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Choroid Plexus Carcinoma ni iki? Ibimenyetso, Intandaro, n'Ubuvuzi

Created at:1/16/2025

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Choroid plexus carcinoma ni uburibwe bwa kanseri bwo mu bwonko buhora gake, bukaba bubaho mu gice cyitwa choroid plexus, ikintu gitunganya amazi yo mu bwonko (cerebrospinal fluid). Aya mazi akora nk'igisubizo cyo kurinda ubwonko n'umugongo, akagenda mu byumba bidasanzwe byitwa ventricles.

Nubwo izina rishobora gutera ubwoba, gusobanukirwa iyi ndwara bishobora kugufasha kumva uriteguye kandi ufite amakuru ahagije. Aya mibiri y'indwara ni gake cyane, ikaba iboneka ku bantu bake cyane, kandi ikunze kugaragara mu bana bato bari munsi y'imyaka 5.

Choroid Plexus Carcinoma ni iki?

Choroid plexus carcinoma ni uburibwe bwa kanseri bukura mu mitsi ya choroid plexus. Tekereza kuri choroid plexus nk'inganda nto, zihariye ziri mu bwonko bwawe zikora amazi yo mu bwonko (cerebrospinal fluid).

Ubu buribwe buri mu itsinda ryitwa choroid plexus tumors, bishobora kuba byiza (bitari kanseri) cyangwa bibi (kanseri). Carcinomas ni ubwoko bubi, bisobanura ko bishobora gukura vuba kandi bikaba byakwirakwira mu bindi bice by'ubwonko cyangwa umugongo.

Ubu buribwe buvangura imikorere isanzwe y'amazi n'imikorere yayo, ibyo bikaba bishobora gutuma amazi yo mu bwonko (cerebrospinal fluid) yiyongera mu bwonko. Iyi ndwara, yitwa hydrocephalus, itera umuvuduko mwinshi mu mutwe kandi itera ibimenyetso byinshi abantu bahura na byo.

Ibimenyetso bya Choroid Plexus Carcinoma ni ibihe?

Ibimenyetso bya choroid plexus carcinoma bigaragara kubera ko ubu buribwe buhagarika imikorere isanzwe y'amazi mu bwonko, bigatera umuvuduko. Kubera ko iyi mibiri y'indwara ikunze kwibasira abana bato n'abana, ibimenyetso bishobora kuba bito mu ntangiriro.

Ibimenyetso bikunze kugaragara ushobora kubona birimo:

  • Umutwe ukura cyane mu bana bato (macrocephaly)
  • Kuruka kenshi, cyane cyane mu gitondo
  • Umutwe ukomeye ukaza uko iminsi igenda
  • Uburakari budasanzwe cyangwa impinduka mu myitwarire
  • Kugira ikibazo cyo kubona umubiri cyangwa kugenda
  • Ibibazo by'amaso cyangwa impinduka mu mikorere y'amaso
  • Imihindagurikire itunguranye
  • Uburwayi cyangwa ubunebwe bwinshi

Mu bana bato, ushobora kandi kubona ibice byoroshye ku mutwe wabo (fontanelles) bivuye hanze cyangwa bikaba bikomeye. Bamwe mu bana bashobora kugira ikibazo cyo konsa cyangwa bagaragara nk'abafite ikibazo kitagaragara.

Ibimenyetso bidafite akamaro ariko bikomeye bishobora kuba harimo intege ku ruhande rumwe rw'umubiri, ibibazo byo kuvuga, cyangwa impinduka mu bwenge. Aya bimenyetso akenshi atangira gahoro gahoro mu byumweru cyangwa amezi uko ubu buribwe bukura kandi umuvuduko ukagenda uzamuka.

Intandaro ya Choroid Plexus Carcinoma ni iyihe?

Intandaro nyayo ya choroid plexus carcinoma ntirazwi neza, ibyo bishobora gutera ikibazo iyo ushaka ibisubizo. Nk'uko bimeze kuri kanseri nyinshi zidafite akamaro, isa nkaho iterwa n'impinduka zidasanzwe muri ADN y'uturemangingo twa choroid plexus.

