Scleroderma ni iki? Ibimenyetso, Intandaro, n'Ubuvuzi

Scleroderma ni indwara iterwa n'ubudahangarwa bw'umubiri aho ubwirinzi bw'umubiri bugaba igitero ku mubiri, bigatuma uruhu n'ingingo z'umubiri zikaba zikomeye kandi zikagira ubukonje. Tekereza ko umubiri wawe ukora collagen nyinshi, ikintu gitanga imiterere ku ruhu na za ngingo.

Iyi ndwara igira ingaruka kuri buri wese mu buryo butandukanye. Bamwe bagira impinduka nke ku ruhu, abandi bagira ingaruka zikwirakwira ku zindi ngingo z'imbere. Inkuru nziza ni uko, ubufasha bw'abaganga n'impinduka mu mibereho, abantu benshi barwaye scleroderma babasha kubaho ubuzima bwiza kandi buhamye.

Ni ubwoko ki bwa scleroderma?

Scleroderma ifite ubwoko bubiri nyamukuru, kandi kumenya ubwoko ufite bigufasha mu gutoranya ubuvuzi bukwiriye. Muganga wawe azakorana nawe kugira ngo amenye ubwoko ufite hashingiwe ku bimenyetso n'ibisubizo by'ibizamini.

Scleroderma y'uruhu ruto ikunda kwibasira uruhu rw'amaboko, ibirenge, mu maso, no mu maboko yo hasi. Ubu bwoko bushiraho buhoro buhoro kandi bishobora kumara imyaka kugira ngo buze ku rwego rwo hejuru. Abantu benshi barwaye ubu bwoko bagira indwara yitwa CREST syndrome, irimo imyanda ya calcium munsi y'uruhu, impinduka z'amabara mu myanya y'intoki n'ibirenge, no kugira ikibazo cyo kurya.

Scleroderma y'uruhu rwagutse ikwirakwira ku duce twinshi tw'uruhu kandi ishobora kwibasira ingingo z'imbere nka mutima, ibihaha, n'impyiko. Ubu bwoko bushiraho vuba kurusha ubwoko buto, akenshi mu myaka mike nyuma y'aho ibimenyetso bigaragariye.

Hari kandi systemic sclerosis sine scleroderma, ubwoko buke cyane aho ingingo z'imbere zibasirwa ariko impinduka ku ruhu ziba nke cyangwa ntazo.

Ni ibihe bimenyetso bya scleroderma?

Ibimenyetso bya scleroderma bishobora gutandukana cyane ukurikije umuntu, ariko akenshi bigaragara buhoro buhoro mu mezi cyangwa imyaka. Umubiri wawe ushobora kugaragaza ibimenyetso mu buryo butandukanye, kandi kubimenya hakiri kare bigufasha kubona ubuvuzi ukeneye vuba.

Ibimenyetso bisanzwe ushobora kubona birimo:

• Uruhu rukaba rukomeye kandi rukagira ubukonje - Bisanzwe bitangirira mu ntoki, hanyuma bikwirakwira mu maboko, mu maso, no ku mubiri
• Raynaud's phenomenon - Imyanya y'intoki n'ibirenge bihinduka umweru, ubururu, cyangwa umutuku iyo byashyizwe ahatonye cyangwa hari umunaniro
• Kubyimbagira mu ntoki no mu birenge - Bigaragara cyane mu gitondo cyangwa nyuma y'igihe kirekire utari gukora imyitozo
• Kubabara no gukomera kw'ingingo - Bimeze kimwe na arthritis, bikaba bikomeye cyane mu gitondo
• Ikibazo cyo kurya - Ibiryo bishobora kumva biri gukomerera mu muhogo cyangwa mu gituza
• Umuvuduko w'umutima cyangwa acid reflux - Bitewe n'impinduka mu munwa
• Guhumeka nabi - Cyane cyane mu gihe ukora imyitozo
• Umunaniro - Kumva unaniwe cyane nubwo uburuhukira bihagije

Ibimenyetso bitagenda bikunze kugaragara ariko bikaba by'ingenzi birimo inkorora idashira, kugabanuka kw'ibiro bitasobanuwe, n'ibibazo by'impyiko bishobora kugaragara nk'umuvuduko w'amaraso mwinshi cyangwa impinduka mu kunywa.

