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Undifferentiated Pleomorphic Sarcoma ni iki? Ibimenyetso, Intandaro, n'Ubuvuzi

Created at:1/16/2025

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Undifferentiated pleomorphic sarcoma (UPS), ni ubwoko bwa kanseri y'umubiri muto ishobora kugaragara ahantu hose mu mubiri wawe, nubwo ikunda kugaragara mu maboko, mu maguru, cyangwa mu gatuza. Iyi kanseri yiswe kuri ubwo buryo kuko uturemangingo tuyigize tugaragara bitandukanye cyane iyo turebwe kuri mikoroskopi kandi ntiduhuza neza n'ubwoko runaka bw'umubiri usanzwe.

UPS ifatwa nk'indwara ya kanseri idaheruka, igera ku muntu umwe kuri 100.000 buri mwaka. Nubwo kwakira iyi ndwara bishobora gutera ubwoba, gusobanukirwa ibyo uhura na byo bishobora kugufasha kumva witeguye kandi ufite icyizere mu rugendo rwawe rwo kuvurwa.

Undifferentiated pleomorphic sarcoma ni iki?

Undifferentiated pleomorphic sarcoma ni kanseri itera mu mubiri muto nk'imikaya, amavuta, imiyoboro y'amaraso, cyangwa imikaya ihuza. Ijambo "undifferentiated" risobanura ko uturemangingo twa kanseri tudasa n'ubwoko runaka bw'uturemangingo dusanzwe, bituma bigorana kubyirondora.

Ijambo "Pleomorphic" risobanura uburyo utwo turemangingo twa kanseri tugira imiterere myinshi itandukanye iyo turebwe kuri mikoroskopi. Ubu buryo bwo kugaragara ni kimwe mu bimenyetso by'ingenzi abaganga bakoresha mu kumenya ubwo bwoko bwa sarcoma.

UPS ikunda gukura nk'igituntu gikomeye, kitabagira ububabare, gishobora kugira uburebure kuva kuri sentimetero nke kugeza ku burebure bunini. Abantu benshi babanza kubona nk'igituntu cyiyongera buhoro buhoro mu mezi cyangwa mu byumweru.

Iyi kanseri ikunda kwibasira abantu bakuru bafite imyaka iri hagati ya 50 na 70, nubwo ishobora kugaragara mu kigero icyo aricyo cyose. Abagabo n'abagore barayibasirwa kimwe, kandi ishobora kugaragara mu bantu b'amoko yose.

Ibimenyetso bya undifferentiated pleomorphic sarcoma ni ibihe?

Ikimenyetso cya mbere cyane cya UPS ni igituntu cyangwa igice cy'umubiri utababaza ushobora kumva munsi y'uruhu rwawe. Iki gice cy'umubiri gikunda kumera nk'igikomeye cyangwa gikomeye kandi gishobora gukura buhoro buhoro mu gihe.

Abantu benshi ntibababara mu ntangiriro, ibi bikaba byatuma batinda gushaka ubuvuzi. Dore ibimenyetso ushobora kubona:

  • Igituntu gikomeye, gikura cyangwa igice cy'umubiri ahantu hose mu mubiri wawe
  • Kubyimbagira mu gice cyibasiwe
  • Kubabara cyangwa kubabara, cyane cyane uko igituntu gikura
  • Kugira imbaraga nke mu mikorere y'umubiri niba igituntu kibasiye imikaya cyangwa ingingo
  • Kubabara cyangwa kugira uburibwe niba igituntu gishyira igitutu ku mitsi

Bamwe mu bantu bagira ibimenyetso byihariye bitewe n'aho igituntu gikura. Niba UPS ikura mu kuguru cyangwa mu kuboko, ushobora kubona intege nke cyangwa ugakora nabi.

Mu bihe bidasanzwe, iyo UPS ikura mu mubiri wo imbere cyangwa igakora ku ngingo zo imbere, ushobora kugira ibimenyetso rusange nko kugabanuka k'uburemere, umunaniro, cyangwa umuriro. Ariko, ibi bimenyetso ni bike cyane kandi bikunda kugaragara gusa iyo indwara igeze kure.

Intandaro ya undifferentiated pleomorphic sarcoma ni iyihe?

Intandaro nyayo ya undifferentiated pleomorphic sarcoma ntiyumvikana neza, ariko abashakashatsi bemeza ko itera iyo uturemangingo dusanzwe mu mubiri muto tugize impinduka z'imiterere zituma bikura mu buryo budakwiye. Izi mpinduka zikunda kubaho mu buryo butunguranye aho kuba zaraherwe ababyeyi bawe.

