Neuroma y'ijwi ni igisebe kitazana kanseri gikura ku murambo munini ujyana kuva mu gutwi ryo imbere ujya mu bwonko. Uwo murambo witwa umurambo wa vestibular. Amashami y'uwo murambo agira ingaruka ku kubona umubiri ukomeye no kumva. Igisubizo cya neuroma y'ijwi gishobora gutera igihombo cyo kumva, gucumuza mu gutwi n'ibibazo byo kubona umubiri ukomeye. Irindi zina rya neuroma y'ijwi ni vestibular schwannoma. Neuroma y'ijwi ikura mu mitsi ya Schwann ikingira umurambo wa vestibular. Neuroma y'ijwi itera buhoro buhoro. Gake, ishobora gukura vuba ikaba nini bihagije kugira ngo ishikamire ku bwonko kandi igire ingaruka ku mirimo y'ingenzi. Ubuvuzi bwa neuroma y'ijwi burimo gukurikirana, imirasire n'ukuyikuraho.
Uko iyangabira ikura, bishobora kuba byoroshye gutera ibimenyetso bifatika cyangwa bibi kurushaho. Ibimenyetso bisanzwe bya acoustic neuroma birimo:
Impamvu y'ibibazo by'akama (acoustic neuromas) rimwe na rimwe ishobora guhuzwa n'ikibazo kiri kuri gene iri kuri chromosome ya 22. Ubusanzwe, iyi gene ikora poroteyine ibuza ubukoko (tumor suppressor protein) ifasha kugenzura ukura kw'uturemangingo twa Schwann dupfunyitse imiyoboro y'imbere. Impuguke ntizizi icyateye iki kibazo kuri iyi gene. Akenshi nta mpamvu izwi y'ibibazo by'akama. Iyi mpinduka ya gene iragenderwa mu bantu barwaye indwara y'akataraboneka yitwa neurofibromatosis type 2. Abantu barwaye neurofibromatosis type 2 ubusanzwe bagira ubukoko ku muyoboro w'umva n'uw'uburinganire ku mpande zombi z'umutwe. Ibi bibazo bizwi nka bilateral vestibular schwannomas.
Mu ndwara iterwa na gene iyobora izindi (autosomal dominant disorder), gene yahindutse ni gene iyobora izindi. Iherereye kuri imwe mu mpinga z'uturemangingo tudatwara igitsina, twitwa autosomes. Gene imwe gusa yahindutse irakenewe kugira ngo umuntu arwara ubu bwoko bw'uburwayi. Umuntu ufite uburwayi bwa autosomal dominant—muri uru rugero, se—afite amahirwe 50% yo kubyara umwana urwaye ufite gene imwe yahindutse na 50% yo kubyara umwana udahwaye.
Ikintu kimwe rukumbi cyemewe cyongera ibyago byo kurwara acoustic neuromas ni ukugira umubyeyi urwaye neurofibromatosis type 2, indwara idasanzwe iterwa na gene. Ariko rero, neurofibromatosis type 2 itera acoustic neuroma ku kigero cya 5% gusa.
Ibiranga neurofibromatosis type 2 ni uburibwe budatera kanseri ku mitsi y'umutekano ku mpande zombi z'umutwe. Uburibwe bushobora kandi kuvuka ku yandi mitsi.
Neurofibromatosis type 2 izwi nk'indwara iterwa na gene iyobora izindi (autosomal dominant disorder). Ibi bivuze ko gene ifitanye isano n'ubwo burwayi ishobora guherwa umwana n'umubyeyi umwe gusa. Buri mwana w'umubyeyi urwaye afite amahirwe 50-50 yo kuyihera.
Uburwayi bwa neurome acoustique bushobora gutera ingaruka zidakira, zirimo:
Isuzuma rusange ry'umubiri, harimo n'isuzuma ry'amatwi, akenshi ni intambwe ya mbere mu gupima no kuvura acoustic neuroma.
Acoustic neuroma akenshi biragoye kuyipima mu ntangiriro kuko ibimenyetso bishobora kuba byoroshye kubirengagiza kandi bikamera gahoro gahoro. Ibimenyetso bisanzwe nko kubura kumva, binashamikiye ku zindi ngingo nyinshi z'amatwi yo hagati n'amatwi yo imbere.
Nyuma yo kubaza ibibazo ku bimenyetso byawe, umwe mu bagize itsinda ry'ubuzima bwawe azakora isuzuma ry'amatwi. Ushobora kuba ukeneye ibizamini bikurikira:
Isuzuma ry'umva, rizwi nka audiometry. Iki kizamini gikorerwa n'inzobere mu by'umva yitwa audiologist. Mu gihe cy'ikizamini, amajwi ajyanwa mu gutwi rimwe. Audiologist atanga urugero rw'amajwi y'injyana zitandukanye. Ugaragaza buri gihe wumvise ijwi. Buri njyana isubirwamo ku rwego rwo hasi kugira ngo umenye igihe utabasha kumva.
Audiologist ashobora kandi gutanga amagambo atandukanye kugira ngo apime uburyo wumva.
Amashusho. Magnetic resonance imaging (MRI) ikoresheje ibara ry'amabara ikoreshwa cyane mu gupima acoustic neuroma. Iki kizamini cyo kubona amashusho gishobora kumenya ibibyimba bito cyane nk'iby'ubunini bwa milimeteri 1 kugeza kuri 2. Niba MRI itaboneka cyangwa udashobora gukora MRI, computerized tomography (CT) ishobora gukoreshwa. Ariko, CT scan ishobora kubura ibibyimba bito.
Isuzuma ry'umva, rizwi nka audiometry. Iki kizamini gikorerwa n'inzobere mu by'umva yitwa audiologist. Mu gihe cy'ikizamini, amajwi ajyanwa mu gutwi rimwe. Audiologist atanga urugero rw'amajwi y'injyana zitandukanye. Ugaragaza buri gihe wumvise ijwi. Buri njyana isubirwamo ku rwego rwo hasi kugira ngo umenye igihe utabasha kumva.
Audiologist ashobora kandi gutanga amagambo atandukanye kugira ngo apime uburyo wumva.
Ubuvuzi bwa neuroma yawe y'ijwi bushobora gutandukana, bitewe na:
Umuhakana: Kanama ni urubuga rw'amakuru y'ubuzima kandi ibisubizo byayo ntibigize inama z'ubuvuzi. Jya ubona umuganga ufite uruhushya rwo gukorera hafi yawe mbere yo gukora impinduka izo ari zo zose.