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Neurome Acoustique

Incamake

Neuroma y'ijwi ni igisebe kitazana kanseri gikura ku murambo munini ujyana kuva mu gutwi ryo imbere ujya mu bwonko. Uwo murambo witwa umurambo wa vestibular. Amashami y'uwo murambo agira ingaruka ku kubona umubiri ukomeye no kumva. Igisubizo cya neuroma y'ijwi gishobora gutera igihombo cyo kumva, gucumuza mu gutwi n'ibibazo byo kubona umubiri ukomeye. Irindi zina rya neuroma y'ijwi ni vestibular schwannoma. Neuroma y'ijwi ikura mu mitsi ya Schwann ikingira umurambo wa vestibular. Neuroma y'ijwi itera buhoro buhoro. Gake, ishobora gukura vuba ikaba nini bihagije kugira ngo ishikamire ku bwonko kandi igire ingaruka ku mirimo y'ingenzi. Ubuvuzi bwa neuroma y'ijwi burimo gukurikirana, imirasire n'ukuyikuraho.

Ibimenyetso

Uko iyangabira ikura, bishobora kuba byoroshye gutera ibimenyetso bifatika cyangwa bibi kurushaho. Ibimenyetso bisanzwe bya acoustic neuroma birimo:

  • Kugira ikibazo cyo kumva, akenshi buhoro buhoro mu mezi cyangwa imyaka. Mu bihe bitoroshye, kubura kumva bishobora kuba kudasubira inyuma. Kubura kumva akenshi bibaho ku ruhande rumwe cyangwa bikaba bibi kurushaho ku ruhande rumwe.
  • Gucana amatwi mu gutwi gufatwaho, bizwi nka tinnitus.
  • Kubura ubusugire cyangwa kudahumura.
  • Kuzenguruka.
  • Ubugufi bw'umubiri no, mu bihe bitoroshye cyane, intege nke cyangwa kubura kwihuta kw'imitsi. Egera umuganga wita ku buzima niba ubona ikibazo cyo kumva mu gutwi rumwe, gucana amatwi cyangwa ibibazo byo kugira umutekano. Kumenya hakiri kare acoustic neuroma bishobora gufasha mu kwirinda ko iyangabira ikura ikaze cyane ku buryo itera ingaruka mbi nko kubura kumva burundu. Andika kuri email kugira ngo wumve amakuru mashya yerekeye kuvura, ibizamini no kubaga indwara z'ubwonko.
Impamvu

Impamvu y'ibibazo by'akama (acoustic neuromas) rimwe na rimwe ishobora guhuzwa n'ikibazo kiri kuri gene iri kuri chromosome ya 22. Ubusanzwe, iyi gene ikora poroteyine ibuza ubukoko (tumor suppressor protein) ifasha kugenzura ukura kw'uturemangingo twa Schwann dupfunyitse imiyoboro y'imbere. Impuguke ntizizi icyateye iki kibazo kuri iyi gene. Akenshi nta mpamvu izwi y'ibibazo by'akama. Iyi mpinduka ya gene iragenderwa mu bantu barwaye indwara y'akataraboneka yitwa neurofibromatosis type 2. Abantu barwaye neurofibromatosis type 2 ubusanzwe bagira ubukoko ku muyoboro w'umva n'uw'uburinganire ku mpande zombi z'umutwe. Ibi bibazo bizwi nka bilateral vestibular schwannomas.

Ingaruka zishobora guteza

Mu ndwara iterwa na gene iyobora izindi (autosomal dominant disorder), gene yahindutse ni gene iyobora izindi. Iherereye kuri imwe mu mpinga z'uturemangingo tudatwara igitsina, twitwa autosomes. Gene imwe gusa yahindutse irakenewe kugira ngo umuntu arwara ubu bwoko bw'uburwayi. Umuntu ufite uburwayi bwa autosomal dominant—muri uru rugero, se—afite amahirwe 50% yo kubyara umwana urwaye ufite gene imwe yahindutse na 50% yo kubyara umwana udahwaye.

Ikintu kimwe rukumbi cyemewe cyongera ibyago byo kurwara acoustic neuromas ni ukugira umubyeyi urwaye neurofibromatosis type 2, indwara idasanzwe iterwa na gene. Ariko rero, neurofibromatosis type 2 itera acoustic neuroma ku kigero cya 5% gusa.

Ibiranga neurofibromatosis type 2 ni uburibwe budatera kanseri ku mitsi y'umutekano ku mpande zombi z'umutwe. Uburibwe bushobora kandi kuvuka ku yandi mitsi.

Neurofibromatosis type 2 izwi nk'indwara iterwa na gene iyobora izindi (autosomal dominant disorder). Ibi bivuze ko gene ifitanye isano n'ubwo burwayi ishobora guherwa umwana n'umubyeyi umwe gusa. Buri mwana w'umubyeyi urwaye afite amahirwe 50-50 yo kuyihera.

