Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR): Ibimenyetso, Intandaro, n’Ubuvuzi

Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR, Partial anomalous pulmonary venous return) ni uburwayi bw’umutima aho imitsi imwe y’amaraso yo mu mwijima ihuza nabi n’igice cy’umutima. Aho imitsi ine y’amaraso yose yagombye kugarura amaraso yuzuye umwuka uva mu mwijima ajya mu gice cy’umutima cy’ibumoso, imwe cyangwa nyinshi muri iyo mitsi ihuza nabi n’igice cy’umutima cy’iburyo cyangwa ibindi bice by’umutima.

Ubu burwayi bw’umutima buva ku ivuka, buboneka kuri 0.4 kugeza kuri 0.7% by’abantu bose, bityo bukaba butari bwose ariko ntabwo ari bwo buke cyane. Abantu benshi bafite PAPVR babayeho ubuzima busanzwe batabizi, cyane cyane iyo umusemburo umwe gusa ari wo ubangamiwe.

Ibimenyetso by’Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR) ni ibihe?

Abantu benshi bafite PAPVR nta bimenyetso bagira, cyane cyane iyo uburwayi buri mu rwego rworoshye. Uburemere bw’ibimenyetso biterwa n’umubare w’imitsi y’amaraso yo mu mwijima ihujwe nabi n’ingano y’amaraso menshi ajya mu gice cy’umutima cy’iburyo.

Iyo ibimenyetso bigaragaye, bisanzwe bigenda bigaragara buhoro buhoro kandi bishobora kuba birimo:

• Guhumeka nabi mu gihe cy’imikino cyangwa imyitozo ngororamubiri
• Umunaniro udakunze kugaragara ugereranije n’ibyo wakoze
• Indwara z’ubuhumekero kenshi cyangwa gukira gahoro gahoro nyuma y’imbeho
• Gukubita kw’umutima cyangwa kumva umutima ukubita
• Kugabanuka kw’ubushobozi bwo gukora imyitozo ngororamubiri ugereranije n’abandi
• Kubabara mu gituza cyangwa kubabara gato mu gituza mu gihe cy’imikino

Mu bihe bikomeye, ushobora kubona kubyimba mu maguru cyangwa mu birenge, cyane cyane mu mpera z’umunsi. Bamwe bagira n’inkorora idashira isa n’itavuka ku burwayi.

Abana bafite PAPVR bashobora kugaragaza iterambere ridafite imbaraga cyangwa bagaragara nk’abananiwe cyane mu gihe cy’imikino ugereranije n’abandi bana b’imyaka yabo. Ariko, ibyo bimenyetso bishobora kuba bito cyane kandi bikagenda bitaboneka imyaka myinshi.

Ubwoko bw’Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR) ni ubuhe?

PAPVR ihabwa ubwoko hashingiwe ku mitsi y’amaraso yo mu mwijima ibangamiwe n’aho ihuza nabi. Ubwoko busanzwe ni ubwo imitsi y’amaraso yo mu mwijima iburyo hejuru, bugera kuri 90% by’ibibazo bya PAPVR byose.

Ubwoko nyamukuru burimo:

• PAPVR y’umusemburo w’amaraso wo mu mwijima iburyo hejuru: Ubwoko busanzwe, busanzwe buhuza n’umusemburo munini w’amaraso
• PAPVR y’umusemburo w’amaraso wo mu mwijima iburyo hasi: Buke, bushobora guhuza n’umusemburo muto w’amaraso cyangwa igice cy’umutima cy’iburyo
• PAPVR yo ku ruhande rw’ibumoso: Buke, ihuza imitsi y’amaraso yo mu mwijima ibumoso ihuza nabi
• Scimitar syndrome: Ubwoko bw’umwihariko aho imitsi y’amaraso yo mu mwijima iburyo ikora ishusho y’inkota ya scimitar ku bipimo by’ama rayons X by’igituza

Buri bwoko bugira ibibazo bitandukanye kandi bishobora gusaba uburyo butandukanye bw’ubuvuzi. Umuganga w’indwara z’umutima azamenya neza ubwoko ufite binyuze mu bipimo byihariye byo kubona amashusho.

