Created at:1/16/2025
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Neuroblastoma ni ubwoko bwa kanseri itera mu uturemangingo tudakomeye tw’imiterere y’ubwonko twitwa neuroblasts. Aya turemangingo agomba gukura akaba uturemangingo tw’imiterere y’ubwonko dusanzwe, ariko muri neuroblastoma, akura birenze urugero maze akaba imikaya.
Iyi kanseri igaragara hafi ya gusa ku bana, aho ingero nyinshi zigaragara mbere y’imyaka 5. Nubwo ijambo “kanseri” rishobora gutera ubwoba, ni ingenzi kumenya ko abana benshi barwaye neuroblastoma bagira ubuvuzi bwiza, cyane cyane iyo imenyekanye hakiri kare.
Ibimenyetso bya neuroblastoma bishobora gutandukana cyane bitewe n’aho ikibyimba gikura n’ubunini bwacyo. Kubera ko iyi kanseri ishobora gutera ahantu hatandukanye mu mubiri w’umwana wawe, ibimenyetso bishobora kugaragara bitari bifitanye isano mu ntangiro.
Dore ibimenyetso ushobora kubona, byashyizwe hamwe bitewe n’aho bigaragara:
Ibimenyetso rusange bigira ingaruka ku mubiri wose:
Ibimenyetso byo mu nda (kubera ko imikaya myinshi itangirira mu gice cy’inda):
Ibimenyetso bifitanye isano n’ibituza:
Ibimenyetso bidakunze kugaragara ariko by’ingenzi byo kwitondera:
Ibi bimenyetso bishobora kuza buhoro buhoro mu byumweru cyangwa amezi. Byinshi muri ibi bimenyetso bishobora guterwa n’indwara zisanzwe z’abana, nuko rero ntukagire impungenge niba ubona kimwe cyangwa bibiri. Ariko rero, niba ibindi bimenyetso byinshi bigaragara rimwe cyangwa bikomeza nubwo waba warafashe imiti, byaba byiza kubiganiraho na muganga w’abana.
Abaganga basobanura neuroblastoma mu buryo butandukanye kugira ngo bafashe mu gupima uburyo bwiza bwo kuvura. Uburyo nyamukuru babikoraho ni ukureba urwego rw’ubukaka, ibyo bigafasha kumenya uko kanseri ishobora kwitwara.
Ukurikije urwego rw’ubukaka:
Ukurikije aho ziba mu mubiri:
Itsinda ry’abaganga bita ku mwana wawe rizakoresha ubwo bwoko bw’indwara hamwe n’ibindi bintu nka kuba umwana afite imyaka ingahe n’imiterere yihariye y’igituntu kugira ngo bagire gahunda y’ubuvuzi iboneye. Buri bwoko bw’indwara bugira uburyo bwihariye bwo kuvurwa, niyo mpamvu ubu buryo bwo gukora ubwoko bw’indwara ari ingirakamaro cyane.
Icyateye neuroblastoma ntikirasobanuwe neza, ariko abashakashatsi bizera ko bibaho iyo hari ikintu kidakora neza mu gihe cy’iterambere ry’umwana uri mu nda. Mu gihe cyo gutwita, utunyangingo twihariye twitwa neural crest cells bigomba guhinduka utunyangingo tw’imitsi dukuru, ariko rimwe na rimwe uwo mucyo nturangira neza.
Urugero rwinshi rwa neuroblastoma rubaho ku buryo butunguranye, bisobanura ko nta kintu ababyeyi bakoze cyangwa batakoze cyabiteye. Ibi bita kanseri “ya hato na hato”, kandi bigize hafi 98% by’ibibazo byose bya neuroblastoma.
Mu bihe bitoroshye (hafi 1-2% by’igihe), neuroblastoma ishobora kuvanwa mu miryango, bisobanura ko iherwa mu miryango. Ibi bibaho iyo hari impinduka mu mimerere y’imisemburo igenzura uko utunyangingo tw’imitsi dukura. Imiryango ifite neuroblastoma iherwa mu miryango ikunda kugira abantu benshi bo mu muryango barwaye kandi bashobora kurwara iyo kanseri bakiri bato.
