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Henoch-Schonlein Purpura

Incamake

Henoch-Schönlein purpura (izwi kandi nka IgA vasculitis) ni indwara itera uburibwe n'imvura mu mitsi mito y'amaraso yo ku ruhu, mu bice by'ingingo, mu mara no mu mpyiko.

Ibimenyetso

Ibiranga by'ingenzi bine bya Henoch-Schonlein purpura birimo:

  • Ukwishima (purpura). Imicanga y'umutuku-umwijima isa n'ibikomere bigaragara ku matama, amaguru n'ibirenge. Ukwishima gushobora kandi kugaragara ku maboko, mu maso no ku mubiri, kandi bishobora kuba bibi cyane mu bice by'umubiri byashyizweho igitutu, nko ku mutwe w'isogisi n'umukandara.
  • Ibihombo, imvune z'ingingo (arthritis). Abantu bafite Henoch-Schonlein purpura bakunze kugira ububabare n'ubwuzu buremereye mu ngingo - ahanini mu mavi no mu birenge. Ububabare bw'ingingo rimwe na rimwe buza imbere y'ubukonje busanzwe mu cyumweru kimwe cyangwa bibiri. Ibi bimenyetso biracika iyo indwara irangiye kandi ntibisiga ibibazo by'igihe kirekire.
  • Ibimenyetso by'ubuhumekero. Abana benshi bafite Henoch-Schonlein purpura bagira ububabare mu nda, isereri, kuruka n'amatembabuzi avuyemo amaraso. Aya bimenyetso rimwe na rimwe aba mbere y'uko ubukonje bugaragara.
  • Ingaruka ku mpyiko. Henoch-Schonlein purpura ishobora kandi kugira ingaruka ku mpyiko. Mu bihe byinshi, ibi bigaragara nk'amaprotéine cyangwa amaraso mu mpiswi, ibyo ushobora kutamenya keretse ukoze isuzuma ry'impiswi. Ubusanzwe ibi biracika iyo indwara irangiye, ariko bamwe bagira indwara y'impyiko idakira.
Impamvu

Mu gisebe cya Henoch-Schonlein, imiyoboro y'amaraso mito yo mu mubiri irakabakaba, ibyo bikaba bishobora gutera kuva amaraso ku ruhu, mu nda no mu mpyiko. Ntabwo birasobanutse icyateye ubwo kubabara kwambere. Bishobora kuba ari ibyavuye ku buryo bw'umubiri bwo kurwanya indwara budakwiye ku bintu bimwe na bimwe.

Abantu hafi kimwe cya kabiri bafite igisebe cya Henoch-Schonlein baragize icyo gisebe nyuma y'indwara y'ubuhumekero bwo hejuru, nko gukonja. Ibindi bintu bikurura icyo gisebe harimo ibicurane, uburwayi bwa strep, igicurane cy'impiswi, indwara y'umwijima, imiti imwe n'imwe, ibiryo, ukururwa n'udukoko no kwibasirwa n'ubukonje bukabije.

Ingaruka zishobora guteza

Ibintu byongera ibyago byo kwandura Henoch-Schonlein purpura birimo:

  • Imyaka. Indwara ikunda kwibasira abana bari munsi y'imyaka 10.
  • Ibitsina. Henoch-Schonlein purpura ikunda kugaragara mu bahungu kurusha abakobwa.
  • Ubwoko. Abana b'abazungu n'ab'Abayasiya bafite ibyago byinshi byo kwandura Henoch-Schonlein purpura kurusha abana b'Abirabura.
Ingaruka

Kuri benshi, ibimenyetso birakira mu gihe cy'ukwezi, nta kibazo gihoraho gisigara. Ariko gusubira kwaduka ni kenshi.

Ingaruka ziterwa na Henoch-Schonlein purpura zirimo:

  • Akagirire k'impyiko. Ingaruka ikomeye ya Henoch-Schonlein purpura ni ukwangirika kw'impyiko. Iyi kamere ikabije mu bakuru kurusha abana. Rimwe na rimwe akagirire kaba kabi cyane ku buryo hakenewe imiti igabanya uburozi mu maraso cyangwa gutera impyiko.
  • Kubera imbogamizi mu mara. Mu bihe bitoroshye, Henoch-Schonlein purpura ishobora gutera intussusception - uburwayi aho igice cy'umura gifata ikindi nk'ikinyabiziga, bigatuma ibintu bidakora neza mu mara.
Kupima

Muganga wawe azashobora kumenya neza ko ufite indwara ya Henoch-Schonlein purpura niba ufite ibimenyetso bisanzwe byayo, birimo ubusembwa, ububabare bw'ingingo n'ibibazo byo mu mara. Niba kimwe muri ibi bimenyetso cyabuze, muganga wawe ashobora kugusaba gukora ibizamini bimwe cyangwa byinshi bikurikira.

