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Necrosis Ya Epidermis Ikabije

Incamake

TEN itera ibice binini by'uruhu rwo kubyimba, rukavura.

Toxic epidermal necrolysis (TEN) ni uburwayi bwo ku ruhu buke, buhitana, busanzwe buterwa n'imiti. Ni ubwoko bukomeye bwa Stevens-Johnson syndrome (SJS). Mu bantu barwaye SJS, TEN imenyekana iyo arenga 30% y'uruhu rwo hejuru rugizweho ingaruka kandi imyanya y'umubiri ifite ubuhehere (imikaya) ikaba yangiritse cyane.

TEN ni uburwayi buhitana bukorera abantu b'imyaka yose. TEN isanzwe ivurwa mu bitaro. Mu gihe uruhu rukira, kwitaho abantu harimo guhagarika ububabare, kwita ku dukombe no kugenzura ko uboneye amazi ahagije. Gukira bishobora gufata ibyumweru ku mezi.

Niba uburwayi bwawe bwaterewe n'imiti, uzakenera kwirinda iyo miti burundu n'izindi zijyanye na yo.

Ibimenyetso

Ibimenyetso n'ibibonwa bya toxic epidermal necrolysis birimo: Ububabare bukabije bw'uruhu Ukwishima kw'uruhu ku mubiri urenga 30% Ibibyimba n'uruhu rwinshi rw'uruhu Ibyondo, kubyimba no gukomera ku mumaso, harimo akanwa, amaso n'inda Kwitabaza ubuvuzi hakiri kare ni ingenzi ku bantu barwaye Stevens-Johnson syndrome/toxic epidermal necrolysis (SJS/TEN). Niba ufite ibimenyetso, shaka ubuvuzi bw'ihutirwa. Uzakeneye kwitabwaho n'inzobere mu kuvura indwara z'uruhu (dermatologue) n'abandi bahanga mu bitaro.

Igihe cyo kubona umuganga

Kuvurwa hakiri kare ni ingenzi ku bantu barwaye Stevens-Johnson syndrome/toxic epidermal necrolysis (SJS/TEN). Niba ufite ibimenyetso, shaka ubufasha bwa muganga vuba. Uzakeneye kwitabwaho n'inzobere mu kuvura indwara z'uruhu (dermatologue) n'abandi bahanga mu bitaro.

Impamvu

SJS/TEN iterwa ahanini n'uburyo umubiri uhangana n'imiti. Ibimenyetso bishobora kugaragara nyuma y'icyumweru kimwe kugeza ku byumweru bine utangiye gufata imiti mishya.

Imiti ikunze gutera SJS/TEN irimo antibiyotike, imiti y'indwara z'ubwonko, imiti irimo sulfa na allopurinol (Aloprim, Zyloprim).

Ingaruka zishobora guteza

Ibintu byongera ibyago byo kwibasirwa na SJS/TEN birimo:

  • Ubwandu bwa HIV. Mu bantu bafite ubwandu bwa HIV, ubwandu bwa SJS/TEN burenze inshuro 100 ugereranyije n'abaturage muri rusange.
  • Ubudahangarwa bw'umubiri butameze neza. Ubudahangarwa bw'umubiri bushobora kwibasirwa n'ihindurwa ry'imirimo y'umubiri, HIV/SIDA n'indwara ziterwa no kudahangana kw'umubiri.
  • ** Kanseri.** Abantu barwaye kanseri, cyane cyane kanseri y'amaraso (hematologic malignancies), bafite ibyago byinshi byo kwibasirwa na SJS/TEN.
  • Amateka ya SJS/TEN. Niba warwaye iyi ndwara iterwa n'imiti, uri mu kaga ko kongera kuyirwara niba ukoresha iyo miti ukundi.
  • Amateka y'umuryango wa SJS/TEN. Niba umuntu wo mu muryango wawe wa hafi, nka mubyeyi cyangwa mwene wabo, yarwaye SJS/TEN, ushobora kuba ufite ibyago byinshi byo kuyirwara.
  • Ibintu by'umuzuko. Kugira impinduka zimwe na zimwe mu mubiri byongera ibyago byo kwibasirwa na SJS/TEN, cyane cyane niba unywa imiti yo kuvura indwara zifata ubwonko, indwara y'igicuri cyangwa indwara zo mu mutwe.
Ingaruka

Abantu bafite ibyago byinshi byo kwibasirwa n’ingaruka za TEN ni abarengeje imyaka 70 n’abafite indwara y’umwijima cyangwa kanseri ikwirakwira (metastatique). Ingaruka za TEN zirimo:

  • Ubwandu bw’amaraso (sepsis). Sepsis ibaho iyo udukoko dutera indwara two mu bwandu winjira mu maraso yawe ukwirakwira mu mubiri wawe wose. Sepsis ni indwara itera vuba cyane, ikaba ikomeye cyane ku buryo ishobora gutera ishoke n’ikibazo cy’imikorere y’ingingo.
  • Ikibazo cy’ibihaha. Ibi bishobora gutera inkorora, kugorana guhumeka, kandi, iyo indwara ikomeye, guhagarara kw’ubuhumekero.
  • Ikibazo cy’ubuhumekero. TEN ishobora gutera ibibazo by’amaso, nko kumara amaso, ijisho ryinjira mu ijisho, ibikomere by’umunyura, kandi, gake cyane, ubuhumbu.
  • Iguma ry’uruhu. Nyuma yo gukira TEN, uruhu rwawe rushobora kugira ibintu byuzuye, inenge n’amabara atandukanye. Ibibazo by’uruhu biramba bishobora gutuma umusatsi wawe ukomoka, kandi imisumari y’amaboko n’ibirenge byawe bishobora kudakura neza.
  • Ibyo kubabara mu gitsina. Ku bagore, TEN ishobora gutera ibikomere mu mubiri uri mu gitsina, bigatuma ubabara cyangwa, niba bitavuwe, gukomera kw’igitsina.
  • Umujinya. Iyi ndwara itera umujinya kandi ishobora kugira ingaruka mbi ku bitekerezo mu gihe kirekire.
Kwirinda

Kugira ngo wirinda ikindi gihe cya TEN, menya niba cyatewe n'umuti. Niba ari byo, ntuzongere gufata uwo muti cyangwa undi umeze nkayo. Gusubira kwakwica cyangwa kukwangiza cyane. Nanone, bwira abaganga bose bazakwitaho mu gihe kizaza amateka yawe ya TEN, kandi wambare ikimenyetso cy'ubuzima cyangwa umunyururu ufite amakuru yerekeye uburwayi bwawe. Cyangwa ujyanire pasiporo y'allergie.

Kupima

TEN imenyekanwa iyo abantu bafite SJS bagize indwara ikomeye ireba umubiri urenze 30%.

Uburyo bwo kuvura

Niba muganga wawe akeka ko TEN yawe yatewe n'imiti wafashe, uzakenera guhagarika gufata iyo miti. Hanyuma ushobora kwimurirwa mu bitaro kuvurirwayo, bishoboka ko mu ishami ry'abafashwe n'inkongi cyangwa mu cyumba cy'ubuvuzi bwo kuvura abarwaye cyane. Gukira neza bishobora gufata amezi menshi.

Ubuvuzi nyamukuru bwa TEN ni ugukora uko bishoboka kose kugira ngo ugume utuje mu gihe uruhu rwawe rukira. Uzabona ubwo buvuzi bwo kubafasha mu gihe uri mu bitaro. Bishobora kuba birimo:

  • Gusubiza amazi n'imirire. Kubera ko gutakaza uruhu bishobora gutera gutakaza amazi mu mubiri, ni ingenzi gusubiza amazi n'ibintu by'amanywa. Ushobora guhabwa amazi n'imirire binyuze mu muyoboro ushyirwa mu mazuru ukayoborwa mu gifu (umuyoboro wa nasogastric).
  • Kuvura ibikomere. Itsinda ry'abaganga bawe rishobora gusukura uruhu rwafashwe neza no gushyiraho imyenda yihariye irimo peteroli jelly (Vaseline) cyangwa imiti. Itsinda ry'abaganga bawe kandi rikugenzura kugira ngo barebe niba hari ubwandu kandi baguha antibiyotike niba bibaye ngombwa.
  • Guhumeka gufasha. Ushobora kuba ukeneye ibizamini n'uburyo bwo gusuzuma inzira yawe y'ubuhumekero no gufasha kuyirinda. Mu ndwara ikomeye, ushobora kuba ukeneye intubation cyangwa gufasha guhumeka gikozwe n'imashini (ventilation).
  • Kugabanya ububabare. Uzabona imiti igabanya ububabare kugira ngo ugabanye ibibi. Kubabara mu kanwa, ushobora guhabwa amazi yo kumesa akanwa arimo umuti ukomera, nka lidocaine.
  • Kwita ku maso. Ku bimenyetso byoroheje by'amaso, ushobora kungukirwa no gushyira amarira y'imiti adafite ibintu byongera ubuzima byibuze inshuro enye ku munsi. Amavuta yo mu maso arimo corticosteroids ashobora gukoreshwa kugira ngo hagabanuke kubyimba kw'amaso. Itsinda ry'abaganga bawe rishobora kuba ririmo inzobere mu maso (ophthalmologist).

Ubuvuzi bwa TEN bushobora kandi kuba burimo imiti imwe cyangwa imiti ivangwa ifata umubiri wose (imiti ya systemic), nka cyclosporine (Neoral, Sandimmune), etanercept (Enbrel) na immunoglobulin ya intravenous (IVIG). Haracyenewe ubushakashatsi bwo kumenya akamaro kayo, niba hariho.

Aderesi: 506/507, 1st Main Rd, Murugeshpalya, K R Garden, Bengaluru, Karnataka 560075

Umuhakana: Kanama ni urubuga rw'amakuru y'ubuzima kandi ibisubizo byayo ntibigize inama z'ubuvuzi. Jya ubona umuganga ufite uruhushya rwo gukorera hafi yawe mbere yo gukora impinduka izo ari zo zose.

Yakorewe mu Buhinde, ku isi