, ka tino mamae pea te mahunga me te kauae i te ngau. Ko te arteritis Takayasu e pā ana ki ngā wāhine taitamariki, ā, kei roto i te aorta me ona peka matua, ka ngoikore pea te ringa, te rerekētanga rānei o te toto i waenga i ngā ringa.
Ko te vasculitis oko toto waenga e whakauru ana i ngā āhuatanga penei i te polyarteritis nodosa, e taea te pā ki ngā whatunga maha tae atu ki ngā whatukuhu, ngā io, me te kiri. Ko te mate Kawasaki, ahakoa he tino noa i ngā tamariki, e pā ana ki ngā ātiretī o te rahi waenga, ā, ka whakauru pea i te ngakau.
Ko te vasculitis oko toto iti e whakauru ana i ngā āhuatanga maha e pā ana ki ngā oko toto iti i roto i tō tinana. Ko te granulomatosis me te polyangiitis e whakauru ana ki ngā manawa, ngā whatukuhu, me ngā sinuses. Ko te microscopic polyangiitis e pā ana ki ngā whatukuhu me ngā manawa, ko te eosinophilic granulomatosis me te polyangiitis e whakauru ana ki ngā tohu rite ki te mate huango.
Ko ētahi momo e whakaarohia ana he onge engari he mea nui ki te mohio. Ko te mate Behçet e puta ai ngā whewhe waha me ngā whewhe ira tāne me te mumura o te kanohi. Ko te vasculitis ngawari e puta ana hei pupuhi kiri e whakaohotia ana e ngā rongoā, ngā mate rānei.
Ko te take tika o te nuinga o ngā momo vasculitis kāore i te marama, engari e whakapono ana ngā tākuta ka puta i te whakaeke o tō pūnaha ārai i ō ake oko toto. Ko tēnei mahi ārai whaiaro te take o te mumura e tohu ana i ngā momo vasculitis katoa.
He maha ngā take ka whakaoho i tēnei whakapohehe o te pūnaha ārai. Ko ngā mate e mahi ana hei whakamārama tuatahi, me ngā huaketo penei i te hepatitis B, C rānei, ngā pūkohukohu, ngā mate rānei e taea te whakarewa i te tukanga mumura. Ko te ngana a tō tinana ki te whawhai ki ēnei mate ka taea te whakaeke i ngā pakitara o te oko toto.
Ko ngā rongoā ka taea te whakaoho i te vasculitis i roto i ngā tāngata ngawari. Ko ētahi rongoā, ngā kaiwhakaheke toto, ngā rongoā rānei ka taea te whakaoho i tō pūnaha ārai ki te whakaeke i ngā oko toto. Ko tēnei momo e pai ake ana i te mutu o te rongoā whakaoho.
He mahi ngā take ira i roto i te ngoikoretanga o ētahi tāngata ki te vasculitis. Ahakoa kāore koe e whiwhi vasculitis tika, ko ētahi tohu ira e tino pā ana ki ētahi tāngata ki te whanake i ngā āhuatanga whaiaro i te whakaatu ki ngā whakaoho taiao.
I roto i te maha o ngā take, ka puta te vasculitis mai i te mahi hono o te ngoikoretanga ira me ngā take taiao. Ko te whakakotahitanga o ngā whakaoho maha i te wa roa, ka uaua te kimi i tetahi take motuhake mō te āhuatanga o te tangata.
Me whakapiri atu koe ki tō tākuta ki te rongo koe i ngā tohu tonu e kore e pai ake me te okioki, ngā maimoatanga rānei o te toa. Ahakoa he maha ngā tohu vasculitis e rite ana ki ngā mate noa i te timatanga, ko te roa, te whakakotahitanga rānei o rātou me whakamāramahia te aromatawai hauora.
Tātaihia ngā tohu whakatūpato e whakaatu ana i tetahi mea nui atu i te mate huaketo noa. Ko te kirika kaore he take e roa atu ana i ngā rā torutoru, te ngenge tonu e āwangawanga ana i ngā mahi o ia rā, ngā pupuhi kiri hou e kore e whakautu ki te tiaki taketake e tika ana te tiaki hauora.
Rapua te tiaki hauora wawe ki te whanake koe i ngā tohu ohorere, nui. Ko ngā huringa o te tirohanga, ngā mamae o te mahunga nui e kore e rite ki ētahi atu i mua, te uaua ki te manawa, te mamae o te uma, te tohu rānei o te pēhanga e hiahia ana ki te aromatawai ohorere. Ka taea e ēnei tohu te tohu i te vasculitis e pā ana ki ngā whatunga nui.