Nta kizami cy'ubuvuzi cyonyine gishobora kwemeza ko ufite indwara ya Henoch-Schonlein purpura, ariko ibizamini bimwe na bimwe bishobora kugufasha gukuraho izindi ndwara kandi bigatuma ukekwaho kuba ufite iyo ndwara. Ibyo bizamini bishobora kuba ibi bikurikira:

Abantu bafite indwara ya Henoch-Schonlein purpura bakunze kugira imyanda ya poroteyine runaka, IgA (immunoglobulin A), ku mubiri wabo ubangamiwe. Muganga wawe ashobora gufata igice gito cy'uruhu kugira ngo gipimwe muri laboratwari. Mu gihe impyiko zangiritse cyane, muganga wawe ashobora kugusaba gukora biopsie y'impyiko kugira ngo afashe mu gufata ibyemezo byo kuvura.

Muganga wawe ashobora kugusaba gukora ultrasound kugira ngo akureho izindi mpamvu zishobora gutera ububabare mu nda no kugenzura ibibazo bishobora kuvuka, nko gufungana kw'amara.

  • Ibizamini by'amaraso. Amaraso yawe ashobora gupimwa niba ubuvuzi bwawe budasobanutse hashingiwe ku bimenyetso byawe.
  • Ibizamini by'inkari. Inkari zawe zishobora gupimwa kugira ngo harebwe niba hari amaraso, poroteyine cyangwa ibindi bintu bidasanzwe kugira ngo hamenyekane niba impyiko zawe zikora neza.
Uburyo bwo kuvura

Igisebe cya Henoch-Schonlein gikira kigacika ukundi mu gihe kitarenze ukwezi, nta ngaruka zikomeye zigisigaye. Kuruhuka, kunywa amazi ahagije no gufata imiti igabanya ububabare iboneka mu maduka bishobora gufasha mu kurwanya ibimenyetso. 

Corticosteroids, nka prednisone, bishobora gufasha kugabanya igihe n'uburemere bw'ububabare bw'ingingo n'ubwo mu nda. Kubera ko iyi miti ishobora kugira ingaruka mbi zikomeye, gabagisha muganga ibyiza n'ibibi byo kuyikoresha.

Niba igice cy'umwijima cyiyunganiyeho cyangwa gikomerekeye, hari ubwo hakenerwa kubagwa.

Kwitaho

Kwita ku muntu murugo byibanda ku gutuma umuntu ufite indwara ya Henoch-Schonlein purpura ya make iruhura mu gihe iyi ndwara ikomeza. Kuruhuka, kunywa amazi ahagije no gufata imiti igabanya ububabare iboneka mu maduka bishobora gufasha.

Kwitegura guhura na muganga

Uzabanza kubonana na muganga wawe usanzwe cyangwa umuganga wita ku bana (pédiatre) kubera iyi ndwara. Nyuma yaho, ushobora koherezwa kwa muganga wita ku ndwara z'impyiko (nephrologue) niba hari ibibazo by'impyiko bigaragara. Dore amakuru ashobora kugufasha kwitegura igihe cy'isuzumwa ryawe.

Mbere y'isuzumwa ryawe, andika ibisubizo by'ibi bibazo bikurikira:

Ibibazo ushobora kwibaza muganga wawe birimo:

Muganga wawe arashobora kugusaba ibibazo byinshi, nka:

  • Ibimenyetso byatangiye ryari?

  • Byaje bitunguranye cyangwa buhoro buhoro?

  • Umuntu ufite ibicurane (wowe cyangwa umwana wawe) yari arwaye mbere y'uko ibicurane bitangira?

  • Ni imiti iyihe n'ibindi byongerwamo umuntu ufite ibicurane afata buri gihe?

  • Ni iki gishobora kuba cyateye ibi bimenyetso?

  • Ni ibizamini ibihe bikenewe kugira ngo hamenyekane neza indwara?

  • Iyi ndwara ni iy'igihe gito cyangwa iramara igihe kirekire?

  • Nzabimenya bite niba hari ikibazo cy'impyiko? Byagenda bite niba byagaragaye nyuma?

  • Henoch-Schonlein purpura ivurwa gute?

  • Ingaruka mbi z'ubuvuzi ni izihe?

  • Ufite ibitabo ku iyi ndwara? Ushobora kutugira inama y'urubuga rwa interineti aho twasoma byinshi?

  • Ibicurane byari bimeze bite igihe byatangiraga?

  • Ibicurane birababaza? Biraryarya?

  • Umuntu ufite ibicurane afite ibindi bimenyetso, nko kubabara mu nda cyangwa mu ngingo?

Aderesi: 506/507, 1st Main Rd, Murugeshpalya, K R Garden, Bengaluru, Karnataka 560075

Umuhakana: Kanama ni urubuga rw'amakuru y'ubuzima kandi ibisubizo byayo ntibigize inama z'ubuvuzi. Jya ubona umuganga ufite uruhushya rwo gukorera hafi yawe mbere yo gukora impinduka izo ari zo zose.

Yakorewe mu Buhinde, ku isi