He aha te Antihemophilic Factor VIII me von Willebrand Factor (Ara Iwi)? Ngā tohumate, ngā take, me te rongoā i te kāinga

Ko te Antihemophilic Factor VIII me von Willebrand Factor he rongoā whakaora-ora e tukuna ana mā te IV hei āwhina i tō toto kia tika te pūhi. E whakakapi ana tēnei rongoā i ngā pūmua pūhi toto ngaro, hē rānei i roto i ngā tāngata e pā ana ki ētahi mate toto, e āwhina ana ki te ārai i ngā wāhanga toto kino.

Ko te tikanga, ka hangaia e tō tinana ēnei pūmua hei aukati i te toto ina whara koe. Ki te kore ēnei pūmua e mahi tika ana, e ngaro ana rānei, ka taea e ngā tapahi iti te arahi ki ngā raruraru toto nui e kore e mutu noa.

He aha te Antihemophilic Factor VIII me von Willebrand Factor?

Kei roto i tēnei rongoā e rua ngā pūmua pūhi toto nui e mahi ngātahi ana me he tīma. Ka mahi te Factor VIII hei pūmua āwhina e whakatere ana i te tukanga pūhi, i te wā e āwhina ana te von Willebrand Factor i ō pūtau toto kia piri ngātahi hei hanga i ngā pūhi.

I hangaia te rongoā mai i te plasma toto tangata i tūao i āta tukatukahia, i purea hoki. Ka tukuna tika ki roto i tō rerenga toto mā te IV, i te nuinga o te wā i roto i te hōhipera, i te whare haumanu rānei i te wāhi e taea ai e ngā tākuta te mātakitaki i a koe.

I hangaia tēnei rongoā mō ngā tāngata kāore e hanga ana i ēnei mea pūhi toto i te taiao. E whakakapi ana i te mea e ngaro ana i tō tinana, e āwhina ana ki te whakahoki i te mahi pūhi toto noa.

He aha te ahua o te whiwhi i tēnei rongoā?

Ko te nuinga o ngā tāngata ka rongo i te whakaurunga IV me he wero iti, pērā i te tango toto mō te mahi taiwhanga. Kia tīmata te rere o te rongoā, kāore koe e rongo i tētahi mea rerekē i roto i tō rerenga toto.

I te wā o te whakauru, ka pā pea ētahi pānga taha ngawari ki a koe. Kei roto i ēnei he mamae paku i te upoko, te wera, te whero rānei, ētahi whakapairuaki rānei. I te nuinga o te wā ka ngaro wawe ēnei āhuatanga, ehara hoki i te take e māharahara ai.

E ai ki ētahi tāngata ka nui ake te kaha, ka mārie rānei i muri i te rongoā, ina koa i te wā e raru ana rātou i ngā raruraru toto e haere tonu ana. Ka mātakitaki tō rōpū hauora i a koe i te wā o te whakaurunga me muri iho kia mōhio ai kei te pai tō urupare.

He aha te take i hiahiatia ai tēnei rongoā?

Ko te take i hiahiatia ai tēnei rongoā nā ngā mate toto tuku iho e pā ana ki te pēhea te pūhi o tō toto. Ka puta ēnei āhuatanga i roto i ngā whānau, ā, kei reira mai i te whānautanga, ahakoa kāore pea ngā tohumate e puta mai tae noa ki muri mai i te ao.

Koinei ngā āhuatanga matua e hiahiatia ana tēnei rongoā:

• Hemophilia A - ina kāore tō tinana e hanga ana i te pūmua Factor VIII
• Te mate von Willebrand - ina kāore te Factor von Willebrand e mahi tika ana, kua ngaro rānei
• Te ngoikoretanga o te Factor VIII me te Factor von Willebrand - he āhuatanga onge e pā ana ki ngā pūmua e rua
• Ngā raruraru toto i riro mai - i ētahi wā ka puta mai i muri mai i te ao nā ētahi atu āhuatanga hauora

Kāore ēnei i ngā āhuatanga ka taea e koe te hopu mai i tētahi atu, te whakawhanake rānei mai i ngā whiringa oranga. Ka puta mai ēnei nā te huringa i roto i ō ira e pā ana ki te pēhea te hanga o ngā pūmua pūhi toto e tō tinana.

He aha tēnei rongoā he tohu, he tohumate rānei o?