Ibintu byinshi bishobora gutera UPS, nubwo ufite ibyo bintu bitavuze ko uzabona kanseri:

  • Ubuvuzi bwakozwe hakoreshejwe imirasire kuri kanseri indi
  • Kuhura n'ibintu runaka cyangwa uburozi
  • Kubabara cyangwa imvune mu mubiri muto
  • Indwara zimwe na zimwe z'imiterere (bihora bike)
  • Impinduka z'uturemangingo zijyanye n'imyaka

Ubuvuzi bwakozwe hakoreshejwe imirasire ni kimwe mu bintu by'ingenzi bizwi. Niba wakiriye ubuvuzi bwakozwe hakoreshejwe imirasire kuri kanseri indi mu myaka ishize, hari ibyago bike byo kurwara UPS mu gice cyavuwe.

Ariko rero, ni ingenzi kumenya ko abantu benshi bafite UPS nta bintu by'ingenzi byabateye. Kanseri isa n'iterwa mu buryo butunguranye mu bantu bazima, ibyo bishobora gutera agahinda iyo ugerageza gusobanukirwa impamvu ibi byakubayeho.

Ni ryari ukwiye kubona muganga kubera undifferentiated pleomorphic sarcoma?

Ukwiye kubona muganga niba ubona igituntu gishya cyangwa igice cy'umubiri gikomeza ibyumweru birenga bike, cyane cyane niba gikura cyangwa kigahinduka. Nubwo ibituntu byinshi bigaragara ko bitari kanseri, bihora ari byiza kubipimisha hakiri kare.

Tegura gahunda yawe vuba niba ubona ibi bimenyetso:

  • Igituntu kinini kurusha santimetero 5
  • Igice cy'umubiri icyo aricyo cyose gikura cyangwa kigahindura imiterere
  • Igituntu kimeretse cyangwa gifatanye
  • Kubabara, kubabara, cyangwa intege nke mu gice cyibasiwe
  • Igituntu icyo aricyo cyose kibangamira imikorere isanzwe

Ntugatege amatwi niba igituntu gikubangamiye cyangwa kigira ingaruka ku mirimo yawe ya buri munsi. Kumenya hakiri kare no kuvurwa bikunda gutera ibyiza kuri sarcomas.

Niba ufite amateka yo kuvurwa hakoreshejwe imirasire, kora ibishoboka byose kugira ngo wirinde ibituntu bishya mu bice byavuwe. Nubwo ibyago biguma ari bike, muganga wawe azashaka gusuzuma ibituntu bishya neza.

Ibyago bya undifferentiated pleomorphic sarcoma ni ibihe?

Gusobanukirwa ibyago bishobora kugufasha kumenya ibimenyetso by'uburwayi, nubwo ufite ibyago bitavuze ko uzabona UPS. Abantu benshi bafite iyi kanseri nta bintu by'ingenzi byabateye.

Ibyago by'ingenzi abaganga bamenye harimo:

  • Imyaka iri hagati ya 50-70 (nubwo ishobora kugaragara mu kigero icyo aricyo cyose)
  • Ubuvuzi bwakozwe hakoreshejwe imirasire, busanzwe bukorwa imyaka 10-20 mbere
  • Indwara zimwe na zimwe z'imiterere nk'iya Li-Fraumeni
  • Kuhura n'ibintu runaka mu mirimo
  • Lymphedema idakira (kubyimbagira igihe kirekire)

Ubuvuzi bwakozwe hakoreshejwe imirasire ni cyo kintu cy'ingenzi cyane cyamenyekanye. Niba wakiriye imirasire kubera kanseri yo mu mabere, lymphoma, cyangwa kanseri indi, hari ibyago bike byo kurwara UPS mu gice cyavuwe nyuma y'imyaka myinshi.

Indwara zimwe na zimwe z'imiterere zishobora kandi kongera ibyago, ariko izi zigize munsi ya 5% by'ibintu byose bya UPS. Abantu benshi bafite UPS nta mateka y'umuryango wa kanseri kandi nta bintu by'imiterere bizwi.

Ni byiza kuzirikana ko ibintu bijyanye n'ubuzima nk'imirire, imyitozo ngororamubiri, cyangwa itabi ntibigira ingaruka ku byago bya UPS. Iyi kanseri isa n'iterwa ahanini mu buryo butunguranye aho kuba iterwa n'ibintu bishobora kwirindwa.

Ingaruka zishoboka za undifferentiated pleomorphic sarcoma ni izihe?