Ariko kandi, abashakashatsi bamenye bimwe mu bintu by'imiterere y'umuntu bishobora kongera ibyago. Ishusho ikomeye ihuza Li-Fraumeni syndrome, indwara idasanzwe ikomoka ku muryango iterwa n'impinduka muri gene TP53. Imiryango ifite iyi syndrome ifite amahirwe menshi yo kurwara kanseri zitandukanye, harimo choroid plexus carcinomas.

Ubushakashatsi bumwe bugaragaza ko indwara zimwe na zimwe ziterwa na virusi mu gihe cyo gutwita bishobora kugira uruhare, ariko iyi mibanire ntiyemewe neza. Ibintu byo mu kirere ntibyahujwe neza n'iyi mibiri y'indwara, kandi ntibigaragara ko biterwa n'icyo ababyeyi bakoze cyangwa batakoze mu gihe cyo gutwita.

Icy'ingenzi cyo gusobanukirwa ni uko iyi mibiri y'indwara itera wenyine mu bihe byinshi. Ntiterwa n'imikorere y'ubuzima, indyo, cyangwa ibintu byo mu kirere byari byakumirwa.

Ni ryari ukwiye kubona muganga kubera Choroid Plexus Carcinoma?

Ugomba gushaka ubufasha bw'abaganga vuba ubonye ibimenyetso biramba bigaragaza umuvuduko mwinshi mu bwonko, cyane cyane mu bana bato. Izera icyo wumva nk'umubyeyi cyangwa umuntu witaye ku mwana.

Hamagara muganga wawe ako kanya ubonye umutwe ukomeye cyangwa ukomeza kuba mubi, kuruka kenshi, impinduka mu maso, cyangwa imihindagurikire mishya. Mu bana bato, umutwe ukura vuba, ibice byoroshye ku mutwe bivuye hanze, cyangwa impinduka zikomeye mu konsa cyangwa imyitwarire bisaba isuzuma ryihuse.

Ntugatege amatwi niba ibimenyetso bigaragara ko bikomeza kuba bibi mu minsi cyangwa mu byumweru. Nubwo ibimenyetso byinshi bishobora kuba bifite intandaro zidafite akamaro, uburibwe bw'ubwonko busaba isuzuma ryihuse n'ubuvuzi kugira ngo hamenyekane ibyiza.

Niba umwana wawe yavuwe kuri Li-Fraumeni syndrome cyangwa afite amateka y'iyi ndwara mu muryango, banira hamwe n'itsinda ry'ubuvuzi kugira ngo umenye uko wakorwa isuzuma buri gihe. Kumenya hakiri kare bishobora kugira uruhare rukomeye mu gutsinda ubuvuzi.

Ibyago bya Choroid Plexus Carcinoma ni ibihe?

Ibyago bya choroid plexus carcinoma ni bike cyane, ibyo bigaragaza uko iyi mibiri y'indwara idasanzwe kandi idateganijwe. Gusobanukirwa ibi bintu bishobora kugufasha gushyira ibintu byawe mu buryo.

Ibyago by'ingenzi birimo:

  • Ubwana, cyane cyane kuba munsi y'imyaka 5
  • Kugira Li-Fraumeni syndrome cyangwa impinduka muri gene TP53
  • Amateka y'umuryango wa Li-Fraumeni syndrome
  • Kuba warashyizweho imirasire mu mutwe (bihora gake cyane)

Imyaka ni yo ntandaro ikomeye, hafi 70% y'iyi mibiri y'indwara iboneka mu bana bari munsi y'imyaka 2. Ibyago bigabanuka cyane nyuma y'imyaka 5, kandi iyi mibiri y'indwara ni gake cyane mu bakuru.

Ibintu by'imiterere y'umuntu, nubwo ari ingenzi iyo bihari, bigira uruhare ruto mu bintu. Abana benshi barwara choroid plexus carcinoma nta byago bizwi bafite, ibyo bivuze ko iyi mibiri y'indwara ikunze kubaho uko byagenda kose.

Ingaruka zishoboka za Choroid Plexus Carcinoma ni izihe?

Ingaruka za choroid plexus carcinoma zigaragara ahanini ziterwa n'umuvuduko mwinshi mu bwonko n'aho ubu buribwe buherereye hafi y'ibice by'ingenzi. Gusobanukirwa ibi bishoboka bishobora kugufasha kwitegura ibyo bizaba.

