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Macroglobulinemia Waldenström

Tirohanga whānui

Ko te Waldenstrom macroglobulinemia (mak-roe-glob-u-lih-NEE-me-uh) he momo mate pukupuku e tīmata ana i ngā pū toto ma. Ka whakaarohia te Waldenstrom macroglobulinemia he momo lymphoma kore-Hodgkin. I etahi wā ka kiia ko te lymphoma lymphoplasmacytic.

I te Waldenstrom macroglobulinemia, ka puta etahi huringa ki ētahi pū toto ma, ka huri ai rātou hei pū mate pukupuku. Ka taea e ngā pū mate pukupuku te hanga i roto i te mea pūha i roto i ngā wheua, te wāhi e hangaia ai ngā pū toto. Ko te ingoa o tēnei mea ko te wheua wheua. Ka pehia e ngā pū mate pukupuku ngā pū toto ora i waho o te wheua wheua. Ka taea hoki e ngā pū mate pukupuku te hanga i ētahi atu wāhanga o te tinana, pēnei i ngā kōpū lymph me te kōpū kōpū.

Ka hangaia e ngā pū mate pukupuku tētahi pūmua ka taea te hanga i roto i te toto. Ko te nui rawa o te pūmua ka taea te whakaiti i te rere toto i roto i te tinana, ā, ka puta mai ētahi atu raruraru.

Ngā tohu

Ko te tipu o te macroglobulinemia a Waldenstrom he iti te tere. Ka taea pea te kore e puta mai he tohu mo nga tau. Ki te puta mai, ko nga tohu o te macroglobulinemia a Waldenstrom ka uru atu ki enei: Te ngenge. Te kirika. Te ngaro o te taumaha. Te wera i te po. Te maminga o nga ringa, o nga waewae ranei. Te pupuhi o nga whekau lymph. Te mamae, te ki tonu ranei i raro i nga ihu i to taha maui, ka puta pea tenei na te nui haere o te kiko ate. Te ngawari ki te whara. Te toto i te ihu, i nga kanohi ranei. Te mamae o te upoko. Te poto o te manawa. Te huringa o te tirohanga. Te pohehe. Me whakarite he hui ki to kaiwhakarato tiaki matua mena kei a koe etahi tohu haere tonu e awangawanga ana koe.

Āhea te kite i te tākuta

Whakatau rā hui me tō kaiwhakarato rongoā matua ki te pēhea nei ngā tohu e awangawanga ana koe. Ohauru kore utu ka whiwhi koe i te aratohu hohonu ki te whakahaere i te mate pukupuku, me ngā korero whai hua e pā ana ki te whiwhi i tētahi atu whakaaro. Ka taea e koe te whakakore i tō ohaurunga i tetahi wā. Ka tae mai tō aratohu hohonu mō te whakahaere i te mate pukupuku ki tō pouakaroto i roto i ngā wā poto. Ka

Ngā take

Ka puta te mate pukupuku ina puta he huringa ki te DNA o ngā pūtau. Kei roto i te DNA o te pūtau ngā tohutohu e kōrero ana ki te pūtau me aha. Ka kī ngā huringa ki ngā pūtau kia tere te tupu. Ka mau tonu te ora o ngā pūtau ahakoa ka mate ngā pūtau hauora hei wāhanga o tō rātou oranga noa.

I te Waldenstrom macroglobulinemia, ka puta ngā huringa ki ngā pūtau toto ma. Ka huri ngā huringa i ētahi o ngā pūtau toto ma hei pūtau mate pukupuku. Kāore i te mārama he aha te take o ngā huringa.

Ka taea e ngā pūtau mate pukupuku te hanga i roto i te mea ngongo kei roto i ngā wheua kei reira te hanga o ngā pūtau toto. Ko te ingoa o tēnei mea ko te wheua wheua. Ka whakakī ngā pūtau mate pukupuku i ngā pūtau toto hauora i waho o te wheua wheua. Ka taea hoki e ngā pūtau mate pukupuku te hanga i roto i ngā wheua lymph me te kōpū.