Bimwe mu bintu abashakashatsi bari gukoraho ubushakashatsi birimo kwibasirwa na chimique zimwe na zimwe mu gihe cyo gutwita, ariko nta mpamvu z’ibidukikije zizewe ziramenyekana. Ikintu gikomeye cyo gusobanukirwa ni uko neuroblastoma iterwa n’ikintu udashobora gukumira cyangwa kugenzura.
Wagomba kuvugana na muganga wita ku mwana wawe niba ubona ibimenyetso byavuzwe haruguru, cyane cyane niba bikomeje ibyumweru birenga kimwe cyangwa bibiri. Nubwo ibimenyetso byinshi muri ibyo bikunze guterwa n’indwara zisanzwe z’abana, bihora byiza kubigenzura.
Shaka ubuvuzi vuba niba umwana wawe afite:
Gira icyizere icyo umutima wawe nk’umubyeyi ukubwira. Niba hari ikintu kidasanzwe ku buzima bw’umwana wawe cyangwa imyitwarire ye, ntutinye guhamagara muganga wawe. Abaganga bita ku bana bamenyereye ababyeyi bafite impungenge kandi bakunda cyane gusuzuma ikintu kigaragara nk’icya make kuruta gutakaza ikintu gikomeye.
Kumenya hakiri kare bishobora gutuma habaho itandukaniro rikomeye mu buryo bw’ivura, bityo kuba maso ku mpinduka z’ubuzima bw’umwana wawe ni kimwe mu bintu by’agaciro cyane ushobora gukora.
Bitandukanye na kanseri nyinshi z’abantu bakuru, neuroblastoma ntabwo ifite ibintu byinshi byongera ibyago ababyeyi bashobora kugenzura. Abana benshi barwara iyi kanseri nta bintu byongera ibyago bizwi na gato.
Ibintu by’ingenzi byongera ibyago abaganga bamenye harimo:
Imyaka: Iki nicyo kintu cy’ingenzi cyongera ibyago. Hafi 90% by’ababana na neuroblastoma ni abana bari munsi y’imyaka 5, aho ibyago byinshi biri mu mwaka wa mbere w’ubuzima. Ibyago bigabanuka cyane uko abana bakura.
Igitsina: Abahungu bafite ibyago byinshi byo kurwara neuroblastoma kuruta abakobwa, ariko itandukaniro ni rito.
Amateka y’umuryango: Mu bihe bitoroshye cyane (1-2% by’ibintu byose), neuroblastoma ishobora kuba mu miryango. Abana bafite umubyeyi cyangwa umuvandimwe warwaye neuroblastoma bafite ibyago byinshi, ariko ibi bigize igice gito cyane cy’ibintu.
Indwara z’imiterere: Indwara zimwe na zimwe z’imiterere zishobora kongera ibyago gato, ariko izo ndwara ubwazo ni nke cyane.
Birakomeye gusobanukirwa ko abana benshi bafite neuroblastoma badafite ibyo bibazo by’ubuzima. Kanseri isanzwe itera mu buryo butunguranye mu gihe cy’intangiriro z’umwana, kandi nta kintu ababyeyi bashoboraga gukora kugira ngo bayikumire. Ntabwo iterwa n’imirire, imibereho, cyangwa ibintu byo mu kirere wamenya.
Ibibazo bituruka kuri neuroblastoma bishobora guterwa n’ubundi buganga ubwawo cyangwa uburyo bwo kuvura. Gusobanukirwa ibyo bishoboka bishobora kugufasha kumenya icyo ugomba kwitondera no kumva witeguye urugendo rwo kwita ku mwana wawe.
Ibibazo bituruka ku buganga:
Ibibazo bijyanye no kuvura:
Nubwo uru rutonde rushobora kugaragara nk'uruhariye, ibuka ko itsinda ry’abaganga bita ku mwana wawe rifite ubunararibonye mu gukumira no guhangana n'ibibazo nk'ibi. Abana benshi baranyura mu buvuzi batagize ibibazo bikomeye, kandi abagize ibibazo bakunda gukira neza bafashijwe n'ubuvuzi bukwiye.