Ingaruka za hafi zirimo:

  • Hydrocephalus isaba kuvurwa n'ubuganga
  • Ibibazo by'amaso cyangwa ubuhumyi buterwa n'umuvuduko ku mitsi y'amaso
  • Gutinda mu iterambere mu bana bato
  • Imihindagurikire ishobora gukomeza nyuma yo kuvurwa
  • Intege cyangwa ubumuga buterwa n'umuvuduko ku bice by'umubiri bigenzura imikorere
  • Kubura kumva guturuka ku muvuduko ku nzira zumva

Ingaruka z'igihe kirekire zishobora kuba zirimo ingaruka ku bwenge, cyane cyane mu bana bato ubwonko bwabo bugikura. Bamwe mu bana bashobora kugira ibibazo byo kwiga, ibibazo byo kwibuka, cyangwa gutinda kugera ku ntambwe z'iterambere.

Ingaruka ziterwa n'ubuvuzi nazo zishoboka, harimo ingaruka ziterwa n'ubuganga, imiti yo kurwanya kanseri, cyangwa imirasire. Ariko kandi, itsinda ryawe ry'ubuvuzi rizaharanira kugabanya ibi byago mu gihe kivura neza ubu buribwe.

Choroid Plexus Carcinoma imenyekanwa gute?

Kumenya choroid plexus carcinoma bisaba intambwe nyinshi, bitangirira ku mateka y'ubuzima n'isuzuma rusange. Muganga azakubaza ibimenyetso kandi ashobora gukora ibizamini by'ubwonko kugira ngo arebe imikorere y'imitsi, uburyo bwo guhuza ibintu, n'imikorere y'ubwonko.

Igikoresho cy'ingenzi cyo gupima ni magnetic resonance imaging (MRI) y'ubwonko. Iyi shusho igaragaza ubunini bw'uburibwe, aho buherereye, n'aho buhuriye n'ibice by'ubwonko biri hafi. MRI ifasha kandi kumenya hydrocephalus no gutegura uburyo bwo kuvura.

Computed tomography (CT) scan ishobora gukoreshwa mu ntangiriro, cyane cyane mu bihe by'amahirwe make, ariko MRI itanga amakuru arambuye. Muganga wawe ashobora kandi gutegeka MRI y'umugongo kugira ngo arebe niba ubu buribwe bwakwirakwiriye.

Kumenya neza uburibwe bisaba igice cy'umubiri, akenshi gifatwa mu gihe cy'ubuganga bwo gukuraho ubu buribwe. Umuganga areba iyi mitsi munsi ya mikoroskopi kugira ngo yemeze uburibwe kandi amenye imico y'uburibwe.

Ibizamini byongeyeho bishobora kuba harimo ibizamini by'imiterere y'umuntu kugira ngo barebe Li-Fraumeni syndrome, cyane cyane niba hari amateka y'umuryango wa kanseri. Isuzuma ry'amazi yo mu bwonko (cerebrospinal fluid) rishobora kandi gukorwa kugira ngo harebwe imisemburo y'uburibwe.

Ubuvuzi bwa Choroid Plexus Carcinoma ni buhe?

Ubuvuzi bwa choroid plexus carcinoma busanzwe burimo ubufatanye bw'abaganga, buhuza ubuganga, imiti yo kurwanya kanseri, rimwe na rimwe imirasire. Igishushanyo cyihariye gishingira ku myaka y'umwana, ubunini n'aho ubu buribwe buherereye, niba bwakwirakwiriye.

Ubuganga busanzwe ari bwo bwa mbere, bugamije gukuraho ubu buribwe bwinshi uko bishoboka. Gukuraho byose bitanga amahirwe meza yo gukira, nubwo atari byo bishoboka buri gihe kubera aho ubu buribwe buherereye hafi y'ibice by'ingenzi by'ubwonko.

Imiti yo kurwanya kanseri ikurikira ubuganga mu bihe byinshi, ikoresha imiti igabanya imisemburo ya kanseri mu mubiri wose. Imiti n'igihe cyayo biterwa n'ibintu nk'imyaka y'umwana wawe n'ubunini bw'uburibwe bwakuweho mu gihe cy'ubuganga.

