Sapropterin (inzira yo kunywa)
Amoko ahari
Kuvan
Ibyerekeye uyu muti
Sapropterin ikoreshwa mu kugabanya urwego rwa phenylalanine mu maraso y'abarwaye phenylketonuria (PKU). Urwego rwinshi rwa phenylalanine (asidi amino) mu maraso rushobora gutera ibibazo bikomeye ku bwonko, birimo ubusembwa bukabije bw'ubwenge, ibitotsi, guhindagurika, cyangwa kugabanuka k'ubushobozi bwo kwiga. Ubu buti imyaka isanzwe itangwa hamwe na gahunda yihariye y'imirire. Ubu buti bugurwa gusa ku rupapuro rw'umuganga. Iyi miti iboneka mu buryo bukurikira bwo kuyipima:
Mbere yo gukoresha uyu muti
Mu gufata icyemezo cyo gukoresha imiti, ibyago byo gufata iyo miti bigomba guhanurwa n'akamaro izagira. Iki ni icyemezo uzatanga hamwe na muganga wawe. Kuri iyi miti, ibi bikurikira bigomba kwitabwaho:
Uburyo bwo gukoresha uyu muti
Fata iyi miti gusa nkuko muganga wawe yabikuye. Ntugafate umunaniro wayo, ntuyifate kenshi, kandi ntuyifate igihe kirekire kurusha igihe muganga wawe yategetse. Kubikora bishobora kongera amahirwe yo kugira ingaruka mbi. Iyi miti igomba kuza hamwe n'amabwiriza y'umuganga. Soma kandi ukurebereho aya mabwiriza neza. Baza muganga wawe niba ufite ikibazo icyo ari cyo cyose. Ni byiza gufata iyi miti hamwe n'ibiribwa mu gihe kimwe buri munsi. Kora neza amabwiriza ya muganga wawe yerekeye ibyokurya byihariye. Ni ngombwa ko ugumana indyo ifite umubare muke wa phenylalanine. Abarwayi bapima ibiro birenga 10, bakoresha ifu yo kuvanga mumazi: Suka ibikubiye mu icupa rya 100 mg cyangwa 500 mg muri garama 120 kugeza kuri 240 (1/2 kugeza kuri 1 igikombe) cy'amazi cyangwa umutobe w'inzuki. Vanga neza. Nunya iyi mvange mbere y'iminota 30. Ushobora kuyongera mu bwinshi buke bw'ibiribwa, nka applesauce cyangwa pudding mbere yo gufata. Abarwayi bapima ibiro birenga 10 bakoresha imiti: Ushobora kumanuka imiti yose cyangwa kuyivanga muri garama 120 kugeza kuri 240 (1/2 kugeza kuri 1 igikombe) cy'amazi cyangwa umutobe w'inzuki mbere yo gufata. Bishobora gufata iminota mike kugirango imiti ikemuke. Kugirango imiti ikemuke vuba, ushobora kuyikubita cyangwa kuyimenagura. Nunya iyi mvange mbere y'iminota 15. Ushobora kandi guca imiti hanyuma ukayivanga mu bwinshi buke bw'ibiribwa byoroshye, nka applesauce cyangwa pudding mbere yo gufata. Igipimo cyiyi miti kizaba kitandukanye ku barwayi batandukanye. Kora amabwiriza ya muganga wawe cyangwa amabwiriza ari ku kinywanyi. Amakuru akurikira harimo gusa ibipimo by'iyi miti. Niba igipimo cyawe kitandukanye, ntukiguhindura keretse muganga wawe akubwiye kubikora. Ubwinshi bw'imiti ufata biterwa n'imbaraga z'imiti. Nanone, umubare w'ibipimo ufata buri munsi, igihe cyemererwa hagati y'ibipimo, n'igihe ufata imiti biterwa n'ikibazo cy'ubuzima uri gukoresha imiti. Niba ubuze igipimo cyiyi miti, gifate vuba bishoboka. Ariko, niba hafi igihe cyo gufata igipimo cyawe gikurikira, sipa igipimo wabuze hanyuma usubire ku gahunda yawe isanzwe yo gufata imiti. Ntukarengere ibipimo. Komereza kure y'abana. Ntukagumane imiti ishaje cyangwa imiti idakenewe ukundi. Baza umwuga wita ku buzima uburyo wakwirukana imiti iyo ari yo yose utabeshya. Gabanya imiti mu gikombe gifunze ku bushyuhe bw'icyumba, kure y'ubushyuhe, ubushuhe, n'umucyo ugaragara. Kwirinda gukonjesha. Komereza icupa rifunze neza. Komereza imiti mu icupa ryambere wari wahawe muri farumasi.
Umuhakana: Kanama ni urubuga rw'amakuru y'ubuzima kandi ibisubizo byayo ntibigize inama z'ubuvuzi. Jya ubona umuganga ufite uruhushya rwo gukorera hafi yawe mbere yo gukora impinduka izo ari zo zose.