Kaua e whakaroa te rapu awhina ki te kite koe i ngā tohu e pā ana ki ngā pūnaha tinana maha i te wa kotahi. Ko te vasculitis e tino puta ai ngā raruraru kaore e hono ana i ngā wahi rerekē o tō tinana, ā, ko te mohio wawe ki ēnei tauira ka ārahi ki te maimoatanga pai ake.
He mahi nui te pakeke i roto i te morearea vasculitis, ahakoa he rerekē ngā momo e pā ana ki ngā tāngata i ngā wā rerekē o te ora. Ko te arteritis pūtau nui e tino pā ana ki ngā tāngata neke atu i te 50, ko te mate Kawasaki e tino puta ana i ngā tamariki iti i raro i te 5 tau.
Ka taea e tō ira tangata te awe i te morearea vasculitis i ētahi momo. Ko te arteritis Takayasu e pā ana ki ngā wāhine neke atu i te iwa te maha atu i ngā tāne, i te nuinga i o rātou tau tekau mā rima me ngā rua tekau. Heoi, ko ētahi atu momo penei i te polyarteritis nodosa e pā ana ki ngā tāne me ngā wāhine rite tonu.
Ko te whai i ētahi āhuatanga whaiaro ka piki pea tō morearea vasculitis. Ko ngā tāngata e mate rewiti ana, lupus, mate puku mumura rānei he nui ake te tupono ki te whanake i te vasculitis tuarua. Ko ēnei āhuatanga e whakaatu ana i ngā tauira pūnaha ārai rite.
He whakauru te papamuri ira ki te morearea i ngā huarahi uaua. Ko ētahi rōpū iwi e whakaatu ana i ngā reiti teitei o ngā momo vasculitis motuhake, ā, ko te whai i ngā mema whānau e mate ana i ngā mate whaiaro ka piki pea tō morearea, ahakoa he onge te rere o te vasculitis tika i roto i ngā whānau.
Ka taea e ngā take taiao me ngā mate te mahi hei whakaoho i roto i ngā tāngata ngawari. Ko ngā mate hepatitis B, C roa, ētahi mate pūkohukohu, te whakaatu rānei ki ētahi rongoā ka taea te whakarewa i te vasculitis i roto i ngā tāngata e ngoikore ana te ira.
Ko ngā raruraru vasculitis kei te whakawhirinaki ki tehea ngā oko toto e pā ana, me te kaha o te mumura e pakaru ana i a rātou. Ka whakaroa te rere o te toto ki ngā whatunga, kaore pea ēnei whatunga e mahi tika, ka pakaru rānei.
Ko te mārama ki ngā raruraru pea ka āwhina i a koe ki te mohio ki te wa e hiahia ana ngā tohu ki te tiaki wawe. Ko ēnei ngā raruraru tino awangawanga e taea te whanake:
Ko ētahi raruraru e whanake ana i te wa roa i roto i ngā marama, ngā tau rānei, ko ētahi atu ka puta ohorere. Ko te whakauru whatukuhu e tino haere tonu ana i te ngāwari, koia te take he mea nui te arotake tonu mā ngā whakamātautau toto me te mimi i te wa o te maimoatanga.
Ko ngā raruraru onge engari nui ka taea te pā ki tetahi pūnaha whatunga. Ka taea e ēnei te whakauru i te toto o te whekau, te pakaru o te waahanga ngakau, ngā raruraru neurological nui rānei. Ahakoa he onge ēnei hua me te maimoatanga tika, ka whakakitea te hiranga o te mahi tata me tō rōpū hauora.
Ko te rongo pai ko te maha o ngā raruraru ka taea te aukati, te whakaiti rānei me te tautuhi wawe me te maimoatanga tika. Ko te arotake tonu ka taea ai e tō tākuta te kite i ngā raruraru i mua i te nui, te whakarite rānei i tō maimoatanga.
Ko te tautuhi i te vasculitis e hiahia ana ki te mahi whakahirahira na te mea he maha ngā tohu e rite ana ki ētahi atu āhuatanga. Ka tīmata tō tākuta me te kōrero taipitopito mō ō tohu, te hītori hauora, me te whakamātautau tinana ki te titiro ki ngā tauira e tohu ana i te vasculitis.
Ko ngā whakamātautau toto e homai ana ngā korero nui mō te mumura i roto i tō tinana. Ko ngā whakamātautau penei i te tere o te noho o te erythrocyte (ESR) me te pūtau C-reactive (CRP) e ine ana i ngā taumata mumura whānui, ko ngā whakamātautau antibody motuhake ka taea te tautuhi i ngā momo vasculitis motuhake.