Imirasire ishobora gusabwa ku bana bakuru, akenshi abarengeje imyaka 3, cyane cyane niba ubu buribwe budashobora gukurwaho rwose. Ariko kandi, imirasire ikunze kwirindwa mu bana bato cyane kubera ingaruka zishobora kuba ku bwonko bugikura.

Niba hydrocephalus ibayeho, umwana wawe ashobora gukenera shunt, igikoresho gito gikuye amazi yo mu bwonko (cerebrospinal fluid) mu bwonko ajya mu bindi bice by'umubiri. Iyi nzira ishobora gufasha guhita ikemura ibimenyetso biterwa n'umuvuduko mwinshi mu bwonko.

Uko wakwita ku mwana wawe mu rugo mu gihe cy'ubuvuzi

Kwita ku mwana mu rugo mu gihe cy'ubuvuzi bisaba kwihangana, gutegura, no kuvugana neza n'itsinda ry'ubuvuzi. Kurema ibidukikije byiza bishobora gufasha umwana wawe guhangana n'ibibazo by'ubuvuzi.

Fata umwanya wo gukomeza gahunda uko bishoboka kose mu gihe uhindagurika iyo ingaruka z'ubuvuzi zibangamye. Kora dosiye y'ibimenyetso, imiti, n'impinduka ubonye, kuko ayo makuru afasha itsinda ryawe ry'ubuvuzi guhindura ubuvuzi uko bikenewe.

Ibiryo biba ingenzi cyane mu gihe cy'ubuvuzi. Korera hamwe n'umuganga w'ibiryo kugira ngo umenye neza ko umwana wawe abona ibiryo n'ibintu bihagije, nubwo adafite ubushake bwo kurya. Ibiryo bike, bikunze kuba byiza kuruta ibiryo byinshi.

Kora isuzuma ry'ibimenyetso by'indwara, nko guhindagurika, umunaniro udakunze kubaho, cyangwa impinduka mu myitwarire, kubera ko imiti yo kurwanya kanseri ishobora kugabanya ubudahangarwa bw'umubiri. Hamagara itsinda ryawe ry'ubuvuzi vuba ubonye ibimenyetso bibangamye.

Ntiwibagirwe kwita kuri wowe n'abandi bantu bo mu muryango muri iki gihe gikomeye. Emerera ubufasha bw'inshuti n'umuryango, kandi utekereze ku guhuza n'amatsinda y'ubufasha cyangwa serivisi zo kugisha inama.

Uko wakwitegura gusura muganga

Kwitegura gusura muganga bishobora kugufasha gukoresha neza igihe cyawe hamwe n'itsinda ry'ubuvuzi kandi bikaba byiza kubaza ibibazo by'ingenzi. Tangira wandike ibimenyetso byose wabonye, harimo igihe byatangiye n'uko byahindutse.

Zana urutonde rw'imiti yose, ibintu byongera imbaraga, n'ubuvuzi umwana wawe ahabwa ubu. Harimo umunaniro n'igihe, kuko ayo makuru afasha abaganga kwirinda ibintu bishobora kubangamira.

Tegura ibibazo byawe mbere, ubanza ku bibazo by'ingenzi. Tekereza ku kubaza ibyerekeye uburyo bwo kuvura, ibyitezwe, ingaruka zishoboka, n'uko wakwita ku bimenyetso mu rugo.

Zana umuntu wo mu muryango cyangwa inshuti yizewe mu gihe cy'ibikorwa. Bashobora gufasha kwibuka amakuru yavuzwe no gutanga ubufasha mu gihe cy'ibiganiro bikomeye.

Ntuzuyaze gusaba amakuru yandikiwe cyangwa ibikoresho byerekeye uburwayi bw'umwana wawe. Imiryango myinshi isanga ari byiza kwandika ibice by'ingenzi by'ikiganiro (wemererwa) kugira ngo usubiremo nyuma.

Icy'ingenzi cyo kumenya kuri Choroid Plexus Carcinoma

Choroid plexus carcinoma ni uburibwe bwa kanseri bwo mu bwonko buhora gake ariko bukaba bukomeye, bukaba bubasira abana bato. Nubwo kumenya ubu burwayi bishobora gutera ubwoba, iterambere mu buvuzi ryongereye cyane ibyiza ku bana benshi barwaye iyi ndwara.