Ko te hiahia ki tēnei rongoā e tohu ana he mate toto tōu e pā ana ki te kaha o tō toto ki te pūhi i te tikanga. Ehara tēnei i te tohumate i a ia anō, engari he rongoā hauora mō ngā āhuatanga kei raro.

Ko ngā āhuatanga kei raro e whakatikahia ana e tēnei rongoā ko ētahi momo mate toto:

• Hemophilia A - te mate pūhaehae tino nui, e pā ana ki ngā tāne te nuinga
• Momo 2N von Willebrand mate - i te wā e kore e taea e von Willebrand Factor te kawe tika i te Factor VIII
• Momo 3 von Willebrand mate - te momo tino kaha, i te wā e tino iti ana ngā pūmua e rua
• Hemophilia i riro mai - he āhua onge i te wā e whakaeke ana tō pūnaha ārai mate i ō ake mea whakakotahi
• Ngā āhua ngoikore tahi - ngā āhua tino onge e pā ana ki te maha o ngā pūmua whakakotahi

Ka mahia e tō tākuta ngā whakamātautau toto motuhake hei whakatau tika i te āhua e pā ana ki a koe. Ka āwhina tēnei i a rātou ki te whiriwhiri i te rongoā tika me te inenga mō tō āhuatanga motuhake.

Ka taea e ngā mate pūhaehae te pai ake i a rātou anō?

Ko te mea pouri, e kore e ngaro noa ngā mate pūhaehae i riro mai i te mea nā ngā huringa ira i puta. Ka raru tonu tō tinana ki te hanga, ki te whakamahi rānei i ēnei pūmua whakakotahi me te kore rongoā rongoā.

Heoi, ko te rongoā pai ko te rongoā tika, ka taea e te nuinga o te hunga e mate pūhaehae te noho i ngā oranga noa, kaha. Ka āwhina te rongoā auau ki te ārai i ngā wāhanga pūhaehae nui me te tiaki i ō hononga me ō okana mai i te kino.

Kāore pea ētahi tāngata e pā ana ki ngā momo ngawari o ēnei āhuatanga e hiahia rongoā i ngā wā katoa. Ka mahi tō tākuta ki a koe ki te hanga i tētahi mahere rongoā e hāngai ana ki ō hiahia me tō oranga.

Me pēhea te whakahaere i ngā mate pūhaehae i te kāinga?

Ahakoa e kore e taea e koe te rongoā i te āhua i raro i te kāinga, he huarahi nui hei tiaki i a koe anō me te whakahaere i tō hauora i waenga i ngā rongoā rongoā.

Anei ngā rautaki whakahaere kāinga matua ka āwhina i a koe kia noho haumaru:

• Ārearea ngā mahi e mōrearea ana te whara, pēnei i ngā hākinakina whakapā, te whakamahi rānei i ngā taputapu koi me te kore tūpato
• Kia mau ki te kete āwhina tuatahi kua whakakiia, me te mōhio ki te pēhi tika i ngā patunga e toto ana
• Mauhia ngā whakapaipai whakatūpato hauora e tohu ana i tō mate toto
• Tangohia ngā rongoā kua whakaritea kia rite tonu ki te tohutohu, tae atu ki ngā rongoā ārai
• Kia mau ki te whakapāpāpā tonu ki tō rōpū hauora, me te pūrongo i ngā toto rereke
• Kia mau ki te akuaku niho pai hei ārai i te toto mai i ngā kapia me ngā tikanga niho

He mea nui hoki te kōrero ki ō kaiwhakarato hauora katoa mō tō mate toto i mua i ngā tikanga katoa. Kei roto i tēnei ko ngā tākuta niho, ngā tākuta pokanga, me tō tākuta tiaki tuatahi mō te tiaki i ia rā.

He aha te rongoā hauora mō ngā mate toto?

E arotahi ana te rongoā hauora ki te whakakapi i ngā mea e kore e kitea e pā ana ki te toto, me te ārai i ngā wāhanga toto. Ka hangaia tō mahere rongoā kia hāngai ki tō āhuatanga me te kaha o tō mate.