Uburyo bwa none bwo kuvura bwagenewe kuba bufite ingaruka nziza uko bishoboka kose mu gihe bigabanya ibyago. Itsinda ry’abaganga bawe rizajya rikurikirana umwana wawe hafi mu gihe cyose cy'ubuvuzi kugira ngo bamenye kandi bakemure ibibazo byose hakiri kare.
Kumenya neuroblastoma bisaba intambwe nyinshi, kandi itsinda ry’abaganga bita ku mwana wawe rizajya rikora gahunda kugira ngo babone ishusho yuzuye. Uyu muhanda ubusanzwe utangira ku isuzuma ry’umuganga wawe, hanyuma ukajya ku bipimo byihariye.
Isuzuma rya mbere:
Muganga wawe azatangira akuzuye isuzuma ry’umubiri, akareba niba hari ibintu byavuze cyangwa byabumbabumbanye, cyane cyane mu nda. Azabaza ibibazo birambuye ku birebana n'ibimenyetso by'umwana wawe n'igihe byatangiye.
Ibizamini byo kubona amashusho:
Ibizamini bya Laboratwari:
Biopsie y'umubiri:
Kugira ngo hamenyekane neza icyo ari cyo, birakenewe gusuzuma umutwe w'igiturika hakoreshejwe microscope. Ibi bikorwa hakoreshejwe uburyo buto bwo kubaga kugira ngo hakurweho igice cy'igiturika.
Uburyo bwose bwo gupima busaba iminsi myinshi cyangwa ibyumweru bike. Mu gihe utegereje ibisubizo bishobora gutera umunaniro, ariko isuzuma rihamye rifasha guha umwana wawe ubuvuzi bukwiye ku kibazo cye.
Ubuvuzi bwa neuroblastoma bugengwa n'imyaka y'umwana, imiterere y'igiturika, n'aho cyageze. Inkuru nziza ni uko uburyo bwo kuvura bwarushijeho kuba bwiza mu myaka yashize, kandi abana benshi barwaye neuroblastoma bakomeza kubaho ubuzima bwiza kandi busanzwe.
Kubaga:
Kubaga kenshi ni bwo buvuzi bwa mbere, cyane cyane ku mitwe itararakwirakwira. Intego ni ukukuraho igiturika cyose uko bishoboka kose, ukarinda imyanya y'imbere n'ibindi bice. Rimwe na rimwe, gukuraho byose ntibishoboka, kubaga bishobora gukorwa nyuma y'andi mavuriro agabanya igiturika.
Chimiothérapie:
Aya ni imiti ikomeye igabanya uturemangingo twa kanseri mu mubiri wose. Umwana wawe ashobora guhabwa imiti itandukanye ya chimiothérapie mu gihe cy'amezi. Ubuvuzi buhabwa hakoreshejwe umurongo wa centrale (IV idasanzwe) kugira ngo birusheho koroherwa.
Radiothérapie:
Imiterere y'ingufu nyinshi ikoreshwa mu kurimbura uturemangingo twa kanseri mu bice bimwe na bimwe. Ubu buvuzi butegurwa neza kugira ngo bugere ku gice cy'igiturika, ukarinda imyanya myiza. Abana bose barwaye neuroblastoma ntibakenera radiothérapie.
Gusimbuza uturemangingo:
Ku bimenyetso bifite ibyago byinshi, abaganga bashobora kugusaba gukusanya uturemangingo twiza tw'umwana wawe mbere yo guha doze nyinshi za chimiothérapie, hanyuma ugasubiza uturemangingo kugira ngo ufashe kongera ubudahangarwa bw'umubiri.
Immunothérapie:
Iyi miti mishya ifasha ubudahangarwa bw’umwana wawe kumenya no kurwanya ibishegesho bya kanseri neza. Ibyo byabaye igice cy’ingenzi cyo kuvura abana benshi barwaye neuroblastoma.