Ni iki gitera scleroderma?

Intandaro nyakuri ya scleroderma ntiyaramenyekana neza, ariko abashakashatsi bemeza ko iterwa n'ubudahangarwa bw'umubiri bukorera cyane bugatangira kugaba igitero ku ngingo z'umubiri. Ibi bituma umubiri ukora collagen nyinshi, bigatuma uruhu n'ingingo zikaba zikomeye.

Ibintu byinshi bishobora guhurira hamwe kugira ngo bitere iyi ndwara:

• Uburanga - Gene zimwe na zimwe zishobora kukugiraho ingaruka, nubwo scleroderma idakunda guherwa mu muryango
• Ibintu byo mu kirere - Kwibera mu biyobyabwenge bimwe na bimwe, indwara, cyangwa imvune zishobora gutera iyi ndwara ku bantu bayibonekamo
• Hormones - Abagore barwara scleroderma kurusha abagabo, bigaragaza ko hormones zigira uruhare
• Uburangare bw'ubudahangarwa bw'umubiri - Ibibazo by'uburyo ubwirinzi bw'umubiri bubigenzura

Ni ngombwa kumenya ko scleroderma atari indwara yandura kandi ko idaterwa n'icyo wakoze cyangwa utarakora. Iyi ndwara isa n'iterwa n'imikorere iri hagati ya gene nawe n'ibidukikije.

Ni ibihe bintu byongera ibyago byo kurwara scleroderma?

Nubwo umuntu wese ashobora kurwara scleroderma, hari ibintu bimwe na bimwe bishobora kongera ibyago byo kurwara iyi ndwara. Kumenya ibi bintu bishobora kugufasha kumenya ibimenyetso hakiri kare, nubwo ufite ibi bintu bidakubwira ko uzayirwara.

Ibintu by'ingenzi byongera ibyago birimo:

• Ibitsina - Abagore barwara scleroderma kurusha abagabo
• Imyaka - Abantu benshi barwaye iyi ndwara bafite imyaka iri hagati ya 30 na 50, nubwo ishobora kugaragara mu myaka yose
• Ubwoko n'akarere - Abanyamerika b'Abirabura n'Abanyamerika bakomoka mu bwoko bw'aba-Native bafite ibyago byinshi kandi bashobora kurwara ubwoko bukomeye
• Amateka y'umuryango - Kugira umuntu wa hafi ufite scleroderma cyangwa indi ndwara iterwa n'ubudahangarwa bw'umubiri byongera ibyago
• Ibintu byo mu kirere - Ibintu bimwe na bimwe byo mu kazi nka silica dust, organic solvents, cyangwa ibindi biyobyabwenge
• Izindi ndwara ziterwa n'ubudahangarwa bw'umubiri - Kugira indwara nka rheumatoid arthritis cyangwa lupus byongera ibyago

Wibuke ko abantu benshi bafite ibi bintu byongera ibyago batarwara scleroderma. Ibi bintu bifasha abashakashatsi kumenya uko iyi ndwara ikwirakwira.

Ni ryari ukwiye kujya kwa muganga kubera scleroderma?

Ukwiye kujya kwa muganga niba ubona impinduka ku ruhu, cyane cyane niba uruhu rwawe rukaba rukomeye, rukagira ubukonje, cyangwa rukaba rumeze neza mu ntoki, mu myanya y'intoki, cyangwa mu maso. Kubona ubuvuzi hakiri kare bishobora gufasha gucunga ibimenyetso no gukumira ingaruka.

Shaka ubufasha bw'abaganga niba ufite:

• Uruhu rukomeye cyangwa rugira ubukonje bidashira mu byumweru bike
• Raynaud's phenomenon yashya, ikomeye, cyangwa ifatanije n'impinduka ku ruhu
• Kubabara no gukomera kw'ingingo bidakemuka
• Ikibazo cyo kurya cyangwa umuvuduko w'umutima udashira
• Guhumeka nabi cyangwa inkorora idashira
• Impinduka z'umuvuduko w'amaraso cyangwa imikorere y'impyiko

Ntugategereze niba ufite ibimenyetso byinshi, nubwo bigaragara ko ari bito. Gutabara hakiri kare bishobora kugira uruhare mu gucunga scleroderma no gukumira ingaruka.

Ni izihe ngaruka zishoboka za scleroderma?