Ko ngā rangahau whakaahua e āwhina ana ki te kite i ō oko toto me te kite i ngā wāhi mumura, te pakaru rānei. Ko ngā tirohanga CT, MRI, te angiography motuhake rānei ka taea te whakaatu i te whakaiti o te oko, ngā aukatinga, ngā rerekētanga rānei e tohu ana i te vasculitis.
Ko te wā e hiahia ana pea tō tākuta ki te biopsy, kei reira te tauira kiko iti e tirohia ana i raro i te microscope. Ka taea e tēnei te whakauru i te kiri, te whatukuhu, ngā whatunga rānei e pā ana, ā, ka taea te homai i te mārama mo te mumura o te oko toto.
Ko te tukanga tautuhi ka roa na te mea e hiahia ana tō tākuta ki te whakakore i ētahi atu āhuatanga me te tautuhi i te momo vasculitis motuhake kei a koe. Ko tēnei mārama e whakarite ana ka whiwhi koe i te maimoatanga tika mō tō āhuatanga motuhake.
Ko te maimoatanga vasculitis e whai ana ki te whakaiti i te mumura, te aukati i te pakaru o te whatunga, te āwhina rānei i a koe ki te pupuri i te kounga ora pai rawa atu. Ko te nuinga o ngā mahere maimoatanga e whakauru ana i ngā rongoā e whakahāwea ana i tō pūnaha ārai nui.
Ko ngā corticosteroids penei i te prednisone te raina tuatahi o te maimoatanga na te mea ka whakaiti wawe i te mumura. Ka tīmata pea tō tākuta me ngā rāpoi teitei ki te whakahaere i te mumura mahi, ka whakaiti haere i te nui i te pai ake o ō tohu.
Ka taea te tāpiri i ngā rongoā immunosuppressive ki te āwhina i te whakahaere i te mumura i te wa e taea ai e tō tākuta te whakaiti i ngā rāpoi steroid. Ka taea e ēnei te whakauru i te methotrexate, azathioprine, ngā rongoā hou rānei e whakaeke ana i ngā wāhanga motuhake o tō pūnaha ārai.
Ka whakaritea tō mahere maimoatanga ki tō momo vasculitis motuhake me te kaha o te pā ki ō whatunga. Ko ētahi tāngata e hiahia ana ki te maimoatanga nui i te timatanga, ko ētahi atu ka taea te whakahaere pai me ngā huarahi ngawari.
He mea nui te arotake tonu i te wa o te maimoatanga ki te tirotiro me pēhea te mahi o ngā rongoā me te titiro ki ngā pānga taha. Ka whakaritea e tō tākuta tō maimoatanga i runga i tō whakautu me ētahi atu huringa i tō āhuatanga i te wa roa.
Ko te whakahaere i te vasculitis i te kāinga e whakauru ana i te tautoko i tō hauora whānui i te wa e mahi ana me tō maimoatanga hauora. Ko te tiaki pai mō te tinana ka āwhina i a koe ki te pai ake, ā, ka pai ake pea te mahi o tō maimoatanga.
Tūpatohia te okioki me te whakahaere i te ahotea na te mea ko te ahotea tinana me te ngakau ka taea te whakaoho i ngā mura. Ko te whiwhi moe tika, te mahi i ngā tikanga whakahāwea, te whakarite i ō mahi ka āwhina i tō tinana ki te whakahaere pai i te maimoatanga.
Pupurihia he kai hauora e whai hua ana i ngā kai e tautoko ana i tō pūnaha ārai me te hauora wheua. He mea nui tēnei, ina koa ki te kai koe i ngā corticosteroids, e taea te pā ki te mātotorutanga wheua me ngā taumata huka toto.
Noho mahi i roto i ō rohe mā te whakakori ngawari penei i te hikoi, te kauhoe rānei. Ko te nekehanga tonu e āwhina ana ki te pupuri i te kaha o ngā uaua, te hauora wheua, te ngakau, engari whakarongo ki tō tinana, okioki hoki ina hiahiatia.
Tātaihia ō tohu i roto i te pukapuka, te taupānga waea rānei. Ko ēnei korero e āwhina ana i tō tākuta ki te mārama me pēhea te mahi o tō maimoatanga me te wa e hiahiatia ana ngā whakarerekētanga.
Ko te whakarite mō tō hui vasculitis e āwhina ana ki te whakarite ka whiwhi koe i te pai rawa atu i tō wā me tō rōpū hauora. Haere mai kia rite ki te kōrero taipitopito mō ō tohu me te ui i ngā pātai nui mō tō tiaki.
