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Scleroderma

Incamake

Scleroderma (sklair-oh-DUR-muh), izwi kandi nka systemic sclerosis, ni indwara zidakunze kugaragara zifata uruhu rugatinda kandi rugasiga. Scleroderma ishobora kandi guteza ibibazo mu mitsi y'amaraso, mu ngingo z'imbere no mu mara.

Scleroderma ikunze kugaragara nk'ito cyangwa ikwirakwira, ibi bikaba bivuga gusa urugero rw'uruhu rwibasiwe. Ubwoko bwombi bushobora kugira ibindi bimenyetso by'imitsi y'amaraso cyangwa by'ingingo biri mu ndwara. Scleroderma yibasiye ahantu runaka, izwi kandi nka morphea, ibagira uruhu gusa.

Nubwo nta muti uwo ari wo wose wa scleroderma, ubuvuzi bushobora kugabanya ibimenyetso, kugabanya umuvuduko no kunoza ubuzima.

Ibimenyetso

Ibimenyetso bya scleroderma bitandukanye ku muntu ku wundi, bitewe n'ibice by'umubiri byagizweho ingaruka. Hafi abantu bose bafite scleroderma bagira uburibwe n'ugukomera kw'uruhu. Ibice by'umubiri bigira ingaruka mbere ni intoki, amaboko, ibirenge n'isura. Kuri bamwe, ukubyimba kw'uruhu bishobora kandi kugaragara mu maboko, amaboko yo hejuru, ikibuno, igifu, amaguru yo hasi n'imikaya. Ibimenyetso bya mbere bishobora kuba harimo kubyimbagana no gukorora. Ibara ry'uruhu rwagizweho ingaruka rishobora guhinduka rikaba ryiza cyangwa rikomereye, kandi uruhu rushobora kugaragara nk'urwiza kubera ukubana. Bamwe bagira kandi ibikomere bito by'umutuku, bizwi nka telangiectasia, ku ntoki no mu maso. Umunyu wa calcium ushobora gukorwa munsi y'uruhu, cyane cyane ku ntoki, ugatera ibibyimba bishobora kuboneka kuri X-rays. Raynaud's phenomenon igaragara cyane muri scleroderma. Bibaho kubera kugabanyuka gukabije kw'imijyana mito y'amaraso mu ntoki no mu birenge mu gihe cy'ubukonje cyangwa impagarara. Ibi bibaye, intoki zishobora kubabara cyangwa zikagira ubuzimu, zikaba zera, zikaba zibisi, zikaba zirabura cyangwa zitukura. Raynaud's phenomenon ishobora kandi kuba ku bantu badafite scleroderma. Scleroderma ishobora kugira ingaruka ku gice icyo ari cyo cyose cy'ubwonko bw'igogorwa, kuva mu munwa kugera mu kibuno. Bitewe n'ibice by'ubwonko bw'igogorwa byagizweho ingaruka, ibimenyetso bishobora kuba birimo:

  • Umuriro mu gifu.
  • Kugorana kw'umunwa.
  • Kubyimbagana.
  • Impiswi.
  • Kubabara mu nda.
  • Kudafata neza umubiri. Iyo scleroderma igize ingaruka ku mutima cyangwa mu mpyiko, ishobora gutera guhumeka nabi, kugabanuka kw'ubushobozi bwo gukora imyitozo ngororamubiri no gucika intege. Scleroderma ishobora gutera uburibwe mu mpyiko bishobora gutera guhumeka nabi buhoro buhoro. Hari imiti ishobora gufasha kugabanya iterambere ry'ibyangiritse by'impyiko. Iyo scleroderma igize ingaruka ku mutima, umutima ushobora guhora uhindagurika. Kugira ikibazo cy'umutima bishobora kandi kubaho kuri bamwe.
Impamvu

Scleroderma ibaho iyo umubiri utanze collagen nyinshi ikaba ikusanyiriza mu mubiri. Collagen ni ubu bwoko bwa poroteyine ifite ibara ry'ubunyunyu bwo mu mubiri, harimo n'uruhu.

Abahanga ntibabizi neza icyateye uyu muhora gutangira, ariko ubudahangarwa bw'umubiri bugaragara ko bufite uruhare. Birashoboka cyane ko scleroderma iterwa n'ibintu byinshi birimo ibibazo by'ubudahangarwa bw'umubiri, imvange n'ibintu by'ibidukikije.

Ingaruka zishobora guteza

Umuntu wese arashobora kurwara scleroderma, ariko igaragara cyane mu bantu bagenerwa igitsina gore bavuka. Abantu bakunze kurwara scleroderma bafite imyaka iri hagati ya 30 na 50. Abantu b'Abirabura bakunze kuyirwara kare kandi bafite ibyago byinshi byo kugira ibibazo byinshi by'uruhu n'iby'ubuhumekero.