Ko ngā kōwhiringa rongoā matua ko:

1. Te rongoā whakakapi ā-mea - ngā whakaurunga i ngā pūmua toto e ngaro ana
2. Te rongoā ārai - ngā whakaurunga ārai hei pupuri i ngā taumata tika o te mea toto
3. Te rongoā i runga i te tono - ngā whakaurunga ka hoatu ina puta te toto, i mua rānei i ngā tikanga
4. Desmopressin (DDAVP) - he rongoā ka taea te whakanui i te hanga mea toto o tō tinana i ētahi wā
5. Ngā rongoā antifibrinolytic - ngā rongoā hei āwhina i te whakapūmau i ngā pūhui toto ina hangaia

Ka aroturukihia e tō tākuta tō urupare ki te rongoā mā ngā whakamātautau toto i ia wā. Ka whakatikatikahia e rātou tō mahere rongoā ina hiahiatia kia mōhio ai koe kei te whiwhi koe i te whakamarumaru pai rawa atu i te toto.

Āhea au e kite ai i te tākuta mō ngā āwangawanga toto?

Me whakapā atu koe ki tō rōpū hauora i te wā tonu mena ka pā ki a koe he toto nui kāore e mutu mā ngā tikanga awhina tuatahi noa. He mea nui tēnei mēnā he mate tō toto e mōhiotia ana.

Rapua he āwhina hauora ohorere mō ēnei tūāhuatanga:

• He wharanga ki te upoko, he mamae nui rānei ki te upoko e tohu ana i te toto i roto
• He toto nui e mākū ana i ngā pātene, kāore rānei e mutu i muri i te 15 meneti o te pēhi tika
• He mamae tahi me te pūhi e tohu ana i te toto i roto
• He pāpāringa rerekē e puta ana kāore he wharanga, e tere ana te tipu
• He toto i roto i te mimi, te tūtae, te ruaki rānei
• He mamae nui ki te puku, ki te tuara rānei e tohu ana i te toto i roto

Kaua e tatari kia kite mena ka mutu noa te toto. Ki ngā mate toto, he pai ake te rapu āwhina wawe atu i muri, nā te mea ka ārai te rongoā wawe i ngā raruraru.

He aha ngā āhuatanga tūpono mō te whakawhanake i ngā mate toto?

Ko te nuinga o ngā mate toto he tūāuri, arā, ka tukuna iho mā ngā whānau. Ko te āhuatanga tūpono nui ko te whai mātua, whanaunga rānei e pā ana ki ēnei āhuatanga.

Ngā āhuatanga tūpono nui:

• He hītori whānau mō ngā mate toto - te tohu kaha rawa
• He tāne - mō te hemophilia A, e mau ana i te chromosome X
• He mātua e mau ana i ngā ira mō ngā mate toto
• Ētahi momo iwi e nui ake ana ngā reiti o ngā mate toto motuhake
• Te pakeketanga - mō ngā mate toto i riro mai i muri mai i te ora
• Ngā āhuatanga autoimmune - e ētahi wā ka whakaoho i ngā mate toto i riro mai

Mēnā he hītori whānau tō mō ngā mate toto, ka āwhina te tohutohu ira ki a koe ki te mārama ki ō tūponotanga. He mea nui tēnei mēnā kei te whakamahere koe ki te whai tamariki.

He aha ngā raruraru ka puta mai i ngā mate toto kāore i rongoatia?

Ki te kore e tika te rongoā, ka puta ngā raruraru nui i ngā mate toto, ka pā ki tō oranga me te hauora whānui. Ko te rongo pai, ka taea te ārai i te nuinga o ēnei raruraru mā te manaaki hauora tika.

Ngā raruraru ka puta:

• Te kino o ngā hononga mai i te toto e rere ana ki roto i ngā hononga, ka puta te rūmātiki me te iti o te nekehanga
• Te toto i roto i ngā uaua ka puta te mamae, te pūhi, me te kino tūturu
• Te toto o roto e mōrearea ana ki te ora, ina koa i roto i te roro, i te pūnaha kūnatu rānei
• Te anemia nui mai i te ngaronga toto tonu
• Ngā raruraru i te wā o te pokanga, i ngā mahi niho rānei
• Ngā pānga hinengaro mai i te noho me te mataku ki ngā wāhanga toto

Mā te rongoā hou, ka taea e te nuinga o te hunga e mate ana i ngā mate toto te karo i ēnei raruraru. Ko te manaaki hauora i ngā wā katoa me te whai i tō mahere rongoā te mea nui kia noho hauora me te kaha.

He pai, he kino rānei te rongoā Factor VIII me von Willebrand Factor mō ngā mate toto?