Ka hanga e ngā pūtau Waldenstrom macroglobulinemia tētahi pūmua kaore e taea e te tinana te whakamahi. Ko te pūmua ko te immunoglobulin M, e kiia ana hoki ko IgM. Ka taea e te IgM te hanga i roto i te toto. Ka taea e tēnei te whakaiti i te rere o te toto i roto i te tinana me te whakaoho i ētahi atu raruraru.

Ngā āhuatanga tūpono

Ko ngā take ka piki ake ai te tūponotanga o te Waldenstrom macroglobulinemia ko ēnei:

  • Te pakeketanga. Ka taea te puta o te Waldenstrom macroglobulinemia i tetahi tau, engari ko te nuinga o te wā ka kitea i roto i ngā tāngata pakeke 70 tau me te pakeke ake.
  • Ko te tane. He nui ake te tūponotanga o ngā tāne ki te Waldenstrom macroglobulinemia.
  • Ko te Pākehā. He nui ake te tūponotanga o ngā Pākehā ki te whanake i te mate, ki te whakataurite ki ngā iwi o ētahi atu momo.
  • Te whānau me te hītori o te lymphoma. Ko te whai whānau e pangia ana e te Waldenstrom macroglobulinemia, tetahi atu momo rānei o te lymphoma B-cell, ka piki pea te tūponotanga.
Ngā raruraru

Kaore he uara (NaN)

Te ārai

Kaore he uauatanga

Te tātaritanga

Ko te whakamātautau tinana, te hītori hauora me ngā whakamātautau e whai ake nei e whakamahia ana hei whakatau i te macroglobulinemia Waldenstrom: Ngā whakamātautau toto. Ka taea e ngā whakamātautau toto te whakaatu mena he iti rawa ngā pūtau toto ora. I tua atu, ka kitea e ngā whakamātautau toto te pūmua i hangaia e ngā pūtau mate pukupuku. Ko te pūmua nei ko te immunoglobulin M, e kiia ana hoki ko IgM. Ka taea hoki e ngā whakamātautau toto te whakaatu i te pai o te mahi o ngā whekau. Ka taea e ngā hua te whakaatu mena kei te kino ngā pūmua IgM i ngā whekau, pēnei i ngā whatukuhu me te ate. Ko te kohikohi i te tauira o te wheua wheua mō te whakamātautau. I te wā o te biopsy wheua wheua, ka whakamahia he ngira hei tango i ētahi wheua wheua mai i te wheua huha. Ka haere te tauira ki te taiwhanga kei reira ka whakamātautauhia mō ngā pūtau mate pukupuku. Mena kei reira ngā pūtau mate pukupuku, ka taea e ngā whakamātautau atu te tuku atu i ngā mōhiohio atu mō ngā pūtau. Ngā whakamātautau whakaahua. Ka taea e ngā whakamātautau whakaahua te āwhina i te whakaatu mena kua horapa te mate pukupuku ki ētahi atu wāhi o te tinana. Ka uru pea ngā whakamātautau whakaahua ki ngā