Scleroderma (sklair-oh-DUR-muh), izwi kandi nka systemic sclerosis, ni indwara zidakunze kugaragara zifata uruhu rugatinda kandi rugasiga. Scleroderma ishobora kandi guteza ibibazo mu mitsi y'amaraso, mu ngingo z'imbere no mu mara.
Scleroderma ikunze kugaragara nk'ito cyangwa ikwirakwira, ibi bikaba bivuga gusa urugero rw'uruhu rwibasiwe. Ubwoko bwombi bushobora kugira ibindi bimenyetso by'imitsi y'amaraso cyangwa by'ingingo biri mu ndwara. Scleroderma yibasiye ahantu runaka, izwi kandi nka morphea, ibagira uruhu gusa.
Nubwo nta muti uwo ari wo wose wa scleroderma, ubuvuzi bushobora kugabanya ibimenyetso, kugabanya umuvuduko no kunoza ubuzima.
Ibimenyetso bya scleroderma bitandukanye ku muntu ku wundi, bitewe n'ibice by'umubiri byagizweho ingaruka. Hafi abantu bose bafite scleroderma bagira uburibwe n'ugukomera kw'uruhu. Ibice by'umubiri bigira ingaruka mbere ni intoki, amaboko, ibirenge n'isura. Kuri bamwe, ukubyimba kw'uruhu bishobora kandi kugaragara mu maboko, amaboko yo hejuru, ikibuno, igifu, amaguru yo hasi n'imikaya. Ibimenyetso bya mbere bishobora kuba harimo kubyimbagana no gukorora. Ibara ry'uruhu rwagizweho ingaruka rishobora guhinduka rikaba ryiza cyangwa rikomereye, kandi uruhu rushobora kugaragara nk'urwiza kubera ukubana. Bamwe bagira kandi ibikomere bito by'umutuku, bizwi nka telangiectasia, ku ntoki no mu maso. Umunyu wa calcium ushobora gukorwa munsi y'uruhu, cyane cyane ku ntoki, ugatera ibibyimba bishobora kuboneka kuri X-rays. Raynaud's phenomenon igaragara cyane muri scleroderma. Bibaho kubera kugabanyuka gukabije kw'imijyana mito y'amaraso mu ntoki no mu birenge mu gihe cy'ubukonje cyangwa impagarara. Ibi bibaye, intoki zishobora kubabara cyangwa zikagira ubuzimu, zikaba zera, zikaba zibisi, zikaba zirabura cyangwa zitukura. Raynaud's phenomenon ishobora kandi kuba ku bantu badafite scleroderma. Scleroderma ishobora kugira ingaruka ku gice icyo ari cyo cyose cy'ubwonko bw'igogorwa, kuva mu munwa kugera mu kibuno. Bitewe n'ibice by'ubwonko bw'igogorwa byagizweho ingaruka, ibimenyetso bishobora kuba birimo:
Scleroderma ibaho iyo umubiri utanze collagen nyinshi ikaba ikusanyiriza mu mubiri. Collagen ni ubu bwoko bwa poroteyine ifite ibara ry'ubunyunyu bwo mu mubiri, harimo n'uruhu.
Abahanga ntibabizi neza icyateye uyu muhora gutangira, ariko ubudahangarwa bw'umubiri bugaragara ko bufite uruhare. Birashoboka cyane ko scleroderma iterwa n'ibintu byinshi birimo ibibazo by'ubudahangarwa bw'umubiri, imvange n'ibintu by'ibidukikije.
Umuntu wese arashobora kurwara scleroderma, ariko igaragara cyane mu bantu bagenerwa igitsina gore bavuka. Abantu bakunze kurwara scleroderma bafite imyaka iri hagati ya 30 na 50. Abantu b'Abirabura bakunze kuyirwara kare kandi bafite ibyago byinshi byo kugira ibibazo byinshi by'uruhu n'iby'ubuhumekero.
Hari izindi mpamvu nyinshi zifatanije zisa nkaho zigira uruhare mu kuba umuntu yakwandura scleroderma:
Ingaruka za Scleroderma ziratandukanye kuva ku nto kugeza ku zikomeye kandi zishobora kugira ingaruka kuri:
Kubera ko scleroderma ishobora kugaragara mu buryo bwinshi kandi ikagira ingaruka ku bice byinshi byumubiri, birashobora kugorana kuyivura.
Nyuma yo gusuzuma umubiri neza, umuganga wawe ashobora kugusaba gupimisha amaraso kugira ngo barebe niba hari antibodies nyinshi zikora mu mubiri.
Umuganga wawe ashobora kandi kugusaba izindi nsuzure z'amaraso, amashusho cyangwa ibizamini by'imikorere y'ingingo. Ibi bizamini bishobora gufasha kumenya niba uruvange rw'ibiryo, umutima, imyanya y'ubuhumekero cyangwa impyiko byagizweho ingaruka.
Nta muti uwo ari wo wose ushobora gukiza cyangwa guhagarika umusaruro ukabije wa collagen uba mu maraso mu ndwara ya scleroderma. Ariko hari uburyo bwinshi bwo kuvura bushobora gufasha kugenzura ibimenyetso no gukumira ingaruka.
Kuko scleroderma ishobora kugira ingaruka ku bice byinshi byumubiri, imiti itorerwa bitewe nibimenyetso. Ingero zirimo imiti igabanya:
Abaganga bita ku mubiri cyangwa abaganga bita ku kazi bashobora kugufasha kunoza imbaraga zawe no kugenda neza no kugumana ubwigenge mubikorwa bya buri munsi. Ubuvuzi bw'intoki bushobora gufasha gukumira ubugufi bw'intoki, bita kandi amagufwa.
Gusimbuza uturemangingo bishobora kuba amahitamo ku bantu bafite ibimenyetso bikomeye bitaravurwa nimiti isanzwe. Niba imyanya y'ubuhumekero cyangwa impyiko byangiritse cyane, hashobora gutekerezwa ku gusimbuza imyanya y'ubuhumekero cyangwa impyiko.
Umuhakana: Kanama ni urubuga rw'amakuru y'ubuzima kandi ibisubizo byayo ntibigize inama z'ubuvuzi. Jya ubona umuganga ufite uruhushya rwo gukorera hafi yawe mbere yo gukora impinduka izo ari zo zose.