Tuhia ō tohu katoa, tae atu ki te wa i tīmata ai rātou, te maha o te puta, me te aha e pai ake ai, te kino rānei. Whakauruhia ngā tohu kaore e hono ana na te mea ka taea e te vasculitis te pā ki ngā pūnaha tinana maha i ngā huarahi kaore e tūmanakohia.
Maua mai he rārangi katoa o ngā rongoā, ngā taapiri, me ngā huaora katoa e inu ana koe. Whakauruhia ngā taonga o te toa me ngā taapiri otaota, na te mea ka taea e ēnei te mahi tahi i ngā maimoatanga vasculitis.
Whakaritea ngā pātai mō tō momo vasculitis motuhake, ngā whiringa maimoatanga, ngā pānga taha pea, me te aha e tūmanakohia ana i mua. Kaua e whakaroa te ui mō tetahi mea e awangawanga ana koe, te kore rānei e marama.
Whakaarohia te mau mai i tetahi mema whānau whakawhirinaki, hoa rānei ki ngā hui nui. Ka taea e rātou te āwhina i a koe ki te mahara ki ngā korero i kōrerotia, te homai rānei i te tautoko ngakau i te mea ka rongo pea he nui ngā kōrero.
Ko te vasculitis he āhuatanga e taea te whakahaere i te wa e tautuhia ana, e maimoatia ana, ahakoa e hiahia ana ki te tiaki hauora tonu. Ahakoa ka rongo pea te tautuhi he nui i te timatanga, he maha ngā tāngata e mate ana i te vasculitis e ora ana i ngā oranga katoa, mahi me te maimoatanga tika.
Ko te tautuhi wawe me te maimoatanga e tino pai ake ai ngā hua, ā, e āwhina ana ki te aukati i ngā raruraru nui. Ko te mahi tata me tō rōpū hauora me te whai i tō mahere maimoatanga e homai ana te tupono pai rawa atu ki te whakahaere i te mumura me te tiaki i ō whatunga.
Mahara ko te vasculitis e pā ana ki te katoa i ngā huarahi rerekē, na reira pea kāore tō wheako e rite ki te mea e whakaatuhia ana e ētahi atu. Aro atu ki ō ake tohu me te whakautu ki te maimoatanga kaua ki te whakataurite i a koe ki ētahi atu e mate ana i te āhuatanga kotahi.
Noho tumanako, whakauru hoki ki tō tiaki. Ko te mārama hauora me ngā whiringa maimoatanga mō te vasculitis e haere tonu ana te pai ake, e homai ana ngā tirohanga pai ake mō ngā tāngata i tautuhia hou me ēnei āhuatanga.
Kāo, ehara te vasculitis i te mate pāhoko, kāore hoki e taea te horapa mai i te tangata ki te tangata. He āhuatanga whaiaro kei reira tō ake pūnaha ārai e whakaeke ana i ō oko toto, ehara i te mate e taea te tuku ki ētahi atu.
Ahakoa kāore he rongoā pumau mō te nuinga o ngā momo vasculitis, ka taea te whakahaere pai te āhuatanga me te maimoatanga. He maha ngā tāngata e whiwhi ana i te whakaora roa, ko te tikanga ka ngaro ō rātou tohu, ka kore te mumura e kitea, ahakoa ka hiahia pea rātou ki te arotake tonu me te maimoatanga.
Kei te whakawhirinaki tēnei ki tō momo vasculitis motuhake me te whakautu ki te maimoatanga. Ko ētahi tāngata ka taea te mutu i ngā rongoā ka noho tonu i te whakaora, ko ētahi atu e hiahia ana ki te maimoatanga roa ki te aukati i ngā mura. Ka mahi tahi tō tākuta me koe ki te kimi i te maimoatanga iti e pupuri ana i tō āhuatanga.
He maha ngā tāngata e mate ana i te vasculitis e taea te whānau tamariki hauora, engari e hiahia ana tēnei ki te whakarite me te arotake me tō rheumatologist me tō obstetrician. Ko ētahi rongoā vasculitis e hiahia ana ki te whakarerekē, te whakarereke rānei i mua i te whānautanga, na reira kōrerohia te whakarite whānau me tō rōpū hauora i mua.
Ko te auau o ngā whai muri e rerekē ana i runga i te kaha o tō āhuatanga me te whakautu ki te maimoatanga. I te timatanga, ka kite pea koe i tō tākuta i ia wiki, marama rānei ki te arotake i te whai hua o te maimoatanga me ngā pānga taha. I te wa e pumau ana tō āhuatanga, ka iti pea ngā hui, engari e tino haere tonu ana i ia 3-6 marama mō te arotake tonu.