Nubwo abantu benshi barwaye scleroderma babasha kubaho neza uko babigenzura, iyi ndwara ishobora rimwe na rimwe kwibasira ingingo z'imbere. Kumenya ingaruka zishoboka bigufasha gukorana n'abaganga bawe kugira ngo ukumire cyangwa umenye ibibazo hakiri kare.

Ingaruka zisanzwe harimo:

• Ibibazo by'impyiko - Umuvuduko w'amaraso mwinshi no kugabanuka kw'imikorere y'impyiko, bishobora kuba bibi ariko bigacungwa neza n'imiti
• Ibibazo by'ibihaha - Gukomera kw'ibihaha cyangwa umuvuduko mwinshi w'amaraso mu mitsi y'ibihaha, bigatera guhumeka nabi
• Ibibazo by'umutima - Umutima ukomera, gucika intege kw'umutima, cyangwa kubabara kw'ingingo z'umutima
• Ibibazo by'igogorwa - Umuvuduko w'umutima mwinshi, ikibazo cyo kunywa ibiryo, cyangwa gufunga kw'amara
• Ibibazo by'uruhu - Ibisebe ku myanya y'intoki cyangwa ahantu hagaragara cyane bikira buhoro
• Ibibazo by'ingingo - Gukomera cyangwa guhinduka kw'intoki n'ibirenge

Ingaruka zidafata igihe kinini ariko zikaba zikomeye harimo pulmonary hypertension ikomeye, ikibazo cy'impyiko gifite umuvuduko mwinshi w'amaraso, n'ubudahangarwa bw'umutima. Gukurikiranwa n'abaganga bigufasha kumenya ibibazo hakiri kare.

Scleroderma imenyekanwa gute?

Kumenya scleroderma bikubiyemo isuzuma ry'umubiri, amateka y'uburwayi, n'ibizamini byihariye. Muganga wawe azashakisha ibimenyetso byihariye kandi azakuraho izindi ndwara zishobora gutera ibimenyetso nk'ibyo.

Uburyo bwo kubimenya busanzwe burimo:

• Isuzuma ry'umubiri - Muganga wawe azasuzumira uruhu rwawe, ingingo, n'ingingo z'imbere kugira ngo arebe ibimenyetso bya scleroderma
• Ibizamini by'amaraso - Ashaka antibodies nka ANA, anti-centromere, na anti-topoisomerase I
• Ibizamini byo kubona amashusho - CT scans y'igituza kugira ngo arebe ibihaha, cyangwa echocardiograms kugira ngo asuzume umutima
• Ibizamini by'imikorere y'ibihaha - Bipima uko ibihaha byawe bikora
• Biopsy y'uruhu - Ntibikunze gukoreshwa, ariko bishobora gukorwa niba ubuvuzi butaramenyekana
• Nailfold capillaroscopy - Isuzuma ryihariye ry'imitsi y'amaraso mito iri hasi y'imisumari

Muganga wawe ashobora kandi gutegeka ibindi bizamini hashingiwe ku bimenyetso byawe, nko gusuzuma imikorere y'impyiko, gukurikirana umutima, cyangwa ibizamini byo gusuzuma igogorwa. Uburyo bwo kubimenya bushobora gutwara igihe, ariko gusuzuma neza bifasha guha ubuvuzi bukwiriye.

Ni ubuhe buvuzi bwa scleroderma?

Ubuvuzi bwa scleroderma bugamije gucunga ibimenyetso, gukumira ingaruka, no kubungabunga ubuzima bwawe. Nubwo nta muti uravura, hari ubuvuzi bwinshi bushobora gufasha gucunga iyi ndwara no kugabanya uburyo itera imbere.