Ingaruka

Uburwayi bwa neurome acoustique bushobora gutera ingaruka zidakira, zirimo:

  • Gutakaza kumva.
  • Kubabara no kunanirwa mu maso.
  • Ibibazo byo kubura umutekano.
  • Gucana amatwi.
Kupima

Isuzuma rusange ry'umubiri, harimo n'isuzuma ry'amatwi, akenshi ni intambwe ya mbere mu gupima no kuvura acoustic neuroma.

Acoustic neuroma akenshi biragoye kuyipima mu ntangiriro kuko ibimenyetso bishobora kuba byoroshye kubirengagiza kandi bikamera gahoro gahoro. Ibimenyetso bisanzwe nko kubura kumva, binashamikiye ku zindi ngingo nyinshi z'amatwi yo hagati n'amatwi yo imbere.

Nyuma yo kubaza ibibazo ku bimenyetso byawe, umwe mu bagize itsinda ry'ubuzima bwawe azakora isuzuma ry'amatwi. Ushobora kuba ukeneye ibizamini bikurikira:

  • Isuzuma ry'umva, rizwi nka audiometry. Iki kizamini gikorerwa n'inzobere mu by'umva yitwa audiologist. Mu gihe cy'ikizamini, amajwi ajyanwa mu gutwi rimwe. Audiologist atanga urugero rw'amajwi y'injyana zitandukanye. Ugaragaza buri gihe wumvise ijwi. Buri njyana isubirwamo ku rwego rwo hasi kugira ngo umenye igihe utabasha kumva.

    Audiologist ashobora kandi gutanga amagambo atandukanye kugira ngo apime uburyo wumva.

  • Amashusho. Magnetic resonance imaging (MRI) ikoresheje ibara ry'amabara ikoreshwa cyane mu gupima acoustic neuroma. Iki kizamini cyo kubona amashusho gishobora kumenya ibibyimba bito cyane nk'iby'ubunini bwa milimeteri 1 kugeza kuri 2. Niba MRI itaboneka cyangwa udashobora gukora MRI, computerized tomography (CT) ishobora gukoreshwa. Ariko, CT scan ishobora kubura ibibyimba bito.

Isuzuma ry'umva, rizwi nka audiometry. Iki kizamini gikorerwa n'inzobere mu by'umva yitwa audiologist. Mu gihe cy'ikizamini, amajwi ajyanwa mu gutwi rimwe. Audiologist atanga urugero rw'amajwi y'injyana zitandukanye. Ugaragaza buri gihe wumvise ijwi. Buri njyana isubirwamo ku rwego rwo hasi kugira ngo umenye igihe utabasha kumva.

Audiologist ashobora kandi gutanga amagambo atandukanye kugira ngo apime uburyo wumva.

Uburyo bwo kuvura

Ubuvuzi bwa neuroma yawe y'ijwi bushobora gutandukana, bitewe na:

  • Ubunini n'umuvuduko wo gukura kwa neuroma y'ijwi.
  • Ubuzima bwawe muri rusange.
  • Ibimenyetso byawe. Hariho uburyo butatu bwo kuvura neuroma y'ijwi: gukurikirana, kubaga cyangwa kuvura hakoreshejwe imirasire. Wowe n'itsinda ry'abaganga bawe mushobora guhitamo gukurikirana neuroma y'ijwi niba ari nto kandi idakura cyangwa niba ikura buhoro buhoro. Ibi bishobora kuba amahitamo niba neuroma y'ijwi itatera ibimenyetso bike cyangwa nta bimenyetso na bimwe. Gukurikirana bishobora kandi kugirwa inama niba uri umuntu mukuru cyangwa niba utari umukandida mwiza wo kuvurwa bikomeye. Mu gihe ukomeje gukurikiranwa, uzakenera ibizamini byo kubona amashusho n'ibizamini by'umva, ubusanzwe buri mezi 6 kugeza kuri 12. Ibi bizamini bishobora kumenya niba uburibwe bukomeje gukura n'umuvuduko wabwo. Niba ibizamini byerekana ko uburibwe bukomeje gukura cyangwa niba uburibwe butera ibimenyetso bibi cyangwa ibindi bibazo, ushobora kuba ukeneye kubagwa cyangwa kuvurwa hakoreshejwe imirasire. Ushobora kuba ukeneye kubagwa kugira ngo ukureho neuroma y'ijwi, cyane cyane niba uburibwe ari:
  • Bukomeje gukura.
  • Bunini cyane.
  • Buteye ibimenyetso. Umuganga wawe ashobora gukoresha imwe mu mbaraga nyinshi zo gukuraho neuroma y'ijwi. Uburyo bwo kubaga biterwa n'ubunini bw'uburibwe, uko wumva n'ibindi bintu. Intego yo kubaga ni ukukuraho uburibwe no kubungabunga umutsi w'isura kugira ngo wirinde ubugufi bw'imitsi yo mu maso yawe. Gukuraho uburibwe bwose bishobora kudahora bishoboka. Urugero, niba uburibwe buri hafi cyane y'ibice by'ingenzi by'ubwonko cyangwa umutsi w'isura, igice kimwe cy'uburibwe gishobora gukurwaho gusa. Kubaga neuroma y'ijwi bikorwa hakoreshejwe anesthésie générale. Kubaga bikubiyemo gukuraho uburibwe binyuze mu gutwi ryo imbere cyangwa binyuze mu idirishya riri mu gatuza kawe. Rimwe na rimwe gukuraho uburibwe bishobora kongera ibimenyetso niba kumva, kubona umubiri, cyangwa imitsi y'isura bikanganye cyangwa bikomeretse mu gihe cy'igihe cyo kubaga. Kumva bishobora gucika ku ruhande habagwa. Kubona umubiri ubusanzwe bigira ingaruka by'igihe gito. Ingaruka zishobora kubaho zirimo:
  • Kuvuza amazi akikije ubwonko bwawe n'umugongo, bizwi nka cerebrospinal fluid. Kuvuza bishobora kuba binyuze mu kibyimba.
  • Gutakaza kumva.
  • Ubugufi bw'isura cyangwa kubabara.
  • Gucana mu gutwi.
  • Ibibazo byo kubona umubiri.
  • Kubabara umutwe bidashira.
  • Gake cyane, kwandura kwa cerebrospinal fluid, bizwi nka meningitis.
  • Gake cyane, stroke cyangwa kuva amaraso mu bwonko. Ubukorerabuhanga bwa stereotactic radiosurgery bukoresha imirasire myinshi ya gamma kugira ngo butange umwanya uhamye w'imirasire ku ntego. Hariho ubwoko butandukanye bw'ubuvuzi hakoreshejwe imirasire bukoreshwa mu kuvura neuroma y'ijwi:
  • Stereotactic radiosurgery. Ubwoko bw'ubuvuzi hakoreshejwe imirasire buzwi nka stereotactic radiosurgery bushobora kuvura neuroma y'ijwi. Akenshi ikoreshwa niba uburibwe ari buto - butarenga santimetero 2.5 z'umurambararo. Ubuvuzi hakoreshejwe imirasire bushobora kandi gukoreshwa niba uri umuntu mukuru cyangwa niba udashobora kwihanganira kubagwa kubera impamvu z'ubuzima. Stereotactic radiosurgery, nka Gamma Knife na CyberKnife, ikoresha imirasire myinshi ya gamma kugira ngo itange umwanya uhamye w'imirasire ku buribwe. Ubu buryo butanga ubuvuzi bidakomeretsa imyenda iikikije cyangwa gukora incision. Intego ya stereotactic radiosurgery ni uguhagarika gukura kw'uburibwe, kubungabunga imikorere y'umutsi w'isura kandi bishoboka ko bikabungabunga kumva. Bishobora kumara ibyumweru, amezi cyangwa imyaka mbere y'uko ubona ingaruka za radiosurgery. Itsinda ry'abaganga bawe rikurikirana amajyambere yawe hakoreshejwe ibizamini byo kubona amashusho n'ibizamini by'umva. Ibyago bya radiosurgery birimo:
    • Gutakaza kumva.
    • Gucana mu gutwi.
    • Ubugufi bw'isura cyangwa kubabara.
    • Ibibazo byo kubona umubiri.
    • Gukomeza gukura kw'uburibwe.
  • Gutakaza kumva.
  • Gucana mu gutwi.
  • Ubugufi bw'isura cyangwa kubabara.
  • Ibibazo byo kubona umubiri.