Nubwo abantu benshi bafite UPS bashobora kuvurwa neza, gusobanukirwa ingaruka zishoboka bigufasha kumenya ibyo ugomba kwitondera n'igihe ukwiye kuvugana n'itsinda ryawe ry'ubuvuzi. Ikibazo gikomeye kuri UPS ni ubushobozi bwayo bwo gukwirakwira mu bindi bice by'umubiri wawe niba bitavuwe vuba.

Ingaruka zikomeye harimo:

  • Kwiyamamaza (gukwirakwira) mu mpyiko, mu gituza, cyangwa mu zindi ngingo
  • Kugaruka kw'indwara nyuma yo kuvurwa
  • Kubabara kw'imitsi niba igituntu gishyira igitutu ku mitsi ikomeye
  • Gutakaza imbaraga mu mikaya cyangwa ingingo zibasiwe
  • Ingaruka ziterwa n'ubuvuzi cyangwa ubundi buvuzi

UPS ifite ubushobozi bwo gukwirakwira mu maraso, aho imyanya y'ubuhumekero ari yo hantu hakunze kugaragara. Niyo mpamvu muganga wawe azakora ibizamini byo mu myanya y'ubuhumekero nk'igice cyo gusuzuma bwa mbere no gukurikirana.

Kugaruka kw'indwara, aho kanseri isubira mu gice kimwe nyuma yo kuvurwa, bishobora kubaho niba uturemangingo duto twa kanseri tukiguma nyuma yo kubagwa. Niyo mpamvu gukuraho igituntu rwose hamwe n'ibice byiza by'umubiri ari ingenzi cyane.

Mu bihe bidasanzwe, ibituntu binini bishobora gutera ingaruka zikomeye mbere yo kuvurwa. Ibi bishobora kuba harimo gushyira igitutu ku myanya y'amaraso, imitsi, cyangwa ingingo, bitewe n'aho igituntu kiri.

Undifferentiated pleomorphic sarcoma imenyekanwa gute?

Kumenya UPS bisaba intambwe nyinshi kugira ngo hamenyekane ubwoko bwa kanseri n'aho yageze. Muganga wawe azatangira asuzume umubiri wawe hanyuma ategeke ibizamini byihariye kugira ngo abone ishusho yuzuye.

Uburyo bwo gusuzuma busanzwe burimo:

  1. Kusuzuma umubiri n'amateka y'ubuzima
  2. Ibizamini by'amashusho (MRI, CT scan, cyangwa ultrasound)
  3. Biopsy kugira ngo harebwe umubiri kuri mikoroskopi
  4. Ibizamini by'inyongera kugira ngo harebwe niba yageze kure (staging)
  5. Ibizamini by'imiterere y'igituntu (mu bihe bimwe na bimwe)

Biopsy ni intambwe ikomeye kuko ari yo nzira yonyine yo kumenya neza UPS. Muganga wawe azakuramo igice gito cy'igituntu akoresheje umugozi cyangwa agace gato k'ubuganga.

Ibizamini by'amashusho bifasha kumenya uburebure n'aho igituntu kiri, ndetse n'aho gihuriye n'ibindi bice nk'imijyana y'amaraso, imitsi, n'amagufwa. Aya makuru ni ingenzi mu gutegura ubuvuzi bwawe.

Ibizamini byo kumenya aho kanseri igeze, bishobora kuba harimo X-rays cyangwa CT scans, bifasha kumenya niba kanseri yageze mu bindi bice by'umubiri wawe. Aya makuru agira ingaruka ku buryo bwo kuvurwa no ku kubaho.

Ubuvuzi bwa undifferentiated pleomorphic sarcoma ni buhe?

Ubuvuzi bwa UPS busanzwe burimo uburyo butandukanye buhuye n'imiterere yawe. Kubagwa ni bwo buvuzi nyamukuru, busanzwe buhuzwa n'ubuvuzi bw'imirasire cyangwa chemotherapy kugira ngo ugire amahirwe yo gukira.

Gahunda yawe yo kuvurwa ishobora kuba irimo:

  • Kubagwa kugira ngo bakureho igituntu hamwe n'ibice byiza by'umubiri
  • Ubuvuzi bw'imirasire mbere cyangwa nyuma yo kubagwa
  • Chemotherapy, cyane cyane kubintu binini cyangwa byo hejuru
  • Ubuvuzi bugenewe cyangwa immunotherapy (mu bihe bimwe na bimwe)
  • Kugarura ubuzima n'ubuvuzi bwo gufasha

Kubagwa bigamije gukuraho igituntu cyose hamwe n'ibice byiza by'umubiri biri hafi yacyo. Rimwe na rimwe ibi bisaba gukuraho imikaya, kandi mu bihe bidasanzwe, gukata umugongo bishobora kuba ngombwa, nubwo kubagwa kudakata umugongo bishoboka mu bihe byinshi.