Kumenya ibimenyetso hakiri kare no gushaka ubufasha bw'abaganga vuba ni ingenzi kugira ngo hamenyekane ibyiza. Guhuza ubuganga, imiti yo kurwanya kanseri, n'ubuvuzi bwo gufasha bitanga ibyiringiro ku miryango myinshi ihanganye n'iyi ndwara.

Wibuke ko ubuzima bwa buri mwana ari bwite, kandi itsinda ryawe ry'ubuvuzi rizakorana nawe kugira ngo ritegure gahunda y'ubuvuzi ikwiye. Ntuzuyaze kubaza ibibazo, gushaka ibindi byifuzo, cyangwa gusaba ubufasha bundi igihe ubikeneye.

Nubwo urugendo ruzaba imbere rushobora kuba rugoranye, nturi kururwana wenyine. Ibigo by'ubuvuzi bw'abana bifite uburambe mu kuvura iyi mibiri y'indwara idasanzwe no gufasha imiryango mu nzira yose.

Ibibazo Bikunze Kubahwa kuri Choroid Plexus Carcinoma

Q.1 Choroid plexus carcinoma ihora gake gute?

Choroid plexus carcinoma ihora gake cyane, ikaba iboneka ku bantu bake cyane. Igira uruhare ruto cyane mu buribwe bw'ubwonko bwose n'ubwo mu bana. Ibihe byinshi bibaho mu bana bari munsi y'imyaka 5, aho bibaho cyane mu bana bari munsi y'imyaka 2.

Q.2 Ni ayahe mahirwe yo kubaho nyuma ya choroid plexus carcinoma?

Amahirwe yo kubaho atandukanye cyane bitewe n'ibintu nk'imyaka y'umwana, uko ubu buribwe bwakuweho, n'uko bwakiriwe mu buvuzi. Muri rusange, amahirwe yo kubaho mu myaka 5 ari hagati ya 40-70%, aho ibyiza bibaho iyo ubu buribwe bushobora gukurwaho rwose. Abana bavuwe bakiri bato n'abafite ubu buribwe bwakuweho rwose bagira amahirwe meza.

Q.3 Choroid plexus carcinoma ishobora gukwirakwira mu bindi bice by'umubiri?

Choroid plexus carcinoma ishobora gukwirakwira mu mikorere y'ubwonko n'umugongo binyuze mu nzira z'amazi yo mu bwonko, bikaba bishobora kugira ingaruka ku bindi bice by'ubwonko cyangwa umugongo. Ariko kandi, gukwirakwira hanze y'imikorere y'ubwonko ku bindi bice by'umubiri ni gake cyane. Niyo mpamvu abaganga bakora isuzuma ry'umugongo na MRI kandi bashobora gusesengura amazi yo mu bwonko mu gihe cyo gupima.

Q.4 Umwana wanjye azagira ingaruka z'igihe kirekire nyuma yo kuvurwa?

Ingaruka z'igihe kirekire ziterwa n'ibintu bitandukanye birimo aho ubu buribwe buherereye, ubukana bw'ubuvuzi, n'imyaka y'umwana mu gihe cyo kuvurwa. Bamwe mu bana bagira impinduka mu bwenge, ibibazo byo kwiga, cyangwa gutinda mu iterambere, abandi bakira neza. Gukurikirana buri gihe hamwe n'inzobere bifasha gukurikirana iterambere no gutanga ubufasha hakiri kare igihe bikenewe.

Q.5 Choroid plexus carcinoma ikomoka mu muryango?

Ibihe byinshi bya choroid plexus carcinoma bibaho uko byagenda kose kandi ntibikomoka mu muryango. Ariko kandi, hafi 10-15% by'ibihe bihujwe na Li-Fraumeni syndrome, indwara ikomoka mu muryango iterwa n'impinduka muri gene TP53. Niba umwana wawe yavuwe kuri ubu buribwe, kugisha inama ku miterere y'umuryango bishobora gusabwa kugira ngo harebwe ibyago by'umuryango.

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