Intandaro y’Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR) ni iyihe?

PAPVR itera mu ntangiriro z’inda iyo umutima n’imitsi y’amaraso birimo gukura. Ibi bibaho hagati y’icyumweru cya kane n’icyenda cy’inda, mbere y’uko abagore benshi bamenya ko batwite.

Ubu burwayi buva ku buryo busanzwe bw’iterambere ry’imitsi y’amaraso yo mu mwijima ritagenda neza. Mu gihe cy’iterambere ry’umwana uri mu nda, imitsi y’amaraso yo mu mwijima igomba kujya ihuza n’igice cy’umutima cy’ibumoso, ariko rimwe na rimwe uwo mucyo nturangira neza.

Bitandukanye n’ibindi burwayi bw’umutima, PAPVR ntabwo iterwa n’ibyo ababyeyi bakoze cyangwa batakoze mu gihe cy’inda. Ni ukubura uburyo umutima uterambere, kimwe n’uko bamwe bavukana ibara ry’amaso ritandukanye.

Ibyinshi bibaho ku bushake nta mateka y’ibibazo by’umutima mu muryango. Ariko, gake cyane, PAPVR ishobora kuba igice cy’indwara z’imyororokere cyangwa ikaba mu muryango, nubwo ibi bigaragara ku kigero gito cyane cy’ibibazo.

Ni ryari ukwiye kujya kwa muganga kubera Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR)?

Ukwiye kuvugana na muganga wawe niba ufite guhumeka nabi bitasobanuwe, cyane cyane mu bikorwa bitari byakubangamira mbere. Ibi ni ingenzi cyane niba guhumeka nabi bigenda bikomeza uko iminsi igenda ishira.

Ibindi bimenyetso bibangamira bisaba ubuvuzi birimo umunaniro udashira ubangamira ibikorwa byawe bya buri munsi, indwara z’ubuhumekero kenshi, cyangwa gukubita kw’umutima bikubabaza cyangwa bikutera impungenge.

Niba uri umubyeyi, banza kureba ibimenyetso mu mwana wawe nko kugorana gukurikira bagenzi be mu mikino, kunanirwa bitunguranye nyuma y’ibikorwa bike, cyangwa imbeho kenshi isa n’iyamarara igihe kirekire.

Ntuzuyaze gushaka ubuvuzi bw’ihutirwa niba ufite ububabare mu gituza, guhumeka nabi cyane ukiri aho uri, cyangwa kwangirika kw’ibimenyetso byose. Nubwo PAPVR idakunze gutera ibibazo byihutirwa, ibyo bimenyetso bishobora kugaragaza ibibazo bisaba kwitabwaho vuba.

Ibyago byo kugira Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR) ni ibihe?

Kubera ko PAPVR ari uburwayi buva ku ivuka butera mbere y’uko umwana avuka, ibintu bisanzwe byongera ibyago nko kubaho nabi ntabwo bikora. Ariko, ibintu bimwe bishobora kongera gato amahirwe yo kugira ubu burwayi.

Ibyago nyamukuru birimo:

• Amateka y’uburwayi bw’umutima buva ku ivuka mu muryango, nubwo ibi bidahagije
• Kuba ufite ibindi burwayi bw’umutima buva ku ivuka
• Kuvukana indwara zimwe z’imyororokere
• Diyabete ya nyina mu gihe cy’inda, nubwo ubuhuza buke

Ni ingenzi kumva ko kugira ibyo byago ntibisobanura ko wowe cyangwa umwana wawe muzaba mufite PAPVR. Abantu benshi bafite ubu burwayi nta byago byagaragaye na gato.

Ubu burwayi bugira ingaruka ku bagabo n’abagore kimwe kandi buboneka mu matsinda y’abantu bose. Imyaka si ikintu cyongera ibyago kuko uvuka ufite ubu burwayi, nubwo ibimenyetso bishobora kugaragara cyane uko ugenda ukura.

Ibibazo bishoboka by’Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR) ni ibihe?

