Waikawa Carglumic (ara waha)

Carbaglu

Ka whakamahia ngā waikawa carglumic me te kai me ētahi atu rongoā hei whakaora me te aukati i te hyperammonemia (tēra atu te ammonia i roto i te toto) e puta mai ana i te kore o te enzyme ate e kiia nei ko te N-acetylglutamate synthase (NAGS). Ka whakamahia hoki ngā waikawa carglumic me te kai me ētahi atu rongoā hei aukati i te hyperammonemia e puta mai ana i ētahi mate ira e kiia nei ko te propionic acidemia (PA) rānei ko te methylmalonic acidemia (MMA). Ka hanga te ammonia i roto i te tinana ina kai tatou i te pūmua. Kāore te tangata kāore nei i te enzyme NAGS e taea te tukatuka tika i te ammonia, ā, ka nui rawa te ammonia ka kohikohi ki roto i te toto. Ka puta mai ētahi pānga kino nui. Ka mahi ngā waikawa carglumic mā te whakakapi i te enzyme NAGS ā, ka āwhina i te whakaiti i te nui o te ammonia i roto i te toto. Kei te wātea tēnei rongoā mā te tākuta anake. Kei te wātea tēnei hua i ngā āhua horoinga e whai ake nei:

I te whakatau ki te whakamahi i te rongoā, me whakarite te tūpono o te tango i te rongoā ki te pai ka puta mai. Ko tēnei he whakatau ka mahia e koe me tō tākuta. Mō tēnei rongoā, me whakaarohia enei: Korero atu ki tō tākuta mēnā kua pāngia koe e tetahi āhuatanga rerekē, te mate pāwera rānei ki tēnei rongoā, ki ētahi atu rongoā rānei. Korero atu hoki ki tō kaimahi hauora mēnā kei a koe ētahi atu momo mate pāwera, pēnei i ngā kai, ngā tae, ngā whakaora, ngā kararehe rānei. Mō ngā hua kore-tūtohu, panuihia te tohu, te kōwae rānei o ngā kai āta. Kāo te whakaatu i ngā rangahau tika i mahia tae noa ki tēnei wā i ngā raruraru motuhake a ngā tamariki ka ārai i te whakamahi o te waikawa carglumic i ngā tamariki. Kua whakapumautia te ora me te whai hua. Kāo te mahi i ngā rangahau tika i runga i te hononga o te tau ki ngā pānga o te waikawa carglumic i te taupori geriatric. Kāo te whakapumautia te ora me te whai hua. Kāo he rangahau tika i ngā wāhine mō te whakatau i te tūpono o te pēpi ina whakamahi i tēnei rongoā i te wā e whāngai u. Whakarite te hua pea ki ngā tūpono pea i mua i te tango i tēnei rongoā i te wā e whāngai u ana. Ahakoa kāo te whakamahi tahi i ētahi rongoā, i ētahi atu take ka taea te whakamahi tahi i ngā rongoā rerekē e rua ahakoa pea ka puta he mahi tahi. I enei take, kei te hiahia pea tō tākuta ki te whakarereke i te horo, te whakamahi rānei i ētahi atu tūpato. Korero atu ki tō kaimahi hauora mēnā kei te tango koe i ētahi atu rongoā tūtohu, kore-tūtohu rānei (over-the-counter [OTC]). Kāo te whakamahi i ētahi rongoā i te wā, i te taha rānei o te kai, te kai rānei i ētahi momo kai, no te mea pea ka puta he mahi tahi. Ko te whakamahi i te waipiro, te tapeka rānei me ētahi rongoā ka puta pea he mahi tahi. Kōrero atu ki tō kaimahi hauora te whakamahinga o tō rongoā me te kai, te waipiro, te tapeka rānei.