  • Gukomeza gukura kw'uburibwe.
  • Fractionated stereotactic radiotherapy. Fractionated stereotactic radiotherapy (SRT) itanga umwanya muto w'imirasire ku buribwe mu byiciro byinshi. SRT ikorwa kugira ngo igabanye gukura kw'uburibwe bidakomeretsa imyenda y'ubwonko iikikije.
  • Proton beam therapy. Ubwoko bw'ubuvuzi hakoreshejwe imirasire bukoresha imirasire ifite imbaraga nyinshi y'ibice byashyizweho umuzigo bizwi nka protons. Imirasire ya proton itangwa mu gice cyangiritse mu bice byateganijwe kugira ngo ivure uburibwe. Ubwoko bw'ubuvuzi buragabanya imirasire igera mu gice cyikikije. Stereotactic radiosurgery. Ubwoko bw'ubuvuzi hakoreshejwe imirasire buzwi nka stereotactic radiosurgery bushobora kuvura neuroma y'ijwi. Akenshi ikoreshwa niba uburibwe ari buto - butarenga santimetero 2.5 z'umurambararo. Ubuvuzi hakoreshejwe imirasire bushobora kandi gukoreshwa niba uri umuntu mukuru cyangwa niba udashobora kwihanganira kubagwa kubera impamvu z'ubuzima. Stereotactic radiosurgery, nka Gamma Knife na CyberKnife, ikoresha imirasire myinshi ya gamma kugira ngo itange umwanya uhamye w'imirasire ku buribwe. Ubu buryo butanga ubuvuzi bidakomeretsa imyenda iikikije cyangwa gukora incision. Intego ya stereotactic radiosurgery ni uguhagarika gukura kw'uburibwe, kubungabunga imikorere y'umutsi w'isura kandi bishoboka ko bikabungabunga kumva. Bishobora kumara ibyumweru, amezi cyangwa imyaka mbere y'uko ubona ingaruka za radiosurgery. Itsinda ry'abaganga bawe rikurikirana amajyambere yawe hakoreshejwe ibizamini byo kubona amashusho n'ibizamini by'umva. Ibyago bya radiosurgery birimo:
  • Gutakaza kumva.
  • Gucana mu gutwi.
  • Ubugufi bw'isura cyangwa kubabara.
  • Ibibazo byo kubona umubiri.
  • Gukomeza gukura kw'uburibwe. Uretse ubuvuzi bwo gukuraho cyangwa guhagarika gukura kw'uburibwe, ubuvuzi bwo gufasha bushobora gufasha. Ubuvuzi bwo gufasha buvura ibimenyetso cyangwa ingaruka za neuroma y'ijwi n'ubuvuzi bwayo, nko guhindagurika cyangwa ibibazo byo kubona umubiri. Ibisimbuzo by'amatwi cyangwa ibindi bivura bishobora gukoreshwa mu gutakaza kumva. Kwandikisha ubuntu kandi ubone amakuru mashya ku buvuzi bw'ubwonko, ibizamini n'ubuganga. inkuru yo gukuramo imeri. Kwitwara n'amahirwe yo gutakaza kumva no gucika intege mu maso bishobora kuba bigoye cyane. Guhitamo ubuvuzi bwaba bukubereye na bwo bishobora kuba bigoye. Ibi bitekerezo bishobora gufasha:
  • Menyesha ibyerekeye acoustic neuromas. Uko umenya byinshi, ni ko witegura neza kugira ngo utore neza ubuvuzi. Uretse kuvugana n'itsinda ry'abaganga bawe n'umuganga wawe w'amatwi, ushobora kwifuza kuvugana n'umujyanama cyangwa umukozi w'imibereho. Cyangwa ushobora kubona ko ari ingirakamaro kuvugana n'abandi bantu bafite acoustic neuroma. Bishobora gufasha kumenya byinshi ku byabayeho byabo mu gihe cyo kuvurwa no nyuma yacyo.
  • Gabanya ubufasha bukomeye. Umuryango n'inshuti bashobora kugufasha mu gihe uhanganye n'iki gihe gikomeye. Rimwe na rimwe, ariko, ushobora kubona ko impungenge n'ubwumvikane bw'abandi bantu bafite acoustic neuroma ari byo biguhumuriza cyane. Itsinda ry'abaganga bawe cyangwa umukozi w'imibereho ashobora kugushyira mu itsinda ry'ubufasha. Cyangwa ushobora kubona itsinda ry'ubufasha ryihariye cyangwa rya online binyuze muri Acoustic Neuroma Association. Gabanya ubufasha bukomeye. Umuryango n'inshuti bashobora kugufasha mu gihe uhanganye n'iki gihe gikomeye. Rimwe na rimwe, ariko, ushobora kubona ko impungenge n'ubwumvikane bw'abandi bantu bafite acoustic neuroma ari byo biguhumuriza cyane. Itsinda ry'abaganga bawe cyangwa umukozi w'imibereho ashobora kugushyira mu itsinda ry'ubufasha. Cyangwa ushobora kubona itsinda ry'ubufasha ryihariye cyangwa rya online binyuze muri Acoustic Neuroma Association.

Aderesi: 506/507, 1st Main Rd, Murugeshpalya, K R Garden, Bengaluru, Karnataka 560075

Umuhakana: Kanama ni urubuga rw'amakuru y'ubuzima kandi ibisubizo byayo ntibigize inama z'ubuvuzi. Jya ubona umuganga ufite uruhushya rwo gukorera hafi yawe mbere yo gukora impinduka izo ari zo zose.

Yakorewe mu Buhinde, ku isi