Abantu benshi bafite PAPVR ntabwo bagira ibibazo, cyane cyane iyo umusemburo umwe gusa ari wo ubangamiwe. Ariko, kumva ibibazo bishoboka bigufasha kuba maso ku mpinduka mu buzima bwawe.

Ibibazo bisanzwe bigenda bigaragara buhoro buhoro imyaka myinshi kandi birimo:

• Kubyimba kw’igice cy’umutima cy’iburyo kubera gutwara amaraso menshi
• Umuvuduko w’amaraso muri arteri z’imwijima (pulmonary hypertension)
• Ibyago byiyongereye byo kugira ibibazo by’umutima
• Kugabanuka kw’ubushobozi bwo gukora imyitozo ngororamubiri buhora buzamuka
• Kugira ubushobozi buke bwo kurwanya indwara z’ubuhumekero

Mu bihe bidahagije, ibibazo bikomeye bishobora kugaragara, cyane cyane iyo imitsi myinshi y’amaraso ari yo ibangamiwe. Ibyo bishobora kuba harimo gucika intege kw’umutima, umuvuduko w’amaraso muri arteri z’imwijima ukabije, cyangwa ibibazo bikomeye by’umutima.

Inkuru nziza ni uko, hakurikijwe ubugenzuzi n’ubuvuzi uko bikenewe, ibibazo byinshi bishobora kwirindwa cyangwa bigacungwa neza. Kusuzuma buri gihe kwa muganga w’indwara z’umutima bigufasha kubona impinduka zose hakiri kare.

Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR) bupimwa gute?

PAPVR ikunze kuvumburwa mu buryo butunguranye mu bipimo byakozwe kubera izindi mpamvu, kubera ko abantu benshi nta bimenyetso bigaragara bafite. Muganga wawe ashobora kubanza gushidikanya kuri ubu burwayi niba yumvise umutima ukubita nabi mu isuzuma rya buri munsi.

Uburyo bwo gupima busanzwe butangira hakoreshejwe ikizamini cy’umutima (échographie), gikoreshwa amajwi yo gukora amashusho y’umutima. Iki kizamini gishobora kugaragaza imiterere y’amaraso idasanzwe kandi gifasha kumenya aho imitsi y’amaraso yo mu mwijima ihuza.

Ibindi bipimo bishobora kuba birimo:

• Isuzuma ry’ama rayons X y’igituza kugira ngo harebwe kubyimba kw’umutima cyangwa imiterere y’imitsi y’amaraso idasanzwe
• Isuzuma rya MRI y’umutima kugira ngo haboneke amashusho arambuye y’imiterere y’umutima n’imitere y’amaraso
• Isuzuma rya CT scan hamwe n’ibintu byongera amashusho kugira ngo harebwe neza imitsi y’amaraso yo mu mwijima
• Kwinjiza umusemburo mu mutima mu bihe bimwe kugira ngo hapimaze umuvuduko w’amaraso kandi hameze neza uburwayi

Ibyo bipimo bifasha muganga w’indwara z’umutima kumenya neza imitsi y’amaraso ibangamiwe n’ingano y’amaraso menshi ajya mu gice cy’umutima kitari cyo. Ibyo bimenyetso ni ingenzi mu gufata icyemezo cy’uko ubuvuzi bukenewe.

Ubuvuzi bw’Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR) ni ubuhe?

Ubuvuzi bwa PAPVR biterwa n’ingano y’amaraso menshi ajya mu gice cy’umutima cy’iburyo n’uko ufite ibimenyetso. Abantu benshi bafite PAPVR yoroshye bakeneye gusa ubugenzuzi buhoraho nta kubagwa.

Iyo ubuvuzi bukenewe, kubagwa ni bwo buryo nyamukuru. Kubagwa bikubiyemo guhindura imitsi y’amaraso yo mu mwijima ihuza nabi kugira ngo ijyane mu gice cy’umutima cy’ibumoso aho ikwiye, bigasubiza imiterere isanzwe y’amaraso.