Ubuvuzi bw'imirasire bukoresha imirasire ifite imbaraga nyinshi yo kwica uturemangingo twa kanseri kandi busanzwe butangwa mbere yo kubagwa kugira ngo hagororwe igituntu cyangwa nyuma yo kubagwa kugira ngo hacicwe uturemangingo twa kanseri dushigaje. Igihe cyabyo biterwa n'imiterere yawe.

Chemotherapy ishobora kugerwaho niba igituntu cyawe kinini, cyo hejuru, cyangwa niba hari impungenge z'uko cyakwirakwira. Nubwo UPS idakira cyane kuri chemotherapy, ishobora gufasha mu bihe bimwe na bimwe.

Itsinda ryawe ry'abaganga bazakorana kugira ngo baguhangire gahunda ikuha amahirwe yo gukira mu gihe ukomeza imikorere myinshi mu gice cyibasiwe.

Uko wakwitwara mu rugo ufite undifferentiated pleomorphic sarcoma

Kwitwara mu rugo ufite UPS bisobanura kwita ku buzima bwawe mu gihe cyo kuvurwa no gukira mu gihe ukomeza kwitondera impinduka zikenewe kuvurwa. Amahoro yawe n'imibereho myiza ni ibice by'ingenzi by'ubuvuzi bwawe.

Dore uburyo bwo gufasha ubuzima bwawe mu gihe cyo kuvurwa:

  • Kugendera ku gahunda yawe y'imiti nk'uko byategetswe
  • Komeza ahantu habaguwe hatuje kandi humye nk'uko byategetswe
  • Kugira imirire myiza kugira ngo ufashe gukira
  • Komeza ukore nk'uko muganga wawe abitegetse
  • Kwitondera ibimenyetso by'indwara cyangwa ingaruka

Witondere impinduka zose mu gice cyabaguwe, nko kwiyongera kw'umutuku, kubyimbagira, ubushyuhe, cyangwa amazi. Ibi bishobora kuba ibimenyetso by'indwara bikeneye kuvurwa vuba.

Imikino myoroheje na physiotherapy, nk'uko itsinda ryawe ry'ubuvuzi ribitegetse, bishobora gufasha kugumana imbaraga n'ubushobozi mu gihe cyo gukira. Ntukarengere imbaraga, ariko kuguma ukora umurimo uboneye bikunda gufasha mu gukira.

Kwitwara ingaruka za chemotherapy cyangwa imirasire bishobora kuba harimo kurya ibiryo bike, bikunze kubaho niba ufite isesemi, kuguma unywa amazi, no kuruhuka igihe unaniwe.

Uko wakwitegura ku bw'ihuriro ryawe na muganga

Kwitwara ku bw'ihuriro ryawe bifasha kwemeza ko uboneye igihe cyawe cyane hamwe n'itsinda ryawe ry'ubuvuzi. Kugira ibibazo byawe n'impungenge zateguwe bishobora kugabanya impungenge kandi bikabuza ikintu icyo aricyo cyose cy'ingenzi kitazibagirana.

Mbere y'ihuriro ryawe, kora ibi bikurikira:

  • Urutonde rw'imiti yawe yose n'ibindi byongera
  • Amateka yawe yose y'ubuzima, harimo kanseri zabanje
  • Amateka y'umuryango wa kanseri cyangwa indwara z'imiterere
  • Ibizamini by'amashusho cyangwa ibyavuye mu bizamini byakozwe n'abandi baganga
  • Amakuru y'ubwisungane n'amafishi yo kwerekeza niba bikenewe

Andika ibibazo byawe mbere y'igihe kugira ngo utabyibagirwa mu gihe cy'ihuriro. Ibibazo bisanzwe bishobora kuba harimo kubaza ibyerekeye uburyo bwo kuvurwa, ingaruka zishoboka, uko bizagenda, n'uko ubuvuzi bushobora kugira ingaruka ku buzima bwawe bwa buri munsi.

Tegereza umuntu w'umuryango cyangwa inshuti kugira ngo aguhe inkunga mu kwibuka amakuru yavuzwe mu gihe cy'ihuriro. Kugira inkunga yo mu mutima bishobora kandi gufasha mu gihe uhura n'indwara ya kanseri.

Ntuzuyaze gusaba muganga wawe gusobanura ikintu icyo aricyo cyose utumva. Ni ingenzi kumva utekanye na gahunda yawe yo kuvurwa kandi ukamenya icyo utegereje.

