Livmarli
Maralixibat ikoreshwa mu kuvura gukorora kw'uruhu (gushaka kw'uruhu) mu barwayi bafite indwara ya Alagille (ALGS) na progressive familial intrahepatic cholestasis (PFIC). Iyi miti iboneka gusa uhawe uruhushya na muganga wawe. Iyi miti iboneka mu buryo bukurikira bwo kuyikoresha:
Mu gufata icyemezo cyo gukoresha imiti, ibyago byo gufata iyo miti bigomba guhagararirwa n'akamaro izagira. Iki ni icyemezo uzatanga hamwe na muganga wawe. Kuri iyi miti, ibi bikurikira bigomba kwitabwaho: Bwira muganga wawe niba warigeze ugira uburwayi budasanzwe cyangwa ubwoko bw'uburwayi buterwa na iyi miti cyangwa izindi miti. Nanone, bwira umuhanga mu by'ubuzima ufite andi moko y'uburwayi buterwa na allergie, nko ku biribwa, amabara, ibintu byongera ubuzima bw'ibicuruzwa, cyangwa inyamaswa. Ku bicuruzwa bitagomba kwandikwa na muganga, soma witonze ibikubiye ku gipfunyika cyangwa mu byanditseho. Ubushakashatsi bukwiye ntabwo bwakozwe ku isano iri hagati y'imyaka n'ingaruka za maralixibat mu kuvura gukorora kw'uruhu hamwe na Alagille syndrome (ALGS) mu bana bari munsi y'amezi atatu, no kuvura gukorora kw'uruhu hamwe na progressive familial intrahepatic cholestasis (PFIC) mu bana bari munsi y'amezi 12. Ubuziranenge n'ingaruka nziza ntibyarangiye. Ubushakashatsi bukwiye ntabwo bwakozwe ku isano iri hagati y'imyaka n'ingaruka za maralixibat mu barwayi bakuze. Ubuziranenge n'ingaruka nziza ntibyarangiye. Nta bushakashatsi buhagije ku bagore bwo kumenya ibyago by'uruhinja mu gihe bakoresha iyi miti mu gihe cyo konsa. Pima inyungu zishoboka ugereranije n'ibyago bishoboka mbere yo gufata iyi miti mu gihe cyo konsa. Nubwo imiti imwe n'imwe idakwiye gukoreshwa hamwe, mu bindi bihe imiti ibiri itandukanye ishobora gukoreshwa hamwe nubwo hariho isano ishobora kubaho. Muri ubwo buryo, muganga wawe ashobora kwifuza guhindura umwanya, cyangwa izindi ngamba zishobora kuba ngombwa. Bwira umuhanga mu by'ubuzima ufite indi miti y'amabwiriza cyangwa itandikwamo na muganga (over-the-counter [OTC]). Imiti imwe n'imwe ntikwiye gukoreshwa mu gihe cyo kurya cyangwa hafi yacyo, cyangwa kurya bimwe mu bintu runaka, kuko isano ishobora kubaho. Gukoresha inzoga cyangwa itabi hamwe n'imiti imwe nabyo bishobora gutera isano. Gabagana n'umuhanga mu by'ubuzima wawe gukoresha imiti yawe hamwe n'ibiribwa, inzoga, cyangwa itabi. Kuba hari ibindi bibazo by'ubuzima bishobora kugira ingaruka ku ikoreshwa ry'iyi miti. Menya neza kubwira muganga wawe niba ufite ibindi bibazo by'ubuzima, cyane cyane:
Fata iyi imiti ukurikije uko muganga wawe yabikuye. Ntukarenge urugero, ntuyifate kenshi, kandi ntuyifate igihe kirekire kurusha igihe muganga wawe yategetse. Iyi miti ifite igitabo cy'amabwiriza y'imiti n'amabwiriza y'abarwayi. Soma kandi ukurebereho aya mabwiriza neza. Baza muganga wawe niba ufite ikibazo icyo ari cyo cyose. Fata iyi miti nibura iminota 30 mbere y'ifunguro rya mbere rya buri munsi. Suzuma umusemburo uri mu icupa. Igomba kuba isobanutse cyangwa hafi yo kuba isobanutse kandi idafite ibara cyangwa ifite ibara ry'umuhondo utoroshye. Ntukifashishe iyi miti niba umusemburo uhinduye ibara, cyangwa ufite ibice by'ibintu byinshi. Kugira ngo uyifate: Fata iyi miti nibura amasaha 4 mbere cyangwa amasaha 4 nyuma yo gukoresha imiti igabanya aside ya bile (urugero, cholestyramine, colesevelam, colestipol). Igipimo cy'iyi miti kizaba kitandukanye ku barwayi batandukanye. Kurikiza amabwiriza y'umuganga wawe cyangwa amabwiriza ari ku gipfunyika. Amakuru akurikira arimo gusa ibipimo bisanzwe by'iyi miti. Niba igipimo cyawe kitandukanye, ntukiguhindura keretse muganga wawe akubwiye kubikora. Ubwinshi bw'imiti ufata biterwa n'imbaraga z'imiti. Nanone, umubare w'ibipimo ufata buri munsi, igihe cyemererwa hagati y'ibipimo, n'igihe ufata imiti biterwa n'ikibazo cy'ubuzima urimo kuvura. Niba ubuze igipimo cy'iyi miti, gifate vuba bishoboka. Ariko, niba hafi igihe cyo gufata igipimo gikurikira, siyanika igipimo wabuze kandi usubire ku gahunda yawe isanzwe yo gufata imiti. Ntukarenge ibipimo. Gukoresha rimwe ku munsi: Niba igipimo cyabuze amasaha 12 cyangwa munsi yaho, gifate vuba bishoboka, hanyuma usubire ku gahunda yawe isanzwe. Niba igipimo cyabuze amasaha arenga 12, ntugafate igipimo cyongeyeho. Fata igipimo gikurikira ku gihe giteganijwe. Gukoresha kabiri ku munsi: Niba igipimo cyabuze amasaha 6 cyangwa munsi yaho, gifate vuba bishoboka, hanyuma usubire ku gahunda yawe isanzwe. Niba igipimo cyabuze amasaha arenga 6, ntugafate igipimo cyongeyeho. Fata igipimo gikurikira ku gihe giteganijwe. Komereza kure y'abana. Ntukagumane imiti ishaje cyangwa imiti utakikiri kenera. Baza umwuga wita ku buzima uko wakwirukana imiti iyo ari yo yose utabifashishije. Gabika imiti mu kibindi gifunze ku bushyuhe bw'icyumba, kure y'ubushyuhe, ubushuhe, n'izuba ry'izuba. Kwirinda gukonjesha. Gabika iyi miti ufite igipfundikizo ku icupa. Joga imiti itarakoreshejwe nyuma y'iminsi 100 ufunguye icupa.