Ubuvuzi bugamije:
Aya miti agerwa ku bintu byihariye by’ibishegesho bya kanseri, asize utundi turemangingo tudakozweho.
Ubuvuzi busanzwe buramara amezi 12-18, nubwo ibi bihinduka cyane. Itsinda ry’abaganga bavura kanseri bazategura gahunda y’ubuvuzi ihamye kandi bayihindura uko bikenewe bitewe n’uko umwana wawe asubiza.
Kwita ku mwana wawe mu rugo mu gihe cyo kuvurwa neuroblastoma bisobanura gucunga ibintu by’umubiri n’iby’amarangamutima mu rugendo rwe. Ikipe yawe y’abaganga izakugira inama zihariye, ariko hano hari amabwiriza rusange ashobora kugufasha.
Gucunga ingaruka mbi z’ubuvuzi:
Kumenya ibibazo:
Andika buri munsi ubushyuhe bw’umwana wawe, uburyo arya, n’ingufu afite. Hamagara ikipe yawe y’abaganga ako kanya niba ubona umuriro, ibimenyetso by’ubwandu, kuva amaraso bidasanzwe, cyangwa isereri n’kuruka bikabije.
Inkunga yo mu mutwe:
Mugumuke ku rugero rushoboka rwose mu buzima busanzwe bw'umwana wawe. Komeza ibikorwa akunda iyo yumva ameze neza. Amavuriro menshi afite abahanga mu buzima bw'abana bashobora gutanga ubufasha mu gufasha abana guhangana n'ubuvuzi.
Ishuri n'imibanire y'abantu:
Korana n'ishuri ry'umwana wawe kugira ngo mutegure gukomeza amasomo mu gihe cy'ubuvuzi. Abana benshi bashobora gukomeza amasomo amwe mu rugo cyangwa bagasubira ku ishuri hagati y'igihe cy'ubuvuzi.
Zirikana ko ugomba gucunga byose wenyine. Ikipe yawe y'abaganga, abakozi b'imibereho myiza, n'andi miryango ica mu bihe nk'ibyo bashobora gutanga inkunga ikomeye n'inama zifatika.
Gutegura neza igihe ugiye kwa muganga bishobora kugufasha gukoresha neza igihe cyawe n'ikipe y'abaganga yita ku mwana wawe kandi bikakwemerera kubona amakuru yose ukeneye. Dore uko wakwitegura igihe ugiye gusuzumwa bwa mbere n'igihe ugiye gukurikiranwa.
Mbere y'igihe ugiye kwa muganga:
Ibibazo ushobora kwibaza:
Mu gihe uri kwa muganga:
Ntukaze kugira ikibazo niba hari ikintu kitumvikana. Fata inyandiko cyangwa ubaze niba ushobora gufata amashusho y’ibice by’ingenzi by’ikiganiro. Menya neza ko ubumva intambwe zikurikira mbere yo kugenda.
Icyo wakwizana:
Zana amakarita yawe y’ubwisungane, urutonde rw’imiti ukoresha ubu, ibintu bishimisha umwana wawe, ibyokurya, n’ibintu bimushimisha mu gihe cy’ibyumba bishobora kumara igihe kirekire.
Wibuke ko itsinda ryanyu ry’abaganga rishaka gukorana nawe mu kwita ku mwana wawe. Biteze ibibazo kandi bashaka ko wumva uhawe amakuru kandi ufite icyizere cy’uburyo bwo kuvura.
Neuroblastoma ni kanseri y’abana, nubwo ari ikibazo gikomeye, imaze kugira iterambere rihambaye mu buryo bwo kuvura mu myaka mike ishize. Abana benshi barwaye neuroblastoma bakomeza kubaho ubuzima bwiza kandi busanzwe nyuma yo kuvurwa.
Ibintu by’ingenzi byo kuzirikana ni uko kubimenya hakiri kare bigira akamaro, kuvura bigenwa n’umwihariko w’umwana wawe, kandi nturi wenyine muri uru rugendo. Amakipe ya kijyambere y’abaganga afite ubunararibonye mu kuvura neuroblastoma no gufasha imiryango muri uwo mujyo.