He tino pai tēnei rongoā mō te hunga e mate ana i ngā mate toto - he maha ngā wā ka whakaora i te ora, ā, ka tino pai ake te oranga. He nui ake ngā painga i ngā tūponotanga mō te hunga e hiahia ana ki tēnei rongoā.

Ka whai hua tonu te rongoā mā te whakahoki mai i te kaha o tō toto ki te whakakotahi tika. Ko te tikanga, he iti ake ngā wāhanga toto, he iti ake te kino o ngā hononga, me te kaha ki te whai wāhi ki ngā mahi noa.

Pērā i ngā rongoā katoa, ka puta ngā pānga taha, engari he onge ngā tauhohenga nui. Ka pai te nuinga o te hunga ki te rongoā, ā, ka kite i te whakapai ake i ō rātou tohumate me te hauora whānui.

He aha te mea ka pohehehia tēnei rongoā?

I ētahi wā ka pohehe te tangata i tēnei rongoā ātaahua ki ētahi atu hua toto, rongoā rānei. He mea nui kia mārama koe ki te mea e whiwhi ana koe, me te aha i whiriwhiria ai mō tō āhua.

Ka pohehe pea tēnei rongoā ki:

• Ngā whakawhitinga toto – e whakakapi ana i te toto katoa, kaua i ngā pūmua whakakotahi motuhake
• Ngā whakawhitinga plasma – kei roto i ēnei ngā pūmua maha, ehara i te mea ko ngā mea e hiahia ana koe
• Ētahi atu pūmua whakakotahi – kei roto pea i ēnei ngā huinga rerekē o ngā pūmua
• Ngā rongoā whakakotahi waihanga – e mahi rerekē ana i te rongoā whakakapi
• Ngā wai IV whānui – kāore he pūmua whakakotahi kei roto

Ka whakarite tō rōpū hauora kia mārama koe ki te rongoā e whiwhi ana koe. Kaua e whakaroa ki te pātai pātai mō tō rongoā me te aha te mea pai rawa atu mō tō āhuatanga motuhake.

Ngā pātai e pātai pinepine ana mō te rongoā Factor VIII me von Willebrand Factor

Kia pēhea te roa o ia wā rongoā?

Ko te nuinga o ngā whakaurunga e 30 meneti ki te 2 hāora, i runga i tō horopeta me te pēhea te urupare a tō tinana. Ka aroturuki tō rōpū hauora i a koe i tēnei wā kia mōhio ai kei te pai koe me te urupare pai ki te rongoā.

Kia pēhea te auau o taku hiahia ki ngā rongoā?

He rerekē rawa te auau o te rongoā i runga i tō āhuatanga motuhake me te kaha. Ko ētahi tāngata e hiahia ana ki ngā whakaurunga i ngā wā maha i te wiki mō te ārai, i te wā e puta ana te toto, i mua rānei i ngā tikanga. Ka waihanga tō tākuta i tētahi hōtaka e tika ana mō koe.

Ka taea e au te haere i te wā e whiwhi ana i tēnei rongoā?

Āe, he maha ngā tāngata e mate toto ana e haere angitu ana. Me whakamahere i mua mā te mahi tahi me ngā pokapū rongoā i tō ūnga me te kawe pea i ngā taonga ohorere. Ka taea e tō rōpū hauora te āwhina i a koe ki te whakarite mō te haere haumaru.

He pānga wā roa anō o tēnei rongoā?

Ki te nuinga o te tangata, he tino pai ngā pānga wā-roa – he pai ake te hauora, he iti ake ngā wā toto, me te pai ake o te kounga o te oranga. I ētahi wā, ka puta pea ngā paturopi i ētahi tāngata ka kore ai e whai hua te rongoā, engari ka aroturukihia tēnei e ō tākuta, ā, ka taea te whakatika i te rongoā ki te hiahiatia.

Kei te hipokina tēnei rongoā e te inihua?

Ko te nuinga o ngā mahere inihua e hipoki ana i tēnei rongoā nā te mea e whakaarohia ana he mea tika ā-hauora mō te hunga e mate toto ana. Heoi, he rerekē ngā kōrero mō te hipoki, nō reira he mea nui kia mahi tahi koe me tō rōpū hauora me te kamupene inihua kia mārama ki ō painga motuhake me ētahi utu ka puta.