Hari izindi mpamvu nyinshi zifatanije zisa nkaho zigira uruhare mu kuba umuntu yakwandura scleroderma:

  • Uburanga. Abantu bafite impinduka runaka mu mbaraga zabo z'umubiri basa nkaho bafite ibyago byinshi byo kurwara scleroderma. Ibi bishobora gusobanura impamvu scleroderma isa nkaho ikwirakwira mu miryango mu bantu bake, kandi impamvu zimwe na zimwe za scleroderma zihari cyane mu bantu bo mu matsinda runaka y'amoko n'ubwoko.
  • Ibintu byo mu kirere bibitera. Ubushakashatsi bwerekana ko kuri bamwe, ibimenyetso bya scleroderma bishobora guterwa no kwandura virusi, imiti cyangwa ibiyobyabwenge. Kwandura kenshi, nko mu kazi, ibintu cyangwa imiti mibi bishobora kandi kongera ibyago byo kurwara scleroderma. Impamvu yo mu kirere itera iyi ndwara ntiboneka kuri benshi.
  • Indwara zifata ubudahangarwa bw'umubiri. Scleroderma yizwe ko ari indwara y'ubudahangarwa bw'umubiri. Ibi bivuze ko iterwa mu gice kimwe no kuba ubudahangarwa bw'umubiri butangira gutera ubusembwa. Abantu barwaye scleroderma bashobora kandi kugira ibimenyetso by'izindi ndwara z'ubudahangarwa bw'umubiri nka rhumatoïde arthritis, lupus cyangwa Sjogren syndrome.
Ingaruka

Ingaruka za Scleroderma ziratandukanye kuva ku nto kugeza ku zikomeye kandi zishobora kugira ingaruka kuri:

  • Imyanya y'intoki. Muri systemic sclerosis, ikibazo cya Raynaud gishobora kuba kibi cyane ku buryo amaraso adatembera neza akangiza burundu imyanya y'intoki, bigatera ibibyimba cyangwa ibikomere. Mu bamwe, imyanya y'intoki ishobora gupfa.
  • Umutima. Gukomera kw'imyakura y'umutima byongera ibyago byo kudakora neza kw'umutima no kunanirwa kw'umutima. Scleroderma ishobora kandi guteza umuriro mu gice gikikije umutima.
  • Sisitemu y'igogorwa. Ingaruka za scleroderma ku igogorwa zirimo guhinda umuriro no kugorana kw'umunwa. Scleroderma ishobora kandi guteza ibibazo by'amavunja, kubyimba, impatwe cyangwa isesemi. Bamwe mu barwaye scleroderma bashobora kugira ibibazo byo kunywa intungamubiri kubera kwiyongera kw'ibinyabuzima mu mara.
  • Ibyomoko. Uruhu rwo hejuru y'ibyomoko rushobora gukomera cyane ku buryo rubangamira kugenda neza no kugenda, cyane cyane mu ntoki.
Kupima

Kubera ko scleroderma ishobora kugaragara mu buryo bwinshi kandi ikagira ingaruka ku bice byinshi byumubiri, birashobora kugorana kuyivura.

Nyuma yo gusuzuma umubiri neza, umuganga wawe ashobora kugusaba gupimisha amaraso kugira ngo barebe niba hari antibodies nyinshi zikora mu mubiri.

Umuganga wawe ashobora kandi kugusaba izindi nsuzure z'amaraso, amashusho cyangwa ibizamini by'imikorere y'ingingo. Ibi bizamini bishobora gufasha kumenya niba uruvange rw'ibiryo, umutima, imyanya y'ubuhumekero cyangwa impyiko byagizweho ingaruka.

Uburyo bwo kuvura

Nta muti uwo ari wo wose ushobora gukiza cyangwa guhagarika umusaruro ukabije wa collagen uba mu maraso mu ndwara ya scleroderma. Ariko hari uburyo bwinshi bwo kuvura bushobora gufasha kugenzura ibimenyetso no gukumira ingaruka.

Kuko scleroderma ishobora kugira ingaruka ku bice byinshi byumubiri, imiti itorerwa bitewe nibimenyetso. Ingero zirimo imiti igabanya:

  • Igabanya ibimenyetso byo mu gifu. Ibinini bigabanya aside mu gifu bishobora gufasha kugabanya ibibazo byo mu gifu. Antibiyotike nimiti ifasha ibiryo kunyura mu mara bishobora kugabanya kubyimbagira, impiswi no gucibwamo.
  • Gukumira indwara zandura. Inkingo zigomba gukorwa kugirango ziringanize abantu barwaye scleroderma ku ndwara zandura. Ganira na muganga wawe kubijyanye ningingo zikingira igicurane, pneumonia, shingles, HPV, COVID-19 na RSV.
  • Kugabanya ububabare. Niba imiti igabanya ububabare iboneka atakazi idafasha bihagije, muganga wawe ashobora kugutekerezaho imiti ivura ububabare.

Abaganga bita ku mubiri cyangwa abaganga bita ku kazi bashobora kugufasha kunoza imbaraga zawe no kugenda neza no kugumana ubwigenge mubikorwa bya buri munsi. Ubuvuzi bw'intoki bushobora gufasha gukumira ubugufi bw'intoki, bita kandi amagufwa.

Gusimbuza uturemangingo bishobora kuba amahitamo ku bantu bafite ibimenyetso bikomeye bitaravurwa nimiti isanzwe. Niba imyanya y'ubuhumekero cyangwa impyiko byangiritse cyane, hashobora gutekerezwa ku gusimbuza imyanya y'ubuhumekero cyangwa impyiko.

Aderesi: 506/507, 1st Main Rd, Murugeshpalya, K R Garden, Bengaluru, Karnataka 560075

Umuhakana: Kanama ni urubuga rw'amakuru y'ubuzima kandi ibisubizo byayo ntibigize inama z'ubuvuzi. Jya ubona umuganga ufite uruhushya rwo gukorera hafi yawe mbere yo gukora impinduka izo ari zo zose.

Yakorewe mu Buhinde, ku isi