Muganga w’indwara z’umutima azagutegeka kubagwa niba:

• Ufite ibimenyetso bikomeye bigira ingaruka ku mibereho yawe
• Igice cy’umutima cy’iburyo cyiyongereye kubera gutwara amaraso menshi
• Ibizamini bigaragaza amaraso menshi adasanzwe
• Ugaragaza ibibazo nko kuzamuka kw’umuvuduko w’amaraso muri arteri z’imwijima

Uburyo bwo kubagwa busanzwe bukorerwa mu kubaga umutima, nubwo ibigo bimwe birimo gusuzuma uburyo buke butera ibibazo. Abarwayi benshi barakira neza kandi bagaragaza iterambere rikomeye mu bimenyetso byabo nyuma yo kubagwa.

Niba kubagwa bitakenewe vuba, muganga wawe azategura gusuzuma buri gihe kugira ngo akurikirane uburwayi bwawe kandi arebe impinduka zishobora gusaba kuvurwa nyuma.

Uko wakwitwara mu rugo mu gihe ufite Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR)

Nubwo ubuvuzi ari bwo buryo nyamukuru bwo kuvura PAPVR, hari ibintu byinshi ushobora gukora mu rugo kugira ngo ufashe gucunga ibimenyetso no gushyigikira ubuzima bwawe bw’umutima muri rusange.

Fata iya mbere mu kugira ubuzima bwiza bw’umutima mu rwego rushoboka. Imikino ngororamubiri isanzwe, nk’ugenda cyangwa koga, ishobora gufasha gukomeza umutima wawe, ariko utega amatwi umubiri wawe kandi ntukomeze guhumeka nabi cyangwa kubabara mu gituza.

Witondere kwirinda indwara z’ubuhumekero, zishobora kuba zikomeye ku bantu bafite PAPVR:

• Fata inkingo za grippe buri mwaka kandi ube uzi inkingo zindi zigufasha
• Kora isuku y’intoki kenshi, cyane cyane mu gihe cy’imbeho n’ibicurane
• Irinde guhura n’abantu barwaye igihe bishoboka
• Tegereza gukoresha umwuka w’ubushyuhe kugira ngo ugume umwuka mu myanya y’ubuhumekero

Mugire imibereho myiza y’umutima ifite indyo yuzuye, ibitotsi bihagije, no gucunga umunaniro. Nubwo ibi bitavura PAPVR, bishyigikira ubuzima bwawe bw’umutima muri rusange kandi bishobora kugufasha kumva umeze neza buri munsi.

Uko wakwitegura gusura muganga wawe

Kwitunganya gusura muganga w’indwara z’umutima bigufasha kugira icyo umenye mu ruzinduko rwawe kandi ntukibagirwe ibibazo cyangwa amakuru akomeye.

Mbere yo gusura muganga, andika ibimenyetso byawe byose, harimo igihe bibaho n’ibyababangiza. Bandika impinduka zose mu bushobozi bwawe bwo gukora imyitozo ngororamubiri cyangwa mu mbaraga zawe, nubwo zasa n’ntoya.

Zana urutonde rwuzuye rw’imiti ukoresha, harimo imiti yo mu maduka n’imiti y’imiti. Kandi uzane ibisubizo by’ibizamini byabanje, cyane cyane ibizamini bijyanye n’umutima nko gusuzuma umutima cyangwa ama rayons X y’igituza.

Tegura ibibazo byawe mbere. Tekereza kubabaza ibi bikurikira:

• Uburemere bw’uburwayi bwawe bwa PAPVR ni ubuhe?
• Ni ibihe bimenyetso bikwiye kukubwira guhamagara muganga vuba?
• Hariho ibikorwa ugomba kwirinda?
• Uzakenera gusuzuma buri kangahe?
• Ni ibihe bimenyetso bishobora kugaragaza ko ukeneye kubagwa mu gihe kiri imbere?

Tegereza kuzana umuntu wo mu muryango cyangwa inshuti kugira ngo aguhe gufata amakuru yavuzwe mu gihe cy’isura yawe, cyane cyane niba utuje kubera uburwayi.