tirotiro CT, ki ngā tirotiro positron emission tomography rānei, e kiia ana hoki ko ngā tirotiro PET. Ngā Rāhui i te Kura Hauora Mayo Ka taea e to tātou rōpū manaaki o ngā tohunga Kura Hauora Mayo te āwhina i a koe ki ō kaupapa hauora e pā ana ki te macroglobulinemia Waldenstrom Tīmata Mai konei Tono mo te whakarite He raru kei te mōhiohio i tohuhia i raro nei, ā, tukuna anō te puka. Whiwhi i te matauranga mate pukupuku a te Kura Hauora Mayo ki tō pouakaroto. Ohauru mō te kore utu ka whiwhi i te aratohu hohonu ki te whakahaere i te mate pukupuku, me ngā mōhiohio whai hua mo te whiwhi i te whakaaro tuarua. Ka taea e koe te whakakore i te ohaurunga i tetahi wā. Pāwhiri konei mō te tirohanga īmēra. Wāhitau īmēra Kei te hiahia ahau ki te ako atu mō Ngā purongo me ngā rangahau hou mō te mate pukupuku Ngā rāhui tiaki me te whakahaere mate pukupuku a te Kura Hauora Mayo He hapa Kōwhiri tētahi kaupapa He hapa Kei te hiahiatia te mara īmēra He hapa Tāpirihia he wāhitau īmēra tika Wāhitau 1 Ohauru Ako atu mō te whakamahinga raraunga a te Kura Hauora Mayo. Hei whakarato i ngā mōhiohio tino tika me te whai hua ki a koe, me te mārama i ngā mōhiohio e whai hua ana, ka taea e mātou te whakakotahi i ō mōhiohio īmēra me te whakamahinga paetukutuku me ētahi atu mōhiohio kei a mātou mōu. Mena he tūmanako koe o te Kura Hauora Mayo, ka uru pea tenei ki ngā mōhiohio hauora tiaki. Mena ka whakakotahi mātou i ēnei mōhiohio ki ō mōhiohio hauora tiaki, ka whakahaere mātou i aua mōhiohio katoa hei mōhiohio hauora tiaki, ā, ka whakamahi noa rānei, ka whakapuaki rānei i aua mōhiohio pera me te whakaritea i roto i to mātou panui mō ngā tikanga tūmataiti. Ka taea e koe te whakakore i ngā korero īmēra i tetahi wā mā te pāwhiri i te hononga whakakore i roto i te īmēra. Mauruuru mō tō ohaurunga Ka tae mai tō aratohu hohonu ki te whakahaere i te mate pukupuku ki tō pouakaroto i roto i ngā meneti. Ka whiwhi hoki koe i ngā īmēra mai i te Kura Hauora Mayo mō ngā mea hou mō ngā purongo mate pukupuku, ngā rangahau, me te tiaki. Mena kaore koe e whiwhi i to īmēra i roto i ngā meneti 5, tirohia tō kōpaki SPAM, katahi ka whakapiri mai ki a mātou i [email protected]. Ka mutu tetahi mea i tō ohaurunga Tēnā, ngana anō i roto i ngā meneti torutoru Whakamātauria anō