Nubwo ibyavuye mu isuzuma bishobora kuguha ikibazo, shyira imbaraga mu gukora ibintu intambwe ku yindi. Itsinda ry’abaganga b’umwana wawe rizaguherekeza muri buri cyiciro cyo kuvura kandi rizagufasha kumva icyo witeze. Imiryango myinshi isanga guhuza n’andi miryango yanyuzemo ibyabaye bisa ari ubufasha n’ibitekerezo by’agaciro.
Gira icyizere itsinda ryanyu ry’abaganga, komereza guhuza n’umuryango wawe ushyigikiye, kandi wibuke ko abana bafite imbaraga zidasanzwe. Hamwe no kuvurwa neza no kwitabwaho, abana benshi barwaye neuroblastoma bakomeza gukura neza.
Q1: Neuroblastoma ihora yica?
Oya, neuroblastoma ntabwo ihora ipfana. Mu by'ukuri, abana benshi barwaye neuroblastoma barakira kandi bakomeza kubaho ubuzima busanzwe. Uko bizagenda biterwa n'ibintu byinshi birimo imyaka y'umwana, aho kanseri yageze, n'imiterere yihariye y'ibibyimba. Neuroblastoma ifite ibyago bike cyane ifite ibyago byo gukira byiza cyane, akenshi birenga 95%. Ndetse n'ibyago byinshi byarushijeho kugira umusaruro mwiza ukoresheje uburyo bwo kuvura bugezweho.
Q2: Neuroblastoma ishobora gusubira inyuma nyuma yo kuvurwa?
Yego, neuroblastoma ishobora gusubira, ariko ibi ntibibaho ku bana benshi. Ibyago byo gusubira biterwa n'icyiciro cy'ibanze cy'ibibyimba. Umusubizo ugaragara cyane uba mu myaka ibiri ya mbere nyuma yo kuvurwa, niyo mpamvu kwitabwaho gukurikirana ari ingenzi cyane. Niba neuroblastoma isubiye, hakiri uburyo bwo kuvura buhari, harimo uburyo bushya bwari butaboneka mbere.
Q3: Umwana wanjye azashobora kugira ubuzima busanzwe nyuma yo kuvurwa neuroblastoma?
Abana benshi barokotse neuroblastoma bakomeza kubaho ubuzima busanzwe kandi bwiza. Bashobora kujya ku ishuri, gukina imikino, no kwitabira ibikorwa byose bisanzwe by'abana. Bamwe mu bana bashobora kugira ingaruka z'igihe kirekire ziterwa no kuvurwa, ariko byinshi muri ibyo bishobora guhangana neza. Ikipe yawe y'abaganga izakurikirana iterambere n'ubuzima bw'umwana wawe kandi ikemure ibibazo byose byabaho.
Q4: Neuroblastoma yandura?
Oya, neuroblastoma ntiyandura. Ntishobora gukwirakwira kuva ku muntu umwe ajya ku wundi binyuze mu guhura, gusangira ibiryo, cyangwa ubundi buryo ubwo aribwo bwose. Kanseri itera impinduka mu miterere y'umuntu ubwe, atari mu gihe cy'ubwandu bw'udukoko cyangwa virusi. Umwana wawe ashobora guhura n'inshuti, abagize umuryango, na bagenzi be nta kaga ko kwanduza indwara.
Q5: Ndagomba gupimisha imirire y'umuryango wanjye?
Ibizamini bya genetika bisabwa gusa mu mimerere yihariye cyane, kuko neuroblastoma ikomoka ku miryango iba ari nke cyane (1-2% by’ababwanduye). Muganga wawe ashobora kugutekerezaho kugirana inama ku bijyanye na genetika niba neuroblastoma iri mu muryango wanyu, niba umwana wawe yayirwaye akiri muto cyane, cyangwa niba hari ibindi bimenyetso bidasanzwe. Ku muryango munini, ibizamini bya genetika ntabwo bikenewe kuko umubare munini w’ababana na neuroblastoma babirwara ku mpamvu z’impanuka.