Icyo ukwiye kumenya cyane kuri Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR)

PAPVR ni uburwayi bw’umutima bushobora kuvurwa kandi abantu benshi babayeho neza ubuzima bwabo bwose. Nubwo byumvikana bibi, ukuri ni uko ibyinshi muri byo biroroshye kandi ntabwo bigira ingaruka ku mibereho ya buri munsi.

Ikintu cy’ingenzi cyo kwibuka ni uko kugira PAPVR ntibisobanura ko udashobora kubaho ubuzima buhamye, buzuye. Hamwe no kugenzura kwa muganga no kuvurwa uko bikenewe, abantu benshi bafite ubu burwayi bakora neza cyane.

Komeza guhuza n’itsinda ryawe ry’ubuvuzi kandi ntutinye kubabaza ibibazo cyangwa gutangaza ibimenyetso bishya. Kumenya hakiri kare impinduka zose bituma habaho kuvurwa vuba, bigatuma habaho ibyiza.

Wibuke ko ubumenyi bw’ubuvuzi n’ubuvuzi bwa PAPVR bikomeza gutera imbere. Ikintu cy’ingenzi ni ugukorana na muganga w’indwara z’umutima kugira ngo mutegure gahunda yo kugenzura no kuvura ibereye uko uhagaze.

Ibibazo byakunze kubazwa kuri Ubuhinduka bw’imitsi y’amaraso mu mutima (PAPVR)

Urashobora gukora imyitozo ngororamubiri nk’ibisanzwe ufite PAPVR?

Abantu benshi bafite PAPVR yoroshye bashobora gukora imyitozo ngororamubiri nk’ibisanzwe, nubwo ukwiye kuvugana na muganga w’indwara z’umutima ku bijyanye n’amabwiriza yo gukora imyitozo ngororamubiri. Bashobora kugutegeka kwirinda ibikorwa bikomeye cyangwa imikino yo guhatana, bitewe n’uko uhagaze. Tega amatwi umubiri wawe kandi uhagarare niba ufite guhumeka nabi, ububabare mu gituza, cyangwa gucika intege mu gihe cy’imyitozo ngororamubiri.

PAPVR izakomeza kuba mbi uko iminsi igenda ishira?

PAPVR ubwayo ntigenda iba mbi kuko ari uburwayi bw’imiterere y’umubiri uvuka ufite. Ariko, ingaruka ku mutima wawe zishobora gutera imbere uko iminsi igenda ishira niba amaraso menshi arimo kugenda nabi. Niyo mpamvu gusuzuma buri gihe kwa muganga w’indwara z’umutima ari ingenzi kugira ngo harebwe impinduka zishobora gusaba ubuvuzi.

Abagore bafite PAPVR bashobora gutwita neza?

Abagore benshi bafite PAPVR bashobora gutwita neza, ariko ibi bisaba ubugenzuzi buhoraho bwa muganga w’indwara z’umutima n’umuganga w’inda. Gutwita bisaba umutima gukora cyane, bityo abaganga bawe bazashaka gusuzuma uko uhagaze kandi bashobora kugutegeka gusuzuma kenshi mu gihe cy’inda.

PAPVR irakomoka mu muryango?

Ibyinshi bya PAPVR bibaho ku bushake kandi ntibiva ku babyeyi. Ariko, hari amahirwe make yo kuba byakomoka mu muryango cyangwa bikaba bifitanye isano n’indwara z’imyororokere. Niba ufite PAPVR kandi uteganya kubyara, biganiro na muganga w’indwara z’umutima kandi utekereze ku bijyanye n’imyororokere niba byakugirira akamaro.

Ni iki kibaho niba PAPVR itabayeho?

Abantu benshi bafite PAPVR yoroshye ntabwo bakenera ubuvuzi kandi babayeho ubuzima busanzwe. Ariko, niba amaraso menshi adasanzwe atabayeho, ashobora gutera kubyimba kw’igice cy’umutima cy’iburyo, kuzamuka kw’umuvuduko w’amaraso muri arteri z’imwijima, cyangwa ibibazo by’umutima. Niyo mpamvu ubugenzuzi buhoraho ari ingenzi, nubwo ubu utakiri kubagwa.