Te rongoā

Ko ētahi o ngā tikanga whakaora mō te Waldenstrom macroglobulinemia:

  • Te tatari atawhai. Ki te mea kei roto i te toto ngā pūmua IgM, engari kāore he tohu, pea kaore e hiahiatia te whakaora i te wa poto. Engari, pea ka whakamātauhia tou toto i ia toru marama kia aroturukihia ai tō āhuatanga. Ka karanga ngā tākua i tēnei hei tatari atawhai. Pea kāore he hiahia mō te whakaora mō ngā tau maha.
  • Te whakawhiti plasma. Ka tangohia ngā pūmua IgM i te toto i te whakawhiti plasma, e mohiotia ana hoki ko te plasmapheresis. Ka whakakapia ngā pūmua IgM ki te plasma toto hauora. Ka taea e te whakawhiti plasma te whakaora i ngā tohu e puta mai ana i te nui o ngā pūmua IgM kei roto i te toto.
  • Te chemotherapy. Ka whakamahia e te chemotherapy ngā rongoā kaha hei whakamate i ngā pūtau mate pukupuku puta noa i te tinana. Ko te chemotherapy anake, te whakamahi ranei me ētahi atu rongoā, pea ko te whakaora tuatahi mō te hunga he tohu o te Waldenstrom macroglobulinemia. I tua atu, ka taea e te chemotherapy nui te mutu i te mahi a te wheua wheua ki te hanga pūtau, ā, pea ka whakamahia hei whakarite i te whakawhiti wheua wheua.
  • Te rongoā whāinga. Ka whakamahia e te rongoā whāinga ngā rongoā e whakaeke ana i ngā matū motuhake kei roto i ngā pūtau mate pukupuku. Mā te aukati i ēnei matū, ka taea e ngā maimoatanga whāinga te whakamate i ngā pūtau mate pukupuku. Pea ka whakamahia ngā rongoā rongoā whāinga me ētahi atu maimoatanga, pēnei i te chemotherapy, te immunotherapy rānei.
  • Te immunotherapy. Ko te immunotherapy he maimoatanga me te rongoā e āwhina ana i te pūnaha ārai mate o tō tinana ki te whakamate i ngā pūtau mate pukupuku. Ka whawhai te pūnaha ārai mate o tō tinana ki ngā mate mā te whakaeke i ngā mate pukupuku me ētahi atu pūtau kāore e tika kia noho ki roto i tō tinana. Ka ora ngā pūtau mate pukupuku mā te huna i a rātou anō i te pūnaha ārai mate. Ka āwhina te immunotherapy i ngā pūtau o te pūnaha ārai mate ki te kimi me te whakamate i ngā pūtau mate pukupuku.
  • Te whakawhiti wheua wheua. I ētahi wā, ko te whakawhiti wheua wheua, e mohiotia ana hoki ko te whakawhiti pūtau pakiaka, pea he maimoatanga mō te Waldenstrom macroglobulinemia. I te wa o tēnei mahi, ka horoia e ngā rongoā nui o te chemotherapy te wheua wheua. Ka tomo ngā pūtau pakiaka toto hauora ki te tinana hei hanga hou i te wheua wheua hauora.
  • Te tiaki tautoko. Ko te tiaki tautoko, e kiia ana hoki ko te tiaki whakaora mamae, e aro nui ana ki te whakaora i te mamae me ētahi atu tohu o te mate kino. Ka taea e tēnei paparanga tautoko atu te tautoko i a koe i a koe e whiwhi ana i ētahi atu maimoatanga, pēnei i te chemotherapy.
Te tiaki whaiaro

Kaore he uauatanga

Te whakarite mō tō whakaritenga

Mēnā he tohu kei a koe e awangawanga ana koe, whakaritea he whakatau me tō kaiwhakarato tiaki matua. Ki te whakaaro to kaiwhakarato tiaki matua kei a koe te Waldenstrom macroglobulinemia, ka tukuna pea koe ki te tohunga mātauranga i te whakaora i ngā āhuatanga o te toto me te wheua wheua, e mohiotia ana hoki ko te hematologist. Koinei etahi korero hei āwhina i a koe ki te whakarite mo tō whakatau. Ngā mea ka taea e koe Kia kawea mai te mema o te whānau, te hoa rānei hei āwhina i a koe ki te maumahara ki ngā korero ka whiwhi koe. Hangaia he rārangi o: ō tohu me te wā i tīmata ai rātou. Ngā rongoā katoa, ngā huaora, ngā taapiri rānei e inu ana koe, tae atu ki ngā rāpoi. Ngā pātai hei ui ki tō kaiwhakarato hauora. Ngā pātai hei ui pea: He aha te take pea o ō tohu? He take ke atu pea? Ngā whakamātautau e hiahia ana ahau? Ngā pātai hei ui ki te tohunga mena ka tukuna koe ki tētahi, tae atu ki: Kei ahau te Waldenstrom macroglobulinemia? Me tīmata tonu te whakaora? He aha ngā whāinga o te whakaora mōku? He aha te whakaora e tūtohutia ana e koe? He aha ngā pānga kino pea o te whakaora? He aha te tirohanga mō tōku āhuatanga? Kia tino ui ki ētahi atu pātai kei a koe. Ngā mea e tumanakohia ana mai i tō tākua Ka ui pea tō kaiwhakarato ki a koe i ētahi pātai, pēnei i: Pehea te huringa o ō tohu i te wā? He aha te mea e whakaiti ana, e pai ake rānei? He āhuatanga hauora ke atu kei a koe? He tangata i roto i tō whānau i pangia e te lymphoma? Na te kaimahi o te Kura Hauora o Mayo

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