Icyo ukwiye kumenya cyane kuri undifferentiated pleomorphic sarcoma

Undifferentiated pleomorphic sarcoma ni kanseri idaheruka ariko ivurwa isaba kuvurwa vuba kandi buhamye. Nubwo kwakira iyi ndwara bishobora gutera ubwoba, abantu benshi bafite UPS bashobora kuvurwa neza, cyane cyane iyo kanseri imenyekanye hakiri kare kandi itarakwirakwira mu bindi bice by'umubiri.

Ikintu cy'ingenzi cyo kwibuka ni uko kumenya hakiri kare no kuvurwa n'itsinda ry'abaganga b'inzobere muri sarcoma byongera ibyiza. Niba ubona igituntu gikomeza gukura, ntuzategereze kugipimisha.

Ubuzima bwa buri muntu ni bwihariye, kandi gahunda yawe yo kuvurwa izahuzwa n'ibyo ukeneye. Gukorana n'itsinda ryawe ry'ubuvuzi, kubaza ibibazo, no kuguma uzi ibyerekeye uburwayi bwawe bizagufasha kumva ufite ubushobozi mu rugendo rwawe.

Nubwo inzira iri imbere ishobora kugaragara nk'ingorabahizi, ibuka ko iterambere mu buvuzi bwa sarcoma rikomeza kongera ibyiza ku bantu bafite UPS. Itsinda ryawe ry'abaganga riri aho kugufasha intambwe ku yindi.

Ibibazo bikunze kubaho kuri undifferentiated pleomorphic sarcoma

Q.1 Undifferentiated pleomorphic sarcoma ihora yica?

Oya, UPS ntihora yica. Abantu benshi bafite UPS bashobora gukira, cyane cyane iyo kanseri imenyekanye hakiri kare kandi itarakwirakwira mu bindi bice by'umubiri. Uko bizagenda biterwa n'ibintu nk'uburebure n'aho igituntu kiri, niba cyarakwirakwiye, n'uko kivura. Hamwe n'ubuvuzi bukwiye buturuka ku itsinda ry'abaganga b'inzobere muri sarcoma, abarwayi benshi bakomeza kubaho ubuzima busanzwe kandi bwiza.

Q.2 Undifferentiated pleomorphic sarcoma ishobora gusubira nyuma yo kuvurwa?

Yego, UPS ishobora gusubira nyuma yo kuvurwa, nubwo ibi bitabaho kuri bose. Kugaruka kw'indwara mu gice kimwe bibaho kuri 10-20% by'ibintu, mu gihe kugaruka kure (metastasis) ari bike. Niyo mpamvu gukurikirana inama n'ibizamini by'amashusho ari ingenzi cyane. Kumenya hakiri kare kugaruka kw'indwara biha ubuvuzi vuba, bushobora kuba bugira akamaro.

Q.3 Undifferentiated pleomorphic sarcoma ikura vuba gute?

UPS ikunda gukura buhoro buhoro mu mezi cyangwa mu byumweru, nubwo umuvuduko wo gukura ushobora gutandukana ukurikije umuntu. Ibintu bimwe bishobora gukura vuba, mu gihe ibindi bikura buhoro buhoro mu gihe kirekire. Icyiciro cy'igituntu, gisobanura uburyo uturemangingo twa kanseri tugaragara kuri mikoroskopi, gishobora guha abaganga igitekerezo cy'umuvuduko wo gukura no gukwirakwira.

Q.4 Nzakenera gukata umugongo niba mfite undifferentiated pleomorphic sarcoma?

Gukata umugongo ntabwo bikunda kuba ngombwa kuri UPS. Mu bihe byinshi, kubagwa kudakata umugongo bishobora gukuraho igituntu mu gihe umugongo usigaye. Ubu buryo bwa none bwo kubagwa, buhujwe n'ubuvuzi bw'imirasire, buha abaganga ubushobozi bwo kugera ku gukumira kanseri mu gihe imikorere isigaye. Gukata umugongo ni byo bigerwaho mu bihe bidasanzwe gusa aho ari ngombwa rwose gukuraho kanseri rwose.

Q.5 Undifferentiated pleomorphic sarcoma irasanzwe mu muryango?

UPS ntabwo ikunda kuba mu muryango. Munsi ya 5% by'ibintu bihujwe n'indwara z'imiterere nk'iya Li-Fraumeni. Abantu benshi bafite UPS nta mateka y'umuryango w'iyi ndwara kandi nta bintu by'imiterere. Kanseri ikunda gukura kubera impinduka z'imiterere ziba mu buzima bw'umuntu aho kuba zaraherwe ababyeyi.

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