Health Library Logo

Health Library

Calciphylaxis

Incamake

Calciphylaxis (kal-sih-fuh-LAK-sis) ni indwara y'akataraboneka kandi ikomeye. Igaragara mu kubitsa kwa calcium mu mitsi mito y'amaraso yo mu mitsi y'ibinure n'uruhu.

Ibimenyetso bya Calciphylaxis birimo imikaya y'amaraso, ibice biri munsi y'uruhu, n'ibisebe byafunguye bibabaza bitwa uduce. Iyo uduce twanduye, bishobora kuba bibi ku buryo bwangiza ubuzima.

Intandaro nyakuri ya calciphylaxis ntiirasobanutse. Ariko abantu barwaye iyi ndwara bakunze kugira ibibazo by'impyiko. Icyo ni ikibazo aho impyiko zitakora nk'uko bikwiye. Akenshi, abo bantu baba baravuwe indwara z'impyiko nka dialyse cyangwa gutera impyiko. Calciphylaxis ishobora kubaho no mu bantu badafite indwara z'impyiko.

Ubuvuzi bwa Calciphylaxis burimo imiti itandukanye, uburyo n'ubuganga. Ubuvuzi bushobora gufasha gukumira imikaya y'amaraso n'indwara, kugabanya ubwinshi bwa calcium, gukiza ibisebe, no kugabanya ububabare.

Ibimenyetso

Ibimenyetso bya Calciphylaxis birimo:

  • Ubururu bugari ku ruhu bufite ishusho isa n'iy'umuyoboro, bushobora kugaragara nk'umutuku-umukara.
  • Ibisebe bikomeye, bibabaza ku ruhu bishobora guhinduka ibyo kubabara. Ibyo bibabaza bikunze kugira agasanduku k'umukara-umukara kadakira ubwakwo. Ibibabaza bikunze kugaragara ahantu hari amavuta menshi, nko mu nda, mu mavi, mu kibuno no mu mabere. Ariko bishobora kuvuka ahantu hose.
  • Imyanda iterwa n'ibibabaza bidakira.
Impamvu

Intandukwa nyakuri ya calciphylaxis ntirazwi. Indwara irimo umunywane w'umucanga mu bice bito cyane by'imitsi mu mitsi y'amavuta no mu ruhu.

Abantu benshi barwara calciphylaxis nabo bafite ibibazo by'impyiko cyangwa bakora dialyse. Ntibiramenyekana impamvu abantu bafite ibibazo by'impyiko cyangwa abakora dialyse bafite ibyago byinshi byo kurwara calciphylaxis.

Kuri bamwe, umunywane w'umucanga muri calciphylaxis uhujwe n'imikaya mito iri mu ijosi yitwa parathyroid glands. Niba izo mikaya isohora imisemburo myinshi ya parathyroid, bishobora gutuma umucanga ugereranya. Ariko umubano nturasobanuka. Abantu benshi bafite ibibazo bikomeye bya parathyroid glands ntibarwara calciphylaxis. Kandi abantu benshi bafite ibibazo by'impyiko na calciphylaxis ntabwo bafite ibibazo bya parathyroid glands.

Ibindi bintu bisa nkaho bigira uruhare muri calciphylaxis birimo:

  • Gushaka kw'amaraso gukomera. Amaraso ashobora kubura umwuka n'ibiribwa mu mitsi y'amavuta no mu ruhu.
  • Kugabanuka kw'amaraso mu mitsi mito, bishobora gutuma habaho ibibyimba n'ibicurane by'uruhu.
  • Kugira umubiri ukomeye cyangwa ibikomere, byitwa fibrosis.
  • Gukomeretsa bikomeza ku rwego rwo hanze rw'uturemangingo duto dukingira imiyoboro y'amaraso. Ibi kandi byitwa vascular endothelial injury.
  • Kubyimba, byitwa inflammation, mu mubiri.
Ingaruka zishobora guteza

Calciphylaxis ikunda kwibasira abantu bafite ibibazo by'impumyi. Ibindi bintu byongera ibyago birimo:

  • Kuvuka ari umugore.
  • Guhera.
  • Diabete mellitus.
  • Gucika intege kw'umwijima, iyo umwijima uhagaritse gukora nkuko bikwiye.
  • Amateka ya dialyse. Ubu buryo buvana imyanda n'amazi y'umubiri mu maraso iyo impumyi zitakibasha kubikora.
  • Gutendeka kw'amaraso kurushaho, bizwi kandi nka hypercoagulable state.
  • Kubura ubusugire bw'umubiri bw'imyunyu y'ubutare ya calcium cyangwa phosphate, cyangwa ya proteine ya albumin.
  • Imiti imwe, nka warfarin (Jantoven), ibintu bifunga calcium na corticosteroids.
Ingaruka

Ingaruka mbi za calciphylaxis zirimo:

  • Ububabare bukomeye.
  • Ibyo kubora bikomeye kandi binini bidakira ubwabyo.
  • Imyanda y'amaraso.
  • Urupfu, ahanini bitewe n'indwara cyangwa kudakora neza kw'imirimo y'ingingo.

Akenshi, icyerekezo cy'abantu barwaye calciphylaxis ntikiba cyiza. Gushaka no kuvura vuba indwara ni ingenzi mu gukumira ingaruka mbi zikomeye.