Ubuvuzi bwawe bushobora kuba:

• Imiti yo kuvura ibimenyetso by'uruhu - Imiti yo kwisiga n'imiti nka methotrexate cyangwa mycophenolate kugira ngo igabanye kubabara
• Gucagura Raynaud's - Calcium channel blockers cyangwa indi miti yo kunoza amaraso mu ntoki no mu birenge
• Gufasha igogorwa - Proton pump inhibitors yo kuvura umuvuduko w'umutima n'imiti yo gufasha ibibazo by'amara
• Ubuvuzi bw'ibihaha - Imiti igabanya ubudahangarwa bw'umubiri cyangwa imiti yo kuvura ibihaha
• Gucagura umuvuduko w'amaraso - ACE inhibitors yo kurinda impyiko no gucunga umuvuduko w'amaraso
• Ubuvuzi ngororamubiri - Imikino yo kubungabunga uburyo bw'ingingo

Ku ngaruka nke nka pulmonary hypertension ikomeye, muganga wawe ashobora kugutegeka ubuvuzi bwihariye nka endothelin receptor antagonists cyangwa prostacyclin therapy. Kugira uruhare mu guhindura uturemangingo rimwe na rimwe bifatwa mu gihe cy'indwara ikomeye kandi itera imbere vuba, nubwo ibi bikorerwa mu bihe byihariye.

Uko wacunga scleroderma mu rugo

Kwita ku buzima bwawe mu rugo ni ingenzi mu gucunga scleroderma. Imikorere yoroshye ya buri munsi ishobora kugufasha kumva umeze neza kandi ishobora kugabanya uburyo ibimenyetso biterera imbere.

Dore intambwe ushobora gukora:

• Kwirinda gukonja - Kwambara imyenda myinshi, gukoresha utuboko twashyushujwe, no kwirinda ahantu hatonye kugira ngo wirinde Raynaud's attacks
• Kurinda uruhu rwawe - Koresha amavuta yo kwisiga meza, adafite impumuro nziza, kandi wirinde ibintu bikomeye
• Kora imyitozo ngororamubiri - Imikino yoroshye nko koga, kugenda, cyangwa yoga bifasha kubungabunga uburyo bw'ingingo
• Kurya ibiryo bike, byinshi - Ibi bifasha mu igogorwa kandi bigabanya umuvuduko w'umutima
• Kureka kunywa itabi - Kunywa itabi bituma amaraso adatembera neza kandi bishobora kwihutisha kwangirika kw'ibihaha
• Gucagura umunaniro - Koresha uburyo bwo kuruhuka, kuko umunaniro ushobora gutera ibimenyetso

Ugomba kandi gukurikirana ibimenyetso byawe no kwandika impinduka zose kugira ngo ubiganireho n'abaganga bawe. Kwita ku ruhu, kunywa amazi ahagije, no kuruhuka bihagije ni uburyo bworoheje ariko bukaba bwiza bwo kubungabunga ubuzima bwawe.

Uko wakwirinda scleroderma

Ikibabaje ni uko nta buryo bwo kwirinda scleroderma buramenyekana kuko intandaro yayo nyakuri itarebwa neza. Ariko rero, niba ufite ibintu byongera ibyago cyangwa ibimenyetso bya mbere by'iyi ndwara, hari intambwe ushobora gutera kugira ngo uhagarike uburyo itera imbere.

Nubwo utazi kwirinda scleroderma rwose, ushobora:

• Kwima ibintu bizatera - Kwirinda silica dust n'ibindi biyobyabwenge byo mu kazi
• Kureka kunywa itabi - Kunywa itabi bishobora kongera ibibazo by'amaraso no kongera ingaruka
• Gucagura izindi ndwara ziterwa n'ubudahangarwa bw'umubiri - Ubuvuzi bukwiriye bw'izindi ndwara bushobora kugabanya ibikorwa by'ubudahangarwa bw'umubiri
• Kugira ubuzima bwiza - Imikino ngororamubiri, ibiryo byiza, no gucunga umunaniro bifasha ubwirinzi bw'umubiri
• Kujya gusuzuma buri gihe - Kubona ubuvuzi hakiri kare bishobora gukumira ingaruka

Niba ufite abagize umuryango barwaye scleroderma cyangwa izindi ndwara ziterwa n'ubudahangarwa bw'umubiri, kora ibishoboka byose kugira ngo umenye ibimenyetso hakiri kare kandi ubiganireho n'abaganga bawe. Nubwo udashyira mu gaciro ibintu by'uburanga, kumenya ibintu bishobora gutuma umuntu arwara iyi ndwara bigufasha kubona ubuvuzi hakiri kare.

Uko wakitegura kujya kwa muganga

Kwitunganya neza mbere yo kujya kwa muganga bigufasha kubona ibyiza byinshi mu gihe cyawe n'abaganga bawe. Gutegura neza bishobora gutuma habaho itumanaho ryiza kandi ubuvuzi bugakorwa neza.