Kwirinda

Nta buryo bugaragara bwo gukumira indwara ya calciphylaxis. Ariko niba uri kuri dialyse cyangwa ufite akazi k'impyiko kaciriritse kubera indwara y'impyiko zidakira ikomeye, ni ngombwa kugumana urwego rw'ubushuhe bw'amaraso rwa calcium na phosphore. Kugumana urwego rw'ubushuhe bw'amaraso rwa phosphore munsi y'uburyo buhagije akenshi biba ikibazo. Umuganga wawe ashobora kugusaba gufata imiti mugihe cyo kurya. Ushobora kandi gukenera kwirinda ibiryo bimwe na bimwe birimo phosphore nyinshi. Ni ngombwa cyane gukurikiza amabwiriza y'abaganga bawe no kujya mu bugenzuzi bwose bw'ubuzima. Niba ufite calciphylaxis, itsinda ry'abaganga bakwitaho riragufasha gukumira ubwandu bw'ibisebe cyangwa ibindi bibazo. Ushobora kuba ukeneye gushyira imyenda yihariye ku bibisebe cyangwa ukakaraba buri munsi kugira ngo wirinde mikorobe zitwa bacteria gukura.

Kupima

Kumenya icyateye indwara bisobanura kureba niba calciphylaxis ari yo yateye ibimenyetso urimo. Umuganga wawe areba amateka yawe y’ubuzima, akubaza ibimenyetso urimo, akakora isuzuma ngaruka mbere.

Ushobora kandi gukenera ibizamini nkibi:

  • Ubusembwa bw'uruhu. Muri ubu buryo, umuganga wawe akuramo igice gito cy'umubiri mu gice cy'uruhu rwahuye n'uburwayi. Hanyuma, laboratwari igenzura icyo kigice.
  • Ibizamini by'amaraso. Laboratwari ishobora kupima ibintu bitandukanye biri mu maraso yawe. Ibi birimo creatinine, calcium, phosphorus, parathyroid hormone na vitamine D. Ibyavuye muri ibi bizamini bifasha itsinda ry'abaganga bawe kureba uko impyiko zawe zikora.
  • Ibizamini byo kubona ishusho. Ibi bishobora kugira akamaro niba ibyavuye mu busembwa atari byumvikana neza cyangwa niba ubusembwa budashoboka. X-rays ishobora kwerekana uburyo calcium yubatswe mu mitsi y'amaraso. Ubu buryo bwo kubaka ni bwo busanzwe muri calciphylaxis no mu zindi ndwara zikomeye z'impyiko.
Uburyo bwo kuvura

Kuvura ibikomere ni igice cy'ingenzi cyo kuvura indwara ya calciphylaxis. Bityo, byaba byiza cyane kugira itsinda ry'inzobere mu kuvura ibikomere.

Kugabanya uburyo umunyu wa calcium wikwirakwira mu mitsi bishobora gufashwa na:

  • Dialysis. Niba uhabwa ubuvuzi bwa dialysis y'impyiko, umuganga wawe ashobora guhindura imiti ikoreshwa ndetse n'igihe n'uburyo uhabwa dialysis. Byaba byiza kongera umubare n'igihe cy'ibikorwa bya dialysis.
  • Guhindura imiti. Umuganga wawe asuzuma imiti ukoresha ubu kandi akuraho ibintu bishobora gutera calciphylaxis. Ibi bintu birimo warfarin, corticosteroids na fer. Niba ufashe calcium cyangwa vitamin D, umuganga wawe ashobora guhindura umubare wabyo cyangwa akakubuza kubifata.
  • Guta imiti. Imiti yitwa sodium thiosulfate ishobora kugabanya uburyo umunyu wa calcium wikwirakwira mu mitsi mito. Itangwa hakoreshejwe igishishwa mu mutsi gatatu mu cyumweru, akenshi mu gihe cya dialysis. Umuganga wawe ashobora kugusaba gufata imiti yitwa cinacalcet (Sensipar), ishobora gufasha kugenzura hormone ya parathyroid (PTH). Izindi miti ishobora gukoreshwa kugira ngo iboneze uburyo calcium na phosphorus bihuza mu mubiri wawe.
  • Ubuvuzi. Niba umusemburo wa parathyroid ukora cyane ukora PTH nyinshi ugira uruhare mu ndwara yawe, ubuvuzi bushobora kuba igisubizo. Ubuvuzi bwitwa parathyroidectomy bushobora gukuraho igice cyangwa byose by'umusemburo wa parathyroid.

Kugira ngo ibikomere bikire, bimwe mu bice byangijwe na calciphylaxis bishobora gukenera gukurwaho hakoreshejwe ubuvuzi. Ibi bita debridement. Rimwe na rimwe, imyenda ishobora gukurwaho hakoreshejwe ubundi buryo, nko gukoresha imyenda y'amazi. Imiti yitwa antibiyotike ishobora gukuraho indwara ziterwa na mikorobe. Antibiyotike ishobora gufasha kuvura no gukumira indwara z'ibikomere.

Uzahura n'imiti yo guhangana n'ububabare buterwa na calciphylaxis cyangwa mu gihe cyo kuvura ibikomere. Inzobere mu kuvura ububabare ishobora gukenerwa niba uhawe imiti igabanya ububabare ya opioid.

Aderesi: 506/507, 1st Main Rd, Murugeshpalya, K R Garden, Bengaluru, Karnataka 560075

Umuhakana: Kanama ni urubuga rw'amakuru y'ubuzima kandi ibisubizo byayo ntibigize inama z'ubuvuzi. Jya ubona umuganga ufite uruhushya rwo gukorera hafi yawe mbere yo gukora impinduka izo ari zo zose.

Yakorewe mu Buhinde, ku isi