Mbere y'uruzinduko rwawe:

• Andika ibimenyetso byawe - Andika igihe byatangiye, uko byahindutse, n'icyo bibafasha cyangwa kibitera
• Andika amateka y'uburwayi bwawe - Harimo amateka y'umuryango w'indwara ziterwa n'ubudahangarwa bw'umubiri
• Zana imiti yose - Harimo imiti y'abaganga, imiti yo mu maduka, n'ibindi
• Tegura ibibazo - Andika ibyo ushaka kumenya ku ndwara yawe n'uburyo bwo kuyivura
• Tegura umuntu uzakujyana - Umuryango cyangwa inshuti ishobora kugufasha kwibuka amakuru y'ingenzi
• Zana ibisubizo by'ibizamini byabanje - Niba wabonye abandi baganga, zana kopi y'ibizamini n'ibindi

Mu gihe cy'uruzinduko rwawe, ntutinye gusaba ibisobanuro niba hari ikintu kitumvikana. Muganga wawe ashaka kugufasha kumva indwara yawe no kumva ufite icyizere mu buvuzi bwawe.

Icyingenzi kuri scleroderma

Scleroderma ni indwara ikomeye iterwa n'ubudahangarwa bw'umubiri ikagira ingaruka kuri buri wese mu buryo butandukanye, ariko ubufasha bw'abaganga n'uburyo bwo kwivuza, abantu benshi babasha kubaho ubuzima bwiza kandi buhamye. Ikintu cy'ingenzi ni ugukorana n'abaganga bawe kugira ngo mugire gahunda y'ubuvuzi ihuye n'ibimenyetso byawe n'ibyo ukeneye.

Wibuke ko ubushakashatsi kuri scleroderma burakomeje, kandi ubuvuzi bushya burakorwa buri gihe. Ikintu cy'ingenzi ni ukumenya amakuru ku ndwara yawe, gukurikiza gahunda y'ubuvuzi bwawe, no kugira itumanaho ryiza n'abaganga bawe.

Nubwo kubaho ufite scleroderma bishobora kuba bigoye, nturi wenyine. Amashyirahamwe y'abantu barwaye iyi ndwara, haba mu bantu no kuri internet, ashobora kukubera umufasha.

Ibibazo bikunze kubaho kuri scleroderma

Ese scleroderma iherwa mu muryango?

Scleroderma ifite ibintu by'uburanga, ariko ntiherwa mu muryango nk'izindi ndwara. Kugira umuntu wo mu muryango ufite scleroderma cyangwa indi ndwara iterwa n'ubudahangarwa bw'umubiri byongera ibyago, ariko abantu benshi barwaye scleroderma nta bagize umuryango barwaye iyi ndwara.

Ese scleroderma iravurwa?

Kuri ubu, nta muti uravura scleroderma, ariko ibi ntibisobanura ko utazi kubaho neza ufite iyi ndwara. Hari ubuvuzi bwinshi bushobora gucunga ibimenyetso, kugabanya uburyo itera imbere, no gukumira ingaruka.

Ese scleroderma itera imbere vuba?

Uburyo scleroderma itera imbere butandukana cyane ukurikije umuntu. Bamwe bagira impinduka zikomeye mu myaka mike ya mbere, hanyuma bagahorana, abandi bagira iterambere rihoro rihoro mu myaka myinshi. Scleroderma y'uruhu ruto itera imbere buhoro kurusha scleroderma y'uruhu rwagutse.

Ese gutwita bishobora kugira ingaruka kuri scleroderma?

Gutwita bishoboka kuri benshi mu bagore barwaye scleroderma, ariko bisaba gukurikiranwa neza no gutegura neza. Bamwe mu bagore bagira ibimenyetso byiza mu gihe cyo gutwita, abandi bashobora kugira ibyago byinshi by'ingaruka.

Ese indyo igira ingaruka ku bimenyetso bya scleroderma?

Nubwo nta ndyo iboneka ishobora kuvura scleroderma, impinduka zimwe na zimwe mu mirire zishobora gufasha gucunga ibimenyetso. Kurya ibiryo bike, byinshi bishobora gufasha mu bibazo by'igogorwa, mu gihe kwirinda ibiryo bishyushye cyangwa bikonje bishobora kugabanya ububabare.